COLUMBIA LIBRARIES OFFSITE HEALriKiCII NCI '.'.[MIUmD HX00030430 mi- :'-V:' Digitized by the Internet Archive in 2010 with funding from Open Knowledge Commons http://www.archive.org/details/acutecontagiousdOOwelc ACUTE CONTAGIOUS DISEASES. BY WILLIAM M. WELCH, M.D., DIAtiNOS'ilCIAN TO THli BUREAU OIC HEALTH AND CONSULTING PHYSICIAN TO THE PHILADKLPHIA MUNICIPAL HOSPITAL FOR CONTAGIOUS AND INFECTIOUS DISEASES; FOR THIKTY-THREK YEARS PHYSICIAN-IN-CHARGE OF THE MUNICIPAL HOSPITAL; FELLOW OF THE COLLEGE OF PHYSICIANS OF PHILADELPHIA; AND JAY F. SOHAMBERG, A.B., M.D., PROFESSOR OF DERMATOLOGY AND OF INFECTIOUS ERUPTIVE DISEASES, PHILADELPHIA POLY- CLINIC AND COLLEGE FOR GRADUATES IN MEDICINE; ASSISTANT DIAGNOSTICIAN TO THE BUREAU OP HEALTH AND CONSULTING PHYSICIAN TO THE MUNICIPAL ^ HOSPITAL FOR CONTAGIOUS AND INFECTIOUS DISEASES; FELLOW OF THE COLLEGE OF PHYSICIANS OF PHILADELPHIA; MEMBER OF THE AMERICAN DERMATOLOGICAL ASSOCIATION. ILLUSTRATED WITH 109 ENGRAVINGS AND 61 FULL-PAGE PLATES. LEA BROTHERS & CO., PHILADELPHIA AND NEW YORK. 1905. Entered according to the Act of Congress, in the 3'ear 1905, by LEA BROTHERS & CO., In the Office of the Librarian of Congress. All rights reserved. DOEN.'VN, PRINTER. PREFACE. In this work on Acute Contagious Diseases the writers have endeav- ored to present a practical treatise for the guidance of students and practitioners of medicine. Perhaps some explanation may be sought for the adoption of the title. We have somewhat arbitrarily included in this work but a small group of diseases, particularly those with which we have had experience in the Municipal Hospital of Philadelphia. The use of the term "infectious diseases" would have necessitated the inclusion of a great number of maladies upon which we do not feel specially qualified to write. Furthermore, the group of contagious diseases is distin- guished by great transmissibility, being communicated by the merest contact or even by proximity, and therefore the term in its strict etymological sense appears to us to be justified. Vaccinia is, of course, not contagious, but its relation to the prophylaxis of smallpox makes the consideration of the two inseparable. The comparative infrequency of epidemics of smallpox renders it quite possible for accomplished and otherwise experienced physicians to be somewhat unfamiliar with this disease. We have, therefore, devoted to this affection, and particularly to its diagnosis, an amount of space not usually accorded to it in text-books of medicine. We have furthermore endeavored to elucidate the subject-matter with numerous photographs of patients under our care. The text is based upon a personal study of over 9000 cases of smallpox, 9000 cases of scarlet fever, and 10,000 cases of diphtheria, in addition to a considerable number of cases of the other diseases discussed, all of which have been treated in the Municipal Hospital of Philadelphia during the past thirty-five years. vi PREFACE We desire to acknowledge our indebtedness to Dr. E. L. Graf, formerly Resident Physician in the Municipal Hospital, for assist- ance in securing some of the photographs; to Dr. Burton K. Chance, for the contribution of the chapters on Eye Complications and Treat- ment in Variola; and to the publishers^ Lea Brothers & Co., for the uniform courtesy extended to us. W. M. W. Philadelphia, Mat, 1905. t xri o J. r. o. CONTENTS. CllAVlTAi I. PAGE Vaccinia 17 CHAPTER II. The Relationship oi- Cowpox or Vaccinia to Smallpox 87 CHAPTER III. The Variolous Diseases of Lower Animals 135 CHAPTER IV. Smallpox 144 CHAPTER V. Complications and Sequels of Smallpox 229 CHAPTER VI. Chickenpox 316 CHAPTER VII. Scarlet Fever 341 CHAPTER VIII. The Diagnosis of Scarlet Fever 447 CHAPTER IX. Measles 476 ,•;; CONTENTS VUl CHAPTER X. PAGE 547 Rubella CHAPTER XI. Typhus Fever CHAPTER Xn. .... 598 Diphtheria CHAPTER Xni. The Treatment of Diphtheria CHAPTER XIV. The Serum Treatment of Diphtheria 730 CHAPTER XV. Disinfection (MIAPTER r. VACCINIA. Synonyms. ^ — Latin, vaccinia, or variola vaccina; fJenner); P^nglish, cowpox or Jcinepox; French, la vaccine; German, Kuhpocken, ImpfpocJcen, Schutzbldttern; Italian, vaccinia; Spanish, vacuna. Definition. — Vaccinia is a disease commiinical^le only by inocula- tion, and is characterized by one or more skin lesions, accordinf( to the number of insertions of the specific virus, running through the stages of papulation, vesiculation and pustulation, ending in desiccation and falling of the crusts at the end of the third week. The process is attended * by slight febrile disturbance, and when completed confers immunity against smallpox. History.— When Edward Jenner was pursuing his professional studies with his master at Sodbury, a young country woman, on hearing small- pox mentioned, immediately observed, "I cannot take that disease, for I have had the cowpox." This incident created a deep impression in the mind of the young medical student, and may be said to have been the awakening impulse, which, after years of patient study and experi- ment, culminated in a discovery which has conferred the greatest bene- fits upon the human race. To properly appreciate the life-saving value of Jenner's discovery it is necessary to know something of the fearful mortality of smallpox in the prevaccination days. It was the most dreadful of all scourges, not excluding the plague, for that disease came but rarely, while small- pox was always present. Admiral Berkeley, chairman of the committee of the House of Commons (in 1S02) to investigate the petition of Jenner for a Parliamentary grant, in an elociuent speech said:^ "The discovery of Dr. Jenner is unquestionably the greatest discovery ever made for the preservation of the human species. It is proved that in these united kingdoms alone 45,000 persons die annually of the smallpox; but through- out the world what is it? Not a second is struck by the hand of time but a victim is sacrificed at the altar of that most horrible of all dis- orders, the smallpox." King Frederick William III. of Prussia stated in 1803 that 40,000 people succumbed annually to smallpox in his kingdom. The French Minister of the Interior, in reporting on vaccination in 1811, estimated that 150,000 persons died annually in France from smallpox. In ' Quoted by Baron. Baron's Life of Jenner. 2 18 VACCINIA Russia smallpox is reported to have destroyed 2,000,000 lives in a single year.^ The mathematician, BernouilK, calculated that not less than 15,000,000 human beings died of smallpox every twenty-five years, which would give a yearly average of 600,000. Dr. Lettsom estimated that Europe alone claimed 210,000 victims each year. When to this number are added the deaths produced by devastating epidemics in Asia, Africa, and America, the aggregate estimate mentioned is seen to be conser- vative. The early records of the London Asylum for the indigent blind showed that three-quarters of the inmates had lost their sight through smallpox.^ De la Condamine says that this disease destroyed, maimed, or disfigured the fourth part of mankind. Traditions Concerning Cowpox Protection. — The fact that cowpox con- ferred protection against smallpox appears to have been noticed by dairymen in England as far back as the middle of the eighteenth cen- tury. It was observed by these people that when smallpox prevailed, those who had been accidentally infected by the matter exuding from certain sores, known as cowpox, which often appeared on the teats • and udders of cows, resisted the infection of smallpox. It is said that Benjamin Jesty, a Yetminster farmer, was the first person in England to employ cowpox virus for the purpose of protecting against smallpox. In 1774 he vaccinated his wife and children with matter taken from the teats of cows that had the cowpox. In about a week the arms became inflamed and considerable constitutional dis- turbance was present. The children were later inoculated with small- pox matter without result. In Germany the protective influence of cowpox was known and prac- tised prior to this date. Jobst Bose, a government official, called atten- tion (General Conversations of Gottingen, part 39, May 24, 1769) to the fact that the protection conferred by cowpox against smallpox was recognized by reputable persons. He says: "I am reminded of the not unknown attacks of cowpox which were prevalent in this country, and to which to this day milkmaids are subject. In passing I wish to remark that, in this country, those who have had the cowpox flatter themselves to be entirely free from all danger of getting smallpox, and assert, as I myself, to have heard this same statement made by entirely reliable persons."^ In 1791 a school teacher by the name of Piatt, who lived in Starken- dorf, near Kiel, vaccinated several children of his landlord to protect them against a prevailing epidemic of smallpox. Several years later they escaped smallpox, although intimately exposed to the disease. He was prompted to perform this procedure by the popular belief concern- ing cowpox protection that prevailed in Saxony and in Holstein. A 1 Woodville on Smallpox. Quoted by Baron. 2 According to Sir William Aitken 90 per cent, of the cases of blindness met with in the bazaars in India are due to same disease. 3 Quoted by Kubler, History of Smallpox and Vaccination, Berlin, 1901. Kubler states that the writer of the above commentaries was a man with practical experience in farming. DISaOV/'^RV OF VAC'CTNATfON 19 Holstein fanner, JeiiscMi by iiuine, is also said to have etii{)lrjyed prophy- lactic cowpox inoculation. The same tradition, according to Humboldt, existed in certain parts of Mexico for many years, and similar statements are made concerning this belief in Baluchistan. But it remained for Jenner to crystallize this half -forgotten tradition into a scientific theory, and then, by painstiiking study and experiment, to establish its truth and prove it to the world. Referring to the vaccinations performed prior to -Tenner's time, Dr. Baron says: "They did not advance the knowledge or the practice of vaccination beyond what casual observation and popular rumor had rendered common in many districts; if indeed they ever took place (which I think more than doubtful) they were quite unknown to Dr. Jenner, and had it not been for his publication they never would have been drawn forth from their obscurity." Early Practice in England. — Edward Jenner was born in the vicarage at Berkeley, in Gloucestershire, in 1749. He was the third son of Stephen Jenner, rector of Rockhampton and vicar of Berkeley. He exhibited an early taste for natural history, and as a boy interested himself in zoology and geology. After his scholastic education was finished he removed to Sodbury, where he became apprenticed to Mr. Ludlow, an eminent surgeon there, to be instructed in surgery and pharmacy. In 1770 he went to London to study medicine under the direction of the celebrated John Hunter, with whom he lived for two years. In 1778 Jenner won the fellowship of the Royal Society, chiefly through his admirable essay On the Natural History of the Cuckoo. Despite his studies in natural history, the tradition concerning cowpox gave him much food for thought and was frequently mentioned by him in conversation with his friends. After completing his course in medicine and locating in Berkeley, England, where dairy farming was common, Jenner gave close atten- tion to this tradition, and it was not long until he was convinced of its reality. In medical coteries and societies he frequently expressed his belief in the protective power of cowpox, but his views on this subject were always regarded by his confreres as idle fancies of an overcredii- lous mind. On one or more occasions, in a certain medical society to which Jenner was a liberal contributor, the proposition was made, half earnestly and half jokingly, to expel him if he did not cease boring them with his absurd notions about the prophylactic power of cowpox. But the evidence he had already collected from various sources was too convincing to be set aside by such idle threats. At length, after having devoted much time and thought to the sub- ject, Jenner determined to inoculate into a human being the vaccine disease, and to test its efficacy by actual experimentation. James Phipps, a lad of eight years, has had his name made historical by ha%ing been the first subject to undergo the experiment. The wus used was taken from a vesicle on the hand of a milkmaid named Sarah Xelms, who had been accidentally infected while milking a cow. This vaccina- 20 VACCINIA tion was performed May 14, 1796, and was the beginning of Jenner's work which has made his name immortal. On the second day of July following Jenner proceeded to test the efficacy of this vaccination by inoculating the lad with smallpox matter taken from a patient suffering from that disease, but no result followed. At various intervals after- ward, until this lad grew to be a man, he was inoculated with smallpox matter, in all as often as twenty times, and each time was found to be immune to that disease. It is no wonder, then, that Jenner arrived at the conclusion in his treatise on vaccinia that a single vaccination con- fers permanent immunity from smallpox. The course of the vaccine disease in this case was very carefully noted by Jenner each day fram the time the virus was introduced until the crust came off spontaneously, and, finding the affection was benign and wholly unattended by unpleasant results, he proceeded to subject others to the "new inoculation," as vaccination was called in those days. All his early cases were subjected to the same crucial test that was applied in the case of James Phipps, to prove the protective power of cowpox. It will thus be seen that the investigations of Jenner were conducted so carefully and thoroughly as to demonstrate most con- clusively the value of his discovery before he ventured to publish his observations to the world. Quoting his own words: "I placed it on a rock, where I knew it would be immovable, before I invited the public to look at it." It was not, therefore, until Jenner felt perfectly secure of his position that he ventured to detail his experiments and formulate his conclusions in a paper. This paper was prepared in 1797. It was Jenner's inten- tion that this should first appear in the Transactions of the Royal Society, but this design was abandoned and the work subsequently appeared as an independent publication. In 1798 he published it as a modest brochure, entitled An Inquiry into the Causes and Effects of the Varioloe VaccincB, a Disease Discovered in Some of the Westerji Counties of England, Particularly Gloucestershire, and Known by the Name of Cow- pox. This publication at once attracted great attention from the medi- cal profession in London and throughout England. Like all innova- tions, the "new inoculation" was viewed favorably by some, with distrust and skepticism by others, while a few resolved to test it for themselves. Among the first in London to make use of the new discovery were Dr. George Pearson, physician to St. George's Hospital, and Dr. William Woodville, physician to the Smallpox and Inoculation Hospital. But the early work of these gentlemen tended to impair confidence in vac- cination. They reported that vaccinia was attended with a generalized eruption more or less copious, resembling that of variola. When Jen- ner's attention was called to the matter he denied that such a result followed true vaccinia, and, on investigating the cases presenting this eruption, he found that Woodville had carelessly permitted the virus which he and Pearson were using to become contaminated with the KAIUA' IIISTOnV OF V/\ CCINA T/0 \' 21 infection of sinallpox. A coiisi(lorji})l(; ((uuntify of lliis virus was sent by these gentlemen to viirioiis j),'irts of Eii/^land aixl tfic C>)ntinent, and in many instances its use was followed by disastrous results. Foreseeing that vaccination was likely to be (Jiseredittive of vaccinia, and recpiested that they he ^iveri to sf>nie careful and dis- cerning practitioner — to his own family physician, if he preferred. He also sent a lengthy letter full of instruction as to the use f)f the virus, and courteously reim"nded the ('resident that amidst the pelting storms of his adversaries Jenner had the countenance of his sovereign; that the Duke of York v\^as a patron of the London Vaccine Institution; that Bonaparte took a lively interest in the dissemination of vaccination in France, and so did the German nobility at the Court of Vienna. He e.xpressed the hope that the President of the United States would lend his influence to extend the blessings of the new discovery to the Middle and Southern States, believing, as he said, if it came from the hands of the Chief Executive of the nation it would make a greater and more favorable impression on the minds of the public. The President's reply convinced Waterhouse that he had made Jio mistake in the course he decided upon. The virus which had been sent him was entrusted to a judicious and successful physician, but it failed to communicate the vaccine disease. So also did the second and even the third lot sent to the President by Waterhouse. A number of com- munications passed between these gentlemen, when at last Jefferson suggested that as the weather was warm the virus be placed in a small vial hermetically sealed, and that this vial be immersed in water in a larger one, which must also be hermeticallly sealed. The virus thus conveyed was used on some members of the President's family by Dr. Wardlaw, of Monticello, and proved successful. This occurred August 6, 1801. From his own family the President supplied Dr. Gantt, of Washington, with a small quantity of vaccine matter, and thus was the seed of vaccination planted at the capital of the United States. All apphcations made to the President for virus received his careful attention. To him belongs the honor of sowing the seed of vaccination not only in the District of Columbia, but in Pennsylvania, Maryland, Virginia, and the States farther South. He studied the process of vaccinia so carefully that he was able to advise others as to the proper time for taking the virus. This period he fixed at eight times twenty- four hours from the date of vaccination. His advice in this matter, we regret to say, was frequently disregarded by physicians, who be- lieved themselves wiser than he, but never Avithout detriment to vaccin- ation. Waterhouse had the satisfaction of knowing that the virus which first proved effective in New York City came from him. To speak more definitely, it was taken from the arm of Governor Sargent's domestic, who had been vaccinated in Boston by Waterhouse, and thence was inoculated into several persons in New York City, on ]May 22, 1801, by Dr. Valentine Seaman. Vaccine virus first reached Philadelphia in an eft'ective state November 9, 1801. It was forwarded by Jefferson, through Mr. John Vaughan, to Dr. John Redman Coxe, and was accompanied by a personal letter from the President, full of valuable instruction as 30 VACCINIA to its proper use. The first person who is said to have been successfully vaccinated in Philadelphia was Dr. Coxe himself. Soon after Jenner's brochure was published there appeared in almost every civilized country in the world one or more supporters of the new discovery who adhered more faithfully than others to the teachings of the master, and consequently achieved distinction in this new field of beneficent work. Waterhouse, of Boston; Sacco, of Milan; and De Carro, of Vienna, were the most faithful followers of Jenner. Of his many disciples, Waterhouse was probably the ablest and worthiest. It is, perhaps, not too much to say he was so regarded by the great benefactor himself. The published letters of Jenner clearly indicate his high esteem of this disciple. He well deserved the confidence of the master; for, single handed and alone, in his own city, he faithfully and earnestly defended and vindicated vaccination against the ridicule of the profession and the prejudice of the public for seven years, or until conviction became too strong for argument, and theoretical objections were forced to give way to stubborn facts. So earnestly, constantly, and successfully did Waterhouse devote his time and talent to the dissemination of vaccina- tion in this country, and always so precisely in accordance with the teachings of Jenner, that he received the complimentary title of the "Jenner of America;" not, as might be supposed, by favor of the medi- cal profession of his own country, but by the unanimous voice of the London Medical Society. THE HYGIENE OF VACCINATION. In order that a vaccination may pursue a perfect course and remain free of subsequent complications it is important that certain precautions be observed. These may be classified as follows: Care as to (1) purity of the vaccine virus; (2) condition of the vaccinee; (3) asepsis dur- ing insertion of the virus; (4) subsequent protection of the vaccine lesion. Purity of Vaccine Virus. — Vaccine virus may be of human or bovine origin. Within recent years the use of calf-lymph has become generally and, indeed, almost universally adopted. The German government^ in 1884 passed a law that vaccinations and revaccinations in the Empire of Germany be performed exclusively with animal vaccine.^ Humanized Virus.— In cases where it is necessary to employ human- ized lymph, it is best taken from a vaccine pock from the fifth to the eighth day. Virus should only be used from a perfect, primary, vaccine vesicle containing clear or opalescent fluid. Where there is excessive inflammation or any other irregularity present, the vaccinifer should be rejected. The employment of the contents of lesions which have become 1 Resolution of the Imperial Vaccine Commission of 1884 ; approval of the resolution by the Bundesrath, 1885. - In Mexico humanized lymph is still extensively employed, and is preferred by the physicians of that country to bovine virus. Till': II Yd I EN K OF VACCINATION 31 purulent is strongly to he condemned. Jcniicr's dicfinii \v;i.s flujl lympli should never he taken from a lesion after the fornuition of th(r areola; this he regarded as the "golden rule of vaccination." 'I'he vaccine crust is inferior to direct arm-to-arm vaccination with fhiiri lymph. When a crust is employed at the present day it should be moistened v^ith boiled water and rubbed up upon a sterile piece of glass. The condition of health of the vaccinifer is of the greatest importance. When humanized virus is employed careful incjuiry as to the health of the parental antecedents should be made. The subject from whom the vaccine is obtained should be in thoroughly good health. The greatest care should be taken to determine that the vaccinifer is free of hereditary syphilis. While the transmission of this disease by vaccina- tion is extremely rare, its possibility is sufficiently well established to warrant every precaution being taken. It is the custom to obtain vaccine virus only from young subjects; these are, of course, less apt to be suffering from certain transmissible diseases. It is well, however, that the infant vaccinifer should have reached the age of six months or thereabouts, so as to have passed the period at which evidences of hereditary syphilis usually make their appearance. To obtain human vaccine lymph the vesicle, after having been pre- viously cleansed with soap and boiled water, should be punctured in several places with a lancet and the droplets of lymph allowed to flow out. These are then transferred upon a clean lancet to the individual about to be vaccinated; or if the lymph is to be used later or employed upon some one at a distance, it may be collected in a sterile capillary tube. After the vesicle is punctured the tube is thrust through the opening, the lymph filling the tube by capillary attraction. When it is about two-thirds full the tube is withdrawn and the ends sealed by heating them in a Bunsen flame. The tubes should be kept in a cool place until used. To expel the lymph from the tube the ends should be broken off and the fluid blown out with a small rubber bulb. At the present day we are chiefly concerned with hovine lymph . This material is employed in two different forms — as a lymph and as a vesicle pulp. Lymph, which is the clear fluid contents of well-developed vac- cine vesicles, has been in use a long time. Pulp, which is a combination of the lymph and the interior epithelial structure of the pock, has more recently come into favor, and is at the present time regarded as possessing greater vaccinal activity than the clear fluid. Vaccine lymph is used either in the dry form upon strips of ivory or celluloid (so-called "dry points") or in sealed capillary tubes in the form of a glycerin emulsion. There is a growing sentiment among the best observers in favor of the use of glycerinated lymph. This form of lymph has the sanction and endorsement of the British Royal Vaccination Commission. The method of preparation of dry and glycerinated lymph is elsewhere considered. Condition of the Vaccinee. — There is nothing in the condition of a child that constitutes a sufficient contraindication to the performance 32 VACCINIA of vaccination, if there be liability of exposure to the infection of small- pox. We have vaccinated scores of children suffering from scarlet fever and diphtheria in the Municipal Hospital during the presence on the grounds of smallpox cases. We have never seen any untoward results from vaccinating these patients, but the vesicles have not always been as perfect as we would have liked to see them. When smallpox is not prevalent it is proper for physicians to exercise discretion in choosing the time for the vaccination of an infant. There being no urgency, the medical adviser may wait until the child has reached a favorable age and is in good condition for the reception of the vaccine disease. Age of Child. — In order that the proper protection against smallpox may be granted to infants it is advisable that they should be vaccinated during the first year of life. The vaccination laws of Germany require that every child be subjected to this measure before the expiration of the first year of life, unless it is contraindicated by reason of poor health. The age which is generally considered most appropriate is between Jour and six months, for at this period the child has not yet begun to be dis- turbed by the process of dentition. If there be danger of smallpox there is no reason to delay because of the tender age of the child. We have on a number of occasions vaccinated infants immediately upon their appearance into the world, and we do not recall any bad effects that have resulted from such early vaccinations. Indeed, we have been impressed with the very slight degree of constitutional disturbance that has attended such vaccinations. Where, however, no haste is necessary, we deem it well to wait for several months until the child becomes stronger and more accustomed to its mundane environment. Health of the Child .^ — It is best to delay the performance of vaccina- tion (provided smallpox be not prevalent) if the child is poorly nour- ished, or suffering from diarrhoea or vomiting, scrofulous glands, eczema, etc., or if the infant has been recently weaned or placed upon some new food. Vaccination of such children is prohibited by the regulations of the English Local Government Board. In general terms it may be said that when smallpox is not prevalent the physician may select such time for the vaccination of an infant as may find it in the best physical condition. TECHNIQUE OF VACCINATION. Vaccination being in a sense a surgical procedure, its performance must be guarded by those precautions of asepsis which at the present time apply to all chirurgical manipulations. Laboratory studies and practical experience have both shown that even in the most trivial of all surgical procedures — the introduction of a hypodermic needle into the skin — certain precautions as to bacterial cleanliness are necessary. Many years ago, before the days of bacteriology, this truth was not known and consequently proper care was not, as a rule, observed either in surgery or in the practice of vaccination. TECIINIQIJI': OF VACfUNATION \\\\ Asepsis.- It is, of course, dcsirahlc that the vaccine lynipli he free of foreign bacteria. In oi'der that all wcjurui infections niay be avcjifled it is advisable that the arm of tlu; vaccinae, the instrutiKint to be em- ployed, and the hands of the vaccinator 1)6 perfectly clean. Further- more, the vaccine vesicle must l)e so y)r()te(-ted as to prevent subsecjuent infection at the site of vaccination. Disinfection of the Skin. Some difference of ojjinion exists as to the thor()U(>;hness with which disinfection of the j)roj)()sed vaccination area should be carried out. Some writers urj^e such a preparation of the skin as is practised prior to an ordinary surgical operation. Others believe that the use of strong antiseptics is to be avoifled, inasmuch as they may destroy the activity of the vaccine material when placed upon the skin. We would counsel the following techni(jue: It is advisable for the patient to take a tub bath on or before the day on which the vaccination is to be performed, and to put on clean undergarments. fUnfoitunately, it is difficult to have these measures carried out in the very people who most need them.) The vaccination area, usually the arm, is to be thoroughly washed with potash soap and hot water, some friction being used so as to dis- tend the cutaneous capillaries. Personally, we prefer to follow this cleansing with the application of alcohol, although in cleanly persons this is perhaps not necessary. The arm is then to be dried with sterile absorbent cotton, or, when this is not available, a perfectly clean towel. The operator may employ an ordinary lancet or a needle to produce the necessary abrasion. If the former is used it should be previously disinfected by boiling, immersion in an antiseptic solution, or thorough cleansing with soap and water or alcohol. It is perhaps better to employ a needle for the purpose, inasmuch as a new and clean one can be used for each vaccination. The insertion of the deltoid muscle is the site usually selected for the introduction of the virus. The skin is made tense through the grasping of the inner side of the arm with the left hand. The epidermis is then abraded over an area of a third or a half inch; this is done either by vertical or cross scarification with a needle or simple scraping with a lancet or scalpel. It is important that the ahrasion he not too deep. The drawing of blood is to be avoided, inasmuch as it may float away the lymph and prevent absorption; it is further claimed that the deep scarification is more likely to be followed by an excessive degree of inflammation. It is not desirable to abrade deeper than is necessary to see the little red- dish points which represent the loops of the papillary bloodvessels. It is a matter of some importance to rub the virus well into the abraded surface. The hasty smearing of the hiiiph upon the arm with no further manipulation is probably responsible for a certain percentage of failures. Some writers have advocated vaccination by hypodermic or, rather, intradermic puncture. This is accomplished by expelling the iMnph upon the previously cleansed vaccination site, and then passing a thoroughly 34 VACCINIA sterile hypodermic needle obliquely through the skin over this area. Several punctures should be made v^ithin an area of 1 cm. square, but they should not be deep enough to draw blood. The puncture carries the lymph into the skin. The alleged advantage that little or no scar results from this method appears to us to be in reality a disadvantage — for the presence of a scar and its character constitute, as a rule, visible evidence of the amount of protection against smallpox which the individual enjoys. We therefore see no special advantage of this over other methods of vaccination. It is best to allow the lymph to dry upon the arm by exposure to the air; this will ordinarily take from ten to thirty minutes. Where it is inconvenient to keep the arm bared for this time, there is no objection to protecting the abraded surface for a few hours with a loosely fitting shield made of pressed linen. It is important that no shield should be applied which congests the parts by peripheral pressure or which exerts any suction. The vaccine vesicle when formed should be sedulously guarded against mechanical violence or injury. Nature provides an excellent protective covering for the vaccine wound — a hard, concrete, firmly attached crust. This crust is formed by desiccation of the vaccine pock. When the vesicle is ruptured by traumatism, some of the con- tents escape and form an irregular, friable crust which is easily detached, leaving an open wound which is liable to infection with pathogenic organisms. Shields. — Various forms of shields have been devised to protect the vaccine lesion from injury and infection. Many of these have failed utterly of their purpose, and some have done actual injury by increasing the inflammation, and by rubbing off the scabs and thus producing open sores. Some writers condemn all shields; we have seen a few made of a light metal like aluminum which appeared to protect the vaccine lesions from the adhesion of the sleeve and from accidental injury without exerting any injurious compression. The use of such a shield, which can be easily sterilized, may be recommended. The application of a sterile gauze compress over the vaccine vesicle is also advocated; there is no objection to this save where the vesicle becomes ruptured, when the crust will adhere to the gauze and be torn off with its removal. Patients should be advised not to allow the sleeve of the shirt or undershirt to rub against the vaccine vesicle. It is often a good plan to have a thoroughly clean piece of linen sewed into that portion of the sleeve which comes in contact with the vesicle. Caution should be given patients against rubbing, scratching, or otherwise fingering the vaccination scab; manipulation of this character is a fertile source of ulceration and late wound infection. Number of Insertions. — It is the custom abroad to insert the lymph at several sites. When this is done the scarifications should not be too close, for fear of interfering with the vitality of the intervening skin, thus leading to sloughing. It is best to allow three-quarters of an inch 8YMPT0MH AND ractice (jf a col- leajijue — thirteen attempts at vaccination to he made Ix-fore a snccessfnl result was obtained. Insusceptibility to vaccinia, or rather failure of result after repeated attempts to vaccinate, does not of necessity indicate an insusceptibility to smallpox. We recall to mind a youn^ ])hysician who had been repeatedly vaccinated in childhood aiul youth without successful result, who on brief exposure to a mild case of variola contracted a severe attack of confluent smallpox. We have also in mind a young woman wlio fell ill with hemorrhan;ic smallpox, although she liad had seven unavailing trials at vaccination made upon her, three of which were performed within a year preceding the attack of smallpox. The late Mr. Spurgin, of Northampton, forwarded some years ago to the Epidemiological Society the particulars of a case in which in 1825, a boy fourteen years old, whose family was greatly opposed to vaccination, was inoculated with variola six or seven times without any result, that disease being then prevalent. The father then allowed vaccination to be tried, and the boy was vaccinated six or seven times, but equally without effect. About a year after, when at a distance from home, he contracted natural smallpox of the discrete kind, and went through the disease favorably (Seaton). REVACCINATION. Experience has demonstrated the fact that in a certain number of persons the protection from vaccinia in infancy is permanent, while in others it gradually diminishes, and after the lapse of a number of years may become entirely extinguished. The extinction of immunity is evi- denced by the large number of persons in adolescent and adult life who are susceptible of revaccination; also by the observation that in all epi- demics of smallpox a large proportion of the cases occur among persons who were vaccinated in infantile life. The statistics of smallpox hospitals in this country and in England show that from 41 to 78 per cent, of the admissions are postvaccinal cases. It is very difficult to determine the proportion of persons vaccinated in infancy that fail of permanent pro- tection, but it is beheved to be not far from 75 per cent. Some yeais ago a very careful observation in a certain American city showed that of 2362 persons revaccinated with reliable virus (no child under twelve years old with a good scar being included in this nimiber) 77.1 per cent, were susceptible to some form of vaccinia. We have no means of ascertaining the age or period of life at which the protection from vaccinia in infancy is liable to diminish or cease entirely, save by applying the test of revaccination or by noting at what age after primary vaccination any considerable number of persons suffer from smallpox. Data tending to demonstrate the latter may be found in the followino- table: 46 VACCINIA Cases. Deaths Percentage of deaths. Under one year j Unvaccinated Vaccinated Unvaccinated Vaccinated in infancy, good scars " " " fair " " " poor " Total number vaccinated Unvaccinated Vaccinated in infancy, good scars " " " fair " " poor " Total number vaccinated Unvaccinated Vaccinated in infancy, good sears " " " fair " " " poor Total number vaccinated 134 2 g6 64.18 0.0 676 280 41.42 One to seven years .... 11 11 16 1 1 0.0 9.09 6.25 . 38 2 5.26 320 61 24 64 87 2 2 9 27.19 Seven to fourteen years . . 3.28 8.33 14.06 L 149 13 8.72 r 1742 868 49.83 Fourteen years and upward 1864 894 1240 138 114 313 7.4 12.75 25.24 3998 565 14.13 Among over 9000 cases of smallpox admitted to the Municipal Hos- pital of Philadelphia during the past thirty-four years we have admitted only two vaccinated patients under one year old. One of these was a child eleven months old who had been vaccinated two months pre- viously and showed a good scar. The eruption consisted of only six small vesicles, and the child's health was scarcely at all disturbed. The other patient had the diseass so indistinctly marked that it was almost impossible to feel certain of the diagnosis of varioloid. An exceedingly modified form of smallpox was occasionally seen among well-vaccinated children between the ages of one and seven years, but no deaths occurred except where there was a serious complication. The child that died, whose case is classified under the head of "fair scars," was a foundhng about a year old, badly nourished and very feeble, with a disordered digestion. The eruption consisted of only a very few small vesicles. Death really resulted from inanition. Very little need be said of the cases classified in this age period under the head of "poor scars," as the vaccination in them had been in good part either imperfect or spurious. The query is often asked, What constitutes a successful revaccina- tion ? This is a question about which there is considerable diversity of opinion. Many believe that, unless the vesicle and areola observe the course of true vaccinia, the effect is merely local and devoid of prophy- lactic power. But it is evident on a little reflection that there is no more reason why we should expect the vaccine disease produced by revac- cination to be typical than we should expect smallpox after vaccination to run the typical course of variola vera. If there be modified smallpox or varioloid after vaccination, so should there be modified vaccinia or UKVAddlNATION 47 vaccinoid. l^'rom tlicsc; premises the coiicliision m;iy Ix' (Iciliiccrl thai }is varioloid conlors iitiiniiiiity a(i;a,iii,sl a rcciirrcncc oF smallpox, so also (Iocs tlic inodificd form ol" vaccinia, I'csiilliii^ IVoiri rcvaccinalioii rciriove froni the individiiaJ whatever siisccplihilily U> the disease riiay he present. It is frecjucntly a matter of ^reut didiculty in revaccinations to dis- tinfi;uish between irritative local reactions and lesions which rcsnit from the S])ecific action of the vaccine princij)le. Course of Revaccination. The S(;a h's 5X RETROVACCINATION OR VACCINATION FROM TKE HUMAN SUBJECT BACK TO THE BOVINE SPECIES. The inoculation of lyin[)li from a Imiiian vaccination into tin; cow produces quite constantly a ty})i('al vaccine lesion. 'J'his expedient was at one time resorted to with the viev^^ of restoring j)otency to the"" attenuated lymph of lonf^" humanization. ]\Iost careful investij^ators concluded, however, that lonr^ humanized virus so transplanted gained neither in strength nor in purity, and, indeed, became more difficult to retransfer back to the human subject, although this (Jifficulty was overcome in the second human remove. Retrovaccination is seldom employed at the present day. VACCINAL SCARS. Physicians are often in doubt as to what constitutes a typical vaccine cicatrix. We deem the subject of sufficient importance to warrant a brief study of the objective features of vaccination scars. When an individual has undergone a vaccinia which has been per- fect in every respect, there is left after the fall of the crust a cicatrix which is characteristically distinctive in its features. Such a scar is indicative of the fact that the bearer thereof has passed through the vaccine disease in its most perfect form. The typical cicatrix is round or oval, distinctly excavated, with well-defined margins, reticulated or foveolated, and altogether presenting the appearance of having been stamped into the skin with a sharply cut die. Not all true vaccinations are followed by scars presenting these characteristics, but the more closely the cicatrix approaches to this standard the greater is the assur- ance that the vaccine disease has been genuine in every respect, and is calculated to give the greatest degree of immunity against smallpox. However, the appearance of the scar may vary within certain limita- tions and still be regarded as the sequential imprint of a genuine vac- cinia. The variety of vaccine scars is very great; the most frequent ^•aria- tions from the type above depicted are the result of the employment of lymph which has become more or less enfeebled by long human transmission. Modifications of the resulting scar may also be due to abnormalities or complications of the vaccine process, and to mechanical injury or interference with the normal development of the vesicle. In 1851, Decanteleu, of Paris, published an excellent monograph on the subject of vaccine scars, in which the classification is given after the system of Lamarck.^ The author distinguishes fifteen species of vaccine scars and depicts these and many sub^•arieties in .well-executed drawings, some of which are here reproduced. These drawings represent the type of each species. Fig. 10 represents examples of perfect scars resulting from vaccinations with vigorous bovine l^inph or of an early 1 Monographic des cicatrices de la vaccine, par J. E. B. Deuarp-Decanteleu. Paris, 1S51. Quoted by Dr. H. A. Martin. 62 VACCINIA human remove therefrom. The centre of the cicatrix is rounded, smooth, and convex, and surrounded by a deep, depressed, circular furrow or sulcus, which is traversed by short ridges radiating from the centre to the periphery. Most of these scars are round, but occasionally those of oval shape are encountered. Decanteleu found this type of scar in 24 per cent, of over five thousand scars examined. Fig. 10 J a ■■ 'I ! (I Ih Various forms of good vaccinal scars, showing a central, elevated disk surrounded by a furrow with radiating bands ; the scars look as if they had been' punched out with a die. (Alter Denarp- Decanteleu.) Fig. 11 Smooth scars on a level with the surrounding skin, showing slight pitting; such scars may result from genuine vaccination with long humanized virus. (After Denarp-Decanteleu.) It is but natural that vaccine scars should present variations. A cutaneous scar, no matter from what cause, is the result of the destruc- tion of dermal tissue. When merely epidermis is lost no scar results, for the cells of the rete mucosum proliferate and restore the complete integrity of the cuticle. When, however, a portion of the cutis proper is destroyed, repair takes place through the formation of fibrous con- nective tissue, which is scar tissue. The appearance of a cicatrix will depend upon the character, extent, and depth of the tissue loss, and sometimes upon certain personal pre- dispositions. The minute joveolations or 'pits which are commonly seen in vaccine VA (JCJ/NA L S(!A ILS 53 scars, and which are ref^arded by some as essci)ti;il (o tlif [x-rfcrt cifjdrix, represent the (h'latcd orifices of hair folhclcs and schaccous ^hirids. It is readily seen that if tlie vaccine [process (h-stroys tlic si,aymen and even physicians are too prone under such circumstances to apply the prin- ciple of post hoc ergo propter hoc. Vaccination immunizes only against smallpox; it will not protect one from tuberculosis, syphilis, skin dis- eases, etc. Therefore, as these are common diseases, it will of necessity happen that they will from time to time attack persons who have been recently vaccinated. We do not desire to convey the impression that vaccination never does any harm, but we are convinced that many mor- bid conditions are attributed to vaccination which bear no relation to it save a chronological one. 1 Quoted by Holt, Diseases of Children. - History of Smallpox and Vacciiiation, 1901. 60 VACCINIA Vaccination and Cutaneous Disease. — The following classification of skin diseases associated with vaccination is a modification of that formnlated by Malcolm Morris and later revised by Frank: Local . { Eruptions attributable to , the vaccine virus pure j and simple. t Constitutional II. Eruptions attributable to mixed infection at time of vaccination or later. Local . Constitutional Normal vaccinia. Erythematous dermatitis (areola). Generalized vaccinia. Diffuse vaccine erythema. Vaccinal roseola . Vaccinal lichen. Vaccinal miliaria. Purpura. Erythema multiforme. Urticaria. {Erysipelas. Impetigo contagiosa. Furunculosis. Vaccinal ulcer. Localized gangrene. L Cellulitis. f Disseminated gangrene. Syphilis. Leprosy (?). Tuberculosis (?). III. Eruptions sometimes fol- lowing vaccination. f Eczema. I Bullous eruptions (acute pemphigus, dermatitis bullosa, j dermatitis herpetiformis). 1 Psoriasis. I Furunculosis. i Urticaria. The above classification is doubtless faulty in many respects and open to criticism, but will perhaps serve the purpose of indicating in a general way the etiological factors in the production of the various der- matoses that may complicate vaccinia. Generalized Vaccinia. — This is perhaps the only eruption among those enumerated (with the exception, of course, of the normal vaccine dis- ease) which may with positiveness be attributed to the pure vaccine virus. There are two varieties of generalized vaccinia — 1. Spontaneous generalized vaccinia (vaccinal eruptive fever, vaccinola). 2. General- ized vaccinia from autoinoculation. Spontaneous generalized vaccinia is an extremely rare condition; many cases formerly regarded as instances of spontaneous diffusion of the eruption are in all likelihood cases of autoinoculated vaccinia. The eruption appears usually from the fourth to the tenth day after vaccination and most often from the sixth to the ninth day. The lesions appear in successive crops and pass through the stages of papule, vesicle, and pustule. The eruptive lesions, being of different age, may be seen in varying stages of development. Complete subsi- dence of the efflorescence usually occurs before the twenty-first day. The lesions may be few or numerous and may appear upon any portion of the body surface. Fever is absent in some cases and present in others, being usually proportionate to the extent of the eruption and the asso- ciated complications, particularly glandular enlargement. The causes of generalized vaccinia are but poorly understood. An ab- normal susceptibility to the vaccine virus has been invoked as a cause. The administration of the vaccine material through the digestive, cir- culatory, or respiratory system is regarded by Acland as capable of VACCINA 1. COMPIJdArrONS AND fNJfl/if/'JS fj] iiuluciiij^ ii j^ciKTiiliziitioii of llic cnipdc))!. This wrilcr niciilion-, ;iii observation of Etieiine tfiut a ^(Micralized vaccinal crii})tion had been |)ro(liice(l in children who had sucked their vaccination pocks; general- ized vaccinia has also been produced by the intentional feedinj^ of pow- dered vaccine crusts to subjects |)reviously rej^arded as insusceptible to vaccinia. Chauveau was able to produce a generalized eruption in horses by subcutaneous injection of vaccine lymph and also by administration through the res])irat()ry and digestive tracts. Generalized vaccinia may present a considerable resemblanr-e to variola. It may usually be distinguished by the absence of an initial stage, its occurrence after vaccination, the appearance of the eruption in crops, and the irregular distribution of the lesions. Its differentiation from inoculated variola is rather more difficult. Generalized Vaccinia from Autoinoculation. — This foim of generaliza- tion of the vaccine lesions is by no means rare. Many writers at the present day are inclined to regard the vast majority of cases of general- ized vaccinia as due to external inoculation. French writers have reported a number of instances of diffusion of the vaccinal eruption over an extensive cutaneous area the seat of a moist eczema. Unless there is danger of exposure to smallpox, it is, indeed, advisable to post- pone vaccination if the subject is suffering from a dermatosis in which there is denudation of the skin. The number of lesions may be but two or three or there may be a profuse eruption. The development of a few supermnnerary lesions in the neighborhood of the original vaccine insertion is by no means uncommon; this may occur even when there is no demonstrable abrasion of the skin. The virus may be transferred by the patient himself through scratching, or it may be conveyed by a second person. Fig. 12 represents six vaccine lesions upon the face of a woman which were produced by the finger-nails of an infant in arms; both the mother and child had been vaccinated upon the arm. We recall the case of an infant born of a variolous mother at seven and a half months. The child was immediately vaccinated, the insertions "taking:" well. From eleven to fourteen davs after the vaccina- tion, lesions indistinguishable from vaccine vesicles appeared upon the left side of the thigh, the left loin, the middle of the back, the hip, the splenic region, and the scrotum. These varied in diam- eter from five-eighths of an inch to three-quarters of an inch, were depressed in the centre, the depression later acquiring brownish crusts. Sixteen days after the vaccination a half-doxen firm variolous papules developed upon the face, neck, scalp, and foot. The infant was feeble and died a few^ days later. In this case it w^as difficult to determine whether the multiplicity of vaccine lesions was due to circulatory diffu- sion or autoinoculation. Accidental vaccine lesions may appear upon any portion of the cutaneous or mucous surfaces. They may even occur upon the conjunctiva or upon the eyeball. In the latter case there may be loss of vision. One of the writers recently saw in the practice of a medical friend, an ophthalmologist, a case in which a vaccine lesion 62 VACCINIA had been accidentally produced upon the bulbar conjunctiva. The family physician while vaccinating several children was requested by the mother to remove a foreign body from her eye. The physician, without cleansing his hands, everted the eyelids to determine the pres- ence of the offending substance. In the due course of time a vaccine vesicle appeared, accompanied by tremendous chemosis; the eye was saved only after prolonged skilful treatment. The lesions in vaccinia generalized by autoinoculation appear at intervals after the original vesicle is well advanced; they seldom con- tinue to make their appearance after the third week. Fig. 12 Accidental, multiple vaccinations produced by the scratching of an infant's hand contaminated from a vaccine lesion on its own arm. Sore Arm. — Under this caption we shall discuss a condition which only in its severer phases is to be regarded as a complication. A certain amount of inflammatory reaction (areola) about the fully developed vesicle is to be viewed as a not undesirable and probably an essential part of the normal evolution of the vaccine lesion. It not infrequently happens that instead of a moderate erythema and oedema of the skin, these phenomena are present to an excessive degree. Now and then the inflammation about a vaccination reaches a violent degree of inten- sity and spreads over a considerable portion or the whole of the affected arm. In such cases the cellular tissue may become implicated, giving VA(/('fNy\fj COMI'lJdATIONH AND / N.KU!/ i:S C/.i rise to a difl'iise cdluliiis. Tlie Jirin uruJer such coixliiicjiis is i'(;fl, swfjllcn, hot, and painful, and there is apt to be some associated systemic dis- turbance. In other cases the inflammation is more circumscribed and its force is spent upon the vaccine lesion and the skin in its imni(;diatc ncifrhbor- hood. In such cases a necrosis of the cutaneous and suljcutaneous tissues may occur, with the formation of a slouch. Wlien this is thrown off an ulcer is left at the site of vaccination. In other cases the vaccinia may pursue a normal course to the development and decline of the areola, but instead of the formation of a typical scab an excavated ulcer appears, covered by a soft, thin crust, which fre(|uently falls off and is renewed, the idcer persisting in this manner for a lont^ time. Mar- Fro, i:'. Sloughing at the vacciuation site accompanying au unusually inflammatory vaccination. tin, of Boston, repeatedly observed this irregular course upon arms which had been vaccinated with long humanized virus, whereas upon the opposite arm on which bovine virus had been simultaneously em- ployed a perfect result was obtained. This observation, as well as the scientific investigations of later-day observers, suggests that the excessively "sore arm" is due to the intro- duction of something in addition to the pure vaccine \urus, and, further- more, that this additional something is of the nature of extraneous micro-organisms. The Lancet Special Commission on Glycerinated liymph^ says that "the presence of a large number of organisms in an 1 London Lancet, 1902 64 VACCINIA active vaccine lymph renders the local lesion more severe," and that "many of the bad results obtained in vaccination are due to imperfect sterilization of the skin and want of protection against the invasion of the weakened and abraded tissues by extraneous organisms." It is also stated that "one of the most certain methods of producing severe oedema is for the patient to use his arm freely and to bring about per- spiration just before and after the vesicles have begun to form." Tt is not uncommon for the arm to become very "sore" as the result of thoughtless or accidental traumatism on the part of the vaccinee. The vesicle is frequently ruptured by a blow, friction of clothing, scratch- ing, and other like causes. Where the vesicle is unprotected the shirt- sleeve often becomes glued to the vaccination lesion, and attempts at separation cause a detachment of the crust. All of these forms of trau- matism doubtless act in the same manner; they prevent the formation of a firm, compact crust which is nature's protective covering of the vaccine wound. By opening up the wound they permit of infection with extraneous germs which may produce merely excessive inflamma- tion or may lead to ulceration or other more severe vaccinal complications. Inasmuch as we can obtain a lymph which is rendered free of extra- neous germs by the process of glycerinization, by proper care of the arm before, during, and after vaccination, we should be able, in the vast majority of instances, to prevent the development of "sore arms." Vaccinia Hemorrhagica. — From time to time cases of vaccinia are seen in which the areola about the vesicle at the acme of its development becomes hemorrhagic, assuming the appearance of a diffuse ecchyraosis. In some instances the skin beyond the areola may present a bluish appearance. In rare cases there may occur scattered petechise and ecchymosis and hemorrhages from some of the mucous membranes. The cause of this complication is obscure; it is doubtless not so much due to any peculiarity of the lymph as to some underlying systemic condition favoring hemorrhagic extravasation, such as scorbutus. Vaccinal Ulceration. — Ulceration at the site of insertion of the lymph is by no means an uncommon complication of vaccinia. Acland' says that nearly 4 per cent, of the vaccinal injuries inquired into by the English Local Government Board (1888-91) were due either to ulcera- tion or glandular abscess. There is in all probability one of two factors which may give rise to vaccinal ulceration — either the introduction into the skin of extraneous micro-organisms (at the time of vaccination or later) capable of producing a tissue necrosis, or an abnormal or vitiated state of health which permits of an excessive and unusual local reaction. Both of these factors appeared to play an important role in the produc- tion of "bad arms" among the soldiers during the United States Civil War. In the admirable report of the Board of Health of Louisiana of 1884, compiled by Dr. Joseph Jones, we read the following: "In scor- butic patients all injuries tended to form ulcers of an unhealthy charac- ter, and the vaccine vesicles, even when they appeared at the proper time and manifested many of the usual symptoms of the vaccine disease, 1 Article on Vaccinia, Allbutt's System of Medicine, p. 59G. VA(J(JINAIj (JOMriJdATIONS and INJlfltll'lS 65 were nevertheless larger and more slow in licalin^r, und tlic srahs [jrc- sented an enlarged, scaly, dark, unhealthy aj)j)caranc-e. In many cases a large ulcer, covered with a thick, laminated crust, from f)M(;-f|uarter to one inch in diameter, followed the introduction of the vaccine matter into scorbutic patients." In the same report Dr. Paul F. Eve describes certain abnormal manifestations of the vaccine disease due to the use of an improper scab. "The scab used in Atlanta which did so much mischief was soft, porous, and spongy, resembling concrete inspissated pus In every instance in which vaccination was attempted with it, premature effects were developed. No proper period of incuba- tion nor papular nor vesicular eruption was observed, but in a few days, even as early as the second, inflammation had set up, and by the fourth or fifth day sores were produced, covered by a thick, dirty crust, with an ichorous discharge. Soon an ill-constituted ulcer, with perpendicular edges, ensued, extending through the dermoid to the cellular and mus- cular tissues, and involving the neighboring lymphatics." These cita- tions indicate that either a weakened resistance on the one hand, or an extraneous infection on the other, may be responsible for vaccinal ulcerations. We have seen a few cases of ulceration at the vaccination sites follow- ing the use of bovine lymph. Fig. 13 shows such an ulceration occur- ring about the fifteenth day after vaccination. Septicaemia and Pyaemia Following Vaccination. — Blood poisoning is a rare condition after vaccination at the present day, and with care in the propagation and preservation of lymph, an aseptic technique, and proper protection of the vaccinated arm, this unfortunate complication will doubtless become rarer still. Several appalling epidemics of sep- tictemia after vaccination are on record; one occurred in the United States, one in Germany, and one in France. In all three the disastrous results followed the use of humanized virus; in two instances there was the grossest negligence in the preservation and preparation of the crusts, and in the third a lymph was used which was producing in progressive transmissions increasingly abnormal reactions. These epidemics are of much importance, and a brief account of theui is herewith presented: In 1860, during the prevalence of smallpox in Westford, Massachu- setts, a physician vaccinated a number of people with crusts which had been shaken up in a bottle with snow-water in order to provide a suffi- cient quantity of vaccine material. For ten or eleven days patients were vaccinated with a lancet which was from time to time dipped into the bottle. None of these people showed any results; but on the eleventh or twelfth day, by which time the bottle of liquid emitted a horrible stench, he "vaccinated" twenty-five more people. There at once ensued in half the cases diffuse abscesses. Three of the oldest vaccinees died in a short time, and a dozen or more of the remainder were only saved by the most prompt and energetic treatment.^ As Dr. Martin, who was foreman of the coroner's jury on this occasion, stated, "the 1 Mentioned by Dr. Henry A. Martin. Reprint from a letter in the Erie Observer. 5 QQ VACCINIA fearful results were clearly to be ascribed to the development of a septic poison of intense and virulent malignanty at a certain stage of the de- composition of animal matter." In 1878, at Grabnick, a similar but more extensive epidemic of septicaemia occurred among children infected with some old virus which had been exposed to the air for a long time. Fifty-three children were inoculated with the decomposed vaccine material, and of this number fifteen died. Some of the children had morbilliform and scarla- tiniform eruptions, and others abscesses and erysipelatous symptoms. According to Pincus the vaccine material contained septic bacteria. Autopsies were made upon two children and the deaths ascribed to septicaemia, BrouardeP reports a series of cases of blood poisoning following vaccination at Asprieres, France, in 1885. Brouardel, Pasteur, and Proust were commissioned to determine the responsibility of the attend- ing physician. The commission says: "In our investigations we were enabled to trace the vaccine back through five generations and to deter- mine that it was by employing a virus originally good, but which gave rise successively to accidents, at first of slight gravity, then more and more serious, that the preparation was made for the final disaster." Forty-two children were vaccinated from the arm of a little girl who herself had developed fever the first night after her vaccination, and whose vaccination "took" on the following day. Of this number four died within twenty hours and two others later. Almost all of those vaccinated were more or less ill. The symptoms were fever, vomiting, diarrhoea, and in the fatal cases convulsions. The fever appeared at the latest eighteen hours after vaccination; in those who recovered it lasted from two to four days. All the children developed on the first day an inflamed area about 1 cm. in diameter surrounding the point of inoculation. A serous or seropurulent discharge occurred from the first to the third day. In all of the children a local and generalized impetiginous eruption followed the inoculation. These cases represent examples of acute intense septicaemia analo- gous to that resulting from bad dissection wounds. The septic micro- organisms were doubtless increased in virulency by successive trans- missions from one subject to another. A case of pyoemia^ after vaccination is recorded in the Lancet, 1884, vol. i. p. 857. A child, aged six months, vaccinated with two other children from the same source, showed on the ninth day appearances of successful vaccination with no unusual symptoms, but on the six- teenth day the sores were ulcerated and freely discharging pus. The child was also suffering from bronchitis. Death took place on the twenty-fifth day after vaccination. The autopsy revealed the presence of pus in the left ankle, right sternoclavicular joint, both temporomaxil- lary articulations, and in the bursa over the right olecranon. The lungs presented a number of hemorrhagic infarcts. 1 Twentieth Century Practice of Medicine. Article on Vaccinia, p. 534. 2 Mentioned by Poole, Vaccination Eruptions, Edinburgh, 1893, p. 118. VyiC('fNAIj (lOMI'lJdATIONS AND IN.iriilKS 07 There was in the .same house a man vnfh an ah.srrs.s of llie /oo/, unci occasionally \\w. mother had washed some linen in the water which Ijufl been used for cleansinn; his foot. This fact, with the early normal devel- opment of the vaccine lesion, and the exeinj)tif)n of th(; other two chil- dren vaccinated, constitute strong presumptive evidence that the septic infection occurred subsefjuent to vaccination, probably through neglect on the part of the child's carelakers. Glandular and Subcutaneous Abscess. — In most normal vaccinations enlargement and tenderness of the neighboring lymj)hatic glands are observed. Where there is an unusual degree of inflammation about the vaccine lesion or actual ulceration, the swollen glands not infre(juently undergo suppuration. As has been already stated, glandular abscess and vaccinal ulceration comprised nearly 4 per cent, of vaccination injuries reported to the English Local Government ]}oard from 1888 to 1S91. Sinigar' reports four cases of abscess among 1160 vaccinations. One appeared on the twentieth day in the lower half of the posterior triangle of the neck, one between the pocks on the arm on the twenty- fourth day, one on the arm on the twenty-ninth day, and one in the axilla on the thirty-second day. These abscesses are seldom of serious portent, usually healing rapidly after incision and evacuation. Localized Vaccinal Gangrene. — In extremely rare instances death of the tissues eii masse at the site of vaccination may occur, producing a locahzed gangrene. It would seem that in these cases the gangrene is due to low vitahty of the tissues rather than to any impurity of the lymph. In cases observed by Balzer, Wheaton, and Acland, the chil- dren were of syphilitic parentage. Hutchinson, however, saw three cases of vaccinal gangrene in children in wdiom no such cause could be invoked. The view that the condition of the tissues is the most important etiological factor in the production of this complication is corroborated by the experience of surgeons in the Confederate army during the United States Civil War. Dr. Joseph Jones' writes: "After careful inquiry w^e were led to the conclusion that these accidents were, in the case of Federal prisoners, referable wdiolly to the scorbutic condition of their blood and the crowded condition of the stockade and hospital. The smallest accidental injuries and abrasions of the surface, as from splinters or bites of insects, were in a number of instances followed by such extensive gangrene as to necessitate amputation. The gangrene following vaccination appeared to be due essentially to the same cause, and in the condition of blood of these patients would most probably have attacked any puncture made by a lancet, without any vaccine matter or any other extraneous material." Vaccinia Gangraenosa. — As has been pointed out by Crocker and others, the term vaccinia gangrrenosa is a misnomer, inasmuch as the affection recorded under this title occurs after varicella (varicella gan- gnenosa) and other discrete pustular eruptions. Disseminated necrosis of the skin which in rare instances follows vaccinia, varicella, and 1 Lftiicot, 1902. = Report of Louisiana Board of HeaUh, ]&<^S4. 68 VACCINIA pustular dermatoses may occur independently of these diseases in apparently healthy infants; a better designation, therefore, for this con- dition is dermatitis gangroenosa infantum. The gangrenous changes in the skin may occur early or late. Stokes/ of Dublin, reports a case of so-called vaccinia gangrgenosa developing forty-eight hours after vac- cination. The vaccinal or varicellous pustules may be directly con- verted into blackish sloughs, which are thrown off and leave deep, ex- cavated ulcers; or the gangrene may not set in until a week or two has elapsed, beginning as papulopustules which crust over, become sur- rounded by an areola, and then break down and ulcerate. High fever is often present. The cause of this rare condition is obscure; it usually supervenes in the course of some pustular febrile disease,^ particularly in tuberculous, syphilitic, or rachitic children. It is quite possible that the gangrene is due to infection with some virulent micro-organism. Vaccinal Roseola (roseola vaccinosa, vaccinal rash, or erythema). — Under the above designations has been described a rosy, macular rash, which occasionally appears in vaccinated persons about the time of maturation of the vesicle. While this eruption is ordinarily seen about the tenth day after vaccination, it has been observed as early as the third day and as late as the eighteenth. It usually appears first upon the vaccinated arm, rapidly spreading to the trunk and other portions of the body. The macules are large, irregular, blotchy in appearance, of a rosy tint, and not elevated above the level of the skin. In rare instances the macules may coalesce, giving rise to a diffuse erythema. The erup- tion is of brief duration, lasting from a few hours to a day or two. It may be accompanied by moderate elevation of temperature. The rash is not unlike that of measles, with which, indeed, it has not infrequently been confounded. The eruption of measles is more elevated, being maculopapular in character and more persistent, and is accom- panied by higher fever and the characteristic catarrhal symptoms of this disease. During epidemics of smallpox, vaccinal roseola has been mistaken for the beginning eruption of confluent smallpox. Roseola vaccinosa has a complete analogue in the roseola variolosa, an exanthem pre- senting almost identical features, which is not infrequently observed just before the appearance of the eruption of modified smallpox. Vaccinal Lichen. — Crocker states that in his experience vaccine lichen has been the most common of the true vaccinal exanthema. He has made notes of twenty cases of this eruption. He states that it may be either papular, papulovesicular or pustular. It appears from the fourth to the eighteenth day, most commonly on the eighth; in about one-half the cases it is seen first on the arms, appearing in the remainder on the trunk, neck, or face; the eruption then extends in successive crops over large portions or the entire cutaneous surface (Fig. 14). 1 Dublin Journal of Medical Science, June, 1880. Quoted by Crocker. 2 The writers recall the case of a young girl suffering from smallpox, who developed at the end of the third week numerous punched-out areas of cutaneous gangrene. Tlie patient succumbed to this complication, which was doubtless a condition analogous to the so-called vaccinia gangreenosa. PLATE III. Roseola Vaccinosa Appearing upon the Tenth Day after Vaccination. VA(J(!/NAIj aOMI'LKIATIONS AND IN.IUIUI'IS 69 The j);i,j)nl(',s urc rcuhJisli, (-(Hiic^al, piiilicad .siz(;(J, .siinoiiiidcd hy a reddisli halo, and often surmounted by minute vesicles or pustules. In the experience of the writers vaccine lichen has l)een excessively rare. KiG. H VacciuiUion upon the tenth da}', showing an unusually inteiife areola. A papular vaccinal eruption is also seen upon the face. Vaccinal Miliaria. — In rare cases instead of a papular eruption a vesicular outbreak may take place, usually from the eighth to the eleventh day. Danchez^ writes: "We give the name vaccinal miliaria to a satel- lite eruption of the vaccinal fever, appearing from the eighth to the twelfth day (very rarely later) after vaccination. It is constituted by small vesi- cles of the size of a grain of millet, accumulated in great numbers over large surfaces, containing a transparent liquid at first, then opaque, fol- lowed by slight furfuration, and never leaving cicatrices after it." 1 Vaccinides, "^hHe de Paris, 1SS3. 70 VACCINIA A miliary vesicular eruption is occasionally seen in or around the vaccination areola. These vesicles are not true vaccine lesions, for Martin has shown that the contents inoculated upon another individual fails to produce the vaccine disease. Erythema Multiforme and Urticaria after Vaccination. — The erup- tion of multiform erythema is occasionally seen in vaccinated individuals between the first and the tenth day after the insertion of the virus. In some cases the eruption is delayed considerably beyond this period. The lesions may be erythematous, papular, tuberculous, vesiculobullous or mixed. At times the eruption is annular. Crocker saw a well-marked case which began on the ninth day after vaccination, and was characterized by shilling-sized annulopapular patches. Napier observed a case on the eleventh day which began as rings. Not infrequently urticarial lesions are present, the eruption being a type of combined erythema multiforme and urticaria. Allen and Sobel regard urticaria as one of the most common of the generalized vaccinal eruptions. Norman Walker^ has observed five cases of erythema multiforme after vaccinations with glycerinated lymph. In all, the early course of the vaccination was uneventful. The eruption was invariably seen on the hands and face, but on other parts as well. In a review of the vaccinal complications in 1160 vaccinations, Sinigar^ states that there were 23 cases of erythema, including simple erythema- tous blushes, finely punctate erythemata, erythema of papular or urti- carial type, and erythema multiforme. Concerning the date of appear- ance, 1 rash appeared on the third day, 5 on the eighth, 2 on the ninth, 5 on the tenth, 4 on the eleventh, 1 on the twelfth, 4 on the thirteenth, and 1 on the sixteenth day. No age was exempted ; in 4 cases the patient was over seventy years of age. The average duration of the rash was forty-eight hours, but in 1 severe case it lasted six days. Impetigo Contagiosa. — This contagious disease of the skin is ex- tremely common, independent of vaccination, among dirty and poorly nourished children. Any abrasion of the skin increases the liability to its development. Its occasional occurrence after vaccination, par- ticularly among children in poor hygienic circumstances, is therefore scarcely to be marvelled at. The introduction of the infection of impetigo with the insertion of the vaccine virus must be an occurrence of the greatest rarity; inasmuch as impetigo sores develop rapidly (from one to two days) after the skin is infected, we would expect, if the disease were invaceinated, to discover the impetigo lesions twenty-four to forty- eight hours after the vaccination. As a matter of experience, however, impetigo usually develops at a considerably later period; it may make its appearance at any period up to the complete healing of the vaccinal wound. It is not infrequently observed at the end of the second or third week after vaccination. The 1 British Medical Journal, 1901, p. 1201. 2 Lancet, 1902. VyiCC/Nyil. aoMI'LldATIONH AND I S.I IJ III HS 71 first lesions are usually seen about the site* of iusertirtn (jf the vaeciiK- lyriipli. This area may heeoine quitc^ irifiain(!(l, the surrounding epi- dermis raised up by a seropurulent fluid, and the process extend upon the periphery, with the production of voluminous ochre-colored crusts. From this as a focus other ])ortions of the skin become infected by aut()ino(nilation through scratchinn; or other means. At times impetigo may assume a bullous form, simulating ])emphigus; most oF the pem- Secondary impetigo engrafted upon a late vaccination and subsequently upon other regions. phigoid eruptions after vaccination would appear, however, to belong to the group of bullous dermatitis presently to be described.^ In 1885 an outbreak of a cutaneous disease, said to have presented the clinical features of impetigo, occurred in villages on the Island of Rtigen, in the Baltic Sea, after the vaccination of seventy-nine children. ' Engman and Grindon have each described (Journal of Cutaneous and Genito-urinary Diseases, 1901, pp. 180 and 188) extensive cases of bullous impetigo, not, however, related to vaccination. They state that this form of the disease is quite common in St. Louis, and that epidemics occasionally occur in foundling asylums, attacking particularly weak and undernourished infants. Some of the cases reported terminated fatally. [The differential diagnosis between bullous impetigo, acute pemphigus, and dermatitis herpetiformis is sometimes fraught with difficulty.] 72 VACCINIA Impetigo contagiosa is caused by invasion of the skin with the germs of contagious pus, independently of its source. There are probably two chief varieties due respectively to the streptococcus and the staphylococ- cus pyogenes. Vaccinal Erysipelas. — Erysipelas is an acute infectious disease resulting from invasion of the body with the streptococcus of Fehleisen. In the vast majority of cases of this malady the infection gains its entrance to the system through a wound of the cutaneous or mucous surfaces; the disease therefore is essentially a wound infection. Inasmuch as vaccinia is attended with the production of a wound of the skin, it is not surprising, particularly in view of the frequent neglect of vaccination wounds, that erysipelas should occasionally occur after this procedure. The erysipelatous infection is usually conveyed to the vaccination wound at some period subsequent to the insertion of the vaccine virus; in rare cases, however, the specific germs of erysipelas may be present in the lymph, in which event this complication develops on the second or third day after vaccination. Erysipelas may develop in an infant after vaccination and still be independent thereof. Erysipelas is a common disease among infants; according to Dr. Ogle's testimony before the British Royal Vaccination Commission, two thousand per million infants under three months of age perish from it. It has been known to develop after very trivial injuries, such as the scratch of a pin, abrasion from the friction of clothing, etc. Both vaccinal erysipelas and erysipelas from other causes are attended with a rather high mortality rate in infants. Of the deaths attributed to vaccination in England between 1886 and 1891 almost one-half resulted from erysipelas. Erysipelas may result from the employment of lymph containing streptococci, from infected instruments, unclean hands, contact of soiled linen, or from previous contamination of the skin at the vaccina- tion site. When the disease develops late it is often favored by injury or rupture of the vesicle, or forcible and premature detachment of the crust. Bad hygienic surroundings and uncleanliness of the body or garments increase the liability to infection. Humanized lymph derived from a vaccinifer with an inflamed arm may give rise to erysipelas. The improper preservation of crusts has likewise given rise to some cases. One of the writers saw some years ago a series of cases of ery- sipelas follow vaccination with a humanized crust which had been rubbed up with water and kept in the pocket between two glass slides for several days, during which time decomposition had taken place. As a vaccinal complication, erysipelas appears to be distinctly on the decrease. In 1877 Lotz was able to collect in Germany but two cases of death from this cause in 1,252,554 vaccinations. The increased attention to asepsis in vaccination, the careful protec- tion of the vesicle when formed, and the employment of bovine lymph will doubtless continue to lessen the frequency of this complication. It is claimed that animal virus, on account of the comparative insus- VACOfNAL (!()M/'/J(!AT/()NS AND IN.HHill-lS 70 ceptibility of the bovine species to erysipelas, gives a greater security affainst this disease than humanized virus. In 1877 II. A. Martin emphasized this advantage of animal lymph in the most positive terms. He Mfrote: "During the sixteen years in which I snpj)li(;d humanized virus the presence of this pest (erysipelas) in my prac-tice and in that of my correspondents w^as the one great and serious drawback, the one formidable source of anxiety and blame. Since I have issued bovine virus to a far greater extent (from eight to nine thousand corre- spondents),! have never received a single complaint of the (n-crurrence of erysipelas. It is said to attack particularly cases of revaccination, but in 1872-73 I revaccinated about twelve thousand patients with my own hand, and there was not one case of erysipelas among them all, nor have I ever known a case following the use of the bovine virus at any other time." Martin abandoned the collection and propagation of humanized virus in 1873 because in one week he had five cases of erysipelas. These children were vaccinated on one arm with the hum an- ized lymph and on the other with the bovine product, and in each in- stance erysipelas appeared on the arm on which humanized virus had been employed. True vaccinal erysipelas should be trenchantly distinguished from the dermatocellulitis which is not infrequently observed about the vac- cine lesion, and which occasionally involves the entire upper arm and even the forearm; this is nothing more than an exaggeration of the inflammatory areola.^ The arm is swollen and intensely reddened, but there is no tendency for the process to spread to other parts of the body, the inflammatory phenomena subsiding after the height of the vaccinia has been reached. Tetanus Following Vaccination. — The development of lockjaw after vaccination was until a few years ago an occurrence of the greatest rarity. The minority contingent of the British Royal Vaccination Com- mission in 1896, after extended investigation, was able to mention but a single instance of this complication. Tetanus after vaccination is said to be unknown in France, Germany, and other continental countries of Europe. Within the past five years (and particularly in 1901) a rather alarming number of cases has been reported in the United States. Dr. R. N. Willson and Dr. Joseph McFarland^ have independently presented analytical studies of all of the cases recorded and of other cases personally communicated to them. Willson reports 52 cases and McFarland 95, 28 of which, however, are shrouded in considerable doubt. Willson, from a painstaking study of the records of the cases reported, came to the conclusion that while the tetanus infection gained entrance at the site of vaccination, it was not introduced with the vaccine ^-irus, but at some period subsequent to this. 1 Some of the older writers, including Jenner, referred to this condition under the rather mislead- ing designation of "erysipelatous inflammation ;" but, as Jenner himself explains, it was not regarded as true erysipelas, but as merely bearing a resemblance to it. 2 Proceedings of the Philadelphia County ^Medical Society, September, 1902. 74 VACCINIA McFarland, on the other hand, beHeves that tetanus organisms may be present in the virus, being derived from manure and hay; he further states that the future avoidance of the comphcation is to be sought for in greater care, in the preparation of the virus. In October, November, and December, of 1901, there v^^as a small epidemic of tetanus after vaccination in Camden, Philadelphia, and to a certain extent in some nearby towns. Camden had 11 cases, and Philadelphia even more than this number. These groups of cases have been adduced as evidence in favor of the view that the tetanus infection is in the virus. Willson, however, shows that there occurred in Philadelphia during the above period 12 cases of tetanus inde- pendent of vaccination. In Baltimore during the month of August there were 6 cases of tetanus independent of vaccination, in September 6 cases, and in October (the month in which the Camden outbreak occurred) 8 cases. In 1899, in New York City, there were 63 deaths from tetanus unrelated to vaccination; in Philadelphia, in 1901, there were 29 deaths from similar cases, and in Cook County, Illinois, from June 25 to July 14, 1900, 27 deaths from tetanus from causes other than vaccination. In 1903 there occurred throughout the United States 406 deaths from tetanus as a result of wounds received on the Fourth of July from toy pistols and blank cartridges (special article in Journal of the American Medical Association). These figures indicate that such epidemics of tetanus as occurred after vaccination in Philadelphia and Camden might readily have developed from other causes. Improper care of the vaccine wound and the development of exces- sive inflammation and ulceration appear to be important factors in predisposing to tetanus infection. Willson says: "In every instance in the series of cases included in this paper, in which any information could be obtained whatsoever, there has been found some gross breach in the care of the wound, and usually the presence of some active influ- ence that would offer more than a likely means of entrance for tetanus or any other infection." " Nearly every case showed for days a large open ulcer, burrowing deep into the tissues. Two cases were those of soldiers, sleeping anywhere and everywhere, and looking on a bath as a luxury. Several children lived^over^ and next to and played continually in stables, the hotbed of the tetanus bacillus. One slept in bed every night with her father, who had charge of horses. Two at least are known to have forcibly maltreated the vaccine wound. Many removed the scab for inspection. Two threw or dropped the scab on the ground and replaced it in the wound, one wearing it for hours. One threw his bandage on the ground and replaced it on the arm at a later time. Several wore a shield over the wound without cleansing or removing it until it was full of pus and dirt and foul to smell; one of these reached the eighteenth day and the writer's case the twenty-eighth with the shield still in place. One, when tetanus developed, exhibited a merino shirt-sleeve, that had never been washed, matted in the vaccine wound." VAddlNAIj (JOMI'IjICATIONS AND IS'.HIIHI-IS 75 Rosenau/ in a study of the bacterial impurities of vaeoirif; virus, was uiiahle to find tetaruis or(>;anistns in any of a consirtc(l by Marcolini (IS]4 in IJdinej, Cerioli (1SI2 in Crenioiia;, 'Jassani (1841 in (innnello), Wetreler (1840 in Coblentzj, Oherfianken i\^',2 in Freienfels), Marone (18r>() in Liipaiaj, J'accliiotti fhSf)) in liivaltaj, Depaul (18GG in Morbihan, France), Kocevar (1870 in Schleinitz and St. Veix), Jonathan Hutchinson (1871 in London, two series of cases), and I>ayet (1880 in Algiers and 1885 in Turin). A brief account of the Rivalta and Lupara epidemics, which are fairly typical of all the rest, is herewith subjoined: In 1801 Pacchiotti^ reported an extensive epidemic of vaccinal sy}>hilis occurring in Rivalta, Italy: 46 children were vaccinated from the origi- nal vaccinifer; of these 40 contracted syphilis. From 1 of these subjects 7 other children became infected through vaccination. In a(lditif)n 20 mothers or nurses contracted syphilis through contact with these children. But 17 out of G3 vaccinees escaped infection. About the same time Marone^ published an account of a similar epidemic that occurred at Lupara in 1856. A large number of infants were vaccinated with humanized lymph received in tid)es from Campo- basso, and 23 were infected with syphilis. From 1 of these children 1 1 other infants were inoculated with the disease. As in the Rivalta tragedy, a number of mothers and nurses subsequently developed chancres of the nipple. It will be seen that more than half of the cases of vaccinal syphilis that have been recorded have occurred in Italy. The remainder have been found in France, Germany, and England. Fortunately, such infections in the United States have been extremely rare. It has been estimated that the aggregate number of cases of vaccinal syphilis that have occurred is about seven hundred. When we think of the millions of lives that have been saved by vaccination during the past century, we recognize the fact that the sacrifices, however deplorable, have been relatively small. Many blessings are leavened with misfortune. Pacchiotti, in 1861, laid down the following rules to be observed in vaccinating: 1. Enquire into the state of the patient's health. 2. Take the lymph in preference from those children who have passed the fourth or fifth month, as hereditary syphilis appears, in general, before that time. 3. Do not use lymph taken from a vesicle which has passed its eighth day, because on the ninth and tenth days the lymph becomes mixed with pus, which later may be of an infectious character. 4. In taking the lymph, avoid hemorrhage, as there is less danger with hiiiph free from blood. 5. Do not vaccinate too many children with the same lymph. The observance of these precautions would obviate much of the risk of transmitting syphilis, but would not confer absolute security against such infection. The British Royal Commission on Vaccination says: "Absolute freedom from risks of syphilis can be had only when calf- 1 Sifilide Transmissa per Mezzo Delia Vaceiiiazione in Rivalta Presso Acqui. Gazetta Delia Asso ciazlone Meri., October 20, l^Bl. s Impraziale de Florence, November 5, 1862. 78 VACCINIA lymph is used, though where the antecedents of the vaccinifer are fully ascertained, and due care is used, the risk may for practical purposes be regarded as absent." Inasmuch as bovine virus is at the present time generally and, indeed, almost universally employed, the subject of syphilis may be dismissed in a discussion of the complications of vaccination. The employment of calf-lymph and the complete elimination of the risk of transferring syphilis to the vaccinee have robbed the opponents of vaccination of one of their most potent arguments against the enforce- ment of vaccination. The Relation of Vaccination to Tuberculosis. — Whether or not it is possible to transmit tuberculosis in vaccine lymph is an undeter- mined question. Toussaint^ claims to have successfully inoculated rabbits and a pig w^ith tuberculosis with lymph taken from a vaccine vesicle induced upon the vulva of a tuberculous cow. On the other hand, Josserand^ injected lymph taken from vaccine vesicles in tuber- culous individuals into the peritoneal cavity, under the skin, and into the anterior chamber of the eye in 47 animals. Post-mortem exami- nations gave absolutely negative results in 43 of these, and in no animal was there conclusive evidence of tuberculosis. The danger of conveying tuberculosis in bovine lymph is almost inappreciable. The virus is obtained from calves, and it is pretty well established that calves are but rarely the subjects of tuberculosis. It is stated by Fiirst, on the authority of Pfeiffer, that but one case of tuberculosis was found among 34,400 calves under four months of age.^ The statistics of the abattoirs of Augsburg and Munich corroborate the above figures; only one tuberculous calf was discovered at Augs- burg among 22,230 slaughtered, and a smaller percentage at Munich.'' Furthermore, in well-regulated vaccine establishments calves are subjected to the tuberculin test before vaccination, and are autopsied before the lymph is distributed for use. Even though it were possible, despite these precautions, for tubercle bacilli to get into the lymph, they would perish if the lymph were glycerinated. Copeman,^ speaking of glycerinated lymph, says : " The tubercle bacillus is effectually destroyed even when large quantities of virulent cultures have been purposely added to the lymph." Bollinger, Heron, and Acland all seriously doubt whether tubercu- losis has ever been transmitted by vaccination. Postvaccinal Lupus Vulgaris. — Cases of lupus occurring in and around vaccination scars have been reported by I^enander, Besnier," Perry,'' Little,^ Colcott Fox, x^cland,^ Stelwagon,^" and others. Most of 1 French Academy of Sciences, August 8, 1881, quoted by Acland, Allbutt's System of Medicine, p. 619. 2 Contribution a Tetude des contamination vaccinales, Lyons, 1884, p. 30, quoted by Aclaud. 3 Fiirst. DiePathologiederSchutz-Pocljen-Impfung, Berlin, 1896, par. 431, p. 112, quoted by Acland. * Strauss. Gaz. hebdom. de mod. et de chirurg., 1885, p. 143, quoted by Acland. s Vaccination, its Natural History and Pathology, London, 1899, p. 181. 8 Annales de dermat. et de syph. 1889, p. 576. ? British Journal of Dermatology, 1898, )>. r.m, 8 Ibid., 1900, p. 60. « Loc. cit. '" Journal of the American Medical A.ssociation, November 22, 1902, VAddlNA L aOMPLKIATlONS AND INJUIUES 7(j these observers saw the lupus years after the vaccination had been per- formed. Fox saw a case of hjpus begin in a vaccination scar shortly after tlie sore had licalcd. Tl)(M"hild subsccjucntly d(;v.(?Iopcd a di.sserni- nated hi])ns, subperiosteal tuberculous nodules, and jjulnionary phthisis. It is higlily probable that this child was already tuberculous, as another child in the family had previously died of this disease. Stelwagon saw a palm-sized patch of lupus on the arm in a girl ten or twelve years after a vaccination which was said to have been immediately followed by the development of the lupus, the history being given by a physician, the brother of the patient. All that can be stated as regards the rela- tionship of vaccination to lupus is that vaccination may in rare cases in tuberculous individuals give rise to a lupus at the site of vaccination. That lupus should occasionally choose a vaccination scar for its seat is no proof that it was caused by vaccination. Vaccination and Leprosy.^ — Since the general adoption of bovine lymph for vaccination, the question of the invaccination of leprosy has resolved itself into one of academic and retrospective interest. It is well, however, for physicians in leprous countries, if required by unusual circumstances to employ humanized lymph, to remember that leprosy has probably in isolated instances been conveyed by vaccination. Gaird- ner,"^ Daubler,^ and Hillis have each recorded instances of vaccinal leprosy, although some doubt attaches to all of these cases. Beavan Rake and Buckmaster, who have given this matter much study, believe "that the alleged cases of transmission of leprosy by vaccination are open to serious doubt." Hansen,^ of Bergen, in 1890, made extensive inquiry by circular to all of the physicians of Norway as to the occurrence of vaccination leprosy. In not a single case was there any ground to suspect such an origin. This statement is of espe- cial importance inasmuch as there is much leprosy in Norway, and vaccination is practised extensively in that country. From experimental evidence we Would scarcely expect leprosy to be transmissible by vaccination. Inoculation of man and lower animals has been I'epeatedly attempted by Daniellson, Profeta, Hansen, and others, who inserted fragments of leprous tissue and injected blood from lepers beneath the skin, but with entirely negative results. There is indeed no conclusive case on record of the successful experimental transmission of leprosy. It is true that lepra bacilli have occasionally been found in vaccine lymph in vesicles raised upon leprous skin, but, as Beavan Rake properly states, no responsible person would think of vaccinating a leper in an affected part and using such l^aiiph for further vaccinations. Eczema Following Vaccination. — Vaccination may now and then induce the appearance of an eczema in a child predisposed to the dis- ease, just as an attack of measles, scarlet fever, or simple teething may act as an exciting cause. Eczema is an extremely common disease ' A Remarkable Experience Concerning Leprosy, Briiisb Nfedical Journal, 1SS7, vol. i. p. 12C9. - Monatsheft. f. prakt. Derm., 1SS9, p. VIZ. ■■' Mentioned by Acland, Allbutt's System of Medicine, p. 6Jo. 80 VACCINIA among infants and young children, and is particularly referable to faulty feeding and digestive disturbances. Of 600 cases of eczema under the care of Dr. T. Colcott Fox, 249, or 41.5 per cent., were seen before the end of the first year; in 40 of these eczema was known to have appeared before vaccination. Doubtless if these had appeared after vaccination, the latter would have been viewed as a probable etiological factor. Crocker^ says: "In no case can vaccination be held responsible where the vaccinia pustule has completely healed before eczema appears." Eczematous children, if in good health otherwise, may usually be vaccinated without any aggravation of the existing cutaneous disease. Van Harlingen^ has carefully studied the influence of vaccination on previously existing skin diseases. He writes: "During the smallpox epidemic of 1872 I observed all cases of skin disease coming under my notice in which vaccination had been practised. In a few some aggrava- tion of the symptoms followed ; in others an apparent improvement took place. But in the great majority of cases vaccination did not appear to exercise any influence whatever on the course of the more common diseases of the skin coming under my observation." We have from time to time vaccinated persons with eczema and other cutaneous dis- eases without any injury whatsoever. On the other hand, vaccination has on a number of occasions been followed by improvement and even cure of eczemas. Stelwagon^ says: "I have noted in several instances that amelioration followed vaccination, and in one instance, in a chronic case, a disappearance of the eczema." Duhring, Tait, and others have testified to the occasional curative influence of vaccination on eczema. While we would not elect to perform vaccination upon a child suffer- ing from eczema, we should not consider the latter condition a sufficient contraindication if smallpox were prevalent. Bullous Eruptions (dermatitis bullosa; dermatitis herpetiforTnis ; acute pemphigus). — In relatively rare instances vesicobullous eruptions variously designated as pemphigus, bullous dermatitis, and dermatitis herpetiformis (Duhring's disease) have followed vaccination. While we have no proof positive of a causative relationship between vaccinia and these eruptions, they have now been reported by careful observers in a sufficient number of instances to warrant the assumption that the antecedent vaccination has been of some etiological moment. Pusey* reported a case of this character under the title of dermatitis herpetiformis, in which the lesions were vesicobullous and erythema- tous, followed by pigmentation. Dyer^ reported two similar cases under the same title after vaccina- tion. One case occurred three weeks after vaccination and one several (?) weeks thereafter. 1 Diseases of the Skin, p. 324. 2 Remarks on Vaccination, in Relation to Skin Diseases and Eruptions Following Vaccination, Philadelphia Medical Journal, 1902, p. 184. 3 Vaccinal Eruptions, Journal of the American Medical Association, November 22, 1902. ■* Journal of Cutaneous and Genito-urinary Diseases, 1897. 5 St. Louis Medical Gazette, 1898. VACCINA [j (lOMI'LldATIONS AND IS.HHilHS 81 Bowen* has placed on record a series of six casfs f)f l)iil!f>ii,s dci-rnatitis resemblinfij dermatitis herpetiformis following vaffination. In three of the cases the eruption is stat(;d to iiav(; made its appearance within two weeks after vaccination, in one within a week, while in two it did not show itself until after the lapse of a month. Corlett exhibits two photo- graphs of postvaccinal bullous dermatitis in his work on tlie acute infectious exanthemata. Stelwagon^ saw within one year three cases of bullous eruption after vaccination, two of which he regarded as acute peni'phigus, and the third as a persistent bullous erythema multiforme or dermatitis herpetiformis. In these cases the vaccination was what is usually described as a "good take," but was somewhat slow in heal- ing, the crust remaining adherent a long time. The eruption appeared from two to four weeks after vaccination, and had persisted at the time they were reported three, four, and eight months, respect- ively. Sequeira^ showed to the Dermatological Society of T.ondon in 1902 a case of 'pemphigus in a man aged thirty-nine years, the eruption appearing three weeks after a revaccination. Three vaccine insertions were made, and the first bleb is alleged to have developed at the site of one of these. This was followed in several weeks by bullre on the arms, and later on the thighs. Cultures from the early blebs were sterile, and inoculations of this fluid into animals were negative. In all of the above cases save the last, the patients were children under twelve years of age. The eruption usually appeared from two to three weeks after vaccination, and in no case after six weeks. In most cases the eruption was extensive and of long duration, with marked tendency to relapse. Some of the cases were cured at the end of three or six months, but some persisted much longer. Pusey's case continued to have relapses for four and a half years. Rowen says : " The chief features that these cases present in common, and that lead to a conviction that they have a common etiology, are their occurrence in children after vaccination; their course, varying from ssveral months to several years or perhaps longer; their urfiformly vesicular and bullous character, with only occasional evidences of mul- tiformity; the almost complete exemption of the trunk; the character- istic grouping about the mouth, nose, ears, wrists, ankles, and feet, and the very slight prominence of itching or other subjective symptoms." While most of these cases run a relatively benign course, one of the writers* saw a fatal termination in a case of bullous eruption of the acute pemphigus type. This occurred in a girl of five years, the eruption beginning two weeks after vaccination. The writers have also seen four other cases of generalized bullous eruption of the t}^e described above, occurring shortly after vaccination. A remarkable series of bullous eruptions occurring after vaccination 1 Journal of Cutaneous and Genito-uriuary Diseases, September, 1901, p. 401. - Journal of the American Medical Association, November 22, 1902. 3 British Dermatological Journal, May, 1902, p. 174. * Schamberg and Keech. A Case of Acute Fatal Pemphigus, Annals of Gynecology and Pediatries February, 1901, p. 321. 6 82 VACCINIA is reported by' Howe/ of Boston. Ten cases are referred to, all but one occurring in persons who had been recently vaccinated. The skin lesions began on an average of five weeks after vaccination; the longest time elapsing between vaccination and the appearance of the eruption was sixteen Weeks, and the shortest period three weeks. All of the patients were adults, the ages varying from twenty-one to fifty-two years. Six of the ten cases proved fatal; the average duration until recovery or death occurred was six weeks. It will be seen that these cases present points of variation from the cases described by Bowen. The interval between vaccination and the appearance of the eruption in Bowen's cases was about two and a half weeks; in Howe's cases it was double this period. Bowen's cases occurred in children; none of them were fatal, and the trunk was, as a rule, free of eruption, which was not true in the cases described by Howe. Howe was inclined to attribute the eruptions to infectious material introduced at the time of or after vaccination. The cases occurred at a time when smallpox was prevalent in epidemic form, and when thou- sands of vaccinations were being performed. While these eruptions, when compared with the number of vaccina- tions performed, are extremely rare, no effort should be spared to deter- mine their cause with a view to their future avoidance. It is possible that they are manifestations of an extraneous infection through the vaccine wound. In this connection the investigations of Fernet and Bulloch^ into the causation of acute pemphigus are of interest. These writers report and analyze eight cases of acute pemphigus in butchers; six of the cases proved fatal in from twenty-four hours to eighteen days. Three patients gave histories of wounds which continued to suppurate up to the time of the pemphigus outbreak. The period of incubation would appear to be very long if the disease arose from an infection, as is suggested. In the three cases referred to the wound antedated the eruption three months, two months, and five weeks, respectively. Special interest attaches to one case, in which the patient is alleged to have inoculated himself by contact with a bullous eruption on the udders of a coAV. Psoriasis. — Psoriasis is known to have made its first appearance at the point of vaccination, and also as a generalized outbreak after vaccinia. No one, however, who is at all familiar with this disease would look upon vaccination as a cause of psoriasis. It may simply determine the time of outbreak in an individual predisposed to this common skin affection; it is quite possible that those persons who developed psoriasis after vaccination would not have been attacked with this disease until a later period. The occurrence of postvaccinal outbreaks of psoriasis has been noted by Klamann,^ 1 case; Camp- bell,* 1 case; Roh€,* 2 acute general cases of psoriasis after vacci- 1 Cases of Bullous Dermatitis Following Vaccination, Journal of Cutaneous Diseases, 1903, p. 254. 2 British Journal of Dermatology, 1896, pp. 157 and 205. 3 Jahrbuch f. Kinderheilk., 1879, Bd. iv. p. 371. ^ Arch. f. Derm., 1877, p. 311. 5 Journal of Ciitaueous and Genito-urinary Diseases, 1882-83, p. 11. UlSTOLOd Y Of TIIK Vy\(!(!INK LESION 8'} nation; Piffard/ 1 case; Wood,^ 2 case."?' Hyde,'' 1 ease; Gaskoin/ 5 cases; Chain})ard,''' 1 case; and Kiohlanc," 1 case. Furunculosis. — (Jropsof fxjils have occasionally been observed dur- ing the course of and following vaccination. The complication is usually a trivial one, the furuncles disappearing in a short time. Sinigar^ met v^ith 21 cases of furuncles among IKK) vaecinations in a large institution, l^he boils develojx'd, as a rule, late in the course of the vaccinia. One case appeared on the tenth day, 1 on the sixteenth, 4 on the twenty-second, 1 on the twenty-fifth, 2 on the twenty-seventh, 2 on the twenty-eighth, 4 on the twenty-ninth, 3 on the thirtieth, and 3 on the thirty-fifth day after vaccination. As bearing on the cau.se of this complication, it is interesting to note that 13 of these cases developed among epileptics, who, as Sinigar remarks, include some of the dirtiest and most troublesome patients in the asylum. HISTOLOGY OF THE VACCINE LESION. But little literature is available upon the subject of the histological changes in the vaccine pock. The following description is condensed from Copeman's'^ presentation of the subject: The vaccine lesion passes through three more or less defined stages — namely, papule, vesicle, and pustule — just as does the characteristic lesion of smallpox. In both diseases the papule results from inflam- matory changes which are most pronounced in the epithelial cells of the mucous layer of the epidermis. Through certain degenerative processes, the most conspicuous of which are cell liquefaction and intercellular oedema, the papule becomes converted into a vesicle. The vesicle is made up of numerous loculi or compartments which are formed by the spinning out of elongated epithelial cells. The more pronounced swelling and vacuolation of the cells upon the advancing edge of the vesicle leads to greater bulging upon the periphery, giving rise to the umhilication. The process is identical in vaccine and vario- lous vesicles. Kent^ examined a series of vaccine vesicles removed by Copeman at various stages of development from the calf. At a quite early stage an outpouring of leukocytes occurs toward the site of injury. In the course of time each bloodvessel is surrounded by a mass of leukocytes which rapidly increase and convert the originally transparent fluid of the vesicle into a purulent fluid, thus giving rise to the pustule. The rupture of the epithelial trabecule or partitions converts the multilocular pock into a unilocular one. The fluid now gradually becomes inspissated and with the necrosed remains of epithelial cells dries into a crust. Cicatrization and healing go on beneath the crust; 1 Journal of Cutaneous and Geuito-urinary Diseases, 1882-S3, p. 119. 2 Ibid., p. 161. 3 itid., p. 14. * On Psoriasis or Lepra, 1875, p. 49. 5 Annales de derm., 1895, p. 498. « Ibid., p. 880. ^ Vaccinal Complications, Lancet, 1902. s Loc. cit., p. 73. 9 Britisb Medical Journal, 1894, vol. ii. p. 633. Quoted by Copeman. 84 VACCINIA the depth of the resulting scar depends upon the extent of destruction of the true skin. The minute histological changes in the vaccine lesion have been studied by Gustav Mann,^ for whom Copeman excised lesions at differ- ent stages of development from the calf. In a specimen removed within an hour after vaccination the wound is blocked by a clot which externally is of a coarse, granular nature, and between the edges of the epidermis finely granular. The bloodvessels close to the injury are dilated and many completely thrombosed with leukocytes. Red corpuscles may be seen adhering to the lumen of the capillaries and arteries. The nuclei of both the epidermal and dermal cells are swollen and the basophile chromatin contained in them is doubly increased. In the dermis an infiltration of leukocytes into the loose connective tissue is visible. At the end of twenty-four hours the epithelium close to the injury has increased twofold or threefold in thickness and a characteristic phenom- enon is already noticed, namely, the formation of Guarnieri's supposed parasites. The nuclear and nucleolar chromatin is increased and a considerable portion of the latter leaves the nucleus and is found lying free in the cytoplasm. The granules may fuse and give rise to more or less solid spheres lying alongside of the nucleus or even indenting it. From the twenty-fourth to the forty-eighth hour the dermis shows a gradually increasing oedema, associated with an emigration of leuko- cytes. As a result of the oedematous condition the lymph is prevented from escaping downward by the dense elastic layer of the dermis and the thick fibrous bundles of the hypoderm. Toward the periphery the lymph channels are blocked by leukocytes, and there is left but one path for the lymph, namely, through the basal membrane and then through the spaces between the epithelial cells. These lymph spaces are distended by the fluid, which becomes limited by the dense and resistant horny layer. At the end of three days three zones may be distinguished. Farther away from the line of inoculation the only noticeable change is a dilata- tion of the interepithelial lymph channels. All of the cells immediately within this region, save the horny cells, are swollen and contain granules like those in the granular layer, thus indicating a premature aging of the cells. The dermis beneath fonns large bullae, the walls of which are made up of compressed connective-tissue cells and leukocytes. No wander- ing cells are seen in the blebs, but fairly numerous bacilli singly and in pairs. Still nearer the point of inoculation the epithelial cells show enlarged nuclei, which undergo fragmentation into six or twelve smaller nuclei. Concurrently with the formation of these multinucleated giant cells there are seen greatly distended lymph vesicles in the epithehum, the 1 Quoted by Copeman, loc. cit. lIlSTOLOdY OF Till': VA(J(;[NI<: LESION 85 walls of which are made up of stretched and degenerated ej;iUirli;il cells. The vesicles contain a fibrin reticuluin and vaiions rnifMo-organ- isms. Internal to the zone just described the giant cells are re[>iaced by cells but a fifth to a quarter of their size, and containing but one or two nuclei, which appear to be derived from the multinucleated giant cells. The centre of the vaccinated area shows no living epithelial fells, but merely the remains of the horny layer and a dense, dri(;d blood chjt. The above changes hold good for the fifth day, the only diH'erence being an increase in size of the central necrosed area and a lateral spreading of the zone of infection. The increased infiltration of leukocytes causes the central area to necrose more and more, the connective-tissue elements succu]id)ing to the pressure exerted by the wandering cells. The hypoderm shows, especially about the fifth day, a considerable swelling of the thick, white, fibrous bundles called forth by the great activity of the fixed connective- tissue cells. Copeman considers the most characteristic feature of vaccination to be the appearance, immediately outside the necrosed area in the super- ficial, loose dermal tissue, of a number of globular masses, varying in size and arranged singly or in pairs, and which are colored by a special staining process. At the spreading edge, very short bacilli are seen. It is suggested that the large globules represent either a capsulated, sporulated, or involuted stage of the bacillus which Copeman elsewhere intimates may be the specific microbe of the disease. Much that pertains to the bacteriology of vaccinia will be found in the chapter on the pathology of variola. Tyzzer^ made a careful experimental study of vaccination and vario- lation lesions in animals, particularly with reference to the presence of Guarnieri's bodies. He successfully inoculated the corneas of twenty- five rabbits with vaccine lymph, and the corneas of twenty rabbits with variolous lymph. In addition a number of calves were vaccinated, some upon the cornea and others upon different parts of the cutaneous and mucous surfaces. He interprets the cycle of development of the c}i;orrhyctes variola; in vaccinia as follows: Injection: Epithelial cells are invaded by small forms in which it is difficult to distinguish structure. These small forms are found between cells and in various parts of the cytoplasm, but after their entrance into the cell they take a position near the nucleus. Groivth : After becoming located near the nucleus they become larger, and with tliis growth the character of their structure becomes apparent. They then consist of a reticular protoplasm in which is a clear spot containing a mass of basic staining material. Although it is impossible to distinguish a nuclear membrane bounding this clear spot, it seems probable that this clear spot with the granule in it is the chromatin of the organism. The 1 The Etiology and Pathology of Vaccinia, Journal of Medical Research. February, 1904. 86 VACCINIA organism is situated n a space in the cell, generally many times its own volume. This space is usually continuous with or is a part of the perinuclear space. Division of the Nuclear Material: Certain forms, in which the chromatin mass is irregular, precede those in which the chromatin is divided. In the latter the chromatin granules may be few or numerous. The chromatin granules later take a peripheral position, where they then form the centres of minute masses which bulge from the surface. Multiplication : These small masses, becoming free, are found in the space occupied by the segmenting form and in the cytoplasm of the same cell. They constitute the small forms described as the first of the series. They now scatter and penetrate neighboring cells. The invasion of the surrounding normal cells by the small forms resulting from this multiplicative process constitutes autoinfection, and by it the process extends. The immediate effect of the parasite is to cause an increase in size of the epithelial cells. This increase in cell volume is accompanied in the corneal lesion by proliferation. The' exudation which usually accompanies the lesions is secondary to the degeneration of the epithelium. Tyzzer states that he is "fully convinced that the vaccine body is an organism and represents the etiological agent in this disease." THE BLOOD IN VACCINIA. There is a constant leukocytosis during vaccination, the leukocytosis appearing in two waves, according to Sobotka.^ The primary one (varying from 12,000 to 23,000) is observed from the third to the seventh day, and a secondary wave (10,000 to 17,500) from the tenth to the twelfth day. Billings^ states that, no changes are exerted upon the haemoglobin or red cells by vaccination, but a definite leukocytosis is produced. The counts average about 15,000 leukocytes per cubic millimetre. The maximum of the leukocytosis is reached during the height of pus- tulation of the vaccine lesion, after which a gradual diminution in the white cells takes place. 1 Zeitschr. f. Heilk., 1893, Bd. xiv. p. 349. 2 Medical News, lh98, vol. Ixxiii. p. 301. CHAPTER 11. THE RELATIONSHIP OF COWPOX OR VACCINIA TO SMALLPOX. It has taken almost a century of experiiiKsntution to prove the truth of the statements, made by Jenner in his first publication, that smallpox and cowpox were modifications of the same disease. What a tribute to the intuitive discernment of this great man! The experiments which have led to the general (although not univer- sal) acceptance of this view have been in the direction of the conversion of smallpox into vaccine by variolation of the cow. It is impossible to produce in the cow a generalized eruption similar to the smallpox erup- tion in man; it is, moreover, impossible to intensify the virulence of, cowpox and convert it into smallpox, but it is possible to convert the virus of human smallpox into vaccine virus by passage through the bovine species. The English Royal Commission on Vaccination presents in its official report (1898) a valuable review of this subject, from which we freely abstract. Most of the endeavors to transfer smallpox from man to the bovine species have been unattended with success, and have usually been with- out any definite result. This has been true not only in attempts to produce the disease by infection through the respiratory and digestive tract, but also in many instances by direct inoculation. Most of the inoculation experiments may be grouped in three categories. The first class includes experiments in which inoculation of smallpox matter into the cow produced a vesicle identical with or closely resem- bling the vesicle produced by vaccine inoculation. If a typical vesicle was not produced at the first inoculation, the transference of the mate- rial from the first vesicle would in a second or third remove in the cow give a typical vesicle capable of producing in man results indistinguish- able from ordinary vaccination. Such experiments were carried out by Thiele (1838),'Ceeley (1840), Badcock (between 1840 and 1860), Voigt (1881), Haccius and Eternod (1890), King (1891), Simpson (1892), and Hime (1892). In the second category belong the experiments performed by Klein and Copeman. Klein, who in 1879 had apparently failed in thirty-one attempts, subsequently found, in 1892, that the result of the first inocu- lation in the cow of smallpox matter was not a distinct vesicle, but merely a thickening and redness of the wound. Lymph pressed from the thickened wound produced, when inoculated into a second animal, a similar but more pronounced result. In the third and fourth cow the reddening and thickening were still greater. L^^Bph squeezed 88 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX from the wounds of the fourth cow produced typical vaccinia in a child, and the crust from the child when reinoculated into the cow produced similar vaccine vesicles. Copeman obtained results of a similar char- acter, and succeeded in the third remove in the cow in producing a reaction which showed commencing vesiculation. In the third class may be placed the results obtained in an elaborate investigation conducted by a commission of the Society of Medical Sciences of Lyons, under the direction of Chauveau (1865). Their results may be briefly summarized as follows: Inoculation of the cow with smallpox matter in any one of the thirty animals experimented upon did not give rise to a vaccine vesicle. Never- theless a definite result was obtained in the form, not of a vesicle, but of a thickening and inflammation of the wound; when a puncture was made this became a papule. Lymph squeezed from such a papule and inserted into a second animal gave rise to a like papule; and this, again, might be used for a third animal, but often failed; and the effect could in no case be carried through more than three or four removes. When the inoculation was repeated on an animal in which a previous inocula- tion had produced such a papule, no distinct papule was formed, and, moreover, lymph squeezed from the seat of inoculation produced no effect at all when used for subsequent inoculation of another animal. Thus Chauveau and his commission found that smallpox implanted in the cow gave rise to a specific effect which was not cowpox, but was of the nature of smallpox, though its manifestations in the cow were different from those of smallpox in man. Lymph from the lesions in the first cow was capable of producing smallpox in the human subject. It is evident from the above experiments that the results obtained from attempted variolation of the cow have exhibited marked varia- bility. The vast majority of the inoculations have been of a negative character. These, however, do not invalidate the positive results which have now attained a very considerable number, and which have been reported by careful and trustworthy investigators at different times and in different countries. When reaction does result from the insertion of variolous material into the cow, the local effects vary somewhat. There may be directly produced a typical vaccine vesicle, or, as occurs in most instances, a papule or inflammatory induration which on further inoculation yields a vaccine vesicle. We are thus forced to the conclusion that smallpox _^s converted into cowpox by passage through the tissues of the bovine species. The transformation is at times sudden and complet&. _at other^ __times^gradual and incomplete, and sometimes fails altogether^__ The circumstances wliichTavor such' a are but little unHer stood, although it would appear that the youth of the inoculated animal is a factor. The best results have been obtained with calves not ove rjjiree or four months old. " ~~ — ^ It is claimed that it is possible for cows to develop cowpox through inhalation of the contagium of variola. In this connection it is inter- esting to refer to an occurrence noted by Ceely in 1840. This writer BELATIONSmr OF f/OWPOX on VAC'C'/NFA TO SMALLPOX HU states that he observed cowpox develoj) in five; out of eight milch cows twelve to fourteen days after they were seen li<.'king some floek from a mattress upon which a jjatiejit died of eonfliuMit smallj)OX, and which had been spread upon the ground to be aired. (Jareful investigation revealed the fact that the animals, which had been on the farm for considerable time, were in good health before their admission to the pasture where the exposed bedding lay. There had not been any cow- pox in the neighborhood. That the cowpox may have resultcfl hom a volatile contagium derived from the smallpox-infected bedding is not improbable, in view of the simultaneous sickening of the cows after a period of incubation of about two weeks. The possibility of infection through the digestive tract, which Chauveau and others have shown may take place, must not be entirely ehminated in seeking the explana- tion of the manner in which the disease was received. That the transformation of the smallpox into the vaccine virus is frequently a gradual process which is not completed in the first bovine inoculation has been on more than one occasion unfortunately proven by the transference of true smallpox to persons who were vaccinated with material taken from the first cow. In 1836 J. C. Martin, of Attleborough, Massachusetts, inserted into the udder of a cow lymph taken from a smallpox lesion upon the body of a man who died of variola. Subsequently matter derived from the cow was inserted into the arm of about fifty persons. Nearly all of these individuals developed smallpox in the due course of time, and three of the number died. The disaster so preyed upon the mind of the unfortunate physician that he became insane. A similar occurrence has been reported by Dr. Thomas F. Wood.^ We quote his own words: "I had occasion just after the war (1865- 66), while in charge of the Wilmington Smallpox Hospital during an epidemic of the disease, to go over the same ground of attempting the production of artificial cowpox. It happened, during the progress of the experiment that an army medical inspector, whose name I have forgotten, was making a tour of the hospitals; hearing of my experi- ments, he visited my hospital and after examination pronounced the small vesicles genuine cowpox, and confirmed his faith in his opinion by making some inoculations on the arms of two children in an Irish family near by. The inoculations resulted in a genuine smallpox, which went through the family in various grades of intensity." Other instances of a similar character have been recorded. That such infections are not the result of inoculation with the unchanged variolous material originally introduced into the cow is evidenced by the fact that smallpox has been conveyed to the human subject from a papule of the second remove. (Lyons Commission.) These deplorable accidents have directed attention to the unwisdom of using material of the first or second bovine generation, and empha- size the importance of passing the variolous virus through four or five or more animals before employing it upon man. 1 Chicago liledical Journal and'Examiner, October, ISSl. 90 RELATIONSHIP OF GOWPOX ORIVACCINIA TO SMALLPOX The demonstration of the fact that vaccine virus may be produced from a variolous source is of great importance. It is readily seen that an epidemic of smallpox occurring in some inaccessible country, w^here active vaccine lymph could not be obtained, could be made to supply the material for its own suppression. The proof of the common ancestry of vaccinia and variola refutes the theoretical arguments advanced by Crookshank and others against the protective influence of vaccination. These writers have attempted to fortify their belief in the inefiicacy of vaccination by assuming the duality of these two affections, the opinion being maintained that an attack of disease could only afford protection against the same disease. The premise being false, the entire inference falls to the ground. Modern bacteriological research strongly supports the empiric dis- covery of Jenner. Pasteur and others have shown that it is quite possi- ble, by the use of an attenuated virus, to produce a mild attack of an infectious disease and thus protect against a more severe type of the same infection. That vaccinia and variola are in essence the same disease is scarcely to be doubted. The passage of smallpox matter through the compara- tively insusceptible tissues of the bovine species attenuates the virus to such an extent that it is permanently robbed of the virulence which it once possessed. Instead of producing a dangerous and contagious disease, it gives rise to an innocent affection capable of transmission only by inoculation, and having the beneficent property of protecting against the original disease which gave it birth. Shakespeare might well have had vaccination in mind when he wrote: " Take thou some new infection to thine eye, And the rank poison of the old will die." Jenner was strongly impressed with the fact that smallpox and cow- pox were one and the same disease. Baron quotes the following notes which were left by Jenner in one of his journals: "The origin of the smallpox is the same as that of the cowpox; and as the latter was probably coeval with the brute creation, the former was only a variety springing from it." Cowpox and smallpox are "not hona fide dissimilar in their nature ; but, on the contrary, identical. On this ground I gave my first book the title of * An Inquiry into the Causes and Effects of the Variolm Vaccinae' — a circumstance which has been since regarded by many as the happy foresight of a connection which was destined by further evidence to become more warranted." From the above it will also be seen that Jenner regarded cowpox as the progenitor of human smallpox. This belief he reiterated on a number of occasions. It will be remembered that in the beginning of the "Inquiry" he says: "This fluid (from the grease) seems capable of generating a disease in the human body (after it has undergone the modification I shall presently speak of — viz., transmission through the cow) which bears so strong a resemblance to smallpox that I think it highly probable that it may be the source of that disease." Again, in a NAT!/ HAL SOUnaiCH OF LYMPH 91 letter to l)e Carro in IS()3 he remarks: "1 am happy to find an ojjinif^n taken up by in(! <\,m\ nicntionc^l in my first [)ubli('jition hu.s so able a supporter as yours(!lf. I thought it highly probal^lc tliat tlic smallpox might be a mahgnant variety of the cowpox, but this idc-a was scouted by my countrymen, particularly P. (Pearson) and W. (VVoodville)." ' Whether smallpox is a cowpox of exalted virulence or cowpox an attenuated smallpox remains apparently unsolvable. Copeman is inclined to support the view championed by Jenner. He says:^ "The artificially inoculated form of cowpox which we term vaccinia is noth- ing more nor less than variola modified by transmission through the bovine animal. Perhaps the most reasonable inter[)retation of such results may be that smallpox and vaccinia are both of them descended from a common stock — from an ancestor, for instance, which res(;m- bled vaccinia far more than it resembled smallpox. It is conceivable, indeed, that the seeming vaccinia, obtained in the calf by inoculation of smallpox matter into that animal, may after all be but a reversion to an antecedent type." The Various Natural Sources of Lymph. — During the investigation of the casual cowpox, Jenner conceived the idea of propagating the dis- ease by inoculation after the manner of the smallpox, first from the cow, and finally from one human being to another. The first vaccina- tion was performed in 1796 upon a lad by the name of James Phipps, the virus being taken from the hand of Sarah Nelmes, a dairymaid who had been accidentally infected with the cowpox. Notwithstanding the resemblance of the vesicle produced to that obtained by variolous inoculation, Jenner could scarcely believe that the patient was secure from the smallpox. He was, however, inoculated with smallpox virus some months afterward and on numerous occasions subsequently, but each time without result. In 1798 Jenner again came into possession of virus from the cow and made arrangements for a series of inoculations. "A number of children," he says, "were inoculated in succession, one from the other; and after several months had elapsed they were exposed to the infection of smallpox, some by inoculation, others by variolous effiuvia, and some in both ways, but they all resisted it." This strain of lymph was suffered to die out and none was found until Woodville, in 1799, discovered a case of natural cowpox in Gray's Inn Lane. With this lymph he vaccinated seven persons, and likewise certain others from the hand of a dairj^maid who had contracted cow- pox from one of the cows at this place. This virus was successively passed through hundreds of persons and became known as "Wood- ville's lymph." Dr. Pearson also discovered a case of cowpox in a dairy at ]Maryle- bone Road, although some of the lymph which he sent out was probably obtained from Woodville's cases. Woodville and Pearson both dis- tributed the lymph widely, and supplied it to many of the continental 1 Vaccination, Loudon, 1899, p. 64. 92 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX cities. Although Jenner himself used some of Woodville's lymph, he later found another source of supply in the dairy of Mr. Clark, in Kentish Town. Dr. Waterhouse, of Boston, secured some of Jenner's lymph through Dr. Haygarth, of Bath, who obtained it from Mr. Greaser. De Carro of Vienna, Stromeyer of Hanover, and others also obtained some of the Jennerian stock. At this time other instances of natural cowpox became known. Sacco, a faithful disciple of Jenner, discovered a case of cowpox on the plains of Lombardy in 1800. A strain of lymph was developed from this, some of which was sent to De Carro, at Vienna. This enthusiastic vaccinator forwarded a supply to Constantinople, and subsequently other lymph of Italian origin to India; the latter virus was of equine ancestry, having been developed by Sacco from a case of accidental horsepox in a coachman. Natural cowpox is said to have been found in Naples in 1812, and in Piedmont in 1830. Macerdoni discovered it in cows of Swiss breed in Rome in 1832 and 1834, and in the latter year a lymph stock was established. Cowpox occurred in Wiirtemberg in 1802, and in 1812 Bremer observed it in Berlin. Fischer saw a case near Luneberg, and Mende noted one in Greifswalde. Giesker, Luders, Ritter, Riss, and Albers encountered cases in various portions of Germany. Numann says that in Holland cowpox was seen in 1805, 1811, and 1824. An epizootic of this disease among cows is said to have occurred in Russia in 1838, in a small village near St. Petersburg. In France cowpox was first observed in 1810 in the department of La Meurthe; in 1822 it was found in Clairvieux. In the next half-cen- tury it was discovered some score or more times in different parts of the country. A famous strain of lymph was derived by Bousquet in 1836 from a case of cowpox at Passy, in the environs of Paris. The disease occurred upon the hand of a dairymaid, from whom Bousquet vaccinated a number of children. In the second and subsequent removes, the virus proved itself much superior to the lymph which had then been long in use. Bousquet in a painstaking memoir accurately compared the course of the old and the new lymph. These results were confirmed by Bruchir, of Versailles, and by Steinbrenner, who worked with Mrs. Pass's lymph in 1840, and compared it with virus obtained from other sources in 1841 and 1845. Similar results were obtained by Estlin, of Bristol, in 1838 with lymph derived from a Gloucestershire farm. Don F. Xavier Balmes, director of the Spanish Vaccine Expedition, discovered cases of natural cowpox in the Peruvian Andes and in other regions of South America. Ceely, in 1841, stated that he had experimented with lymph from more than fifteen sources, six of which represented cases of natural cowpox. In 1866 a milch cow with cowpox was discovered at Beaugency, France. A valuable strain of lymph was developed from this case by Professor Depaid. It was from this source that Martin, of Boston, ANIMAL VA(H!INATr()N 93 obtained lymph with which he inaugurated animal vaccination in America in 1870. It may be worth while to state the great probability that in America only has th(^ "stock" of the Beaugency virus been perpetuated. The strain of lymph now used by the English Government Animal Vaccine Establishment was derived in 1881 from a case of cowpox at Tvaforet, near Bordeaux. In 1881 Martin, of Boston, observed a case of spontaneous cowpox at Cohasset, a small town in Massachusetts. The Cohasset and the Beaugency stocks were for a while propagated separately in this country, but subsequently became mixed. Fischer and Voigt in Germany, Haccius in Switzerland, King in India, and others have of late years propagated cowpox virus by vario- lating heifers, producing thus what has been called variola-vaccine lymph. We are conscious of a reassuring sense of security in the knowledge that reliable vaccine lymph can be produced by the inoculation of vario- lous material into a succession of bovine animals, for if existing strains of lymph are lost or become too much attenuated, we have at hand a means of replenishing the prophylactic virus. Animal Vaccination.— By the term animal vaccination is meant the propagation of lymph through successive series of calves or heifers, the original virus being derived ah initio from a case of spontaneous cowpox. Martin^ says the term can and has been applied to: 1. Vac- cination casually or intentionally from the original spontaneously occur- ring disease in the milch cow. 2. Retrovaccination with virus obtained from the vaccine disease in the human subject. 3. From vesicles, said to be vaccine vesicles, obtained by variolation of kine, or the inocula- tion of bovine animals with the virus of smallpox. 4. The method of true animal vaccination, or the inoculation of a bovine animal with the virus of original spontaneous cowpox; from this another, and so on in continuous and endless series as a source of vaccine virus. In 1810 a Neapolitan physician, Galbiati by name, published an article advocating animal vaccination. He had employed this method for some seven years, believing that it ensured greater vigor and purity of the lymph. Galbiati seems to have espoused this procedure because of the occasional transmission of syphilis by arm-to-arm vaccination. The method was at first extremely unpopular, and its author, abused and ridiculed, is said to have become insane and to have ended his life by suicide. His disciple and successor, Negri (to whom Ballard gives credit for the origin and introduction of animal vaccination), continued the propagation of lymph from animal to animal, and successfully brought the practice into general favor. The l}Tiiph wliich he employed at first (in 1842) appears to have been of human origin, but subsequently he obtained material from a case of natural co'u^ox in Calabria. Palas- ciano, a townsman of Negri and a strong'advocate of animal vaccina- 1 Report on Animal Vaccination, read before the American Medical Association, 1S77. We are indebted for much of the information conveyed in this chapter to this admirable report. 94 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX tion, disseminated knowledge on this subject throughout Europe, by an address before the Medical Congress of Lyons. A young French physician, Lanoix, one of those present, became greatly interested in the subject and subsequently went to Naples to study animal vaccina- tion under Negri. In 1864 he returned to Paris with a heifer which had been vaccinated at Naples. Chauveau and Diday were permitted to take some lymph from this animal at the Lyons railway station. Lanoix proceeded to Paris and in company with Chambon established a private institution for the propagation of animal lymph. The new practice excited considerable interest, and the Academy of Medicine, encouraged by a government appropriation, appointed a commission with Professor Depaul at its head to investigate the subject. The report was favorable to animal vaccination, although some dissentient opinions were expressed. About this time natural cowpox was discovered at Beaugency, and Depaul had an opportunity of employing lymph from this source. It is said that this lymph stock was lost during the siege of Paris in the Franco-Prussian War, and that the only extant derivative from this source is that sent to America. From Paris the practice of animal vaccination spread to Belgium through the efforts of Warlomont, who obtained some Neopolitan lymph from Lanoix. He later, in 1868, discovered a case of spontaneous cowpox at Esneux (Liege). Through private enterprise animal vaccine establishments were organized in the various European capitals. The commercial spirit rendered a real service to humanitarian science. Pissin opened up such an animal vaccine institution in Berlin, and Vienna soon had a similarly equipped establishment. Haccius in 1882 founded the "Institute Vaccinale Suisse," which received a cer- tain recognition at the hands of the Swiss government. Paris now has an "Institut de Vaccine Animale," which under the direction of Cham- bon and St. Yves Menard, supplies the municipality with all the lymph required for public vaccinations. In Germany all or nearly all of the vaccine establishments are under governmental control and supervision. England in 1881 authorized the founding of the Government Animal Vaccine Establishment in Lamb's Conduit Street, and the use of animal lymph has now practically superseded arm-to-arm vaccination. To Dr. H. A. Martin, of Boston, belongs the credit of introducing animal vaccination into the United States. In 1870 he sent a special agent to France, who returned with an abundant supply of Beaugency lymph. Having secured a herd of young, healthy animals, he at once began the propagation of animal lymph. He and his son subsequently discovered a case of spontaneous cowpox in Cohasset, Massachusetts. Advantages of Animal Vaccination. — The use of calf-transmitted lymph has certain advantages over long humanized virus; these maybe stated as follows: 1. Animal vaccination produces a vaccinia which approaches more nearly the Jennerian prototype, and reaches therefore a greater degree ADVANTAfJICS OF AN/AfAL VA(!N 95 of perfection than that produced by long liunianizcd virus. The cow- pox casually produced on the hands of dairymaids was believed by Jenner to confer full and cotn])lete protection against smallpox. The bovine species ap[)ears to be; the natural soil of the j)roj)hylacti(; pock, and the view is maintained by numy that l)ovine lymph, or that fJerived from an early human remove, creates a more complete and more lasting immunity. The inferiority of humanized virus is doubtless due to a weakening or degeneration of the lymph product as a result of the long- continued transmission through the human subject. Jenner really anticipated such a deterioration in the quality of vaccine lymph from this cause. Copeman says that "in the present state of our knowledge, however, such enfeeblement of the specific virus can hardly be regarded as probable, except. under conditions that may be obviated by reasona- ble skill and care on the part of the operator. Jenner early discovered that vaccine lymph only exhibited its full degree of activity when taken at the stage of maturation of the vesicle, and before its contents became at all purulent. If this precaution be observed, together with strict cleanliness in the removal and insertion of the lymph, experience has shown that no appreciable degeneration can be demonstrated." 2. The use of animal lymph precludes the possibility of transmitting by vaccination diseases peculiar to the human species. One of the most weighty reasons that led to the adoption of animal vaccination and to its preference over arm-to-arm transmission was the recognition of the possibility of inducing syphilis by vaccine inoculation. No matter how rare such an accident might be, the remotest liability of such an occurrence constitutes a serious argument against the use of humanized lymph. The bovine species being totally insusceptible to syphilis, l^-mph derived from this source is incapable of transmitting such infection. Erysipelas appears to be a much rarer complication of vaccinia since the general employment of animal l}Tnph. It is probable that many cases of vaccinal erysipelas in the past were due to secondary infection of the vesicle at the time that it was punctured to withdraw lymph for further inoculations. The almost universal use of animal lymph removes the necessity of tapping the vaccine vesicle, thus ren- dering erysipelas from this cause practically non-existent. Again, many cases of erysipelas were doubtless the result of the emplo}aiient of crusts which had not been wisely selected or properly preserved. "\Miat- ever the cause or causes may have been, actual experience shows an enormous reduction in the relative and aggregate incidence of this com- plication since vaccination w^ith humanized lymph has fallen into desuetude. There is little or no danger of transmitting tuberculosis in bovine lymph, inasmuch as, in addition to the diagnostic use of tuberculin, all calves are killed and carefully examined in well-regulated establish- ments before the virus is sent out; furthermore, it has been sho-um that the admixture of glycerin to the l>Tnph is capable of destropng the life of any tubercle bacilli that may be present. 3. Animal vaccination offers an almost inexhaustible supply of vac- 96 RELATIONSHIP OF COWPOX OR VACCINIA TO SMALLPOX cine lymph, for the number of calves yielding the same can be multi- plied at will. During extensive epidemics of smallpox, v^hen human vaccine was employed, the community was often placed in an embarrass- ing and dangerous predicament owing to an insufficient supply of vaccine material. During the great pandemic of smallpox from 1870 to 1873, a veritable vaccine famine existed in many countries. All sorts of vaccinifers were drawn upon, and much worthless lymph derived from spurious and irregular cases was employed, of course, with entirely unsatisfactory results. 4. Animal lymph appears to give a much larger percentage of suc- cessful revaccinations than long humanized virus. Martin says: "The number of those who, in revaccination with the old, long humanized virus (not that of early human removes) experience vaccinal effect may be stated at the outside at 35 per cent. The number of those revaccinated with equal care and repetition with animal virus and virus of very early human removes, I affirm to be a fraction over 80 per cent. — a differ- ence of 45 per cent. ; and this 45 per cent. I firmly believe to approxi- mately represent the number of those insensible to the enfeebled influ- ence of long humanized virus, but sensible to the intense contagium of variola just in the same degree as sensible to the intense power of bovine virus and that of the early human removes from it." Comparison of the Course of Vaccinia Produced by Original Cow- pox Virus, Long Humanized Virus, and Calf-transmitted Virus, Re- spectively. Original Cowpox Virus. — ^The vaccine disease produced by virus from a case of original cowpox or from early human removes therefrom lasts from twenty-one to thirty-two days, counting from the insertion of the lymph to the falling of the crust. At the end of the third or beginning of the fourth day papulation occurs; vesiculation takes place at the end of the fifth day, but the vesicle continues to grow until the decline of the areola or even a few days after this. The vesicle has a pearly or slightly bluish tint; it really resembles, as Jenner re- marked, "a section of a pearl on a rose-leaf." The areola appears first about the end of the ninth or beginning of the tenth day and persists until the twelfth, thirteenth, or fourteenth day. Desiccation and forma- tion of the crust are not complete before the sixteenth or seventeenth day; the crust is never spontaneously detached before the twenty-first day and usually not before the twenty-fifth to the twenty-eighth day. Occasionally it will remain upon the vaccine site until the thirtieth or thirty-second day. The crust is round, thick, umbilicated, and of a rich brown or mahogany tint. A very decided febrile reaction attends the rise, development, and decline of the areola. This febrile disturbance was considered to be of great importance by the early vaccinators, especially Jenner, who regarded it as a sine qua non of vaccinal impression upon the system, and an indelible characteristic cicatrix remains after the termination of the disease. In the early days it was not at all rare for the vesicle to break down and ulcerate, leading to a spreading and troublesome loss of tissue and occasionally to erysipelatous infection. COURSE OF VA(J(JJNIA WITH D/FFFJU'JNT LVM/'J/S f)7 Long Humanized Virus. — ^The most distirif^uisliirif^ characteristic of the vaccinia produced l)y lonf^ huinanizcd virus is the f)revitv of the course of the disease. The duration varies very much with different lymph stocks. With a virus used by Martin and obtained from Ceely, the course of the disease from the time of insertion of the lymph to the spontaneous detachment of the crust was l)ut eleven days; whereas with a lymph of French origin employed by Martin, th(! crust came off from the twenty-first to the twenty-sixth day. Lymph from the National Vaccine Institution of Great Britain ran a course of fourteen days to the falling of the crust. These various "stocks," although propagated for years, preserved their distinctive durations. It was even found, when two different lymphs were inserted — one on one arm and the second on the other — that each strain retained its special features. In brief, it may be stated that long humanized lymph produces a vaccinia of shorter duration and milder intensity than original and early virus. With the lymph which induced a vaccinia of eleven days' duration, the areola was formed on the seventh day and sometimes on the sixth. The Jennerian "stock" of the British Vaccine Institution induced a vaccina of fourteen days' duration, the areola developing on the seventh or eighth day. The crust derived from vaccination with long humanized lymph is very small, thin, and often devoid of umbilication. The febrile reac- tion accompanying such a vaccinia is slight or absent, even when many insertions are made. Calf-transmitted Virus. — As would be expected the vaccinia resulting from the employment of calf-transmitted lymph closely resembles the disease induced by early human removes from original cowpox, such as were observed by Jenner. With the animal-transmitted virus, how- ever, the reaction is not so violently inflammatory as that which occurred with original cowpox lymph. Ceely, in 1840, stated his belief that the tendency to undesirable intensity in the original cowpox is tempered by successive transmissions through young animals. He inoculated a series of eleven calves and found that the objectionable qualities of the lymph, as determined by human vaccinations, w-ere gradually but pro- gressively eliminated. The animal virus now used usually runs its course from twenty-one to thirty days. Glycerinated Lymph. — To S. Monckton Copeman^ belongs the credit of advocating the addition of glycerin as a vaccine purifier, and of establishing the employment of glycerinated l}'mph upon a scientific basis. Glycerin had previously been used for the purpose of increasing the volume of the lymph and also as a Ivmph preservative. As far back as March, 1850, Mr. R. Cheyne- advocated (in a letter appearing in the Medical Times) the use of fluid hmph to which some glycerin had been added as superior to the dry points. In 1853 he 1 We desire to acknowledge our indebtedness for much of the material presented in this chapter to the admirable book of S. Monckton Copeman (Vaccination, its Natural History and Pathology, London, 1899), which we have freely consulted. * Copeman appears to have been unaware of Cheyne's work until a few years ago. 7 98 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX demonstrated to the presidents of the Royal Colleges of Physicians and Surgeons a child whom he had successfully vaccinated with glycer- inated lymph prepared six months previously. Cheyne admitted that he was indebted for knowledge of this procedure to the previous publi- cations of Mr. J. Startin on the therapeutic uses of glycerin. Miiller, of Berlin, further demonstrated the fact that vaccine lymph could be considerably increased in quantity by the admixture of glyc- erin without interfering with its specific activity. He proved that the lymph might be diluted with three times its bulk of glycerin without in any way lessening its potency. It is evident that Miiller's chief object was to increase the quantity of available l}Tiiph, a matter of much importance during smallpox epidemics, particularly when there was danger of a vaccine famine. With the same object in view Dr. Stephen Mackenzie, of the London Hospital, during the great smallpox epidemic in 1870-71, added glyc- erin to lymph in order to increase the amount just before conducting a large series of vaccinations. Dr. Warlomont, of Brussels, in 1882 placed upon the market, under English patent, a method of admixture of glycerin with vaccine lymph, but no mention was made of the contained glycerin until some years later. Copeman, in a paper presented to the International Congress of Hygiene, held in London in 1891, advocated the addition of glycerin to vaccine lymph for the purpose of purifying and preserving it. The method consisted in the "intimate admixture of a given amount of lymph, or rather vesicle pulp, with a sterilized 50 per cent, solution of chemically pure glycerin in distilled water, and in subsequent storage of the resultant emulsion in sealed capillary tubes for several weeks." Copeman had previously endeavored by diverse means to inhibit the growth in vaccine material of the various extraneous organisms, and if possible destroy them without weakening the specific activity of the lymph. These measures failing, he resorted to the addition of glycerin. Previous to Copeman's experiments there had been no appreciation of the influence of the glycerin as a bacteriological purifier of lymph when the mixture is stored for some time and protected from the access of light and air. When a glycerin emulsion of vaccine is prepared in the manner indicated by Copeman, an inhibition and later destruction of the foreign aerobic bacteria is brought about. The purification is a gradual one, as can be determined by making plate cultures of the lymph from time to time, and estimating the number of colonies of organisms present. Since the publication of Copeman's paper in 1891, other careful observers have fully substantiated the claims of this investigator. Chambon and Menard, in 1892, were not only able to purify and pre- serve lymph by glycerin admixture, but they claim to have produced an improvement in the activity of lymph which in its fresh state had given only mediocre results. Such a lymph produced after fifteen days' (iLYCERINATKI) LYMI'll 99 admixture with glycerin a |)assal)le vesiele, aiul ;ifl,(;i- forty, fifty, or sixty days a typical one. The improvcnnent in pot(!ncy was attrihuted by them to the gradual destruction of foreign bacteria in the fluid. Professor Straus, who made plate cultures of this lymph, achieved results identical with those obtained by Copeman, although the work was done prior to the publication of ("of)ernan's article. Fresh glyceiin- ated lymph gave rise to numerous colonies of various organisms, espe- cially the staphylococcus pyogenes aureus and staphylococcus albus, but when stored for fifty to sixty days plate cultures proved to be absolutely sterile as regards these extraneous bacteria. These experi- ments were repeated many times, but always with the same result. Leoni, in a paper read before the International Medical Congress, held in Rome in 1894, concludes that (1) recently collected vaccine is a contaminated vaccine, containing numerous foreign germs, some of which are capable of exerting pathogenic properties when inoculated into the system; (2) the contaminating organisms become extinguished in vaccine preserved for a certain period in glycerin; (3) vaccine pre- served in glycerin from one to four months after it is collected is the type of fure vaccine, with an exclusively specific virulence; (4) this is the quality of vaccine with which the hygienist of to-day should con- cern himself in the prophylaxis of variola. Klein has added the weight of his testimony as to the purifying influ- ence of glycerin on vaccine lymph. In stating his belief that the specific organism of variola is probably a spore-bearing bacillus, he incidentally remarks: " .... it is established that the active principle of vaccine is preserved in glycerin, although, as is also known, glycerin is a germicide for cocci and sporeless bacilli." In 1896 the German government appointed a commission presided over by Schmidtmann, and including Koch, Pfeiffer, and Frosch, together with the Directors of the Vaccine Institutes of Berlin, Cologne, and Stettin, to investigate into the best methods for the collection, preservation, storage, distribution, and use of vaccine lymph. The report stated that fresh lymph contained numerous bacteria which diminish progressively under the influence of the glycerin admixture. Streptococci and diphtheria organisms added to the hinph were killed in eleven days and twenty days, respectively. These experimenters, as well as Kitasato, in Japan, determined that glycerin w^ith distilled water could be added to the extent of from fifteen to twenty times the weight of vesicle pulp without destroying the vaccine principle. Copeman and Blaxall have shown that not only are the ordinary foreign bacteria of fresh lymph destroyed by glycerinization, but that pathogenic organisms such as those of tuberculosis and erysipelas, when added in large number for experimental purposes, also perish. The fact that the tubercle bacillus thrives particularly well upon agar containing 6 per cent, of glycerin does not invalidate the claim that this agent in a strength of 40 to 50 per cent, is a valuable microbicide. Indeed, Copeman and Blaxall and likewise Klein have proven that tubercle bacilli cannot be recovered after exposure for a month to the 100 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX action of glycerin, present to the extent of about 40 per cent., either in a culture in sterile bouillon or in fresh vaccine material. These investigators have furthermore shown that an emulsion of glycerinated lymph inoculated with active tubercle bacilli, and allowed to stand for a month, was incapable of producing tuberculosis in guinea-pigs, whereas the contaminated vaccine lymph without the glycerin added invariably produced this disease. Rosenau^ (1903), in a study of the germicidal action of glycerin, concluded that it has distinct but very feeble germicidal and antiseptic properties. Small quantities of glycerin, less than 10 per cent., added to nutrient media, have well-known powers of favoring the growth and multiplica- tion of many forms of bacteria. The presence of 50 per cent, of glycerin will restrain all bacterial growth. No growth or multiplication of bacteria takes place in nutrient media containing 32 per cent, of glycerin, but moulds grow in stronger percentages, viz., 40 to 49 per cent. In order to prevent the growth and development of pus cocci, at least 33 per cent, of glycerin must be present. The germicidal action of glycerin is probably due to its affinity for water, causing a dehydration of the bacteria. Glycerin ordinarily destroys the micrococci of suppuration, whether the^e be in pure culture or in the pus itself, within two weeks. This action varies according to the temperature. Pus cocci may live in glycerin for months in the ice-chest, whereas at the body temperature they die in a week. Glycerin has a selective influence upon the diphtheria bacillus, which succumbs much more quickly than most other organisms. The bacteria of the typhoid and colon group often show a marked resistance to the effects of glycerin in strong proportions. Glycerin in all strengths has practically no effect upon endogenous spores. Anthrax spores were kept alive and virulent two hundred days in the strongest percentages of glycerin, and at warm temperatures. Tetanus spores in pure culture, freed of all organic matter and washed free of toxin, may lose their virulence in glycerin in thirty days at the body temperature, but they live for months (one hundred and eighty days) at room temperature or in the ice-chest. Glycerin, therefore, cannot be depended upon to purify vaccine or other organic matter containing this contamination. The virulence of the spores is lost long before they actually die, for they still retain the power of growing and multiplying if placed under favorable conditions. Under these circumstances, therefore, they also regain their original pathogenoid properties. Glycerin has practically no effect on diph- theria toxin. At a meeting of the British Medical Association in 1896, Copeman and Blaxall presented a paper on " The Influence of Glycerin upon the 1 Director of the Hygienic Laboratory, United States Public Health and Marine Hospital Service, Bulletin 16, 1903. GLYCERIN ATI: I) LYAff'lf 101 Growth of liacteria." The bacteria employed in the experimentations comprised staphylococcus pyogenes aureus, staphylococcus pyogenes albus, streptococcus pyogenes, baf;illus pyocyuneus, hafillus subtilis, bacillus coli communis, bacillus diphtherite, and bacillus tuberculosis. Smallpox and vaccine material in the form of "crusts" and lymph were also employed. "Results: 1. No visible development of the micro-organisms em- ployed took place in the presence of more than 30 per cent, of glycerin. "2. None of the micro-organisms experimented with could be recov- ered after exposure for a month to the action of from 30 to 40 per cent, glycerin, with the exception of bacillus coli communis and bacillus subtilis when kept in the cold. "3. Bacillus coli communis, unlike bacillus typhosus, resists the action of 50 per cent, glycerin in the cold for a considerable period — a fact likely to prove of value as an addition to our present methods of differentiating these microbes one from another. "4. The samples of smallpox and vaccine material, whether as 'crusts' or lymph, were sterihzed completely, so far as extraneous microbes were concerned, in a week, by the presence of glycerin to the extent of about 40 per cent, in the broth tubes. This short period of resistance is, doubtless, in part to be explained by the fact that the smallpox crusts used in these experiments had been obtained several months beforehand. Presumably, therefore, the number of microbes which had been able to survive for so long a period the process of dry- ing would be much less than might be expected to be present in * crusts' recently obtained." Copeman sets forth the advantages of glycerinated lymph in the following terms: "1. By employing the method of glycerination of lymph pulp, great increase in quantity can be obtained without any consequent deteriora- tion in quality, the percentage of insertion success following on its use being equal to that obtained with perfectly active fresh lymph. "2. Glycerinated lymph does not dry up rapidly as does unglycerin- ated lymph, thus simplifying the process of vaccination. "3. Glycerinated lymph does not coagulate; so that it never becomes necessary to discard a tube on this account. "4. Glycerinated lymph can be produced absolutely free from the various streptococci and staphylococci which are usually to be found in untreated calf lymph, and which are, under certain circumstances, liable to occasion suppuration. "5. In like manner the streptococcus of erysipelas, in the event of its having been originally present in the IjTnph material, is rapidly killed out by the germicidal action of the glycerin. "6. The tubercle bacillus is effectually destroyed even when large quantities of virulent cultures have been purposely added to the Ijinph. "7. The possibility of inoculation of sj^hilis is eliminated, as the calf is not subject to this disease. " 8. The necessity for collecting children together, with the attendant 102 BELATIONSRIP OF COWPOX OB VACCINIA TO SMALLPOX risk of spread of infectious diseases, or of transporting a calf from place to place, is obviated, while the danger of 'late' erysipelas in the child is diminished by reason of there being no necessity to open the mature vesicles for the purpose of obtaining lymph. "9. The bacteriological purity and clinical activity of large quantities of the lymph can be readily tested prior to distribution. " 10. By reason of the possibility of keeping large stocks of glycer- inated lymph on hand for considerable periods of time v^^ithout appre- ciable deterioration, any sudden demand, such as is likely to arise on the outbreak of epidemic smallpox, can be promptly met. "11. The expense of producing glycerinated lymph is proportionately small, since the amount obtainable from each calf is enormously in- creased." Rosenau^ made a study of the bacteriological impurities of vaccine virus as it occurs in commercial preparations upon the market in the United States. The virus of ten different vaccine propagators was examined during a period of more than a year. Of 190 dry points examined, an average of 4354 bacteria per point was found. A number of the points contained over 15,000 and one as high as 44,000 organisms. Of 244 tubes of glycerinated virus examined, an average of 1742 bacteria per tube was found. A number of the capillary tubes con- tained over 10,000 bacteria, and one as high as 30,000. This evidenced lack of care in the preparation of the lymph. Pus cocci, pathogenic for laboratory animals, were found both in dry points and the glycerinated virus. Much of the virus above referred to was "green" — i. e., it had not been glycerinated for a sufficient period. During the winter of 1901-02 the glycerinated virus contained an average of 4698 bacteria per tube. In the spring of 1902 the average fell to 1058 bacteria per tube. In the winter of 1 902, 89 tubes examined gave an average of 29 bacteria per tube; the maximum was 239. Glycerinated virus when properly prepared is freer from impurities than dry points made with fresh lymph. There is practically no difference between the glycerinated virus dried upon ivory points and that hermetically sealed in capillary tubes, so far as bacteriological impurities are concerned. Tetanus spores may live a long time in vaccine virus; they remained alive and virulent on dry points after two hundred and ninety-five days, and in glycerinated virus sealed in capillary tubes three hundred and fifty days. Rosenau was unable to find tetanus germs or spores in any of the considerable number of glycerinated points and tubes examined with this object in view. He states that tetanus organisms cannot grow or produce their toxin either in glycerinated virus or on the dry points. "It would take gross carelessness to contaminate the vaccine with a sufficient number of tetanus spores to carry the disease to those vac- cinated." i Loc cit., Bulletin 12, 1903. QLYGEBINATED LYMPH 103 The writer concludes that the excessive irDpuriti(;s found in some of the glycerinated virus upon the market is largely due to the overcon- fidence in the germicidal value of glycerin. Vaccine propagators become careless, ti-usting to the glycerin to purify the product. Glycerin is too feehh; a germicide to purify vaccine matter which has a great initial contamination. The virus is also at times put upon the market with undue haste when an unusual demand exists. Howard' found actinomyces in virus from five vaccine establishments twenty-four times in a total of ninety-five cultures. Nine difi'erent species of actinomyces were found, of which six appeared to be pre- viously undescribed. The organisms are supposed to reach the virus from the air, water, soil, hay, straw, and hide. The writer thinks it is not improbable that some of the postvaccinal suppuration infections are caused by these organisms and are cases of atypical actinomycosis. Sabrazis, and Jolly and FoUi, also found actinomyces in vaccine virus. The Preparation of Glycerinated Calf Lymph (Copeman). — "The method best adapted for the production of glycerinated calf lymph which shall be free from all extraneous organisms, of perfect efficacy, and yet afford- ing material for the vaccination of many more children than the original unglycerinated calf lymph, is briefly as follows: "The Preparation of the Calf. — A female calf of suitable age, about from three to six months, should be kept under observation for a week, after which, if found to be quite healthy, it may be removed to the vaccination station. It is there placed on a tilting table, and the lower part of the abdomen, reaching as far forward as the umbilicus, is shaved and thoroughly washed with a solution of carbolic acid and then rinsed with sterile water and dried with soft, sterilized towels. " Inoculation of the Calf. — With a sterilized, sharp scalpel incisions about four inches long and half an inch apart, parallel to the long axis of the body, are made on this clean-shaven area. The depth of the incision should be such as to pass through the epidermis and to open the rete Malpighii, if possible without drawing blood. As these incisions are made, glycerinated calf lymph, which by examination has been proved to be free from extraneous organisms, is run into them by means of a sterilized blunt instrument, and the point of the scalpel is from time to time dipped into the vaccine emulsion. "Collection from the Calf. — After five days (one hundred and twenty hours) the vaccinated surface of the calf is first thoroughly washed with warm water and soap, rubbed over it by the clean hand of the operator, and finally the whole area is carefully cleansed with sterile water. The remaining moisture is then removed by sterilized sheets of blotting paper. The vaccinated incisions will now appear as lines of continuous vesicles raised above the surface, each line separated from its neigh- bor by about a quarter of an inch of clear skin. Aiiy crusts wliich appear 1 A Study of Actinomyces Cultivated from Commercial Vaccine Virus, Journal of Medical Researchj January, 1904. 104 BELATIONSHIP OF COWPOX OR VACCINIA TO SMALLPOX in the vesicular lines are picked off with a blunt, sterilized instrument. The vesicles and their contents are then removed by means of a steril- ized Volkmann spoon, and transferred to a sterilized bottle of known weight. By going over the lines only once with the spoon, it is quite easy to remove the whole of the pulp without any admixture of blood. The abraded surface is carefully washed, and may be dusted over with fine oatmeal or starch and boracic powder. Subsequently, the calf is transferred to the slaughter house and the carcass is examined by the veterinary surgeon, who forwards a certificate of its condition. Should this not be satisfactory, the vaccine pulp obtained from the animal is destroyed. Fig. 16 Belly of heifer, showing one of the approved modern methods of propagating vaccine virus ; lesions photographed at the end of five days. (Courtesy of Dr. Wm. F. Elgin.) "Preparation and Glycerination of the Lymph Pulp. — ^The bottle containing the vaccine pulp is taken to the laboratory and the exact weight of the material ascertained. A calf vaccinated in this way will yield from 18 to 24 grams, or even more, of lymph pulp. This material is then thoroughly rubbed up in a sterilized mortar or in a mechanical triturating machine. When it has been brought to a fine state of division, it is mixed with six times its weight of a sterilized solution of 50 per cent, chemically pure glycerin in distilled water. The resulting emulsion is then transferred to small test-tubes, which are then aseptically sealed and should be stored in a cool place protected from light. When required for distribution it is drawn up into sterilized capillary tubes, which are subsequently sealed in the flame of a spirit lamp. STATISTTCJAL EVIDENCE OF EFFfdAdY OF VA CO f NATION lOo 'Bacteriological Examination of the Lymph Emulsion. — As soon as the vesicular pulp is thoroughly emulsified with the glycerin solu- tion, agar-agar plates are established from it, and, after suitable incubation for seven days, the colonies that have developed on the plates are counted and examined. Week by week this process is repeated, and invariably the number of colonies diminishes with the age of the emulsion, until at the end of the fourth week after the collection and glycerination of the lymph material the agar-agar plates inoculated at that time show no development of colonies. The lymph is then subjected to further culture experiments, and if these results of freedom from extraneous organisms are confirmed the emulsion is ready for distribution. The elimination of the extraneous organisms in our experiments has occurred with marked regularity at the end of the fourth week. The only excep- tion to this rule arises when the lymph originally contained a consider- able number of spores or bacilli of the hay bacillus or bacillus mesen- tericus. These organisms are very resistant to the action of glycerin, but if the precautions detailed are carried out in the treatment of the calf their presence may generally be excluded. "Duration of Activity of Glycerinated Calf Lymph. — This varies in all probability with atmospheric conditions, with the fineness of division of the vesicle pulp, and, above all, with the condition of the calf itself. Some calves yield an excellent lymph, others a poor lymph, and the problem is to determine the value of the lymph yielded by any given calf. A lymph which was collected and glycerinated on July 13, 1897, has since been used at intervals of from twenty-four weeks to thirty-two weeks after glycerination for the vaccination of children. During this period sixty-one children have been vaccinated with this lymph in five places each, with a mean insertion success of 98 per cent. Thus, by the methods described, glycerinated calf lymph can be pre- pared which becomes freed from extraneous organisms, is available for a large number of vaccinations, at least 5000 from an average calf, and retains full activity for eight months, and will, under favorable circumstances continue to do so in all probability for still longer periods, if necessary." STATISTICAL EVIDENCE OF THE EFFICACY OF VACCINATION. Although smallpox dates back many centuries, we have no trust- worthy record of the extent of its prevalence before the fifteenth century. About this time it began to be common in Western Europe, increasing during the sixteenth and particularly the seventeenth century, and prevailing still more extensively in the eighteenth. The begimiing of the nineteenth century was characterized by a sudden and striking decrease in the morbidity and mortality of smallpox. Inasmuch as the announcement of the protective influence of vac- cination (1798) and the diffusion of this practice immediately preceded this decline, there is the strongest reason to regard Jenner's epoch- making discovery as the causative influence. 106 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX As has been previously shown, smallpox was a great scourge before the days of vaccination. But a small percentage of the population escaped its ravages. It is claimed that in the eighteenth century, accord- ing to contemporaneous writers, 95 per cent, of the inhabitants of European countries suffered at one time or other from the smallpox. In other words, but five persons out of every hundred went through life without being attacked by this dread malady. This is rendered credible when we appreciate the fact that smallpox is among the most contagious of all diseases, and that nearly every human being is highly susceptible to it. Haygarth, who lived in the eighteenth century, stated that the proportion of mankind incapable of infection by smallpox "was observed to amount to one in twenty;" this would account for the exemption of the 5 per cent, referred to. Fig. 17 annual deaths per million of population. 7000 6000 5000 - 4000 3000 2000 1000 500 BEFORE VACCINATION AFTER VACCINATION SMALLPOX WITH MEASLES SMALLPOX SMALLPOX © © © lO ^ t- © © e (M » e !^ '" 2 © © © © © ■-< e^ M •=Si IS \ cx) or> ao 1 1 - 1 \ 1 1 - - - 1 li 1 III - - - - 1 1 HI— 1 Hli r 1 ij H m ill ■IL j| iM 1 1 ■ ■ ■ I ■ ■ ■ 1 ■ m ■ 111 u. Li \m JJ 6000 5000 4000 3000 2000 1000 500 Smallpox death rates for Sweden from 1749 to 1855. (Calculated by Mr. Haile Ijom returns com- municated by the Swedish government. Published in papers communicated to the Houses of Parliament, London, 1857.) This author reports an epidemic of smallpox in Chester^in 1774, at which time, out of a population of 14,713, 1202 persons took the disease and 202 died. At the termination of the epidemic there were but 1060 persons, or 7 per cent., of the population who had never had smallpox. In an epidemic of smallpox at Warrington in 1773, in a population of 8000, 211 persons succumbed to the disease. The total deaths during the year from all causes were 473. In 1722 an epidemic raged in the small English town of Ware, which had a population of 2515. Of this number there were only 914 persons susceptible to smallpox, as 1601 had already had the disease. During the epidemic 612 persons were attacked, leaving but 302 individuals in the entire town who had never had smallpox. STATfSTKJylL EVI I) l<:Nl<' l':FFI(!y\(JY OF VA(!(JINATI()N 107 Rapid Decline in Smallpox Mortality After the Introduction of Vaccination. — iiiHsniuch as accurutc rcf-ocds of siiKillpox iMorlulity wiM'c kept ill vjxrioiis coiiiitrics, it is possible to prove by (loeiiiiientary evidence that a strikirif); fall in the niiiiihcr of deaths from this disease oceurred shortly after the introduction of vaccination. Sweden. — Vaccination was introduced into this country in Oetoher, 1801. According to the official fi<^ures of the Medical College, there were performed 2^), ()()() vaccinations hy the year ISOo, 2."<,()()() in 1S05, and about 19,000 in 1800. Vaccination was made compulsory in 1810. The average death rates per million of j)opulation for the decades from 1774 to 1821 show a decided and progressive decrease in the mortality of smallpox. (See Fig. 17.) Average Yearly Death Rates from Smai.ltox per Million of PorULATION FOR DeCADES FROM 1774 TO 1821. SWEIiEN. (Bight years), 1774 to 1781 (before vaccination) 1999 Decade, 1782 " 1791 " " 2219 " 1792 " 1801 " " 1914 " 1802 " 1811 (after vaccination) 623 1812 " 1821 " " 133 The influence of vaccination in lessening smallpox mortality in Sweden is so clearly shown in the above table as to require no fuither discussion. The contrast in smallpox mortality may be expressed in another manner. In the twenty-eight years before vaccination in Sweden, there died each year from smallpox, out of each million of population, 2050 persons; during the forty years folloiving vaccination, out of each million of population the smallpox deaths annually averaged 158. The official figures of the Medical Faculty of the University of Prague (published in papers on vaccination issued by the London Board of Health, 1857) are no less conclusive: Population, Total Deaths, and Deaths by Smallpox During Seven Years Before the General Introduction of Vaccination. Prague. Population. Deaths. Year. Total number. From smallpox. Remarks. 1796 1797 1798 1799 1800 1801 1802 3,003,482 2,991,346 3,045,926 3,041,608 3,047,740 8,036,481 3,111,472 92,242 86,855 84,743 99,079 110,730 105,576 85,460 6,6S6 1,988 3,105 17,587 17,077 3,169 4,029 (The proportion of the deaths generally \ to population = 1 : 32. /Deaths from smallpox to populations 1 = 1 : 396P:,. /Deaths from smallpox to the total t number of deaths = 1 : 12J^. Total 21.278,055 664,685 53,641 Average 3.039,722Vt 94,955 7,663 108 BELATIONSHIP OF GOWPOX OR VACCINIA TO SMALLPOX During Twenty-four Years Subsequent to Introduction op Vaccination. Prague. Population. Deaths. Year. Remarks. Total number. From smallpox. 1832 1 1833 i 3,888,828 1 139,061 121,679 807 533 1834 ■) i 122,171 285 The proportion of the total number 1835 Y 3,945,875 122,952 337 of deaths to popuJation = 1 : Z2%. 1836 j ( 124,015 291 1837 ) (■ 141,982 104 1838 Y 4,027,581 \ 108,419 62 1839 J 1 121,400 128 1840 ") 118,471 699 Deaths from smallpox to population 1841 Y 4,145,715 ) 116,575 697 = 1 : 14,7413^. 1842 ) j 124,019 339 1843 ) ( 142,876 332 1844 Y 4,285,730 J 118,184 150 1845 ) 1 178,826 62 1846 ■) j" 132,379 59 Deaths from smallpox to total number 1847 Y 4,480,661 J 134,490 9 of deaths = 1 :457^. 1848 j j 141,409 115 1849 ' 1850 131,493 383 176,211 478 1851 r 4,613,080 \ 133,245 508 1852 134,921 343 1853 1 124,617 42 1854 \ 1855 1 4,593,770 { 124,746 124,764 68 64 Total 33,985,240 3,153,905 6895 Average 4,248,155 131,412' 7/24 287 '/24 Tables Comparing Smallpox Mortality in Various Localities Before AND After the Introduction of Vaccination. Terms of years respecting which particulars are given. Before After vaccination, vaccination. 1777-1806 and 1807-1850 1777-1806 " 1807-1850 1777-1806 ' 1807-1850 1777-1806 ' 1807-1850 1777-1806 ' 1807-1850 1777-1803 ' 1807-1850 1777-1806 ' 1807-1850 1777-1806 ' 1807-1850 1777-1806 ' 1807-1850 1777-1806 ' 1807-1850 1787-1806 ' 1807-1850 1817-1850 1817-1850 1817-1850 1831-1850 1776-1780 ' 1810-1850 1780 ' 1810-1850 1780 ' 1816-1850 1776-1780 ' 1810-1850 1776-1780 ' 1816-1850 1776-1780 ' 1816-1850 1781-1805 ' 1810-1850 1776-1780 ' 1816-1850 1780 ' 1810-1850 1810-1850 1774-1801 ' ' 1810-1850 1751-1800 ' ' 1801-1850 Territory. Austria, Lower . Austria, Upper, and Salzburg Styria Illyria , Trieste Tyrol and Voralberg Bohemia Moravia Silesia (Austrian) Gallicia Bukowina . Dalmatia . Lombardy . Venice Military Frontier Prussia (East Province) Prussia (West Province) Posen . Brandenburgh . Westphaha Rhenish Provinces Berlin . Saxony (Prussian) Ponierania . Silesia (Prussian) Sweden Copenhagen Approximate average. Annual death rate by smallpox per million of living population. Before intro- duction of vaccination. 2,484 1,421 1,052 518 14,046 911 2,174 5,402 5,812 1,194 3,527 3,321 2,272 1,911 2,181 2,643 908 3,422 719 1,774 After intro- duction of vaccination. 2,050 3,128 340 501 446 244 182 170 215 255 198 676 516 86 87 70 288 556 356 743 181 114 90 176 170 130 310 158 286 STATIHTIdAf. l<:Vn)ICN(!l<: Oh' KFFKIAdY Oh' VAdCfNATfOy l()f) It will be seen from the above tables tliat whereas in the seven years preceding the introduction of vaccination smallpox in Prague caused one-twelfth of the total numher of deaths, this disease during twenty years of the vaccination period caused but -2^^-^ of the total numher of deaths. In Westphalia the annual deaths from smallpox from 177G to 1780 were 2G43 per million of population; during the tliirty-five years from 1816 to 1850 the death rate was only 114 per million. In Copenhagen, for the half-century 1751 to 1800, the smallpox death rate was 3128, whereas for the next fifty years it was only 286. In Berlin for twenty-four years preceding vaccination the death rate from smallpox was 3422, and for the first forty years of the vaccination era it was 176. By the middle of the nineteenth century the fatality of smallpox had been reduced in Copenhagen to one-eleventh of the pre vaccination death rate; in Sweden to a little over a thirteenth; in Berlin, and in a large part of Austria, a twentieth; and in Westphalia, a twenty-fifth. In the last-named place but four persons died about the middle of the century compared to 100 in the prevaccination days. Smallpox Deaths Each Year, from the " Bills of Mortality," London, 1801 to 1830. Before vaccination era. After vaccination era. Decade. Smallpox deaths. Decade. Smallpox deaths 1761-1770 . 20,434 1801- -1810 12,534 1771-1780 . 20,923 1811- -1820 7,858 1781-1790 . 17,867 1821- -1830 6,990 1791-1800 . 18,477 1801-1810 1811-1820 1821 -1830 1831- -1837 1801 . . 1,461 1811. . . 751 1821. . . 508 1831. . 563 1802. . 1,597 1812 . . . 1287 1822 . . . 604 1832. . 771 1803 . . 1,202 1813 ... 898 1823. . . 774 1833. . 574 1804. . . 622 1814 . , . 638 1824. . . 725 1834. . 334 1805. . . 1,685 1815. . . 725 1825. . . 1299 1835 . . 863 1806 . . . 1,158 1816 ... 653 1826. . . 503 1836. . 536 1807 . . . 1,279 1817 . . . 1051 1827. . . 616 1837. . 217 1808 . . 1,169 1818. . . 421 1828. . . 598 1809 . . . 1,163 1819. . . 712 1829. . . 736 1810. . . 1,198 1820 ... 722 1830. . . 627 Smallpox, 12,534 78D6 6990 3858 The above figures show a decided contrast in smallpox mortality between the decades immediately preceding and following the intro- duction of vaccination. In the twenty-seven years elapsing from 1811 to 1837 the smallpox deaths exceeded 1000 but three times. Berlin. — Below are compared the deaths from smallpox per 100,000 inhabitants \\\ the prevaccination and postvaccination periods: 1758-1762 . . 407 persons. 1790-1794 . 310 persons 1763-1767 . 364 " 1795-1799 . 239 1768-1772 . 294 " 1S00-1S04 . 261 1773-1784 . ? " 1805-1809 . 308 1785-1789 . 360 " 110 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX (In the first decade of the nineteenth century vaccination was not actively practised in BerHn; it became generally employed in the year 1810.) 1810-1814 ^ . 31 persons. 1840-1844 13 person 1815-1819 . 40 1845-1849 2 1820-1824 4 1850-1854 5 1825-1829 . 13 1855-1859 . 18 1830-1834 . 19 1860-1864 . 30 1835-1839 . 18 1865-1869 . 26 In the quinquennium 1870-1874 occurred the great pandemic of smallpox which swept the entire civilized world. There died in Berlin during this period, per 100,000 population, a yearly average of 160; this number considerably exceeds all the previous years of this period, but still falls far below the average of the prevaccination years. From 1795 to 1799, before the days of vaccination, smallpox caused 6.5 per cent, of all deaths in Berlin. In the five years following the introduction of vaccination the figures were: 7.5 per cent., 6.4 per cent., 0.7 per cent., 1.3 per cent., and 0.2 per cent.^ Copenhagen. — Between 1794-1798 (prevaccination period) smallpox caused on an average 373 deaths each year. 1799 (before vaccination) . . 54 1800 . 35 1801 . 486 1802 . 73 1803 (after vaccination) . . 5 1804 . 13 805 (after vaccination) 806 809 810 From 1811 to 1823 not a death occurred from smallpox. (A period of thirteen years. )^ It is thus seen from the statistics above quoted that after the discovery of vaccination the deaths from smallpox markedly decreased in every country in which this practice was introduced. 1 Denkschrift, li. k. Gesundheitsamt, Berlin. - Beitrage aus der Gesundheitsamte. Quoted by Edvvardes, Smallpox and Vaccination in Europe, London, 1902. STATISTICAL KV I I)I<:Nriod of thirty-one years. During this time the total deaths were .'iSfJO, and the deaths from smallj)ox 022. 'I'here were nine epidemics of smallpox reenrrini;e of nine person.s was not known. In ChcMcr, in the epidemic of 1774, all of the smallpox deaths, nuiidxT- inn^ 202, occurred in children under ten years of age, and onc-(|ii;irter of them under one year. In Kilmarnock, of 622 deaths from smallpox l)etween 172S and 1763, only seven were of those above ten years. In 1773, Warrington^ sustained an epidemic of smallpox which resulted in 211 deaths (population SOOO). In 1S03 another epiflemic occurred which resulted in 62 deaths (population 54,084, of whom 53,645 were vaccinated). The ages of the patients fatally attacked are tabulated as follows: Smallpox Deaths. Age. Under 1 year 1 to 2 years 2 " 3 3 " 4 4 " 5 5 " 6 6 " 7 7 " 8 8 " 9 9 " 15 15 " 20 20 " 30 30 " 60 Over 60 773. Vaccinated. Not vaccinated. 49 8 (under 1 month) 84 1 33 18 1 15 1 4 2 2 4 1 1 1 1 1 2 10 4 24 5 1 211 24 In 1773 all of the deaths were under ten years, and nine-tenths were under five years of age. In 1893 among the vaccinated not a death occurred under eight years of age; indeed, not one vaccinated child under eight years of age contracted smallpox. The statement may be considered as proven that vaccination has changed the age incidence of smallpox. It is a rarity for a successfully vaccinated child under five years of age to die of smallpox. It is even uncommon for a successfully vaccinated child under ten years to succumb to the disease, as will be seen from the following table compiled by the British Royal Vaccination Commission: Quoted by Edwardes, loc. cit. S 114 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX Smallpox in Children of the Age of 1 to 10 Years. Vaccinated. Not vaccinated. Attacks 570 Attacks 1235 Deathsi 16 Deaths 375 Fatality . . . .2.8 per ct. Fatality .... 30.3 per ct. The saving of infant life by vaccination should have reduced the general infant mortality in the postvaccination period; the following table shows that such a reduction in infant mortality did take place. It will be seen that the diminution in the general death rate of children under ten, and more particularly under five years of age, is far more pronounced than during adult life. Annual Mortality to 1000 Persons Living. Sweden, Before vaccination. After vaccination. Ages. 21 years 20 years 20 years 10 years (1755-1775). (1776-1795). (1821-1840). (1841-1850). Under 5 years ...... 90.1 85.0 64.3 56.9 5 to 10 " 14.2 13.6 7.6 7.8 10 " 15 " 6.6 6.2 4.7 4.4 15 " 20 " 7.6 7.0 4.9 4.8 20 " 30 " 9.2 8.9 7.8 6.8 30 " 40 " 12.2 11.6 11.8 9.8 40 " 50 " 17.4 16.1 16.7 14.5 iSO " 60 " 26.4 23.9 26.0 23.6 60 " 70 " 48.1 49.3 49.4 46.3 70 " 80 " 102.3 104.1 112.9 102.8 80 " 90 " 207.8 197.4 243.7 228.5 90 " and upward 394.1 351.3 396.4 375.8 All age s 28.9 26.8 23.3 20.5 The opponents of vaccination urge that the decline of mortality from smallpox at the beginning of the nineteenth century was not due to vaccination, but to the discontinuance of inoculation. It is probable that inoculation did tend to increase the prevalence of smallpox, but there is no evidence to prove that it increased the mortality. As the Royal Commission remarks: "It must be borne in mind that inoculated smallpox was on the whole much less fatal than that naturally acquired. The class of inoculated persons may thus have contributed less to the fatal cases of smallpox than if they had been left to the chances of natural contagion." While inoculation was introduced into England in 1721, it found but Httle favor until 1740. The Suttons popularized the practice in 1763, and between 1770 and 1780 it was widely employed. Inoculation was therefore only practised on a large scale in England in the second half of the eighteenth century, and particularly in the last twenty-five years of this period. The antivaccinationists claim that the increase of small- pox mortality in the eighteenth century over the seventeenth was due to the practice of inoculation. If this were true, the mortality should have shown its increase particularly during the second half of the I Six of tiiese deaths occurred in children in whom the success of the vaccination was doubtful. STATISTIC A Ij KV f DICNd K Oh' KI^'lCAdY Oh' VAddlNATIOS 1|5 century. But the mortality wus as n;rca(, fil" woi ^n-c;i(d (,li;it inocnhition did not cntir-cly cease in England upon the introduction of vaccination, but continued to be practised for a number of years, until it was declared illegal by act of Parliament in 1(S40. It is evident from these considerations that the disc/'JN(,'JX 12'A Carinthia, 1834-1835 . 1,626 14^ Yt. Adriatic, 1835 1,002 15'/5 H Lower Austria, 1835 2,287 25ry. This was passed A|)ril S, IS74, and went into cH'cct on April I, JSyr;. Its essential provisions an; as follows: Every eliild nnist be vaeeinated before the expiration of the first year of its life, unless it has had small- pox or unless some physical disability exists; in the latter event the va(;einati()n is undertaken within one year of the removal of the existing disability. Every ])U])il of a ])iiblie or private educational institution must be vaccinated between the age of thirteen and fourteen years, unless there is medical proof that he has had an attack of smallpox within five years or has been successfully vaccinated within that time. Parents, caretakers, guardians, or heads of schools who fail to comply with the law are subject to fine or imprisonment. Vaccination must be performed only by physicians, and anyone vaccinating illegally is punished by a fine not exceeding 150 marks or imprisonment not exceeding fourteen days. Fig. 18 PRUSSIA, 1847-1897. ^ SMALL-POX DEATHS PER MILLION OF POPULATION. AUSTRIA, 1847-1.897. SMALL-POX DEATHS PER MILLION OF POPULATION. Tables showing the decline of smallpox in Germany after the enaction of compulsory vaccination in 1874; smallpox mortality is compared with that of Austria. The Results of the German Compulsory Vaccination Law. — If there was in existence no other statistical evidence of the efficacy of vacci- nation and revaccination, the history of smallpox in Germany since 1875 would be all sufficient testimony. From 1816 to 1870 the annual mortality from smallpox in Prussia varied from 7.32 to 62.0 per 100,000 of population. This death rate was small compared with the prevaccination periods. During the disastrous pandemic of 1871-72 the rate was 243.2 and 262.67, respectively. After the law of 1875 went into effect the annual 124 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX mortality in Prussia fell so that between 1875 and 1886 the average yearly mortahty per 100,000 of population was 1.91, the maximum reaching 3.6 (in 1877). On the other hand, in Austria, where the lax vaccination and revacci- nation requirements remained unchanged, the mortality rate from small- pox during about the same period (1875 to 1884) increased, varying between 39.28 (1876) and 94.79 in 1882. (See Fig. 18.) The results of the German vaccination law in the principal states of the Empire are given in the following table: The Results of the Geemak VAcciNATioisr Law, 1874. (Smallpox deaths per million living. ) Year. Prussia. Bavaria. Wtirtemberg. German Empire. Contrast Austria. 1866 620 120 133 ...1 368 1867 432 250 63 484 1868 188 190 19 370 1869 194 101 74 374 1870 175 75 293 293 1871 2432 1045 1130 383 1872 2624 611 637 1866 1873 356 176 30 3094 1874 95 47 3 1725 2. Since 1874. 1875 36 17 3 576 1876 31 13 1 406 1877 3.4 17 2 555 1878 7.1 13 631 1879 12.6 5 534 1880 26 12 5.6 674 1881 36.2 15 3.6 807 1882 36.4 12 6.6 947 1883 19.6 6 35.2 596 1884 14.4 1 11.6 530 1885 14 3 600 1886 4.9 1 1 4.2 400 1887 5 1.8 3.5 417 1888 2.9 3.8 0.5 2.3 615 1889 5.4 5.2 4.1 537 1890 1.2 1.5 1.2 249 1891 1.2 1.2 1.0 287 1892 3 0.5 2.1 256 1893 4.4 0.7 1 3.1 244 1894 2.5 0.3 1.7 105 1895 0.8 0.2 0.5 49 1896 0.2 0.2 0.2 36 1897 0.2 0.1 61 1898 0.4 0.3 0.3 1899 0.5 The remarkable results of compulsory vaccination and revaccination in Germany are perhaps the more striking when the mortality rate of smallpox in Gerrnan cities is compared with cities of other countries. After compulsory revaccination in 1875 the average annual death rate from variola from 1875 to 1886 in the followins" cities was as follows: 1 No statistics. VA C(,'JNA TION STA TISTICS 125 Death Ratk i^'kom SMAiii.i'ox i-ioii 100,000 ov I'oimjla'iion. Uennai) (.'ities. Oilier CilioK. Berlin .... I.IO iicrsons. Pariw .... 2C>.'i\ \>trtv>iin. Hamburg . . . 0.74 " .St. I'cterwburfj . . 3.'). 82 " Breslau .... 1.11 " Vioiina .... M.'M " Dresden .... 1.03 " fragile .... 147.90 " There is hut one e.xphuiation for the inarvcloiisly low dc'itli nitf iti the German cities as compared with other coiiliiiciilnl (•(■ii(i«v^; ilmt explanation is carrjvl and universal vaccination and rcracriiKilion. A comparison of total .smallpox aUaclcs in the (jcrman, Frciicli, aiul Austrian armies aft(M- 1X75 is e((ua,lly instructive: German army (1875-1887) 148 men. French army (1875-1881) 5,605 " Austrian army (1875-1886) 10,238 " In the German army, despite greater numbers and a longer period of time, the smallpox attacks were enormously less than in the French and Austrian armies. Since the law of 1875 went into effect in Germany, there have been no epidemics of smallpox in that country. The smallpox is frequently introduced by foreigners, particularly on the frontiers, but the disea.se can find no foothold. In 1899 there occurred in the German Empire, among 54,000,000 people, 28 deaths from smallpox; these occurred in twenty-one different districts, the largest number in any one district being 3. Not a case occurred in a large town. Kiibler^ in speaking of the importation of smallpox into Germany, says: "Among the fatal cases there were many who had come from foreign countries; in the interior of the Empire aliens, chiefly Russian- Polish laborers, constituted a large percentage of those who contracted the disease. The annual recurrence of the pestilence among these people has recently necessitated a regulation that workmen before being admitted to employment within the realms must produce proof of successful vaccination or recovery from an attack of smallpox, and in case they were unable to do so they must submit to vaccination." The following figures indicate the prevalence of smallpox on the German frontier as compared with the interior. The mortality from smallpox in Germany from 1886 to 1889 was: At the Frontier. In the Interior. 1886 UO cases. 45 cases. 1887 119 " 49 '• 1888 94 " 16 " 1889 188 " 12 " In 1897 there were but five deaths from smallpox in the entire German Empire (54,000,000 population). Furthermore, for a period of th irtcen years in a population comprising two-fifths of the total inhabitants of Germany, there were only five instances of death from smallpox in successfully rcvaccinated persons. 1 Geschichte der Impfung und Blattern, 1901. 126 RELATIONSHIP OF COWPOX OR VACCINIA TO SMALLPOX Germany has taught the world how to utihze Jenner's great discovery SO as to exterminate smallpox. The German Vaccination Commission of 1884, referring to the influ- ence of the compulsory vaccination law, says: "Previously to 1871 smallpox mortality in Austria behaved much like that of Prussia, though higher on the whole. The great epidemic of 1872-74 was more fatal and lasted longer than in Prussia. During the next two years the mortality fell, as usual after epidemics. Here the influence of the epidemic in lowering the mortality ceases, and the latter rises at once to its old figures, viz., as before the epidemic, and even higher, and this rise was not merely temporary. "The remarkable and persistent decline in Prussia since 1875 can only be due to the vaccination law of 1874, because all other conditions remain the same in the two countries. The only difference is that in Prussia the revaccination of all school-children at the age of twelve years was made compulsory in 1874." The Board of Health of Berlin has prepared tables comparing the number of deaths occurring between the years 1886 and 1889 in countries having compulsory vaccination, and those without such provision: Population. 1886. Smallpoj 1887. c deaths. 1888. 1889. Average of deaths. Average per million of popu- lation. >. . f Sweden, 4,746,465 . ^f Ireland, 4,808,728 . B<'3 -1 Scotland, 4,013,029 . a§ Germany, 47,923,735 . 5 ** l England, 28,247,151 . Switzerland, 2,922,430 . Belgium, 5,940,365 . Russia, 92,822,470 . Austria, 23,000,000 . Italy, 29,717,982 . Spain, 11,864,000 . 1 2 24 197 275 182 1,213 16,938 8,794 1 5 14 17 168 505 14 610 25,884 9,591 16,249 1 9 3 112 1,026 17 865 1 2 6 200 28 3 1,212 1 4 5 12 169 458 54 975 21,411 11,220 15,925 11,425 1 1 1 1 3 1- 3.5 1 16 J 18.5 164 231 14,138 18,110 14,378 12,358 13,416 8,472 510 536 1 963 But a glance is necessary to show the striking difference between the number of deaths in those countries having compulsory vaccination and those in which there is no such measure. The average deaths per million in the compulsory vaccination countries is eighty tiTues less than in the others. Furthermore, England is the least vaccinated of the compulsory countries and her death rate is the highest among these. The Imperial Board of Health of the German Empire gives the frequency of smallpox in various European countries between 1893 and 1897 inclusive, a period of five years.^ 1 No statistics. " Quoted by Kiibler, loc. cit. VA (J(UNA TION ST A 'I'lS'l'IdS Vll TlfE FllEQUfiNCY 01'' SmALM'OX FN EUROt'KAN SlATKH HIO'IWKKN IHD.'i-lSO? rNCI.UHfVK (5 YKARS). Average yearly Actual Country. I'opulation. 52,042,282 mortality in every million fjopulatlon. 1.1 number Hmallpux deatOH. YearH. Germanv 287 5 Denmark 79»,3:)6 0.5 2 6 Sweden 4,894,790 2.1 41 4 Norway 2,045,900 0.6 5 4 England and Wales 30,389,524 20.2 8,066 5 Scotland 4,155,880 12.3 256 5 Ireland 4,580,5.55 9.9 226 5 Switzerland 3,032,901 5.1 78 5 Netherlands 4,707,249 38.7 929 5 Belgium 6,419,498 99.9 3,208 5 French States 8,253,079 90.2 3,721 5 Russian Empire including Asiatic Russia 118,950,400 463. 2 275,502 5 Austria 23,000,000 99.1 11,799 5 Italy 31,007,422 72.7 11,278 5 Spain 10,596,649 563. 4 23,881 4 Hungary 18,234,916 134. 3 12,241 5 Here, again, the countries which during this period have the most stringent vaccination laws suffer the least smallpox, namely, Germany, Denmark, Sweden and Norway. In well-vaccinated Germany, but one person a year in every million died of smallpox. In England and Wales, where vaccination is generally but not univer- sally practised, 20 persons per million died each year. In Austria, where the vaccination laws are poorly enforced, 99 persons per million died each year. It is, indeed, quite possible to know to what extent vaccination is practised in the various countries by noting the mortality from small- pox. There is an inverse proportion between these factors. It is evident, therefore, that in Spain and in Russia (including Asiatic Russia) vacci- nation must be greatly neglected. The tables teach another lesson, namely, that without vaccination smallpox is still to be regarded as a dread scourge, as a great destroyer of human life. For in the five years from 1893 to 1897, in the sixteen countries mentioned, 346,520 lives were sacrificed to smallpox; of this number Russia lost 275,502. These figures are the more terrible when it is recognized that these lives might have been saved by the application of a prophylactic measure within the reach of all. Immunity of Physicians and Nurses in Smallpox Hospitals. — If it can be demonstrated that physicians and nurses in smallpox hospitals are protected by vaccination, this must be regarded as a crucial test. For if these persons, living in the same atmosphere with scores or hundreds of smallpox patients, breathing in their very exhalations, are enabled to escape the infection, it certainly should be possible for others much less exposed to acquire similar immunity. Experience shows that physicians, nurses and others, if recently success- fully vaccinated, may live in smallpox hospitals with perfect safety. The 128 RELATIONSHIP OF COWPOX OR VACCINIA TO SMALLPOX immunity of employes (when properly revaccinated) is a uniform experience in practically all smallpox hospitals. In the hospitals of London, from 1876-79, there were admitted 11,412 smallpox patients who had been vaccinated in infancy, but not a single case was known to have occurred in a person who had been successfully revaccinated. It was the rule to revaccinate all nurses and employes before entering the hospital, and the number thus employed amounted to about 1000; of these only some half-dozen took smallpox, and they, for some cause or other, had escaped revaccination. Dr. Marson,^ physician to the Smallpox Hospital of London for many years, giving evidence in 1871, stated that during the preceding thirty-five years no nurse or servant at the hospital had been attacked with smallpox. Since that period one case only has occurred, and that in an unrevacci- nated gardener. Thus, during a period of sixty years but one case of smallpox has occurred among hundreds of persons who were in the closest contact with the disease. Dr. Marson took the precaution of revaccinating all persons before permitting them to go on duty. Dr. Collie,^ whose experience is also large, says: "During the epidemic of 1871, out of 110 smallpox attendants at Homerton, all but 2 were revaccinated, and these 2 took smallpox." At a meeting of the German Vaccination Commission (1884) Dr. Eulenburg related "that a manufacturer in Posen had all his workmen vaccinated except one, who refused. This man alone of the 150 took smallpox shortly afterward and died." In 1885 a committee of the Epidemiological Society of London reported that out of 1500 attendants in smallpox hospitals, 43 took smallpox and not 1 of the Jj.3 had been revaccinated.^ "The experience of the epidemic of 1876-77 was of the same kind, all revaccinated attendants having escaped, while the only one who had not been vaccinated took the disease and died of it."* In the epidemic of 1881 in London, of 90 nurses and other attend- ants of the Atlas Smallpox Hospital Ship, the only person who con- tracted smallpox was a housemaid who had not been revaccinated.^ Dr. T. F. Ricketts,*' the medical superintendent of the Smallpox Hospital Ships on the Thames, shows that out of 1201 persons in attend- ance on board the smallpox ships since 1884, only 6 contracted the disease, and all recovered. None of these persons had been successfully revaccinated before going on duty. At the Southampton Fever Hospital all persons employed during the smallpox epidemic of 1893 were revaccinated before going on duty, and, although freely exposed to the disease, not a single individual con- tracted smallpox.^ According to Dr. Hill, of Birmingham, during the epidemic in 1893 over 100 persons were employed at the City Smallpox Hospital, all of 1 E. J. Edwardes, The Practitioner, May, 1896. 2 Ibid., loc. cit. 3 Transactions of the Epidemiological Society, vol. v., new series. * Dr. Collie, Quain's Dictionary of Medicine. 6 Mentioned by Ernest Hart. Allbutt's System of Medicine. 6 Report of the Metropolitan Asylums Board for 1892. ' Hart, loc. cit. IMMUNITY OF Vy\(!(; I NAT HI) l>ll YSKHA NS A N I) Nl'llSHS ];>] jiot rcspoiidiiifi; to vacciiiiitioii after two or three earefiil trials. Of the entii'e niirnher of students one contra(;te(I srnalljjox, anrl it was suhse- qiiently foniul that he had never })cen suecessfiilly vaccinated. Since the present ej)idemi(; he^an, al)Out 200 })ersons, inchjdin^ })hysieians, run-ses, ward niaids, cooks, hiundresses, and the like, liave been employed in the smallpox department, and not one has contracted the disease. These facts are not wondered at by those who are familiar witli smallpox; they are anticipated. P^vidence of this same nature has accumulated for nearly a half-century. P>very ej)idemic adds fresh data. The innn unity of revaccinated nurses and physicians against smallpox constitutes testimony in favor of the efficacy of vaccination which is irrefutable. Further Direct Evidence of the Efficacy of Vaccination.. Much convincing evidence of the protection afforded by vaccinati(jn against smallpox never appears in morbidity or mortality statistics. Every physician who is familiar with smallpox can cite numerous instances of such protection. Jenner and other early vaccinators established direct proof of the virtue of vaccination by showing that smallpox could not be given to an individual recently successfully vaccinated. Dr. Jenner in 1801 wrote: "Upward of 6000 persons have now been inoculated with the virus of cowpox, and the far greater part of them have since been inoculated with that of smallpox, and exposed to its infection in every rational way that could be devised, without effect." And Dr. Woodville, in 1802, stated that within two years there were vaccinated at the Smallpox Hospital 7500 persons, of whom about one- half were subsequently inoculated with smallpox matter, and in none of them did smallpox produce any effect. Smallpox is one of the most highly contagious of all diseases, and nearly every human being is susceptible to it; we could cite scores of instances of protection granted to persons by vaccination after admission to the Municipal Hospital. A few examples which occurred during the recent epidemic (1901-04) and of wdiich we have notes will suffice. A child of one year, who had been successfully vaccinated about ten days before admission, was sent to the hospital with roseola vaccinosa which had been diagnosed as variola. The child remained in the smallpox wards about three wrecks and continued perfectly well. Another child, of nine years, with exactly the same history, returned home perfectly well after a constant exposure of over three weeks. An un- vaccinated colored child, about tw^o years old, was brought into the hospital with a sister who was suffering from smallpox. Immediately after admission vaccination was performed, and although the child was constantly exposed to the infection for three weeks he did not take the disease. Several other children and also some adults, who were sent to the hospital under erroneous diagnosis, were vaccinated for the first time after admission and were rendered absolutely immime. In every epidemic of smallpox that has occurred in Philadelphia within the past thirty years, instances have been observed of whole 132 BELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX families being removed to the hospital because of an outbreak of the disease in these famihes. In such instances the unvaccinated children have suffered and often perished, while those who were vaccinated remained perfectly exempt, although living, eating, and sleeping in the infected atmosphere for several weeks. But we have yet to see unvac- cinated children escape the disease under similar conditions of exposwe. Furthermore, we have more than once seen a vaccinated infant take its daily supply of nourishment from the breast of its mother who was suffering from varioloid, and the infant continue as free from smallpox as if the disease were one hundred miles away and the food derived from the most wholesome source. This is evidence of the prophylactic power of vaccination that does not appear in mortality reports nor in statistical records. Ravages of Smallpox in Countries where Vaccination is Neglected. — In most of the European countries and in the United States smallpox at the present day is a comparatively rare disease, appearing, as it does, in epidemics at infrequent intervals. Many physicians who have been in practice for fifteen or more years have never encountered even a single case of this disease. In well-vaccinated countries the epidemics are small and of short duration. In countries, however, in which vaccination is neglected, the epidemics may attain in extent and mor- tality the terrible numbers that were reached in the days before vacci- nation. In the Russian Empire, including Asiatic Russia, there were 275,502 deaths from smallpox in the five years from 1893 to 1898. In Spain, with a population of only.ten and a half million people, there were 23,881 deaths from smallpox during this period. Hungary had 12,241 deaths, and Italy and Austria each over 11,000 deaths. In Germany, where there is compulsory vaccination and revaccination the smallpox deaths during the same five years numbered only 287. Dr. Jeanselme^ is authority for the statement that smallpox is still a murderous disease in Indo-China and other parts of the East. He estimates that a quarter of the infantile population succumbs to this disease. During times of epidemic recrudescence the death rate is higher still. In 1900 Dr. Jeanselme saw the population of the village of Loos almost completely swept away by smallpox, a few old people, protected by a previous attack, being the only survivors. Children under the age of five years furnish the greatest number of victims. The Annamites and Cambodgians regard variola as a necessary evil, and children who have not gone through it practically do not count as members of the family. Vaccination is greatly neglected, but inocula- tion is practised. The blind in Indo-China are numerous, the loss of vision in large part being due to smallpox.^ The above conditions might readily prevail in all countries if the opponents of vaccination were successful with their propaganda. 1 Quoted in the British Medical Journal, August 16, 1902. 2 it,id. UNANIMITY OF OI'INION AS TO VAI.UK OF VAfKJ/NATfON ];>/.>, UNANIMITY OF OPINION AS TO THE VALUE OF VACCINATION. There lius j)rol)ul)ly never heeii in tlie history oF iiiiiiikiiid a ^reat discovery the acceptance of which some men (\'u\ not (Hspute. The fijreat truth which -lenner j^ave to the world offers no cxcei^tion to this general statenuMit. There urc (hssenters wlio do not hcheve in vacci- nation, but tliey are chiefly to he found outside of the inctheal |)rofession. We know of no eminent physician wito is not conoinced of the efficacy of vaccination; those physicians who have had a large practical experience with smallpox are the most ardent advocates of vaccination, for they have had the best op])()rtunity of notiuji; the behavior (;f vaccinated individuals in the presence of smallpox. The few physicians who are found in the ranks of the antivaccinationists are usually men without practical experience in smallpox; they argue with statistics (often wit- tingly or unwittingly distorted) and not with facts derived from j)er- sonal observation. As a prophylactic remedy against smallpox vaccination was generally accepted by the medical profession at an early date. In 1856 the Medical Officer of the London Board of Health, John Simon, sent circular letters to 542 prominent members of the medical profession in the United Kingdom and in some of the other European countries, requesting their opinions as to the value of vaccination. Five hundred and thirty-nine replies were received and there w^as absolute unanimity as to the efficacy of vaccination as a protective measure against smallpox. The most distinguished medical bodies in every country have time and time again affirmed their confidence in the protective influence of vaccination, and the most enlightened nations of the earth have officially recognized its value and have encouraged its practice. Thomas Jeflferson's appreciation of the value of Jenner's discovery may be judged from the following letter addressed to the discoverer of vaccination: MoNTiCELLO, Virginia, May 14, 1806. Sir : I have received a copy of the evidence at large, respecting the discovery of the vaccine inoculation, which you have been pleased to send me, and for which I return you many thanks. Having been among the early converts of this part of the globe to Its efficacy I took an early part in recommending it to my countrymen, I avail myself of this occasion to render you my portion of the tribute and gratitude due to you from the whole human family. Medicine has never before produced any single improvement of such utility. Harvey's discovery of the circulation of the blood was a beautiful addition to our knowledge of the ancient economy ; but on a review of the practice of medicine before and since that epoch, I do not see any great amelioration which has been derived from that discovery. You have erased from the calendar of human afflictions one of its greatest. Yours is the comfortable reflection that mankind can never forget that you have lived ; future nations will know by history onli/ that the loathsome smallpox has existed, and by you has been extirpated. Accept the most fervent wishes for your health and happiness, and assurance of the greatest respect and consideration. Th. Jkfpkeson. Thomas Jefferson's prophecy that "future nations will know by history only that the loathsome smallpox has existed" fails of fulfilment only because vaccination and revaccination are not universally adopted. 134 RELATIONSHIP OF COWPOX OB VACCINIA TO SMALLPOX OPPOSITION TO VACCINATION. It is a remarkable fact that, despite one hundred years of incontrovert- ible testimony of the value of vaccination, there should still exist at the present day an organized antivaccination movement. To be sure the active opponents of vaccination comprise but a very small percentage of the people, but their influence is none the less noxious. Curiously enough the opposition to vaccination is most acute in the very country whence this great discovery sprang; this fact is a sad commentary upon the common sense of this portion of the English population. The opponents of vaccination include a number of persons of prominence in the literary world ; indeed, a large library of antivaccination literature has gradually arisen. No great truth is ever promulgated that does not meet with opposition ; the truth of the value of vaccination has satisfied the pidgment of Tnedical- men, but a certain number of individuals outside of the profession dissent therefrom. These persons have, in various countries, banded together to antagonize the practice of vaccination and to oppose its compulsory enforcement. We prefer to look upon these persons as misguided rather than regard them in a less charitable light. The evidence in favor of vaccination is so strong and irrefutable that an unbiased student of the subject can arrive at but one conclusion. There is no truth more clearly established than that vaccination and revaccination properly performed protect against smallpox. And yet some antivaccinationists persist in mis- interpreting facts and figures with a view of discrediting vaccination; this is often so patent as to clearly establish the effort as wilful perversion. Antivaccination propaganda have caused many innocent victims to he consigned by smallpox to a premature grave. There is but one rational argument for opposition to vaccination, namely, that the practice of this measure is not entirely devoid of some danger. But the danger is so slight in any individual instance that it is almost a negligible quantity. No human act is completely unattended with risk. When the rare instances of death following vaccination are compared with the frightful slaughter of thousands by smallpox before the days of vaccination, and even at the present day in countries where vaccination is neglected, the benefits of Jenner's God-given discovery may be appreciated. CHAPTER I II. THE VARIOLOUS DISEASES OF LOWER ANIMALS. A NUMBER of domesticated animals ap[)ear to l)c siiscc|)til)I<' to pock diseases which are more or less closely allied to human smallpox. Those affections are, by reason of difference in behavior, divisible into two natural grou})S. The diseases comprised in the first <(roup are communi- cable throufi;li the atmosphere; they are accompanied by a generalized eruption, and may be regarded as death-dealing pestilences; in this class are to be included human variola and sheeppox. In the second group the diseases are only capable of transmission by inoculation (accidental or intentional); the eruption is usually limited to the sites of inoculation, and death rarely takes place. In the second group belong cowpox, horsepox, apepox, and other domestic animal pock diseases presently to be described. Jenner was firmly of the belief that many of the common farm animals were subject to eruptive diseases allied to variola. He says:^ "Our domestic animals are subject to a variety of eruptive diseases — the horse, the cow, the sheep, the hog, the dog, and many others. Even poultry come in for their share. Again, there certainly must be a reason why the term chicken is annexed to a species of pock which infests the human skin. In the province of Bengal the poultry are subject to eruptions like the smallpox, which becomes epidemic and kills them by the hundreds." Dr. Baron^ says: "It seems certain that there are, at least, four animals— namely, the horse, the cow, the sheep and the goat — which are aft'ected with a disorder communicable to man, and capable of securing him from what appears to be a malignant form of the same disease. It is, moreover, proved that other animals may take the vaccine disease by inoculation, and that matter taken from pustules so produced affords the genuine cowpox in man. The animals on which these experiments have been tried are the dog, the goat, the she-ass, and the sheep. The fact as regards the dog was ascertained by Dr. Jenner." Indeed, Jenner alleges to have found dogs very susceptible of the variolse vaccinae; he believed that an attack of this disease rendered the dog immune against the distemper. Smallpox of Sheep. — Sheeppox, variola ovina, or clavelee, is an acute contagious and epizootic disease characterized by SNanptoms closely simulating the manifestations of variola in the human subject. Variola ovina is supposed to have arisen in Asia, and, like smallpox, to have extended thence to the continent of Europe. Various countries 1 Manuscript of Jenner, quoted by Baron. - Life of Jenner, p. 243. 136 THE VARIOLOUS DISEASES OF LOWER ANIMALS have, from time to time, experienced devastating epidemics which have greatly interfered with the sheep-growing industry. The period of incubation of the disease is somewhat variable, but is ordinarily between nine and twelve days. It is stated that sheep may now and then- remain unaffected for a period of one or even two months, although intimately exposed to the contagion of the disease. Some Continental observers state that the eruption is preceded by two or three days of fever, but Simonds and other English writers affirm that in their experience they have never noted any illness prior to the appear- ance of the eruption. At this time the infected sheep separates himself from his fellows, looks weak and dejected, lies down and refuses food, although he will drink water freely. The breathing is quick and short and the heart beats accelerated. The conjunctivae are reddened, the lids swollen, and the tears trickle down the face. A mucous discharge issues from the nose and tends to block the nostrils. These symptoms begin synchro- nously with the eruption and continue until vesiculation begins, when there is commonly an abatement of these manifestations. The eruption appears as florid-red papules, which are firm and unyielding to the touch. These are usually observed first on the inner side of the extremities, and on the cheeks and lips, where the skin is hairy, but not covered with wool. Nude portions of the body, such as the prepuce, labia, anus, and inferior surface of the tail may be simul- taneously attacked. The eruption rapidly spreads over the entire integument, manifesting itself either in a discrete or confluent form. In certain species the face is profusely involved, in which case the disease proves extremely fatal. The duration of the papular stage may vary between two and six days, averaging three in the majority of cases; this stage is somewhat protracted in confluent cases. The reddish papules become gradually converted into whitish vesicles containing a limpid fluid. Many of the vesicles are small, and nearly all are unilocular, contrasting in this respect with the multilocular character of the vesicles in human variola. The transformation of the papules into vesicles is not uniform, some undergoing this change a day or two after others, while some papules may disappear without vesiculating at all. The vesicles are not sur- rounded by an areola at an early stage, but only after they have fully matured. In the perfectly formed vesicle of sheeppox a central depres- sion may be seen, but this is far from being constant. The duration of the vesicular stage is variable. In the milder cases the eruption may not progress beyond the stage of vesiculation, and pustules may therefore be absent. In severe and protracted cases, however, a purulent fluid is secreted and the vesicles are converted into pustules. Deep ulcerations may develop when a large quantity of pus is produced; in confluent cases the inflammation may be so severe as to lead to patches of gangrene, particularly upon the abdomen and legs. The stage of vesiculation or pustulation is followed by crusting of THE VA R fO /. US T) THE A SES O F L W EAi A NIMA LS ] .'J7 the lesions, constituting tlic process of dcsiccidion. 'I'lic scabs arc of a l)roiwnisli-ycIlow or l)lackisli color, and vary considerably in voluin(;. When tluvse fall olf jyil.s nvv seen in the skin, which v;iry in dej>tli accord- ing to the severity of the disease. Two to four weeks may elafxse before the complete iiealing of the sores. At the sites of the lesions {permanent defects remain in the wool of the animal. In confiuent cases the fever remains high, there is rapid respiration, moaning, frothy discharge from the n)outh, and at times destructive lesions of the eyelids and eyeball; a severe diarrhrx-a may hasten the fatal termination. Jn such cases the slightest ap{)lication of force may cause the wool to separate from the skin. Captain J. Carr (quoted l)y Simonds) thus describes this malignant form: "The pulse becomes increasingly rapid, the mouth dry and hot, the breath fetid, and the eyelids and even head so much swollen that the creature can scarcely be recognized. The pustules mav produce malignant ulcers and render the poor animal lame or blind." Sacco states that "impregnated ewes are certain to al)ort their lamljs." The mortality rate is high, varying between 25 and 50 per cent. When death takes place it is most apt to occur during the first week of the eruption. That the disease may be conveyed through the atmosphere is evidenced by the fact that sheep that have never come in contact with infected anim.als, but have been kept in neighboring pens, have contracted the disease. Youatt states of sheeppox that "if it broke out in a flock, it was almost sure to be communicated, sooner or later, to all that were within a few hundred yards of it." The disease may also be conveyed by inoculation , or ovination, as it has been termed. Ovination has been extensively employed in order to mitigate the ravages of natural sheeppox. The disease under such circumstances commonly develops after four to eight days, and when performed with special precautions usually produces a milder malady than when contracted in the usual manner. D'Arboval records the fact that of 32,317 sheep inoculated, 32,121 took the disease, of which 31,851 recovered and 270 died. The inoculated sheep to the number of 7697 were subsequently exposed to the infection of sheeppox without any of them contracting it. Inoculation was not so successful in the hands of Simonds and of Ceely, who lost in their first experiments almost 20 per cent, of their sheep. ^ It has been stated that ovination of pregnant ewes will subsequently protect the newborn. This is denied by D'Arboval, who says that the lambs born of sheep which had been affected wdth the natural clavelee (sheeppox), or those which were inoculated during pregnancy, do not acquire an immunity thereby from the malady. Some difference of opinion exists as to the prophylactic power of vaccination against variola ovina. D'Arboval contends that inoculation ' These experiments were conducted on a much smaller scale than those of D'Arboval. 138 THE VARIOLOUS DISEASES OF LOWER ANIMALS of a large number of sheep with virus from the cow failed to protect them against sheeppox. Sacco, on the other hand, declares that "he has fully satisfied himself by repeated experiments of the power of vaccination to destroy the susceptibility of sheep to contract variola ovina." Human Ovination. — Sacco inoculated about 300 children with the virus of sheeppox and claimed that the ovination protected them against smallpox. He states: "I subsequently determined to inoculate two children with ovine lymph on one arm and vaccine on the other; the vesicles were so similar in appearance that had I not marked the arms I should not have been able to distinguish the one vesicle from the other. A few days after the desiccation of the vesicles the children were inoculated with the virus of human smallpox, but no consequences, either local or general, resulted therefrom." The successful inoculation of sheep virus in the human subject is, however, much more difficult than would appear from the above state- ment, inasmuch as Simonds, Ceely, and Marson all failed in similar attempts, although the two latter investigators performed no less than 250 inoculations. D'Arboval also failed in conveying ovine lymph to the human subject, for he states that he successfully vaccinated a number of children after ovination had been tried. He also remarks that efforts to communicate sheeppox by inoculation to horses, oxen, goats, deer, pigs, dogs, monkeys, rabbits, and various birds were likewise unsuccessful. We believe the conclusion may be drawn that while the smallpox of sheep and that of man resemble each other clinically, and are doubtless closely related to one another, the two diseases are not identical. It would appear that sheeppox may at times be inoculated into the human subject, but there is no reason to believe in the intercommunicability of human and ovine variola by ordinary infection. No one has ever observed the smallpox of sheep give rise to smallpox in man, nor has the reverse route of infection ever been recorded. Goatpox. — The existence of a primary goatpox is doubted by most authors, the view being held that this animal, which is zoologically closely related to the sheep, contracts the disease from the sheeppox. The goatpox is accompanied by high fever and a generalized eruption. The disease is extremely rare. That the goatpox is similar in its nature to cowpox appears probable from information contained in a letter written by Prof. Heydeck to Dr. Dunning, and quoted by Baron. The letter reads: "The King ordered in September that all the children in the Foundling House should be inoculated with the goatpock, which did its effects." Variola Equina, Horsepox, Grease or Eaux aux Jambes.— The various appellations here mentioned have been applied to a pock disease in the horse which bears a close relationship to vaccinia and variola. The term grease, Jenner tells us, was employed by farriers to designate this disease upon the heels of horses. It is regretted by some writers that Jenner used this term instead of variola equina, for the employment 77//'; VMiioLous i>isI':asi<:s of low/'JH, animals ]'.>/.) of this name has given rise to some conriision. iyii|jtoi)' in ISOf) pointed out that the true analogy of eowpox in the liors(; was not tin- f/rea.fe nor any form of (jrcase, hut a disease regarded ijy the neighhoring farmers as widely different from it, and caUed by them "serateiiy heel." Loy in 1801 (listinguish(>(l two forms of grease, the aente and the ehronie, the former of whieli alone was capable of imparting the disease to the bovine of human sj)eeies. llorscpox, unlike the variolous disease in man and in sheep, d(jes not seem to arise through the action of a volatile contagiurn, but practi- cally always results from inoculation, either accidental or intended, '^rhe disease is ushered in with fever, but this in many cases is slight and often al)sent. The eru})tion exhibits a decided preference for the fetlock joints of the hind legs, perhaps because these parts are most subjected to traumatisms. The eruption is in many cases limited to this region, but a more general eruption may exist either primarily or result second- arily from autoinoculation. Perhaps the not infrequent presence of lesions in the nasolabial region may be explained upon the grounds of autoinoculation. Occasionally, more particularly in certain epizootics, an extensive eruption may be present, involving the head, belly, and legs. Such profuse eruptions may be primary or may appear after the ordinary local symptoms have manifested themselves. The lesions begin as firm papules, which soon become flattened and are often umbilicated. By the eighth or ninth day there are seen pea-sized, round, notably elevated vesicles, which on rupture give exit to a viscid, yellowish fluid. The surrounding skin is reddened and tumefied. The pocks may now be transformed into superficial, slowly healing ulcers, or may be covered with crusts, which fall off from the fifteenth to the twenty- fifth day. Jenner briefly refers to grease in the following words: "The skin of a horse is subject to an eruptive disease of a vesicular character, which vesicle contains a limpid fluid, showing itself most commonly in the heels. The legs first become oedematous, and then fissures are observed. The skin contiguous to these fissures, when actually examined, is seen studded with small vesicles surrounded by an areola. These vesicles contain the specific fluid." It will be seen from the above description that equine and bovine variola closely resemble each other. The disease in the horse distin- guishes itself from that in the cow principally by the locality of the eruption — usually the heels and the nasolabial mucous membrane, the occasional tendency to generalization of the eruption, and by attacking the male as well as the female. The Relation of the Equine Disease to Cowpox.— Great interest attaches to this subject inasmuch as Jenner regarded grease as the progenitor of cowpox. Jenner informs us that in dairy counties in England it was frequently the custom for farm hands to dress the sores on horses and subsequently, without due attention to cleanliness, to 1 Medical and Physical Journal, November, ISOO, vol. iv. 140 THE VARIOLOUS DISEASES OF LOWER ANIMALS milk the cows. In this manner infectious matter was carried to the teats of cows, producing the cowpox. From this source other cows and many of the dairy hands became infected. Numerous experiments have proven the correctness of Jenner's assertion that' cowpox results from inoculation with matter from the grease. Woodville took exception to this view, basing his contentions upon the negative experiments of the veterinary professor, Coleman ; the latter, however, after many unsuccessful results, succeeded in producing cowpox from the grease. The horsepox has been artificially produced in the horse and other animals by inoculation. This can be done with equine lymph directly transferred from horse to horse, with equine lymph that has been successfully passed through the cow (in other words, with vaccine virus of equine origin), and finally with pure cow lymph. In horsepox produced by inoculation, the eruption, almost without exception, is limited to the site of the introduction of the lymph. The belief entertained by Jenner, that the grease was the invariable source of natural cowpox, is not concurred in by most observers. There are many modern writers who are of the opinion that horsepox is noth- ing more than a variola or vaccinia accidentally derived from the human or bovine species. That the latter theory is correct is rendered probable in view of the fact that both cowpox and human variola may be trans- planted to the horse with the production of horsepox. Chauveau injected vaccine lymph beneath the skin and into the bloodvessels and lymphatics of colts, and produced ageneralized eruption of horsepox. Copeman remarks that in all probability Jenner was mistaken in his assumption that "grease," in the sense of horsepox, was a necessary antecedent to cowpox; but at the same time there can be little doubt that the two diseases are very closely allied, if, indeed, they be not identical," We may assume that the two diseases have a common ancestry, without unavailingly attempting to adduce proof as to the priority of either. There is equal reason to believe that the hands of the groom may carry the infection from the cow to the horse as well as from the horse to the cow. Human Equination. — Horsepox has been successfully inoculated into the human subject, with the production of vesicles similar to those observed in cowpox, and with the effect of conferring immunity against smallpox. J. G. Loy^ succeeded in transferring lymph from cases of equine variola to the teats of cows, producing in them typical cowpox. From the vesicles thus formed he inoculated children and secured beautiful vaccine lesions. He furthermore inoculated horsepox directly into the human species. We quote his description of the results : "Some grease matter, obtained from the same horse, was inserted in the arm of a child. On the third day a small degree of inflammation surrounded 1 Experiments on the Origin of the Cowpox, England, 1801, pamphlet of 29 pages. Till: VA/i/(}fJ)IIS DISICASKH OF LOW Ell ANIMALS \\\ tlui wound. On (,li(^ roui'lJi (liiy tin; iiiociiljilcd phicc was iniich elevated, and a vesicle oi" a purple color was fornied on tlie fil'lli day; on the sixth and seventh (hiys the vesicle increased and the inflannruition ext<;nded and became of a deeper color; on the san)e day a, chilliness came on, attended w^ith nausea and some vomiting. 'J'hcse w(;re soon succeeded by increased heat, pains in the head, and a frerjuency of breathirif^; the feverish symptoms soon abated and disapj)cared entirely on the ninth day. On the sixth day smallpox virus was inserted into the same arm in which the matter of grease had been placed, but at a considerable distance from it. On the fourth and fifth days of the smallpox inocu- lation some redness appeai-ed al)out the wound, and on the sixth a small vesicle. '^Fhe inflamniation now decreased and on llic tiinlli day the vesicle was converted into a scab." From this child, on the sixth day, before the smallpox firus was inserted, matter was procured and inoculated int(j five other children. A vesicle was produced in each case. Ten days after the insertion of the lymph the children were all inoculated with smallpox virus, but nothing developed save a little inflammation at the site of the punc- tures. The Italian investigator, Sacco, in a letter written to Jenner in ISO'3, describes similar experiments: "A coachman came to the hospital for an eruption which he had on his hands. It was immediately recog- nized that he had contracted horsepox in caring for and dressing horses. I made nine inoculations (from the sores) on as many children. Three of these contracted an eruption exactly like that of vaccinia. I made other inoculations with the material from these children, and it has already been reproduced in four generations, with the same effect as the vaccine disease. I inoculated several of these individuals with smallpox, but without any effect. I also finally obtained, with the virus of grease inoculated into six other children, two lesions exactly like vaccine lesions." Martin, of Boston, observed a case of casual horsepox in 1881, and obtained typical vaccine vesicles therefrom. He was "called to a man of about sixty, in bed with considerable headache and febrile reaction. He presented vesicular sores, two upon the right hand and one upon the nose, surrounded by areolae, and very painful. These lesions had existed for about five or six days. The patient was employed as a groom in a horse-car stable in which were a large number of horses suflfering from sore heels, and his duties obliged him to constantly handle these heels. The lesions in the groom closely resembled vaccine vesicles, and the exuding lymph was therefore collected upon ivory points and inoculated into several children and a number of heifers. In every case a typical vaccinal result was obtained. This '"stock' was continued through cows for some time." It is interesting to note that Martin discovered casual cowpox at Cohasset during the same month. A number of other competent observers have confirmed the above experiments; so that it may be accepted that human beings can be 142 THE VARIOLOUS DISEASES OF LOWER ANIMALS equinated with virus taken from the horse, and that such inoculations protect against smallpox. Retro-equination has been successfully essayed in horses with bovine or human virus of equine origin. Natural Vaccinia, or Cowpox in the Cow. — Cowpox of spontaneous development is occasionally discovered in members of the bovine species. The disease in such cases is designated natural cowpox in contradis- tinction to the affection inoculated by design. Natural cowpox is an uncommon disease; indeed, it is so rare that to each case attaches an historical interest. From each cow with spontaneous cowpox a special strain of lymph is cultivated and perpetuated, so that these first sources are most highly prized. The disease is most apt to be observed in spring and early summer, when cattle yield the most milk; while any member of the bovine family (even the bull) may be attacked, it is particularly the milch cow in which the disease is found. The eruption is never generalized, but is circumscribed to the udders or their base. The location of the lesions constitutes strong evidence that the hands of the milker are the most important factor in the transmission of the disease. When the disease once appears in the herd, it spreads with considerable rapidity from one cow to another. The disease is described by the older writers as beginning with the formation of vesicles, although these are doubtless preceded by a brief stage of papulation. The vesicles are of a bluish color and situated upon a reddened and swollen base. If rupture takes place the vesicle is converted into a superficial ulcer with irregular edges, which may heal with great slowness. Desiccation begins about the twelfth day. During the suppurative stage there is usually some elevation of temper- ature, loss of appetite, and a lessening of the milk secretion. Natural cowpox frequently exhibits a succession of lesions, coming out in crops, in this respect differing from the inoculated disease. After the termi- nation of the disease depressed scars are left which may often be dis- tinguished for years. Cowpox, both the natural and inoculated form, confers a permanent immunity against a second attack. No authentic case has been reported in which a cow has twice suffered from the disease. Casual or Accidental Cowpox in Man. — It was from observation of cases of casual cowpox in dairy attendants that Jenner first conceived the theory of vaccination. These infections result from the contact of fluid from the lesions on the cow's teats with abrasions upon the hands of the milkers; one, two, or more lesions are produced, according to the number of excoriations present. Upon areas of reddened skin there soon spring up vesicles or blebs, which are of a bluish color, rounded, flat, and depressed in the centre. These contain a lymph fluid which later becomes purulent. The surrounding skin becomes reddened and tumefied, owing to the development of an erysipelatoid areola about each lesion. The neighboring lymphatic glands become swollen and painful, and the patient becomes feverish. In severe cases the illness may be sufficiently pronounced to enforce confinement to bed for a few 77//'; VA/UOLOirS DlSh'ASh'S OF IJ)\V/'JI{, y\NIMALS |.J;> (lays. In a f(!W days, however, ilien; is an ahalcnieiil, of llie loe;il infhiin- inatory distiirhanee, and of tlie eonsliint.ional syniplonis, and (lie |>iJS- tules cither become encrusted or form ulcers which j^radually heal \)y granulation. In casual cowpox the local and constitutional symptoms are more severe than when the disease is intentionally inoculated, probably because in the latter case special precaulions are observed. Apepox. — ^^rhe monkey aj)])ears to be susceptible both to smallpox and vaccinia. Zuelzer claims that he produced true variola in monkeys by inoculation with the blood and crusts of human variola. Cope- man has also succeeded in inoculating monkeys with the fluid from lesions of human smallpox. More recently successful inoculations have been carried out by Magrath and Brinckerhoff."^ Usually the resulting eruption is limited to the sites of inoculation, but occasionally a generalized outbreak occurs which may cover the entire surface of the body. Inoculated smallpox in the monkey is, however, seldom fatal. The monkey may be rendered insusceptible to smallpox by previous vaccination. It is claimed that in the tropics apes sometimes die in large numbers of natural smallpox. Anderson, of Glasgow, states that while smallpox was raging with great violence at St. Jago, on the west coast of New Grenada, monkeys were attacked with the disease in the forests near David, sixty or seventy miles away. Dying and dead monkeys were seen on the ground covered with perfect pustules of smallpox, and several ill monkeys w'ere seen on the trees, moving about in a sickly manner. In the course of a fort- night one-half of the inhabitants of the town of David were stricken with smallpox.^ Smallpox in the Camel. — In the province of Lus, in Beloochistan, the camels are said to be subject to a disease called "Photoshootur," or the smallpox of camels. This disease is said to be communicable to the camel milkers, and is alleged to protect them against smallpox.^ .' Journal of Medical Resonrcli, February, 1904. 2 Quoted by William Aitlceu, Practice of Medicine, ISGS, p. 258. ^ Quoted by Son ton, Indian Journal of Medical Sciences, October, 1839. CHAPTER IV. SMALLPOX. Synonyms. — Latin, Variola; French, La Petite Verole; German, Blattern, or Pocken; Italian, Vajuola. Definition. — Smallpox is an acute infectious disease characterized by an initial fever of about three days' duration, succeeded by an eruption passing through the stages of papule, vesicle, and pustule, ending in incrustation and leaving pits or scars, the fever either intermitting or remitting in the papular stage and increasing in the pustular stage. Derivation of Name. — Some difference of opinion exists as to the derivation of the term variola. It is alleged by some that it was coined by the monks during the Middle Ages, and that it is the diminutive form of the Latin word Varus (a papule, pimple, or tubercle), a word found in Pliny. Other writers, however, believe it to be derived from the word varius, which means spotted or variegated. The Saxon equivalent pocca, meaning a bag or pouch, has given rise to the English pock and the German Pocken. Syphilis appeared in Europe about 1498 and caused some confusion of nomenclature, so that it became necessary to prefix the adjective small to the term pock, or pox, in order to distinguish it from the great pox, or syphilis. The same change was made in French phraseology; so that at the present day, variola is designated smallpox, or la petite verole, and syphilis the pox, or la verole. History. — It is claimed by some writers that the antiquity of smallpox dates back to the time of the Tsche-u dynasty in China, at a period not less remote than a thousand years before the Christian era. It is stated that temples were erected in honor of the disease, and the goddess of smallpox was thus glorified. Inoculation, or "sowing the smallpox," it would appear was practised in China at a very early period, the result being crudely attained by thrusting crusts into the nostrils. Tradition has it also that smallpox existed among the Brahmin caste of India from time immemorial. Descriptions in some of the ancient sacred writings of spotted and pustular skin diseases are alleged to relate to smallpox. Like the Chinese, the inhabitants of Hindoostan are also said to have worshipped at smallpox shrines and to have offered sacrifices to the presiding goddess to grant them protection. That the Greek physicians were acquainted with smallpox is open to most serious doubt. Some authors have labored diligently to prove that the great vesicular and pustular eruptions and ''anthrakes" which Hippocrates (460-377 B.C.) speaks of relate to smallpox. While the descriptions are somewhat suggestive of this disease, they are far from constituting satisfactory evidence. SMyiLLPOX IJo The first writings of tlu; Roman period ])c,Sirin^ upon I he siilijccl. ;irf; those of the Jewish y)liilo,sof)her of Alexanfh'ia, IMiilo, wlio lived in the first c(Mitnry. II !s (l('S('ri|)tion of the Egyptian phij^ue' might witli greater reason he a,ssnm(>(l to refer to smallf)ox than the writings of Ilippoerates: "From the great suffering, natural to the fermentation of festers so extensive, their bodies were tortured and their minds fiJIerl with horror. The lesions tin-own out soon merged into extensive })listers filled with pus, as if the ])arts had been burned. It extended over the whole body from head to foot." This deseription is, as Ilaeser contends, strongly suggestive of confluent smallpox. Haeser^ concludes, from a study of the Greek and Roman writings, "that knowledge of smallpox among the ancient Greeks and Romans probably existed, although we cannot with absolute certainty either affirm or deny this assertion." The word " variola" is first mentioned by Bishop Marius,of Ivausanne, who employed the term (et variola Italiam Galliamque afflixit) in 570 a.d. in describing a devastating epidemic that swept through Italy and France. The same epidemic was doubtless referred to by Bishop Gregory, of Tours, who, in 582, under the name of "lues cum vesicis," described a disease characterized at the beginning by high fever, vomit- ing, and "back pains," followed by the appearance of a painful eruption of hard, white vesicles, which occurred most conspicuously over the face, hands, and feet; the vesicles became pustules, and in many cases death occurred on the twelfth or fourteenth day. Procopius, in a chapter "De Bello Persico" (hb. ii., cap. 27), described a dreadful pestilence which began in Pelusium, Egypt, in the year 544. It was accompanied by buboes and carbuncles (suggesting bubonic plague), but was widespread, raged independent of season, spared neither age nor sex, attacked pregnant women severely, and was a new- disease but little understood by physicians. A short time afterward, unequivocal traces of smallpox are met with in countries bordering on the Red Sea; for we read of caliphs and caliphs' daughters being pitted and having white spots in their eyes. In 569 A.D. smallpox appears to have broken out in virulent form in the Abyssinian army of Abraha, which was besieging Mecca. The soldiers were decimated by the pestilence, necessitating the raising of the siege. Reference to a lost treatise on smallpox (seventh century) by an Alexandrian physician, Aaron, is found in the w^ritings of Rhazes. Edwardes'^ says: "The first clear description of smallpox by a physician, which has come down to us, is by Isaac, the Jew% who lived in the ninth century. A manusci'ipt latin translation of his work is in the town library of Mainz (Isaaci Israeliti. . . . opera omnia)." The most scientific and comprehensive description of smallpox handed down from these times, however, is from the pen of Rhazes, who wrote 1 Vita Moses, I, C. 22, Ed. Tauchnitz (Bonn, 1S38), tome iii. p. 151. - Geschiclite der Epidemisehen Krankheiten, Jena, 1S65, p. 27. 3 Smallpox and Vaccination in Europe, 1902. 10 146 SMALLPOX in about 910. The Bagdad physician was a prohfic writer and a close observer, and has been called "the Arabian Galen." The following quotations are of interest: "As soon as the symptoms of smallpox appear we must take especial care of the eyes, and then of the throat, and afterward of the nose, ears, and joints If a severe pain arises in the soles of the feet, then take care to anoint them with tepid oil, and foment them with hot water and cotton, .... for these and the like things soften and relax the skin, and thus facilitate the eruption of the pustules and lessen the pain." "All those pustules that are very large should be pricked, and the fluid that drops from them be soaked up with a soft, clean rag in which there is nothing that may hurt or excoriate the skin." "When the desiccation of the pustules is effected, and scabs and dry eschars still remain upon the body, examine them well, and upon those that are thin and perfectly dry, and under which there is no moisture, drop warm oil of sesamum every now and then, until they are softened and fall off." . and in order to efface the pock holes, and render them even with the surface of the body, let the patient endeavor to grow fat and fleshy, and use the bath frequently and have the body well rubbed." The above therapeutic suggestions might be incorporated in a modern treatise on smallpox with but little revision. Rhazes credits Galen with a knowledge of the disease, and also quotes from Hippocrates, Aaron, and Masawaih. The last-named writer is cited as saying : ". . . Your first care should be directed to the eye, for which you should use a coUyrium made of sumach and rose-water, in order to prevent any pustules from coming out in it." Avicenna (980-1037), an Arabian physician, was the first to dis- tinguish smallpox from measles. In the Canon Medicince he states of measles "that in it more tears flow." He also conceded the possibility of second attacks of smallpox. Franciscus de Pedemontium (1330) referred to red coverings and warm air as tending to expel the pustules to the surface, for, "according to Avicenna the sight of red bodies moves the blood." Constantinus Africanus (1075 a.d.), a Carthaginian, who lectured at Salerno, the first European medical school, closely followed, as did his contemporaries, the Arabian doctrines. He restricted the term variola, which was at that time loosely employed, to smaflpox. A tenth century Anglo-Saxon manuscript, in the Harleian collection in the British Museum, contains an exorcism and prayer in which the follow- ing words appear: ". . . , Geskyldath me vid de lathan Poccas, " which, rendered into modern English, reads: "Shield me against the hideous pocks." A Cottonian manuscript, evidently written in the eleventh century, contains a prayer to Saint Nicaise, who had the smallpox, and whose name was to be worn in an amulet to grant protection. The term pocca, which was the Anglo-Saxon equivalent of variola, SMALfJ'OX 147 is first encountered in a tenth-century leech-book of f he physician Bald. The death of Baldwin (1)01), son of the Earl of Flanders, from "variolas Sive poccas" is set forth in tlu; Jiniitiidii (Hirdniclc. Smallpox is sup|)osed to have invaded England between the tenth and thirteenth centuries, llolinshed, describing an e[;ideniic in the reign of Edward III., writes: "Also many died of small jjoklce.s, both men, women, and children." According to Ilirsch, Iceland suflVnerl frcHn smallpox in L30f), having received the infection from Denmark. John of Gaddesden, physician of Edward II. and author of Ro.ia Anglica, followed the Arabian treatment of surrounding the patif-nt with red bed-clothing, hangings, etc. He acquired a great reputation, but, according to Watson, was a "very sad knave." During the epidemic of 1694, Queen Mary, the wife of William III., died at the age of thirty-three of hemorrhagic smallpox. I>ord Macaulay, writing of the ravages of this disease, says: "That disease, over which science has achieved a succession of glorious and beneficent victories, was then the most terrible of all ministers of death. The havoc of the plague had been far more rapid ; but the plague had visited our shores only once or twice within living memory; and the smallpox was always present, filling the church-yards with corpses, tormenting with constant fears all whom it had not yet stricken, leaving on those whose lives it spared the hideous traces of its power, turning the babe into a changeling at which the mother shuddered, and making the eyes and cheeks of a betrothed maiden objects of horror to the lover." Smallpox was treated in diverse and various manners in different periods. In 1640 the hot or sweating treatment, by which the peccant humors were to be expelled, was in vogue. Diemerbroeck, a Dutch physician and professor, was an advocate of this method. Gregory remarks that when Sydenham began his medical reform, in 1667, "he had an Augean stable to cleanse." The "Enghsh Hippocrates," how- ever, was equal to the task, and succeeded in completely changing the practice with regard to smallpox. He insisted upon fresh air, and sub- stituted the cooling for the sweating treatment. He also described the disease admirably, and was the first to trenchantly distinguish between measles and smallpox. Boerbaave (1668-1738) was a warm admirer of Sydenham. He deserves the credit of having maintained that smallpox was contagious and due to a specific miasm. Smallpox in America. — It is said that smallpox reached Mexico in 1518, having been brought by a negro slave who accompanied the troops of Cortez from Cuba. According to Toribio it swept the country, destroying the lives of three and a half millions of people. De la Con- damine states that whole tribes of Indians were exterminated, and in some places no one was left to bury the dead. The disease then reap- peared at regular intervals of seventeen or eighteen years. In 1633 the Indians of Massachusetts were attacked by smallpox and slain by the thousands. The disease first appeared in Boston in 1649. Referring to the importation of smallpox into America, Gregory 148 SMALLPOX humorously remarks: "If America gave us, as people confidently say it did, the great pox, we have more than returned the compliment by introducing to her acquaintance the smallpox." In 1707 smallpox reached Iceland, destroying the lives of 16,000 people, almost one-third of the population of the island. Period of Inoculation. — Inoculation was first practised in Constan- tinople about the year 1674. Dr. Timoni (1714), Dr. Kennedy (1715), and Dr. Pylarini (1716) wrote on the subject of inoculation, but the pro- fession in England ignored the publications. It remained for the charming and accomplished Lady Mary Wortley Montague, wife of the British Ambassador to Turkey, to introduce inoculation to the Euro- pean world. The now famous letter to her friend. Miss Sarah Chis- well, written in 1717, is here appended: ". . . Apropos of distempers, I am going to tell you a thing that will make you wish yourself here. The smallpox, so fatal and so general amongst us, is here entirely harmless by the invention of engrafting, which is the term they give it. There is a set of old women who make it their business to perform the operation, every autumn in the month of September, when the great heat is abated. People send to each other to know if any of their family has a mind to have the smallpox : they make parties for this purpose, and when they are met (commonly fifteen or sixteen together) the old woman comes in with a nutshell of the best sort of smallpox, and asks what vein you please to have opened. She immediately rips open that you offer to her with a large needle (which gives no more pain than a common scratch), and puts into the vein as much matter as can lie upon the head of her needle, and after that binds up the little wound with a hollow bit of shell, and in this manner opens four or five veins. . . . The children or young patients play together all the rest of the day and are in perfect health to the eighth. Then the fever begins to seize them, and they keep their beds two days, very seldom three. They have very rarely above twenty or thirty on their faces (sic), which never mark, and in eight days' time they are as well as before their illness. Where they are wounded there remain running sores during the distemper, which I do not doubt is a great relief to it. Every year thousands undergo this operation, and the French Ambassador says, pleasantly, that they take the smallpox here by way of diversion, as they take the waters in other countries. There is no example of anyone that has died of it, and you may believe that I am well satisfied of the safety of this experiment, since I intend to try it on my dear little son. I am patriot enough to take pains to bring this useful invention into fashion in England, and I should not fail to write to some of our doctors very particularly about it, if I knew any one of them that I thought had virtue enough to destroy such a considerable branch of their revenue for the good of mankind. But that distemper is too beneficial to them, not to expose to all their resentment the hardy wight that should undertake to put an end to it. Perhaps if I live to return, I may, however, have courage to war upon them. Upon this occasion admire the heroism in the heart of "Your friend," etc. The daughter of Lady Montague was the first person ever inoculated in England (1727), although her son had previously been inoculated in Constantinople. In the following year, after six condemned criminals had been successfully inoculated, the two daughters of the Princess of Wales submitted to the new process. During the first ten years of its career inoculation met with great opposition. Later it became more firmly established, and was exten- sively practised in England up to 1800. It never, however, became popular on the Continent. The average death rate from inoculation was about one in three hundred cases, although it often rose above this. In 1798 Jenner announced his discovery of vaccination. In 1808 the inoculation of out-door patients was discontinued at the London Small- pox Hospital, and fourteen years later inoculation of in-door patients was abandoned. In 1843 Gregory wrote: "In 1840 the practice of inoculation, the introduction of which has conferred immortality on smaIjIjPox 140 the name of Lady Montague, which had been sanctiouc*! hy the College of Physicians, which had saved the lives of many kings, (queens, and princes, and of thousands of their subjects during the greater part of the preceding century, was declared illegal by the Knglish J'arliarnent, and all offenders were sent to j)rison with a gf)od flianre of the tread- mill. . . . Such are the reverses of fortune tf) vvhicli all siibhjriyry things are doomed." Inoculation was first practised in America in 1721 . It was introduced into this country, at the suggestion of the Rev. Cotton Mather, by Dr. Zabdiel Boylston, of Boston, who first inoculatecl his only son anrl then two negro servants. Before the practice was generally aecept(;d, how- ever, it was necessary to overcome here, as in England, niueli \io!ent opposition. The principal advantage claimed for inoculation was that smallpox thus produced was much milder in type than when the infection was received in the natural way; while the death rate from smallpox was one out of every three or four persons attacked, it was, at the highest from tlie inoculated disease, not greater than one out of fifty, and some- times as low as one out of three hundred, the average death rate being somewhere between the two. Not only the number of deaths, but the marred visages of persons in every community, testified to the frequency of smallpox before the days of inoculation. Indeed, it was so preva- lent in the Middle Ages as to lead to the common saying that "from smallpox and love but few remain free." The disadvantage of inocu- lation was that smallpox produced in this manner, although milder in type, was just as contagious as when contracted naturally; hence inocu- lation had the effect of keeping the disease almost constantly in existence. Prevalence of Smallpox in the Prevaccination Days. — Smallpox was so universal a disease that Ben Jonson wrote of it: "Envious and foul disease, could there not be One beauty in an age and free from thee?" Smallpox was mainly a disease of children in former times, and the adult population consisted for the most part of the survivors from an attack in childhood, therefore permanently pi'otected. The disease was regarded as universal or almost universal. According to Dr. Lettsom, most children in London had smallpox before the seventh year. Juncker estimated that 400,000 smallpox deaths occurred yearly in Europe on an average, and that five-sixths of mankind were attacked. Many writers were of the opinion that every one was attacked sooner or later. King Frederick William III. of Prussia, in a dispatch dated October 31, 1803, states that smallpox caused on an average 40,000 deaths yearly in Prussia.^ That smallpox did not respect royalty is evidenced by the formidable list of kings, queens, and princes who died of the disease: William II of Orange, Emperor Joseph I. of Austria, Louis XV. of France, two 1 The above statements are quoted from Edwardes' Smallpox and Vaccination in Europe, 1902. 150 SMALLPOX children of Charles I. of England, a son of James II. of England, his daughter Queen Mary, and her uncle, the Duke of Gloucester; the son of Louis XIV.; Louis, Duke of Burgundy; the dauphin, his wife, and their son, the Due de Bretagne; Peter 11. , Emperor of Russia; Henry, Prince of Prussia; the last Elector of Bavaria, two German empresses, six Austrian archdukes and archduchesses, an Elector of Saxony, and the Queen of Sweden (174L) The following were attacked with the disease, but recovered: Queen Anne of England, Peter HI. of Russia, Louis XIV. of France, William of Orange (afterward Will- iam III.), and Queen Maria Theresa of Austria. George Washington was "strongly attacked by the smallpox" during his early manhood, while on a visit to the West Indies. THE ETIOLOGY OF SMALLPOX. That smallpox may prevail in the frigid climes of Greenland and in the torrid regions of Africa is evidence of the fact that conditions of soil or climate exert but little influence over the disease. Practically no civilized country on the globe has been exempt from the ravages of smallpox. It follows, like other transmissible diseases, the channels of trade and human intercourse. W^hen the contagium of the disease is brought to an unprotected community, there the malady takes root and spreads. Susceptibility to smallpox is almost universal; but few persons can boast of natural immunity from this disease. Yet this individual pecu- liarity is occasionally encountered, as may be seen by reference to the his- tory of the disease during the prevaccination period. Persons have been known to go through life constantly exposed to the infection without suffering from any manifestation of smallpox. It is said that Morgagni, Boerhaave, and Diemerbroeck enjoyed this privilege. It is not impos- sible that such immunity may have resulted from a mild attack of smallpox, from which such persons may have suffered in utero, even without their mothers having presented any manifestations of the disease. Instances are recorded in which persons have resisted the infection when exposed in the usual manner, but have yielded to the disease by inoculation later in life. Gregory gives an example of this kind in the case of a lady who brought up a large family of children, many of whom she nursed through smallpox without receiving the infection herself, but at the age of eighty-three she took the disease by inoculation. While but few are naturally insusceptible to smallpox, through the agency of vaccination, individual susceptibility at the present day, is greatly changed; absolute immunity, indeed, is enjoyed by the greater part of the population. Instances are met with, under rare circumstances, of apparently healthy persons resisting the infection of smallpox at one time and yielding to it at another. We will relate a case in point: In 1874 a colored man of thirty years came under our care suffering from con- THE ETIOLOd Y Oh' SMA LLI'OX 151 fluent variola. He stated that vaccination had \ntvA) \n-YU)vu\i-A at difi:'erent times during his life, but never successfully: In 1871 he belonged to the crew of a sailing vessel in v^^hich several cases of smallpox occurred, and his duties required him to fre(|ii('ntly come in ffjiitact with those who were ill, yet he did not take the disease. He was vao cinated at that time, but, as before, without result. When he fell ill with variola three years later he was unable to account f(;r the source of the infection. The attack proved fatal. In the days when inoculation was extensively practised it was noticed that some persons exhibited a temporary insusceptibility to the infec- tion. Gregory informs us that Woodville found one out of every sixty children, and one out of twenty adults, to be temporarily insusceptible to inoculation. Experience demonstrates that the susceptibility to smallpox may at one time be diminished and at another greatly increased. The existence of acute and chronic infectious diseases is said by some writers to temporarily lessen the susceptibility to the infection of variola. Curschmann asserts " that for an individual suffering from scarlet fever, measles, or typhoid fever, there is during the entire duration of the affection only a very slight susceptibility to an attack of variola." He observed in the hospital at Mayence (where the smallpox building was near the general wards) that variolous infections never took place during the course of the typhoid process. A considerable number of typhoid convalescents, however, were attacked after their temperatures had become permanently normal. He was led to this conclusion from the fact that the interval between the time of the subsidence of the fever and the beginning of the initial stage of variola corresponded to the longest period of incubation that is encountered — namely, fourteen to nineteen days. There is no doubt, however, that the variolous infection does frequently occur during the existence of an acute disease, only the incubation period in such cases is often greatly prolonged. Smallpox has been known to exist with the acute exanthemata, particularly scarlet fever and measles. We have seen unprotected children, while suffering from measles in its most acute stage, exposed not longer than two minutes to the infection of variola, sicken with the disease after the usual incubation period. We have also observed this sequence of events to develop in connection with a diphtheria patient. In at least a half- dozen instances we have noted the coexistence of smallpox and scarlet fever. Chronic infectious maladies, such as syphilis and tuberculosis, not infrequently exist in individuals who are attacked by smallpox. Recurrent Smallpox (Second Attacks). — The susceptibility to small- pox is removed by vaccination, but frequently reappears to a greater or less degree in a variable period of time. So also one attack of smallpox does not invariably protect the individual for the remainder of his life against a future attack. It is undoubtedly the rule that a person does not suffer from the disease more than once, but well-authenticated cases of second attacks are recorded. Indeed, some writers allege that the predisposition to smallpox in some persons is so strongly marked as to render them susceptible to the infection more than twice, even as 152 SMALLPOX often as five or six times. The authenticity of reported cases of this kind, however, is not to be taken for granted, but accepted with extreme caution, as there are many sources of error. As to the frequency of secondary or recurrent smallpox, there is some difference of opinion on the part of authors. Many of the cases reported in the olden times were doubtless based upon an error of diagnosis, for the second attacks appear to have occurred almost exclusively in children. Some of the more practical writers of the early part of the last century hesitated very long before believing that it was possible for the disease to recur. The infrequency of such cases was accurately observed during the time inoculation was in vogue. Jenner, who closely studied casual and inoculated smallpox for more than thirty years, was very positive in his views as to the permanency of the protection which one attack of the disease conferred, and it was doubtless his positive convictions on this point that led him to announce his oversanguine belief in the permanency of the vaccine influence. Gregory, who enjoyed unusual opportunities for studying variola, was very incredulous on the subject of recurrence of the disease. Most of the reported cases which he was called upon to examine he found incorrectly reported. Echthyma, pustular syphilis, and particularly varicella, he states were fruitful sources of error. But few patients claiming to have had smallpox previously came under his care as physician to the vSmallpox Hospital of London for more than twenty years, and of these few only a very small fraction could stand the test of rigid scrutiny. Koch states that in the great epidemic of 1871-72, among 12,000 cases of smallpox in South Germany, no second attack occurred. Marson is responsible for the statement that during the one hundred and nineteen years since the founding of the London Smallpox Hospital, there is no record of a patient having been admitted twice, suffering from smallpox. He reports, however, the following interesting instance of recurrent smallpox: "An Irishman, the son of a medical officer of the army, who had been vaccinated in infancy by his father, and who had a large cicatrix remaining from the vaccination, and who was attended by his father for smallpox in early life and bore decided pits of the disease, in 1844, at twenty-three years of age, was admitted to the Smallpox Hospital with severe confluent smallpox, of which he died." Marson believes that exposure for a time to a great change of climate, either hot or cold, seems to predispose the constitution to receive a second attack of smallpox. It is said that Grossheim observed a light form of variola in a patient three months after the first attack, but this peculiar case was the only instance of recurrence which he noted among 22,641 in the German Military Hospitals. In regard to the historic case of Louis XV., Gregory has the following to say: "The most remarkable case of recurrent smallpox on record is that of Louis XV., King of France, who died of it in the year 1774, at the age of sixty-four, after having, as it is alleged, undergone that 77//'; ICTIOLOdY OF SMAfJJ'OX 1 Tjf} disease casually in 1724, wlicn Ik; w;is foiiitccn years of a^c. 1 liavo been at soitk; pains to iiiv(\stij)carcd to favor the spread of smallpox were: (1) Absence of sunshine; (2) presence of the sun aboNc tlx; horizfju for less than eighty hours a week — i. e., less than eleven hours j>er day; (3) temperature of the air below 50° F. ; and (4) humidity above 75° (the saturation point being taken as 100°). The Infection of Smallpox.— No one would deny at the present day that smallpox is due to a specific micro-organism. There is, further- more, no doubt that the disease is spread by means of this orgam'sm, which is reproduced in every patient. A small quantity of the fluid from a pustule inoculated into an unprotected person gives rise to the disease; this is conclusive proof of the fact that the germ is resident in the pustules. It is also present in the exhalations from the patient and in the blood. Ziilzer proved that it is contained in the blood by success- fully inoculating a monkey with blood taken from a smallpox patient. It would appear from the experiments of the older waiters that the physiological secretions and excretions, the saliva, sputum, urine, feces,' etc., are not in themselves infectious; w^hen, however, they become contaminated with particles derived from the skin and mucous-membrane lesions, they doubtless acquire an infectiousness. The contagium emitted by a patient is most intense in his immediate vicinity, but it may be transported in an active state for some distance by the atmosphere. If a susceptible person should enter a poorly ventilated small apartment containing one or more severe cases of smallpox, infection would almost certainly occur, while if the apartment were large and well ventilated and the cases few and mild, the risk of infection would be diminished; if he should approach equally near the same patient in the open air, the risk would be still less. Infectious Period of Smallpox. — Smallpox is undoubtedly infectious in all stages characterized by symptoms. It is alleged by some that the disease is even infectious during the period of incubation, but we think there is very little reason to believe that such is the case. It is possible, however, that the blood of an individual at this stage might convey the infection if it w^ere introduced into the system of a susceptible person. Schafer, quoted by Cursclimann, reports an interesting case in this' connection: "In the Charity Hospital of Berlin small pieces of skin were taken for transplantation upon other individuals from the ampu- 1 Medical Times and Gazette, March 11, 1S71. = Abstract in Lancet, October -l,. 1902. 158 SMALLPOX tated arm of a person who, before and at the time of the amputation, did not manifest the shghtest symptoms of general disease. Several hours after the amputation the patient was attacked with violent fever, followed two days later by the eruption of smallpox. One of the indi- viduals upon whom the transplanted skin had been placed was attacked by variola on the sixth day after the operation. The three others remained exempt. The disease is least infectious during the initial stage and most highly so during the suppurative and early period of the desiccative stages. The scabs are unquestionably infectious, and as long as these remain on the skin the patient should be regarded as dangerous to the com- munity. Apart from the experience of modern observers, evidence of the infectiousness of the crusts is found in the ancient custom in vogue among the Chinese of inoculating smallpox by inserting the crusts in the nose. Even after death the body retains the power of transmitting the contagium. This fact has been demonstrated more than once where public funerals have not been interdicted, and where bodies of persons who have died of smallpox have by accident found their way into dissecting rooms. It is said that a corpse may retain the infection in a condition to transmit the disease for an indefinite period — even for the almost incredible period of several years. ^ Austin Flint records an interesting case in which the disease was spread by a cadaver: "During the winter of 1848-49, a young man, a member of the Medical Class of the New York University, died suddenly and un- expectedly in the night under the care of a physician who had not thought him seriously ill. I was invited to the autopsy, and observed, when the corpse was uncovered, a few dark-red spots on the surface, which were supposed to be petechial, the principal symptoms of his attack having been gastric, with great debility, as we were informed. The coffin was taken to a New England village for burial, where at the funeral some of the relatives approached and opened it to see the face of the deceased before it was inhumed. Of this number eight were attacked with smallpox, no other person in the neighborhood being assailed." The infection of smallpox may be conveyed in the following ways: 1. Through direct exposure to the patient, or to infected secretions and excretions. 2. Through contact with objects which have been infected by the patient — for example, sick-room articles. 3. Through infection carried in the clothing or on the person of healthy individuals. 4. Through air transmission. 5. Through transmission by insects and domestic animals. Infection through Direct Exposure to the Patient. — The vast majority of cases of smallpox result from exposure to individuals suffering from 1 Vide Nouveau Dictionary, article Contagion. 77//'; i<:r[()ij<)() v of sma ijj'ox 1 5U the disease. Smallpox is the most typical exam[>lc oi the fontagious op catching disease. The briefest possible exposure on the part of a susceptible person will suffice to fjroduce the disease. Many victims never discover the source of their infection; this is not sl(r of surcharging the a,tmos|)here of the sick-room. The older writers believed that the sphere of contagious influence of small[)ox was ex- tremely limited. Haygarth, quoted by Gregory, was of the opin'on that it did nf^t extend "more than a few feet from the patient's })ody." Ilirsch says that the small{)()x contagion "can be spread by atmos- pheric currents within a small range," and that there is "no mathe- matical expression to be found for the extent of that range; at the utmost it extends no farther than the immediate surroundings of the sick." English physicians have within recent years devoted considerable study to the determination of the striking distance of the disease. In the epidemic of 1881, Mr. W. H. Power,* after excluding all possible infection through ordinary intercourse, formulated an hypothesis of atmospheric convection of the smallpox poison. He assumerl that smallpox infective material was "particulate," and that certain favorable conditions could disseminate such particulate matter over an area of a quarter or half a mile. The particulate matter, or infectious dust, may be held in suspension in the water particles in the air, in fog and mist, and may be driven l)y air currents and deposited at some distance. During periods of still- ness of the air about the hospital the infection is taken up and then wafted by the winds. The absence of ozone in the atmosphere is also said to be favorable to spread of infection. Periods of small move- ment of air and absence of ozone are said by INIr. Power to have preceded each of the more notable epidemic extensions in the neigh- borhood of the Fulham Hospital. Parkes^says: "The exceptional incidence of smallpox in the immediate neighborhood of some of the London Smallpox Hospitals can admit of but one explanation, viz., that when a sufficient number of cases in the acute stages are collected together in one building on a small area of ground, the hospital becomes a centre of infection to the surrounding neighborhood." (See Fig. 20.) "As regards the number of cases aggregated in a hospital necessary to enable it to exert an influence on the surrounding neighborhood, Dr. Power's reports of 1884-85 show that this influence was exerted when the number of acute cases had been restricted to twenty, while on one occasion he found the excess of smallpox in the neighborhood of the Fulham Hospital was quite remarkable at a time when the total admissions to the hospital had not exceeded nine, only five of these being cases in an acute stage." 1 Supplement to Local Government Board, lSSO-81, also 1SS4-S5. - Hygiene and Public Health, London, 1901. 11 162 SMALLPOX Mr. A. W; Blyth^ remarks. "The usual spread of smallpox is from person to person, but, from inquiries which have taken place as to the influence of smallpox hospitals upon a surrounding population, it is certain that the infection can strike at a distance. Special area around Fulham Hospital divided into sections of li,%, ^, and 1 mile radii, show- ing in the different areas the number of houses (out of every 100) invaded by smallpox from May 25, 1884, to September 26, 1885. Between N. and W. the hospital was greatly isolated from traffic because of few roadways. Belt of houses between W. and S. comparatively narrow. Between N. and E. houses few within 34 mile ; beyond they completely encompass the hospital. The so-called special area was within 500 feet from the hospital centre. The influence of the Sheffield Hospital in the epidemic of 1887-88 could be distinctly traced for a circle of four thousand feet : the following percentages of households attacked at successive distances from the hospital are given in the original reports by Dr. Barry,^ inspector of the Local Government Board for England: to 1000 feet 1.75 1 1 " 2000 " 0.50 j 2 " 3000 " 0.14 \ 3 " 4000 " 0.05 I Elsewhere 0.02 J Percentage of houses attacked at varying distances from Sheffield Hospital. The possibility of smallpox spreading by aerial infection increases greatly both the hospital difficulty and that of individual isolation." 1 Manual of Public Health. 2 Report of an Epidemic of Smallpox at Sheffield, 1887-88 ; London, 1889. nil': KTioLodY of smalIjI'ox 163 Evans,' from ohscirvatioii of r;i(lfon!, came to the .same eoricliisioii ;i,.s l>;irry. I)iiriiioi.sf>n iuu\ tlie rjiifhrcak of the disease can oc(;asionally he detennined witli a fonsidcrahh; degree of accuracy, ^riiis is more easily accomph'shed in sj)oradic cases, where an indivi(hial has l)een exposed bnt once and for a brief period of time. Where the exj)osure is frccjnent or extends f>ver a long period it is (hfficult to (h'vine the exact moment when the infection is received. When the (hsease prevails in epidemic form it is not impos- sible for an unknown exposure to precede the one of which the indi- vidual has knowledge; in such cases the com])nted [X'riod of incubation would appear to be unusually short. Erroneous calculatif)ns f)f tlie duration of the period of incubation have (ioul)tless arisen from fnihire to recognize this fact. In the majority of cases in which we have had the opportunity of carefully studying the incubation stage, we have found it to 1>P t*^" j^} twej^g, dia.yS7 xind we would, with other writers, regard this as the normal - period. In a few instances it is true we have known persons to fall ill with smallpox after the raising of a two weeks' quarantine of the houses in which they were confined and in which smallpox had existed. W^e have also been able in a few cases to reckon with tolerable certainty a period of incubation of sixteen days, the eruption appearing on the eighteenth. Some writers have recorded instances in which the incu-_ bation period has been prolonged to twenty days. On the other hand, we have known a young physician, exposed to smallpox, to develop the first symptoms at the end of five and a half days, and the eruption at the termination of ten and one-half days. Ordinarily, however, the . period is seldozii, less. than eight days or more than fourteen. The incubation period is ordinarily not characterized by any active symptoms. Patients usually pursue their daily occupations ignorant of the fact that there is developing within them a dread disease. There are, however, frequent exceptions to this rule. It is not rare for patients to lose their appetite and complain of lassitude, chilliness, headache, gastric uneasiness, etc. These symptoms, when they occur, are com- monly noted during the last few days of the incubation period. They may, however, develop as early as a week before the invasive chill. Now and then a patient will complain of slight sore throat during the last days of this stage. The Stage of Invasion, or Initial Stage. — This stage is frequently ushered in with suddenness and with considerable violence. The earliest symptom is most frequently a chill. This may be severe enough to be accompanied by chattering of the teeth, or it may consist of a succession of creepy sensations scarcely sufficient to attract the patient's attention. Synchronously with the chill or immediately following it the fever appears. The temperature on the first day often rises to 103° or 104° F., and on the second and third day, with perhaps the exception of slight morning remissions, it rises still higher, frequently reaching 105°, and in some cases even 107° F. The elevation of temperature is usually sudden; in but few diseases does it rise so quickly from the normal to a high degree. Even in varioloid the early sjTiip- 168 SMALLPOX toms are not infrequently equally severe, although occasionally they are so mild as to escape attention. But the eruption of unmodified smallpox seldom if ever appears without being preceded by a well- marked invasive stage. , During the continuance of the fever the skin is hot and sometimes dry. Profuse sweating, however, is by no means uncommon; this is apt to come on in the evening. The pulse, as a rule, is full, tense, and rapid, its frequency generally corresponding with the temperature curve. In adults it varies between 100 and 130, while in children it not infrequently reaches 160. In some cases the pulse during the initial stage will be found to be relatively slow and entirely disproportionate to the height of the fever. We have on a number of occasions noted a pulse of 90, 80, and even 70, with a tem- perature of 104° or 105° F. These cases were seen in the hospital on the first and second day of the eruption ; consequently we are not able to state whether this pulse rate was present at the onset of the initial symptoms. The respirations -are almost always increased in frequency, espe- cially when the temperature is excessively high. Prostration is often extreme, being out of all proportion to the length of the illness. Strong and robust patients are frequently unable to stand without support, and when in the upright position soon become pale and liable to be attacked by vertigo or syncope. Thirst is great, the lips and tongue are parched and dry, and there is complete loss of appetite. Constipation is a common symptom and is apt to persist throughout the course of the disease. The tongue is usually coated with a thick, yellowish covering, and the breath is heavy and offensive. iVccording to some authors, the odor from the body of a patient at this stage of the disease is so peculiar and distinctive as to make it possible for the diag- nosis of smallpox to be made by this symptom alone. We must confess that our olfactories have not acquired the degree of acuteness to detect such an odor. Irritabihty of the stomach is a very frequent manifestation. Occa- sionally the first symptom noted by the patient is severe and persistent vomiting. In such cases the disease has on more than one occasion been regarded as gastritis. The vomiting often continues for two or three days. It is apt to be accompanied by marked tenderness and pain in the pit of the stomach. The irritability usually ceases when the eruption appears. When it continues longer it should be viewed with some soHcitude. Especially in hemorrhagic smallpox is this symptom, together with epigastric pain, apt to be distressing and prominent. Nausea and retching are present in some cases without actual emesis. _ Headache is the,moat.prominent-amongthe..early nervous symptoms. It usually follows shortly after the chill, but in a certain proportion of cases it precedes it, being not infrequently the earliest evidence of ill- ness. Its intensity varies greatly, corresponding in a measure with the height of the febrile action. At times it is so excruciating as to cause even self-restrained individuals to cry aloud. The face is often flushed, 77//'; S YMPTOMA TOIJX! V OF SMA L/J'OX 169 the carotids visibly pulsating. Restlessness and sleeplessness are com- mon symptoms diirino- this stage. Children, on the contrary, are some- times drowsy and sl('cj)y. When the temj)erature is high, delirium is prone to supervene. This usually takes the fonn of talkative incoher- ence, although some patients become! (|uite violent. Coma is rare in adults, but not uncommon in children. Convulsions are frequently seen in children, more so ])erhaps in this disease than in any other of the exanthemata. They may be severe and repeated, and may contimie even after the appearance of the eruption. Pain in the back is a symptom so commonly observed that it is believed to be of special diagnostic value. It is nol ;is (onstant as some of the otlier symptoms, yet it occurs in more than one-half of the cases. In perhaps one-third of the cases it is sufficiently severe to cause the patient to volunteer information concerning it. Its diagnostic import, therefore, is due rather to its infrequency in the other acute infectious diseases than to its constancy in smallpox. The lumbar and sacral regions are the parts to which the pain is usually referred, although it may extend to the dorsal region. As a rule, it is more severe in unmodified sma]l})ox than in varioloid, yet this rule is subject to many exceptions. In hemor- rh agic cas.e.s th e pain is often of an excruciating violence. Lumllaf pain is more constantly seen among female than male patients, owing to the fact that the menstrual function is very liable to be excited by the initial illness of smallpox. In the vast majority of women who are stricken with smallpox the menses appear out of their regular period. This is - true of mild as well as severe cases. The premature onset of the men- strual flow occurs with more striking frequency in this disease than in any other of the infectious maladies. Pregnant women are exceedingly liable to suffer from abortion or premature delivery. The pain in the back owing to these causes is given greater .prominence in women- General aches and pains are frequently complained of, appearing at the same time as the headache and backache. These may occur any- where, but are usually referred to the lower extremities, particularly about the knees. Thk-S-oreness of the general muscular system may Isaxi-to^ confusion of diagnosis with ia griffe. Veriigo, which is particularly manifest upon the patients assuming the erect position, is a common early symptom. It is often well marked, even in mild cases, for these patients are more apt to rise from their beds. Syncopal attacks may occur in weak individuals. •"¥r©^iisseau records having seen during the initial stage patients who suffered from temporary loss of power in the lower extremities, asso- x^olaiecl in a few instances with retention of urine. When this condition occurs, it is, in our experience, most likely to be encountered at a later period of the disease. There is a considerable deg^ree of variation in the character and sequence of the symptoms constituting the initial stage of smallpox. This is shown in the following analysis of ICO cases occurring in the epidemic of 1901 and 1902: The patients, who were taken without selection, were closely interrogated as to the nature and chrono- 170 SMALLPOX logical development of the various symptoms. The number includes 28 cases of confluent smallpox, 15 with very profuse and semiconfluent eruptions, 29 with eruptions of moderate severity, and 29 cases of mild varioloid. Of this series of 100 patients, 22 died. Headache was the most constant of the initial symptoms. The various symptoms men- tioned were present in the following percentages: Headache, 86 per cent.; chills or chilKness, 78 per cent.; backache, 70 per cent.; vertigo, 57 per cent. ; vomiting, 55 per cent. ; nausea without emesis, 10 per cent. In some of these cases the symptoms were of marked severity, while in others they were extremely mild. An effort was made to determine the earliest symptom observed by these patients. It is recognized that some inaccuracy must arise from an attempt to chronologically arrange the symptoms from histories thus obtained. Chilliness or a decided, chill was the first symptom in Headache was the first symptom in . . . Backache ■< " " " .... Vomiting " " " "... General aches and pains were the first symptoms in Vertigo was the first symptom in . 35 eases. 26 " 16 " 9 " 7 " 2 " In but 2 patients out of the 100 was Jhei;e. complete absence ^f initial illness; 1 of these was a man, aged twenty-six years, witlfi a very mild varioloid, and the other a colored woman, aged twenty- seven years, with an eruption of moderate severity. Upon close inquiry the latter patient admitted experiencing fatigue upon the day preceding the eruption. It is possible that some negative histories of this character may be due to poor memory or lack of intelligence on the part of the patients. In the severe cases the initial illness was always well marked, although the classic symptoms were not invariably present. A man, aged fifty- five years, who had a fatal confluent attack had merely as prodromes a severe chill, fever, and prostration; headache, backache, vertigo, and vomiting were absent. A male patient, aged twenty-nine years, with an eruption of moderate severity, experienced, during the initial stage, fever, repeated vomiting, and pain in the stomach, without any other symptoms. On the other hand, quite a number of patients with very mild eruptions gave a perfect history of the classic initial syndrome. A young woman of twenty years, for instance, with only three or four lesions on the face and a few upon the arms and hands, experienced, at the onset of the disease, headache, backache, repeated vomiting, severe chills, vertigo, and aching in the legs. These observations are in accord with those of most writers, and seem to illustrate the impossibility of forecasting the extent of the eruption from the degree of severity of the initial symptoms. We have frequently seen the most aggravated febrile symptoms followed by a "perfectly insignificant eruption. Mild initial manifestations are rarely succeeded by a severe cutaneous outbreak. In general terms it may be stated that severe initial symptoms may be followed either by a profuse or a sparse eruption, and that mild initial symptoms are nearly always followed by a mild eruption. THE 8 YMPTOMA TO L d V F SMA fJJ'OX 17] The urine, in the initial staf^e, is usually more or lc.-,s diuiinishcd aceordin*^ to the (le^rc(^ of tlie fever. 'J'Ik; solid constituents are nf>t out of their normal proportion, excej)t the chlorides, which are cc>nsiderahly diminished. In severe cases, especially thos(; about to hecrjuK; hemor- rhafijic, albuminuria may be present. A high gracJe of fever might be responsible for a small (juantity of albumin, but if it be present in great abundance a malignant type of the disease should })e suspected. Before giving an unfavorable prognosis, however, care should ])t taken to exclude the possibility of pre-existing (Jisease of the kidneys. The spleen may be found enlarged in the initial stage of severe small- pox. In mikl cases no enlargement, as a rule, can be detected. I'eculiar prodromal rashes often make their appearance during the initial illness. When they develop it is usually j^ji^ori .the second day of .Jije invasive fever. They disappear ordinarily in from twenty-four to forty-eight hours. They may, however, continue several days after the "appearance of the eruption. The frequency of these rashes appears to vary in different epidemics. During the widespread and malignant epidemics of 1871 and 1872 they were very common. Osier noted these rashes during this period in 13 per cent, of his cases. These eruptions are not so apt to be observed in smallpox hospitals, inasmuch as they disappear commonly before the diagnosis is made and the patient conveyed to the hospital. The most common type is that resemhling measles, with which disease, indeed, it is liable to be confounded. The eruption has an irregular distribution, bei-ng at times generalized and at other times limited to certain regions of the body. It, moreover, differs from the eruption of measles in that the rash is not elevated above the level of the skin and therefore scarcely appreciable to the finger when passed over it. Its ephemeral character is also a differ- entiating feature. This roseola variolosa, as it has been designated, has a close analogue in the roseola vaccinosa which occasionally appears about the ninth to the eleventh day after vaccination. — JTh fi jcarZajt74^z/orm rash is less common than the measles-Hke eruption. It may involve a large part of the cutaneous surface, but is more apt to affect certain areas, as the thighs, inguinal regions, extensor surfaces of the extremities, and the trunk. Some authors refer to the appearance of an urticarial eruption in rare cases. The petechial or hemorrhagic initial rash has a special predilection for certain regions of the body which were carefully studied by Simon, of Hamburg. This writer pointed out the frequent occurrence of the eruption in the lower abdominal, inguinal, and genital regions and inner aspects of the thighs, constituting a triangle whose base traverses the neighborhood of the umbilicus (the so-called crural triangle of Simon). The " axillary triangle," including the inner aspect of the arm, axilla, and pectoral region is also a commonly affected area. The petechial rash is also frequently seen along the lateral surface of the thorax and abdomen. The eruption consists of closely aggregated, pinpoint to pinhead sized, purplish or clarety spots, which are in such intimate juxtaposition as to convey the impression of a diffuse redness. 172 SMALLPOX Being the result of a hemorrhagic extravasation into the skin, the discoloration does not disappear upon pressure. Occasionally an erythematopetechial rash is seen, the eruption partaking of the characters of both the erythematous and hemorrhagic rashes. The petechial eruptions may occur in cases which later .prove to be . quite mild. More often, iioweyer, they arejhe harbingers of severe smallpox of the-^hemoi'diagic type. The morbijliform eruptions in"mlr~ experience are muchino-re .common -in,,, cases o|]jaHoloM7~aildTE(SF" " Qccurreuce, therefore,, may ♦be regarded as an auspicous sign. We are able to recall two cases of smallpox in vaccinated individuals in which the roseolous eruption was practically the only cutaneous manifestation. In one of these cases, it is true, about half a dozen small variolous papules appeared as the initial rash faded away, but they disappeared in two or three days without becoming in the slightest degree vesicular. ' These cases belong to the class commonly designated variola sine exantkemate, which is the most benignant form that smallpox may assume. That such cases are occasionally encountered is evident from the writings of both ancient and modern authors. Perhaps in every epidemic patients are seen who give a history of exposure to smallpox and who, in due course of time, are suddenly seized with chills, followed by headache, fever, vomiting, prostration, and pain in the back. These symptoras continue iox three or four days, and.,iheik^;UJ3si4e~jftdth,0Lut. the development of any eruption except perhaps one of .lhe.4irQ.dromal ^rashes to jvhich reference has been made. It is impossible to explain such cases on any other supposition than that th^ disease-jy as.. , XMJQ^ without. the eruption. Trousseau refers to cases observed by him in which the only symptoms characteristic of the disease were a "few pustules on the pharynx and the pendulous veil of the palate." It may be of interest to record the histories of two patients under our observation upon whom but a single variolous lesion appeared: B. H., aged twenty-six years, suffering from measles, was sent into the Municipal Hospital under the erroneous diagnosis of smallpox. He was immediately vaccinated, but this and subsequent attempts failed. ,^_^^,^ At the end of ten days he was seized with high fever (104° F.), headache, ^/^ and vomiting. A few days later^a single papulE ap pearei Lin JJie-rPight loin. This went onT6""vesTcTe formation, becoming characteristically iimbilicated, but dried up within a few days. The patient claimed to have had smallpox at the age of eight years, but showed merely a single pit upon the- face. The following case presents a somewhat similar history: W. G., a colored lad, aged fifteen years, was vaccinated four years prior to admission; he presents a good vaccination cicatrix. He was brought into the hospital from a house from which several patients with smallpox were removed. On admission he had a temperature of 102° F. and presented other well-marked initial symptoms. On the sub- sidence of these symptoms he developed a single typical papule on the trunk. ^--^ "^ 77/ /-; S YMI'TO MA TO L CI Y O F SMA 1, 1. 1 'OX ] 7;j These cases come almost within the flefinition of viiriol.-i wiMioul an exaiithem. If smallpox may occur with tlic a[)()Ciiruiic<' of hut one lesion, there is no reason why it should not at times rjevelop witlifjut any eni|)ti()n whatsoever. The duration of the initial stage is commonly iorty-ei;i;lil lo seventy- two hours; it is rarely less, but it may be somewhat prolonged. Trousscair held that the longer the ernj)tion was delayed in its aj)j)earance, tlu; more favorable was the prognosis. This is scarcely bf^rne out by exyx-ri- ence. It is misleading to draw any prognostic conclusions from fli(; duration of this stage. It is commonly stated in text-books that u|)on (lie appearance of the eruption of smnllpox the fever subsides and a general abatement of the systemic symptoms occurs. In_our_^ejqp£nence a decided rennssion in the t emperature does- not. take place in unmodified smallpox until the second, third, or fourth day of the eruption. In very mild cases, "more particularly in those modified by previous vaccination, the temper- "atui'e may fall to normal as the exanthem makes its appearance. "\Vith tlTe fall of the fever there is a cessation of the pains and a general improve- ment in the condition of the patient. In mild cases of varioloid the illness of the patient is terminated at this stage. In severe cases the improvement constitutes but a brief respite, and then the grim struggle with the disease begins. Stage of Eruption. ^ — By carefully observing the early stage of the disease it will be found that the true erujDtion makes its appearance with remarkable regularity on the third 3ay oi the illness, calculating from The clay on which the initial chill or rigor occurred. In modified smallpox deviations from this rule may be noted. The eruption almost always appears first on the forehead and temples near the edge of the hair, "ana on the wrists. Not infrequently it is seen first on the upper lip SLiKTaround the mouth. It rapidly spreads to the scalp, face, neck, ears, forearms, and hands, always showing a decided preference for the cutaneous surfaces habitually exposed to the atmosphere. In the course of twenty-four hours, sometimes somewhat earlier, it extends to the body and lower extremities. It does not simultaneouslv afifect these regions, but attacks in succession the back, arms, breast, and finally the legs and feet. In rare cases the exanthem may be first noted on the trunk or extremities. TheJ[i,ill complement of lesions does not make its appearance at once in_any given part; the eruption continues rather to multiply for two or three days before its definite limit is reached, ^ii varioloid^iiew lesions , may continue to appear for a longer period of time. I pon carefully examining the eruption it is seen that many lesions develop at the sites of hair follicles or orifices of the sebaceous and sudorific glands. The eruption begins as small red spots or >Ji£cidcs some of which may be so small and faint as to be scarcely visible, while others reach the size of a lentil-seed. The color is at first pinkish-red, later assuming a deeper tint. In many cases the lesions on the trunk and extremities present the appearance of flea-bites. The lesions gradually increase in 174 SMALLPOX size and number, becoming more and more prominent,, so that in twenty^., _iau4?-]iQurs they assume the form of elevated papules, with a cEaracteristic feel. The early papules, particularly about the forehead and cheeks, may be more demonstrable to the sense of touch than to the eye. They possess a peculiar induration, and convey to the finger a sensation similar to that which would be produced by grains of shot embedded in the skin. The "shotty" feel varies in degree in different cases. Some papules are extremely hard, while others possess comparatively little induration. They are at first always discrete, but they may rapidly increase in number and become confluent, even before the vesicular stage is reached. On the third day of the eruption, or the fifth day of the disease, very many of the lesions which made their appearance first will be found to contain a little clear serum. Indeed, in many patients, one will be able to note on the second day a lesion here and there which has become vesicular in advance of the general eruption. These precocious vesicles are frequently of diagnostic import, enabling one in doubtful cases to assert the variolous nature of the disease. By the fourth or fifth day all of the lesions are converted into vesicles. At this stage they commonly' have the size and shape of a split-pea. Small vesicles are apt to be conical or acuminate, while the larger lesions have a convexly flat or hemispherical appearance. The vesicle of smallpox is extremely firm; not infrequently it feels harder to the finger than the papule from which it developed. In no other disease do the vesicles acquire such a degree of induration and hardness. The color of the vesicle is at first pinkish, the tint extending to the areola surrounding it. Later, as the fluid exudation into it increases, it assumes a peculiar opaline or pearly hue. This, with the shining and glistening surface, imparts to the vesicle a most distinctive appearance. One of the most characteristic features of the smallpox vesicle is the so-called "umbilication." In the smaller acuminate vesicles this is seen as a minute central depression or invagi- nation, representing in all probability the mouth of a hair follicle or sweat duct. This form of umbilication may occasionally be met with in other cutaneous diseases, when the lesions are situated at the mouths of the pilary or sudoriparous orifices. In the larger, pea-sized vesicles the umbilication is seen as a round, oval, or slightly irregular indentation. In this case the depression is flatter and is probably due to the bulging of the periphery of the pock. This latter form of umbilication is of important diagnostic value, as but few other vesicular diseases produce quite the same appearance. The forearms and the backs of the hands are, perhaps, the regions upon which umbilication is most character- istically seen. Umbilication is only observed in a certain proportion of vesicles. It is by no means a constant feature of smallpox eruption- and, indeed, is not infrequently absent altogether. This is particu- larly true of cases of varioloid. A^form of secondary umbilication is commonly seen during the stage of- decline or desiccation, when the pustules, as the result of rupture or drying, show a depression in the centre. Till': S YMI'TOMA TOLOd Y OF AM/.I LLI'OX 175 If one ()l),serv(^s closely ilic lar/^c, clear vesicles of nlioiil iIk- fifili or sixth (lay, j)ar<,iciiliirly those; situated on tiie dorsal surfaces ot" tin; hands, one can fre(juently discern jliroii^di (lie epidermal roof srjrriefhing of the interior construction of the lesions. 'I'hey will \h', seen 1o he made up of compartments which are divided by vertical septa, very much Hke the divisions of an orange. The vertical partitions are formed by the spiiniing out and reticulation of the epithelial cells f)f the rete mucosuin. This accounts for the nudtilocular chai'acter of the smallpox vesicle, and explains the inability to completely evacuate its contents by a single puncture. T^arge, fully developed vesicles frecjuently show at their central summit a disk of the color of yellowish serum, and around the periphery a whitish, puriform ring looking not unlike an arcus senilis. The predominance of the eruption of smallpox on the face and term- inal extremities is to be accounted for by the greater vascularity of the skin in these regions. That lesions are attracted by an overfilling of Fig. 22 Smallpox eruption showing confluence over an area upon which iodine had been applied before the eruption appeared. the cutaneous vessels is seen in the excessive development of the erup- tion wherever the skin has been irritated or congested. It is a common \ experience in the hospital to see in a discrete case of smallpox a profusion of lesions over a rectangular area in the lumbar or epigastric region where a mustard plaster had been applied during the initial stage for the relief of pain. Fig. 22 shows a marked confluence of the pustules in the form of a band on the wrist where the patient had applied iodine for a sprain received before his illness. An intense coalescence of the eruption upon the forearm is seen in Fig. 23. This was occasioned by the presence of a sunburn upon these parts. It is only when mechanical or chemical irritation is applied to the skin before the appearance of the eruption that an increase in the num- ber of lesions is produced. We have frequently applied tincture of iodine and similar applications to the skin in the early days of the erup- tion without augmenting the variolous crop in the region thus treated. Some of the older physicians purposely irritated the skin of certain 176 SMALLPOX portions of the body with the hope of deflecting the eruption from the face to the regions thus treated. Unfortunately, the eruption was increased in the manipulated areas without diminishing the number of lesions on the face. Pig. 23 Smallpox eruption showing areas of extreme confluence which had been the seat of a sunburn before the eruption appeared. Stage of Suppuration. — The contents of the vesicles gradually become more and more turbid, as the result of the increased exudation of leukocytes, until the lesions become frankly purulent. This condition is usually reached in unmodified smallpox about ihe .sixth day of the eruption, and marks the beginning of the stage of suJ3puration. The pustules now, in good part, become large and globular, and stand out prominently from the skin. Their color varies somewhat in different cases. At times the pustules acquire a distinctly yellowish tint not unlike the color of ordinary pus. Frequently, they retain until ruptured a peculiar chalky or grayish-white hue. The reddish areola, which is observed about the vesicles, develops in this stage into a broader, deeper-hued, violaceous halo. Where the lesions are closely aggregated the entire interpustular integument becomes reddened and tumefied. PLATE XV. Well-pronouneed Discrete Smallpox in an Unvaecinated. Subject on the Eighth Day of Eruption, showing the relative sparsity of the lesions upon the trunk. THE SYMI'TOMATOIJX; Y OF SMAIJJ'OX 177 On the face and scalp, where the eruption is apt fo be profiis<;, tlie redness and intninesc;enec are so extreme as to Hinder tli(! features of the [)atients eoni[)letely unrecogni/ahle. The eyeh'ds, as the result of oedema of the loose areolar tissue, l)ecome enormously f)uffed and com- pletely close the palpebral cleft, which is bathed in a puriform secretion. The patient for a time is unable to see, owinj^ to a complete closure of the eyelids. The lips, nose, and ears are distorted, the normal contour of the face is lost, and the entire head swollen beyond human [)ropor- tions. The patient presents a most revolting and loathsome appear- ance. One seeino; the disease for the first time in this stage is apt to be appalled by the horrible spectacle. The patient is sorely distressed by the inflammation and swelling of the scalp, inasmuch as contact with the pillow is a source of unendurable pain. Fig. 24 Discrete smallpox eruption on tbe ninth day, showing marked oedema of the face, completely closing the eyelids. As the eruption on the body and lower extremities is later in making its appearance than that on the face, so also is it later in reaching matur- ation. When the lesions upon the face have become vesicular, it will be found that the efflorescence upon the trunk and extremities is still in the papular stage. In like manner the facial lesions will have advanced to pustulation by the time that the eruption on the body has become vesicular. There is noticeable, therefore, this regular multiformity in the character of the lesions upon the different portions of the body. About the eighth day the pustules on the face have reached their greatest (levelopmcMit, and the process of retrogression then begins. They become yellowish, present a shrunken or shrivelled appearance, and rupture or collapse. On rupturing the pustules give exit to a viscid, glairy, dirty-yellow pus, which dries in the form of yello^\"ish or brownish crusts. A gradual subsidence in the inflammation and swelling takes place, and the normal outhnes of the face are once more restored. 12 178 SMALLPOX During the stage of pustulation the lesions which exhibited umbili- cation become distended and globular, thus effacing the central depres- sion. The epithelial bands holding down the centre of the lesion, in all probability become dissolved away, permitting the roof of the pustule to assume an hemispherical form. The eruption on the,,trwn4^is-atoee*~a4^way«m-U,ch les jon other parts of the body^,^ Not m|rgqjufijattyjjbe.i^^^ quite Jree from pustules, even wheii^ffiemce and hands show a marked degree of confluence. Exceptions to this rule are, however, occasionally met with. We have seen patients the skin of whose body was so profusely covered that it would have been impossible to place the tip of the finger Fig. 25 Large, full pustules on the seventh day of the eruption. upon a healthy area of skin. Of course, in such cases the danger to the patient is correspondingly increased, inasmuch as the gravity of the disease is, as a rule, directly proportionate to the extent of the eruption. In a well-pronounced case of semiconfluent smallpox under our care an approximate count of the number of lesions was made. This was accomplished by dividing the cutaneous surface into certain areas by means of a colored crayon and counting the pustules within these bound- aries. Upon the face and scalp the confluence of the pustules precluded the possibility of their being counted. A conservative estimate of the number present was therefore made. The number of lesions computed upon the different portions of the body is herewith appended: 77//'; S YM/'TOMA TOIJXl Y OF SMA LLI'OX 179 Total oil (IngerH of one hand • 'I'hiiinb ()1 I Index finger '.)! Middle " 05 r ... 392 Ring " 81 I llorsfil .surl'uce of one hand 3H2 Palmar " " " 129 Total lesions on both hands . I,Wk; PorearniR ■i,W) Anns 2,8io Chest 1.000 Abdomen 17.5 Thighs 4,180 Legs 2,8.')0 Feet 7.50 Back 5,700 Estimated number on face and scalp 3,000 Total 20,701 By evacuating some of the pustules with a pipette we estimated that the lesions at the height of their development each contained about three drops of pus. Such a computation developed the surprising fact that the patient referred to carried in his skin about five quarts of pus. We have seen large men with more profuse eruptions, who must have had in the neighborhood of forty thousand pustules. With this prodigious amount of purulent material in the skin the wonder is that any patient thus afflicted should recover. 'J^^llfL-pustulcs on the trunk appear to have a more superficial seat in . JJieL,akm than on cutaneous -surfaces constantly exposed to the air; hence,, ijtiiey arc not accompanied by the same amount of inflammatory swell- ing ov ulcerative destruction of the cutis. _ There_ is, _inQreover, vei iitlle tendency on the trunk and lower extremities to confluence of~lEe~ lesions. We frequently note a coalescence of two or three pustules as a result of their contiguity, but the vast majority of the lesions remain discrete. This statement, however, does not apply to the efflorescence on the hands and. feet. In these regions the degree of confluence may be intense and cause the patient great suffering. As a result of the thickness of" the overlying epidermis on the palms and soles, the pustules do not acquire as great a prominence as elsewhere. Being bound down by the tense and unyielding horny layer of skin, pressure is made upon the dehcate underlying cutaneous nerves, producing distressing pain. In a severe attack of smallpox the palms and soles, the fingers and toes, and the dorsal surfaces of the hands and feet are profusely covered. "\Mien the pustular stage is reached the patient becomes perfectly helpless; he is unable to feed himself or in any way utihze his hands. It is pitiful to behold him in bed, with his hands and fingers semiflexed, and his arms • outstretched for fear of the dreaded contact with the bed-clothing. At times the pustules on the back of the hands fuse and produce large bulla?, or even an extensive undermining of the epidermis similar to that seen in a bad scald. During the suppurative stage a most penetrating and offensive odor 180 SMALLPOX emanates from the body of the patient, and from the pus-stained bed and body hnen. This stench results from the decomposition of the effete and purulent discharge, and is not peculiar to smallpox. In neglected cases the odor is most sickening, and may pervade the atmos- phere of a room or, indeed, of an entire house. Eruption upon the Mucous Membranes.— Simuhaneous with the appearance of the smallpox efflorescence upon the cutaneous surface, or a little earlier, the eruption develops upon the adjacent mucous membranes. The involvement is almost exclusively confined to those mucous surfaces which are near the external orifices, or to which the air has access. The eruption early attacks the lining of the Fig. 26 Well-pronounced smallpox on the eighth day, occurring during a particularly mild epidemic, the lesions being very superficial. mouth, nose, and pharynx, and in severe cases the larynx, bronchi, and oesophagus. The extent of the enanthem bears a direct relation to the severity of the eruption of the skin. The lesions, however, are seldom as profuse upon the mucous surfaces as upon the integument. If an examination of the mouth and fauces be made at the very begin- ning of the eruptive stage, small yet distinct red spots may be seen upon the roof of the mouth, buccal surfaces, and anterior arches of the palate. These macules are pinhead sized and larger, and of an intense red color, which contrasts with the violaceous or bluish-red tint of the sur- rounding mucous membrane. In a short time the spots become slightly elevated or papular, frequently exhibiting a whitish, glistening centre. The parallelism with the evolution of the cutaneous pock ceases at this THE S YMI'TOMA TO LOG Y OF SMA /. LI'OX \ 8 ] stage of the (l('V('l()[)?iicii(. Ttic riiucous-rnenihr;iiie lesion (l(;c.s not pass tlu'ongh llic stage of j)aj)iile, vesicle, ainl pustule, l)iit pursues a eliarae- teristic eoiirst; wliicli is detennined \)y its j)eeuliar structure and its dif- ferent environment. I'here is perhaps an effort on the part of nature toward the formation of vesicles, but the thin and delicate e[>ithelium which serves as a covering is destroyed by the macerating influence of the moist secretion in which they are constantly bathed. As the eruption upon the skin becomes vesicular and j)ustular, the lesions in the mouth assume a whitish or grayish appearance, with but little if any elevation above the surface. 'Vhv denudation of the ey)itheHfd r-ovcring of the pocks leads to the j)ro(lu('ti()n of circumscribed cios oii^ or super- ficial ulcerations. '~'^^^^txricii'ii of Ike /Aroa/, particularly on swallowing, is one of the most distressing symptoms of the early eruptive stage. But few patients with well-marked attacks escape this suffering. Even when the patient is feeling otherwise well the condition of the throat constitutes a source of bitter complaint. In severe cases, at a later stage, the mucous mem- brane of the mouth is so abraded, swollen, and painful that the use of solid food is rendered impossible, and the patient is forced to subsist entirely on a liquid diet. ►XJae tongue is often the seat of lesions which seriously embarrass its movement in speaking and eating. Occasionally an intense form of glossitis is set up, causing the organ to swell so enormously as to pre- vent its retention wholly within the mouth. This condition, which was designated by the older writers as glossitis variolosa, is apt to greatly interfere with swr.llowing, and is under all circumstances to be regarded as an unfavorable sign. Much annoyance is occasioned by the presence of the eruption in the nasal cavities. The mucous membrane is at first swollen and inflamed, and later covered with crusts which obstruct the nares and render nasal breathing difficult and often impossible. This is particularly a source of distress to nursing infants, who are obliged to release the nipple from time to time to obtain the necessary amount of air. The eruptive process may involve both the pharynx ancl l9,r^ix and cause so much inflammation and swelling as to make deglutition difficult or impossible, or it may lead to the production of hoarseness and complete jiutb-On ia. In severe cases an acute oedema of the glottis may develop, which may seriously or even fatally impede respiration. Trousseau re- cords several fatal cases of this character: " Three smallpox patients, on the eighth day of the disease, which had run a perfectly normal course, were suddenly seized with a fit of suffocation which carried them ofl' in a few seconds, before there was time for anyone to come to their assist- ance. In one patient autopsy showed laryngitis, with variolous lesions below the glottis." In severe smallpox in children we have found it necessary in four instances to employ intubation in order to prevent asphyxia. In all of these cases there was laryngitis with considerable swelling of the mucous membrane. Although relief was temporarily alYorded, death ultimately 182 SMALLPOX occurred in all four cases. In one of the children the laryngeal stenosis came on late after complete decrustation had occurred on the skin, and at a time when the child appeared to be on the road to recovery. The mucous membranes of the lower portion of the body may also be involved. The eruption may attack the vulva and the mucous sur- faces of the vagina, but the lesions in these parts are not apt to be abun- dant. The lower part of the rectal mucosa may also be the seat of the variolous eruption. The meatus urinarius is occasionally involved in both males and females, but the urethral channel nearly always escapes. Delirium. — As previously stated, a variable degree of delirium may accompany the high fever of the initial stage. In our experience the most violent disturbance of cerebration occurs during the early eruptive period. This may be, in some cases, merely the continuation of the earlier delirium, but in others it seems to begin after the exanthem has made its appearance. Some patients are apparently the subjects of delusions of persecution and of hallucinations, and imagine that some one is about to do them bodily harm. Acting on this supposition the demented patient attempts to escape from the hospital and, what is quite strange, will almost always prefer to gain egress through the window. On a number of occasions patients, by the exercise of cun- ning and the awaiting of a favorable opportunity, have effected their flight with marvellous celerity, and have gained a temporary liberty in this manner. In some patients the temporary derangement takes the form of a suicidal or homicidal mania. One of our patients at- tempted self-destruction by striking himself on the head with a drinking mug, inflicting several large and painful wounds. On another occasion a female, by cunningly embracing an opportune moment, quickly ran to an open fire-grate, on which she seated herself. While her clothing was burning around her and her flesh charring, she violently resisted the efforts of the nurse to extricate her. We recall another patient who rose from his bed at night, struck the nurse to the floor, and effected his escape in his night-clothes; he wandered a considerable distance from the hospital, and succeeded, by a shrewd and plausible story, in prevailing upon the credulity of a wagon driver, who conveyed him to his desired destination. These patients are often able to answer questions coherently, and one, unprepared, may be completely deceived as to their mental condition. They are apt to exhibit, however, some injection of the conjunctivae and a wild expression of the countenance. This form of delirium was called by the older writers delirium ferox. Patients thus affected require to be closely watched, and, if neces- sary, restrained in bed by straps or other means. When a patient com- plains of persecution or asks to be permitted to attend to some business at home for a day or two, close surveillance is necessary. •"^-We^have observed this .active delirium most_pJ[ten_d^ and vesicular stag-e of the eruption. When it occurs it is usually asso- ciated with the confluent variety of smallpox, yet we have known it to occur in comparatively mild forms of the disease or when the patient 77//'; S VM/'TOMA TOLOd Y OF SMA IJJ'OX 1 8.*} had become (|uite a})yr(!l,ic;. The persistence of (lie (Iciiiiiiin for ,'i niimlxT of days is a symptom of evil portent. The delirium which is seen later, during tlie (jcclinc of iIk; cruplifjii, is'oT a d'iff(ifCTt"Char?iLf't;CT. Tt is "then of a low, nmllcriii^ form, and fre- ■ quen'fTy^ssocTated with general tremor, dry t(jiigii(;, quick and tremu- lous pulse, and a collapsed appearance of the features. These nervous symptoms are not ])eculiar to smallpox, hut may be seen in the terminal stage of typhoid and other fevers. The various forms of delirium, while more frequently observed in alcoholics, appear to be the result of the poison of the disease acting upon the nerve centres. It has already been stated that the jjj^i^yL^^y^ in unmodified small- ^QiX^ acmti nues> high until the third or fourth day of the eruption, when there occurs either a well-marked remission or a brief period of apy- rexia. In very mild cases the fever subsides earlier. The fall of the temperature, at this stage, even in severe cases, is not infrequently very rapid, so rapid, indeed, as to drop from a high degree to normal or even subnormal in the course of twelve or eighteen hours. The difference between the morning and evening temperature is not great, although the latter, as a rule, is slightly higher. When the temperature falls there is usually amelioration of all the symptoms. The pulse becomes almost normal; the respirations are easier; the pain in the back, head- ache, and irritability of the stomach all disappear, except in critical cases; the delirium ceases, enabling the patient to rest and enjoy re- freshing slumber. Even the appetite may return, and tlie patient may be led to believe that the critical period of the disease has passed and that recovery has begun. The subsidence of the symptoms is never so complete in variola vera as it is in varioloid. In the latter variety the fever and other systemic symptoms frequently disappear, and the begin- ning of convalescence is established; but in the former the chief danger is yet to be encountered. At or sliortly after the cornmencemeut of the stage of suppuration tTie ten\peratin-e again begins to rise, and continues elevated until the completion of the eruptive process, or longer if complications arise. This rise constitutes the so-called secondary or suppurative fever of smallpox. This latter .pyrexiaas, not apt to equal in. intensity the initial elevation of temperature. When the disease is of moderate severity ""^le^temperature may not rise above 102° F. or 103° F., but in well- marked confluent cases it frequently reaches 104° F., rarely exceeding that point. When hyperpyrexia develops, the thermometer registering 105° F., 106° F., or 107° F., the danger of a fatal outcome is corres- pondingly increased. The maximum degree of fever is often reached during the hours which immediately precede dissolution. Wunderlich reports an antemortem temperature of 109.2° F., and Simon has seen temperatures of 110° and 112° F. immediately after death, jrke secondary fever commences ordinarily on the. fifth or. sixth dajx^, ,,,^the eruption, when the vesicles begin to fill with .pus.. It is of indefi- nite duration, depending directly upon the extent and severity of the 184 SMALLPOX UJ 1 1 l-S (M S ■ J^ ra oS LU :::: ,<' i " ^ »8 - S ^ CO ts t.U „_ ^ CO 89 CO S .> - oS i.'i -, << „__., »S o s __j:.- f-S UJ 88 CO S' T 3' o8 UJ 06 ^ s "Tilii;^=? " »8 UJ J_ ' C-Lj =2 001 S5 2 _^=i ^ f8 UJ CO CD S °"-'-^, - w 88 Ol UJ :::::::::"":]^^:::::^, 001 S 1 50 (M UJ <-=tL:T 90 (M 2 _____.^^^___^ ^ CO UJ l-==C rr ,^ Wl 1-5 CO s JC J=i4 '^' 50 05 lU 1 R~-- -*' GOT I-E ?;i s I;i=<' ^' no 05 ui "T^^-f BO fZ 55 S 50 81 UJ '-^^-Li 001 05 s T 00 81 UJ : •= cC! z^ ■ ' ' ' rt toi i-5 CS 5 1 ; ~M :?=" 1 ^' 90 05 UI t •<" -+ 001 05 00 S 00 05 UJ 'Hi;'' 001 81 !^ s _3 ^ • '"' f-OI 05 UJ •4==:-L._ OD 801 05 CO 5 --=P, -H 001 91 UJ <-r==fc:I 1 SOI fS »o 5 K)I 1-5 UI '~=pf^-- 501 OS -cT* 2 ~ 801 IE UI "==i=:i]II 511 85 CO 2 < WI 05 UI , It?=" -^ 501 15 CI s r "'^H3A3S'SiLaONri3 0VN ;Hd ^ SOI I-- UJ "=fc3Z~ _|_ J i , '•-' 911 S5 s 2 ~^^ •W V 01 BSJ_-ao NI130VN: Hd "^ oil 15 UI Y~— '' 9U 1-5 o s _^^ 801 1-5 UJ '^yz;" rt 'd !> awv 3 XV ss4_-aj NilaovN Hd ^ 911 S5 o 2 ^>' ^ oil 15 UJ .-=^ Oil to » S oil 1-5 UJ "^FC 911 05 !r- s r^" ~rz3^ '^ 801 OS UJ "=T^ ' 801 1-5 CO s ~~j^ "^ 90 01 UJ j -^= ^ Oil 05 lO 2 511 91 UJ t""^ -- -1- 051 1-5 -* S 1^-3, = 801 OS UJ > o op §1 ^ S 1- < 5 »n 2 ^ THE SYMPTOMA TO/.Od Y OF SMA IJJ'OX 1 85 cutaneous oulhrcak. In a well-marked, discrete, or semiconflueiit ,sTnall])()x the pyrexia is apt to last froui three to six days. In severe con- (liicut cases it may continue for eif^ht to tw(;lve days or IfMi^er. It is not uncommon U)Y the secondary fever to nier; tcmj)crature is apt to e(|ual one or two dcffrees. The max- imal elevation usually occurs, in severe cases, between the seventh and tenth days. I^ater, when boils and abscesses develop, the diurnal variations are most pronounced, the evenin<^ fever not infrefjuently reaching 104° or 105° F., while the matinal temperature registers only 99° F. The pulse and respiration correspond in a general way with the temperature curve. The pulse, however, is apt to be higher in propor- tion to the temperature than during the initial stage. With a tempera- ture of 104° or 105° the cardiac pulsations not infrecjuently reach 140 or 150 to the minute. When the morning remission occurs there is a considerable slowing in the pulse rate. As is quite to be expected, the patient experiences more comfort in the mornings than later in the day. During the pustular stage the chief complaint of the patient is the gen- eral soreness of the skin. The couch upon which he lies is metaphor- ically, if not actually, "a bed of thorns;" whichever way he turns he makes pressure upon the sensitive and inflamed pocks. Nervous appre- hension, restlessness, and sleeplessness are prominent symptoms of this period. The patient is conscious of an increasing degree of pros- tration, and is frequently much concerned as to the outcome of the illness. It becomes necessary to allay the nervousness of the patient and induce sleep by the administration of an anodyne. At the end of the eighth or ninth day a sudden improvement in the general condition of the patient is often observed. The sufferer becomes brighter, volunteers information that he feels better, and exhibits altoo;ether a lesser dejjree of prostration. This is usually coincident with the onset of the period of involution and retrogression of the eruption. Period of Involution and Retrogression of the Eruption. — The exanthem of smallpox reaches the acme of its development with the com- pletion of the pustular stage. This constitutes the turning point not only of the eruption, but frequently of the disease. The first evidence of retrogression of the exanthem is noted in the subsidence of the inflammatory swelling of the skin, more particidarly in the immediate neighborhood of the pustules. The abatement is first seen on the face, where the redness and oedema have been most conspicuous. The eye- lids become less swollen, permitting the patient to again perceive the grateful light of day. The tumefied features gradually assume their normal contour, and the patient begins to acquire some semblance of his former self. Synchronous with the disappearance of the intumescence the pustules begin to dry; this period is called, therefore, the stage of desic- cation. The drying of the contents of the pustule is soon followed by 186 SMALLPOX a casting off of the crusts, when the stage of decrustation is entered upon. Nature in this manner attempts to rid the surface of the skin of the effete products which have there collected, and, finally, restore it to its normal condition. The involution of the smallpox exanthem does not occur simulta- neously upon all portions of the body surface, but follows the same sequence observed during the development of the eruption. It is but natural, therefore, that the first evidence of desiccation should be found in the facial lesions. The pustules in this region may dry without rup- ture, although more commonly the purulent contents of the lesions exude upon the surface and dry in the form of yellowish crusts. This color gradually becomes darker until it assumes a brownish tint. In neglected cases the crusts may become almost black, enveloping the face in an unsightly, immovable mask. The adherence of the crusts to the subja- Unusually large and confluent pustules on the ninth day of the eruption. cent tissues varies in degree according to the depth and intensity of the involvement of the cutis. Where the pustule is superficially seated and there is no ulceration of the skin, the crust is readily detached, exposing to view merely a reddened area of the skin. At the same time that desiccation is well established on the face, the trunk and extremities will exhibit lesions distended with fluid pus. These rupture, form crusts, and then pass through the process just described. At this period of the disease the offensive odor previously mentioned becomes most marked; in some cases it is quite unbearable, especially when the contents of the pustules discharge and decompose on the skin, or soak into the bed-clothes and there undergo putrefaction. After the rupture of large pustules the centres frequently dry and sink in, producing a cup-shaped depression or umbilication. This secondary umbilication differs from the primary variety in being dis- tinctly larger, more conspicuous, and occurring at a much later stage of the eruption. This form of umbilication is most typically seen on the dorsal surfaces of the hands. THE SVMPTOMA TOLOd Y OF SMA IJjPOX 180 of the skin and mucous inciiihranes the temperature falls less rapidly, or if complications arise it continues for a varying period according io the nature of the associated conditions. Although the; f(!ver is stearjily pijrative sta^e of the disease. The patient is irninc^rsed for fifteen or twenty rninut(!S in a bath eonsisting of a 1 : I (),()()() to 1 : 20,000 sohition of corrosive sub- Gangrene of the skin complicaUng severe smallpox ; recovery. Fig. .S7 Uangiene of the skin accompanying a severe smallpox ; ultimate recovery. 196 SMALLPOX limate. In other cases we have employed a 1 : 500 solution of creolin. After the bath the patient is dusted with weak antiseptic powders. This course of treatment has a beneficial influence in drying up the impetigo sores and in lessening the tendency to deeper infection. Secondary Toxic or Septic Rashes. — Another secondary eruption in smallpox, to which but little reference has been made in literature, is the toxic or septic rash which appears in a certain percentage of cases during the stage of decrustation. Between the eighth and eighteenth days, and most commonly on the thirteenth or fourteenth, there develops upon the trunk, extremities, and at times the face, a peculiar erythematous efflorescence. In most instances the rash consists of a diffuse, dusky redness bearing a strong resemblance to the exanthem of scarlet fever {scarlatinijorm erythema). At times it is mottled and inclined to become somewhat morbilliform in appearance. The scarlatiniform eruption is peculiar in that the skin immediately surrounding the drying pocks is often exempted, producing a sort of anaemic halo. The rash lasts for two or three days and then fades away. If the erythema has been well marked it is prone to be followed by desquamation, which may be most profuse in character. The exfoliation of the epidermis is usually rapid, and may be out of proportion to the intensity of the rash. Fig. 78 shows desquamation of the cuticle of the palms in large masses on the sixth day of the rash. In this patient the eruption was quite indistinguishable from that of scarlatina. In occasional instances a most inordinate and persistent desquamation follows. A young lad developed on the four- teenth day of the smallpox eruption a severe, deep-red erythema, which was followed by repeated exfoliation of the epidermis. This patient desquamated four or five distinct times, the whole process extending over a period of six or eight weeks. Handfuls of scales could be daily gathered from his bed. The hair of the scalp and eyebrows, and the finger-nails were subsequently lost. A patient recently in the hospital passed through an almost identical attack. Such cases merit the desig- nation of dermatitis exfoliativa variolosa. In rare instances these secondary rashes may become hemorrhagic. Hgemic extravasation into the skin is most apt to occur upon the lower extremities, where the stasis in the vessels is greater owing to gravity. We have seen a severe secondary purpuric rash, the history of which is of sufficient importance to warrant its presentation : H. W., an unvaccinated boy, aged seven and a half years, was admitted to the hospital on September 28, 1901, on the fourth day of the smallpox eruption. The attack was severe, the eruption being semiconfluent. The patient did well for seven or eight days. On the thirteenth day of the eruption, the face, on which the swelling had largely subsided, again became tumefied, the temperature rose, and a profuse macular eruption, rapidly becoming purpuric, and consisting of bluish-red pin- head to finger-nail-sized ecchymoses, developed over the trunk and extremities. The patient sank rapidly and died in two days. The secondary rashes are not infrequently accompanied by rise of temperature. The temperature may suddenly mount to 104°, decline PLATE XXIV. Exfoliative Dermatitis Occurring during tlie Course of a Severe Smallpox. THE S VMI'TOMA TOIJX; V OF SMA LIJ'OX ] U7 rapidly, and tlien remain for some days in (lie nei|^lil)0)'liof»d of lOT' oj- 102° F. Jii some palienls, witli rnslx'S of nioder;i(e sev(;ri(y, no [jyrexial elevation oeeiirs. WliiK; tlie eruption lasts tli(^ |);i(ients are, as a rule, sonniolent, extremely irritable, and eonsiflerahly prostrated. The rashes are more eoinmonly ol^served in patients who have had severe smallpox eruptions. Durinf)^ the epidemie of 1901-03, we observed these eruptions in perhaps 5 per eent. to 8 per eent. of all patients admitted. 'J'he incidence among children seemed to be greater than among adults. In the severe epidemic of smallpox in 1871-72, such rashes were much less fre(|uently observed, and in the year 1904 they were distinctly less frequent than in the two preceding years. J^e scarlat i niform erup ti on is t he t ype b^^^r most commonly seen. The resem blance to IKe^rasn oi 'scarlerlever is so strong that in the beginning the existence of the latter disease was suspected. In a small- pox hospital in a neighboring town, several patients with scarlatincjid rashes of the character referred to were believed to be suffering fi'om scarlet fever and were promptly isolated. The physician, during a visit to our wards, identified the toxic rashes with the eruption he had observed. Perhaps some of the cases of scarlet fever associated with smallpox reported by the older writers were in reality instances of scarlatiniform erythema. In a boy recently treated in the hospital, a severe variolous impetigo developed, and this was followed on the fourteenth day of the smallpox eruption by an intense macnlopapular rash,, which was on the trunk quitejiidisthiguishable from measles; on the face, however, there was relatively little eruption. The duration of the eruption was brief, and catarrhal symptoms were absent. _ The postvariolous rashes., are in all probability septic or toxic in character, due doubtless to the absorption of some j^oisoii into the' blood. Our experience in the Municipal Hospital would indicate that these are more common in patients who have been the subjects of an abundant impetigo. As far as we have been able to ascertain, none of the modern text- books or monographs on smallpox, save the article by Moore, make mention of these rashes. The earlier writers doubtless regarded the development of the erythema as evidence of an intercurrent scarlet fever, and the numerous instances of the coincidence of these two diseases may thus be accounted for. Simon,^ in an article on scarlatina and scarlatiniform eruptions in the course of smallpox, written in 1873, carefully distinguished these two conditions and reported cases representing both true scarlet fever and the secondary erythema which resembles it. In the latter cases he considers the diagnosis of scarlet fever excluded by the date of onset of 1 Ueber Scharlach und Scharlach-aebnliche-ausschlage im Verlauf der Variola, Archiv f. Der- matologie u. Syphilis, 1873, p. 115. 198 SMALLPOX the complication, the absence of adequate invasive symptoms, the mild character of the angina, the absence of or slight character of the des- quamation, and the non-contagiousness of the condition. Of thirteen cases of secondary rash, Simon observed nine develop after the tenth day of the variolous eruption. A few were seen as early as the sixth day and as late as the eighteenth or twentieth day. Simon does not seem to have encountered the profuse desquamation which has occurred in some of our cases. No mention is made by him of morbilliform rashes. According to Simon, Fleischmann also saw some of these cases, as did likewise Bernouilli, who states that in 1865 he saw a case of secondary erythema in variola which he erroneously regarded as an intercurrent attack of scarlet fever. The only other reference to these rashes that we have been able to find is by Meredith Richards,^ Medical Officer of Health of Chesterfield, England. This writer refers also to the bullous and pustular eruptions occurring late in the course of variola. He says: " Less known, and from a practical point of view less important, are certain posteruptive rashes, which include (1) a scarlatiniform erythema, general in distribution, and not differing from that common in various septic states; (2) a development of the smallpox pustules which appears to correspond to what Dr. Crocker has recently described as "impetigo contagiosa gyrata." The smallpox . pustules, instead of drying up and scabbing on the eleventh day, show signs of spreading peripherally, so that in a day or two many of the lesions consist of three well-defined parts, viz., a central scab, a surrounding vesicular ring which rapidly becomes pustular, and a red areola surrounding the pustular ring. Unless treated, the areola and pustular ring continue to spread centrif- ugally until the whole lesion may measure an inch or more in diameter. When abundant, this rash gives rise to a very remarkable appearance, and is clinically important because it is often attended by high temper- ature and other signs of septicaemia. There is no doubt that this is due to a mixed infection, as it has a tendency to occur in particular wards and may be accidentally acquired by attendants. It also merits notice in passing, as, I believe, this variety of secondary infection has not been fully described. (3) Accompanying the previous rash or occurring in other cases exhibiting signs of septicaemia, it is not infrequent to observe cases in which the healthy interpustular epidermis is raised into flaccid bullae, containing a few drops of foul, mucopurulent fluid. These bullae are soon followed by profuse desquamation, which may lead to the shedding of the nails, and are accompanied by severe constitutional symptoms of a septicaemic character. Many of them are fatal, though a good proportion appear to owe their lives to boracic baths combined with good nursing and general tonic treatment." 1 Accidental Rashes Occurring in the Course of the Exanthemata, Quarterly Medical Journal, 1896, p. 31. o ■-15 CD 3 <; ^ ct> ji m a§ d o' B' O O B: o' > X X < 77//'; vmuI':tii<:s 01' sMALLi'ox 199 THE VARIETIES OF SMALLPOX. The course jnst described relates more particularly to that form of the disease iu which the eruption is either discre/e or jiiuuMM44rflifYmf:'- In our ex[)erieuce the yast iuajority of cases met with Ijelon^ to the last- n ajne d v.-iriety that is to say, the eruption is usually cither partially or wholly condiiciil on llic face, the.dorsal surfaces of the hauds, and the lower portions of the f(jrearms, while on the trunk and extremities "^jt is'HiscrHe, save a few lesions, j)erha{)s, which may coalesce. Varia- tions'^" the extent of the eruption may reach extreme limits, from a few small pustules, scarcely characteristic enough to enable one to defi- nitely proclaim the variolous nature of the disease, to the most extensive eruption covering the entire cutaneous surface. Between these two extremes there may occur numerous grades of intermediate severity. Confluent Smallpox (Variola Confluens).— It can hardly be said that there is any symptom during the initial stage of smallpox peculiar to the confluent form of the disease. Inasmuch, however, as the symptoms preceding this type of variola are, with great uniformity, of a severe character, this _g£ave. jo rm may be excluded in tlie presence of mild., initial manifestations. Most prominent among the early symptoms -"aTe'severe headache, persistent retching and vomiting, delirium, or, in children, stupor, violent pain in the back, and high fever. The tem- perature always rises rapidly, and attains frequently an extraordinary height. It is not at all uncommon for the fever to reach 105° or 106°, F. and cases have been recorded in which a temperature of 110° F. w^as registered. . Qn.the third, fourth, or fifth day of the eruption the tempera- ture declines, but this remission is never as complete as in milder cases, 'nor does it continue as long. Xl\inng the remission the temperature is "^iibt far from 101° or 102° F. , at which point it is apt to remain for a period "ortwo or. three, days, when the secondary rise commences.,. The fever, ^iiring. the stage of suppuration, is not usually as intense as in the initial stage, yet it may at times rise considerably higher. The chart shown upon page 1S4 illustrates the temperature curve of a severe case of con- fluent smallpox, and may be taken as a fair type of the cases of this class. It may be well to add that the temperature in the suppurative stage was somewhat influenced by the use of antipyretics. It is sometimes stated that the eruption of confluent smallpox develops early, often on the second day of the initial fever. Our experience leads us to believe that this variety develops less rapidly than in modified , "^Torms of the disease, but there is a shorter interval between the time^ "of its appearance on the face and on other portions of the body. So quickly is the eruption diffused over the whole body that it has been mistaken in the papular stage for measles. -Indeed, it is the confluent form of variola which is particularly apt to be confounded with mor- ^ billi. Ordinarily in forty-eight hours the efflorescence has covered the entire body surface. Owing to the extensive involvement of the skin, redness and swelling begin early. The face is intensely h}^ersemic and the seat of distressing burning and itching. The marked suffusion 200 SMALLPOX of the countenance frequently enables one to prophesy that the disease will take the confluent form. As the ' eruption progresses it passes through the usual stages, though somewhat more slowly than in the milder cases. The papules are thickly set, and even at this stage a coalescence of lesions may be noted. The skin is thickened and indu- rated, and feels like embossed leather. Soon the grayish outlines of the vesicles make their appearance and the confluent aspect of the exanthem becomes accentuated. With the conversion of the vesicular contents into pus, great swelling and oedema develop, particularly about the face and scalp. The eyelids are enormously puffed, and the margin of the upper lid so greatly thickened that it completely overlaps the lower. The nose, lips, and ears are swollen and distorted, imparting to the countenance a most hideous expression. The transformation of the features is so rapid and complete that nurses and physicians who are off duty for a day or two are frequently unable to identify such patients on their return to the wards. The hands and feet are swollen Fig. 38 Profuse eruption upon hands. to double their natural size, and are most exquisitely tender and painful. When full pustulation is established the neighboring lesions coalesce and form large, flat blebs. In severe cases the walls of the pustules are completely swept away, producing flat, purulent, pasty-looking infiltra- tions of enormous proportions. W^hen the pus exudes upon the sur- face and dries, a most disgusting stench arises from the body. In favorable cases, with the beginning of desiccation, a subsidence in the oedema takes place, and the crusts are cast off from the skin. The decrustation is, however, slower than in the discrete and semicon- fluent forms of the disease. TJie suppurative proces§uis*de^,grand iiKJjQe pergigjtsnt, and may lead to the consecutive production inme same areas of large crusts which are successively thrown off as they form. Owing to the greater depth of the purulent inflammation in the integument, more extensive destruction of the true skin occurs and consequently the scarring is deeper and more conspicuous. Instead of discrete pits the face may be seamed with scars in a most frightful manner. 77/ a; va luicri i':s o !<• sMy\ l li-ox 201 In severe cases which are going to (cnniiijii*; i;i(;illy tin- ccjursc pm- .snTuT isTaTIi('rT!ino'rv"i"iit froin llial, above; (lc.scrilM'pie.s.sed and •^ccomp;iiii<'il I)) l)nt little swelling. 'J'he face has a peculiar hinrrerl appeaniiiee. Tlie older writers regarded the swelling of the face as a favoral)l(! sign, inasmneh as it indicated a certain vigor of the consti- tution. Physicians who have had cx[)erience with smallpox will rcco'^- nize the correctness of this observation. ^wplUng of the features is to be weJcom,ed.-aa., a, favorable indication, and the absence of . jpedema, iii confluent eruptions must, be regarded with grave foreboding. An '*ft1ffimo'us sign in these cases is the early development of flat, brownish, depressed scabs on a few of the vesicles on the forehead and cheeks. In these suppressed eruptions the vesicles are only partially filled with fluid, and the features are only slightly swollen; the skin is roughened and presents a somewhat parchmenty appearance. There is most profound prostration, and death results in almost every case. Fig. 39 Swelling of the face on the seventh day in a fatal case of smallpox. In confluent smallpox: the mucous membrane of the mouth, throaty and_ nose H always severely involved. The epithehum of these parts Ti^equently becomes so completely disorganized by the eruptive process that it presents the appearance of diphtheritic membrane. Swelhng of the tonsils and soft palate is often so great as to cause the greatest difficulty in swallowing. It is in the intensely confluent cases that glossitis variolosa is apt to occur. The parotid gland sometimes becomes acutely inflamed, perhaps by extension along the ducts of Steno. Pro- fuse expectoration of saliva is not infrequently noted. The pharvnx and larynx are almost always the seat of an extensive eruption, giA'ing rise to dysphagia, hoarseness, and aphonia. Acute oedema of the glottis is one of the most serious accidents to which this form of the disease is liable; when it develops the patient's life is placed in imminent danger. At a somewhat later period serious submucous infiltrations of pus may develop, producing tonsillar or postpharyngeal abscesses or perichondritis of the larynx. 202 SMALLPOX The constitutional symptoms during the suppurative stage of con- fluent variola are most pronounced. There is marked pyrexia (104° to 105° F.), rapid pulse, frequent cough and expectoration, great restless- ness, inabihty to sleep, and profound prostration. Dehrium is very common, but the patient does not become maniacal as he often does earlier in the disease. At this stage, also, complications are liable to occur, such as corneal ulcer, keratitis, pleurisy, empyema, suppuration of the joints, celluhtis, phlegmonous inflammations, and gangrene of the skin. Vomiting and diarrhoea may supervene, and still further exhaust the patient's ebbing vitality. In fatal cases the patient sinks into a comatose condition, the pulse becomes excessively rapid, and the temperature not infrequently rises to 105°, 106°, or 107° F. Thus closes the final chapter in one of the most distressing, cruel, and frightful diseases "to which human flesh is heir." Fig. 40 lOS" 104" '7103' if 102' ^ 101' MlElMlElME.MiElM'E'MlE M E M E M E M E M E M E M E M E M E M E M E M E M E tl E M E M E in E M E M E M E M E M E M e|« E M E - - — — - - ^ - - - - - - - - - - - - -- - - \- tt - - Z z- - A - r r - - - - = - z z ~ z: qz ~ — z z z z Z Z Z f s.- E E E ^=m-t T^ z- r- "t S= ^ r ^ ^^ E ^ — - z Z = E: :E E E E E E E E E ^l:--'f':ilU::l::A :fl:/: :V^J1— :::r E E i 1 =E =: = ^ = - = - = - Hw ""^''^^'f*'^ = = z - = ~ ^tfl' Z q - E - = ^ = = 1- S 100' S 99' 98' = E ± p: E = = 1 I = E - mm -z = = - - - - = I a E E z z = izjr z: :E — A z = Z : z z: ^nir+- rjt^' " ''Ir-r. f-:|,..,..:::., ::. -4-iq ~ d = z \: « _ _ i. _ _ - - _ „ - „ — h- _ il- L 1 _ _ _ ._ _ ' — ■ 1 - Pr ' — ' - - - - - - - — -^ E- - — ^ - — - — - -\ / \ .-T — ' E : ■ V ' :"!' -i - tmlrm 1 2 3 i 5 G 7 8 9 10 11 12 13 14 15 16 17 ls 19 30 21 22 23 21 25 26 27 2S 29 30 31 PULSE 1 1 1 .1 §|s sjs $ Si S|§S[| i $ ^ I^Hi|2|S s|= !l3 S'= js i ll'gjg m 4 ^ ife M iH 3 = il W. F., aged thirty-seven years. Case of smallpox ia an un vaccinated man, showing the rise of temperature in the initial stage ; the secondary or suppurative fever, and a later irregular fever due to ai scesses and cellulitis ; recovery. \ The mortality rate in confluent smallpox varies in different epidemics, but it is always extremely high. In general terms it may be stated that _^.le,ast one-half of such cases perish. When this form of the disease terminates in recovery it is' tmlyafter^ long and tedious convalescence, interrupted by the development of boils, abscesses, and other compli- cations. Hemorrhagic Smallpox. — Of all the forms of variola the hemorrhagic is the most formidable and mahgnant. .-For. those w-ho contract a-.-Wjellr. ,j3aarked attack ot this type of the disease there is absolutely no hope. According as the hemorrhage precedes or follows the appearance of the variolous lesions, two varieties are distinguished: (1) the so-called \^urpura variolosa, in which the-hemorrbage js the primary exanthem; (2) variola 'pustulos a hemorrhagica, in which it comes on secondarily. In certain epidemics a petechial eruption is frequently seen at the close of the initial stage of the disease, at or about the time when the eruption should appear. This symptom often precedes the purpuric 77//'; vAniH'i'iKs ()!<• sMMj.rox 20;i or hemorrhagic; lonii of the disease, and is IIk rcl'orc, as a rule, an early sign of inaligiiiiMcy. At other tiiDcs pclcchiic and cfc-hymoscs af>)jear between tlie j)a|)iiles or vesicles, or (h-vclo]) actually in the, bases of these lesions. The vesicles and [)ustules may contain })nrulent material or m;i,y fill up witli sanguinopurulent fluid. Consiclerahle diversity of ;i[)j)(!arance is sometimes manifested in the eruption of a single case. There is no satisfactory explanation at hand io elucidate the causation of hemorrhagic small{)OX. It wf)uld aj)pear that the determining factor is largely resident in the individual, inasmuch as such cases may be derived from ordinary smallpox, and, on the other hand, may give rise to the usual forms in other people. The frequency of this form of the disease varies in different epidemics, being commonest when a more malignant type of the disease prevails. It is well known, for example, that hemorrhagic variola was exceptionally common during the virulent pandemic of smallpox in 1871-72. Variola Purpurica. — Variola purpurica, or purpura variolosa, is the gravest and most malignant form that smallpox can assume. Zuelzer has called attention to the observation that 4h€period,Qf incubation in hemorrhagic smallpox is not infrequently abridged to^six. or eight days. The initial stage does not differ essentially from that of ordinary variola. The patient suffers from chill, fever, and headache, although the temper- ature is not as likely to reach so extraordinary a height as in confluent smallpox. The pain in the back is usually violent, and prostration excessive. Furtheriu7)reV'°ihe':"p^^ siiffers from precordial "Histfess, and from severe retching and vomiting. The vomiting in this iorraj)| the disease is a most distressing symptoni, and commonly proves Miiore persistent than in ordinary smallpox. It not iiifi((|ueiirly eon- yjmes^QI_seYeral days after the appearance oi the exantliem. Toward the end of tlie initial stage a diffuse efflorescence appears on various parts of the trunk and extremities, while the face remains for a time exempt. The rash is at first scarlatinoid in appearance, and disappears partially under digital pressure; later it becomes more intense and of a deeper hue, ancl hemarrhagic., extravasation into the skin occurs. Petechia^ vibices", and ecchymoses develop upon the chest, axilla^, lower portion of the abdomen, the groins and legs; the dark-red or purplish discoloration now present no longer fades away under pressure of the finger. The discoloration rapidly extends to the face, which becomes dusky red or livid and swollen. .The conjunctivae are injected, the eyes bloodshot, and the lids bluish, owing to hemorrhage into the cellular "tissue. Frequently the extravasation of blood under the conjunctiva covering the sclerotica is so great as to cause this membrane to project bgyonalhe lids, like a sac hlled with blood. Under siich 'conditions "th-e-pfttreTTt^is unable to completely close the eyes. The cornea retains its normal transparent appearance, but, owing to the elevated conjimctiva about its periphery, appears to be sunken deeply into the eyeball. This condition, together with the dark discoloration of the face and the tumefied features, gives to the patient a peculiarly unnatural expression. A close scrutiny of the skin usually reveals the presence of small abortive 204 SMALLPOX i^ vesicles, which may be almost obscured by the purplish ecchymoses upon which they may be situated. These are most apt to be found upon the forehead, axillae, groins, or wrists. The vesicles, which are of a plum- qolgred or -leaden-gray tint, never develop to any extent, I mt, remain perfectly flat. As the disease progresses the discoloration of the skin deepens on all parts of the body, giving to the integument a deep-indigo hue, which at times almost approaches black. In such cases it is difficult to say, judging from the skin alone, that the patient is not of African origin. Hence, this form of the disease has been known as black smallpox, or variola nigra. ,^The- eruptive process does not always present imequivocal evidence^ of smallpox, for there may be complete absence of true va~riele«s-ksiQjiSu__ A young woman was admitted to the Municipal Hospital, during the spring of 1902, who exhibited upon the skin nothing save a universal scarlatinoid eruption of dusky hue. No vestige of papulation or vesicu- lation was present. There was hemorrhagic extravasation beneath the sclerotic conjunctiva, and bleeding from the mouth, kidneys, and uterus. The diagnosis was rendered possible in this patient by tlie characfer of the initial illness, and the prevalence at the time of an epidemic of smallpox. In another case, observed in a young man some years ago, the eruption consisted of numerous petechise and ecchymoses, but no lesions distinctively variolous were present. Such eruptions might readily be confoupded with those of malignant scarlatina or measles, or purpura hemorrhagica. Patients presenting manifestations of this character were not uncommonly seen during the very malignant epi- demic of 1871-72. In this, as in other types of variola, the pharynx and upper part of the respiratory passages participate in the eruption. There is apt to be more or less cough, with bloody expectoration. The tongue is large and red and covered with blackish blood crusts, which may also be seen on the lips. A fa; tor peculiar to this form of the disease is exhaled; it is of a sickening character, and suggests stale or decomposing blood. Purplish spots may be seen upon the gums, palate, tongue, and buccal surfaces, but the general mucous membrane is usually pale. Hemor- rhages are quite certain to occur from the nose, bronchial mucous membrane, kidneys, rectum, and uterus. Vomiting of blood occurs in quite a large percentage of cases, and bloody stools are by no means infrequent. Indeed, blood may issue from any or all of the mucous surfaces of the body; we have even seen a sanguinolent fluid ooze from the eyes. Women almost always suffer from severe metrorrhagia, and, if pregnant, commonly abort. The temperature is seldom high, usually 100° F. or thereabouts; the pulse, however, is rapid and compressible. In our experience this type of smallpox occurs most commonly in young and vigorous persons. It is rare in young children and in adults of advanced years. The majority of victims are included between the ages of fifteen and forty years. Un vaccinated pregnant women seem particularly susceptible to this dreadful form of the disease. One of the most extraordinary features about this hopeless malady TIIM VA filEri/'JS OF SMA LIJ'OX 206 is tliat i.li( ;_j;i(Mi l;il < nmlilioii of the paticuL j'ciuaiiiii clear almost until the last mouKMit oi life. There may he delirium or stupor, hut usually the hapless vietim faces death with his mind unohscured and his intellect unimpiu'nMl. On one oecjision, one of the writers, sfandin^ Ijy fhe hedside of a most malignant case of purj)uric variola mid not thinking that the patient was conscious, remarked to the residcmt physician that there was absolutely no ground for hope in this case. The patient, although his face was of livid hue, immediately rose in bed, and in a husky voice exclaimed, with surprise, "J)octor, do you m(;an to say that I cannot get well?" In less than twenty-four hours the patient was a corpse. The course of this type of smallpox is extremely rapid. JJeatli usually takes place fypn;i tk a-third-io. llie sixth day of the eruption, common! v as a result ot sudden heart-taikire. Instances have even l)een reconled in which the patient has succumbed during the initial stage, but such cases must be of excessive rarity. No more terrible disease exists than black smallpox, for from this malady there is no hope of recovery. Variola Pustulosa Hemorrhagica. — Hemorrhagic extravasation into the skin may develop at any time during the course of the variolous exanthem. Various types of hemorrhagic smallpox may exist, inter- mediate between variolous purpura and the pustular hemorrhagic form. Htemic effusion may take place during the papular stage of the disease and may occur in the papules themselves or in the intervening areas of skin. Or the cutaneous hemorrhage may first appear during the period of vesiculation. In this case the vesicles, instead of containing clear serum, fill with a sanguinolent fluid. In other cases the extravasa- tion of blood may be delayed until the pustular stage is reached. The later the hemorrhage is postponed, the more conspicuous are the variolous lesions. The earlier it develops, the more will the true smallpox eruption be suppressed. The amount of swelling and oedema is proportionate to the extent and development of the smallpox exanthem. ^Vhen petechia? and ecchymoses develop early the skin has a peculiar livid appearance, and there is not much swelling. Scattered here and there between the flat, poorly formed vesicles are seen non-elevated, pea- sized or larger, bluish, ecchymotic spots. The hemorrhagic condition of the pustules may be limited to certain localities, or it may extend over the entire body. Inspection of the legs will often affard the first evidence of this mahgnant tendencv. During: the papular or vesicular stage it will be noted that some of the lesions upon the lower extremities are surrounded by a lialo of the tint of dilute claret wine. Ai a later period scattered pustules in this region will be seen to have centres of the color of indigo blue. Bv degrees others take on the same appearance and the color gradually deepens, until at last in severe cases the pustules on all parts of the body become distinctly hemorrhagic. At the same time Mxid spots may be seen upon the mucous membrane of the mouth and fauces. The gums are spongy and disposed to bleed. Hemorrhages occur from the nose and internal mucous surfaces, as in purpuric variola. 206 SMALLPOX The temperature hovers about 100° F., but rises higher in the event that the eruption progresses to pustulation. The pulse is rapid and out of proportion in frequency to the moderate febrile movement. As in the primary hemorrhagic type, the mind commonly remains unclouded almost until the end. This form of hemorrhagic smallpox is more protracted in its course than variolous purpura, but offers scarcely more hope for the patient. The severity of the prevailing epidemic influences the prognosis to a certain extent. In the malignant epidemic of 1871-72, patients present- ing even mild evidences of the hemorrhagic tendency almost invariably succumbed to the disease. At other times we have seen recovery take place in a few cases, but only among those in whom the hemorrhagic condition of the pustules was limited to a small number of lesions and appeared at a relatively late period of the disease, and in whom hemor- rhages from the mucous membrane were not excessive nor long continued. In June, 1902, a woman, aged twenty-four years, was admitted to the hospital with a most severe smallpox. She had never been success- fully vaccinated, although she stated the attempt had been made six times. On admission her appearance was such as to lead us to regard her case as practically hopeless. The eruption was extremely profuse and of a dusky-red color. Upon the legs some of the vesicles showed distinctly bluish centres. On raising the upper lids an extensive sub- conjunctival hemorrhage was visible in both eyes. The patient was expectorating blood, and was bleeding from the uterus and kidneys. On the following day the hemorrhagic symptoms began to subside and the variolous lesions to develop more conspicuously. The hemorrhages gradually ceased and the pustules filled up with a yellowish, puriform material. From this time on the case pursued the, usual course of a severe confluent smallpox, the patient finally recovering after a most desperate illness. Special mention is made of this case inasmuch as it is a remarkable exception to the general rule. We have never known recovery to result where all or nearly all of the vesicles assumed the hemorrhagic character at an early stage, and where there were well-marked epistaxis, haematuria, conjunctival hemorrhage, and bloody stools, together with rapid and feeble pulse and the peculiar livid, purplish, or indigo color of the skin. Pustular hemorrhagic small- pox is more apt to develop in aged and debilitated subjects, in pregnant women, and in those addicted to the free use of alcohol. We have occasionally seen distinct hemorrhage into the pustules in the lower extremities of individuals who had a smallpox modified by a remote vaccination. Most of these cases pursued the course of a varioloid and did not appear, to any great extent, to be unfavorably influenced by the bloody extravasation into the lesions. The prognosis in these cases depends somewhat upon the character of the prevailing type of the disease. Modified eruptions associated with hemorrhage might with propriety be termed hemorrhagic varioloid. Exceptionally Mild Smallpox.^ — In every epidemic of variola there are seen patients who, though unprotected by previous vaccination, TIIM VAItlETII'^H, OF SMAfJ.POX 207 present remarkably mild manif(!stalions of the- disease. 'J'lie exantliem in such cases may amount to merely a half-dozen or a clfjzen lesions, or in rare instatices there may be even a complete absence of the eruption. The mildness of the constitutional synijjtoins and the paucity of the eruption in these cases may, with r(;ason, be attributed to a certain degree of natural insusceptibility to the disease. , We desire to call attention to the fact that smallpox, under certain circumstances, may depart from its usual life history and, during epidemic prevalence, exhibit in a more or less iiiiifonn iiuniner an Example of a remarkably mild type of smallpox which has been prevailing for some years in various sections of the United States. Patient unvaccinated. extraordinary mildness. Such an epidemic has been prevailing in various sections of the United States for the past five or six years. It is said to have been imported into this country from Cuba, "vvhere it had existed during the Spanish-Cuban war. From the South this form of smallpox gradually became disseminated throughout the Middle and Western States. The disease was recognized as contagious, as it was seen to spread from one person to another and from town to town. But wherever it appeared it was observed to exiiibit the same mild type, rarely resulting in death. On account of its aberrant symptom- atology there was considerable diversity of opinion among physicians 208 SMALLPOX as to the nature of this disease. Many regarded it as chickenpox; others contended that it was smallpox. Still others, not being able to reconcile the picture with the symptomatology of either of these two diseases, regarded the new form as impetigo contagiosa, or as a cutaneous disease of a new and strange variety. During the years 1898, 1899, and 1900 there were treated in the hospital under our care 162 patients suffering from this mild type of smallpox. Of this number 138 were unvaccinated, and yet not a single death resulted; 12 of the patients were white and 150 were negroes. (The disease appeared to start among the Southern blacks, but later, in other portions of the country, the whites constituted the great majority of the patients.) The onset of this type of smallpox does not differ greatly, except in degree, from that commonly seen in the severer forms of the disease. According to information obtained from many of the patients the entire initial illness was often so mild that they were not obliged to remain constantly in bed; some even stated that they had scarcely been ill at all, and yet on close interrogation it was found that all had suffered to some degree from the usual symptoms. In a few patients the initial stage was marked by its usual severity. The vast majority of patients would not remain in bed after the eruption appeared. They preferred to don their clothes and indulge in various games. It was a novel sight to see these unvaccinated small- pox patients engage in a game of baseball on the eighth or tenth day of the eruption, by which time desiccation was often well advanced. Not more than two or three patients during this epidemic showed symptoms which were at all serious. In some of the mildest cases it was impossible to count as many as a dozen pustules upon the entire cutaneous surface. As a rule, the exanthem was discrete and the lesions sparsely distributed. A few patients, however, exhibited more copious eruptions, even to the extent of producing confluence on the face. In very mild cases the eruption pursued a short, abortive course. Even in the more pronounced cases the duration of the disease was con- siderably abridged. The course of the disease was identical with that seen in varioloid, and yet in the vast majority of the patients there was no known modifying influence operating such as results from vaccination or a previous attack of the disease. Why smallpox in the unvaccinated should present itself so generally in such an exceptionally mild form is a problem most difficult to solve. It has been suggested that this form of variola originated in Cuba and that smallpox in the tropics is less severe than in cold climates. We are not sure that this is true, but, even if it were, there is no reason why the disease should not resume its old and familiar form when transferred to temperate or colder regions. It has furthermore been suggested in explanation of the mild type that the modification is due to hereditary vaccinal influence. That this is not true is evidenced by the fact that the disease in the South prevailed largely among negroes, and it is a notorious fact that this race most flagrantly neglects vaccination. > X X < W £ Co '^s n o r;i ^ en w 0) a :z -X 2X s (/) o ^ a m t O 'o o > p <: PLATE XXIX. Same Patient as in Plate XXVIII. Photograph taken 48 hours later indicating the rapidity of the stages of desiccation and decrustation. THE VAUIF/ril<:H ()[<' SMAhhI'OX 209 Indeed, wc wore able to ascertain l)y iii(|iiiry tliiit I lie parculs of many of our patients had never been vaccinated. A^:i\u, a similar milfl epidemic occurred in the days of Jcinicr, before there would fiave been an opportunity for an hereditary iulhicnce to become; manifest. Jenner in 1798 wrote: "About seven years ago a species of smallpox spread through many of the towns and villages of this part of (Jloucesterslu're. It was of so mild a nature that a fatal instance was sc-arcely ever heard of, and consequently so little dreaded by the lower orders of the com- munity that they scrupled not to hold the same intercourse with each other ks if no infectious disease had been present among them. I never saw nor heard of an instance of its being confluent. The most accurate manner, perhaps, in which I can convey an idea of it is, by saying that had fifty individuals been taken promiscuously and infected by exposure to this contagion they would have had as mild and light a disease as if they had been inoculated with variolous matter in the usual way. The harmless manner in which it showed itself coidd not arise from any peculiarity either in the season or the weather, for I watched its progress upward of a year without perceiving any variation in its general appearance. I consider it, then, as a variety of the smallpox." Sydenham is said to have described a prototype of the mild variety of smallpox in 1771. Van Swieten, the great Dutch physician of the eighteenth century, wrote in 1759 as follows: "The primary fever is often little more than a febricula, and the pustules seldom exceed more than from one to two hundred. The form is so mild that secondary fever is not manifested and constantly is want- ing, convalescence coming on on the eighth day of the eruption." The mildness of the type of smallpox under discussion may be compre- hended from the following figures: During the year ending June 30, 1902, there were in the United States 55,857 cases of smallpox w4th 1852 deaths (a mortality rate of 3.31 per cent.), and in the year previous 38,506 cases and 689 deaths (a mortality rate of 1.79 per cent.). These figures include the smallpox in certain sections of the country where the type was of normal severity. It is reasonable to presume that in such an epidemic the causative germ of smallpox has become attenuated in its virulency, as a result of certain unknown influences. By no other method of reasoning could we account for the singular and uniform mildness which has character- ized this extensive and widespread epidemic. We believe, furthermore, that the infectivity of this mild variety of smallpox is considerably less pronounced than that of classic variola. We have noted that this type of the disease has frequently failed to spread where there appeared abundant opportunity for its diffusion. Varioloid (Variola Benigna; Variola Modificata ; Modified or Miti- gated Smallpox). — The term varioloid, from an etymological point of view, would indicate a disease merely bearing a resemblance to variola. The impression thus conveyed is, of course, a false one, for varioloid 14 210 . SMALLPOX is true smallpox in a modified form. This is evident from the fact that the infection arising from this milder form of the disease gives rise to variola vera in unprotected persons. Since the introduction of vac- cination varioloid has become much more frequent than in former times. Indeed,, in well-vaccinated communities modified smallpox is apt to numerically exceed the cases of ordinary variola. It is well known that the immunity conferred by vaccination, although complete at first, becomes in the course of time more or less impaired in the vast majority of individuals. The protective influence from this procedure diminishes very gradually for a variable period of time and may ultimately become entirely extinguished. It is readily compre- hensible, therefore,. that we may encounter vaccinated persons in whom, on the one hand, there is almost complete protection against smallpox, and, on the other, individuals whose susceptibility to smallpox has quite fully returned. TW farmgrj.^jdien they co smallpox, will exhibit the mildest sort of symptoms, with an insignificant eruption, while the" latter may develop the most severe confluent or even hemorrhagic Tariola. Between these two extremes one may encounter almost every possible intermediate grade. It should be stated, however, that it is exceptional for the vaccinal protection to be completely lost. Usually a modifying influence upon the course of the disease will be exerted, even when it appears at the outset that the patient is going to suffer from confluent smallpox. ^,The vast majority of vaccinated persons who contract smallpox have the Qpurse of the resulting disease favorably influenced. We class as varioloid all vaccinated cases in which the eruption is markedly abridged in its course and in which there is but little if any secondary rise of temperature. To be sure, cases in which a second attack of smallpox is favorably influenced by an antecedent one would also deserve this designation. We regard as variola all un vaccinated cases and all those vaccinated cases in which the eruption pursues its regular course, and is attended with secondary or suppurative fever. There are certain unprotected individuals who possess more or less natural immunity against smallpox and in whom the disease is mild and of short duration. Some writers would include these cases in the category of varioloid, but we prefer to regard them simply as mild forms of variola vera. We not infrequently meet with cases of smallpox in vaccinated indi- viduals which are so near the dividing line that the determination of the class to which they belong must be postponed until the suppura- tive stage has passed. Varioloid cannot always be distinguished in the initial stage from variola vera, since the train of symptoms may be the same and of equal severity in each. In many cases, however, the invasive manifestations in varioloid are extremely mild and will warrant a prediction of a sparse exanthem. Unmodified smallpox is so seldom ushered in with mild symptoms that the likelihood of its occurrence after shght consti- tutional disturbance is remote. It is important to remember, however, Tlll<: VAh'f/^ 4 5 5 1 8 4 3 8K Stage of disease at which abor- tion occurred . Discharged carrying foetus. Aborted 19th day of eruption. Died 7th day without abort. Aborted 7th day of eruption. Aborted 1st day of eruption. Discharged carrying fcetus. Aborted 6th day of eruption. Aborted 1st day of eruption. Died without aborting. Discharged carrying fcetus. Aborted 6th day of eruption. Aborted 4 th day of eruption. Aborted 23d day of eruption. Discharged carrying foetus. Died without aborting. Delivered 21st day of eruption. Aborted 1st day of eruption. Discharged carrying foetus. Aborted 17th day of eruption. Aborted 18th day of eruption. Discharged carrying foetus. Discharged carrying foetus. Aborted 33d day of eruption. Delivered 2 days before eruption. Discharged carrying foetus. Aborted just be- fore death 3d day. Discharged carrying foetus. Delivered on 9th day. Discharged carrying fcetus. Discharged carrying foetus. Result. Remarks. Recov- ered. " Foetus had well-marked variolous vesicles scat- Died. tered over body. Died 7th day. Died 1st day. Recov- ered. Died 6th day. Died Infant infected in utero, 4th day. exhibiting eruption on 9th day of life ; died on 14h day. Died Ceesarean section per- 8th day. formed immediately after death, but infant found dead. Recov- Delivered at term. ered. <. Infant vaccinated at birth ; vaccination " took; later contracted ,. varioloid and died. " Delivered at term. Died. Post-mortem Csesarean section ; foetus dead. Recov- Child vaccinated three ered. times, but without suc- cess remained well. " Child was successfully vaccinated, but soon developed smallpox eruption and died ; in- fection in utero. .< Delivered at term. *' Delivered at term. " Delivered at term. « Child at birth was dead and covered with a dis- crete smallpox in the pustular stage. " Baby vaccinated, but without success ; devel- oped smallpox erup- tion and died. " Delivered at term. Died. Recov- ered. " Child was successfully vaccinated ; smallpox appeared on 7th day. and child died ; infec- tion in utero. " Delivered at term. ** Delivered at term. THE VARIETII'JS f)/'' SMALLPOX 22J No. Age 23 Character ot disease. Variola. Whether vac- cinated, and if so, character of cicatrix. Not vaccinated Month of progn'cy wlicii attacked. 8^ Stage of disease at, vvliii'li ii,l)or- tioii occurred. Result. Recov- RernarkB. 101 Aborted 1st day of eruption. Aborted Utii day of eruption. ered. 102 23 " 1 poor scar. 8 « Child at birth healthv ; successfully vaccinat'd; 12 days later a half- dozen small jK^x paiiules api>eared; child died of erysipelas. 103 21 Varioloid. 1 fair " 8 Delivered Ist day of eruption. " Smallpox eruption ay)- peared on child 10 days 104 24 " 1 good ' ' 4 Discharged carrying fuetus. " after birth ; infection in ulero. 105 23 " 2 good scars. 8 Discharged carrying fa;tus. Delivered at term. 106 42 Variola. 1 fair scar. 2K Discharged carrying fcctus. 1 107 26 Varioloid. 2 poor scars. 9 Delivered at term " 108 29 " 1 fair scar. 4 Aborted 37th day of eruption. Foetus showed a sparse vesicular eruption. 109 25 " 2 good scars. 6 Discharged carrying fcetus. 110 35 " 2 fair " 6 Aborted 28th day of eruption. 111 32 " 2 good " 6 Aborted 1st day of eruption. 112 22 Variola (hemor- Not vaccinated 6 Aborted 5th day of eruption. Died 5th day. 113 27 rhagic). Varioloid Vaccinated 2 Discharged Recov- (mild). 16 days before eruption. carrying foetus. ered. Smallpox in the Foetus.— During an attack of smallpox the causative germ, in all probability, circulates in the blood stream of the patient. Therefore, when a pregnant woman suffers from variola, we would naturally expect the foetus to be likewise attacked and to pass througli all of the phases of the disease simultaneously with the mother. Strange to say, however, this is but seldom the case. In a minority of instances the foetus does become infected, but not synchronously with the infection of the mother. Indeed, in most cases in which the fatus develops smallpox it passes through a period of incubation in the same manner as if it were in the outer world ; that is to say, about two weeks elapse from the time the mother shows symptoms until the disease appears in the child. From this observation, which is quite generally the experience of most writers, it would seem that the infant in utero ordinarily becomes infected, not through the maternal circulation, but through contact or proximity. If the blood of the mother were the infecting medium the disease in the foetus should be of constant occurrence. There are rare cases in which the foetus contracts smallpox after an exposure to the disease by a mother who happens to be an immune. In such cases it is difficult to understand how the causative agent could reach the infant in utero save through the maternal blood. Smallpox may be communicated to the foetus in utero at any time between the fourth month of gestation or possibly earlier and the full term. When infection takes place in the earlier stages of intrauterine life, the foetus usually perishes and is expelled in three or four days, or it may be retained for three or four weeks after hfe has become 222 SMALLPOX extinct. There are well-authenticated instances in which the child suffers and recovers from an intrauterine attack of smallpox, and is born at term with variolous scars. When the infection takes place during the later periods of pregnancy the child at birth may be covered with the eruption, which may represent any stage of development. This occurrence is so well authenticated that it is unnecessary to quote any cases from literature. We have ourselves met with four or five instances of this character. In one case a six months' foetus presented a few red spots which evidently resulted from a mild vesicular eruption. In another instance an infant was born at the eighth month, on whose body at birth the eruption Fig. 43 Smallpox contracted in utero and appearing nine days after birth ; the vaccine lesion seen upon the arm resulted from vaccination on the second day after birth. was just appearing. In a third case a four months' foetus was expelled on the thirty-seventh day of the maternal eruption. The eruption on the child was rather sparse, consisting of two whitish, variolous pocks on the sole of the right foot, one on the heel of the left foot, one on the chest, one on the back, and two firm lesions upon the palm of each hand. The fourth case occurred in a colored child (Fig. 44) born at eight months, on the thirty-third day of the mother's eruption, the latter suffering only from a very mild varioloid. The infant had evidently been dead for some days, as the epidermis was detached from the under- lying corium in large areas. Smallpox lesions in the pustular stage (about fifth or sixth day) were present upon the face, extremities, and body, but not profusely. It was calculated that the exanthem in the Tim vAfin'■ mci \\\\\\ as a sefjiiel of variola, especially in llic lower exireniities, \i\\\\\\!i^ rise to phlegmasia alba dolens. Joint Disease — Joint disease occasionally occurs ;is ;i eornpliejition. or sef(uel ot" siTia,llj)ox, particuhirly in children. One or iu(M-e of the joints may become swollen and painful. The elbows ap})ear most likely to suffer. Chondritis and osteitis may occur, followed by suppu- rati(m and destruction of the joint and fre(|uently by death. Neve has reported a number of cases of joint and bone disease following smallpox in children, and we have likewise met with a few such cases. Abdominal Complications. — Smallpox is singularly exempt from abdominal complications. Diarrhcva not infrefpiently occurs as the result of some derangement of the digestive function. While this symptom is usually controllable, it may occasionally be so severe as to precipitate a fatal issue in those greatly weakened. Peritonitis is a rare complication, and when it occurs may be attrib- uted to some local cause. Orchitis. — We encountered this complication in perhaps six or eight patients during the first two years of the epidemic of 1901-04. The swelling may involve the entire scrotum or may be limited to the testicle and epididymis. One or both organs may be affected. The parts often become extremely firm to the touch. The enlargement commonly per- sists for a few weeks and then gradually subsides, although a variable amount of infiltration may continue for a much longer time. A young man recently under our care had a severe confluent smallpox, complicated by gangrenous inflammation of the arm, iritis, and orchitis. The right testicle was swollen to three times the size of the left. The swelling was firm and not very painful. The infiltration, which extended along the spermatic cord to the external abdominal ring, reached the diameter of an adult thumb. It is said that the analogue of this condition, ovaritis, may develop in the female. We have never observed any symptoms during an attack of smallpox pointing to acute disease of the ovaries. Phimosis. — Phimosis not infrequently occurs in the pustular stage of smallpox as a result of the swelling of the areolar tissue of the prepuce occasioned by the presence of the eruption. This is seen most commonly in young children. Nervous System. — Psychic disturbance in the form of delirium is not uncommon in the early eruptive period of smallpox. Tt may in some cases supervene at a later period of the variolous process. The delirium may persist for some days and then disappear, or in rare cases it may develop into a confusional insaniti/. The following cases of insanity after smallpox have come under our observation: E. M., aged tw^enty-eight years, was admitted to the ^Municipal Hospital on November 29, 1903, wdth smallpox. She bore one good scar from a vaccination in infancy and had a well-marked, discrete variola. On December 6th she was observed to be tlelirious at times. The mental excitement increased and the patient became maniacal 238 SMALLPOX and had to be strapped in bed. From this time on there were occa- sional lucid moments, but for the most part the patient was delirious. She would sing and cry and appeared to be completely demented. Despite the fact that the variolous symptoms had quite subsided, the patient continued to lose weight and strength and died in an insane condition, apparently from exhaustion, on January 24, 1904, two months after the onset of the attack of smallpox. Mrs. A. C. was admitted to the Municipal Hospital on March 10, 1904, with a modified attack of smallpox. She bore two good vaccination scars from infancy. The patient had never exhibited any mental disturbance before the attack of smallpox. Family history negative. On admission the patient exhibited evidences of mental disturbance. She spoke at times rationally, but for the greater part talked inco- herently and almost exclusively upon religious topics. I^ater she became maniacal, jumped from the bed and through an open window; she had to be strapped to her bed to prevent violence. At times refused to eat or drink. She later, when released from her bandages, made several more attempts to jump through the window. She was removed to her home on April 9th, her mental condition having remained unchanged. Another patient, L. E., aged thirty-seven years, who had recovered from a mild attack of smallpox, developed religious mania after con- valescence. He was transferred to a hospital for the insane. It was subsequently ascertained that he had, before his attack of smallpox, suffered from a similar mental disturbance. Several cases of insanity after smallpox are reported by Seppilli and Maragliano. Of three instances referred to, one remained permanently insane, the others recovering after appropriate treatment. The authors also record the remarkable case of a violent maniac, who had been confined for about six weeks in an asylum, who during an attack of confluent smallpox was restored to his senses and after convalescence from variola was discharged from the asylum as a sane man. Brain symptoms sometimes appear during the stage of decline. We cannot recall a single instance where we have observed clear and indub- itable evidence of acute inflammation of this organ, yet we have seen a few cases — perhaps not more than three — lapse into a state of lethargy or coma, when desquamation had almost completed, without evincing any preceding symptoms of inflammatory action. We have met with a few cases in which there were peculiar psychic changes, followed by aphasia. This condition we attributed to the presence of a circum- scribed encephalitis. Westphal has called attention to cases of similar nature. In 1872 he presented before the Berlin Medical Society a patient, who during smallpox had had attacks of delirium or coma, followed by a curious disturbance, characterized by slow, measured, scanning speech, and ataxia of the upper and lower extremities, similar to that seen in tabes. Paralysis. — Various paralyses may develop during the course of variola. During the past few years we have observed eight instances COMPTACATI()NHlANI> SPJQUELjE OF SMALLPOX 289 of paralysis among about 3000 cases of smallpox. Of this niirnher five died and three recovered. In an infant, one year and four months of age, we observed a hemi- plegia occur upon the first day of the (Tuy)tion. This succeeded repeated convulsions which took place immediately before and after the appear- ance of the exanthem. It is probable that this conchtion was not inti- mately connected with the variolous process, but resulted from a brain hemorrhage excited by the convulsive paroxysms. In another patient, a woman, paralytic symptoms appeared during the initial stage of the disease. She was brought into the hfjspifal in a stuporous state, barely able to articulate. There was great difficulty in swallowing and impaired power in the arms and legs; the loss of power in these members subsequently became almost complete, but later a gradual restoration of function occurred. The patient had a most pronounced scanning speech, which was still ])resent when she was discharged from the hospital. The reflexes were markedly exag- gerated. The third patient, a young colored man, had a severe attack of smallpox, complicated by extensive gangrene of the scrotum and penis. At the end of about ten weeks from the onset of the disease he developed partial loss of power in the legs and arms. He could walk with great difficulty with a cane. This condition persisted to the day of his departure from the hospital. Sometimes the spinal cord is preponderantly or exclusively affected, the symptoms being those of a paraplegia. We have observed a half- dozen or more instances of this serious complication, of which the following are of especial interest: Case L— C. M., aged thirty years; unvaccinated ; was seen in con- sultation on April 22, 1902, on the first day of the smallpox exanthem. The eruption was confluent on the face and hands, and covered thickly all parts of the body. The pustides began to shrink on the eleventh day; the secondare' fever was not high, and there was no delirium. The patient was progressing favorably until May 4th, when it was found that he was unable to void his urine, necessitating catheterization. On the following day paralysis of the lower extremities was noted, sensation being, however, preserved. There was also complete loss of power over the bowels and bladder. Immediately preceding the paralysis, there were hebetude and drowsi- ness, which persisted for several days. A week later, on ^Nlay 12th, slight motion returned in the legs. A gradual improvement in all of the symptoms then set in. By June 23d the patient was able to walk a few blocks without difficulty, although control over the bladder and rectum was not quite perfect. Complete lecovery ultimately resulted. Case II. — INIrs. N., married, aged nineteen years, was admitted to the hospital with a smallpox of considerable severity. She was progress- ino; well when durina; the third week of the disease she became unable to move her legs. Sensation was impaired, but not entirely lost. She had loss of control of the bladder and rectum. Within a few davs 240 SMALLPOX partial motion was restored in the lower limbs. Later diarrhoea set in and the patient died. Case III. — J. W., a man aged thirty-eight years, was admitted to the hospital on January 13, 1903. He had a scant, modified eruption, having been vaccinated in infancy. About a dozen lesions were present upon the anterior surface of the body, a few were scattered sparsely over the extremities, and on the face there were about fifty lesions. On the eighth day of the eruption the patient developed loss of power in the legs so that he was unable to raise them from the bed. Sensation was impaired, but not lost. There was no pain. The mental condition was good. Later, retention of urine developed, followed after some days by incontinence of urine and feces. The patient died on the thirty-sixth day of the disease, after ten days of high and irregular fever. Autopsy disclosed the existence of a number of abscesses in the kidneys. A culture from the intradural fluid in the spinal region revealed the presence of staphylococci. The cord from this patient and from Case II. were sent for study to Prof. W. G. Spiller,^ of the University of Pennsylvania. The spinal cord from Case II. had been hardened in alcohol and the microscopic study was, therefore, unsatisfactory, although nothing distinctly abnor- mal could be detected in the cord.^ In regard to Case III., Prof. Spiller states: "Strictly speaking, the case was one of diffuse myelitis, but with the exception of a part of the thoracic cord the myelitis was almost confined to the anterior horns and was an anterior polyomyelitis, and probably of vascular origin." Grave Lesions of the Nervous System Complicating Smallpox with but Scant Eruption. — It would appear that in rare cases the poison of small- pox is largely expended upon the nervous system, the skin escaping with very few lesions. These cases are an exception to the general statement that the gravity of smallpox is proportionate to the extent of the eruption. A remarkable case of this character came under our own observation during the year 1902. E. M., a burly negro, aged twenty-seven years, was admitted to the hospital on April 7, 1902. The patient had never been vaccinated. According to the history, the initial symptoms had been well marked — headache, vomiting, fever, and backache having been present. The entire eruption consisted of about a dozen small papules, scattered over the face, forearms, hands, and trunk. These were arrested in their development and dried up in a few days, as occurs commonly in cases of varioloid. The patient fell into a state of hebetude after admis- sion, although he had walked to the ambulance. He became progres- 1 Prof. Spiller reported the full findings in these cases in a paper entitled " A Report of Two Cases of Paraplegia Occurring in Variola, One heing a Case of Anterior Poliomyelitis m an Adult." Other cases in the literature of the subject are referred to. Brain, Autuinn, 1903, London. 2 Since the above chapter was written an article on ' ' Nervous Complications and Sequelse of Small- pox," by Dr. Charles J. Aldrich, has appeared in The American Journal of the Medical Sciences, February, 1904. The author reports three interesting cases of aphasia after smallpox, and carefully reviews the entire subject, giving a full and extensive bibliography. COMPIJCATIONS AND SMQf/h'f.A': OF SMALLI'OX 241 sively more sfiiporoiis, had difriciilty ii) swallowiiij^, and pailial ana-s- thesia and loss of power in the legs. Later, complete paraj)lcf,n"a wifli incontinence of nrine and feces developed. He died on the fourteenth day of the eru|>lion. The temperature on admission (third day of eruption) was 00.2° V.; it later fluctuated for nine days hcfwccn this point and 101° ¥., rising to 104° F. just before death. The diagnosis of smallpox, owing to the poorly developed lesions, was not entirely certain until about ten days later, when the wife and child of the patient were brought into the hospital with variola. Autopsy showed great softening of the spinal cord in the region of the lower dorsal and upper lumbar vertebne. When the dura over this area was punctured the softened cord ran out like pus. From this portion of the cord a micrococcus w^as grown on culture. The brain showed no gross changes save an intense congestion of the pia mater. It is interesting to note that in one of the cases of paraplegia reported by Westphal the patient had an extremely scant eruption and the "disease was so mild that the patient did not go to bed." MacCombie has also called attention to serious disease of the nervous system develop- ing in the course of mild cases of smallpox. Peripheral Neuritis. — Peripheral neuritis is encountered as a complica- tion or sequel of smallpox with great rarity. In the case of paraplegia, to which we have already referred, in which no microscopic changes were foimd in the cord, the lesion may have been a peripheral neuritis. Combemale believes the disorders of speech occasionally complicating smallpox to be due to paralysis resulting from the action of toxins upon the peripheral nerves. Disseminated Spinal Sclerosis. — An interesting case of typical infectious disseminated sclerosis is reported by Sottas. A young man, aged eighteen years, with a discrete smallpox eruption, presented during his illness most severe nervous symptoms. The patient was semicomatose, had a slow dragging speech, nystagmus, general paralysis, atrophy of the muscles of the trunk and limbs, and later contractures. At a subsequent date there were characteristic tremors, exaggerated reflexes, inco- ordination of voluntary movements, and great mental excitability. Septicaemia and Pyaemia. — Septicaemia is commonly observed in the stage of decrustation in confluent smallpox. In severe cases there may occasionally be seen during the third week a high and irregular fever, rapid pulse, low delirium, and great prostration, without there being discoverable any pus collection to account for these s}Taptoms. Pyaemia is more rare than would be supposed from the writings of the older physicians. Abscesses in the liver, kidney, and lungs have been revealed by autopsies, but with great infrequency. 16 242 " SMALLPOX THE PATHOLOGY OF SMALLPOX. The Histopathology of the Pock. — The microscopic structure of variolous lesions has been studied by Barensprung/ Auspitz and Basch/ Ebstein/ Rindileisch/ Unna/ Weigert/ Touton/ Renaut,^ Leloir,^ Buri/" and others. Weigert regarded the primary changes in the epidermis as necrobiotic and diphtheroid, due to the local effect of the smallpox poison. He claims to have found analogous alterations in the liver, spleen, kidneys, and lymph glands, which he believes to be specifically variolous. Nearly all of the other writers mentioned describe the early changes in the skin as inflammatory in character. According to Barensprung, cited by Curschmann, the red spot, which represents the first clinical evidence of the pock, is produced by a circumscribed hypera3mia of the papillary and deeper bloodvessels. The papule is formed by peculiar changes in the cells of the mucous layer or the rete Malpighii, which become cedematous, enlarged, and granular. The vesicle is explained by an exudation of clear fluid from the papillary bloodvessels, separating the cells above referred to. It is evident from later studies that other important processes (subsequently to be described) enter into the formation of the vesicle. The older writers believed the umbilication to be due to a hair follicle, sweat duct, or epithelial strand holding down the centre of the roof of the pock. Auspitz and Basch first pointed out that it was in reality due to the periphery of the pock swelling more rapidly than the centre. This view is corroborated by Unna, of Hamburg. Unna has carefully studied the structural changes in the skin, employ- ing the most modern histological technique." The following description is condensed from Unna's detailed account: The development of the variolous vesicle is the result of certain peculiar degenerations of the protoplasm of the epithelial cells. The main features which differentiate the vesicle formation in smallpox from that in chickenpox are the slowness of growth and the prompt addition of suppuration to the epithelial degeneration. The changes in the protoplasm of the cells of the mucous layers of the epidermis are of two chief varieties. These have been designated, by Unna, reticulating and ballooning colliquation (softening). Both are special forms of fibrinoid degeneration. Reticulating colliquation occurs as follows : As a result of the poison of the disease the protoplasm of the cells becomes cedematous and I Die Haut-Krankheiten, 1854. 2 virchow's Archiv, Bd. xxviii., S. 337. ^ Ibid., Bd, xxxiv., S. 598. * Handbuch der pathol. Gewebslehre, 1871. 5 Virchow's Arctiiv, Bd. Ixix., S. 409. 6 Anat. Beitriige zur Lehre von den Pocken, Breslau, 1874, Helt 1. 7 Vergleichende Untersuch. liber die Entwick. von Blaseu in der Epidermis, 1882. 8 Archives de la dermat. et de syph., 1881. "^ Archives de la physiol. norm, et pathol., 1880, p. 307. ' w Monatshefte f. prakt. Dermat., 1892, Bd. xiv., 1892. II Histopathology of Diseases of the Skin. Translated from the German by Dr. Norman Walker, 1896. 77//-; I'M'IIOLOCV <>/<' SM.MJJ'OX 24'i midcr^'oes jKirliiil oi- coiiiplcU; li<|iicr;u:(,i«)ii, Uiiis (.unwvvUw^ IIk; coll body into a lar^e cavity. (Coagulation of the albuminoid bodies set free from the protoplasm now tnkes place, ksading to the formation of a line griundiir prccipiliiic; which lies on the well-jjreserved nucleus or the tliiri, disixMided cell wall. The nucleus at first renuiiris healthy, but later shows fibrinoid degeneration. When the li(juci'action of the cells is partial, protoplasmic tral)ecu];c form which coagulate into a network, often radially arranged, and hold the nucleus and cell mantle together. The name "reticulating" collicpiation is given to this degeneration because of the net-like character of the structure. Fig. 47 Microphotograph of smallpox pustule showing reticulating epithelial bands. Magnified 80 diameters. This form of degeneration corresponds with the "alteration cavitaire" described by Leloir and Renaut. Leloir maintained that the cavity formation invariably began with a dilatation of the nuclear cavity; in other words, as a result of the liquefaction of the endoplasm. In the second form of fibrinoid metamorphosis — that designated ballooning colliquation — the whole protoplasm of the cell swells up and becomes cloudy and opaque. The prickle projections are withdrawn and the cell becomes rounded. The shape of the cell is largely deter- mined by its position and external pressure, and may be round or flat, biscuit-shaped, pointed, or drawn out into septoe, or bands. Most of the cells, however, have the form of hollow spheres or balloons, the predominance of which gives rise to the name " ballooning colli- quation." 244 ^ SMALLPOX The reticulating degeneration mainly attacks the older cells, or those in the upper strata of the Malpighian layer, and the ballooning degen- eration the younger cells, or those in the lower strata. This is accounted for by the fact that the younger epithelia contain a homogeneous proto- plasm which readily undergoes homogeneous swelling and coagulation, whereas in the older cells a marginal layer separates from the rest of the protoplasm in its preparation for cornification. Formation of the Smallpox Vesicle.- — During the papular stage the cavity formation begins in the upper prickle-cell layer of the epidermis by a reticulating colliquation of the oedematous epithelium. Owing to the slow advance of this process some of the cells are compressed and thus part of the cavity is, from the commencement, divided by septa into a series of segments, the bands running perpendicularly in the centre and being directed outward at the periphery. At the same time the cells of the lower prickle layer undergo ballooning colliquation. The cells lose their prickles and become detached from one another. As the pock spreads peripherally the differentiation of the process in the upper and lower strata of the prickle layer becomes more marked. In the upper part the cavity extends laterally, many of the marginal cells liquefying and communicating with the general cavity. In the lower part, on the contrary, ballooning and swelling of the cells develop slowly. At the height of the development, therefore, the pock has the shape of a mushroom, the main cavity formation taking place in the upper projecting parts, while the under half is sharply constricted. The cavity is completed by extension of the reticulating degeneration downward, particularly upon the periphery, and by the ballooning and detachment of the deeper cells; the latter subsequently become trans- formed into the compressed bands which traverse the lower portion of the pock. Umbilication. — Exceptionally a sort of umbilication may result from the accidental piercing of the centre of the pock by a hair follicle, the cornified neck of which limits the swelling of the prickle cells. The characteristic depression in the centre of the vesicle is due, however, to another cause. It is the result of the reticulating degeneration and oedematous swelling of the cells. These occur chiefly at the periphery, whereas the ballooning degeneration which occurs slowly and gives rise to less swelling takes place in the centre. The umbilication is, therefore, due rather to a bulging of the periphery of the vesicle than to a retraction of the centre. The pressure of the lateral oedematous cells is so great as to lead to obliteration of the underlying papillae, while in the centre of the pock, before suppuration begins, they not only persist but project into the cavity of the pock. During the vesicular stage the dilatation of the papillary bloodvessels beneath the pock is slight and the emigration of leukocytes is strikingly small. A dense collection of plasma cells is seen in the sheaths of the Tiii<: PAT 1101/ )(:y of ,smaijj>ox 24r> vessels and increases in niiniherjis (Jic vcsific mnliircs. 'I'liis jilxind.'ince of plasma cells is remarkable, considering the acuteness of the process, and is otdy foniid among the pock-lik(^ processes in variola itself. After the fiftli day, the bloodvessels, snpcrficial and deep, become distinctly dilated and a stream of leukocytes is poured out, doubtless attracted by the dead germs in the tissues. The margin between the corimn and epidermis is so densely packed as to be scarcely recognizable. 'I'he cavity of the pock gradually fills uj) completely with these white l)l()od cells. If the horny roof holds, the mass is converted almost into solid tissue; if it ruptures, there is morcor less profuse suppiinition, leading to the formation of crusts. The primary pustulation is due to the variolous j)oisoii, but pro- longed suppuration must l)e ascribed to secondary ])yogenic infection. Healing. — Even before the contents of the pustule are completely dry, a thin layer of epithelial cells lying close on the connective tissue extends from all sides under the pustule. When the scab is thrown off there is displayed a persistent trough-like depression. Where the scab does not to any great extent depress the base of the pock, the papillary layer is not completely flattened out, and the scar is not so deeply excavated. " The depth of the scar consequently depends on the degree and duration of the flattening of the base of the pock beneath the pustule and the scab, and we see therefore that the rational treatment to avoid scars should be mainly directed to the aborting of the pustular stage and the rapid removal of the scab by profuse epithelial new-growth. . . . . Suppuration alone causes no necrosis of the papillary body, but it may, if profuse, lead to a more rapid casting off of the scab, and thus indirectly to the freeing of the base of the pock; the profusely suppurat- ing cases of smallpox are not those which leave the worst scars. No doubt prolonged suppuration, coupled with inappropriate treatment, scratching, etc., may lead in many cases to a purulent sequestration of parts of the cutis and thus to distinct scar formation." For a long time the bloodvessels and all the lymph spaces of the cutis are dilated, and wandering cells and pigment are more abundant than normal. The pocks upon the 'palms of the hands and soles of the feet develop in a somewhat difi^erent manner from those elsewhere. The reticulating and ballooning degenerations are only imperfectly seen here. The "pock body" is usually fan-shaped, undergoes a drier degener- ation, and has a horny character. It is usually more superficially situated in the epidermis. Stokes^ believes that "the primary exudation of plasma cells has not been sufficiently emphasized by Unna. These plasma cells are probably derived in part from proliferation of the endothelial lining of the lymph spaces and bloodvessels. In some sections made from very early cases, the epithelial cells do not show any great injury, but the cutis 1 The Palliology of Smallpox, Johns Hopkins Bull., Xo. 1-19. Aug., 1903. 246 SMALLPOX is swollen and there is increased number of plasma cells in the lymph spaces and around the small bloodvessels. The condition resembles the response to some injury and seems to be the first change in the skin, since the various changes in the epithelial cells are not yet present." In a hemorrhagic case Stokes found the capillaries and lymph spaces greatly distended and numerous hemorrhages present in the connective tissue. Quite recently careful and extended studies of the pathology and etiology of variola have been carried on by Prof. Councilman/ of Harvard College, and a number of his associates. The anatomy and histology of variolous lesions were investigated by Councilman, Magrath, and Brinckeroff. Eight sets of complete serial sections were made through typical vesicles and pustules. In the main Unna's findings are confirmed, but some new facts concerning the histology of the pock are presented. The earliest form of degeneration is said to take place in the nuclei of the cells of the rete mucosum. They become swollen, more vesicular, and exhibit an increased central clumping of the chromatin. In the lesions leading to vesicle formation there is a reticular degeneration of the cytoplasm, with a more advanced degeneration of the nucleus. The nuclei may lose their form and become irregular and shrivelled, assuming peculiar shapes. Advanced forms of cytoplasmic inclusions are common in the nuclear space and in vacuoles in the protoplasm. The proto- plasmic processes connecting the cells disappear, but the periphery of the cells remains and undergoes condensation. It is this degeneration which causes the peculiar reticular appearance of the early vesicle. It is always better seen in the periphery than in the centre of the vesicle. With the increase of the exudate coming from below, the spaces within the cell enlarge, finally rupture, and a network is formed by the coalescence of the cell borders. The typical small vesicle is always fan-shaped, with the handle of the fan seated upon the corium. A later form of degeneration, the ballooning degeneration of Unna, may best be regarded as a hyaline fibrinoid degeneration. The Mal- pighian cells become swollen, lose their granular character, become homogeneous and refractile, and stain more intensely with the acid dyes. The fluid exudate begins early, and in most cases simultaneously with the degeneration. In the smallest visible papule the swelling is due chiefly to the presence of exudate; in no case was degeneration found without evidence of exudation. The early exudate is clear and contains no admixture of cells. Indeed, a conspicuous feature of the smallpox process everywhere is the paucity of cells in the exudate. The cells appear only at a late stage of the process, and are much less than in other deo:enerations and exudations due to bacterial infection. 1 Studies on the Pathology and Etiology of Variola and Vaccinia ; from the Sear Pathological Laboratory, Harvard Medical School ; published in the Journal of Medical Research, February, 1904. THE IWTIIOI/XIY OF SMALLPOX 247 It seems probable that tlie cells appear when the ^m-W'w cli.'inu-ter of the process is passed, they being then attracted to the necrosis. Did'erent viirictics of leukocytes are present, but the polynuclcir neutro- nhilcs prcaler than normal. Nearly all writers refer to degenerative changes in the liver varying from cloudy swelling to a more or less intense fatty deceneriition. Weigert descrihes areas of local coagidation necrosis in which are seen nuclear detritus and many degenerated cells without nuclei. Siderey says there is intense congestion with migration of white blood corpuscles and swelling of the endothelial lining of the capillaries; later the liver cells swell and undergo fatty degeneration. Roger and (larnier' made a microscopic study of the liver in seventeen smallpox cases. They conclude that variolous hepatitis is usually total and may affect the interstitial or parenchymatous tissue. P'atty hepatitis is said to be the most common, having been found in six out of eleven cases of coherent or confluent smallpox. In hemorrhagic smallpox, it is, according to these investigators, constant. Necrotic hepatitis is more rare and is characterized by cellular necrosis in limited foci or diffuse bands. This condition was observed alone in two cases, and in two others associated with fatty degeneration. A third variety, hemorrhagic hepatitis, was found in one case in a child with congenital variola. Ponfick and Curschmaim both state that in purpura variolosa the liver is normal in size and color and does not exhibit the degenerations above referred to. According to Ponfick,^ the spleen in those who die early is swollen, soft, and of a light-red color. It later resumes its normal appearance except in purpura variolosa, in which variety it is small, hard, and dark red, with prominent follicles. Roger and WeilP found the spleen hypertrophied in every one of sixteen fatal cases of confluent smallpox. Among twelve hemorrhagic cases it was enlarged in four instances. The most interesting micro- scopic changes are the presence of nucleated red blood corpuscles, and a predominance of mononuclear leukocytes among the white cells. Perkins and Pay^ noted hemorrhages into the splenic pulp in six out of forty autopsies; three of these were cases of purpura variolosa. The kidneys, like the liver, show changes var^nng from cloudy swelling to fatty degeneration. Arnaud^ made histological examinations of the kidneys in thirteen cases of smallpox. The changes were briefly of two types — an interstitial cell infiltration and lesions of the epithelium of the tubules. Stokes" has recently made a careful study of the kidneys in variola. ' Etude aiiatom. et cliim. du foie dans la variole, Archiv. de mOd. exper., September, 1901. - Ueber die Auat.Veriinderungen der iiinern Organen bei bemor. u. pust. Variola, Berl. klin. Woch., 1872, No. 42. ^ Les maladies infectieuses, Paris, 1902. ■* Tbe Etiology and Pathology of Variola, Journal of Medical Research, October, 1903. 6 Revue de m^d., 1S9S, tome xviii. p. 392. ^ Loc. cit. 250 SMALLPOX Extensive changes were found in every kidney examined. In one case an acute interstitial nephritis such as described by Councilman in diphtheria and scarlet fever was found. In one very malignant case the changes noted Avere as follows: In the glomeruli the capillaries contained clear hyaline material within the lumen. This was due to an actual degeneration of the endothelial lining of the glomerular capillaries. At times the hyaline material formed a large crescentic mass of homogeneous clear material in the capsular space. The epithe- lium of the convoluted tubules was swollen and the cytoplasm of the cells contained numerous granules. In many of the cells the cytoplasm had completely degenerated into a mass of clear droplets which pro- duced hyaline casts in the lumen a of the tubules. The clear droplets took Weigert's stain for fibrin. The adrenal bodies were found by Perkins and Pay^ to frequently show well-marked fatty degeneration of the cells of the medulla. The heart in fatal cases of confluent smallpox is usually relaxed, soft, and somewhat enlarged. Microscopically the changes are those of cloudy swelling and fatty degeneration; fragmentation of the muscle fibres is commonly seen. In purpura variolosa, according to Ponfick, the organ is firm, con- tracted, and of a brownish-red color. The Lymphatic Glands. — Roger and WeilF state that hypertrophy of the glands in variola follows the same rule as splenic enlargement; it is very marked in the pustular variety and slight or absent in the hemorrhagic form. Microscopically the cells found are similar to those seen in variolous bone-marrow; neutrophile myelocytes are notably present and in addition there are some basophile myelocytes and occa- sionally eosinophiles. Giant cells are also seen, and in hemorrhagic smallpox nucleated red blood corpuscles. Stokes examined the cervical and bronchial glands in smallpox and found extensive focal necrosis containing an abundance of streptococci. Bone-marrow. — In 1873 Golgi^ made a study of the bone-marrow in ten cases of pustular and twenty-five cases of hemorrhagic smallpox. In the pustular form he found a great increase of the white cells, while in the hemorrhagic variety he found a great increase of nucleated red cells, a distinct diminution of the white cells, some of which were in process of fatty degeneration, and diffuse hemorrhages in the medul- lary spaces. The medullary tissue was red and almost as fluid as blood. Chiari* found a condition which he designated "osteomyelitis vario- losa" in 72 per cent, of twenty-two cases examined. This process is characterized by pea-sized, whitish, grayish, or yellowish nodules, widely disseminated in the marrow substance. These consist of epithelioid cells derived from proliferation of the marrow cells. An early necrosis 1 Loc. cit. - Maladies infectieuses, p. 721. ■* Sulle Alterazioni del Midollo del ossa nel variola, Rlvisla clinica di Bologna, 1873, p. 238. * Osteomyelitis Variolosa, Ziegler's Beitriige z. pathol. Anat. u. allgemein. Pathol., 1893, Bd. xiii., S. 13 ; and Zeitschrift f. Heilkunde, Bd. vii., S. 385. 77//'; PATIIOhOaV OF SMALLI'OX 251 sots in. C-liiiiri rcf^iii-ds these focjil nenr()S(!S us (lu(; to tlic sj;ccifi(; vari- olous ])oisoii. (!oiinnont and Montiii/)aY of smallpox 261 vaccine lesions, the lyni])h of which gave tyj)ical vesicles when tnms- I'erred to children. C'opeman admits that the results of these interesting exjxuirnents are rendered inconchisive by the fact that the calves cin[)loycd were inocu- lated elsewhere upon the body with ordinary vjiccinc lynijjh; every precaution, however, was taken to prevent c(jntaniination of the defined area inoculated with the egg cuUure. In later experiments Copeman and IJlaxall succeeded in growing the small bacillus on other culture media. In 1900 Nakanishi^ isolated a bacilhis from liuman and bovine vaccine lymph to which he gave the name of "bacillus variabihs Iym[)ha' vaccinalis." This organism belongs to the pseudodi})hthcria group and exhibits great variations in size and form. Inoculation of the cornea of rabbits with cultures of this bacillus produced bodies in the epithelial cells which were said to closely resemble the cytorrhyctes variola; of Guarnieri. In the same year Levy and Finkler^ independently described a l^acillus found in vaccine lymph which they designated "corynebacterium lymphse vaccinalis." This organism belongs to the pseuflodiphtheria class and is probably identical with that described by Nakanishi. Cause of Pustulation in Smallpox. — It is quite definitely estalilished that the suppuration of the variolous pock is the result of the causative agent of the disease and is not due to secondary infection with pyogenic organisms. In the vesicular and even in the early pustular stage of the eruption the lesions will commonly be found to contain no bacteria cultivable upon ordinary media. In an investigation of the contents of smallpox vesicles and pustules' we found 33 out of 34 cultures of lesions before the seventh day sterile. Frequently a drop of pus from a lesion was placed upon a nutrient medium and incubated without any visible growth developing whatsoever. In all, cultures were made from 82 lesions in 51 cases of smallpox; of this number 64 cultures remained absolutely sterile. This work is in accord with most of the investigations upon this subject. Perkins and Pay* made 30 cultures from typical variola lesions at all of the various stages from the beginning vesicle to the full develop- ment of the ripe pustule. These were all negative with the exception of 4 — 1 on the eighth day, 1 on the ninth, and 2 on the tenth days of the eruption. After the seventh or eighth day of the eruption various bacteria, chiefly streptococci, may be found in the lesions. The Streptococcus Pyogenes in Smallpox. — The streptococcus is commonly found in the late pustules of smallpox and in many of the cutaneous complications, such as boils, impetigo, abscesses, erysipelas, gangrene, etc. 1 Centralbl. f. Bakt. u. Parasit., 1900, Bd. xxvii. - Deutsche med. Woch., June 2S, 1900. 3 A Preliminary Study of the Contents of Variolous Vesicles and Pustules, Journal of the Ameri- can Medical Association, 1903. * Journal of Medical Research, October, 1902. 262 - SMALLPOX After death streptococci are found in the cutaneous lesions and in the blood and internal organs in nearly all cases. There would appear to be in many cases an agonal or post-mortem diffusion of streptococci throughout the, tissues. In 40 autopsies on smallpox patients made by Perkins and Pay streptococci were found distributed throughout the body of 38. Ewing^ found streptococci present in about 90 per cent, of the skin lesions cultured at autopsy. He also noted the presence of streptococci in the blood after death in every one of 29 cases examined. In 10 cases of varying severity in which the blood was cultured during life the results were negative. Ai'naud^ found streptococci in the blood during life in 2 cases of hemorrhagic smallpox. Perkins and Pay^ examined the blood in 20 cases of smallpox and found streptococci in 11 cases, before or just after death. Omitting the varioloids and convalescents and considering only the more serious cases, a total of 16, with streptococci in 11, or 69 per cent. It is evident from the above investigations that the streptococcus is almost constantly found in fatal cases of smallpox. While no one can seriously entertain the idea that its role in smallpox is causal, it is so uniformly present that some writers believe it bears a peculiar relation to the disease differing from most secondary infections. It should be remembered, however, that the same statement might be made with equal force in referring to the relationship between the streptococcus and scarlet fever. Many writers regard the streptococcic bacterisemia as the most frequent cause of death in smallpox. Councilman* says: "As the result of the study of the disease, both by culture of the lesions and organs and by microscopic examination of tissues, we are inclined to regard bacterial infection as a more important agent in bringing about a fatal termination than the specific parasite The bacteria are chiefly strepto- cocci." Perkins and Pay, and likewise Councilman, suggest that the strepto- cocci gain entrance to the circulation through the bronchial and pul- monary mucous membranes. Perkins and Pay found that the pathogenicity of the streptococci isolated was markedly different. Some of the strains killed rabbits in two or three days, while others were without effect. The writers suggest that the failure of antistreptococcus serum prepared from one variety of streptococcus may be thus accounted for. Protozoa in Variola and Vaccinia. — Griinhagen^ in 1872 appears to have been the first to call attention to the presence of protozoa in variola and vaccinia. He described in vaccine lymph, clear, refractive, sharply contoured bodies both free and attached to leukocytes. 1 Proceedings of the New York Pathlogical Society, May, 1902. 2 Rev. de m^d., 1900, p. 303. ^ loc. cit. * Journal of Medical Research, February, 1904, p. 358. 5 Bemerkungen Ueber den InfeclionstoflF der Vaccin Lymphe, Arch. f. Dermat. u. Sylph., 1872, p. 150. 77//'; i:.\(;ti<:i!I()I.(i(;v of smallpox 2r;.'i Renault in JSSI described j)e('iiliur Ixxiics which he hchc\cd lo lic parasites in the epithelial cells of variola and vaccinia. In ](SS7 Van ^qv LoefP found in a han^inf^ drf)p of clear vaccine; lymph numerous small, round bodies endowed with arno-bf^id nu>vement; later he discov(!r('d the s;ime bodies in smallpox pustules. L. Pfeill'er pul)lished a series of papers be^^iiminf; in 1887, desciibin^ the presence in variolous and vaccine lymph of the "monocystis epithe- lialis," a small, unicellular, rounded body which he re<^jirfled as the specific cause of smallpox. These bodies were also found in the epithelial cells of the Mal|)i<^hian layer and were said to multiply by division ann- founded with smallpox. The eruption at times may appear rather sud- deidy and j)ass throufijh the stages of papule, vesicle, and pustule in a surprisingly brief period of time. The lesions may be quite firm to the touch and in other respects closely simulate those seen in smallpox. In syphilis one can fre(|uently obtain (1) a hittory of injcrtion and a description of the initial lesion. Indeed, the chancre or its remains may still be detected. Not uncommonly there are present associatfjd evidences of syphilis, such as mucous patches, flat condylomata, ulcer- ation of the tonsils, alopecia, glandular enlargement, etc. The variola- form syphilide may develop after the disappearance of one of the earlier syphilitic eruptions. 2. The onset of the two diseases is, as a rule, quite different. The syphilitic subject will usually give a history of having felt weak and debilitated for some weeks. If fever precedes the eruption it is ordinarily not very high and is not accompanied by severe prostration. When the eruption appears the patient usually calls upon the physician at his office or at the hospital. We do not note that sudden illness which precedes unmodified smallpox. In the latter disease, two or three days before the efflorescence appears, the patient experiences a chill followed by a rise of temperature, often to 103°, 104°, or 105° F. There are severe headache, backache, vomiting or nausea, vertigo, general pains, and severe prostration. The patient, instead of calling upon the physician, sends for him. It must be remembered, however, that in varioloid the initial symp- toms may be mild or absent. On the other hand, in rare cases, syphilis may present an initial illness which strongly counterfeits that of smallpox. 3. The development of the eruption in smallpox is rather sudden. Ordinarily in twenty-four to forty-eight hours the full complement of lesions has appeared. In syphilis the eruption may continue to come out for quite a number of days in successive crops. It must be admitted, however, that in modified smallpox three or four days may sometimes elapse before the complete appearance of the exanthera. 4. The distribution of the variolaform syphilide may be identical with that observed in smallpox. Frequently, however, variations may be noted. The pustular syphilide may involve the trunk more copiously than the face; this would be exceedingly rare in well-marked smallpox. The dorsal surface of the wrists and hands are nearly always involved in smallpox, but may escape entirely in syphilis. The palms of the hands and soles of the feet are always involved in severe smallpox; in moderate eruptions they nearly always present some lesions, and in varioloid they may or may not escape completely. The pustular syphilide, on the contrary, attacks the palmar and plantar surfaces with the greatest rarity. The writers have observed in one case a single lesion 272 SMALLPOX upon the palm of one hand, and in another instance a deep-seated pustule upon the lateral surface of the sole. 5. The character of the eruption in syphilis and smallpox may, in the beginning, be so nearly identical as to make a diagnosis from the eruption alone quite impossible. It will be noted, however, that the efflorescence of smallpox presents a much greater uniformity in the character and development of the lesions over the body than does syphilis. Syphilis is characterized by an essentially multiform erup- tion; it is not uncommon to find small pustules, large pustules, and papules interspersed, and these in varying stages of evolution and invo- lution. The vesicles and pustules of syphilis are usually conical and involve merely the summits of the elevations; they never become full and globular, and fill the entire lesion as do those of smallpox. Beneath the syphilitic crusts considerable ulceration not uncommonly occurs; according as this is slight or severe there will be seen, upon detachment of the crusts, a small, reddish-brown pigmented stain or an excavated ulcer. The latter heals with the production of a depressed scar. 6. The course of the syphilitic eruption is relatively chronic compared with that of smallpox. The lesions of variola undergo a striking change in a few days. The syphilitic efflorescence is indolent, and presents, as a rule, no decided alteration of appearance within this period of time. By the sixth or seventh day in smallpox the lesions develop into those large, full, round, hemispherical pustules which are so characteristic of the disease. Finally, to the physician who has seen much of smallpox, there is a something in the picture, an impression given by the ensemble, which, while not definable in language, is, nevertheless, of subtle aid in the diagnosis. Roseola Vaccinosa. — Vaccination with animal virus sometimes causes an erythematous or rubeoloid rash, known as roseola vaccinosa, to appear from the eighth to the twelfth day of the vaccine disease. We have occasionally known this rash to have been mistaken for the eruption of variola, especially during epidemic visitations of the disease. The distinguishing features are that it accompanies vaccinia, that it is not preceded by a very high temperature, and that it consists of macules rather than papules. Acne. — Mild cases of varioloid exhibiting but a few papulopustules about the face may bear a close resemblance to acne. The history of exposure, the existence of an initial stage, and the progressive evolution of the lesions will speak for the variolous nature of the eruption, while the presence of blackheads, a history of previous outbreaks in the individual, and the absence of preceding illness will decide in favor of acne. Drug Eruptions. — Drug eruptions, particularly those resulting from the ingestion of the iodides and bromides, may simulate the exanthem of smallpox. The history and absence of an invasive stage will usually suffice to make the diagnosis clear. 77//'; I'lKXlNOhllH, OF SMALIJ'OX 275 variola,. C'ontrariwise, in (lie ah,sciif;o of an cpidfinic miM fasf.s of ,sinall|)ox are very likely to be overlooked. Whenever the diagnosis between smallpox and a disease simulating it is in doubt, observation of the progress of the eru[>tion for a perifKl of twenty-four to thirty-six hours will tisnally make elear the nature of the disease. THE PROGNOSIS OF SMALLPOX. Since tlie introduction of vaccination the presence or absence of a typical vaccine scar on a })atient is an important factor in the question of prognosis in smallpox. Formerly, smallpox was not only more common, but uniformly far more fatal, and therefore nnich more dreaded than at the present time. During the last century but few diseases claimed a greater number of victims than variola, but at the present time, especially in countries where vaccination is carefully and systematically practised, the pro- portion of deaths from this malady is not greater than 0.7 per cent, of the entire mortality, and where revaccination at the proper age is also enforced, this proportion is even much less. In the prevaccination period one-tenth of all the children born died from smallpox; now the mortality from that disease among young children where vaccination is compulsory is almost nil. According to Juncker smallpox killed in the prevaccination days on an average 400,000 persons every year in Europe. In 1803 King Frederick William III., of Prussia, stated that the average yearly mortality rate from smallpox in Prussia was 40,000. In Prussia, where vaccination and revaccination are rigidly enforced at the present day, smallpox is almost unknown. Age. — The age of the patient is of the greatest importance in con- sidering the prognosis of smallpox. It is comparatively rare for an infant under one year of age to survive an attack of unmodified small- pox. So also at the other extreme of life the death rate is excessively high. In children of from one to five years of age the disease is also very fatal, but among those of from five to fifteen years the chances of recovery are rather better than in adult life. Smallpox Patients Treated in the Municipal Hospital, showing MoETALiTY According to Age. series i. Age. Cases. Died. Percentage. Under 1 year 60 37 61.66 1 to 15 years :-30 187 35.28 15 " 25 " 1362 402 29.51 25 " 45 " 1215 365 30.04 45 years and upward 227 88 38.77 Total 3394 1079 31.79 276 SMALLPOX ' ] SERIES II. (Similar table with somewhat different age classification ) Age. Cases. Died. Percentage. Under 1 year 57 29 50.87 1 to 5 years 159 50 31.45 5 " 10 " 130 20 15.38 10 " 15 " 66 8 12.12 15 " 25 " 371 55 14.82 25 years and upward 1096 172 15.69 Total 1879 334 17.80 The above tables give the smallpox mortality according to age, and include both the vaccinated and the unvaccinated cases. All of the patients under one year of age were unvaccinated except a few who were vaccinated after infection — i. e., during the incubation period. Likewise, practically all of the children under five years of age were unvaccinated. In Series I. are included the statistics of the large and malignant epidemic of 1871-72, and of a subsequent severe epidemic; while in Series II. are included the statistics of the recent and much milder epidemic of 1901-02. Race. — When smallpox prevails among aboriginal tribes the mortality is extremely high. It is commonly stated that the death rate of variola among negroes is much higher than among whites. This statement has scarcely been borne out by our experience. Negroes are extremely negligent as regards vaccination, and the number of unvaccinated blacks received in smallpox hospitals is apt to relatively exceed the number of unvaccinated whites. A truer comparison of mortality rates will be obtained, therefore, in contrasting the unvaccinated of both races. In the tables here shown, the mortality rate among the negroes is somewhat higher than among the whites, although the difference is not great: Negroes and Whites Admitted to Municipal Hospital. Cases. Deaths. Percentage. White 6131 1530 24.95 Black 1073 407 30.79 Total .... 7204 1937 2689 Unvaccinated Negroes and Whites. Cases. Deaths. Percentage. White 2036 910 44.69 Black 637 315 49.45 Total .... 2673 1225 45.83 Sex. — Sex influences prognosis to little or no extent. Among women the mortality is somewhat increased on account of their liability to suffer from metrorrhagia, or, when pregnant, from miscarriage or premature delivery. The occurrence of either of these accidents or the presence of the parturient state strongly predisposes the patient to the hemorrhagic form of the disease. The mortality 77//'; rnoaNosrs of sma LLpr)X 277 in men is, on the other hand, considerably increased by intemperance. Drunkards or constant imbibers seem particularly prf»nc to suffer Itoiu licmorriiiif^ic; sniall])OX. We have found jdrnost all forms of the disease more severe amonff bartenders, "^'lie powers of resisfanrc against the exhausting influence of variola are often so diminished by chronic alcoholism that death results from a form of the disease from which a |)ati(Mit with more healthy organs would recover. Mania a, polil constitutes, of course, a very serious foniplif.'ition. In- temperate persons are apt to be badly nourislu-d, .'ind Ihis conrliliou is always unfavorable in smallpox. It will be seen from the subjoined Ijible (iiiil I he inorljility rate jimf»ng males and females in our experience has been almost the same: Cases and Mortality According to Sex. Cases. Deaths. Percentage. Male 4593 1207 27.45 Female 2606 670 25.71 Total .... 7204 1937 26.89 Unmodified smallpox is an exceedingly fatal disease, the death rate varying in different epidemics from 15 to 60 per cent. The epidemic which swept over this and other countries in the years 1S70 to 1872 was everywhere characterized by unusual malignancy, and the mortality among the unvaccinated cases was, in some places, as high as 64 per cent. The following table shows the mortality rate among vaccinated and unvaccinated cases treated in the Municipal Hospital during the three largest epidemics experienced since its foundation: Mortality Eate of Vaccinated and Unvaccinated Cases in Different Epidemics, Cases. Deaths. Percentage. 1871-1872. Unvaccinated . . 697 449 64.41 Vaccinated . 1629 276 16 94 Total . . 2326 725 30.74 1881-1885. Unvaccinated . . 447 252 56.37 Vaccinated . . . . 551 81 14.70 Total . 998 333 33.36 1901-1904. Unvaccinated . . 1943 636 32.73 Vaccinated . 1844 124 6.72 Total .... 3787 760 20.06 It will thus be seen that different epidemics vary very greatlv in malignancy. In 1901-04 the mortality rate among the unvaccinated was just one-half that observed in 1871-72, and almost one-half less than the death rate in 1881, Indeed, smallpox may occur in epidemics in which the death rate reaches as low a figure, even among unvaccinated cases, as 2 per cent. Such a remarkable epidemic has been prevailing in various sections of the United States during the past few years. In the absence of an epidemic influence, smallpox is usuallv much 278 SMALLPOX less fatal. It is believed by some authors that the disease is more fatal at the beginning and during the maximum of an epidemic than when it is declining, but we are not sure that such is always the case. Certain seasons of the year are also believed to exercise some influence over the mortality from the disease. It is probably true that a patient is less able to bear the depressing effects of confluent variola when the weather is excessively hot than when the temperature is cooler. Type of Disease. — In considering the prognosis in individual cases various circumstances are to be taken into account. The type of the disease and the extent and depth of the eruption are among the most important factors. The hemorrhagic form of smallpox is frightfully fatal. Indeed, it may be laid down as a rule almost without exception that recovery never takes place from the graver types of this disease. Of 152 cases of hemorrhagic smallpox observed during the epidemic of 1871-72, 146 died. The 6 cases that recovered belonged to the milder variety of this type; 1 had slight bloody vomit, and the other 5 exhibited an eruption which on some parts of the body was purplish, while a number of vesicles contained a dark-blue spot in the centre, showing that blood was exuded into the vesicles. The next most fatal form of smallpox is the confluent variety. When it is comprehended that in such cases there may be forty thousand or more pustules present, the reason for the high death rate is apparent. Of 211 cases of confluent smallpox accurately observed during the epidemic of 1871-72, 168 died, showing a mortality rate of 79.62 per cent. Semiconfluent cases are correspondingly less fatal than the confluent; while in cases with discrete eruptions the mortality falls to a compara- tively low level. Thus it will be seen that the prognosis in any particular case is influ- enced to an enormous extent by the character of the eruption. In varioloid or smallpox so modified by vaccination, inoculation, or previous attack that the secondary fever is slight or absent, the mortality is almost nil, as will be seen from the appended table: Vakiola and Varioloid Treated in the Philadelphia Municipal Hospital. Cases. Deaths. Percentage. Variola 4156 1906 45.93 Varioloid 3048 31 101 Total 7204 1937 26.89 The fatalities in' varioloid result, as a rule, from some complicating condition. It must be remembered that attacks in adult patients who were vaccinated in infancy and showed no appreciable protection are classed under the head of variola. The stage of the disease at which death occurs in smallpox will depend somewhat upon the character of the attack. Patients suffering from hemorrhagic variola usually succumb on the fourth, fifth or sixth day of the eruption. Considering all types of the disease the largest 77//'; f'U()(,'N()SlS OF SMALLPOX 270 number of fatalities occur during the second week of the eruption and particularly upon the ninth, tenth, and eleventh days. As will be seen in the accompanying table, of 1019 fatal cases of sn)all[)ox, 575, or 50.42 per cent., died during the second week, and .'M7, or .':)4.05 percent,, of these exj)ired on the ninth, tenth, and eleventh days. Basing the assertion u[)()n these figures, it may be stated that over one-third of the fatalities occur upon the critical days mentioned, and over one-half of the deaths during the second week. We have occasionally observed death to take place as late as five or six weeks after the onset of the disease, but in these cases the unfavorable termination has been brought about by some complicating affection. Showino the Period of the Disease at which 1019 Cases of Smali.i-ox Proved Fatal. First week : Isl day of ernptinn 1 2d "" " 4 3d " '• 14 4th " " 31 5th " " 63 6th " " 90 7th " " 90 — 293 Second week : 8th day of eruption 84 9th " " 122 10th " " 114 11th " " 101 12th " " 75 13th " " .49 14th " " 30 — 575 Third week : 15th day of eruption 28 16th " " 22 17th " " 12 18th " " 9 19th " " 5 20th " " 8 21st " " 7 — 91 Fourth week and after: 22d day of eruption 7 23d " " . 8 24th " " 6 25th " " 3 26th " " 4 27th " " 3 28th " " 5 29th " " 4 30th " " 4 31st " " 2 32d " " 4 33d " " 1 34th " " 2 35th " " 1 36th " " S 37th " " I 39th " " 1 44tll " " 1 ' — 60 Total 1019 280 SMALLPOX Vaccinal Condition. — ^The vaccinal condition of the individual is a most potent factor in influencing the course of the variolous disease. The degree of protection conferred by the vaccine process can be, in most cases, approximately estimated by the character of the vaccine cicatrix. Every now and then we encounter patients with good vaccina- tion scars from an infantile vaccination, in whom the protection against smallpox has been almost completely lost; and, on the other hand, we may see patients with poor scars who still enjoy considerable protection; but these may be looked upon as exceptions to the general rule. The existence, therefore, of good cicatrices in a patient who is attacked with smallpox may be regarded as of favorable prognostic import. Of 8893 cases of smallpox treated at the Municipal Hospital, 2335 presented good scars; of this number, 152 died, constituting a mortality rate of 6.5 per cent.; 1105 patients with fair scars were treated, of whom 135 died, showing a death rate of 12.21 per cent.; 1524 cases were admitted with poor scars, of whom 345 died, giving a death rate of 22.64 per cent.; 3687 unvaccinated cases were admitted, of whom 1542 died, giving a mortality rate of 41.82 per cent. Thus it is seen that the danger of attacks of smallpox can be measured with a con- siderable degree of accuracy by the vaccinal condition of the patient. Vaccinal Condition and Mortality Rate. Admitted. Died. Percentage. Vaccinated in infancy (good scars) . . 2335 152 6.5 (fair " ) . . 1105 135 12.21 (poor " ) • • 1524 345 22.64 Postvaccinal cases 4964 632 12.53 Unvaccinated " 3687 1542 , 41.82 Unclassified " 242 45 18.18 Total .... 8892 2219 24.95 There is no reliable symptom during the initial stage to indicate the gravity of the attack. Not infrequently the mildest eruption of varioloid is preceded by a very severe febrile stage. If, however, the initial stage be very mild, it is safe to prognosticate a moderate eruption. Severe lumbar pains may be present both in modified and unmodified smallpox, yet if they be extremely severe there would be some reason to anticipate a hemorrhagic form of the disease. Inasmuch as the initial morbilliform exanthem {roseola variolosa) is most often seen in varioloid, we would regard the presence of this rash as an indication that the true eruption will be of modified form. When the rash is of the scarlatiniform type, the ensuing eruption may be moderate or severe; when, however, the prodromal rash is purpuric, it is a symptom of evil portent, preceding as it does the hemorrhagic form of the disease. There are, however, exceptions to this last statement; we have occa- sionally seen erythematopurpuric prodromal rashes in persons who have made perfectly good recoveries. It has been already stated that the quantity and character of the eruption are accurate guides as to the gravity of the disease. The riii<: I'ttOGNOSis of sma/jj'hx 281 condition of the nnicous membrane of the [)[),'uynx, hirynx, and traeliea should he regarded as only second in in)j)(jrtance to the skin lesions in estimating the degree of danger in variola. If these parts become severely im])licated by the variolons f)rocess, giving rise to a fliphtheritir condition of the fances, (lys[)hagia, difhculty of res})iration, or ademji of the glottis, the case shonld be viewed with grave ap|)rehensif>ii. Even hoarseness at the early period of the rnaturative stage shonld be looked npon with suspicion. Favorable Symptoms. — As has })een stated, mild initial manifesta- tions and the occurrence of a roseolous rash are favorable, inasnnich as they precede, as a rule, mild forms of the disease. Even in profuse eruptions, if the pustules become prominent and acuminate well, and are accompanied by considerable swelling, and if those on the extremities are surrounded l)y a pinkish areola, and the patient takes nourishment freely, there is good ground for hope. At a more advanced ])eri(Kl of the disease, if the state of the nervous system be tranquil and the patient passes quiet nights, has a contented disposition, and entertains a confi- dent hope of recovery, the probal)ility of a favorable termination of the disease is greatly increased, even though the eruption be severely confluent. Unfavorable Symptoms. ^ — Among the symptoms which indicate the approach of a hemorrhagic attack are: excruciating backache during the initial stage, a petechial prodromal rash in the axilla and groins, sub- conjunctival ecchymoses and hemorrhages from the various mucous membranes, a claret-colored areola about the lesions upon the extremi- ties, and a bluish or lead-colored discoloration of the centres of the vesicles. The prognosis in a case presenting such symptoms would be almost hopeless. An excessive degree of confluence on all parts of the body renders the prognosis extremely grave. It is an unfavorable sign in confluent cases if the pustules on the face be flat, milky-white in color, and pasty, and if there be absence of sweUing. It is also ominous to see here and there on the face vesicles desiccating prematurely and producing flat, brownish scabs. During the early period of maturation the patient's condition should be regarded as extremely critical if the progress of the eruption be suddenly arrested and the swelling of the face and hands subside, leaving the skin between the pustules pale; if the pustules themselves shrink and collapse; if the pulse be rapid, dicrotic, or feeble; if the delirium and restlessness increase; or if nourishment be refused or taken very reluctantly. Valuable information may often be gained by observing the nervous symptoms, especially at an advanced period of the disease. Great restlessness, insomnia, despondency, constant moaning and grindmg of teeth in children, are unfavorable symptoms. Violent and protracted delirium, convulsions, or coma usually preclude all hope of recovery. Even after the patient has passed safely through the perils of the regular stages of variola, his life may again be placed in jeopardy by 282 SMALLPOX certain complications. Fortunately, those which are most frequent — furuncles and abscesses — rarely lead to a fatal issue. The occurrence of pneumonia, pleuritis with effusion, erysipelas, or abortion should be viewed with deep concern. But the most fatal of the complications liable to arise are suppuration within the joints, pyaemia, and empyema. Gangrene of the scrotum and glossitis variolosa arising earlier in the course of the disease usually portend a fatal outcome. THE TREATMENT OF SMALLPOX. The treatment of smallpox may be considered in its relationship, first, to the patient himself, and, second, to the community at large. The latter aspect of the subject concerns the prophylaxis or preventive treatment of the disease. This may be conveniently classified under the following captions — notification, isolation, surveillance or quarantine, disinfection, and vaccination. Prophylaxis. Notification. — It is important in the interests of public health that the existence of a case of smallpox should be promptly made known to the proper health authorities. It is usually the duty of the physician in attendance to transmit this intelligence. Every practitioner of medicine should feel himself called upon to aid and sustain the sanitary authorities in their efforts to prevent or stamp out a pestilential disease and should willingly comply with any arrange- ments whose object is the attainment of so desirable an end. Most large communities have enacted laws making compulsory the notification of smallpox and other pestilential diseases, under pain of fine or imprisonment. It is only through a knowledge of the distribution and extent of smallpox in an infected district that the health authorities are enabled to intelligently and efficiently inaugurate measures toward its suppression. Isoiation.^ — It is of paramount importance, when smallpox appears in a community, to prevent the dissemination of infection; to this end the isolation of the patient — the source of the infection — becomes essential. This can only be accomplished with any degree of certainty by having the sick removed to a well -organized hospital. General hospitals and other public institutions cannot, with justice to the other patients or inmates, harbor and treat those suffering from smallpox. Even the caring for such patients in isolated pavilions in general hospitals is open to the objection of multiplying the foci of contagion in the city or town. It follows, therefore, that every city and large town should be provided, either temporarily or permanently, with a special institution for the treatment of this disease in the event of its outbreak. It should be located in a healthful district, sufficiently removed from the thickly settled portions of the city to preclude the possibility of transmitting the contagion to inhabited domiciles, but not so remote as to interfere with its accessibility. It is also of importance that such institutions should be constructed in a modern manner, with a view to making the unfortunate patients as comfortable as possible. TIII<: TliNATMHNT OF >SMALLPOX ^HP, Of course, a special hospital of this character should he rnanagefi under strict quariuitine regulations. No person, however well protef:ted, should be allowed to visit a patient in the institution (;xce[)t under extreme circumstances, and then only after every possible precaution shall have been taken to prevent his carrying away the infection. The nurses and attendants should not be allowed to leave the hospital, nor come in contact with other persons, until they have had an antiseptic bath and have chanfrcd their infected clothing. In j)roviding nurses and other employ(5s for the hospital it need not be required that they shall have had smallpox, but they should invariably be vaccinated or revaccinated before entering upon duty. When delay is possible it is wise to await the result of such vaccination before the individual is brought into the infected atmosphere. The hospital should be supplied with closed ambulances for the transportation of patients. Private or public vehicles should never be used for this purpose. Indeed, this is regarded as so important a matter that in some large cities in this country the use of any kind of public conveyance for carrying persons afflicted with smallpox is prohibited by law, and its infringe- ment is made punishable by fine. Lest infection be spread by the ambulance itself it should be dis- infected and provided with clean bedding, blankets, etc., every time it is used. In order that the public may know the character of the disease that it conveys, it should bear the name of the hospital to which it belongs. If the smallpox patient is to be treated at home, every possible effort should be made to seclude him from all persons, excepting only such as are required to act as nurses, and they should be protected by recent vaccination. In selecting the apartment for the patient, a room most completely separated from all other parts of the house is to be preferred. If this is not practicable — which is usually the case in the ordinary city residence — the uppermost room of the house should be preferred. It should be well ventilated, and, if possible, have an open fireplace in which fire should be kept constantly burning. All unnecessary articles of furniture, such as drapery, upholstery, carpets, etc., should be removed. Every precaution in regard to cleanliness and disinfection of bedding, clothing, and everything in use in the room should be exercised, so that the danger of spreading the infection shall be reduced to the minimum, A sheet wrung out in a strong solution of carbolic acid, Labarraque's liquid, or some other disinfectant, and suspended across the doorway may aid in preventing the infection from being disseminated to other parts of the house. The spaces around doors that are not in use, which communicate with parts of the house to be protected, should be sealed by pasting strips of wrapping paper over them. Surveillance or Qaarantine. — When smallpox appears in a house, the question arises. What shall be done with the exposed but well members of the household ? If the patient is treated at home, the other inmates as well as the sufferer should be quarantined. For, if removed to another locality, save to a quarantine station or hospital, the disease 284 SMALLPOX pn might subsequently appear there, and a new centre of infection be thus estabhshed. To depend upon people voluntarily to curtail their personal liberty for the public good would be confiding too much, at the present time, in human benevolence and public spirit. Therefore, the best results "will be obtained, when the patient is retained at home, by stationing reliable guards about the house to enforce detention of the exposed inmates and also all other necessary precautionary measures. On the other hand, when the patient is removed to the hospital it is, in our judgment, not necessary to enforce the above-mentioned restric- tions. Indeed, we are of the belief that the object desired is often defeated in large cities by a routine quarantine of the inmates of houses from which smallpox patients have been removed. To make such a quarantine effective the individuals should be detained for a period of eighteen days, the outside limits of the stage of incubation. Segrega- tion of the inmates of the household for so long a period works a great personal hardship and prompts them, in many instances, to escape before the quarantine is placed upon the house. We have known persons frequently to flee from houses where there existed an individual suspected of having smallpox, but in whom the diagnosis had not been definitely made. The settling of these exposed persons in different parts of the same city and in other cities results in the outbreak of the disease in these various localities. Thus, instead of limiting the infection rigid quarantine laws may favor its dissemination. Furthermore, unpopular restrictive measures tend to provoke evasion of the law and concealment of the existence of the disease. When the patient is removed to the hospital we would advise immediate vaccination of the exposed individuals. To avoid, as far as possible, failures through imperfect virus or technique, three or four insertions with different virus had better be made. At the same time there should be thorough disinfection of the infected articles and apartments. After this has been accomplished the exposed individuals might resume their freedom. They should, however, be kept under medical surveil- lance, and should be daily visited by a physician who should watch for any symptoms of variola. Such inspection should be continued for sixteen days from the onset of the disease in the original patient, at the end of which time the suspected individuals, if well, may be exempted from further surveillance. During his visits the physician can determine whether the vaccinations are "taking," and, if not, the procedure can be repeated, thus giving the patient a still further chance of protection if vaccinal susceptibility exists. The above plan is based upon the assumption that smallpox is not contagious during the period of incubation, and this view is in accord with the belief held by practically all authorities on the subject. Until active symptoms manifest themselves the exposed individual is not a menace to the health of the community, and it is unnecessary and injudicious to restrict his liberty during this period. Furthermore, a large experience has demonstrated to us that under a system such as TTIE TREArM/'JNT OF SMALLPOX 285 outlined, a much larger percentage of exposed individuah v:ill submit to vaccination and a correfijxmdingly increased numljcr of patients V)ill consent to he rem,oved to the hospital, for only those who comply with this advice will be exempted from quarantine. Apart from these considerations, the system of routine (|n;iniritirie, during epidemic prevalence of smallpox, will he f(jnn(l to involve the expenditure of laro;e sums of money. The quarantining of exposed persons may be practicable and wise in dealing with sporadic cases of smallpox or with the first cases in a community, for under such circumstances extraordinary precautions are justified in an endeavor to limit the outbreak of the disease to the original patients. Another means of restricting the spread of smallpox is to apprise the public of the particular locality in which the disease exists, so that no one may unknowingly approach within infecting distance of the place. But how to do this without exciting unnecessary alarm is a problem not easy of solution. The plan adopted in some cities of placarding the infected house with a large and conspicuous poster is believed by many to serve a useful purpose, notwithstanrling the fact that it frequently meets with much opposition. But whether this plan be adopted or not, the sanitary authorities should keep the premises under constant supervision, instituting daily visits by officers qualified and empowered to advise and direct the observance of proper sanitary precautions. Disinfection. — Disinfection is a highly important prophylactic measure. The infection of smallpox is not only imparted to the atmos- phere surrounding the patient, but to all articles which have been used by him or have been near him. It clings to these articles for a variable length of time, and they are, therefore, not infrequently the media by which the infection is conveyed to others. Disinfection consists in the complete destruction of the infecting agent of the disease. Fresh air and sunlight are nature's disinfectants; when infected articles are freely exposed to the atmosphere and rays of the sun for some time the infecting principle becomes less and less active, and finally dis- appears. Therefore, the house, especially the room, occupied by the patient should be freely though cautiously ventilated. If the weather be cool, an open fire upon the hearth would consume much of tlie infected atmosphere. Chemical substances, however, furnish the more speedy and reliable disinfectants, and it is upon such that we mainly depend for the destruc- tion of the disease germs. Some agent of this nature should be brought directly in contact with all the excrementitious matter from the patient, and with everything that has been used by him or has been near him during the progress of the disease. All discharges, not excepting those from the mouth and nose, should be received into a vessel containing some such disinfectant as chloride of lime, carbolic acid, or bichloride of mercury. Under no circumstances should the excreta be allowed to flow into the sewer or be cast awav without first l^a^•in£: undergone 286 SMALLPOX disinfection. In country districts, where disinfectants may not be readily obtained, the discharges should be deeply buried in the ground in a locality where there is no danger of contaminating the water supply. Every handkerchief, towel, and article of bedding and clothing used by the patient should be steeped for some time before leaving the room in a solution of two fluidounces of chloride of zinc or four fluidounces of carbolic acid to the gallon of water, and afterward boiled by them- selves for half an hour or longer in plain water; all small articles, such as bits of linen, sponge, absorbent cotton, and the like should be burned immediately; all utensils used for eating and drinking should be purified by boiling water; and, in short, nothing should be allowed to leave the room without having first been subjected to some form of disin- fection. The attendants should not be more numerous than the necessities of the case require. They should be carefully instructed in regard to the importance of cleanliness, disinfection, and isolation. Not only should they be instructed to exclude from the sick-room all persons not having authority to enter, but also all domestic animals, such as the dog and cat, as they are exceedingly liable to serve as conveyers of the infection. The clothing of the attendants should be of such material as can be readily boiled and washed, and it should be frequently changed and subjected to this process. No attendant while engaged with the case should come in contact with other persons. On leaving, either tempo- rarily or permanently, a bath should first be taken, using freely carbolic acid soap, and the hair should be washed with a solution of mercuric chloride. No clothing that has at any time been in the infected atmos- phere should be worn or carried away from the premises, unless it has first been disinfected. Physicians should also exercise care lest they may be the means of communicating the infection. When called upon to attend a case of smallpox the physician should not remain in the infected atmosphere longer than is necessary to make a proper examination ; the prescription may be written and advice given in another apartment. After each visit he should carefully wash his hands, face, and hair; his hands especially should be washed in some disinfecting solution. He should then expose himself for a considerable time in the open air before visiting another patient. The physician should wear in the sick-chamber a long mackintosh or a linen duster buttoned up to the chin, and a cap to cover the hair, and these garments should be kept hanging in the open air in the intervals of his visits. In hospitals where there are many patients to be examined, and where he is required to spend considerable time in the wards, nothing short of a change of his entire outer clothing before leaving the institution should be considered. It is also of importance for the physician to cover his shoes with rubbers, so that no variolous crusts which may be upon the floor will be carried out of the infected house. THE T UK AT ME NT OF SMAfJ/POX 287 The isolation of a smallpox patient should he continued until all the scabs are removed. The time necessary to effect their separation varies greatly in (h'fferent cases. In severe confluent forms of the flisease a month or more will he required, while in extremely mild and abortive cases of varioloid the skin may be entirely smooth in a week or ten days. Upon the palms and soles the inspissated pocks remain embedded for a long time and recjuire mechanical removal in order to avoid a long and tedious waiting for spontaneous exfoliation. Even after removal of the variolous crusts the patient shoidd not be allowed to associate with the pubHc until he has had one or more antiseptic baths. Perhaps the most reliable antiseptic bath that can be given is one containing corrosive sublimate. The safest way one may proceed in the use of such a bath is by simply sponging the body and carefully wetting the hair with the solution (1:2000) and then have the patient freely bathed in plain water with the use of carbolic acid soap, or the patient may take a full bath in a tub containing a 1:10,000 or 1: 20,000 solution of mercuric chloride. A 5 per cent, solution of Labar- raque's hquid also makes a very reliable disinfecting bath. After this he should put on clothing which has not been exposed to the infection, or, if exposed, has been disinfected, and he may then safely mingle with the public. Inasmuch as the body of a person who has died of smallpox is capable of imparting the infection, some precautions should be observed in regard to it. For instance, the body should be thoroughly wet with a solution of corrosive sublimate (1 : 1000) or with a solution of chloride of lime in proportion of six ounces of the drug to a gallon of water, or with some other equally powerful disinfectant; besides, it should be wrapped in a sheet saturated with one of these solutions and buried at once. The preferable method of disposing of the dead from this disease is by cremation; but this method is yet perhaps too strongly opposed by public sentiment to be practicable. It is not advisable to transport the corpse a long distance or from one city to another for burial, but if this be really necessary, it should first be placed in a metallic coffin hermetically sealed. In its burial it should be put at least six feet under ground, and should not be disinterred unless absolutely necessary, and then only under sanitary supervision. The vehicle used for con- veying the body to the grave should afterw^ard be disinfected. It is, perhaps, unnecessary to say that the funeral should by no means be public. After the sick chamber has been vacated, either by recovery or death of the patient, every article it contains of no great value should be immediately burned. Everything else which will not be injured by the ordinary operation of the laundry may be safely and cheaply disinfected by immersion in boiling water for half an hour. It should be remem- bered, however, that the water must be maintained at the boiling point for that length of time. But if it is impracticable to subject such articles at once to the boihng process, they should be immersed for about four hours in some reHable disinfecting solution — such as^mercuric chloride 288 SMALLPOX In the proportion of 1 : 2000, or carbolic acid 1 : 50 — and subsequently boiled. The sick-room should be disinfected according to the principles laid down in the chapter on disinfection. The room should then remain closed from twelve to twenty-four hours, afterward opened, thoroughly ventilated, and all surfaces, including the furniture, washed with a disinfecting solution (chloride of lime, carbolic acid 1 : 50, or mercuric chloride 1 : 1000) ; afterward the floor and other woodwork should be thoroughly scrubbed with soap and water. The wall-paper, if there be any, should be well moistened with the carbolic acid solution and scraped off and burned. Paper may be reapplied or the walls white- washed, according to fancy. In addition to all these precautions, it is advisable to have the room remain unoccupied for three or four weeks, during which time it should be well aired. For disinfection of outer clothing, carpets, bedding, and all articles which cannot be boiled, there is nothing superior to steam under pressure. The germs of smallpox will certainly perish if exposed for half an hour to this agent at a temperature of 230° F. There are, however, certain articles which would be injured by moist heat, and for the disinfection of these dry heat may be substituted. In this case a temperature of at least 230° F., continued for two hours, will be required. Formal- dehyde, however, could be used instead of dry heat. Vaccination. — Of all of the measures employed to prevent the spread of smallpox, none is so important and efficacious as Jenner's great discovery. There is perhaps no single scientific fact better established than that vaccination, periodically repeated, is capable of effectually preventing the occurrence of that disease in man. In view of this fact it does at first sight seem strange that variola should continue to prevail in civilized communities; and, while nothing appears easier than to control the spread of this disease, or even to eradicate it altogether, yet there are diflaculties in the way of accomplishing this end which seem almost insurmountable. These arise from various causes, but chiefly from individual carelessness or indifference about employing vaccination, and from the absence of a general law making it compulsory. We know that many conscientious citizens are opposed to enforcing vaccination by law, but as every unvaccinated person is liable to contract smallpox and disseminate the infection among others, he should be regarded in the light of a public enemy, and dealt with accordingly. Surely it is not an unreasonable position to assume that no person through ignorance or prejudice should be allowed to contravene the public welfare. But, in the absence of a statutory law requiring the vaccination of all persons, very much can be done in the way of enforcing the measure by restricting the privileges of the unvaccinated. For instance, satis- factory evidence of successful vaccination should be required of every child before admission into public and private schools and institutions for the care of children; no unvaccinated person should be allowed to serve as a soldier in the army or navy, or in the State militia; and no Tiii<: tiii<:atmknt of smallpox 280 unvacci Mated iiinnin;ni,nl, slioiild ho jillowcd lo hmd until \;ifciii;itif>M has been perfoniied. In view, therefore, of the <,n-e;it importance of lliis prophylactic measure, it l)ecomes the (hity of all nmiiicipal and Stjde autliorities to j)rovide gratuitons Viiccination for the ])oor, and, in(h-ed, ff)r all helpless children of careless or improvident j)arents, no matter to what class of society they belong. No expenditure of money should be spared by these authorities in order to protect their citizens against a disease so loathsome and fatal as smallpox. From a purely monetary ])oint of view such expenditure is wise, for a single epidemic of this much dreaded disease in a community may necessitate a greater outlay to care for the indigent sick alone than would be required to purchase the means of protection for that community for a decade of years. If vaccination were universally practised, and repeated from time to time as circumstances recjuired, there would be little need for other means of prevention. Whenever a case of smallpox occurs in a family, the physician's first duty is to vaccinate promptly all members of the family who have never been vaccinated, and revaccinate all others without regard to the character of their previous vaccination. It is a good plan to vaccinate on several successive days those who have never been previously subjected to this procedure, in order to increase the probability of obtaining a successful result. If this be done and the patient sent to the hospital, the disease may be prevented from spreading. Care of Patient.^ — In order to consider in detail the treatment of smallpox it seems most convenient to divide the disease into its various stages, as follows: (1) the stage of incubation; (2) the initial stage; (3) the eruptive stage; (4) the stage of suppuration; (5) the stage of retrogression, or stadium exsiccationis. 1. The Stage of Incubation.- — The interval between the reception of the infecting agent of smallpox into the blood and the earlier manifesta- tions of the disease is usually unattended by symptoms. There is no doubt, however, that certain unknown processes take place during this period. It is very important to know whether an^ihing can be done at this time to arrest or change these processes so as to prevent or modify the approaching disease. Drugs, of course, are powerless for this purpose. Is vaccination at this period capable of exerting any such influence ? From the clinical reports of those who have made extensive use of vaccination at this period of smallpox there seems to be some differences of experience concerning its efficacy. In commenting on this question Curschmann says: "Are we able to exert any influence on the disease in the early stage preceding the eruption? Is it possible in infected persons, during the stages of incubation and invasion, to cut short the disease or to modify its course? INIany attempts have been made to answer these questions affirmatively, but as yet without much result. The first idea was vaccination, and this was employed by some in the ordinary way; by others subcutaneous injections of vaccine lymph have been given, it is said with good results. I must, however, advise great 19 290 SMALLPOX skepticism regarding these assertions. Of the subcutaneous injection of lymph I have no experience; but that ordinary vaccination during the stages of invasion and incubation cannot stay the disease has been proved to me by chance observations and direct experiments. On the contrary, I have seen, in cases in which vaccination was practised after infection with variola, vaccine pustules and smallpox pustules developed side by side. It is, in my opinion, very doubtful whether vaccination can even render the course of the disease milder." The hypodermic use of vaccine lymph is certainly not entitled to any confidence as a prophylactic measure. Immunity does not result from the mere presence of vaccine virus in the blood, but from certain unknown processes which take place in the system in the course of true vaccinia. It is, therefore, evident that the vaccine disease must reach a certain stage of development before it is capable of exerting any prophylactic power whatever. We have had very frequent opportunities of observing that vaccination during the invasive or initial stage of smallpox is utterly valueless, and also that it is equally useless when performed only three or four days prior to the earlier invasive symptoms. A vaccine vesicle resulting from a vaccination performed at the period just mentioned, and the variolous pustules, will, it is true, develop side by side without the one exerting any influence whatever over the other. But Curschmann's experience seems to warrant the inference that at no time within the incubation period of smallpox can vaccination be used with advantage against the approaching disease. If such is his experience, it certainly differs very greatly from our own. We have in numerous instances seen smallpox very markedly modified by vacci- nation performed at this period, and not infrequently have seen it pre- vented absolutely. In order that protection shall be complete it is necessary that the insertion of the vaccine lymph should be made almost immediately after the reception of the contagium; but if made at a somewhat later date a modifying efl^ect may still be obtained. No part of the incubation period should be considered too late to make use of this remedy, since this period is sometimes prolonged beyond its usual limits, in which case a late vaccination may prove of value. It is our opinion that vaccinia does not begin to exert its prophylactic power until the areola commences to form around the vesicle. At this time the mild febrile reaction, which was regarded by Jenner as a sine qua non in true vaccinia, becomes apparent. If this stage of the vesicle be reached before the patient shows any symptoms of smallpox, the disease may be entirely prevented; if not reached until after the febrile symptoms appear, but before the eruption occurs, it may modify the attack. Now, it is well known that in typical vaccinia the areola appears about the seventh day or eighth day from the date of insertion of the lymph, and is at its height on the ninth or tenth day; and it is equally well known that the incubation period of variola is, in the majority of cases, of ten or eleven days' duration, and that the eruption does not appear until about three days later. This renders quite obvious the fact that vaccination, practised shortly after variolous infection has 77//'; rilKATMKNT OF SMAfJ.POX 291 occurred, has an opporditjity in [)()inl of lime to exert more or less prophylactic iiifhience against (he; incuhaling(Jisease. While no inflexi}>!e rule can be laid down, it may be said in a general way that if vaccination be practised on the first or second day after the reception of the infection into the systetn, the protection may })e perfect; and if errif>loyed betv\(;cn this date and the fifth day, it may be j)artial. But we would emphasize the fact that after infection has occurred, every day that is allowed to pass before resorting to vaccination is so much valuable time lost. While the appearance of the areola generally indicates the period of the vaccine process at which its prophylactic power ))egins to }je exerted, yet this period may vary somewhat in different individuals. For instance, we have more than once seen, say, two persons exposed to the contagion of smallpox at the same time in such a manner that there could be no doubt about infection having occurred, have vaccinated these persons at once and with the same virus, and the vaccinia in V)oth cases has pursued an identical course, yet in one the protection was perfect, while in the other it was only partial. In other similar instances one has received partial protection and the other none at all. This difference is doubtless due to some individual peculiarity that cannot be explained. It is much easier to confer protection against smallpox after infection, where revaccination is required to accomplish this result, than where the vaccination is primary. The explanation of this is not difficult. It is because vaccinia in its modified form, such as results from revaccina- tion, develops more speedily, arrives at the areolar stage more quickly, and runs its entire course several days sooner than does the unmodified or true vaccinia; hence, it is clear that the period of protection in such cases must be reached earlier. In endeavoring to confer protection during the incubation stage of smallpox the quality of the vaccine lymph employed has a great deal to do with the success. Nothing is of more vital importance at this period of the disease than that the vaccine virus employed should be fresh and active. The difference between success and failure in pro- ducing vaccinia after exposure often means to the patient the difference between life and death. We know of no virus more reliable or which will give better results than eighth-day lymph taken directly from a typical vaccine vesicle on the arm of an infant. While humanized^ virus has gone out of use in most countries, we cannot refrain from testifying to its reliability and value in persons who are exposed to smallpox. The virus of long humanization possessed the additional advantage of running a rapid course and so bringing about its protective influence promptly. The virus resulting from a long series of human transmissions was, therefore, to be preferred over virus of recent humanization and animal virus. At the present time, however, we are more concerned with bovine virus, which has for certain reasons largely superseded the use of humanized lymph. 1 Humanized virus is still extensively employed in Mexico, where the Iphysicians prefer it to animal lymph, 292 SMALLPOX It is believed by some authors that miihiple insertions quicken the process of vaccinia, and thus hasten the attainment of that stage of the disease at which its prophylactic poM^er begins to be exerted. Water- house was of this opinion, and his remarks on the subject are interesting because they were made a century ago, in the very earliest history of vaccination. He wrote: "I think it proper to publish an important fact for which we are not indebted to Europe, namely. If a person he inoculated with the kinepock two days after having received the casual infection of smallpox, the kinepock will predominate and save the patient. Nay, I will go further and say in some cases three days posterior to infection instead of two ; for there is a mode of expediting the operation of the kinepock virus by increasing the quantity of matter thrust under the epidermis; and it appears, from experiment, that this does not depend so much on increasing the quantity put into a deep puncture as it does on the increase of infected surface. In other words, you may expedite the pro- cess of kinepock inoculation two days if not three, if, instead of two punctures, you make sixteen or twenty; . . . and on the sixth day from the operation we shall have the appearance of the eighth day in ordinary cases; and on the eighth day we shall find the appearance of the tenth, and so on with the febrile symptoms, in which commotion the prophylactic power consists." As there is nothing at this stage of smallpox of greater importance than vaccinia attended by prompt and speedy development of the vesicle, it is evident that the virus employed should be selected and used with the greatest possible care and skill. It is well under these circumstances to employ an active virus; the production of a sore arm is a matter of but little importance when the exposed individual's life is at stake. In order to ensure success, it is advisable to employ virus, when possible, from more than one source. It is desirable at this time to guard as far as possible not only against failure, but also against a vaccine disease of slow progress. A tardy vesicle, or one that is slow in making its appearance and late in arriving at maturity, gives no assurance of safety. In recent years animal lymph has been brought to a high state of perfection by the admixture of glycerin. We have found glycerinated lymph properly prepared and preserved to be more likely to succeed and also more speedy in its action than the dried virus on ivory points. Hence, during the incubation period of smallpox glycerinated lymph may be found almost, if not quite, as effectual as long humanized virus in preventing or modifying the approaching attack. We have had extensive opportunities of testing its power in this direction and have been well pleased with the results. The records of the hospital bear testimony to the fact that during the recent epidemic of smallpox in Philadelphia several unvaccinated persons sent in through error of diagnosis were protected absolutely by the use of glycerinated lymph. Where the protection was not perfect there was marked modification Tlll<: TREATMENT OE SMA/JJ'OX 2!i5 proved unavailing, and we can df) notliin^ (norc ;i( this stji^f fli;in ircai. special symptoms as tliey arise. The popular though erroneous nolion of piist cfnliiiics, lh;i( if is necessary to keep the pjitient hot and swejiling, slill prevails to sf>me extent, and not iid're(|uentiy it is I'oinid very (HffienH to overcome this prejudice. On the contrary, every effort should Ix; flirecled tf)\vard keeping the patient as comfortable as possible, and exj^erience shows that a bedroom well ventilated and having a temperature of from 0')° to 70° F. is best suited for this purpose. The onjinary febrifuge mixtures, such as li(pior ammonia' acetatis, litpior ])otassi citratis, tinctura aconiti, etc., may be given in suitable doses and at stated intervals We are in the habit of using the following formula: l;fe— Spirit, ssther. nitrosi, Syrup. limonis Ctd fSiv. Liquor, ammonii acetatis fSv. — M. Sig.— Give 2 to 4 fluidrachms every two hours in a little ice-water. If there is irritability of the stomach, the effervescing citrate of potas- sium may be preferable. It sometimes happens that the stomach is very irritable, especially in children; in this case lime-water, subnitrate of bismuth, aromatic spirit of ammonia, a little chloroform -water, or any other drug or agent known to be of service in this condition, may be used. The swallowing of small pieces of ice will often give relief when everything else fails. When the skin is hot and dry and the temperature high, frequent sponging with cool water is serviceable. Severe headache may call for the application of cold water, iced com- presses, or an ice-bag to the head. These need not be feared on account of the popular superstition that they tend to suppress the eruption, for such is not the case. Nervous symptoms, such as insomnia, delirium, and convulsions, are often prominent features of the disease and demand appropriate treat- ment. Some of the bromide salts, or chloral, given either separately or in combination, will usually succeed in subduing these symptoms. For the convulsions of children there is perhaps nothing more effective than chloral, given either by the mouth or rectum. When given by the mouth it should be well diluted, since it is very irritating to the throat, which is liable to become implicated in the variolous process quite early. Warm baths are also very useful. There is another nervous symptom commonly present at this stage of smallpox, and that is pain in the back. This is sometimes so distressing as to call for measures of relief. When the stomach is retentive Dover's powder may be given, or some one of the analgesic coal-tar products, now so frequently used to relieve pain. Sometimes there is much restlessness and general irritability; in such cases we have found a little morphine, combined with the febrifuge prescription above referred to, to act most happily. The common practice of applying mustard to the back for the relief of pain or to the epigastrium to lessen gastric irritability cannot be too strongly condemned, since the variolous eruption always appears in much greater abundance on irritated surfaces. "\Mierever there is an 296 SMALLPOX ulcer, a wound, or an excoriated condition of the skin, there the pustules are sure to be found in dense clusters. We have frequently seen the eruption intensely confluent over regions of the skin where a mustard plaster had been applied during the initial stage of the disease. Some have thought that the eruption might in this way be diverted from the face to other localities, but we are convinced that it is not diminished anywhere else by reason of its confluence on these parts through the action of a sinapism; rather is it increased to that extent. The digestion at this §tage is not vigorous; hence the diet should be light and easily assimilable. There is nothing more suitable than animal broths and milk. The best beverages are cold water and iced lemonade. Acidulated drinks seem to be particularly grateful to the palate. Gentle cathartics may, of course, be administered whenever indicated. 3. The Eruptive Stage.— The eruptive stage may be said to comprise a period beginning with the first appearance of the eruption and ending when pustulation has fully occurred. The duration of this stage in variola vera is usually seven or eight days, but in modified smallpox it is short- ened in proportion to the degree of modification. The great desideratum for this period of the disease is a remedy capable of diminishing or modifying the cutaneous manifestations, for there is no doubt that recovery of the patient almost always depends upon the quantity of the eruption and the length of time consumed in running its course. Formerly it was thought that some modification might be brought about by bloodletting, but experience shows that the most confluent eruption has succeeded the most vigorous employment of the lancet. It is, therefore, worse than useless to bleed, for by so doing we expend power that will be required later on to repair the injury done by the disease. The treatment during the eruptive stage of smallpox should be directed toward alleviation of the subjective symptoms and the correc- tion of special symptoms as they arise. Usually it is not until the eruption appears that the disease is recognized and the degree of severity prognosticated. If the case promises to be at all severe, all flannel undergarments should be at once removed, and the hair cut close, so that the head may be kept cool, cleanliness enforced, the risk of cellular inflammation of the scalp diminished, and a better opportunity afforded for the employment of cold applications should delirium or more urgent brain symptoms arise. The febrile symptoms which usher in the disease now usually remit, but increase again as the eruption progresses. For this condition the remedies already mentioned may be continued. It sometimes happens in a depressed condition of the system, particularly in children, that the extremities and even the surface of the body are cool, and that the eruption is too slow in making its appearance. In such cases the appli- cation of heat and the administration of hot stimulating drinks, such as hot toddy, may be of service. This condition in children is apt to be associated with convulsions, in which case there is nothing better than 77//'; THI'IATMKNT OF SMALLPOX 297 a warm batli f()llow(;(l by an envclopineiil, iti vvann blankets. StioiiM the convulsions continue, however, cliloral, by eitlier inonfli or n;(tnni, is quite sure to give relief. We repeat here the caution not to fail to dilute the chloral freely, for the throat is now so much inv(;lve(l in the variolous j)rocess that an irritating draught may give rise to croupous symj)toins, or even acute (edema of the glottis. Tkeatmiont of the TtitioAT. — As the eruption progresses, not only the fauces, but the soft and hard palate, the buccal mucous membrane, the larynx, and sometimes the trachea also become more or less involved in the process, and this is often the source of difficult and painful deglu- tition. This condition requires the use of mouth washes and gargles, such, for example, as those containing chlorate of potash, boric acid, glycerole of tannin, tincture of myrrh, etc. We have found the milder demulcent fluids made from flaxseed, gum arable, or slippery-elm bark particularly grateful. Of these none is more relished by the patient than flaxseed tea, sweetened with white sugar and acidulated with lemon-juice. Careful and frequent cleansing of the mouth affords considerable relief. This may be done by the nurse covering her index finger with a piece of soft linen, dipping it into a solution of boric acid with glycerin added, and then thoroughly and carefully cleansing the entire buccal cavity. During the recent epidemic (1901-04) through which we have passed, we found orthoform, in one-grain lozenges, useful in lessening the distressing soreness of the throat and mouth. In severe cases, however, where the throat was covered with lesions we were obliged to use a cocaine (1 per cent.) spray in order to lessen the pain in swallowing, and thus enable patients to partake of sufficient nourishment. Variolous patients, according to E. Pepper, who advocates cocaine internally in smallpox, show a considerable degree of tolerance toward this drug. We have never noted untoward results from the employment of cocaine internally or in spray form. The pain in the throat and difficulty in swallowing are often benefited by having the patient hold in his mouth small pieces of ice, and allowing these to dissolve slowly. Where there is much glandular swelling the application of the ice-bag externally will be found useful. Some patients, however, will prefer the use of poultices or hot fomentations. When there is much foetor some antiseptic, such as carbolic acid or permanga- nate of potash, may be added to the mouth wash or gargle. We have found dilute chlorine water to answer a good purpose. Variolous glossitis is best treated by mild antiseptic mouth washes and the use of pellets of ice. Should acute oedema of the glottis or of the ary- epiglottic folds occur, an emetic may be given if the patient is not too weak, or local scarification may be practised. When suffocation threatens, tracheotomy offers the best if not the only chance of recovery. Treatment of Nervous Sympto^nis. — Toward the latter part of the eruptive stage of variola persistent insomnia and delirium often occur. Wlien this condition of the patient is attended by a flushed face and bounding pulse, an ice-bag to the head and a brisk cathartic may be 298 SMALLPOX of service. Tartar emetic and sulphate of morphine, in doses of from one-eighth to one-half grain each, will often produce sleep and quiet the delirium. Morphine is a most valuable drug in controlling restless- ness and inducing sleep during the pustular stage of smallpox. To accomplish this end, it is sometimes necessary to administer a half or three-quarters of a grain of the drug in twenty-four hours. However, it is usually well borne and the patients are almost always benefited by its use. Large doses of bromide of potassium, or chloral freely diluted, may be given, and repeated if necessary. Some care, however, must be taken not to push these remedies too far, lest the patient lapse into coma or a state of profound prostration. Occasionally the delirium is of that violent kind which the older writers styled "delirium ferox." This is accompanied by a wild expres-' sion of the countenance, and such a strong tendency to escape from the attendant, or to self-destruction, that too much care cannot be exercised for the safety of both the nurse and the patient. We have known strong and muscular patients, while in this state of mind, to knock the nurse down, jump out of the window, and run to some secluded place, where they would cunningly secrete themselves. We have also known patients to attempt suicide in various ways while the nurse was temporarily absent. The necessities of the case, therefore, often require the use of some artificial means of restraint. For instance, a wide band of stout webbing or canvas may be placed loosely over the patient's chest and secured to each side of the bed. Smaller bands of the same material may be fastened to each wrist and ankle, or leather wristlets and anklets may be used, the former being secured to the sides of the bed, and the latter to the foot of the bed, allowing, however, a little motion of the limbs, so that the patient shall not be subjected to painful restraint. In the mean time every effort should be continued to quiet the delirium, and when the patient refuses to swallow, the drugs and nourishment should be administered by the rectum. It is deemed appropriate to speak of the treatment of hemorrhagic smallpox under this head, for the peculiar manifestations of that type of the disease become strikingly apparent during the eruptive stage; and, moreover, it is rare for a well-marked case to live beyond the limits of the vesicular stage. Treatment is of little avail in this phase of variola. The remedies usually employed are acids, quinine, ergot, and tincture of chloride of iron; but these, we think, are prescribed more in con- formity with general usage than with the expectation of obtaining any real benefit. When hemorrhage takes place in the various cavities or internal organs of the body, it is recommended that styptics be employed, together with injections of ice-water, or the use of cold compresses or tampons, although it is admitted that the beneficial effect of these agents is very slight. Transfusion and hypodermoclysis with sahne solution have been tried, but have not given very encouraging results. This type of the disease in varioloid is not quite so significant of danger as in variola. We have seen a few hemorrhagic cases of varioloid THE TR.EA TMENT OF SMA LLPOX 299 in which the hoin()iThafi;o fi'oiii infernal organs was not very [)rofuse or protracted, althouf^li tlie purjmric s[)ots were well rnarkecJ, recover under the free use of iron and stimulants. In these cases nourishment was freely taken, prostration was at no time profound, and, as the patients passed favorably tlironS'/lf /I TJ.POX 307 the pustules are opened with uii aseptic needle find their contents evacuated. The patient is then wrapped in aseptic linen, which is frequently changed. It is claimed by the author that this treatment notably diminishes the duration of the eruption, lessens the fever, prevents severe ulcei'ation and scarring, jind (hus leads to rapid con- valescence. Similar results are alleged to have fcjllowcd the use of baths contairiing permanganate of potassium, the salt being added until the water is of a rose-red color. Our experience with permanganate baths has been entirely unsatisfactory. The baths were given daily and, in some cases, twice daily from an early period of the eruption. They did not seem to exert any favorable influence upon the course of the eruption or the disease. Indeed, during the employment of this treatment our mortality was more than 50 per cent. Looking back over the literature of the subject, we find that the antiseptic treatment of smallpox by means of external applications is nothing more than the revival of an old practice that was employed and abandoned many years ago. It is true that when these agents were used a half-century and more ago, it was not because they possessed antiseptic properties, for the germ theory was not then known; but ignorance of this fact certainly could have made no difference in the result. As long ago as 1843, Gregory wrote: "The latest mode of treating the surface during the maturative stage of smallpox is that of applying mercurial plasters containing calomel or corrosive muriate of mercury, or covering the whole surface with mercurial ointment. In the French hospitals at the present time the latter mode is in fashion. The reports which have reached us of its success, however, are not very flattering. I have seen all three plans fairly tried at the Smallpox Hospital. The ointment and calomel plasters were inefficient. The plaster of corrosive sublimate converted a mass of confluent vesicles into one painful and extensive blister, but I am still to learn what benefit the patient derived from the change." When the eruption reaches the vesicular stage there is usually experi- enced considerable burning, particularly of the face, hands, and fore- arms. For the purpose of preventing or alleviating this symptom, some ointment or oily substance will be found useful. VaseUn containing about 3 per cent, of carbolic acid makes an efficacious ointment; or, if the odor of carbolic acid be objectionable, oil of eucalyptus or thymol may be substituted. A preparation which we have frequently employed is composed of equal parts of lime-water and olive oil, to w-hich is sometimes added an antiseptic and perhaps a Httle cologne water. This is freely applied with a large camel's hair brush. When the burning sensation and pain are severe there is perhaps nothing which gives so much relief as cold applications, such as cloths wet with cool water and spread over the face and arms. Curschmann believes that cold and moisture are the most efficient remedies for this condition. He says: "In severe cases the application of iced compresses to the face and hands, or to any parts where the eruption is abundant, 308 , SMALLPOX will diminish the severe pain, lessen the swelling and redness of the skin, and make the patient more comfortable." Moore advises the application over the face of a "light mask of lint thoroughly soaked in a mixture of iced water and glycerin (a table- spoonful of the latter in an ounce of water) and covered with oiled silk." The development of the eruption in the thick skin of the palms of the hands, tips of the fingers, and soles of the feet not infrequently gives rise to great pain. Cold applications or iced compresses may prove of service in this condition, although we think we have seen greater benefit follow the use of luke-warm hand and foot baths. The frequent appli- cation of flannel cloths wrung out in tolerably hot water, or the use of hot poultices, is often of great service. The topical applications recommended for the pustular condition of the skin are numerous. To assuage the pain, burning, and itching, to correct the offensive odor, to guard against septicaemia, and to pre- vent pitting are the principal ends aimed at in the selection of these measures. During the period of suppuration the sensation of itching is quite as intolerable as the pain, so that it is almost impossible for the patient to refrain from scratching. In consequence of this, or from other causes, the pustules become ruptured in many localities and their contents discharged. This purulent material undergoes decomposition and gives rise to a highly offensive odor. Remedies are demanded to relieve the itching and correct the odor. Antiseptic and antipruritic washes, such as carbolic acid (1:100), or corrosive sublimate (1:1000), may be employed for this double purpose. About the mouth, nose, and eyes a saturated solution of boric acid in rose-water may be freely used. We have frequently employed a 5 per cent, solution of either carbolic acid or Labarraque's solution, directing that both the patient and the bedding should be sprayed with this solution every two hours. Very excellent results are said to have followed the use of an unguent composed of 100 parts of cold cream to 4 parts of salicylate of sodium. M. Dujardin-Beaumetz reports that this ointment, in his hands, has not only been successful in destroying the repulsive odor in severe cases of smallpox, but has actually prevented suppuration. In addition, he advises that a powder of 100 parts of talc to 6 parts of salicylate of sodium be dusted over the affected localities. We have sometimes been able to lessen or modify the horrible odor by using as a dusting powder, subnitrate of bismuth, boric acid, and, sparingly, iodoform. To either of these, and especially to the latter, talc might be added. We have also derived advantage from a dusting powder composed of 15 to 20 parts of aristol to 100 parts of talc. MacCombie strongly counsels the early removal of the crusts, which he asserts can best be accomplished by the use of a linseed-meal poultice, sprinkled with iodoform. " On the face the method most agreeable to the patient is to cut a mask of a single thickness of lint, with apertures for the nose, mouth, and eyes; then to smear a thin layer of linseed-meal poultice on this, taking care to put on the surface a little vaselin in Tflli TRMATM/'JNT OF SMAfJJ'OX .'{09 wliich iodoform has been mixed, and to apply this poulficc atients bear the painting very well, although many complain of smarting for a time after the treatment. In some patients the skin is so sensitive that this mode of treatment has to be abandoned, although a tincture of one-half the usual strength might })e a])plied in such cases. AV)Out the eighth to the tenth day of the eruption, in unmodified cases, a thin, dry, parchmenty mask is formed wliich begins to crack and peel off. At Fig. 53 Showing the eftfect produced by painting the right arm from the elbow to the wrist daily wiih lincture of iodine. Area painted is free of the secondary impetigo sores seen upon the untreated arm. Left arm was not painted. this time it will be found advisable to substitute an unguentous appli- cation. We believe that the iodine treatment tends to shrink the pustules, to hasten decrustation, and, to some extent, to lessen the pitting, although in severe cases it will not prevent it. The liability to consequent pyogenic complications of the skin appears to be diminished. A notable feature of this treatment is that it completely destroys the ofi'ensive odor arising from the areas of skin to which the iodine is applied. We have also obtained good results from mild emolUent ointments, with or without antiseptic ingredients. We are not sure that any special combination is essentially more useful than plain petrolatum or cold cream. In the early stages of the eruption, these applications are quite grateful to the skin, and later on they serve to soften the purulent 312 SMALLPOX debris, which can then be more easily removed from the face. In severe cases, where the treatment of the face is neglected, the odor is more offensive, and the ulcerations appear to be deeper and followed by more disfiguring pitting. We have frequently incorporated carbolic acid, aristol, biniodide of mercury, etc., in the ointments applied. As above stated, however, Fig. 54 Smallpox eruption at a late stage shovviug extensive dark crusting on the face resulting from neglect of local treatment. these did not seem to materially increase the efficiency of the applications. To soften the crusts from the skin, nothing is better than a salve of the following composition: p;— Sodii bicarbonatis 5ij. Petrolati q. s. ad gj. We have found great benefit to result from the use of baths given during the stage of pustulation and desiccation. These may be made TTiE tI{.i<:atmi<:nt of smallpox pap, antiseptic by tlic addition of (Tcolin (\ :F)(H)) or hicliloride of niercury (1:J0,()()() to 1:20,000). The piindent accumulations and crusts are detached from the skin by the baths, and the associated septic fever is greatly lessened. Furthermore, the liability to [)yogenic skin complica- tions is diminished. When it is inconvenient or impossible to employ antiseptic baths, much good will often be derived from oj^ening and evacuating the pustules, and wasliing the bases with absorbent cotton saturated with a 1. : 5000 solution of bichloride of mercury. When extensive impetigo exists we employ a bichloride bath and then dust the patient with a weak aristol or iodoform talcum powder. An ointment which will be found useful in treating impetigo pustules is: 1^ — Hydrargyri iimmoiiiati gr. x. Pulv. amyli, Pulv. zinci oxidi dd 5ij. Petrolati Sss. Treatment of Eye Complications.' — The air in the sick-room or hospital ward should be changed as frequently as possible. The hands of the patient should be encased in gloves or protective bandages to prevent contamination of the eyes. As a matter of daily routine the eyes should be flushed copiously with warmed, weak, salt or boracic acid solutions. The edges of the eyelids should be anointed with vaselin. In all examinations of the eyes great care must be used in the manipulation, lest the cornea be injured. In the early stages, when the eyes are hot and flushed and feel heavy, a douche or spray of ice-cold water often brings relief. In excessive hyper?emia, frequent bathing with water as hot as can be borne will have a soothing effect. In other cases, cloths saturated w^th lead-water and laudanum, or ice-cold compresses may be laid upon the closed lids. The conjunctival sac should be frequently flushed with warm boracic acid solutions. At bed -time the edges of the lids should be anointed with vaselin, or with yellow oxide of mercur}^ in vaselin, 1 grain to the drachm, to prevent their becoming glued together. When conjunctivitis sets in with a mucous or mucopurulent discharge, mild astringents should be used; saturated solutions of boracic acid, to which may be added a few grains of sodium chloride, can be employed. The lids are to be inverted and the mucous surfaces painted with weak solutions of silver nitrate (1 to 5 grains to the ounce) or protargol in 5 to 10 per cent, solution may be satisfactorily employed. In some instances the discharge may be so free that stronger astringents must be used. Here no more efficient remedy than silver nitrate can be applied, for in its action it is germicidal as well as caustic. ^Mien the lids are tense and board-like, however, and their mucous surfaces covered with a gray film or false membrane, it is not to be used; but only when the lids are relaxed, the discharge creamy, the conjunctiva 1 The chapter on the Treatment of Eye Complications has heen kindly prepared for us by Dr. Buiton K. Chance, whom we have frequently called in consultation to advise us iu the treatment of severe ocular lesions at the Municipal Hospital. 314 SMALLPOX red, and the retrotarsal folds puckered. After thoroughly cleansing them the conjunctival surfaces should be brushed daily with strong silver solution, 10 to 20 grains to the ounce; the excess of the drug is to be washed away by an abundance of common salt solution. These washiiigs are to be repeated until the membrane is clear and red, and as long as the discharge is abundant the use of silver is indi- cated. The edges of the lids are to be greased with vaselin, and they are then to be restored to their normal position. The pressure on the globe, caused by the swollen lids may be so great as to necessitate the cutting of the outer canthus. A canthotomy may have to be done also to facilitate the examination of the conjunctiva and the cornea. Persistent and increasing chemosis of the conjunctiva demands snip- ping in order to relieve the pressure on the cornea. When the lids are tense and the secretion flocculent, the local applica- tion of cold is most useful. The readiest means of applying it is as follows: Small squares of lint of several thicknesses of gauze are placed on a block of ice. When these are cold the excess of water is squeezed out from them and they are laid on the swollen lids. They must be changed sufficiently often to maintain a uniform coldness. In some cases it may be necessary to apply them continuously, while in others they need be used for short periods only several times a day. When the cornea is involved great care must be exercised during any manipulation, lest pressure be exerted on the globe. Efforts at cleanliness must be redoubled. Solutions of atropine of four grains to the ounce are to be used twice or thrice daily, to effect complete mydriasis, when the ulceration is central. But if the ulceration be marginal eserine salicylate in weak solution, one-quarter grain to the ounce, may be used, but with great carefulness, as this drug is liable to increase the hyperaemia of the iris, with consequent iritis. Therefore, the use of this drug should be discontinued when the pupil has become contracted. Ice must be discontinued and hot compresses are to be substituted. Squares of gauze wrung out of water w^hich is kept at about 110° F. are to be frequently applied. Every attempt should be made to remove all of the discharges and to restore the conjunctiva to its normal condition. The lids are to be separated very gently and all of the tenacious secretion is to be wiped off with swabs of cotton. The conjunctival sac is then to be flushed with warm boric solutions. This attention should be given every hour, or, if necessary, at even shorter intervals. Although other stronger antiseptics may be tried, we are of the opinion that the careful and persistent use of mild boric acid or weak bichloride of mercury solutions should yield the best results. Where perforation of the cornea is threatening, the edges of the ulcer must be cauterized at once. Here a dull hot probe, thoroughly applied, may end the process. We have used, besides the hot probe, solutions of carbolic acid, of iodine, and crvstals of trichloracetic acid. If there TJIli Th'/'JATMKNT OF SMALLPOX 315 1)6 not too Mincli (•oiijiiiictiviil swnitioii, .'i, well-applied rf)llcr hiiiida^^f may ad'ord the pro|)er sii})])oi't to the already w(;akeried eorii(;al ineirj- brane. A low ^ra,de of conjunctivitis may {)er,si.st for a week or even months after convalescence from smallpox in persons whose illness has fjeen complicated hy serious conjunctival inflammation. Here the use of stimulatinfii; astringents like the boroglyceride or the glycerole of tanrn'n act with signal advantage. Argentamin, 2 to 5 per cent., or largin, 5 to 10 per cent., may be tried. Formalin, Ir.WOO, or bichloride of mercury, three-quarters of a grain to the pint, may be used with success in more severe cases with considerable discharge. CHAPTER VI. CHICKENPOX. Synonyms. — Varicella; formerly, Variola crystallina, Variola nctha, Variola spuria. English, formerly, water pock, glass pock; German, Varicellen, Wasserpocken, Wind hldttern, Schafpocken; French, la vari- celle, la verolette; Italian, Mcrviglicne, ravaglione. Definition. — Chickenpox is an acute, highly contagious disease, occurring chiefly in children, characterized by an eruption of vesicular type, appearing in crops and accompanied by mild febrile disturbance, which usually begins with the appearance of the cutaneous outbreak. The lesions dry in a few days into crusts. One attack protects for life in the vast majority of cases. History. — Chickenpox is doubtless a disease of great antiquity, although for centuries it was confounded with smallpox. The Arabian physician, Rhazes, who lived in the ninth century, made mention of a mild or spurious eruption which was not protective against epidemic smallpox. The Sicilian physician, Ingrassias, seems to have been the first to have described varicella in accurate terms; this appeared in a work entitled Preternatural Swellings, written in 1553. Vidus Vidius, an anatomist and physician, wrote some forty years later, employing for varicella the term crystalli or varioloe crystallines , a designation which clung to the disease for many years. Sydenham makes no mention of the disease. An admirable descrip- tion, which admits of no room for doubt, has come down to us from the pen of Riverius, who wrote in 1646. Morton's writings on the subject are of historical value, because, according to Gregory, he remarks that the disease was vulgarly known as chickenpox. This appears to be the first mention of this term in literature. The name chickenpox is said to be derived from the word cicer, a chicken-pea, the French word for the same being chiche. Morton (1694) referred to varicella under the title varioloe admodum henigna', re- garding the disease, as did all of his contemporaries, as a variety of small- pox. In 1696 Harvey contributed some important writings on the subject. Although the credit of recognizing the duahty of chickenpox and smallpox is commonly given to Heberden, it in reality belongs to Fuller, who, in 1730, expressed his views in the following interesting language: "The pestilence can never breed the smallpox, nor the smallpox the measles, nor they the crystals or chickenpox, any more than a hen can breed a duck, a wolf a sheep, or a thistle figs, and therefore one sort cannot be preservative against any other sort." ^ 1 Quoted by Gee, Reynolds' System of Medicine, American edition, 1879, p. 124. ciiiCKF.NPnx 317 In 1707 irehordcn rontribiitcd to tlio flrsl, volmrio of (ho. Transactions of the Royal dollccje of Physicians a carefully [prepared thesis in which he urged the dissociation of smallpox and chickenpox. He employed, however, the unfortunate title of variolw, jmsilhr, ignorin/^ the term varicella which had been introduced a few years before (1704) by Vogel in Germany. His work, though at first strongly criticized, became for many years the acknowledged classic on the subject. The term varicella is a diminutive for varus, a pimple. In Germany, Sennert in 1676 was the first writer to call attention to varicella. In Holland, I)iemerl)roek was the physician to achieve this distinction. In the following century the most important literary contributions were made by Frank, of Vienna, in 1805; AVillan, of London, in 1806; Heim, of Berlin, in 1809; and Mohl, of Copenhagen, in 1817. In 1820, Thomson, of Edinburgh, obscured the comprehension of the disease by reasserting the old doctrine of the identity of variola and varicella, thus leading medical opinion into one of those by-paths which so constantly cross the road of medical progress. And again in 1866 there appeared a champion of the doctrine of unity, in no less a person than Ferdinand Hebra, the great Viennese dermatologist. Hebra regarded varicella as a mild form of smallpox. He wrote: "I apply, then, the name variola vera to the most severe form of this disease, that in which the eruption is abundant and the fever intense, and in which a fatal result is often observed. On the other hand, I use the term varicella for cases in wdiich the rash is very scanty and which run a favorable course and always terminate in recovery." And, again, "There is positive proof that varicella may generate variola or varioloid, and, conversely, variola may produce in another individual varicella." When it is remembered that mild cases of smallpox were regarded by Hebra as varicella the above statements need occasion no surprise. It is difficult to conceive, however, how a close observer like Hebra could have convinced himself that there was no chickenpox distinct from smallpox. Hebra's large experience in smallpox and his fame as a teacher led to an acceptance of his view^s in many quarters. Cursch- mann, writing in 1875, says: "Concerning the relation of varicella to variola, no perfect unity of opinion has yet been reached. While Hebra's view of the close connection of the processes was universally respected until a short time since, and has its supporters even at the present day, authoritative voices are again raised in favor of their separation." Hebra's views were taught by his successor, Kaposi, until his death a few years ago. Kassowitz, of Vienna, has also tenaciously adhered to the view of the identity of smallpox and chickenpox. It is remarkable that a proposition so readily capable of proof as the distinctiveness of smallpox and chickenpox should be repudiated by such eminent teachers and observers. The chief explanation of the astounding assertions they make is the unwarranted use of the term varicella to designate very mild cases^of infantile smallpox. This and 318 " CHICKEN POX the failure to recognize chickenpox as a separate disease account for the discrepancies of these observers as compared with the almost universal teaching. With these few exceptions, physicians throughout the world are agreed that chickenpox is a distinct disease having no relationship whatsoever to smallpox. It would be an act of supererogation at the present day to produce the evidence in support of the duality of these two diseases. ETIOLOGY. Age. — Chickenpox is essentially a disease of early childhood. It is most common between the ag6s of one and seven years. Although it develops at times in infants at the breast, they more commonly escape the infection when exposed to it. The statement made by many authors that chickenpox is excessively rare in adults requires qualification; this view has been so commonly held for many years that we have deemed it advisable to discuss the subject of adult varicella under special caption. We have within a few years seen two score or more cases of chicken- pox in adults, and similar experiences have been recently reported by others. The most advanced age at which we have seen the disease is forty-nine years. The youngest period at which varicella appears to have been observed is recorded by Senator, who saw an infant of eleven days with the disease. The following table, compiled by Gee^ from the records of the Chil- dren's Hospital of London, shows the age incidence among children: Boys. Girls. Total. Under 1 month 2 2 " 2 months 2 6 8 " 3 " 4 9 13 " 6 " 29 28 57 " 12 " 45 52 97 " 18 " 34 28 62 " 2 years 36 39 75 " 3 " 36 42 78 " 4 " ........ 47 53 100 " 5 " 44 52 96 " 6 " 33 25 58 " 7 " 19 11 30 " 8 " 10 19 29 " 9 " 4 6 10 " 10 " 3 2 5 " 12 " 1 6 7 349 378 827 Varicella prevails more at certain times than at others and may occur in epidemics. In large centres of population, however, the disease is like scarlet fever, endemic, and to a certain extent always present. The mildness of chickenpox favors its dissemination, inasmuch as children frequently attend schools while still in an infectious state. ' Loc. cit. ETIOLOGY ?AU Susceptibility is not influencecJ by race, tlic negro and (he C.'aucasian taking the disease with ecjual facility. Neither does varicella seem to be influenced by climate or season. While viiricella, is extremely contagions, its infecting [jower is not as intense as that of measles or smallpox, and it is an easier disease to control by isolation. As far as we know, the infection gains entrance to the individual through the respiratory tract. In the vast majority of cases chickeiipf)x is contracted by direct exposure to a person suffering from the disease. It is not impossibl'e that the affection may be carried by a third person or through the agency of infected objects, but this is in all probal)ility uncommon. It is possible for the disease to be transferred before the appearance of the eruption; this is exemy)lified in the following case: A physiciaji's daugliter, aged sixteen years, developed a slight sore throat and a little fever, and was isolated in a room in the upper story of her home. A small, whitish patch was noticed on the posterior pharyngeal wall. On the following day the eruption of chickenpox appeared. An eight-year-old brother who was with the patient on the previous day was kept in a distant part of the house, out of all communi- cation with the sister or her attendants. Sixteen days after exposure, the same having taken place before the appearance of the eruption, the boy developed chickenpox. It is not surprising that varicella should occasionally be communicated before the appearance of the cutaneous outbreak, wdien we remember that smallpox may be transmitted during the initial stage of the dis- ease. How long a patient remains capable of transmitting the infection has not been definitely determined. Nor is it known whether the infective agent is present in the crusts, as is the case in smallpox. In the absence of positive knowledge on this point, it is wise, in order to prevent con- tagion, to isolate the patient until the skin is entirely free of the original crusts. Crusts due to secondary infection of the skin are not capable of transmitting the disease. Second attacks of chickenpox are of great rarity. Thomas never observed a second attack, an experience which corresponds with ours. Gerhardt is said to have treated a child with three attacks, and a similar observation is recorded by Heim. Vetter states that he saw the child of a physician who had two attacks of chickenpox within fourteen days. Neale^ reports a second attack of varicella after an interval of ten days. Trousseau, Boeck, Kassowitz,Huf eland, and Canstatt have also reported cases. These isolated instances do not, however, controvert the general experience of physicians that one attack of chickenpox, in the vast majority of instances, protects against future attacks. Inoculability of Varicellous Fluid. — Numerous investigators have endeavored to determine whether varicella can be communicated by inoculation. Willan believed that the disease could be thus trans- 1 Lancet, 1S91, ii. 320 CHICKENPOX mitted, but Gregory remarks that "his experiments are few and, to my mind, unsatisfactory." Bryce, of Edinburgh, in 1816, made extensive trials, with negative results. He states^ that he has inoculated with the fluid of varicella vera, at all periods of the disease, and at all seasons of the year, children who had never undergone either smallpox or cowpox, and yet he had never been successful in producing from it either variola or varicella. Delpech, in 1843-44, attempted to inoculate patients with varicella at the Hospital Necker in Paris, but with unsuccessful results.^ Hessa^ compiled data of 113 inoculations with varicellous fluid; in 87 of these no result was obtained, in 17 there was merely a local manifestation, and in 9 cases a general eruption ensued. Thomas obtained negative results in his inoculations and mentions the fact that Heim, Vetter, Czakert, and Fleischmann. had similar experiences. J. Lewis Smith in this country likewise failed in his attempts to transfer chickenpox to children who had never had the disease. Steiner* obtained results very different from those above referred to. He claims to have inoculated ten children, eight of whom developed typical chickenpox. The time elapsing between the inoculation and the appearance of the eruption in these cases was eight days. If the possibility of transmission of the disease in the usual manner was entirely excluded in Steiner's cases, his observations go very far toward proving that chickenpox can be communicated by inoculation. In view, however, of the negative results obtained by nearly all other investigators, future experiment will be necessary to confirm the successful inoculations obtained by Steiner. Period of Incubation. — The stage of incubation of chickenpox is ordinarily longer and more variable than that of smallpox or measles. Different observers assign rather variant limits to this period, as will be seen by reference to the following quotations : Gregory^ says "it does not exceed four days and is certainly less than a week;" Heberden^ places it at eight or nine days; Trousseau,'^ "fifteen to twenty-seven days;" Gee,^ "at about a fortnight;" Thomas," thirteen to seventeen days; Delpech, twelve days; Holt,^° "quite uniformly from fourteen to sixteen days;" Corlett,^^ ten to nineteen days. Our experience would lead us to regard fourteen to seventeen days as the usual period, although we have observed it to extend over nineteen days and even as long as twenty-one days. It is possible that in rare cases it may be less than ten days and longer than three weeks. In 16 cases occurring in an outbreak in the Municipal Hospital we 1 See Thomson on Varioloid Diseases, p. 74, quoted by Gregory. 2 Quoted by Gregory. ^ Ueber Varicellen, Leipzig, 1829. 1 Wiener med. Wochen., 1875, No. 16. 5 Lectures on the Eruptive Fevers. First American edition, 1851, p. 295. 6 Quoted by Gee. Loo. cit. ^ Lectures on Clinical Medicine. American edition. Philadelphia, 1882, p. 136. 8 Reynolds' System of Medicine. American edition, Philadelphia, 1879, p. 125. 5 Ziemssen's Encyclopedia of Medicine. 10 Diseases of Infancy and Childhood, p. 929. " Acute Infectious Exanthemata, p. 165. H,YMI'T()MA TOLOCIY 321 were able to fix the hiciihation stage quite accurately. Tlie periofls were as follows: i:i (lays in . . 1 case. 1« 'lay.s in . .1 case. 14 " . . 7 cases. !'•• " ■ . I " 15 " . . 3 " 'il " . . I " 17 " . . 2 " Stciiier, who claims to have successfully iuoculatefl varicella in ei^'ht patients found the incubation stage in these patients to be uniformly eight (lays. During the incubation period there are, as a rule, no evidences of disturbed health. Now and then, however, as in some of the other exanthemata the breeding of the disease may give rise to slight symptoms, such as loss of appetite, lassitude, and general inclisposition. SYMPTOMATOLOGY. Pre-emptive Stage. — In the vast majority of cases chickenpox is not preceded by a ])rodromal illness. The onset of the constitutional manifestations is usually coincident with the appearance of the eruption. The ordinary history elicited from mothers is that the eruption is the first symptom to attract their attention, and that the children are not ill prior to this time. At the Municipal Hospital we have had the opportunity of studying the temperature records of a number of chickenpox patients before the appearance of the eruption; these patients were convalescent from scarlet fever when they developed varicella. In almost every instance the temperature remained about normal until the chickenpox eruption appeared and, indeed, in some cases even after the lesions had developed. In a small percentage of cases some little constitutional disturbance may be observed a day or two before the appearance of the exanthem. This consists of slight rise of temperature, anorexia, vague pains, and chilliness. More common is it to discover these symptoms a half-day or so before the eruptive outbreak. During the night preceding the appearance of the exanthem the child may be slightly feverish and restless. But these mild precursory symptoms should not be regarded as representing a prodromal illness, for by this term as applied to smallpox is meant a distinct stage preceding by two or three days the onset of the eruptive phenomena. It is important, however, to call attention to the fact that varicella in adults may occasionally be preceded by a prodromal stage. While most of these patients give no history of a pre-emptive illness, a minority of them will volunteer such information. We have seen perhaps a half- dozen of adults suffering from varicella who had distinct prodro- mata. These symptoms consist usually of chilliness, lassitude, anorexia, nausea, slight headache and backache, and some elevation of temperature (101° to 102° F.). These manifestations may precede the appearance of the eruption by two or three days, though more often not longer than twenty-four hours. It is rare to observe high fever, vomiting, severe lumbar pain, and prostration — symptoms which usher in a well- pronounced smallpox. 21 322 CHICKENPOX In general, it may be said that a true prodromal stage in children suffering from chickenpox is extremely rare; in adults it is by no means so infrequent. When it does occur it is much milder than the prodromal illness ordinarily observed in smallpox. A prodromal erythema is, in rare cases, seen before the appearance of the varicellous eruption, as it is at times before the eruption of smallpox and measles. Thomas observed "just before the outbreak of a light case of varicella with ephemeral though intense fever (105.8° F., rectal temperature) the appearance of a universal erythema of short duration." He adds, however, that although he watched carefully for these eruptions this was the only one he ever saw. Henoch is also said to have seen and described such an erythema. A prodromal scarlatinoid rash preceding the appearance of the varicella eruption was observed by us in a patient admitted into the scarlet-fever ward of the Municipal Hospital in the early part of 1902. A girl, aged five years, was sent to the hospital from a large foster home. She had had vomiting, some elevation of temperature, and on admission there was a diffuse scarlatiniform rash covering the entire trunk. This resembled scarlet fever so strongly that an experienced interne regarded it as the scarlatina exanthem. The rash faded in the course of twenty-four hours and was followed by the appearance of a number of varicella vesicles. At the end of five days after admission to the ward, a rise of temperature to 103° F. occurred, accompanied by sore throat and a well-pronounced and typical scarlet-fever rash. It was evident that the child contracted scarlet fever in the ward. No scarlet fever existed in the foster home from which the child was received. The Eruptive Stage.- — As has been stated, the eruption is commonly the first symptom to attract attention to the disease. Synchronously with the appearance of the cutaneous outbreak, or a few hours before or afterward, a varying degree of fever sets in. In some cases this does not reach higher than 99° F. ; in others, however, the pyrexial elevation may be most marked. Thomas records one case in which the initial temperature was 105.8° F., and we have on several occasions observed temperatures of 104° and 105° F. This high fever is, as a rule, of brief duration, subsiding in twelve or twenty-four hours to 99° or 100° F. High fever does not necessarily presage the development of a profuse eruption. We have seen a temperature of 104° in a case with scant and abortive lesions. The temperature commonly falls to normal in the course of one to three days. Where the eruption is copious, however, moderate fever may persist for four or five days. In cases in which the varicellous lesions become secondarily infected, the temperature may continue above normal for a fortnight or even longer. The Eruption. — The eruption of chickenpox usually appears first on the back or the face, although other regions may be the seat of the initial lesions. Irregular extension then occurs, new lesions developing on different portions of the cutaneous surface. The hairy scalp is nearly always beset with^some vesicles. SYMPTOM A TOLOaV 323 The distribution of ilic eruption is subjec^t to soino varialioii, hut is tolerubly uniform in the majority of cases. 'J'fie trunk, particularly the hack, is relatively more profusely attacked than the distal portions of the extremities — the wrists, ankles, hands, and feet. The face usually presents a moderalo iiumhcr of discrete vesicles. It is rare for the face to escape coiiij)lc(cly, altlioiif^h at times hut two or three lesions may he present. At other times, in copious eruptions, quite an al)und- ance of lesions may he seen on the face. The arms and legs are seldom j)rofuscly attacked except in unusually extensive cases. It has heen clainicd hy some writers that varicellous lesions do not occur upon the palms and soles. It is true that in most cases the palmar and plantar surfaces are free of eruption; hiit it is hy no means rare Fig. 55 Chickenpox lesions in the crusted stage, about the fourth day of the disease. to find a few vesicles in these regions, and in severe cases the lesions may be fairly numerous. The palms and soles are much less frequently and less abundantly involved than in smallpox, in which disease some lesions are nearly always present in these regions. The dorsal surfaces of the hands and feet are likewise relatively lightly affected compared vnth the general extent of the eruption. In fact it may be stated that the distal portions of the extremities usually suffer but little in chickenpox; the eruption prefers the covered surfaces. The distribution of the eruption may, to some extent, be influenced by ixritation of the skin prior to the appearance of the lesions. We have seen a profuse crop of lesions develop over a rectangular area on the sternum to which a mustard plaster had been applied during the pre-eruptive period. Any irritant by increasing the vascularity of 324 CHWKENPOX the skin may attract lesions to the region thus irritated. It is not so common, however, to observe an increase of the eruption from this cause as it is in smallpox. In the latter disease the influence of cutaneous congestion in determining an increase of the eruption in a given area is emphasized by frequent experience. Ordinarily by the time that the physician is called to see a child with chickenpox vesicles are observable upon the body. If the skin is carefully examined early it will be noted that the vesicles are usually preceded by erythematous spots. These are pea to bean sized, rosy red in color, and in appearance not unlike the rose spots of typhoid fever, or fleabites. Very soon the centres of the macules become raised and small vesicles are formed which rapidly increase in size. In some cases the rosy macules are elevated, somewhat acuminated, and in reality represent papules. The duration of the transitional lesions before vesiculation takes place is extremely variable. At times some of the lesions of varicella abort in the macular or papular stage and never go on to the develop- ment of vesicles. Indeed, Thomas mentions a case, the nature of which was verified by the previous occurrence of varicella in a sister, in which erythematous spots (roseolse) persisted for thirty-six hours and then disappeared without the formation of any vesicles whatever. Varicella without the development of vesicles must, however, be extremely rare. Varicellous vesicles may spring up so rapidly that they appear to arise directly from the normal skin. We were enabled to determine in one instance that vesicles developed in less than four hours. A trained nurse bathed a child at 11 a.m. and carefully examined the skin for an eruption v/ithout discovering any. At 3 p.m., four hours later, we examined the child and found several fully formed, tense, varicellous vesicles on the trunk. The lesions often look as if they had been produced by drops of scalding water sprinkled upon the skin. They are superficially situated, differing in this respect from the deeper-seated vesicles of smallpox. The epidermal roof of the vesicle is thin and readily ruptured. The vesicles of chickenpox vary greatly in size; they may be no larger than a pinhead, or they may reach the dimensions of a large pea. They are commonly tense, although rarely as hard as the variolous vesicle. Slight traumatism, such as is produced by scratching or the friction of clothing, sufifices to rupture the vesicle. The fluid from an early vesicle is clear and watery in appearance; later it becomes turbid or lactescent. The vesicles are round or oval, the shape being some- what determined by the lines of cleavage of the skin. In the axillary and lateral costal regions they are commonly oval, the long axis corre- sponding with the direction of the ribs. Chickenpox vesicles are commonly surrounded by a reddish areola. This may be narrow, measuring but an eighth of an inch; in other cases, however, it may have a breadth of a half -inch or more. Much diagnostic value has been attributed by some observers to the comparative degree of evacuation of chickenpox and smallpox PLATE XL. A Severe Attack of Chiekenpox, showing Lesions in Various Stages of Development (fourth day). Relative sparsity of lesions on the face as coin pared with the trunk. HYMI'TOMA TOI/XiY ;i2o vesicles effected by })uncturin^ llicin willi ii nccHlc. While- il is tnie tliat the varicella vesicle is often coiiiplclctly crnpficd, aiul the variolous vesicle, owiiif^ to its more niultilociilar striicliire, less cotripletely evao uated, hut little value should be phu-ed upon this test. There is too much latitude j)ossibIe in the iiiterprcliilion of the deforce of evacuation effected. s The eru|)tion of chickcii])ox ii,j)pcafs in crops-. 'J'he first outbreak couiinonly consists of a do/en to fifteen lesions. After an interval of some hours, usually a day or so, a second crop appears which often numerically exceeds the first. Twenty-four hours later a third out- break may occur and new lesions may thus continue to appear for four or five days or even a week. Owinfi^ to the fact that the lesions are of ditt'erent age, they are seen in varying stages of evolution and invo- lution. There may be present at the same time small, new, tense vesicles ; older, drying vesicopustules, and, in addition, dark-colored cni.sts which represent the remains of the first vesicles. This multifoi-mity is one of the most distinguishing features of the eruption of chickenpox. The duration of the individual lesions of chickenpox is brief. The vesicles, after reaching the acme of their development, become flaccid, and in from one to three days dry into crusts. The unruptured vesicle desiccates first at its central summit. Lesions which are ruptured by mechanical force give exit to a fluid which forms an irregularly shaped crust. The fluid contained in the vesicle is at first as clear as w-ater; it later becomes turbid and finally, if unruptured, quite purulent. During these changes the vesicle which has in the beginning a "dewdrop-like" appearance acquires a grayish or yellowish color. True umbilication, such as is seen in the early smallpox vesicle, does not occur in chickenpox. There is sometimes seen a pinpoint-sized invagination of the surface of a vesicle due to the presence of a hair follicle. Commonly there is observed a central sinking in of some of the vesicles or vesicopustules due to partial evacuation and central drying. This is also seen in the late pustular stage of smallpox, and might be called a secondary umbilication. As the vesicles of chickenpox begin to dry there not infrequently develops a flat, vesicular, spreading ring upon the border of the crust; beneath the raised-up epidermis is a little puriform fluid. The lesions may, as a result of this process, spread to the size of a silver quarter or half dollar. This condition is extremely common in smallpox and has been called "impetigo variolosa." The process being the same in chickenpox, the condition might be appropriately designated "impetigo varicellosa." The cause of these spreading sores is an infection of the varicellous sites with streptococci and staphylococci present upon the surface of the skin. In extensive eruptions where there is much of this impetigo, moderate elevation of temperature may develop, giving rise to a secondary fever. The extent of the varicellous eruption is extremely variable. The total number of lesions in some cases mav amount to but a half-dozen; 326 CHICKENPOX on the other hand, they may cover almost completely the entire cutaneous surface and number hundreds or even thousands. Thomas says, "as many as eight hundred have been counted or estimated." In a copious eruption in a young boy we counted one thousand four hundred lesions; shortly afterward in an older lad convalescent from scarlatina we encountered a much more extensive eruption. A photograph of this boy is shown in Plate XLII. We estimated that there were in the neighborhood of three thousand lesions upon the skin. While neighboring and closely set vesicles may occasionally coalesce, one never sees a confluence of the lesions such as is observed in smallpox. Scarring After Varicella. — It is not uncommon for some varicella lesions to be followed by scars. Indeed, it is rather the rule for patients to have one or several cicatrices which persist after the disappearance of the eruption. These are from pinhead to pea sized, rounded or oval, and excavated to a variable degree. In severe cases the number may reach a half-dozen or a dozen or more. They are never, however, as numerous as is seen in smallpox. The scars result from a destruction of the papillary layer of the true skin; this may be due to secondary infection as a result of scratching, but it may occur entirely apart from this cause. Chickenpox vesicles at times break down early and produce a necrosis of the underlying corium; the ulcer left heals with the form- ation of a depressed scar. Occasionally a hypertrophic scar or sort of keloid forms at the site of these losses of tissue. The mucous membranes are not infrequently the seat of varicellous lesions. It is quite common to find a few vesicles upon the soft and hard palate, and these in doubtful cases are of diagnostic importance. Lesions are also occasionally noted upon the buccal mucous membrane, tongue, and posterior pharyngeal wall. Situated in these regions the flaccid roof of the vesicle soon ruptures, leaving at first a grayish peUicle of epithelial debris and later a circumscribed superficial abrasion, surrounded by a reddish areola and resembling to some extent the sore of aphthous stomatitis. The eruption in the mouth is usually scant, even in cases characterized by an abundant cutaneous outbreak. The exanthem, as a rule, appears synchronously with the eruption on the skin, but it may precede it. We know of a colleague who was perplexed by the appearance of a circumscribed patch on the posterior pharyngeal wall of his daughter, but who later discovered that it was an early varicellous lesion preceding the general eruption by about twelve hours. Henoch has seen varicellous vesicles on the gums and also on the conjunctival mucous membrane. Thomas observed the latter attacked only when the contiguous portion of the eyelid was affected. He likewise under similar conditions noted involvement of the nasal mucous membrane. Marfan and Halle have recorded two cases of involvement of the larynx, one necessitating tracheotomy. The other case succumbed to other complications and on autopsy the remains of a vesicle were found on the right vocal cord. PLATE XLF. An Unusually Extensive Eruption of Chiekenpox in which the Lesions -were Estimated to Reach SOOO in number. ,S' Y M I 'TO MA TOfAXl V 327 Varicelloiis lesions arc occasionally found in flic; vc;stil)ule of the va<);ina Jind upon the prepuce, in wliich regions the accompanying swelling mjiy cause difficulty in micturition. As far as is known, chickenpox never attacks the mucous membrane of the slonKich or intestines. Partridge, in 1SS7, prcscnicd to the New York l*ii,th()logi(;al Society specimens from a child that hainrnonly complicates varicella.' In mild cases but one or several varicellous lesions may undergo necrosis; in more extensive cases many of the vesicles become involved. The vesicle may either become converted into a bleb, the gangrenous process beginning beneatli this epidermal elevation, or the vesicle may dry into a dark crust and enlarge uj)on th(^ j)eriphcry. I'pori removal of the crust a sharply marginated, punched-ont, freely discliarging ulcer is seen. A dusky-red areola surrounds the ulcer or eschar. In extensive cases the temperature rises to 104° or 105° F., and the patient rapidly sinks. ■ Ivung complications, particularly pulmonary infarction, are common. Mild cases of gangrene may recover. The affection is most common in debilitated infants, more especially those in whom the varicella is preceded by some other illness. In Griffith's case the chickenpox was preceded by measles, diphtheria, and pneumonia. Cases of gangrenous varicella have been reported by Hutchinson, Demme, Abercrombie, Andrew, Crocker, Biichler, Jamieson, Lowen- hardt, Payne, Stanifooth, Haward, Vierordt, Griffith, Lockwood, Silver, Woodward, and others. We have, on several occasions, observed localized gangrene occurring at the site of smallpox pustules; these cases all terminated fatally. Stokes,^ of Dublin, reports a case of vaccinia gangrenosa ending in recovery. Synovitis and Arthritis. — Synovitis and arthritis have been reported as rare complications. Laudon^ and Ferret' have both published examples of joint involvement in chickenpox. The patient of the former, a boy aged four years, developed high fever early in the course of varicella, followed by marked swelling of the left elbow-joint. Re- covery took place after several weeks. Semtschenke, quoted by Rille, saw 2 cases of purulent pleurisy and purulent arthritis in an epidemic of chickenpox in Russia. Hogyes reports a case of varicella in a seven-year-old girl followed by nephritis and subsequently by an inflammation of several joints, accompanied by high fever and ending in recovery. Braquehaye saw a purulent arthritis of the knee and elbow develop on the ninth day of a varicella which w^as apparently running a normal course. Despite incision and drainage death resulted. On autopsy a septic endocarditis was also discovered.^ Marfan and Halle" describe 2 cases of serous involvement of the larynx through the presence of varicellous vesicles. In one case, in a boy of three years, tracheotomy was performed, the patient recovering. In the other, a child of nine months, with a well-marked chickenpox, developed 1 An excellent description of this afiection is given by Crocker under the title o." "Dermatitis Gangrsenosa Infantum." Text-book of Diseases of the Skin. American edition, 1903, p. 535. - Dublin Journal of Medical Sciences, June, ISSO. ^ Deutsche med. Wochenschrift, Leipzig, 1890, xvi. p. 5G7. * Province mt>d. Lyon, 1SS9, iii. pp. 256-261. 6 Quoted by Brown. Twentieth Century Practice of Medicine. 6 Quoted by Brown. Ibid. 332 CHICKENPOX stridor and dyspnoea; diphtheria bacilli were absent. Bronchopneu- monia and diarrhoea supervened and death resulted; the post-mortem examination revealed the presence on the right vocal cord of a round, shallow ulcer, evidently the remains of a varicella vesicle. Nephritis. — Nephritis is one of the most serious of the complications and sequelse of varicella. While it occurs in only a very minute per- centage of cases, there are in the literature a sufficient number of recorded instances to cause physicians to keep in mind the possibility of its development and to watch the kidneys in the treatment of this otherwise trivial disease. Henoch^ was one of the first to mention nephritis as a complication and reported 4 cases following chickenpox. Janssen,^ Hogyes,^ Oppen- heim,* Brunner,^ Unger,® Rille,^ Schwab, von Jiirgensen^ and Dillon Brown'' have all described similar cases. The nephritis usually comes on during the first or second week of the disease. It varies in severity as does this complication in other infectious diseases. In severe cases an abundance of albumin and tube casts may be present in the urine. As a rule, the nephritis is mild, recovery taking place promptly. Dillon Brown, however, reports a case in which the kidney involvement after a mild attack of varicella ran a chronic course, ending fatally some ten years later. Ildgyes' case terminated fatally through complication with pneumonia, and Rille reports an uncomplicated nephritis ending in death and showing on autopsy parenchymatous changes in the kidneys. Bronchitis and Bronchopneumonia. — Bronchitis and bronchopneu- monia are mentioned as complications by Meigs and Pepper, and Rille reports a peculiar form of pleuropneumonia ending fatally on the nineteenth day after varicella. Association of Chickenpox with Other Exanthematous Diseases. — It is not at all uncommon for varicella to develop during convalescence from other acute exanthematous diseases, such as measles, scarlet fever, smallpox, etc. On the other hand, these diseases may develop in patients suffering from varicella. It is rather rare for these eruptive diseases to be synchronously present in their acutest stages; usually the second disease appears as the first is beginning to decline. Chickenpox has repeatedly broken out in the diphtheria and scarlet- fever wards of the Municipal Hospital. Under these circumstances the varicella would naturally appear not earlier than the end of the second week of the original disease. We have often seen varicella appear in scarlet-fever patients who were profusely desquamating. We have also observed these two diseases present at the same time with vaccinia. 1 Berliner klin. Wochenschrift, No. 2, January, 1884. - Nedre. Tijdsch., 1884, B. xx. p. 223. 3 Orvosi hetil., Budapest, 1885, xxix. pp. 11-16. * Berliner klin. Wochenschrift, December 26, 1887. 5 Aerztl. Mitth. a-Baden, Karls nute, 1888, xlii. pp. 49-52. 6 Wien. med. Presse, 1888, xxix. pp. 1449-1451. 7 Wien. klin. Woch., 1889 ; Deutsche med. Woch., 1891. 8 Nothnagel's Encyclopedia of Medicine. Article on " Varicella." 9 Twentieth Century Practice of Medicine. Article on " Varicella." (]()MI'IJ(!.\TI()NH AND Sf'Xjff I'JL.f: OF ('II K' K ICS I'OX ,'},'J.^j Chickenpox may af)|)ciir diiiiiif;- coiivalcsccnfc from smjillprjx. 'I'lif foll()winox at an early age. During the eighteenth century epidemics of scarlatina were observed in all parts of Europe. A severe epidemic of scarlatina prevailed in Lon Quoted by Thomas C. Minor, in a report to the American Public Health Association, 1875. 344 SCARLET FEVER ETIOLOGY. Despite the fact that the causative agent of scarlet fever has not yet been discovered, the statement may be made that the disease is produced by a specific micro-organism. Scarlet fever is so similar in its behavior and manner of transmission to other infectious diseases of proven parasitic origin that, reasoning by analogy, we are irresistibly forced to this conclusion. Not many years ago it was maintained by writers that cases of scarlet fever could arise de novo, independently of pre-existing cases. The spontaneous origin of infectious diseases is no longer credited by medical scientists of the present day. The channels of infection are often so devious and the manner of transmission so mysterious as to make the origin of these diseases in individual instances quite incomprehensible. But the mystery of an infection is dispelled and becomes as clear as the trick of the magician when the solution is at hand. The proposition may, therefore, be accepted that every case of scarlet fever has its origin in an antecedent attack in another individual. Modes of Transmission of the Scarlatina Contagium.— The germ of scarlet fever is chiefly if not exclusively conveyed in two ways: (1) directly from a scarlatina patient to the newly infected subject, and (2) through the intermediation of infected objects. The vast majority of cases of scarlatina doubtless result from exposure to persons suffering from the disease; this is freely admitted. A certain school of German writers, led by von Kerchensteiner, maintains that the disease cannot be conveyed hy a third person. The clinical experience of numerous careful observers is strongly opposed to such an opinion. Indeed, there are recorded instances of such transmission which appear quite conclusive. Dr. Loeb, of Worms, mentions the case of his three-year-old daughter who developed scarlet fever at a time when there were no known cases in the city. The origin of the infection was a mystery until it was discovered that a medical friend and colleague who had been at the house, and upon whose lap the little girl had sat for a long time, had some hours previously visited three cases of severe scarlatina in another city and had not changed his clothes. The disease manifested itself at the end of two days. The circumstances surrounding the case would seem to point in the strongest manner possible to the conveyance of the germs in the clothes of the physician. Thomas saw a case "in which a nurse coming directly from a scar- latinous patient communicated the disease in the short space of three hours to a child who had almost recovered from a tracheotomy." He also quotes Zengerle to the effect that a healthy woman, after a visit to a scarlatinous patient, transmitted the disease to her daughter, who was the first patient affected in the whole city. Murchison was con- vinced, from the testimony he had received from numerous physicians, that the scarlet-fever infection was not rarely carried by them. The infection commonly clings to objects which have come in contact with the scarlet-fever patient, such as bedding, clothing, books, letters, ETIOLOGY 345 toys, etc. Numerous instances are recorded in which such articles have transmitted the infection. IJotli Tiic-htirdson and Peterson traced cases of scarlet fever to infection transjnilled in letters. It is an important matter in infectious-disease hospitals that all outgoing mail lie thor- oughly disinfected. The scarlet-fever contagium may cling tenaciously and for a long time to the sick-room and to certain objects contained therein. Murchison, on the testimony of Richardson, mentions an extremely sad illustration of this. A child having been seized with a fatal attack of scarlet fever in a country house, the three remaining children were fjuickly removed. After a lapse of several weeks one child that was brought home con- tracted in twenty-four hours an attack of scarlet fever to which he rapidly succumbed. The house was then thoroughly cleaned and the walls whitewashed, but the infection was not removed, for a third child that returned after four months took the disease and died in the same manner as the others. It is believed that the infection was retained in a thick layer of straw covering on the children's beds. Von Hildebrand claims to have contracted the disease from a black coat which he had worn a year and a half before while attending a case of scarlet fever in Vienna. The most remarkable claim of longevity of the scarlet- fever infection is mentioned by Boeck (quoted by Johannessen, loc. cif.), who relates the circumstance as follows: "The children of a colleague of mine had obtained permission to play with some things in an old writing desk. In a drawer lay some hair that had been cut from two children that had died of scarlet fever tiventy years before; since that time the drawer had not been touched. Now it was opened and the children took scarlatina. These cases were the first in the city, so that the probability is evident that the infection was transmitted in this way." Immunity and Susceptibility.— There is no such universal suscept- ibility of persons to scarlet fever as is known to exist toward measles and smallpox. Experience teaches that but few people enjoy a natural immunity against these latter diseases. Many persons, however, escape contracting scarlet fever even though freely exposed to its infection. The contagion of scarlet fever is a most ca'pricious one; it may repeat- edly spare an exposed individual and lead him to believe that he is immune against it, only to smite him at some subsequent period. This temporary immunity against scarlet fever has been repeatedly noted by various observers. Nurses have frequently been observed during the closest attendance upon patients suffering from scarlet fever to remain free from infection, and yet later contract the disease. Such a case has recently come under our observation: Mrs. X., aged thirty years, a private trained nurse, was brought into the Municipal Hospital on January 9, 1903, suffering from a well- pronounced attack of scarlet fever. She had never had the disease in childhood. During the past few years she estimated that she had nursed about fifteen cases of the disease. On November 17, 1902, she com- 346 SCARLET FEVER pleted her service in connection with a severe case of scarlet fever in the suburbs of Philadelphia. A little over six weeks later she began to nurse a patient with puerperal scarlet fever. After being on duty four days she herself was taken with a scarlatina of average severity, which ran a typical course and was followed by profuse desquamation. We recall the case of an ambulance driver at the Municipal Hospital who came in almost daily contact with cases of scarlet fever, and who finally at the end of several years contracted a well pronounced attack of the disease. On another occasion one of the nurses at the Municipal Hospital contracted a well marked attack of scarlatina on returning to duty in the scarlet-fever wards after a year's absence. Prior to her departure she had nursed mixed cases of diphtheria and scarlatina for a period of three months. It would appear in these cases that for some reason or other the resisting power of the subject is lowered at the time of infection; this explanation seems to us to be more plausible than the assumption that the attack is determined by an unusually intense infective agent. In some instances it would appear that the temporary immunity against scarlet fever is overcome by infection through unusual channels. The puerperal state and surgical operations are said to favor the develop- ment of the disease. Von Leube^ gives an interesting account of an attack of scarlatina in his own person following a wound received in making an autopsy upon a patient who had died of an unusually severe case of scarlet fever. He states that he had considered himself perfectly immune, having been exposed as a child, and having attended any number of cases under all sorts of circumstances. Ten days after the post-mortem wound upon his finger he developed sore throat, and on the following day he vomited, had a "decided fever," and the scarlatina rash. The course of the disease was one of medium severity. The susceptibility to scarlatina commonly disappears in adult life; at any rate, many adults who have never had the disease escape infection, although freely exposed. Patients suffering from scarlet fever have on numerous occasions been placed in the wards of general hospitals without appearing to disseminate the disease among other occupants of the ward. Such experiences illustrate the very limited suscepti- bility of persons who have passed the age of puberty. During the past few years the students of the various medical colleges in Philadelphia have been conducted through the wards of the Municipal Hospital in order to study the various infectious diseases therein treated. About 700 students in all have taken advantage of this bedside instruc- tion. They were taken into the scarlet-fever wards in which there were 100 or more cases of this disease, and remained from one to two hours in this intensely infected atmosphere. About one-half of these students, according to their statements, had never had scarlet fever, and yet not a 1 Specielle Diagnose der inneren Krankheiten, Bd. ii. p. 364. Leipzig, 1893. ETIOLOGY 347 single one contracted the disease. Tliis is strong proof of (lir; frequent ahrf)gation of the siisc<>|)lil)iliiy of adults to scarlet f(!ver. Epidemics Among Adults. — VogI,' of the (j(;rieral Medical Staff of Bavaria, reports two epidemics of scarlet fever among the Bavarian troops at Munich. In 1884-S5, during a garrison epidemic covering a period of ITSdays, 125 out of 7442 soldiers, or 1.07 per cent., contracted the disease. The mortality rate was 4 per cent. In 1804-95, during a similar epidemic lasting 155 days, 311 out of OfiOS troops, or 3.23 per cent., took scarlatina, of whom 1.2 per cent, dierl. The attack rate among exposed adults is thus seen to be very small. Murchison estimated that the number of persons attacked with scarlet fever in England and Wales was considerably less than one-half of the number of l)irths. It is evident, therefore, that the lessened susceptibility to scarlatina exhibited in adult life is not entirely due to protection granted by an attack in childhood. This is also shown by the figures of scarlatina in virgin countries. From 1873 to 1875 an extensive epidemic^ of scarlatina raged in the Faroe Islands. The disease had not been known in this locality for fifty-seven years and possibly had never occurred at all. From the carefully collected data of Hoff concerning the town of Thorshavn, the chief city of the islands, it is seen that of a population of 930 persons, 237 contracted the disease. Among the entire inhabitants of the islands, of whom none had ever had scarlatina, but 38.3 per cent, contracted the disease during this protracted epidemic. Age. — Age is a most pronounced factor in the determination of susceptibility to scarlet fever. It is a general experience that infants under one year of age exhibit a lessened disposition to contract the disease; this is still more true of nurselings under six months, and in infants under three months of age scarlatina is excessively rare. The infrequency of the disease at this tender age may be judged by the statements of experienced observers in reference thereto. Fleischmann^ saw no cases under six months of age; Eulenberg, none under eight; Thomas, none under five; Boning saw no cases under one year; Senfft saw but one patient under one year, and Gaupp only two. Haller observed a case at five months; Voit, one at two and a half months; Kiipfer, one at two months; and Veit, one at two weeks. This represents an extremely scant number w^hen the large number of cases of scarlatina observed by these men is taken into consideration. In Johannesen's statistics of scarlet fever deaths in Norway from 1862 to 1878, the number of infantile attacks is considerably greater. He reports 15 deaths from scarlatina under six months, and 93 under one year. In our own experience at the Muincipal Hospital we have found that among 5000 cases of scarlet fever admitted into the hospital, about 1 per cent, consisted of infants under one year of age. We have on a number of occasions had infants a few months old brought into the 1 Miinchener med. Wocli., 1895, p. 949. - Mentioned by von Jurgensen in Nothnagel's Encyclopedia of Practical Medicine. 3 Mentioned by Thomas in Ziemssen's Encyclopedia of Practice of Medicine, p. 180. 348 ^ SCARLET FEVER hospital with mothers suffering from scarlatina, but we have seldom observed them to contract the disease. We have seen them suckle at breasts covered with the scarlatinal rash, draw a febrile milk, and yet remain perfectly well. The question whether there is a congenital scarlatina is most difficult to answer. Children are so commonly ushered into the world with a red rash that but little reliance can be placed upon the existence of an exanthem. Furthermore, it is not uncommon for the tender epidermis of the infant to peel off after some days and thus cause a desquamation. Baillou, Ferrario, Stiebel, Hiiter, and others saw infants that were alleged to have scarlatina at birth (most of them being born of mothers suffering from scarlet fever at the time), but the facts do not appear to us to warrant the unreserved acceptance of the diagnosis. Murchison saw two pregnant women with scarlet fever, and in each case the child born at the time was free of the disease. Elsasser also saw a healthy babe born of a mother with scarlatina. Children from two to five years of age appear to be most susceptible to the contagium of scarlatina. From five to ten years the attack rate is somewhat less, and after the period of puberty is reached the suscept- ibility to the disease is greatly lessened. No age, however, appears to guarantee absolute immunity against scarlatina inasmuch as persons even over the age of ninety-five have been known to contract the dis- ease. Murchison's valuable statistics of scarlet-fever deaths in England and Wales, covering the enormous number of 148,829, will give a fairly accurate idea of the incidence of the disease in the different age periods : Under 1 year 9,999 or 6.7 per ct. From 1 to 2 years 20,975 " 14.1 2 " 3 " . 23,842 " 16.0 3 " 4 " 22,528 " 15.1 4 " 6 " 17,726 " 11.9 5 " 10 " 38,591 " 25.9 " 10 " 15 " 8,676 " 5.8 Total under 5 years 95,070 or 63.8 per ct. From 5 to 15 years 47,267 15 " 25 " , . 3,871 " 25 " 35 " 1,306 35 " 45 " . . 671 " 45 " 55 " 331 55 " 65 " 185 " 65 " 75 " 88 " 75 " 85 " 30 " 85 " 95 " 4 Over 95 " . ; 6 Total 148,829 It will be seen from the above tables that considerably over one-half of the deaths of scarlatina occurred in children under five years of age. Almost 90 per cent, occurred in those under ten years, and over 95 per cent, under fifteen years of age. These figures correspond very closely with statistics of scarlet-fever deaths in Berlin from 1875 to 1891, and with Johannesen's statistics for ETIOLOGY :W.) Norway. As showing the fatal cases in cliildrcii.iKKler ouc yrar, the latter statistics are of particular interest : Fatal Cases of Scarlatina in CuRisTrANA (Jndkk Onk Ykarch Af;K, (JOHANNESEN.) iBt month 2(1 to 3d month .'{ 4th " f)th " 12 7th " 12th " 78 The above deaths were out of a total of 1040 fatal cases. Family Predisposition. — Some families, at times, exhibit an unusual susceptibility to scarlatina; this is manifested not only by several mem- bers of the family contracting the disease, but likewise by the severity of the attack. Thomas^ recognizes "an intense family predisposition, showing itself by numerous and severe attacks in the family as soon as one infection has taken place in it." Trousseau says: "Scarlatina epidemics may be full of danger for an entire population, or they may assume this character only for a single family. The malignancy limits itself in a measure to a single hearth, and in such cases the disease is malignant for all persons that live within its circle." Henoch^ expresses much the same idea; he says: "Striking to me appeared the fact that if scarlatina breaks out in a family, very frequently also a second and third child are taken off under similar conditions, and in this way whole families can die out." Copeman,^ during a severe epidemic of scarlet fever in 1844, saw four children in a family die so suddenly that poisoning was suspected ; a fifth child went through an ordinary attack of scarlet fever. A somewhat similar instance has recently come under our observation. In the winter of 1902 we saw a family in which four children were smitten with scarlet fever. All fell suddenly ill with vomiting, which was attributed by the mother to free indulgence in candy. Soon the scarlatinal rash manifested itself. The eldest daughter, a girl of seven- teen, died in five days; a second one had a temperature of 105° F., with intense prostration, and recovered, as did a third child, only after a most desperate illness. The infection in these cases was most viru- lent, and yet the prevailing type of scarlatina in the city at that time was quite mild. These severe family epidemics are difiicult to account for. Henoch presupposes a mixed infection in such cases. Thomas does not seek an explanation in an unusually intense infection, for he says "the infecting cases are frequently of a mild character." Epidemics of this character are happily uncommon. In some instances there is a tendency to family immunity, the members thereof exliibiting an almost complete insusceptibility to the disease. Climate. — Accordingto INIinor,^ who has in a most painstaking manner studied the prevalence of scarlatina in the United States, climatic con- ditions influence the spread of the disease. He says: 1 Loc. cit, p. 175. - Vorlesungen iiber Kinderkrankheiten, p. 654. third edition. 3 Jahresbericht, etc., der Gesammteu Medicin. E. Virchow and A\\%. Hirsch, vi. Jahrgang, 1S71, vol. ii. p. 247. 4 Loc. cit., p. 13. 350 < SCARLET FEVER 1. "The zone of comparative immunity in the Eastern Hemisphere extends from 10° south latitude to 20° north latitude." (In this zone are found Sumatra, Borneo, India, and most of Africa.) 2. "A zone of comparative immunity in the Western Hemisphere extends from the equator to 10° north latitude." (In this zone are found Venezuela- and the States of Colombia.) 3. "Another zone of comparative immunity in the Western Hemisphere extends from 30° to 35° north latitude." (In this zone are found South Carolina, Georgia, Alabama, Mississippi, Louisiana, Texas, and the northern part of Florida.) According to the vital statistics of the United States for the year 1900 these States, with the exception of Texas, had a remarkably small scarlatina mortality compared with other sections of the country. 4. "In times of pandemics, occasional epidemics occur at points within the zones of comparative immunity." The disease in these regions, however, attacks by preference the Caucasian race. Minor furthermore says that in these countries, "lying for the most part in the tropics and near the equator, exposed to the direct rays of the sun, a high mean annual temperature is of course noticeable." This author, after discussing the climatic influences, concludes that "a very high temperature, combined with periodical humid atmos- phere, is unfavorable to the development of any scarlatinous ten- dency." Season. — Hirsch has studied the seasonal incidence of 435 epidemics of scarlet fever occurring in Norway, Sweden, Russia, Germany, Holland, France, Italy, Spain, and North America. Most of the epi- demics occurred in autumn, as will be seen from the following figures: autumn, 29.5 per cent.; winter, 24.7 per cent.; summer, 24 percent., and spring, 21.8 per cent. In England, since the days of Sydenham, it has been recognized that scarlatina prevails most in the fall; 55,956 deaths in London from scarlatina during a period of twenty-four years gave the following percentages: autumn, 35.54 per cent.; winter, 23.85 per cent.; summer, 22.75 per cent.; spring, 17.87 per cent. In the United States scarlatina is most prevalent during the latter part of winter and during the ea^'ly spring months. The vital statistics for 1870 show the largest number of deaths in March. The first five months of the year exhibit a considerably greater mortality than the rest of the year: Scarlatina Deaths by Months in the United States in 1870. January . 2205 February . 2393 March . 2726 April . . 2294 May . June . July . . 2146 . 1826 . 1216 August . 1096 September . 927 October . . . 1000 November . 1281 December . . 1705 Unknown . 5 Total . . . 20,320 I'lTIOUXlY 351 Arranged according to seasons, (Ik^ figures read as follows: Spring Summor 710(1 3038 Aiilnrnii Winder .",208 0303 Tlie- vital statisfics of the United States for the year 1000, although somewliat ditrerently j)resented with reference to scarlet-fever mortality, give similar results: Scarlatina Deatuk by Months i-ek 1000 of Deaths from Ali, (Jaijsrs IN THE United States in 1900. January . . 118.3 AugUHt 50.3 February . . 112.8 September 52.5 March . 1008 October . 69.4 April . 105.7 November 84.8 May . . 98.4 December . 98.7 June . . 50.0 July . . . . 40.3 Total actual deaths 6333 Here again it is seen that the greatest mortality from scarlet fever is in the late winter and early spring months. According to Murchison, epidemics of scarlet fever in France occur more frequently in the spring and summer months. Johannesen classifies as follows 65,785 cases of scarlet fever occurring in Sweden from LSGT to 1878: January February March . April May June 11.3 per ct. 9.2 9.1 6.9 July . August September October November December 6.6 per ct. 0.3 5.7 8.0 10.4 10.7 It is seen that the greatest number of cases occurred in November, December, and January. In Berlin, from 1877 to 1883, there were 5428 deaths from scarlatina, with the following monthly mortality: January . . 6.7 per ct. July . . 8.0 per ct February . 5.3 August . 8.5 March . .5.8 September . 10.7 April . 6.1 October . . 13.8 May . . . . 7.0 November . 10.9 June . 8.1 December . 8.5 " The greatest number of deaths occurred in autumn — September, October, and November, the maximum being reached in October. From the various statistics presented it is seen that season apparently has some influence on scarlatina prevalence. The same months in different countries show, however, Avidely divergent figures. The different character of the climate in the countries mentioned may account for the discrepancies in the monthly morbidity incidence. It will be necessary to carefully compare the climatic and meteorological conditions by month in the various countries before an^-thing can be definitely said as to the influence of season upon the spread of scarlatina. Minor^ studied the influence of temperature on the prevalence of 1 Loc. cit.. p. 51. 352 SCARLET FEVER scarlatina and came to the conclusion that the colder weather seemed to favor the scarlatinous tendency. He states that: 1. The scarlatinous tendency is but slightly, if at all, modified by a temperature ranging from zero to 65° F. 2. The scarlatinous tendency is decidedly modified and lessened by a temperature ranging from 75° to 80 ° F. 3. The scarlatinous tendency is almost entirely destroyed where there is a prolonged high temperature ranging from 80° to 85° F. Influence of Urban and Rural Localities. — As would be naturally expected, the prevalence of scarlatina is greater in city than in country districts. This is to be accounted for by the more extensive intercourse between cities and by the greater crowding and more intimate contact of the people. The vital statistics of the United States for the year 1900 show a very distinct difference between the city and rural death rate by months: Death Rate from Scarlatina by Months in Cities and Rural Districts, PER 1000 OF All Deaths. Cities. Rural. January 1.6 0.8 February 1.8 0.9 March 1.5 0.9 April 1.4 0.8 May 1.4 0.7 June 1.0 0.4 July 0.6 0.3 August 0.5 0.3 September 0.4 0.3 October 0.8 0.4 November 0.8 0.8 December 1.2 0.8 Scarlet fever is practically endemic in the great centres of civilization ; the disease in the large cities of the world increases and decreases from time to time, but never dies out completely. Altitude. — Minor^ says in regard to altitude that " scarlatina prevails at all altitudes, epidemics occurring at New York, Providence, and Bos- ton, on the Atlantic coast; at Pittsburg, Cincinnati, Chicago, Detroit, and St. Louis, in the interior of the continent; finally, among the mountains of Nevada, and at San Francisco on the Pacific slope. In order to determine whether altitude seems to modify or lessen the tendency to scarlatina, we shall group the States as follows: First group. States having average altitudes ranging from 150 to 600 feet, are Tennessee, Vermont, Kentucky, Georgia, North Carolina, Texas, Massachusetts, Maine, Maryland, Alabama, South Carolina, Arkansas, Connecticut, Mississippi, New Jersey, Rhode Island, Delaware, Louisiana, and Florida. Total population of this group, in 1870, was 14,597,384. Second group, States having average altitudes ranging from 600 to 1000 feet: Iowa, Wisconsin, Missouri, Michigan, New York, Pennsylvania, Ohio, Virginia, Indiana, Illinois, and New Hampshire. Total population 1 Loc. cit., p. 54. i<'/ri()[/)GY 353 of this grou|), In IS70, was 21,500,509. Thirrl group, States having average altitudes ranging from 1000 to 5400 feet: Nevada, California, Oregon, Nebraska, Kansas, Minnesota, and West Virginia. 'J'otal population of this group, in 1.S70, was 2,i:i3,:j]6. In these three groups of States, 20,15!) deaths from scarlatina occurred — i. e., 3833 in th(! first, 15,351 in the second, and 1475 in the third. If we analyze these figures, the following is the result: Altitude. JJcaths. 150 to 600 feet 1 death to every 4380 of population. 600 " 1000 " 1 .. » u 1401 " " 1000 " 5400 " 1 ' 1447 " " " NoviT, taking into consideration the density of population in the second group as compared with the third, together with the fact that scarlatina, being a contagious disease, should be more prevalent where it has the largest and densest population to prey upon, we conclude that altitude rather favors an increase of the scarlatinous tendency." A striking difference in the prevalence of scarlatina in certain of the European capitals has been observed. In London,^ from 1868 to 1872, there were nearly 115,000 cases of scarlet fever. In Berlin, from 1877 to 1883, scarlatina caused 5428 deaths. On the other hand, during a period of five years in Paris, the total deaths from scarlet fever were only 67. It is quite inexplicable why London and Berlin should suffer so severely from this disease while Paris possesses a comparative immunity. Race. — There is strong evidence that negroes are less susceptible to scarlet fever than the whites, and, furthermore, that the mortahty rate among the former is very considerably lower than in the Caucasian race. Minor,- writing in 1875, says: "The total number of blacks d\4ng of scarlet fever in the Southern States was 107 out of a total black popu- lation of 3,713,327; so that 1 out of every 34,704 of the aggregate black population died of scarlatina. The total number of whites d>ang of scarlet fever was 446 out of a total white population of 4,811,962; so that 1 out of every 10,790 of aggregate white population died of scarlet fever. It will be at once noticed that the disease is much more frequent among the whites than among the colored population. During epidemics the whites have seemed to be the sufferers, and there is reason to believe that there is a certain immunity from epidemic scar- latina existing among the negroes of the South." During the Civil War^ 378 whites took scarlet fever, of whom 70 died, and 118 negroes contracted the disease, of whom but 2 died. Comparing the number of the white and black troops it is seen that the attack rate was 54 in the black race to 26 in the white; on the other hand 70 deaths occurred among the whites and only 2 among the negro soldiers. The United States census of 1870 demonstrated the fact that the 1 Meutioned by Forchlieimer. Article in Twentieth Century Practice of Medicine. 2 Loc. cit. 3 Medical and Surgical History of the Kebellion, vol. iii.. part i. 23 354 SCARLET FEVER foreign-born population of the country was 5,567,229, and that 1 out of every 6105 died of scarlet fever. The population of the native- born whites was 28,120,788, of whom 1 out of every 1473 died of scarlet fever. The negro population was 4,880,009, of whom 1 out of every 16,886 died of the disease. It is thus seen that scarlet fever destroyed, relative to the population, over ten times more whites than negroes. The census statistics of 1850 give somewhat similar results. The United States census report of 1890 shows a scarlatina death rate among the whites of 14.2 per 1000 deaths from all causes to 2.7 among negroes. The figures of the 1900 census are almost identical — 12.0 death rate among the whites as compared with 2.6 among the blacks. These statistics would indicate that the Caucasian race in the United States is six times more susceptible to scarlatina than the negroes. Inoculability of Scarlatinal Virus. — Attempts, doubtless based upon the success achieved by inoculation of smallpox, have been made to induce a mild form of scarlet fever by this process. These experiments, though often contradictory, have thrown some light upon the etiology of scarlet fever. In 1834 Miquel reported to the French Academy that he had inocu- lated a number of children with the fluid of scarlatina vesicles. The rash was localized to the region of inoculation. Miquel alleges that complete immunity against scarlet fever was conferred. The reported facts made it very doubtful that scarlatina was actually transmitted. In two cases inoculated by Rostan the rash appeared seven days after inoculation. According to the statement of Guersant,^ Petit-Radel made unsuccessfid attempts to produce scarlatina by the introduction of epidermal scales beneath the skin of previously unattacked persons. On the other hand, Stoll is reported to have produced the disease by rubbing into the skin scales from a case of scarlet fever. These experi- ments are seen to be contradictory and permit no conclusions to be drawn. A much more convincing case is the accidental inoculation of Dr. Rupprecht^ with mucus from the trachea. This physician had per- formed a tracheotomy on a mixed case of scarlatina and diphtheria. In insufflating the lungs through an elastic catheter, he received some mucus into the mouth. Sixty hours later an angina developed and in seventy-eight hours a chill. The eruption Avas irregular, but the diag- nosis was said to be certain. Recently some rather conclusive inoculation experiments were carried out by Stickler^ in an effort to induce a mild attack of scarlet fever. Mucus from the mouth and throat of scarlatinal patients was mixed with a 1 : 600 solution of carbolic acid and injected subcutaneously into ten children. Scarlet fever occurred in each child. The period of incubation varied between twelve and seventy-two hours, and averaged thirty-two hours. The author found that the attacks were too severe to 1 Quoted by Thomas. Loc. cit. ■■' Ein Fall von Scharlach. Wiener med. Woch., 1862. Hauptblatt, p. 435. 3 Medical Record, September 9, 1899. F/nomciY 355 warrant I'nrtlicr inoculations, and, therefore, (lesisted. Incidentally the fact was proven that the mn(;us of the upper ;iir passaj^es contains the causa caiuv/n.s of the disease. From the experiments (juoted we are not justified in drawing any conclusions as to the presence in the skin of tlif; infectious principle. A possibility of error, always to be kept in mind, is that persons inocu- lated with scarlatinal virus may have contracti^d the disease throuf^li exposure in the ordinary mamier. Mode of Reception of the Scarlatinal Infection. — 'J'he scarlatinal poison is ordinarily received into the system through the upper air passages. It would seem that the genital tract in puerperal women and cutaneous wounds may also offer a point of ingress for the infection. IJut in the vast majority of cases the poison is "breathed in" just as in the other acute eruptive fevers. Whether the virus effects its entrance into the blood in the lungs, or at some point along the respiratory avenue, is a difficult question to answer. l)owson, in 1893, endeavored to prove that the first and essential localization of the scarlatinal poison was in the throat. Berge,^ following this view, maintains that scarlatina is primarily a local tonsillar infection, and that the eruption both upon the cutaneous and mucous surfaces is the result of the action of an erythemogenic toxin generated in the tonsils. The streptococcus in one of its virulent forms is regarded as the causative agent of the disease. The view is advanced that the infection may exceptionally gain entrance into the system through other channels, as in the case of surgical and puerperal scarlatina. The author cites a number of cases to show that in puerperal and surgical scarlatina the primary tonsillitis is absent, although the buccopharyngeal enanthem may be present. The theory and facts presented by Berge are of interest, but until the cause of scarlatina is satisfactorily demonstrated, we will doubtless remain in ignorance of the site of invasion of the scarlatinal virus. Period of Infectivity of Scarlatina. — In discussing this subject we wish to draw a distinction between the duration of infectiousness of the scarlatinal virus within and without the patient. Reference has already been made to the longevity of the virus outside of the human subject. The contraction of the disease from contact wdth infected objects may constitute a source of error and obscure the proper estimation of the infectious period. There can be no question that at the very beginning of scarlatina the contagiousness is limited. We have frequently known children, exposed to the disease at the very outset, escape infection only to contract it when re-exposed a number of weeks later. Children wlio are im- mediately separated from a case of scarlet fever as soon as it is dis- covered will frequently remain well; in this respect scarlet fever differs strikingly from measles, in which disease the contagion is extremely active even before the appearance of the rash. Scarlet fever is highly contagious during the period of eruption and 1 Pathogonie de la scarlatiue. Paris, 1S95, p. 126. 356 SCARLET FEVER usually for some time following the disappearance of the rash. The view has been generally held that contagiousness persists throughout the entire stage of desquamation, and that the infectious principle is resident in the epidermal scales. There have always been some dissenters from this view and the doubt as to the contagiousness of desquamating epithelium is becoming more generally entertained. Scarlet fever is not only contagious before desquamation begins, but not infrequently after it has completely terminated. It is obvious, therefore, that the infection must reside somewhere in the body apart from the cutaneous surface. Experimental and clinical evidence both point to the throat and adjacent cavities as the probable lurking places of the infectious organisms. It is, therefore, of importance to continue the isolation of patients until discharges from the nose and ears have ceased. It is probable that the prolonged infectivity manifested by certain cases of scarlatina is due to the presence of the scarlatinal contagium in the secretions of the throat or in the nasal and aural discharges. It is practically impossible to state just at what period a case of scarlet fever ceases to be infectious. The more remote the time from the onset of the disease, the greater is the likelihood of the infection having been extinguished. Probably for this reason the isolating of the patient for the full period of desquamation has been found to be a good working rule. Physicians connected with scarlet -fever hospitals not infrequently see patients who have remained in the hospital from eight to twelve weeks, give rise, upon their return home, to other cases in the same household. And this occurs despite the most careful disinfection of the body and the clothing. These return cases occur in the experience of many hospitals in from 2 to 4 per cent, of the patients. We have seen patients at the end of eight, nine, ten, and eleven weeks, after every vestige of desquamation had disappeared, give rise to the disease in others. In a case recently observed by us we learned that, after the dismissal of the child from the hospital, the ear began to discharge again; shortly afterward a second case developed in the family. Some years ago the following sad case came under observation at the Municipal Hospital: A child with a well-marked scarlet fever came to the hospital at an early stage of the disease, the eruption just appearing. The patient remained in the hospital nine weeks. Desquamation had completely ceased. An antiseptic bath was given in a room disconnected from the hospital building, and the child was dressed in clean clothing. The patient had had a discharging ear which had gotten well, but during the last bath slight moisture in the ear was noticed. A few days after the child's return, the mother and two other children were brought to the hospital with scarlet fever. The attack in the mother was severe, the disease terminating fatally in a short time. The mother had been exposed to the child before the latter was first admitted to the hos- pital. The Contagiousness of Desquamating Epithelium. — Almost thirty years af^o Thomas wrote: "'J'lie eonta^ioiisiiess oi" the; postexanthernatic period is usually ascril)e(l to th(; scales of e})i(h^ririis wliieh separate during the process of desfjuamation; hut it seems to me that there is not the shadow of evidence to prove that the contagion is contained n them either exclusive'y or even chiefly; for it may be presumed that the contag on enters from the l)lood into all secretions and excretions of the patient. Volz, in fact, totally denies the contagiousness of the epidermal desquamation." Von Kerchnsteiner states that "the most favorable conditions for contagion exist during the stage of eruption and acme of the exanthem ; the most unfavorable dui'ing desquamation." (This subject is more fully discussed in the chapter on treatment.) There is no evidence to indicate that the scarlet fever contagium is disseminated by aerial transmission. The immediate vicinity of scarlet- fever hospitals appears to be as free of the disease as other .sections of the city. In this respect scarlet fever differs from smallpox, in which disease the territory immediately surrounding the hospital is apt to show a disproportionately large number of smallpox cases. The following figures are taken from the Medical and Surgical Reports of the Boston C a y Hospital, 1897: Radius of one-eighth of a mile from scarlet-fever hospital . . cases. " " one quarter " " " " " " " . . 6h " " one-half " " " " ■' " " . . 71 " " " three-quarters " " " " " " " . . 75 " " " one " " " " " . . 72 " Within one mile of the hospital 2^6 " Beyond the one-mile limit 756 " It is seen from the above figures that no cases developed within the one-eighth mile limit about the hospital. Our experience at the Municipal Hospital would lead us to believe that the striking distance of scarlet fever is extremely limited. It has been exceedingly rare for families in the immediate vicinity of the hospital to become attacked with scarlet fever, although they have not escaped smallpox. The fact that scarlet fever is not carried beyond the confines of the hospital walls rather militates against the view of the infectivity of scales, for in a scarlet-fever ward the air contains myriads of minute particles of desquamating epithelium. Scarlet-fever Infection in Milk. — The transmission of the infection of scarlet fever in milk has attracted the attention of physicians for some years. Thomas, wa-iting in 1875, referred to two epidemics reported by Bell and Taylor in which the dissemination of the disease was ascribed to infected milk. In the latter epidemic one of the first cases of scarlatina occurred in the family of a milkman whose wife milked the cows. The milk was supplied to twelve families, in six of which scarlatina appeared in rapid succession, without contact with the milk server, and at a time 358 SCARLET FEVER when the disease was not epidemic. The milk had been kept in a kitchen in which scarlatinous patients had been treated. In 1886 Power^ observed in London a severe epidemic of scarlet fever which appeared to attack in particular the patrons of Hendon Farm, whose cows were, suffering from a peculiar malady. This disease was studied by Klein/ who came to the conclusion that the animals were suffering from scarlet fever, and that the infection was conveyed in the milk to human subjects. The malady was introduced among the cows by an animal which had elevation of temperature, cough, faucial and oculonasal catarrh, a red rash about the eyes and on the inside of the thighs, followed two weeks later by desquamation and loss of hair. Vesicopustules were present upon the udders, which later gave rise to ulcers. The animal had recently given birth to a calf. Klein found streptococci in the serum from the vesicles which he inoculated into animals. He likewise found streptococci in the blood of some scarlatina patients. This organism he regarded as the specific cause of scarlet fever. In the same year Crookshank and Brown^ noted an epidemic among cows analogous to that observed by Klein. After carefully studying the same and making further inoculations from an accidentally received sore on the hand of a dairyman, they proved that the disease was cowpox. The same streptococcus was obtained by culture. i In 1885 an epidemic of scarlet fever occurred in Rostock, Germany, apparently from milk infection.* A very striking increase in scarlet fever occurred in June, in which month 36 cases developed. It was dis- covered that the families (with two or three exceptions) were supplied with milk from a farm in the village of Gehlsdorf, where 6 cases of scarlet fever and a number of cases of sore throat existed among the farmers' families and employes. Some of those who were taken ill had milked the cows and had handled the milk. According to the investiga- tions of the Rostock physicians, 8 of the 36 cases could with certainty be attributed to infection from the milk. As indicating the presence of the infecting agent in the milk, it was noted that those who drank boiled milk escaped; this was the case in two children, two and four years of age, who remained free, although other children in the same household who drank raw milk contracted the disease. Freeman^ has made a careful study of the transmission of various diseases through infected milk. He states there is conclusive evidence that contaminated milk has caused certain epidemics. In 26 recent epi- demics of scarlet fever in England traceable to milk, 15 were found to be due to the disease in man. Epidemics due to infected milk have within recent years been reported 1 Milk Scarlatina, London. Report of the Medical GfiBcer of the Loral Government Board, Feb- ruary, 1885 and 1886, No. 8, p. 73. - The Etiology of Scarlet Fever. Proceedings of the Royal Society of London, 1887, xlii. 3 Communication to the Pathological Society of London, 1887. < Quoted by von Jiirgensen. Loc. cit., p. 413. 5 Medical Record, March 28, 1896. Quoted by Northrup in von Jiirgensen's article on "Scarlet Fever." Loc. cit., p. 414. i<:ti()L()(1 y 359 in this country. In Plainficld, New Jersey, an epidemic wastra eed to a farm hand who had a mild attack of ,s(;arlet fever ntifl who liandled the milk (hirinfij this tinu^ More rec(Mitly iin ontl)r(>a,k of scarlet fever occurred ainf)n^ .'>o students of Purdue University, Lafayette, Indiana. The i^o cases wen; fed at eleven different boanhng houses, all of which were supplied with milk by the same dairyman. Five private families supplied with the same milk had one or more cases of the disease in their househftids. The infec'tion was attributed to winter c-jothin^ which had just been f)ut on, and which had been laid away the March before, at which time the "dairyman's family ran through a course of scarlet fever." From the now extensive literature upon the subject, we may conchule that scarlatina may be conveyed through a contaminated milk supply. The proposition is not proven beyond the peradventure of a douljt, but the chain of circumstantial evidence is so strong as to render this con- clusion almost irresistible. It would, furthermore, appear that the milk is contaminated through contact with an individual suffering or convalescent from the disease. The view advanced by Klein that the cows themselves suffer from scarlatina remains unproven and is not generally credited. Hall,^ in reviewing the subject of milk infection, makes the following interesting statement: "While scarlet fever occurs in epidemic form in those countries where cows' milk forms a staple article of food, espe- cially among children, it does not occur in countries where cows' milk is not used as a food, or where children are raised upon mothers' milk only." In Japan cows' milk is not used, and scarlet fever is practically an unknown disease there. In India, cows' milk is used, but children are kept at the maternal breast until they are three or four years of age. Scarlet fever is a rare disease in India, seldom occurring in epidemic form. Pregnancy and the Puerperium, — It cannot be said that pregnancy increases the predisposition to scarlet fever, for, according to Senn, Tourtual, and Trousseau, no case of scarlet fever in pregnant women was observed by them during extensive epidemics of the disease. That scarlet fever is an excessively rare occurrence during pregnancy is evidenced also by the statement of Olshausen that he was able to find only seven cases in medical literature. When scarlet fever does complicate gestation it is prone to lead to abortion or premature delivery. Great diversity of opinion is expressed, in the extensive literature^ on the so-called 'puerperal scarlatina, as to the real nature of this affection. Malfatti^ in 1801 published an account of a malignant scarlet fever epidemic which prevailed among puerperal women in confinement in Vienna. The symptoms were: offensive lochial discharge, abdominal tenderness, with later (between the second and seventh days after 1 New York Nfedical Record, November 11, 1S99. " An admirable collation of the literaiure on this subject is presented by Marcel Durand in a Paris thesis entitled " Etude hislorique et critiqne sur la scarlatina pnerperale." Pp. 3J5. Paris, 1S91. '■> Journal der prakt. Heilkunde, by C. \V. Uufeland, Bd. xii., part iii. p. VJO. Berlin, Ungar, ISOl. 360 SCARLET FEVER delivery) chills, headache, ringing in the ears, hot skin, nervousness, and moderately rapid pulse; then a diffuse reddish exanthem, which on the third, fourth, or fifth day became bluish, accompanied by marked nervous symptoms, failure of the vital powers, and death. In 1875 Braxton Hicks read before the London Obstetrical Society a paper in which he' stated that of 89 puerperal cases under his care that had febrile symptoms, he regarded 37 as suffering from scarlet fever. Very few of these patients had an angina of any severity and 17 did not have an eruption. In 2 instances scarlet fever developed in children who were exposed to the puerperal women. In the discussion that followed, some endorsed but many repudiated the diagnosis of scarla- tina in these puerperal fevers. Olshausen^ combats the contention of Hicks and mentions the argu- ments which led Helm and subsequent writers in Germany to regard puerperal fever with scarlatiniform rash as puerperal septicaemia: (1) these epidemics occur in maternities and not synchronously with outside epidemics; (2) the malady has a malignity more in accord with puerperal septicaemia; (3) it is often complicated with peritonitis and other manifestations analogous to those seen in puerperal fever; (4) origin in the early days of the post-partuvi as is observed in septicaemia; (5) in the majority of cases it has been impossible to establish contagion. Olshausen collected 141 cases of scarlatiniform rash occurring during pregnancy and the puerperium; these were reported by Koch (3), Schneider (5), Clemens (2), Simpson (2), Hardy (2), MacClintock (34), Brown (9), Johnston and Sinclair (2), Winkel, Halahan (25), Hicks (18), Lange, Denham (8), Senn (7), Dance (1), Trousseau (1), Gueinot (4), Hervieux (7), and Olshausen (5). Of this number only six occurred during pregnancy. Eight developed immediately after confinement, 62 from the first to the second day after confinement, 27 the third day, and 22 from the third to the eighth day afterward. Winckel,^ in expressing his incredulity concerning the scarlatinal nature of Hicks' cases, mentions the fact that lying-in women in England more frequently exhibit an erythema upon the cutaneous surface than in Germany. Martin^ is of the same opinion and regards true puerperal scarlatina as a rare occurrence. Indeed, in 38,000 accouchements he observed this complication but three times. Von Jiirgensen, after a careful study of Malfatti's cases, does not regard them as true scarlatina, but as puerperal septicaemia. He believes that scarlatina, in the strict meaning of the term, is of slight significance as a factor in the mortality of the puerperium. The fact is recognized that puerperal septicaemia may be attended with a rash which cannot be distinguished from that of scarlet fever. The lying-in woman may develop after confinement either a true scarlet fever or a puerperal fever with a septic scarlatiniform rash. There can 1 Archiv llir Gyntikol. und Obstet. de Cred(§, 1876. 2 Die Pathologie und Therapie des Wochenbettes, third edition, p. 350. Berlin, Hirschwald, 1875. 3 Zeitschr. fiir Geburtsh. und Gynitkol., 1876, vol. ii. ETIOI/XIY 301 be no doubt that in the past many instances of the IjiUcr ffjitflition have been regarded as puerperal srarlatina. Tlie fliflereiilial diaj^nosis is often extremely difliciilt. The following points would indicate a puer- peral infection rather tiian scarlet fever: 1. The absence of an epir a septic rash may he (jiiite indisliiif^iiishiihle from that, of s(;arlet fever. The general symptoms must he considered and the condition of the throat, tongue, glands, ears, and kidneys determined in order to throw the full(\st light n])on these diriicult cases. The diiignosis of scarlatina is sometimes indnhitahly confirmed hy the unfortunate transmission of the (hsease to another subject. THE SYMPTOMATOLOGY OF SCARLET FEVER. Period of Incubation. — By the period of incubation is meant the time elapsing between the reception of the scarlatinal poison into the .sy.stem and the first manifestation of symptoms of the disease. It is well to bear the fact in mind that the reception of the contagion is not invariably coincident with the exposure to the disease. The breeding stage of scarlatina is briefer and at the same time more variable than that of the other acute exanthemata. Within its com- paratively narrow hmits, a considerable degree of variation occurs. The incubation stage of smallpox, although extending over a longer period, is strikingly uniform and reliable; to be sure, there are some variations, but these constitute exceptions. Measles, too, has a com- paratively constant period of incubation. The various writers on scarlet fever, in giving expression to their views as to the duration of the incubation stage, are guided largely l)y their individual experiences. Apart from actual differences in the clinical experiences of physicians, some of the widely divergent incubation periods may possibly be attributed to differences in the discriminating judgment of the observers. The more conservative writers are in general agreed that the most common period of incubation of scarlet fever is between three and seven days; the narrower these limits are con- tracted as a general proposition, the greater is the liability to error. Thomas regards "four to seven days as the most frequent interval," and looks upon shorter or longer periods as exceptions to the rule. Von Leube and Forchheimer both subscribe to this estimate. Vogl believes that the exanthem appears three or at most five days after infection. While these intervals cover the vast majority of cases, there have been recorded occasional authentic instances of much shorter and longer periods of incubation. Trousseau's case of not more than twenty-four hours' incubation is of interest. He writes: "A London merchant had taken one of his daughters to the Eaux Bonnes in the Pyrenees, and had passed the winter with her at Pau. On his way back to London he stopped at Paris, where he wished to remain some days. His eldest daughter was keeping house for him in London. Impatient to embrace her father and sister, she started for Paris. When crossing the channel, she was seized with fever and sore throat, and seven or eight hours later 364 ■ SCARLET FEVER arrived at Paris in the middle of a very serious attack of scarlet fever. She alighted at the hotel, almost at the very moment when her father and sister arrived from Pan. The two sisters remained together in the same room, and in twenty-four hours the sister who had come from Pau showed the first symptoms of a mild attack of scarlatina. In London the disease was then epidemic, but there were no cases at Pau." Trojanowsky, Forster, Sorensen, Murchison, Alonzo Clark, Raven, Hagenbach-Burkhardt, and others have recorded periods of incubation of twenty-four hours or even less; so that it may be accepted that in rare cases the infection may give rise to symptoms almost immediately after entrance into the system. As to long periods of incubation, there is much divergence of opinion. Veit claims it may be twelve to fourteen days; Paasch published a case in which it was twelve days; Gerhardt and Reinhold credited periods of eleven to thirteen days. Bawy records an instance of twenty-one days and Trojanowsky one of twenty-eight days. Murchison, in his wide experience, has only been able to collect a series of 13 cases in which he could be sure of the incubation period; in not a single one of these cases was the period longer than six days. On the other hand, Hagenbach-Burkhardt^ reports 57 cases in which he has been able to study the incubation period. Of this group the remarkable number of 35 had incubation stages of over seven days. Under eight days there were 4 cases; nine days, 2 cases; ten days, 1 case; eleven days, 5 cases; twelve days, 1 case; thirteen days, 4 cases; fourteen days, 2 cases; fifteen days, 5 cases; seventeen days, 2 cases; eighteen days, 1 case; nineteen days, 2 cases; and over twenty days, 6 cases. This is certainly a most remarkable array of long incubation periods to come within the experience of any one observer. Some of these instances and others exhibiting long periods of incu- bation may possibly be explained upon the grounds of a temporary immunity retarding the susceptibility to the scarlet-fever poison. While unprotected individuals are almost invariably susceptible to the con- tagion of smallpox and measles, the same is not true of scarlet fever. Certain individual conditions about which little is known seem to make some persons immune at one time and susceptible at another to the infection of scarlet fever. We have recently had the opportunity of watching a protracted epidemic of scarlet fever in a home for children in this city. For a period of over three months, children contracted the disease two or . three at a time and were sent to the Municipal Hospital. About 40 out of 100 were thus gradually attacked. It would seem that in many of the children the individual susceptibility was temporarily in abeyance or that the infection was not received by them in the beginning in suflflciently intense or concentrated form. It is alleged by some writers that a virulent contagium may shorten the period of incubation, and that a similar abbreviation of this stage may result when the scarlatina occurs in a surgical or puerperal subject. 1 Ueber Spital iafectiouea, Jahrbuch fiir Kiaderheilk., Bd. xxiv. p. 105. Tim SYMPTOM A TOLOflY OF liCAHLF/r FKVRH 365 Holt/ has tabulated records of the incubation periorj in 113 cases, some of which were ol).served by him, but most of which have been abstracted from the literature of the subject: iNfJur.ATioN Pkrioo. 24 hours or lesK . . 6 cases. 7 flays . 8 cajeR 2 days . 15 " 8 " . . . 2 " 3 " . 28 " 9 " . . . 5 " 4 " . 2.') " 11 " 1 case. 5 " . 6 " 14 " . 1 " 6 " . 15 " 21 " . 1 " It is seen that in 87 per cent, of these cases the incubation period was between two and six days. Simple, Usual, or Normal Scarlatina (Scarlatina Simplex). Period of Invasion. — During the stage of incubation no symptoms, as a rule, are present, the morbid process being entirely latent. The Fic . 59 MONTH S! S s s "& S s M CD -i i^v .-!J DAY OF DISEASE - « CO -* ^ o b- <» O - ;-. 1 102° I lOl" < S 100° D 1- < S 99° H 98° A - V \ ' ^ \ ; •s s, 1 \, \j ■s [i ^ ^ V \ \ \ V A V A V \ = -\ 150 HO 130 u, 120 °- 110 100 90 SO \ \ \ \ \ \ \ / N ^ A \ / \ ^ ^ \ \/ \ f \ Y V \ \ V M Si -/ ^s. ^ -/nn \ ^ "N V ^ Temperature and pulse record of scarlatina simplex. J. B., aged six years ; mild case of scarlet fever terminating in recovery. onset of the disease is sudden. The earliest symptoms are : indisposition, fever, headache, vomiting, and sore throat. Chills are usually absent 1 Piseases of Infancy and Childhood, Xew York, 1896, p. 889, 366 SCARLET FEVER except in severe cases. In children vomiting is the earhest as wel as the commonest of the invasive symptoms, and is, therefore, of suggestive diagnostic import. Not infrequently children in the full bloom of health are quite suddenly seized with vomiting rapidly followed by the other symptoms of scarlatina. Billington observed this symptom in about 80 per cent, of his cases. We have obtained a history of the occurrence of emesis in 76 out of 155 cases, or about 50 per cent. We believe that the average frequency of this symptom is greater than would be indicated by these figures. The evacuation of the contents of the stomach may be accompanied by diarrhoea, although usually the bowels are constipated. In severe cases in infants convulsions are not uncommon. There is loss of appetite and the tongue is furred. Adults and older children who are able to appreciate the sequence of the symptoms often indicate sore throat as the first. Temperature. — The temperature rises rapidly, often reaching 102° to 104° F. or more in the course of a few hours. The pulse increases in frequency and, compared with the temperature, is often disproportion- ately rapid. The radial pulsations may number in children 140 to 160 per minute, and in adults 120 to 140. Headache and vertigo are common, and the patient may be alternately somnolent and restless. The thirst is often intense. The patient is greatly prostrated and presents the facies of a very sick person. The skin is hot and dry, the eyes dull and listless, and the face flushed. The fever in scarlatina is subject to great variations, being influ- enced by the severity of the epidemic and the nature of the accom- panying complications. The pyrexial curve is by no means as constant as is seen in the other two important exanthematous diseases — smallpox and measles. Wunderlich^ gives the following as the average febrile course: The temperature at the onset of the disease rises rapidly, and after a few hours reaches 104° to 105° F. or higher. With slight morning remissions the fever still increases from the appearance of the eruption until its complete diffusion over the surface. When the eruption has reached its height, the temperature begins to decline by gradual steps, with slight evening exacerbations. It is thus seen that the fever is a continued one during the invasive and early eruptive period, and that the pyrexia subsides by lysis con- currently with the fading of the exanthem. In well-pronounced cases of what might be called the normal form of scarlet fever the early rise of temperature is seldom below 104°, and it not infrequently reaches 105° or 106° F. The high temperature persists ordinarily for four or five days and then a decline sets in. The intensity and the duration of the fever depend much upon the type of the prevailing epidemic. We have determined the duration of the fever in 265 cases of scarlatina which we treated in the winter of 1902-03, at which time the type of the disease was distinctly mild. 1 Eigenwarme in Krankheiten, 77//'; H^YMPTOMATOLOCY OF SCAULh'/r /''/'JVh'ii Wl Tetn[)()riuy ri.ses of tern[)eratiire occurring late and resulting fio recognized c()iiif)li("itioii,s or .s('f|U(!lir' were not consifjcrefj. Ki(.. 00 ' - -- - - - - - ^ - - - — ~m ■" = - - - z - ::. .'1 r — - 105 , — - — - — — - — •r .f a t 10-1 103 i 103" ^ ^. A I \ r ■<' f ' ' < -■ , 1 \ / , \ •M < V \ J \ I - ■i. T : i i s ^ -2 |\ 1 ' -H _- -J _ — - - — iv 1 -- — ^ — — - _ _ 1 ^ 1 1 \ i .1 1 ' S lOl" < ^ i w i i loo" ^ \ 0. ° 99° 98" 9T" \ 1 \ < < ■ ! 1 ;/\i ^ I ■ A A 1 _ _/ tf> o /\ ' : / \ / \ 1 i — — \ 1 ' \. r\ /\ ' •' E s, / V V V < < ' • s/ to 1 1 1 — DAY Or DISEASE 3 i 5 1 6 7 s 9 10 11 12 13 11 15 16 n PULSE s^^^ ^ N*V^ v'\olv*^,;( V'^,'> ^*i^K^.^h '::<^!^^!^^ ^ % ^ *X % f4 % % ^ 14 ^ RESP. ■' ■# ■'**t"j.^h'^'> '"•;>> •^''■^r-''-s>h , ,.> 1 ,.0 ■ ;^ fi ;^ :^ 'J4 % % fi H x^> fi R. B., aged seven years ; case of scarlet fever with an intense rash and severe early symptoms, terminating rather unusually by crisis. DuEATiox OF Fever in 265 Cases of Scarlet Fevfr Treated Municipal Hospital in the Winter of 1902-03. AT THE Lasting 1 day . 2 2 days . 3 3 " . 17 4 " . 19 5 " . 32 6 " . 40 7 " . 35 8 " . 29 9 " . 22 10 " . 14 11 •' . 14 12 " . . . 10 13 " . . . 4 14 " . . 4 Lasting 15 days 16 " 17 " 18 " 19 " 20 " 21 " 22 " 23 " 24 " 25 " 26 " Total . 5 cas 4 ' 3 ' 1 2 ' 3 ' ' ' 1 ' * 2t5 It will be seen from the above table that in the largest number of cases the fever terminated upon the sixih day of the disease. In 15S cases, or 60 per cent., the fever lasted from five to nine days. It must be remembered that the prevailing form of the disease was mild and the mortality low. Jamieson states that of 200 cases observed by him the maximum temperature was reached— in 11 cases on the first day, in 76 on the 368 SCARLET FEVER second day, in 75 on the third day, in 36 on the fourth day, and in 2 cases on the fifth day/ Deviations from the pyrexial curve above mentioned not infrequently take place. Instead of declining by lysis the temperature may fall by crisis. On the third or fourth day a sudden decline of the fever to normal or subnormal may take place. The temperature may then continue for some days at or slightly above normal. Henoch, Fiirbringer, and Jiirgensen have described such cases and Litten has reported instances of high initial fever followed by an apyretic course. Henoch noted 4 cases out of 175 with normal morning temperature and evening elevation. Litten observed similar cases. Ordinarily, high fever accompanies severe cases with well-marked eruptions, but there are numerous exceptions to this rule. Leichtenstein mentions a case with marked delirium and intense eruption running an almost afebrile course. Cases of a malignant type may be entirely unaccompanied by elevation of temperature, and, indeed, the temper- ature may even be below the normal line. It is not rare for very mild cases to be unaccompanied by pyrexia. We recall an afebrile case developing in the hospital whose temperature record we were enabled to observe for several days before the attack. Fiirbringer^ describes a secondary fever in scarlatina that is inde- pendent of and unaccompanied by any discoverable complication. Wunderlich, quoted by Trousseau, observed a considerable elevation of temperature during the stage of desquamation. Gumprecht and Jiirgensen have also recognized this secondary fever. Thomas^ describes irregular cases of scarlatina with protracted fever. He writes: "When the fever is irregular it fails to defervesce after the normal progress and disappearance of the eruption and angina, but continues for weeks, sometimes with the same intensity and a typhoid character like that of a variety of scarlet fever presently to be described; sometimes with increasing intensity, especially if it is to prove fatal, and at other times it declines gradually as in protracted defervescence. In such cases the pulse is often very rapid, the heart's action violent, and the first sound of the heart diffuse or even replaced by a distinct murmur." And, again, "Not infrequently there occurs still another form of the disease in which there are not only local affections of moderate, perhaps even trifling importance, but also disproportionately severe fever of long duration which characterizes this variety as a typhoid scarlatina." Thomas remarks that in these cases the fev,er is the chief symptom and that it may be protracted for weeks. Hyperpyrexia is more frequently observed in scarlet fever than in the other exanthematous diseases. It is not so rare for 107° F. to be reached ; such cases usually terminate fatally, although when the hyperpyrexia is not protracted recovery may take place. In rare cases the fever may mount to an extraordinary height. Wunderlich records a temperature 1 Quoted by Forchheimer, loc. cit. 2 Realeacyklopadie, Bd. x., 5, p. 472. Quoted by Jiirgensen, loc. cit. 3 Loc. cit., pp. 254 and 269, THE SYMPTOM A rOLOav OF SCA RfJ':!' FEVER 369 of 110.8° K.; Thomas, 111.2° F.; I>oiclit(;ii.sl(;in, 100° and 100.0° F., and Dr. Currie, according to (ircgory, 112°F\ These rises of temperature were, as might be expecte(], shortly followed by death. Throat S'i/mpf<)7ns. — Throat symptoms are, as has been stater), early complained of by adidts. On ins})(;ction, general fancial redness is observed, involving pjirticnlarly the uvnhi, tonsils, and soft j)ahit(;. ^^'hen the cutaneous eruj)tion begins to manifest itself the redness increases and there develops oedema and swelling of the mucous tis.sues. At times a thin, grayish or yellowish film of exudate may be seen on the swollen tonsils. Often the soft palate, uvula, and buccal mucous membrane show a punctated redness similar to that later ol^served ujjoji the skin. The stage of invasion is brief, not lasting ordinarily more than twenty- four hours. In some cases the eruption appears before twelve hours have elapsed. In a series of 84 cases of scarlatina, Barthez and Rilliet observed the eruption appear as the first symptom in 4; in the majority of the cases, however, the eruption manifested itself at the end of twenty-four hours. Trousseau saw a severe case of scarlatina with marked brain symptoms in which the rash was delayed until the eighth day. It is, however, distinctly exceptional for the stage of invasion to last much longer than twenty-four hours. Stage of Eruption. — The exanthem of scarlet fever usually begins upon the neck and subclavicular regions, then spreading rapidly to the chest, face, abdomen, arms, and legs. A variable time elapses in different cases before the acme of the eruption is reached. The milder efflor- escences reach their height earlier than those of greater intensity. In severe cases the rash may take until the third or fourth day before its greatest intensity is attained. The color of the scarlatina exanthem varies in different individuals and is extremely difficult to depict in words. It has been variously designated by writers as scarlet, bright red, boiled-lobster tint, raspberry- juice color, rose colored, wine colored, etc. These terms are permissible because they convey a definite impression to the mind, but when these tints are compared with the exanthem at the bedside the terms are seen to be inaccurate. The color of any inflammatory eruption is due to the blood appearing through the texture of the skin. The amount of blood in the skin as determined by the calibre of the cutaneous bloodvessels, the character of the blood, and the complexion of the individual all influence the coloration. It is a matter of daily observation that the rash in fair-skinned persons is brighter than in those of swarthy com- plexion, whose skin contains a greater amount of epidermal pigment. In general, the scarlatinal rash is reddish, sometimes bright, but more often dull or dusky red. Sometimes the eruption is so brownish-red, particularly in dark-complexioned individuals, as to almost approach a bright terra- cotta color. IMore rarely the element of blue is so well marked, particularly in dependent areas of skin, as to be quite purplish owing to the venous congestion. The color varies not only in different 24 370 SCARLET FEVER persons, but at different periods in the same individual. A bright eruption commonly becomes dusky before it fades. When the scarlatinal exanthem is viewed at a little distance it gives the impression of a uniform reddish blush. When, however, the skin is closely scrutinized it is seen that it is made up of innumerable reddish points or puncta. These are of a deeper tint than the skin intervening between them. At tunes eruptions are seen in which the skin between the puncta is of normal coloration. This appearance may occasionally be noted during the coming out or evolution of the exanthem. Ordinarily the points of greatest color intensity are surrounded by areolae of somewhat brighter hue. When these coalesce, as is usually the case, a diffuse eruption is presented, the puncta being scarcely distinguishable through the obliteration of contrast. At times the areolae are narrower, exhibiting a little intervening normal skin and giving the eruption a more or less speckled appearance. In other cases with larger pale areas a mottled appearance is noted. Finally, there may exist large, irregular patches of healthy skin, particularly on the arms, legs, and buttocks, producing so marked a blotchiness of the exanthem as to suggest a strong resem- blance to measles. The scarlatinal eruption frequently exhibits small pinpo"nt to pin- head-sized, reddish elevations, which occur most commonly at the sites of hair follicles. These are frequently seen upon the extremilies, particularly the lower, but may also appear upon the trunk. This condit on was called by the older writers scarlatina papulosa. In addition to these elevations a general goose-flesh condition of the sk n is not infrequently observed. This is best marked upon the abdo- men and chest, and is characterized by immerous pinhead-sized papules bearing a close resemblance to the "cutis anserina" evoked in the normal skin by exposure to either extreme of temperature. These papules may be faintly red or of the normal skin hue. They differ from ordinary goose-flesh in that they persist usually for some days. At times this condition is so pronounced as to impart to the skin a "nutmeg- grater" feel and appearance. In the older descriptions of scarlet fever one reads of the occurrence of sudamina at the height of the efflorescence. Inasmuch as during this stage the skin is hot and dry with no tendency to sweating, one would not expect to find sudaminous sweat vesicles. It is extremely common, however, to find in well developed rashes innumerable miliary vesicles. To this condition the term scarlatina miliaris or scarlatina vesicularis has been given. The vesicles are conical, epidermal elevations, pin- point to pinhead sized (size of millet-seed), with turbid or lactescent contents, and usually disseminated, although occasionally occurring in groups. They are commonly situated on the abdomen and chest and to a lesser extent on the extremities. The region in which they are frequently most copiously present is the mons veneris, for here the ery- thema is often intense. In this region they are prone to develop into minute but well-marked, yellowish pustules. Till': HYMI'TOMATOLOdV ( )!'' SCA ItLICT i'lCVI'lit ."J] Rarely, f()iiii'i;iioiis vcisielcs iiuiy coalesce, fonninjj; hlc^fts of the size of a ])ea or larger, ccni.stitutiiig tli(! .scarlatina jHnri/ph'Kjoidca f>f the older writers. Miliary vesicles may be seen in nearly all well-pronounced scarlet- fever eruptions. They are much more fref|uent than is generally sup])()sed, l)eing often overlooked on account of their minute proportions. A niagiu'fyiiig glass will often ))riiig them into view wh(;n they are not clearly perceived by the unaided eye. In perhaps 20 per cent, of all cases and 50 per cent, of well j)ronounced eru|)fioiis, vesicles are readily Miliary vesicles with lactescent contents appearing about the axilla with the rash of scarlet fever. visible if looked for; lesions of this size, however, do not intrude them- selves upon one's vision upon cursory inspection of the rash. The vesicles are more conspicuous in severe eruptions than in mild rashes. In decidedly exceptional instances they may be so pronounced as to overshadow the general scarlatinal exanthem and puzzle the physician in the diagnosis. Dr. J. P. C. Griffith, of this city, has reported several such cases. Gee, Squire, Bohn, Rilliet and Barthez, D'Espine and Picot, Moizard, Baginsky, Vogel, and others believe that miliary vesicles are determined by an excessive degree of inflammatory action of the skin. Thomas, on 372 SCARLET FEVER the other hand, thinks that the miHary vesicles are produced by a pecuhar disposition of the skin of patients. He states that in some epidemics this condition has been noticed so often and in such abundance that the normal eruption was observed only in a minority of cases. Griffith^ fully coincides with the latter view. He cites cases in which extensive miliary eruptions accompanied mild scarlatinal rashes. He feels that it is perfectly possible in occasional cases to have the presence of an abundant miliarial eruption cause decided difficulty in the diagnosis and even lead to error. In a large experience with scarlet, fever we have found miliary vesicles to be much more frequently associated with intense rashes than with mild eruptions, although they may occasionally be seen in the latter. The older writers seemed to think that this miliary eruption accom- panied certain epidemics of scarlatina, and they fancied that these "miliary epidemics" represented a peculiar infection rather different from ordinary scarlet fever. During the period of the fading and decline of the eruption, pea-sized or larger, flat, epidermal elevations are often noted. These are whitish and suggest sudamina the contents of which have been absorbed, for one seldom, if ever, discovers fluid in them. They may be readily opened with a needle, and resemble empty pea-pods. The exfoliation of the summits of these lesions and of the miliary vesicles constitutes the beginning desquamation on the trunk, but this will be later referred to. The character of the eruftion on the face varies somewhat. In some cases this region remains entirely free. More commonly the temples and cheeks are the seat of a deep -red flush; it is probably that this flushing is often associated with the true rash, for it is not rare to see the face desquamate profusely. The forehead often shows redness, but this is usually less intense than on the lateral aspects of the face. The tip and alse of the nose, and the upper and lower lips and the chin, commonly appear preternaturally pale. This circumoral pallor defined by the marked flushing of the cheeks gives the patient a most curious appear- ance, which, if not peculiar to, is always strongly suggestive of scarlet fever. On the arms and legs the rash exhibits no peculiarities save its likeli- hood to early involve the flexures of the joints (groins, popliteal spaces, and elbow flexures), and its greater tendency to be blotchy. Upon the palms and soles the eruption is usually diffusely red without any puncta. When pressure is made upon the scarlatinal rash a momentary pallor is produced, then a return of redness and flnally a gradual paling again which persists for some minutes. We have seen on the legs pale bands persist where garters had previously been worn. Indeed, one may inscribe a name upon the efllorescence with a blunt instrument and in a few moments note the white letters stand out upon the red background. This is the reverse of the ordinary dermographism and might be termed ancemic dermographism. This is a vasomotor 1 Scarlatina Miliaris, Jacobi's Festschrift, 1900, pp. 182-186. 77//'; HYMI'TOMATOl/XlY OF SnAUL/'/r /''HVER 873 peculiarity, biii it is douhtful whether it possesses any reliable diagnostic value. Itching is not infr(H|ij(',ntly cxpcricnccrl by scarlet-fever patients. While in most cases it is insi^nii(i( ant or entirely absent, it is occasionally quite severe. It may be noted during the early evolution of the eruption, at its height, or during the decline just before desquamation sets in. In intense eruptions there is often some adema and swelli7if/ of the skin accompanied by an exaggeration of the lines of cleavage. The skin under such circumstances is thickened and shows wrinkling of the epidermis. On the other hand, the eruption may be so mild as to make the diagnosis difficult and even impossible. Indeed, in rare cases the eruption may l)e absent altogether. Fig. fi2 Ansemic bands at the sites of the garters during the height of a scarlet-ltx t-i ti upi i^n, li.i^ is vasomotor phenomenon similar to the white bands following digital stroking. The eruption persists at its maximum intensity but for a brief period — from a few hours to a day or two, and then gradually fades. ]\Iuch variation is shown as to the entire duration of the exantbem; ordinarily the eruption lasts from three to seven days, but its life may be shorter or longer than this period. Cases doubtless occur in which the eruption is of such brief duration as to escape notice entirely; instances of scarlet fever without eruption, but followed by desquamation, are probably to be accounted for by evanescent undiscovered eruptions. In some cases a temporary fading or recession of the rash occurs. It is not rare for the exanthem to be more vivid in color at certain times. The rash is not infrequently brighter in the evening than during the day. It is more rare for the eruption to recede completely and later reappear. The Enanthem, or Mucous -membrane Eruption. — As has already been stated, sore throat is not infrequently among the earliest of the s\Tap- 374 SCARLET FEVER toms ushering in an attack of scarlet fever. In the very beginning there are commonly seen congestion and swelling of the tonsils, uvula, and soft palate. A punctated redness is often visible on the soft and hard palate. During the eruptive stage the gums and buccal mucous membrane usually exhibit some redness and swelling. If the gums are inspected from the second to the fifth day there will oftentimes be seen milk white 'patches which look much as if they had been produced by the application of pure carbolic acid. These represent a desquamation of the epithelial covering of the gingival mucous mem- brane, and can readily be peeled off by slight friction. This process occurs at times in measles and perhaps also in other affections in which there is congestion of the oral mucous membrane. The tongue is, as a rule, heavily covered with a grayish fur at the onset of an attack of scarlatina. Soon the tip and edges assume an angry, reddish coloration, and a roughened or granular appearance. At this time also the fungiform papillae on the dorsal surface of the tongue become swollen and prominent and peep through the surface coating. Usually by the fourth day or thereabouts lingual desquamation takes place and the coating is cast off, disclosing to view a red, raw- looking, often glazed surface studded with enlarged papillae. At times the papillary elevations are numerous and small, looking like the granulations in a wound. At other times they are scattered and more prominent. This condition of the tongue is of considerable diagnostic importance and has been variously described as the "rasp- berry," "strawberry," or "cat's tongue." It should be remembered, however, that mild cases of scarlatina occasionally exhibit no abnor- mality of the tongue whatsoever. During the eruptive stage the condition of the throat undergoes aggravation. The tonsils are usually enlarged, reddened, and covered with a layer of mucopus or actual pseudomembrane. The uvula, anterior pillars, and soft palate are intensely reddened and oedematous. The patient complains of much pain in the throat, particularly on swallowing. Desquamation. — Exfoliation of horny epithelium begins during the decline of the eruptive stage. Desquamation occurs first upon those parts of the cutaneous surface which were first the seat of the exanthem. (Fig. 63.) Where the face has presented much eruption or even intense flushing a branny desquamation will often be noted as early as the fourth day. Almost simultaneously a similar epidermal exfolia- tion occurs upon the neck and the upper portion of the chest. This process is commonly inaugurated about the sixth or seventh day of the disease. If one watches for the first evidence of desquamation on the trunk, it will be noticed as a number of discrete, pinpoint-sized, powdery scales. These represent the desiccated summits of the miliary vesicles. In a day or two these small scales are cast off, leaving minute, jagged rings of desquamation. The horny layer is now lifted off by centrifugal extension of these rings, which grow progressively larger. On meeting Till': SVMI'TOMATfJLor/Y OF HCAULKT VKVKii 370 intestines, etc. On iliis iiccoiinl HawU^y lias suggested \\v,\\. flif; terin lymy)h;i,ti(; fever he siihslitiitefl I'or searlet fever. (^iiil(^ early in the conrse of searl(;t ff'ver do we w^Av. ;in iif)j)rcfiahle ttunefaclion of tlu; suJHMitaneous lyni[)h "[hinds, more j)!irlinij;irly those sitiuitoul ahoiit the angles of the jaws. The following presentation of the eondition of the glands in 100 eases' will give an adecpiate idea of tin; cxicnl of (he lyniphiiOf iii\olvement in searlet fever. Fk;. G7 Pronounced desquamation in large lamellEe. The various lymphatic glands were enlarged in the following pro- portion of cases: Inguinal glands 100 per ct. (a) pea-sized ' 23 per ct. (6} beau-sized 77 " Axillary 96 Maxillary 95 Posterior cervical 77 Anterior cervical 44 Submaxillary 36 Epitrochlear . . . ' 26 Sublingual 25 The inguinal glands were in the main enlarged to the size of a pea or bean, although occasionally they would reach the dimensions of an almond. The epitrochlear glands vary from the size o" a lentil to a pea. Not infrequently the enlargement occurred but upon one side. Occasionally there is a second enlarged gland just above the epitrochlear gland. 1 A Clinical Study of the Lymphatic Glands in One Hundred Cases of Scarlet Fever, by J. F. Schamberg, Annals of Gynecology and Pediatry, December, 1899. 380 SCARLET FEVER The axillary glands vary in size from a pea to an almond. They are usually enlarged in clusters rather than singly. The sublingual gland is scarcely ever larger than a lentil seed. The submaxillary lymphatic glands were found to vary in size from a pea to an almond. In one case a gland reached the dimensions of an orange, broke down, and suppurated. The maxillary glands, or those just behind the angle of the jaw, reach the largest size of any of the lymphatic glands and are the commonest to undergo suppuration. In the above cases they varied from the size of a bean to that of an orange. The average was perhaps represented by the dimensions of an almond or hickory nut. The anterior cervical glands, or those lying in front of the sternocleido- mastoid muscle, were usually pea to bean sized, as were also those posterior to the muscle. The glands were examined at various stages of the disease, as early as the second day, and as late as the fifteenth. In the cases studied upon the second and third days the glandular enlargement was so well marked as to suggest the probability that the glands are already some- what tumefied on the first day of the illness. The duration of the enlargement doubtless varies in different patients. In several cases, examined at intervals of a few days for three weeks, the glands were found to gradually diminish in size, but at the end of this time they were still slightly enlarged. Statistics are frequently misleading, and those presented above are, perhaps, no exception to the rule. While it is true that the inguinal glands were enlarged in every one of the 100 cases of scarlet fever examined, it is more than probable that in some of them the enlarge- ment antedated the attack of scarlet fever. The percentage of appar- ently healthy children with pea-sized or larger inguinal glands must be very considerable. Still the effort was made to eliminate this error as far as possible. It is in most cases not difficult to distinguish between an old and a recently enlarged gland. The former has a decidedly sclerotic feel, with the resistance, say, of cartilage. The latter presents a peculiar resiliency with the consistency of liver. The enlargement of the glands about the jaw and neck is ordinarily proportionate to the amount and intensity of throat involvement. There are, however, occasional exceptions to this rule, and it should be recog- nized that extensive lymphatic swelling may occur with but slight throat symptoms. When the glandular swelling is of moderate extent and of early occurrence, it usually undergoes gradual subsidence. When the swelling is very great, and particularly when it develops late, from the second to the fourth week of the disease, it is extremely prone to suppurate and form a glandular abscess. This will be further referred to under the subject of complications. Respiratory Symptoms. Laryngitis. — Despite the intense inflam- mation of the pharynx in scarlatina there is but little tendency to involve- ment of the laryngeal structures. Trousseau's epigrammatic saying, 77//'; HYMPTOMATOI/XIY OF SCARLI'/r FKVER 381 "Scarlatiriii has no likitifi; for tlic, hirynx," is hornc out, hy (•x})f'ri('r)ce. He fiiHlier r(Miiarks: '"rriio scarliilinou.s sorf^ tfiroat, tlicri, is pJiaryn- geal, (lillV'i-iii^f in this respect from tlic; sore thrfnit of measles, whieh is laryiin-eiti, and from that of smallpox, whieh is hofh [)haryngeal and laryn^ciil." It is only when the inflammation of the throat in scarlatina is severe, with tendency to f>;}ui/Trenoiis ehan^^ ^'^^ ^:^ ^V-^ ■^ ^^ * •V* ^.^ ""'^■v* ■^'.v:. •V* . "^*.,s ..0 ''*-i^ ■S^^a, ■'V^-v^,"V 'V •''^^ ''.^^ - . -.,- > ^1 0. S., aged twenty-five years. Woman with the anginose form of scarlet fever, treated at the Municipal Hospital. Subsidence of temperature on the fifteenth day. Recovery. The glands at the angles of the jaw become rapidly swollen; they commonly attain the size of a walnut or even a small apple. The surrounding cellular tissue participates in the general inflammatory- process, producing great cervical intumescence and often causing the child's head to be bent backward. Upon inspection of the throat the tonsils, arches, uvula, and soft palate are, during the first couple of days, seen to be intensely reddened and oedematous. Even at an early date there is a hypersecretion of a viscid, stringy mucus, which adheres to the tonsils and soft palate, and, becoming dry as a result of the mouth breathing, occasions much annoyance to the patient. Commonly by the third or fourth day a membranous exudate appears upon the tonsils, uvula, and soft palate, 384 SCARLET FEVER extending often to the pharynx and posterior nares. The occlusion of the nasal channels further obstructs the ingress of air and distresses the already harassed patient. The buccal and alveolar mucous membrane is greatly congested, and often the seat of ulcerations from which blood oozes. The teeth, gums, and lips are covered with sordes, and an offensive, at times fetid odor is emitted from the mouth. The tongue is of an angry-red color and occasionally ulcerations, covered with a grayish exudate, are seen upon the edges. As has been stated, the nose discharges a purulent material and commonly shows ulcerations of the mucous lining. The eyelids may also become inflamed, the conjunctiva congested, and a purulent discharge issue from the palpebral cleft. The child is often unable to swallow, water or milk being ejected through the nose. The nasal and faucial respirations are of a rattling character and painful to behold. The extension of the morbid process along the Eustachian tubes leads to a purulent inflammation of the middle ear on one or both sides. Rupture of the tympanic membrane occurs with the evacuation of the purulent accumulation. The external auditory canals become infected by this discharge, and often develop ulcerations which may eat quite deeply into the tissues. The child with a bad anginose scarlatina is a pitiable object — it lies with the head back to prevent the pressure of the swollen glands from compromising the breathing; the neck is greatly tumefied, the overlying skin stretched and glazed, the commissures of the mouth fissured and covered with blood crusts, the nose discharging a sanguinopurulent matter, the eyelids swollen, and the ears expelling a thin, ichorous pus. Indeed, every orifice of the face gives issue to a putrid and foul-smelling discharge, which contaminates the atmosphere about the patient with the stench. The general symptoms are those of a profound septicaemia. In extremely bad cases, and in our experiences more particularly in mixed cases of scarlet fever and diphtheria, extensive ulceration and sloughing of the tonsils or soft palate may take place. The necrosis in such instances involves the entire thickness of the tissues, and leads commonly to perforation of the soft palate. We have in a number of cases seen these perforating ulcers of the soft palate; they may be bilateral, or occur only upon the one side. The accompanying symptoms are pf a septic character, and the prognosis is unqualifiedly bad; death takes place in almost every case. In fatal cases of anginose scarlatina death may occur as a result of the severe primary blood poisoning, or through the development of the later complications, such as nephritis, pneumonia, endocarditis, etc. Bronchopneumonia is more frequent than is commonly believed, the symptoms being masked by the severe angina and the grave toxaemia. The urine is diminished in quantity and nearly always contains albumin. The microscope will often discover the presence of tube casts and also red blood corpuscles. A fatal termination is preceded by rise in the temperature to 106° or 107° F., an increasing prostration and stupor, and a progressive 77//'.' HYMPTOMATOI/XIY OF SCARfJ'/r FHVHIt 385 weakening and augmented frc(|ii(iicy i)\ I he juilsc. Fatal cases usually succumb during the first or scscond wc(;k of the illness. In severe cases of angiiiose scarlatina the lym})halic glands and adjacent tissues, under the influence of intense inflanimatif)n or, y>erfiaps, a special infection, may inulergo f/anr/rene, leading to gr(;at sloughing and even alarming or fatal hemorrhage from the erosion of some large bloodvessel. Trousseau speaks of a case in a boy of fourteen " in whom the gangrene condition was so extensive that tlie muscles of the neck were dissected, as occurs in diffuse phlegmonous inflammations, showing the carotids pulsating at the bottom of a horrible wound." In cases that end in recovery the temperature at about the end of a week or ten days begins to decline, the pulse slows and acquires Ijetter volume, the marked nervous symptoms gradually disappear, and the throat and adjacent cavities show a lessening in the intensity of the inflammatory process. The decline in the temperature is slower and lesS regular than in the usual type of the disease, and the normal is seldom reached before the end of the third or fourth week. Con- valescence is apt to be complicated by nephritis and in some cases by rheumatism and endocarditis. Scarlatina Maligna. Malignant scarlatina, a fortunately rare form nowadays, is char- acterized by such a sudden overwhelming of the vital forces as to cause death in a few days, or, indeed, within twenty-four hours. The symp- toms, consisting of extremely high fever, severe brain symptoms, and profound prostration, with or without hemorrhages into the skin and from the mucous membranes, develop with fearful rapidity, and the patient sinks under the dread influence of the poison. The abruptness of the onset of the disease in these cases is remark- able. Children in the enjoyment of apparent perfect health may be smitten while at play. The child has a severe attack of vomiting, which may be accompanied by purging, and is followed by convulsions or stupor. The temperature rises rapidly to 107° or 108° F., the pulse to 140 or 150. Great restlessness and delirium may alternate with stupor. Excruciating headache and violent pains in the extremities are some- times present. The eruption is usually irregular, appearing often on the hands and feet before it is seen on the body. At times it appears only about the flexures of the joints. The rash may recede after a brief presence, only to appear a few days later. It is sometimes partial, assuming an er\'sipe- latous aspect on the face or legs. It has commonly a h\dd hue, being beset with petechise and vibices. The local symptoms in malignant scarlatina are severe. The throat is so intensely swollen that swallowing is often impossible. The glands are greatly enlarged, and, if the patient hves long enough, the nose and middle ear become involved. Prostration and collapse may occur so suddenly that no eruption 25 386 SCARLET FEVER appears. The skin is pale or livid, the lips blanched, the eyes glassy and sunken with partial closure of the lids, the surface cold, the pulse weak and fluttering, and death imminent and inevitable. This choleraic type at times cannot be diagnosed without the presence of other cases of scarlet fever in the same household. These rapidly fatal cases are rare, but well-authenticated instances are recorded. Morris^ speaks of a child that was taken out apparently in perfect health for its morning airing and brought back within an hour with stupor and general muscular relaxation, cold surface, feeble pulse, and total insensibility; death occurred in twelve hours. Within a few days two other children in the same family were seized with scarlet fever which ran a regular course. Dr. Rush reported "a few instances of adults, who walked about, and even transacted business, until a few hours before they died." Such a case is mentioned by Morris; "A judge Fig. 69 M E M E M E M E M E M E M E M E M E 105° I < 1 104' < lOS' ^ A , \ •* ^^ . \ ID ^^ " S^ O z y \ D / V to V ^ s ^ j ^ < 1 / °/ DAY OF DIS. CJ CO -K o PULSE LOO 162 ICO 106 120 170 100 166 166 172 150 150 150 150 160 161 RESP. 60 46 52 16 18 10 16 50 50 56 15 12 18 40 16 10 W. R., aged three years. Case of malignant scarlet fever with high temperature, dying upon the fifth day of the disease. of one of the courts was seized with nausea while on the bench and retired to his home, where for two days he remained, scarcely willing to admit himself to be sick, and reluctant to confine himself to his chamber, though the rapid, feeble pulse and an imperfect eruption too plainly indicated the nature of the affection; on the third day he died while in the act of shaving himself." A near relative stood beside the corpse and contracted a similar fatal illness. Gregory^ in referring to malignant cases says: "In some extreme cases ... all the ordinary appearances of scarlet fever are masked; petechise, coma, and a sloughy state of the throat alone appear." And further he remarks there are cases "where no affection of the skin takes place at all." As an instance thereof he attended a woman and two grown-up daughters, in all of whom "the nervous system was utterly prostrated, or in the state of collapse. There was no violence, no delirium, no struggling for breath, no rash; but the pulse was small, 1 Pathology and Therapeutics of Scarlet Fever. Philadelphia, 1858. 2 Loc. cit. 77//'; HVMI'TOMATOLOdY OF SCMfLhri' [''KYHIi. 387 the skill cold, iuxl (Ik; whole; syslcm depressed hy llu; inlcnsily reratnre hoverefJ between 99° and 101° F. until the eif^hteenth day, when it rose to 105° F. Accompanying this rise there were headache, abdominal pain and diarrlux'a, and a recurrent, very bright rash; no throat symptoms. Urinary examinations were n(!gative. 'i'lircc; chiys hiter a second desqua- mation began. 'Vhe temperature jk^w grachially d(;cl ned, reaching normal on the twenty-seventh day of the disease. The patient was believed to be well, when on July 6th, or the thirty-second day of the disease, the temperature again rose to 101|° F. The patient com- plained of a sliglit sore throat, and a rash, followed by a fine desfjuama- tion, appeared on the face, arms, and trunk. The tem})erature declined quite promptly; the patient made a good recovery and was discharged from the hospital on July 26th. Fig. 70 105" 104 M - EB /I E M E M E M E M E M F M k" M E M E M E M fi M E M ; ME m E M E M E M E M E M E, M Ej M E P E M e'm'e!m'eVe'm*e'v e mIe - r - - - - - ^ - E E q - E ;^ - - ee! ; - E E E E E z _ - tizh" ^ - 1 :^ E E - - - ~ - ~ E = : Z ~ E E E E : J H = Z E 5 E E E E z E z : ^103" I \ - _ 1 _ - E \ - ; E E -£■ :EE E E ^ E E E E [ ^ EE E E E zzzz £,102' Z ^ „ 1 t ^ If Sl I il\ = E r z ee; :zz E z E z z z z - -♦ zz E : z |iof I 100° s H od" I §- -] i F '] I - y ^ i h y A i \ I 9 t \ i I y I ^ EEi 3:; ^ ^ ^ ? ^ ^ ^ \- tx E E 5" h \ EE 1 E E J=u= 98^ 97" z Ej :E z E = : E z z I : z z E=; :zz 1 = = EE E i- Z E E ^z ^ E : !<>; z n ^ i i u. DAY OF DISEASE 5 c 7 8 9 10 n 12 13 u 15 16 17 18 19 20 21 22 23 24 25 26 27 IS 3 2 33 3i 35 36 PULSE ||g§ i "loSls 4 ± Colo .|..|. ± S s|f-l|; :|| i Eb ft 4 s|g * m °Js i 1 1 ^i^ 4 F^^-h Scarlet fever ; two relapses. A. D., aged twenty-one years. It is seen that the first relapse occurred upon the eighteenth dav of the disease, and the second upon the thirty-second, or just two weeks later. Complications and Sequelae of Scarlet Fever. Throat.^ — Angina is an essential feature of the symptomatology of scarlet fever and cannot be regarded as a complication except where it is excessively developed. The most moderate expression of the scar- latinal sore throat is a uniform congestion of the uvula, anterior pillars, and tonsils. This form has been designated as erythematous angina. In more severe cases the mucous membrane is greatly swollen, and there is extension of the catarrhal inflammation posteriorly to the pharvngeal wall and anter'orly over the soft palate; these parts are of a deep- red color and bathed in a profuse mucoid secretion. The swelling of 396 SCARLET FEVER the soft palate may be so intense as to seriously interfere with swallowing and to cause the regurgitation of liquids through the nose, The tonsils may also exhibit great increase in size and embarrass both deglutition and respiration. In the membranous variety of angina the mucous membrane of the tonsils is covered with an exudate, which is usually of a yellowish or brownish tint and thinner and softer than the membrane of true diph- theria. While in most cases the pseudomembranous deposit is limited to the region of the tonsils, it is not uncommon for it to be present upon the half- arches and also scattered in patches upon the soft palate. It may likewise spread by way of the pharynx into the posterior nares and, in rare cases, to the tongue and buccal mucous membrane. Exten- sion of the process along the Eustachian tube gives rise to inflammation of the middle ear, a most frequent complication of anginose scarlet fever. The glands about the angles of the jaw undergo inflammation and tumefaction and commonly suppurate. Pronounced constitutional symptoms accompany this variety of the disease. The temperature hovers about 104° or 105° F., and there is marked disturbance of the nervous system. Intense restlessness, delirium, stupor, coma, or con- vulsions may be present. The pulse is extremely frequent, often reach- ing 140 or 150 beats per minute. There is profound prostration, the urine contains albumin, and the patient is completely overwhelmed by the poison of the disease. When there is extension of the process to the nose a purulent rhinitis is set up. There is a profuse discharge of a thin mucopurulent and often blood-stained material, frequently containing shreds of membrane. This irritating discharge inflames the nostrils and the upper lip and gives rise to impetiginous sores. The nose is swollen and the nostrils obstructed, causing considerable difficulty in breathing. An offensive odor is given off which can be detected some feet from the bedside. The nasal inflammation is attributed to the action of the streptococcus, the extension of whose pernicious activity may give rise to infection of the nasal sinuses. French writers have called attention to the bad prognosis in these cases of early purulent coryza. The mortality in the Aubervilliers Hospital was over 50 per cent., and this complication was feared more than the most malignant forms of angina. The membranous inflammation may extend to the larynx and produce serious difficulty in respiration. As has already been stated, however, laryngeal involvement is extremely rare in scarlet fever. In normal scarlatina the larynx is exempted, and the mucous mem- brane, being in a healthy state, is not particularly susceptible to the noxious influence of the streptococcus or the diphtheria organism. In measles, on the other hand, the larynx is primarily involved and the soil is rendered favorable for the implantation of these micro-organisms. The gangrenous variety of angina is fortunately rare, and is, for the most part, observed in hospitals. The gangrene may begin upon the tonsil, at the site of the rupture of an abscess. The necrotic process 77//'; (JOM/'fJCATfONS OF SCAUfJ'/r F/CV/af Pjij-J may involve the eiiiiro ton.sil, which .sloughs out enmassc. In soine cases the gangrene is hinited to the tonsillar tissues; in others it spreads beyond, attacking and destroying the palatine arches, the uvula, and a considerable portion of the soft palate. The affected parts are at first covered with a grayish-blac-k, puhaceous de[)osit, which, when thrown off, discloses to view frightful loss of tissue. The odor cmitfcd frf)m these cases is foul and penetrating. The nose and ears are commonly involved and give exit to an ichorous discharge. The glands of the neck are greatly swollen; the constitutional depression is profound. In our experience tlie most common form of gangrenous angina has been characterized by circumscribed necrosis of the soft parts, particularly the soft palate, leading to irregular or rounded perforations about a half- inch in diameter. This condition may develop early, or may be po.st- poned to the second or third week of the disease. We have observ^ed this complication much more often in mixed cases of scarlet fever and diphtheria than in scarlet fever alone. The prognosis in this circum- scribed gangrene is very unfavorable, although patients occasionally recover with considerable deformity of the soft palate. In extremely rare cases gangrene may commit frightful ravages. The connective tissue of the neck may become involved, the overlying skin destroyed, and the muscles and large bloodvessels laid bare. Where the patient does not die of hemorrhage from erosion of the carotid artery, jugular vein, or other large bloodvessels, he is sure to succumb to the blighting influence of the septic poisoning. Recovery can only take place where the gangrene is limited to small areas. Secondary Angina in Scarlet Fever. — The throat involvement thus far described occurs early in scarlatina and influences to a considerable degree the course that the disease takes. A secondary angina may develop late in the disease; indeed, at times after convalescence is established. It is not rare for the tonsils to become the seat of a severe inflammation, increase greatly in size, and after a few days undergo suppuration. The neighboring soft palate becomes reddened and greatly tumefied. There is distressing pain, and speech and swallowing are difficult. W'^e have here the usual symptoms of a suppurative tonsillitis or quinsy. In some cases the tonsillitis subsides without pus formation. We have observed these late anginas in hospital wards, a circumstance wdiich suggests a second infection from without as the cause. Similar attacks of tonsillitis have occurred in ward maids and nurses, a fact which renders this view all the more plausible. Postscarlatinal Diphtheria. — Before the days of bacteriology all cases of membranous angina were regarded as diphtheria. It is now recognized that the membranous deposit frequently seen in the throat early in the course of scarlatina is nearly always due to the streptococcus. Diphtheria is, as a rule, a complication of the stage of convalescence. Caiger^ gives the date of "onset of 408 cases of postscarlatinal diph- theria : 1 Article on Scarlet Fever iii AUbutt's System of Medicine, p. 161. 398 SCARLET FEVER Time of Onset of 408 Cases of Postscablatinal Diphtheria (Caigee.) Percentage Weeks. Cases. of total cages. One 11 2.69 Two 36 8.82 Three " 55 13.48 Pour . . ' 77 18.87 Five 54 13.23 Six 46 11.27 Seven 38 9.31 Eight 27 6.61 Nine 18 4.41 Ten 13 3.18 Eleven ........... 9 2.20 Twelve 9 2.20 Over twelve 15 3.67 It is seen from the above figures that the susceptibihty to diphtheria is most pronounced from the third to the sixth week of scarlet fever. Cases of postscarlatinal diphtheria are much more common in hospital than in private practice. In large hospital wards it doubtless occasionally happens that a secondary diphtheria remains undetected and exposes other patients to the infection. The mortality of mixed cases of scarlatina and diphtheria is, as would naturally be expected, higher than that of primary diphtheria. There is nothing in the clinical or pathological picture of postscar- latinal diphtheria to distinguish it from primary diphtheria. It is usually limited to the tonsils and adjacent half -arches, although it may exhibit greater extent and spread to the posterior nares or to the larynx. The thick, grayish-white exudate contrasts strongly with the thin, smeary, yellowish or brownish deposit seen in the early stages of scarlatina. Paralyses, such as are seen after diphtheria, are excessively rare after scarlet fever. This observation is so well attested that when paralysis occurs after scarlatina there is a reasonable ground for the suspicion that a mixed infection has been present. The diagnosis will, in large measure, rest upon the bacteriological findings. The presence of the Klebs-I.(OefHer bacillus in a throat which is the seat of exudate indicates the existence of diphtheria. Since the specificity of the diphtheria bacillus has been established, numerous examinations of scarlatina throats have been made to deter- mine the character of the membranous angina. Chabade,"^ of St. Petersburg, made cultures of 214 scarlatinal throats; of these, 98 had a catarrhal angina, 33 had a lacunar angina with a pseudomembrane in the tonsillar crypts, and 83 had a pseudomembranous angina involv- ing the tonsils and adjacent soft tissues. In the catarrhal group no diphtheria bacilli were found, but strepto- cocci and, at times, staphylococci were present. In the lacunar anginas the Klebs-Loeffler bacillus was found twice. In the pseudomembranous cases the diphtheria organism was found eleven times, thrice almost in pure culture, and in eight cases associated with the streptococcus. 1 De 1' Association de la scarlatina avec la diphth(Srie, La semaine m6d., 1899, p. 184. Quoted by Northrupln von Jiirgenseu's article on Scarlatina in Nothnagel's Encyclopedia of Practical ^Jledicine, 77//'; COMI'LldATIOSH OF SdAltLHT I'l'lVhlK ,'}li9 Variol jukI I )ev6' examined (lie iliroats of 525 cases of scarlatina. Of this nuiiilx'r ()2 liiul exudate in the tliroat, 'M) of whifh proved fo l;e true dij)htlieriii,. Garret and Waslihourn,'' from cultures of the tliroat of fJOO patients treated in the r.ondon Fever Hospital from 1890 to J SOS, foinid that over 1 per cent, showed Klebs-LoefHer bacilli on admission. For tlu^ |)nst few years we have made cultures of all scarlatina [)atients admitted into the Municipal Hospital. The (;ulturcs were made at the home of the patient, in the ambulance, or after entrance to the ward. In one series of cases, in which cultures were made after the admis.sion of the patients to the ward, there were 1G7 negative results and SO po.si- tive, or 32.85 per cent. In a second series of over 500 cases, in which the cultures were taken either at the home of the patients or immediately after their reception into the ambulance, the results were as follows: Negative cultures . 74 Positive cultures . 26 . HS . . 17 . 77 . . 23 . 65 " M not recorded) 34 . 81 . . 19 . 10 . . 3 390 122 Percentage, 23.8 A further series of 500 cases, some cultured before admission to the wards and some shortly after, gave the following figures: Negative cultures . . 87 Positive cultures . . 13 .84 " " . . 16 .80 " " . . 20 .86 " " . . 14 .80 " " . . 20 417 83 Percentage, 19.9. The aggregate of these figures gives a total of 1259 cases, of which 285, or 29.25 per cent., yielded positive cultures.^ The throats in many of the positive cases showed merely evidences of catarrhal angina. Subsequent cultures in the positive cases would at times be negative, but in not a small number of instances three or four positive cultures were obtained. There were comparatively few patients in whom the diagnosis of diphtheria would have been made from the clinical appearances. The diphtheria patients are treated in a building which is quite apart from that occupied by scarlatina patients. i\Iixed cases are treated in the same building, but in a distant wing. Ears. — Inflammation of the middle ear is, perhaps, the most com- mon complication of scarlet fever. 1 SoG. m6d. des hop., 1900, xvii. p. 1025 ; quoted by Norttirup, loc. cit. 2 Ann. de mtJd. et chir. enfant, 1899, t. iii. ; quoted by Northrup, loc. cit. s These cultures were examined and reported upon by the City Bacteriological Laboratory, which Is under the supervision of Prof. A, C, Abbott, of the University of Peunsylvania, 400 SCARLET FEVER Its frequency varies with the character of the epidemic and with the age of the patient. In the anginose variety of scarlatina middle-ear disease follows in almost every case. Some epidemics appear to be characterized , by a much smaller incidence of ear complications than others. Holt mentions the fact that in an epidemic occurring in the New York Infant Asylum in the spring and summer of 1889, there were 73 cases of scarlet fever and not one developed otitis. In a fall and winter epidemic in the same institution, two years later, of 43 cases of scarlet fever, 20 per cent, developed otitis. The frequency of otitis in different epidemics is influenced by the degree of angina present, and also to some extent by season, middle-ear trouble being more prevalent in the colder months. Infants are more liable to develop otitis media than children of more advanced years. This may be due to the relatively large size of the Eustachian tube in infancy. Finlayson states that otitis was present in 10 per cent, of 4397 cases of scarlet fever reported by him. Caiger^ analyzed 4015 cases of scar- latina, and determined that otitis media with discharge took place in 11.05 per cent, thereof. Burckhart reports this complication in 33 per cent, of cases. In attacks with severe throat involvement otitis occurs, according to Holt, in fully 75 per cent, of cases. Bader and Guinon^ report 33 per cent, involvement in the form of mild or catarrhal otitis, and purulent otitis in but 4.5 per cent, of cases of scarlatina. Middle-ear disease results from direct extension of inflammation from the nasopharynx and doubtless through the action of the bacteria, chiefly the streptococcus. This complication may develop at any time during the course of scarlet fever, even as late as during convalescence. It is apt to develop early in bad cases with severe throat involvement. In 18 cases of otitis media recently observed by us the discharge appeared upon the following days: Day of Scarlet-fever Illkess upon which Eighteen Cases of Otitis Media Developed. 1 on the 6th day. 1 on the . . 18th day 1 " " 8th " 2 " " . . 19th " 2 " " 9th ■' 1 " " . . 20th " 1 " " 10th " 1 .. <. . . 21st " 1 " " nth " 1 " " . . 22d " 1 " " 13th " 1 " " . . 23d " 1 " " 16th " 1 .. .< _ . 32d " 1 " " 17th " 1 <. » _ . 35th " One or both ears may be affected; when both are attacked the dis- charge does not, as a rule, appear simultaneously, an interval of four or five days or a week separating the two attacks. When the ear complication develops early in the course of the disease, while the temperature is high and nervous manifestations still present, the symptoms thereof are apt to be obscured by the general condition of the patient. When the otitis appears^at a later date, after the scar- 1 Scarlet Fever, Allbutt's System of Medicine, New York, 1897, vol. iii, p. 150. ' See Moiisard, Scarlatine, in Traits des mal, de I'enfance, Paris, 1897, vol. i. 77//'; COMI'IjIdATION'H OF .ST.l /,'/./<; 7' FKVKli 401 latinal fever has declined, ils df-vclopincnf, is acicornpanicd by a sharp rise of tcirij)erature. The fever is usually preccicled hy pain, alfhfjugh this symptom is extremely variable. Infants will often carry their hands to their cars and uftcr shar[) shrieks. \w some cases there is eiilar^(;m(Mit and tenderness of lyiiij)ha.fic glands about the (^ar. The otitis may be a simj>lc caiarrhal irdlamination, or it may be furulent or suppurative. In the formc^r variety the duration of the affection is much shorter and of a less serious character. The fever, pain, and tenderness subside rapidly after spontaneous rupture or incision of the tympanic meml)rane. Purulent otitis media pursues a much more protracted course. A mucr)- purulent discharge may continue for weeks or, indeed, the condition may lapse into a chronic suppurative otitis. The immediate dangers associated with this condition are extension of the purulent inflammation to the mastoid cells or meninges of the Ijrain, the erosion of bloodvessels, with the production of serious hemorrhages, and finally the development of septictemia or pysemia. Cases are on record in which the erosion of large bloodvessels has led to fatal hemorrhage. Baader^ reports the case of a three-year-old boy suffering from a purulent otitis complicating scarlatina, who developed on the eleventh day of the disease a severe and uncontrollable hemor- rhage from the . ear which caused death on the third day. Autopsy disclosed a perforation of the posterior wall of the tympanic cavity and an erosion of the lateral sinus. Hessler^ records a case in which a fatal hemorrhage resulted from ulceration of the carotid artery. A similar case is reported by Hynes,^ in which a sudden and unlooked- for hemorrhage poured from the right ear in a four-year-old child. The child later vomited blood in large quantities and died. It was thought that the bleeding came from the internal carotid artery. Hliber* reports a case of hemorrhage from an eroded vessel which caused a haematoma of the neck, the opening of which resulted fatally. Kennedy has reported three fatal cases of hemorrhage, and ]Moller and West each one instance. The following case of septicaemia associated with purulent otitis was observed by us in the Municipal Hospital in 1SS9: F. F., a boy aged thirteen years, was admitted to the hospital on February 2d, with a bad anginose scarlet fever. His condition improved for a week, the temperature reaching normal. On February 10th the patient had a chill with a rise of temperature to 104f ° F. On the follow- ing day another chill and a temperature of 107f ° F. The next day the temperature rose to 107i° F. For a period of ten days there occurred the most violent rises and falls of temperature, the extreme limits being 95i° and 107i° F., an excursion of 12 degrees. Chills recurred each day and on one occasion repeated vomiting. The ear which was discharging 1 Acute Verblutung bei Scharlach, Corres. bl. f. Scbweiz. Aerzte, 1875, Bd. v. 2 Quoted by Forchheimer, loc. cit s Quoted by Forchheimer, loc. cit . ■• Deutsche Archiv f. klia Med., Bd. viii. p. 422. 26 402 SCARLET FEVER was kept thoroughly clean with a carbolized solution. By February 27th the patient had recovered sufficiently to leave his bed (Fig. 71). The immediate dangers of purulent otitis having been passed, there remain severe structural changes which may seriously interfere with the sense of hearing. There may be partial or complete loss of the tympanic membrane upon one or both sides ; occasionally the ossicles are destroyed and thrown off. Ulceration and necrosis of the walls of the tympanum may occur, with the development of further complications to which Fig. 71 _^ ^ ,107 106° 105° .104° ^103° < •;;;102° S 101° r ~ +1-- — !i 2 "-\ T r ? — — —^- E n " ^ ". si T- CL r . W, — £ - 1 "!i: — _5_ S ,._. s -2 T- - - ■ -^ ■ _^ . .^. ^-U ■*-t^ ir ■ 3 ■ -< ■ -i-r- 5 \ . ± . . i : — J- —E^.- "* X — ■ -1 ^___ 1H ^ — i-p -■s — \- 1 — i --, i — jf - HI 2 . r v j=, — 2. -i ^ F' 1 ■ ^ ?L tt ^ _.3_ - s :3:::i: i. - -j: : ^ 100° 99° 98° 97° 96° p= -I- — -- 1 s A /\ \f A •- ■" CL \ A . - £ _ CO - _i - -e-HJ- _ . ^, ( ^ : Va A" ^ ^— -1- i TE - t-'i S X* / " ^. V m --< v^ V— _m L . -^ _ _ ?" o '^ ,_ri / \ /" J^ \-^ J i-A^ "^r:<~ '3X ^f J^ .E_i_ .J E — v^ 2 :;tfc '"' ^ J 2 1; — -1 — "" - 1^ ^ « \ \ r^^ \ 5: 4 — oi — —^ i — \ OJ 5 •^ •- u> DAY OF DISEASE 1 3 3 4 5 6 7 8 9 10 11 12 13 14 15 16 1 7 18 19 S 21 PULSE »=o sg SS o o gg s|s 3|g s^sSi 2"sHS° S^f gS? 3 S § g s I s ss|s g f2 S ^§|§ Remarkable excursions of temperature due to suppurating otitis media. F. F., aged tliirteen years, admitted to liospital in critical condition : bad throat and mouth ; ears discharging on second day of disease. Various rises of temperature accompanied by chills ; ultimate recovery. reference will be made later. The labyrinth may be attacked in rare cases. Pye, Phillips/ and others have reported cases in which laby- rinthine structures were necrosed and discharged en masse. These patients were, of course, left completely deaf. Bezold^ gives the results of 185 cases of scarlatinal otitis: "In 30 there was entire destruction of the membrana tympani, with the loss of one or more bones ; in 59 the perforation comprised two-thirds or more of the membrane; in 13 there were smaller perforations; in 44 there were granulations or polypi; in 1 Quoted by Holt, loc. cit. 2 Quoted by Holt, loc. cit. TIIK COMPLICATIONS OF HCAIfLh'/r FEVhlli 403 15 there was total loss of liearing on one side, and in f»f the cases on both sides; in 77 of the cases the hearin^^ distance U)V low voice was less than twenty inches." Burckhardt-Merian' reported XS cases of ear corn[)hcations of which 72, or 84.7 per cent., involved both ears. Of 4'MY.) cases of acrpiircd deafness and dumbness, 445, or 10. .'i per cent., were due to scarlet fever. May, of New York, has collected similar statistics; of 5613 cases of deaf- mutism, 572 were traceable to attacks of scarlet fever. Purulent otitis may, in rare cases, give rise to disease of the mastoid antrum. This may occur during convalescenc;e from scarlet fever or may develop after the otitis has become chronic. The mastoid region is painful and tender and acquires a characteristic appearance — the great postauricular swelling causing the ear to stand out prominently from the head. The temperature rises to 103° or 104° F., and, unless there is operative interference, brain symptoms may manifest themselves. On incision a mastoid abscess is found present. At times a superficial abscess is found in the region of the mastoid, without actual involvement of the mastoid cells. Thrombosis of Lateral Sinus. — Thrombosis of the lateral sinus is occasionally encountered in cases in which cerebral abscess or meningitis subsequently develops. The onset is sudden, with chills and high and irregular fever. Facial Palsy. — Facial palsy is by no means a rare complication of scarlatinal otitis. We have observed this paralysis in a number of cases of severe middle- ear disease. It is due to an extension of inflammation from the tympanum to the facial nerve, where it passes through the roof of the cavity. The symptoms do not differ essentially from facial palsy occurring from other causes. Abscess of the Brain. — Abscess of the brain may result from extension of the suppurative inflammation from the middle ear. The petro- squamous suture being patulous in children, an avenue of infection to intracranial structures is readily offered. The periosteum of the tym- panum is continuous with the dura mater, and extension of inflammation may occur along this membrane. In addition, the infection may be carried to the brain through the medium of the veins. Purulent Meningitis. — Purulent meningitis is an extremely serious complication that may arise from a suppurative otitis. It may have its origin in thrombosis of the lateral sinus or may develop from necrosis of the roof of the tympanic cavity. There are usually high fever, stiffness of the neck, retraction of the head, vomiting, and, at times, parahiic eye symptoms. Death occurs ordinarily in about a week. The following case will illustrate the symptomatology of this complication: W. J., aged three years, was admitted to the INIunicipal Hospital on April 9, 1903, with a severe attack of scarlet fever. On the sixth day of the disease the right ear discharged. Fever was protracted, the temperature not touching normal until the thirtieth day. Later the 1 Ueber den Scharlach in seinen Beziehungen zum Gehurorgan ; Volkmann"s Sammlung klin. Vortriige Chir., No. 54. 404 SCARLET FEVER temperature rose as the result of a cervical abscess. There was no fever from the forty-fourth to the fifty-fourth day. At this time the temperature began to rise and the patient vomited. He cried out sharply upon being disturbed. A gradually increasing stuporous state developed. The neck was rigid and the head retracted. The pupils were equal and reacted to light. The patient gradually lapsed into complete coma. The temperature rose to 106f ° F. and the patient died on the ninth day of the complication and the sixty-fourth day of the scarlet fever. When the skull was opened at autopsy a foul odor was immediately noticed. A purulent exudate was found covering the entire base of the brain, but involving chiefly the left side. The pia mater under the left cerebellum was infiltrated with pus, and there was free pus in the various fossae. There was no discoverable caries of the petrous portion of the temporal bones, and on opening these no pus could be detected. Cultures from the purulent material demonstrated the presence of the staphylococcus pyogenes aureus. Complete Deafness .^ — Complete deafness not due to middle ear disease occurred in a boy, aged five years, at the Municipal Hospital, during convalescence from a well-marked attack of scarlet fever. The patient had been out of bed for a number of days, when he was suddenly taken ill with high fever, vomiting, heavily coated tongue, and delirium. This was shortly followed by pronounced mental hebetude; vomiting persisted for several days, nothing being retained upon the stomach. Mental dulness continued for several days, after which, upon the clearing up of the mental faculties, it was noticed that the patient was absolutely deaf. There had not been any discharge from the ears nor any other evidence of otitis. The mastoid region was normal. The temperature for a week or ten days was markedly irregular, fluctuating rapidly between 99° and 104° F. About the same time that deafness was noted there was a paralytic strabismus. The patient left the hospital absolutely deaf. The internal ear was doubtless diseased in this case, perhaps as the result of a localized meningitis. Eyes. — In cases of severe scarlet fever, particularly where there is a purulent rhinitis, extension of the inflammation may take place and a severe conjunctivitis set up. More often the conjunctivitis that develops is of a mild character, with injection of the bloodvessels of the sclera and lids, increased lacrymation and photophobia. The lacrymal duct and gland may become involved through the infection that has its origin in a purulent coryza. Through this channel other ocular structures may subsequently be attacked. Primary Keratitis. — Primary keratitis with its unfortunate train of symptoms develops at times, particularly in scrofulous subjects. We recall a corneal ulcer in a colored child, who had previously suffered from keratitis, in whom perforation with prolapse of the iris occurred. Leichtenstern reports 2 cases of corneal ulcer and 1 of hypopyon keratitis occurring in a severe epidemic in the hospital at Cologne. Thomas quotes Schroter as saying that the cornea may be affected primarily and independently, usually in the way of rapidly progressing abscesses Till'] aOMI'LldATIONS OF SCA/ifJ'JT FJ-JVJ'J/i 405 or suppurating ulcers or pernicious keratomalacia, in wliicli tfie cornea of one or both eyes, witliout any marked symptoms, hecfjmes turl^id in a few (lays, is transformed in its totality info a turhid, dirty, grayish- white membrane, and exfoliates piecemeal. The inflammatory |)rocess may travel thence over the uveal tract and cause a panophthal- mitis. Choroiditis. — Choroiditis may, in rare cases, com[)licate scarlet fever. In the epidemic already alluded to TiCiclitenstern saw a case of choroiditis which ended in phthisis bulbi. In those cases in which a severe nephritis is present ophthalmoscopic examination may reveal the existence of an alhuminuric retinitis. Both eyes are usually equally and simultaneously affecterl. After a protracted course more or less complete restoration usually results. Temporary blindness, or amblyopia, may complicate the kidney con- dition; after some days complete visijDn is usually restored. We have personally observed such cases. Porter' saw a young girl with severe complications, develop temporary blindness with exophthalmos from infiltration of the cellular tissue of the orbit. DuvaP saw a similar case of exophthalmos lasting ten days, the sight being subsequently fully restored. Within the past few years we have observed in the Municipal Hospital two cases of orbital cellulitis complicating scarlet fever and leading to a fatal termination. These cases were seen and studied by Dr. Burton K. Chance,^ Assistant Surgeon to the Wills Eye Hospital, Philadelphia, to whom we are indebted for careful notes of the cases: Case I. was a boy, aged seventeen years, who during a protracted convalescence from a severe scarlet fever developed a sudden diffuse cellulitis of the right orbit. A chill and sharp rise of temperature were followed by an effusion of fluid into the areolar tissue, with protrusion of the globe. The eyelids were red and excessively oedematous. The fundus was at first pale, but later intensely red, with fine hemorrhages. There was marked swelling of the disk, an overdistention of the veins, and contraction of the arteries. A day or two before death the cornea became necrotic and the eye was lost. High fever, delirium, and coma preceded death, which took place one week after the development of the complication. The examination of the orbital structures after death revealed only a diffuse serous infiltration; there was no evidence of intraocular suppuration. Case II. was a boy, aged ten years, who was convalescing from scarlet fever, when there developed in the right orbit an acute congestion with infiltration of the tissues, producing proptosis between the intensely oedematous lids. The local symptoms were similar to those in the first case. Throughout the course of the process the cornea remained unaffected. Deep incisions were made into the periocular tissues, evacuating a quantity of blood-tinged serum, but no pus. On the eighth 1 Quoted by Thomas. 2 Quoted by Thomas. 3 Dr. Chance reported his findings in a paper read before the Philadelphia County Medical Society, May 27, ]903. This was published in American Medicine, June 13, 1903, p. 960. 406 SCARLET FEVER day after the onset of the complication the patient was seized with con- vulsions and died. Permission to make an autopsy was refused. In rare cases failure of vision may be due to atrophy of the optic nerve or to detachment of the retina. O'ptic neuritis may occur with meningitis or without such involvement, as in a case reported by Putnam. Heart. — The heart may suffer in scarlet fever from (1) the scarlatinal toxin, (2) as a result of nephritis, and (3) from secondary infections, such as rheumatism, pyaemia, etc. That the scarlatinal poison has a direct influence upon the heart is seen in the early tachycardia, the heart beats being out of all proportion to the temperature. Furthermore, in mahgnant cases that are over- whelmed at the onset by the poison of the disease, the symptoms are those of an acute cardiac failure; the pulse is rapid, small, and irregular; the extremities are cold, and pallor and cyanosis are often present. In severe cases of the disease, the scarlatinal toxin, according to Romberg,^ may early cause a pronounced dilatation of the heart. The occurrence of nephritis in scarlet fever naturally leads to changes in the cardiac muscle. Whenever the kidney involvement is at all pronounced there will be found a hypertrophy and dilatation of the heart. The changes are apt to be present upon both sides, but the preponderant enlargement is nearly always found upon the left side. RiegeP states that in most, if not in all, cases of scarlatinal nephritis there is an increased arterial tension from the very beginning. After the blood pressure has persisted for some time, the heart enlarges as a consequence. In some cases the increased size of the heart may be noticed a few days after the onset of the nephritis. It is readily seen how this form of cardiac disease is produced. The development of nephritis by raising the arterial tension throws an extra burden upon the heart; if the heart has already been injured by the influence of the scarlatinal poison, the strain may be too much and acute dilatation may result. If the heart muscle has more recuperative power a compensatory hypertrophy may take place. If the left heart develops a pronounced insufficiency, a dilatation of the right side will usually occur. When this results we see the usual symptoms of cardiac insufficiency — dyspnoea, rapid pulse, enlargement of the liver, etc. A murmur may or may not be heard over the mitral orifice. It is important to recognize the fact that the bruit is not due to an endocarditis, but to cardiac dilatation. This murmur will be found to disappear as the heart improves. Myocarditis. ^ — ^Myocarditis is the heart condition which is most frequently called into existence by the scarlatinal toxin and by the associated nephritis. The other forms of heart disease are more commonly associated with secondary rheumatism or septic infection. Ashby found endocarditis not uncommon with rheumatoid affections 1 Ueber die Erkrankungen des Herzmuskels bei Typhus Abdominalis, Scharlach, etc., Deutsch. Archiv f. klin. Med., Bd. xlviii. p. 369, and Bd. xlix. p. 413. 2 Ueber die Veriinderungeu des Herzens, etc., bei Acuter Nephritis, Zeitschr. f. klin. Med., 1884, Bd. vii. p. 260 ; quoted by von Jurgensen, loc. cit. TffM aOMf'fJdATfO.MS OF SCARLET FEVER 407 devcloj)inf( in the third or fourth week of scarlet fever, hut not witli tlie early synovitis. Roger^ has found endocarditis an uncommon complication. Out of 2213 cases of scarlet fever (1727 in adults) examined by him, he saw but 2 cases of endocarditis. On the other hand, he noted extracardial murmurs 002 times. McCollom,^ in an analysis of 1000 cases of scarlet fever, says: "A mitral systolic murmur was detected in 187 cases; bruit de (jatop in 5 cases; irrcfj^nlar action of the heart in 54 cases; endocarditis in '> and pericarditis in 5 cases." Many of the murmurs referred to were thought to be due to lack of tonicity of the heart muscle as a result of the action of the scarlatinal poison. Von Jiirgensen expresses the opinion that endocarditis of the cardiac wall is more common in scarlet fever than valvular involvement. He further believes that tliis mural endocarditis may slowly extend to the valves after the attack of scarlet fever is over. Pericarditis. — Pericarditis occurs from time to time in the course of scarlet fever, being much more common in association with nephritis, synovitis, and pyemia than with cases of simple scarlatina. Roger has observed cases of dry pericarditis, both at the height of the disease and during convalescence. In pyaemia endocarditis and pericarditis are commonly present; the exudate in the latter affection in such cases may be purulent. Roger saw a child, aged eight years, with a severe scarlet fever complicated by a purulent otitis media, die on the forty-seventh day of the disease. At autopsy the pericardium was covered with a false membrane; there was an ulcerative endocarditis and an abscess in the wall of the left ventricle. The streptococcus was recovered from these lesions. In our own experience severe cases of endocarditis have been rare, and, w^hen present, have been accompanied by joint involvement. We recall a twelve-year-old boy who during the third week of scarlet fever had articular swellings which recurred from time to time for several weeks. He also had a well-marked albuminuria. This patient developed at a later period an endocarditis which severely damaged the mitral valve; he subsequently exhibited a presystolic murmur with a pro- nounced thrill over the mitral region. The murmur had a peculiar crowing sound of a musical character. After undue exertion he devel- oped a sudden dilatation of the heart with rapid pulse and a change in the character of the murmur which now became blowing. He was tided over this crisis, but a few weeks later he again developed a cardiac dilatation and died. A rather unusual symptom in this patient was a geographic erythema which appeared over the trunk from time to time, recurring apparently with fresh joint involvement and then gradually fading away. In another fatal case we observed a vegetative endocarditis attack- ing the mitral and aortic valves, associated with pleurisy, joint swelUngs, and extensive purpura. 1 Loc. cit., p. 941. ' Scarlatina, Medical and Surgical Reports, Boston City Hospital, 1899. 408 SCARLET FEVER Lymphatic Glands. — A generalized enlargement of the lymph glands constitutes a part of the normal symptomatology of scarlet fever. The subcutaneous lymph nodes in all parts of the body undergo some hyper- plasia, but those situated in the neighborhood of the facial orifices undergo the greatest tumefaction. That this primary lymphatic involve- ment is due to the scarlatinal toxin is evidenced by the fact that the lymphoid elements of the spleen, liver, and intestines become likewise hyperplastic. It is only when the lymph glands become excessively enlarged or undergo suppuration that a complication is added that augments the danger of the disease. The most aggravated cases of lymphadenitis occur in association with the anginose variety of scarlet fever. Greatly swollen and suppurating maxillary glands. In these cases the glands at the angle of the jaw undergo rapid enlarge- ment, causing the head to be thrown backward. This complication increases the suffering and danger of the child, who by this time is already prostrated by the poison from a sloughy throat and discharging ears and nose. The temperature is high, the nervous system markedly disturbed, and death imminent. By the fifth or sixth day of the disease the maxillary glands may already have attained the size of small apples. They are hard at first, but gradually break down and suppurate. In cases of scarlet fever of less severity, but accompanied by pro- nounced angina, it is not at all rare for the glands at the angle of the THE (!(>MrfJC'A7'ff)NS OF SCAUfJ'/J' F/'JV/er ct. Between 1 and 2 years . . 107 " 5 cases 4.6 " " 2 " 3 " . . 106 " 12 " 11.3 " 3 " 4 " . . 79 " IC " 20.2 " " 4 " 5 " . . 80 '• 20 " 23.2 " 5 " " . . 89 " 18 " 21.9 After 6 " . . 300 " 60 " .... . 16.6 While severe cases of scarlet fever are more apt to be followed by nephritis than mild cases, it is impossible in any individual instance to prophesy the development or the non-occurrence of this complication, because the scarlatinal attack may be severe or mild. There appears to be something in the individual make-up which predisposes one toward or protects one against a complicating nephritis. Doubtless each individual has certain organs or tissues whi^ch are more vulnerable to the noxious influence of the scarlatinal poison than others. The opinion formerly held, that "catching cold" plays any important role in the etiology of nephritis complicating scarlatina, is being dis- credited by most writers on the subject. Symptoms of Nephritis. — In some patients albumin appears in the urine for the first time during convalescence ; in other cases albumin- uria is a reawakening of the nephritic process that manifested itself early during the acute stage of the disease. The nephritis with its accompanying symptoms of intoxication ordinarily comes on insidiously, although in some instances it may explode with alarming suddenness. The development of albuminuria is accompanied, or often preceded, by a rise of temperature. A febrile elevation in the third week of scarlet fever will commonly be found to be due to nephritis. The character and duration of the fever are extremely variable. It may persist for a number of days or may drop to normal at the end of forty-eight or seventy-two hours. The tem- perature often exhibits striking irregularities, dropping to normal and suddenly rising again. Ordinarily the pyrexia is moderate in intensity, but it may rise to great height. We have seen a temperature of 106f ° F. 414 SCARLET FEVER accompanying a moderate albuminuria which appeared on the twenty- third day of the disease and disappeared on the twenty-sixth day (Fig. 73). In severe nephritis fever may persist throughout the duration of this compHcation. In some cases no fever is noted whatsoever. Before the appearance of the albumin, there is not infrequently noted a considerable increase in the quantity of the urine voided. As a result of this polyuria urination is frequent and may wake the patient from his sleep at night. Most writers refer to pain in the back as one of the early symptoms of scarlatinal nephritis; this lumbar pain cannot be frequent or severe, at least in children, for it is most rare to hear a complaint in reference thereto. Haematuria may be one of the early symptoms to direct atten- tion to the kidneys. Fig. 73 107" mIe" 2'" ■ " h- '- I - — :: ; - : F - - - - - - £ F - Fh - - — - -i-- "Th - - ■— - - z y^i lOG' 105' ZC EE I E 'Z _ Z. - E E = z E z i E 1 L E z z z - E E E r - - E - E E E E '- E z = z E^E - 1- - ^ - — - '- s - E -- I 101° w 103' < 102' 100' = = ~'Z ~ ^ E E E E = E E E E E E E E E E E _ ^ I E E E E E E j E ~ E E EE eF p 1 -^— ¥^ E EE 1 P 5 ^ ^ T- E - E = E = = E 1 ^ E E \ I E = - E E E E 1 E — E E \4\ E i 99' 98° DISEASE 1 2 ^."^ E E r \ i ; V /' 3 9 10 1 11 l;i E 1 1 5 7 5 1 1 ~ 5 Y : 1 ^ 19 V 2 T 2 1 r 2 2 23 - ~ = 1 21 '° s i 2 = z: E 5 ^ 6 EE PULSE jH M :; 2 2 B 2 3 23 2|§ 3 S ^ 2 3 S S s sjs " - ■= " » s 3|-:s - ^ 2» 5 § s s; : = -:: 25 s s s,s 31 s 1 2|5S;» H 3s RESP. 1^ sv, J! '3 " .. S 3S sjs s s s s S s z s al.s J. -' c^ S s s^ ~ 2 sg 3 s s;;; £ S S! 3- % s^ S3 SS 3 sia|?3 i3 £ & SjSISiS H SjS| Scarlet fever. F. O., aged six years. Chart showing pronounced rise of temperature coincident with the onset of albuminuria. Albumin was first found on the twenty-third day. One of the most characteristic features of scarlatinal nephritis is the marked pallor of the countenance, with puffiness of the eyelids. In walk- ing through a scarlet-fever ward one may frequently pick out the nephritic patients by noting this appearance. GEdema is a particularly common symptom in scarlatinal nephritis. A peculiarity of this com- plication is the tendency to rapid anasarca. This appears to be much more common in the nephritis of scarlatina than in ordinary Bright's disease. In explanation of this it is stated that the oedema is due not alone to the condition of the kidneys, but also to changes in the lymphatics and bloodvessels of the skin. The anasarca is accompanied by a pale or alabaster-like appearance of the skin. The swelhng usually begins about the eyelids and the ankles, but later the legs, genitalia, and lower portion of the abdomen become affected. In severe cases the entire body may be attacked. A thin and poorly nourished child may become rapidly metamorphosed TIII<: C()M/'fJCATfON,S OF SCAUfJ'JT h'EVHIt 41 5 into a plump child within a few hours, as a result of the axlematous infiltration. Anasarca, according to Troijsscau, is met with in cases of medium severity, rather than those of the most serious forms of scarlatina. Its frc(|U(nicy varies !^vv;\\\y in difrcrent epidemics. Barthez and llilliet observed anasarca in one-fifth of their (;ases. Some writers have stated that nearly all of their cases were dropsical. Among the 150 cases of scarlet fever referred to above, we did not see a single instance of anasarca, although UMlema of the face was not an uncommon symptom. Anasarca may affect deej) seated structures or the serous cavities. The fluid may hll up the peritoneal cavity, giving rise to a pronounced ascites, or the pleural or pericardial sacs may be similarly infiltrated. The soft palate, uvula, epiglottis and arytenoepiglottidean ligaments are more rarely attacked, in the latter case giving rise to o'dema of the glottis. In such cases intubation or tracheotomy may have to be per- formed to prevent suffocation. (Edema of the lungs and brain are extremely apt to be present in cases that terminate unfavorably. Anasarca may be present in rare cases without all)umin being found in the urine. This does not indicate that nephritis is not present, for ursemic symptoms may burst forth suddenly and with great intensity. Henoch reports the case of a twelve-year old child admitted to the hospital with oedema of the face and scrotum following scarlet fever. The urine was scanty, but contained neither albumin nor nephritic elements. Two days later convulsions occurred and three days after- ward the child died. The Condition of the Urine. — In the so-called febrile albuminuria, the urine contains albumin for a day or two, after which it disappears, perhaps to reappear at the end of the third week. Microscopic exami- nation reveals the presence of cylindroids and occasionally a few hyaline or epithelial casts. Not infrequently red and white blood corpuscles are present. A cloudiness is often seen in the urine, which is due to the presence of mucus resulting from the presence of degenerated epithelium. With the advent of the true scarlatinal nephritis the urine, as a rule, begins to decrease in quantity, although exceptionally there may be for a short time an increased secretion. The urine becomes quite concentrated and contains an abundance of urates, which give a pronounced ring with the nitric acid test. Albumin is found at first in small quantity, but later in larger amount. In bad cases it may constitute half by bulk with the heat test or, indeed, there may be complete coagulation of the urine. At this time hemorrhage from the parenchyma of the kidney may take place, causing the urine to look brownish-red and smoky. Under the microscope will be seen red blood corpuscles, cylindroids, epithelial detritus, and hyaline, epithelial, fatty, and blood casts. When there is much blood present it will settle as a deep red collection at the bottom of the urine glass. The amount of albumin is corre- spondingly increased with an augmentation in the quantity of blood. 416 SCARLET FEVER Exceptionally albumin may be absent for a number of days, although casts are present; on the other hand, a considerable quantity of albumin may be present without urinary casts being found. The specific gravity varies greatly according to the amount of urine passed. It may be as low as 1004, or as high as 1040 or more; ordinarily it will be between 1020 and 1035. The amount of urine secreted pro- gressively diminishes in severe cases, and there may be complete sup- pression for a period of twenty-four hours or longer. Cases in which this occurs usually succumb. The reaction of the urine is almost invariably acid. The quantity of urea excreted varies with the amount of urine, but is usually under 2 per cent. When dropsy occurs the urine is extremely scanty, high colored, of high specific gravity, and contains an abundance of albumin and casts. It is not at all uncommon for the albumin to disappear every now and then from the urine, only to reappear in a few days. We have frequently noted this irregularity in scarlatinal albuminuria. In certain cases the albumin appears intermittently in the urine. At other times it is absent at certain periods of the day; this peculiarity has been observed in a considerable number of patients in certain epidemics. This occurs independently of those cases in which albumin is absent while the patient remains in a recumbent position, but reappears when a sitting or standing position is assumed. These observations make it a matter of importance to carefully examine the urine at frequent intervals. If an examination is made only from time to time, albumin which is intermittently absent or which disappears at a certain time of the day may be completely overlooked. It is a good plan to examine the urine every other day up to the fifteenth day of the disease and then to make daily analyses. The urine should be examined both for albumin and microscopically, and the amount passed and the specific gravity should be ascertained. With the use of very delicate tests small quantities of albumin will doiibtless be found which are not recognizable by the usual tests employed. For practical purposes, however, the nitric acid or heat test will suffice. In cases that tend toward recovery the urine increases in quantity, the blood and casts disappear, and the albumin gradually diminishes. In our experience the urine in scarlet fever has given a positive diazo reaction in about 25 per cent, of the cases examined. This reaction has little or no diagnostic value. Aubertain^ and Roger have each reported cases of scarlatinal albumin- uria in which albumin was absent in the mornings while the patient remained in bed, but would appear soon after the patient stood upon his feet. Ten minutes' standing posture in one case would produce an albuminuria lasting about two hours. Exercise in the horizontal position failed to excite the presence of albumin. In some of these cases of orthostatic albuminuria a gradual cure takes place; others eventuate in a permanent albuminuria. 1 L'Albuminurie orthostatique au cours de la nephrite scarlatinense. La presse m6d., 1901. TIIK COMPfJCA T/ONS OF SCA HI.KT Fh'VPJfi 41 7 In some cases of severe nephritis, particularly when the urine becomes greatly reduced in cjuantity, symptoms of uramia are prone to develof). These usually come on gradually after distinct evidences of kidney involvement, although tliis is not invariably the case. Indeerl, uncmia may, in rare cases, supervene without the previous existence of albumin- uria. Henoch reports such a case; on the twelfth day of scarlatina, in a four-year-old child, intense right-sided convulsions and stupor devel- oped; examination of the urine on the previous day had failed to show albumin. The patient was catheterized on the development of the symptoms, and a considerable quantity of albumin was then found. Ordinarily the first symptoms in a patient about to develop uraemia are vomiting and, at times, diarrhoea. This is doubtless an effort on the part of nature to eliminate some of the retained poisons through these channels. Leichtenstern claims that one of the most frequent modes of onset of scarlatinal uraemia is the development of pronounced dyspnoea associated with rapid heart action. There is usually some elevation of temperature, which, in bad cases, may become excessive and reach 106° or 107° F. But the symptoms referable to the nervous system dominate the clinical picture. There are frecjuently intense headache, tinnitus aurium, and somnolence or stupor, with occasionally sudden loss of vision. These symptoms are rapidly followed by con- vulsions. The convulsive movements may be partial, that is, limited to one set of muscles, as those about the jaws, in which event there may be a tonic contraction; in other instances they are unilateral or general, affecting the entire body. When the convulsions are limited to certain sets of muscles consciousness is usually preserved, but when there is a general epileptiform seizure it is followed by coma, at least for a time. The convulsive attacks may be of brief duration, lasting but a few minutes, or they may persist for an hour or more. There may be a single seizure, although more commonly there is a succession of convulsions upon the same or successive days. When the convulsions are severe and protracted, death may result from exhaustion, cerebral hemorrhage, or oedema of the lungs. In other cases a fatal termination comes on later, the patient lapsing into a progressively deepening coma. In some cases a gradual oncoming stupor may be the only pronounced symptom of urremia. In favorable cases the convulsions cease, the stupor disappears, the urine increases in quantity, and the patient emerges from the crisis. The amaurosis which develops from time to time in uraemia usually disappears when the convulsions cease, but the blindness may continue for several weeks, ultimately ending in complete recovery. In some cases aphasia and hemiplegia may develop during uraemic conMalsions and disappear when convalescence is established. In rare instances patients may become maniacal after ursemic attacks. Wagner^ saw a patient who had eleven convulsive seizures, each one being followed by the wildest mania; although the temperature registered 107.6° F., the patient recovered. 1 Quoted bv von Jiirgensen, loc. cit. 27 418 SCARLET FEVER Melancholia may also develop as a sequel of uraemia. If the urine now increases in quantity, there is but little likelihood of a recurrence of the severe nervous manifestations. The abnormal urinary constituents gradually disappear from the urine and the patient is entirely restored to health. Prognosis. — The prognosis of scarlatinal nephritis is much more favorable, both as to life and to functional restoration of the kidneys, than would be expected from the nature of the symptoms. The vast majority of patients recover from the nephritic attack, even where alarming urtemic phenomena have been present. Intense and un- remitting headache, protracted convulsions, repeated vomiting, and coma are symptoms of bad omen. The quantity of albumin in the urine is no reliable guide, as a severe nephritis may exist with but little albumin in the urine, and the converse may also be true. The number and character of the casts and particularly the quantity of the urine are more important criteria. Suppression of urine renders the situation extremely grave, although recovery may take place if diuresis can again be established. The opinion has prevailed for a long time that scarlatinal nephritis was but seldom followed by chronic Bright's disease. While it is fortunately true that restitutio ad integrum usually takes place, it is nevertheless certain that the number of cases of permanent nephritis following scarlatina has been much underestimated. We had at the Municipal Hospital, during the winter of 1902, a girl, aged eight years, who was brought in with a well-marked case of scar- latina from a hospital where she was being treated for a nephritis said to date from an attack of scarlet fever five years previously. She had bloody urine for some days, but made a good recovery from the scarlatina and left the hospital many weeks later still suffering from a chronic nephritis. Aufrecht^ reports a case of nephritis after scarlet fever lasting twenty years, and terminating in a contracted kidney. Leyden, Litten, Forch- heimer, and others have reported cases eventuating in chronic Bright's disease. Holt says that he formerly believed such results rare, but larger experience has convinced him that this sequel is not uncommon. Of 77 cases of scarlatinal nephritis occurring in the Southwestern Hospital of London, in 1892, 6 cases, according to Caiger, were dis- charged with chronic albuminuria after a prolonged residence. If delicate tests for albumin were employed and careful microscopic examination of the urinary sediment were uniformly made for months after attacks of scarlatina, it would doubtless be found that a larger proportion of cases eventuate in chronic nephritis than has been supposed. Many of these patients have structurally damaged kidneys, which at some future period, as a result of a variety of causes, may be reawakened into activity. The practical lesson to be borne in mind is that the urine of patients convalescent from scarlatinal nephritis should be 1 Deutsche ArchiT f. klin. Med., Leipzig, 1887, Bd. xlii. p. 517. 77//'; aOMr/JCAT/ONS OF SdAlilJ'lT FKVMIl 419 carefully exarniiHul froin lime to time, and tlie did. and uuAc fjf life rcn;ulat('(l accord inoly. Scarlatinal Rheumatism (Synovitis Scarlatinosa^. — In tlic absence of conclusive evidence that acute articular rheumatism is a specific tnorhid process due always to the same infectious a{2;ency, we are justified iu adlieriuf^ to the old term "scarlatinal rlieumatism." 'J'he attemy)t tf) distiiifijuish lu'tween a scarlatinal synovitis and a coini)licatin[( rh(;niiia- tism is scarcely warranted by our present knowledge of the subject. Synovitis and arthritis occurring in the course of scarlet fever are frequently associated with other phenomena, such as endocarditis, pericarditis, pleurisy, etc., which are common rheumatic coniphca- tions. The frequency of joint involvement in scarlatina appears to vary in different countries and in different epidemics. Trousseau says: "By minute interrogation, and by carefully examining and applying a certain degree of pressure to the joints, articular pains are found to be present in about one-third of the cases (of scarlatina). It is important to know this; for acute affections of the joints, general arthritis, pericarditis, and endocarditis frequently occur during the course of the disease." Ashby observed synovitis to occur 20 times among 900 cases of scarlet fever. Koren,^ of Christiana, noted scarlatinal synovitis of a mild type 27 times in 426 cases (6.3 per cent.) of scarlet fever in the epidemic of 1875-77. Vogl appears to have observed an unusually large number of cases of joint complications in scarlatina. He is authority for the statement that articular involvement occurred in 13.6 per cent, of the cases in the epidemic of 1884-85, and in 10.6 per cent, in 1894-95. Hodger^ saw 217 instances of scarlatinal synovitis among 3000 cases of scarlet fever, or 3.2 per cent. It is seen from the above figures that the frequency of this com- pHcation varies from about 3 to 13 in 100 cases. Our personal experience would lead us to regard the first figure (3 per cent.) as representing more nearly the average incidence of this complica- tion. Two forms of joint involvement are recognized — a simple serous synovitis and a purulent or suppurative arthritis. The mild form is fortunately far more common than the suppurative variety. Articular involvement may occur at any period of the disease, but is most common during the stage of desquamation in the second or third week of the disease. The wrists and fingers are the joints most often attacked, although the ankles and toes not infrequently participate in the process. Sometimes the larger joints, such as the shoulders and knees, become involved. The usual symptoms are pain, stift'ness, and swelling. Redness may or may not be present. Trousseau states that scarlatinal rheumatism is usually mild and of short duration, is commonly localized, and when it disappears does not tend to return. We have seen cases 1 See Johannsen, loc. cit., p. 195. - See Eichhorst's Spec. Pathol, und Therapie, Leipzig, 1897, p. 241 . 420 SCARLET FEVER in which there were periods of disappearance and of recurrent involve- ment. Scarlatinal rheumatism is frequently, although not always, attended with a rise of temperature which commonly reaches 101° or 102° F. In mild cases the articular inflammation subsides in the course of three to five days. In more severe cases it may last for weeks. Suppurative Arthritis. — Suppurative arthritis is a rare complication of scarlet fever, and usually occurs late in the course of the disease. The joint becomes painful, swollen, hot, and reddened; the fever is high, the patient prostrated, and all of the usual symptoms of pyaemia are present. One or several articulations may be involved. In the vast majority of cases a fatal termination supervenes. In rare instances, through surgical intervention, or even at times without, recovery takes place after a long and tedious illness, but with serious impairment of the functional activity of the joints involved. We have seen scarlatinal rheumatism associated in one case with a severe endocarditis and a recurring geographic erythema of the trunk and extremities, and in another fatal case with endocarditis, pleurisy, and hemorrhagic purpura. In persons of scrofulous habit a scarlatinal synovitis may, after a long course, eventuate in tuberculosis of the joint (white swelling). In rare cases of scarlet fever the sheaths of tendons may undergo inflammation (tenosynovitis), which commonly terminates in suppu- ration. In other cases periarticular abscesses may occur and rupture into one of the large joints. Cases of periostitis and ostitis have been reported, involving particu- larly the petrous portion of the temporal bone, the nasal bones, and the cervical vertebrae. Briick^ describes a form of scarlatinal myositis, which attacks most commonly the lumbar, pectoral, abdominal, and intercostal muscles, and which is characterized by pain and soreness and moderate rise of temperature. Purpura Hemorrhagica. — It is important to distinguish between true hemorrhagic scarlatina and secondary purpura developing during the course of the disease. The former condition appears, as a rule, at the outset, and is characterized by constitutional symptoms of great intensity and malignancy, associated with hemorrhages into the skin and from the mucous membranes. Purpura hemorrhagica comes on usually after the subsidence of the acute scarlatinal symptoms and not infrequently during convalescence. Most cases develop during the second or third week, and most commonly from the fourteenth to the twentieth day. The patient loses appetite, is apathetic, and may have some rise of temperature. Nose-bleed is often one of the first symptoms; soon pinhead-sized purpuric spots appear upon the skin of the trunk, extremities, or face; the gums become swollen and bleed; the urine contains blood, and hemorrhage may take 1 Petersb. med. Presse, 1896, No. 18. 77//'; aOMPfJCATfO.VS OF SCAIILFT FHVI'Ht 421 place from \\\v. stomach and l)()wcls. A inarkcd pallor srjon fjevelops, the patient l)(!Conies ])ro.strate(l, and, in seven; eases, d(;atii takes place from loss (^f hlood, Jieniorrhafre into the brain, or (;xhaustion. AlhiHTiiiniria is usually j)resent, even when the urine is free of Vjlood. In mild cases the hemorrhages from the various mucous membranes cease after a short time, and the patient, although intensely ansemic, recovers. These secondiiry purpuras are not seen alone in scarlatina, but in other infectious diseases, such as influenza, rheumatism, smallpox, etc. They are probably due to some secondary infection which rlestroys either the integrity of the blood or the vessel walls. We have seen two cases of heinorrliagic purpura comj)licating scarlatina. A three-year-old child, suifering from a well-marked scarlatina, developed late in the course of the disease swelling of the joints, diffuse Fir,. 74 Purpura hemorrhagica associated with pleurisy, endocarditis and joint trouble, complicating scarlet fever. Fatal termination. ecchymotic patches upon the face, trunk, and extremities, and endo- carditis. The patient after some days' illness died. Autopsy showed vegetations upon the mitral and aortic valves, a right-sided pleurisy, and hemorrhages into the mediastinal and peritoneal cavities. The second case was a girl, aged eight years, who, upon the seven- teenth day of a scarlatina of average severity, became apathetic, had slight rise of temperature, and nose-bleed. The following day, small, pinpoint petechia appeared upon different parts of the body, bleeding occurred from the gums, and an abundance of blood was found in the 422 SCARLET FEVER urine. The bleeding continued for a few days, but ceased under treat- ment and the patient made a good recovery. A pronounced ansemia persisted for a few weeks. Albuminuria was present even after the cessation of hsematuria. Although this complication is uncommon, a number of cases have been published. Biss^ reports the case of a boy, aged three and one- half years, who suffered from a severe attack of scarlet fever compli- cated by double otitis media. On the nineteenth day after admission to the hospital he developed an extensive eruption of pinpoint hemor- rhages over the trunk and limbs, vomited a half-pint of blood, passed a similar quantity by the bowel, and rapidly succumbed. Autopsy showed the kidneys to be " transformed almost entirely into fat." Murray^ saw a two-year-old colored child develop scarlatina after an operation for hernia. On the ninth day of the attack there occurred bleeding from the kidneys, bowels, stomach, nose, and gums, and hemorrhages into the skin and conjunctivae. The red corpuscles numbered 2,000,000 per cubic centimetre. Urine contained blood and epithelial and hyaline casts. Death took place on the fourteenth day. De Boinville^ places on record the case of a boy, aged four and one- half years, who, on the sixteenth day of scarlet fever, had hemorrhages from the nose and hemorrhagic spots on the scalp and about the knees. Although the amount of blood lost was small, the epistaxis could not be checked and the patient died five days later. Phillips* reports the case of a girl, aged fourteen years, suffering from scarlet fever, who had a recurrent rash on the fourteenth day, and swelling of the joints on the twentieth day; six days later petechial patches on the chest and legs and free bleeding from the nose, gums, and kidneys. Patient had albuminuria and acute dilatation of heart, but recovered. Gangrene. — Mention has already been made of the sloughing of the tissues of the neck, which occasionally accompanies cellulitis and abscesses. The muscles and large bloodvessels of the neck may be exposed by gangrene of the overlying skin. Gangrenous stomatitis, or noma, is also seen at times after scarlatina, although it is much rarer than after measles. Apart from these con- ditions, a form of spontaneous gangrene is, in rare instances, observed during the course of scarlatina. When seen, gangrene usually develops during the second or third week of the disease, and usually attacks the extremities. In most of the reported cases the condition has been attributed to embolism. There appear first bluish discoloration, pain, and coldness, and then hemorrhagic extravasation into the skin. In some of the reported cases the gangrene was so deep and extensive as to necessitate amputation of the affected member. 1 Lancet, August 2, 1902, p. 286. - Case of Scarlet Fever with Purpura, Lancet, February 11, 1893, vol. 1. 3 A Peculiar Case of Scarlatina Hemorrhagica, Lancet, August 9, 1903. This case is evidently a purpura hemorrhagica, and not one of true hemorrhagic scarlatina. * Scarlet Fever with Relapse ; Acute Rheumatism and Purpura Hemorrhagica ; Recovery. London Lancet, 1893, vol. ii. TIII<: COMPLKIATinXS OP' SCARL/'JT FKVI'Hi 423 . Cases of gangrene have been reported by Blanpain/ Hudson,* Kiister,' and Chapin/ Wood and Arrigoni'"' ?iave reported oases of gangrene affecting the genitaha, and Wilson" a case of gangrene of the face occurring three weeks after convalescence from scarlatina. Pearson and Littlewood^ rey)ort the case of a boy, aged ff)ur years, who, after an ordinary scarlet fever, on the eighth day developed small, hemorrhagic discolorations of the skin of both legs. In a few days the legs became livid, first upon the feet, thence spreading upward. The femoral pidsation was lost, the legs became cold, intermittent pain occurred, and lines of demarcation formed about three inches above the knees. At the same time slight dilatation of the heart was discovered. On the twenty-third day of the disease the right leg was amputated, and, a week after, the left. The patient recovered. Embolic and thrombotic clots were found in the bloodvessels of the amputated limbs. Buchan* reports the case of a boy, aged thirteen years, whose scarlatinal rash on the second day exhibited a bluish appearance on the legs. A few days later the veins, especially at the apex of Scarpa's triangle, stood out quite prominently. Hemorrhages occurred into the skin of the legs, particularly the right; there were also hsematuria, nose-bleed, and ha?moptysis. The lower part of the right leg became mummified and a definite line of demarcation formed just above the knee, where an amputation was performed. The patient made a rapid recovery. We recall a child treated in the Municipal Hospital in 1900, who developed gangrene about the third week of a severe scarlatina. Ecchy- motic patches developed upon the leg, followed by rather superficial sphacelation of the tissues. A few days later one hand became blue and cold, and shortly after this the other hand became similarly affected. The radial pulse was lost and both hands assumed an indigo-blue color. Before actual gangrene could take place the child, who was greatly prostrated, died. The gangrene in this case was doubtless due to embolism (Fig. 75 j. Skin Complications. — Reference has already been made to the various abnormalities of the rash of scarlet fever, including an excessive development of miliary vesicles. It remains to discuss the occasional complicating skin disorders which are quite apart from' the scarlatinal process. 1 Scarlatine ; gangrene spontaneti des membres ; embolies ; autopsie. Aroh. Med. Beiges, Brux., 1869, 2, ix. pp. 324-334. - Scarlatina Resulting in Mortification of the Right Limb, and Sacceesful Amputation. Transac- tions of the Ohio Medical Society, 1858. ^ Spontan. Gangran des Unter-schenkels nach scarlatina: Ampntatio Femoris : Tod., KasECl, 1876 and 1878. * An Unusual Result of Scarlet Fever; Embolus; Gangrene : Amputation. Medical Age, Detroit, 1884, xi. p. 205. * Quoted by Thomas. ^ Reviewed in Archiv f. Kinderheilk., 1?98, p. 418. 7 Dry Gangrene of Both Legs ; Double Amputation, 1897, 11, p. 84. 8 Lancet, October 5, 1901, p. 915. 424 SCARLET FEVER Febrile herpes occurs every now and then during the invasive stage of the disease. The patches develop usually about the mouth, although they may be situated about the cheeks or ears. While herpes is not very frequent in scarlet fever it is more commonly seen than in smallpox or measles. Urticaria is not an infrequent accompaniment of scarlet fever, although it cannot be considered as bearing any special relation to the disease. It may be seen early or late in the course of the illness, and is usually neither extensive nor protracted. This complication is doubtless due to the presence in the blood of some accidental toxin or drug. Blehs may occasionally develop upon the skin as a result of a coa- lescence of neighboring miliary vesicles in intense rashes. Thomas says that they may reach the size of hazel-nuts. Bullae may also occur upon patches which are destined to terminate in gangrene of the skin. Some Pig. 75 Gangrene of the skin complicating scarlet fever. Patient developed gangrene of both hands and died. authors speak of the occurrence of pemphigus, particularly in certain epidemics. These are, in all probability, not true instances of pemphigus, but of bullous dermatitis of septic origin. We have occasionally seen cases of localized necrosis of the skin in small areas, a condition analogous to the so-called varicella gangrsenosa, but better designated dermatitis gangranosa. Fig 76 shows this condi- tion upon the knees of a young boy. Eczema may occur as a complication of scarlatina, but is more apt to develop as a sequel. Intense desquamation may leave the skin dry, harsh, and fissured, and the seat of eczematoid patches; these may persist for some time after convalescence. In other cases a purulent discharge from the ears or nose may give rise to an impetiginous eczema in the region of these orifices ; the skin becomes moist and covered with crusts as the result of the irritating and infective discharges. 77//'; aOMI'LICATIONS OF SCA.'i'fJ'JT FFVI-'Ji 425 Cutaneous ahscas.sr.s- may occur iijxjii any portion of ttx; integument. This compliciition is iincoinmoii, usually occurrinj^ in scplic cases. We recall an adult })alicnt in whom a, larletely d(;generated. Respiratory Organs. — The larynx may become involved as a result of a secondary diphtheria or a membranous inflammation of strepto- coccic origin, although the latter is much rarer than in measles. CP^Jema of the glottis results at times from extension of inflammation, and on other occasions from nephritis. Perichondritis of the larynx is a rare and fatal complication. Accord- ing to Kraus^ it occurs about once in 200 to 250 cases of scarlatina. Rauchfuss saw 4 cases among 903 cases of scarlatina, and Leichtenstern 2 cases among 467 patients. Its development may necessitate the performance of intubation or tracheotomy. Pulmonary complications are much less common in scarlatina than in measles. The bronchial tubes and lungs, are nevertheless, according to Henoch, much more frequently involved in bad cases than is generally believed. These lesions are masked by the severe constitutional symp- toms, and are often not discovered until autopsy. In a series of 98 fatal cases of scarlatina, reported by McCollom,^ 15 were due to broncho- pneumonia. As would naturally be expected, pulmonary complications are com- moner in infants than in older children and adults. Roger^ gives the following morbidity and mortality statistics of pulmonary complications in scarlatina according to age: Scarlatina. No. of patients. Cases of pneumonia. Mortality. First infancy ... 56 6 (10.7 per ct.) 5 (8.9 per ct). Childhood ... 430 6 (1.3 per ct.) 2 (0.4 per ct.). Adults .... 1727 4 (0.2 per ct.) 3 (0.1 per ct.). All of the pneumonias in the infants were bronchopneumonias. Four of the children of the second group had bronchopneumon'a, and two had apical pneumonia. Bronchopneumonia occurred in two adults. Bronchopneumonia in severe cases appears usually during the first or second week. Henoch remarks: "We found bronchitis and broncho- pneumonia in nearly all the severe cases and also repeatedlv during life." Lobar Pneumonia. — Lobar pneumonia may develop dur ng the height of the disease, or more commonly after nephritis has manifested itself. The upper lobes are more often affected than other parts of the lungs. (Edema of the Lungs. — CEdema of the lungs is by no means a rare complication when the kidneys are severely affected and a general dropsy exists. Serous transudation into the lungs may occur rapidly and lead to sudden death. Involvement of the pleural cavities in scarlatina is uncommon. 1 Prag. med. Wochenschr., 1899, pp. 29 and 30. - Quoted by Corlett, loc. cit. s Loc. cit, p. 9?3. 428 SCARLET FEVER Pleurisy may develop in association with a lobar pneumonia or it may occur independently thereof. The process may be dry or accompanied by serous or purulent exudate; scarlatinal pleurisies show a pronounced tendency to eventuate in empyema, a complication which adds much gravity to the disease. However, desperate cases may at times terminate favorably, as is evidenced in a remarkable case of Trousseau, who drew off from the chest of a fourteen-year old girl 750 grams of pus, the patient making a complete recovery. Thomas says all forms of scarlatinal pleurisy are characterized by rapid development and by but slight local disturbance, even when the affection is very intense. The effusion is usually present only upon one side. Pleural involvement is more frequent in cases complicated by nephritis. It is especially apt to accompany scarlatinal rheumatism. We have already referred to a patient treated in the Municipal Hospital, who had purpura, endocarditis, synovitis, and a fibrinous pleurisy. Farb ringer regards exudative pleurisy as a frequent complication, occurring, in his experience, in 5 per cent, of cases of scarlatina. Johan- nesen, of Norway, found, among 688 deaths from scarlet fever, but 3 that resulted from pleurisy. Nervous System. — While the onset of scarlatina is attended in severe cases by pronounced nervous symptoms, these subside if the course is favorable, and do not add to the gravity of the disease. The early cerebral manifestations are in part due to the scarlatinal poison and in part to the high fever. Headache and dehrium may be present in ordinary cases, but convulsions and coma presage an attack of great severity. Later in the disease severe nervous symptoms, such as delirium, convulsions, coma, sudden blindness, etc., may develop as a result of uraemia. Hemiplegia. — Hemiplegia may occur early from a cerebral hemor- rhage during the invasive convulsions, or it may come on at a later date as the result of embolism. Taylor^ reports a right hemiplegia resulting from embolism of the middle cerebral artery; the patient succumbed later to diphtheria. Addy^ saw a case of partial hemiplegia with amnesia after scarlatina. Meningitis. — Meningitis usually results from extension of inflam- mation and infection from the middle ear or the nasal sinuses. We have already referred to a case of purulent meningitis of the base of the cerebellum which we observed after a purulent otitis media. Roger^ saw a twenty-three-year-old man in whom a severe purulent rhinitis complicating scarlatina was followed by meningitis. At autopsy the left frontal lobe of the brain was covered with purulent plaques and the left sphenoidal sinus contained pus. The presence of the strepto- coccus in pure culture was demonstrated. Similar cases have been 1 Medical Times and Gazette, London, 18S0, ii. p. 686. 2 Glasgow Medical Journal, 1880-85, S. xiii. pp. 463-465. 3 Loc.cit., p. 850. 77//'; COMI'fJdATIONH OF SCARI.F/I' FFVKR 429 reported by other observers. Jiaudelocque' reports a case of meningo- encepliiilitis characterized by headache, vomiting, and convulsions, followed by coina and the loss of speech, hearing, and sight. Althous^ reports a case of spinal meningitis with consecutive lateral and pos- terior sclerosis. Incomplete Paraplegia. — Cases of incomplete paraplegia have been described by Dcinange,'' Roger, and others. Roger says that among 22b'3 patients with scarlatina 4 cases of incomplete paraplegia were observed. Three women liad for al)Out a week great difficulty in standing up or walking. The fourth patient was a man who on the second day of the disease had paralysis of the soft palate. Later the two legs and the right arm became affected ; the palsy passerl off in ten days. Cultures from the throat excluded the possibiHty of diphtherial infection. As has already been stated, facial palsy occurs occasionally from involvement of the facial nerve in the bony roof of the ihiddle ear. Insanity. — Insanity has been reported as a complication and sequel of scarlatina. The mental aberration is usually temporary, but may in some cases persist after convalescence. Mitchell,* Rabuske, and Wagner have each reported attacks of acute mania in scarlet fever, the mania in the last-named case following ursemic convuls ons. Carrieu'' records a case of dementia and Brill a case of scarlatinal insanity with epilepsy. Wildermuth," in a report of 1S7 cases of epilepsy, states that 12 cases followed attacks of scarlet fever. Multiple Neuritis. — Egis^ reports a case of multiple neuritis following scarlatina in which there was an ataxic gait and paralysis of both peroneal nerves. But two other cases of multiple neuritis could be found in literature. Tetany. — Steffen^ reports a case of tetany in a young girl suffering from scarlatina; an attack was noticed after each bath. Kiihn-Ulsar^ mentions a case of tetany in a boy, aged four and one-half years, suffering from scarlet fever. For six weeks muscular spasms and stiffness were noted, at times limited in extent and at other times general. Trismus was present for fourteen days. The patient gradually recovered. Bones. — Necrosis of the petrous portion of the temporal bone and of the ear ossicles occurs in severe cases of purulent otitis media. Necrosis of* other bones sometimes takes place. Brown^° reports a case of necrosis of the lower maxilla after scarlet fever, and Weickert^^ reports a case in which both jaws were thus affected. Neumark^^ reports 30 cases of acute infectious osteomyelitis, of which 5 follow^ed scarlet fever. 1 Gaz. des. hop. de Paris, 1887, xi. pp. 197-199. = Brit. Med. Journal, 1S81, i. p. 50. 3 Bull. Soc. anat. de Paris, 1874, pp. 503-9. < Edinburgh IMedical Journal, 1881-82, xxvii. pp. 721-24. 6 New England Medical Monthly, 1882-83, ii. pp. 55-58. « Quoted by Holt, loc. cit. ' Archiv f. Kinderheilk., 1900, sxviii. s Jacobi's Festschrift, 1900, p. 83. 9 Berliner klin. Wocheuschrift, 1899, No. 39, p. 855. 10 London Lancet, 1844, i. p. 220. 1' Deutsche Klinik, Berlin, 1854, vi.j). 22. i= Archiv f. Kinderheilk.. Bd. xxii. 430 SCARLET FEVER Sequelae. — But few words will be devoted to the sequelae of scarlatina, as they represent merely a continuation of the complications or dis- abilities resulting from structural damage. A weakened and anaemic state of the system may develop after scarlatina as after many other infectious diseases; the patient is thus lowered in resisting power and rendered more susceptible to the other infectious diseases. There is, however, no such increased susceptibility to tuberculosis as exists in patients recovering from measles. The various organs of sense may bear for a long time and in some cases forever the marks of a cruel scarlatinal attack. The mucous membrane of the eyes, throat, and nose may show persistent pathological alteration. It is the ears, however, that most frequently exhibit permanent damage. It is largely because of injury to the sense of hearing that scarlatina is so feared by the laity. A chronic purulent otitis media -may persist after scarlatina and lead at a remote date to mastoid or intracranial disease. Destructive changes involving the middle ear and the contained ossicles may cause auditory disability, varying in degree from slight impairment of hearing to complete deafness. When this occurs very early in life the loss of this sense may lead to deaf- mutism. As has already been suggested, the damage to the kidneys is often more than a transitory one. In a certain proportion of cases albuminuria will persist and eventuate in a chronic Bright's disease. In other cases the kidneys are functionally normal, but are rendered more susceptible to subsequent burdens or infections. Various cutaneous diseases, such as furuncles, eczema, etc., may follow in the wake of scarlatina. Reference has already been m4de to certain psychic disturbances, such as mania and melancholia, which may persist after scarlatina. Chorea. — Chorea may develop a few months after convalescence is established. This sequel is not of great frequency. Carlslaw reports only 3 cases of chorea following 533 cases of scarlet fever, and Priestley^ 13 cases after 5355 attacks of scarlet fever. THE BACTERIOLOGY OF SCARLET FEVER. Within the past quarter of a century numerous investigations have been undertaken to discover the specific cause of scarlet fever. That the disease is produced by a contagium vivum and that every case of scarlet fever receives its infection from a previous one are propositions which command general acquiescence. The exciting cause of the disease is certainly micro-organismal, but the identification of the causal parasite is still shrouded in mystery. As early as 1762, Plenciz,^ of Vienna, attributed the cause of scar- latina to living corpuscles. Hallier^ in 1869 was one of the first observers 1 British Medical Journal, September, 1897, p. 805. 2 Quoted by Berg6, loo. cit. s Jahrbuch f. Kinderh., N. F., ii., 1868, 1869. TIII<: liACTKh'IOr/XlY OF SCARIJ'/r F/'JV/'Jk 431 to search for the microscopic cause of the disease. With the crude magnifying lenses at liis disposal he found a micrococcus in and about the blood corj)usclcs wliicfi lie ref^arded as the morbific agent of the disease. One year later lloilinan examined the sweat of scarlatina patients and discovered the presence of a micrococcus. In 1872 Coze and Felt// found in the blood of scarlet-fever patients bacteria G microns long, which caused the death of nibbits when inocu- lated. Riess^ in 1S72 found certain alleged lower forms of life in the blood, but failed to prove anything by cultures or inoculations. In 1875 Klebs found, in the substance of an inguinal glanrl of a patient suffering from scarlet fever, a sphere made up of micrococci which later changed their form. To this organism he gave the name "monas scarlatinosum." Tschamer^ in 1879 claimed that scarlatina was caused by a crypto- gamic organism, designated by him the "verticillium candelabrum," which is foimd upon rotten wood. He regarded this as one stage of development of the micrococci found by him in the blood cells, scales, and urine. In 1882 Eklund* found bodies in the urine of scarlet-fever patients which he called "plax scindens." He found similar organisms in the soil, in water, and on mouldy walls. Children living in the vicinity of such excavated soil were observed to contract scarlatina. Octerlony observed these same bodies in the blood and urine of scarlatina patients. In 1883 Pohl-Pincus^ found cocci in the epidermic scales and also on the soft palate. Klamann*^ made similar observations in the same year. In 1885 Fraenkel and Freudenberg^ isolated a streptococcus from the liver, kidney, and spleen in three fatal cases of scarlet fever. Babes found in 18 out of 20 fatal cases of scarlet fever a strepto- coccus which he regarded as a variety of the streptococcus pyogenes." Loeffler in 1884 isolated the streptococcus from false membrane in the throats of scarlatinal patients. In 1885 Power^ noted a severe epidemic of scarlet fever in London which began among the patrons of the Hendon farm who were receiving milk from cows which were suffering from a peculiar disease. Klein^° investigated the circumstances of the epidemic. He found that the disease in the cows was transmitted from one to another, and that 1 Recherches cliniques et exporimentelles sur les mal. infect., Paris, 1S72. - Quoted by Bourges, Les recherches microbiennes dans la scarlatine, Gaz. hebdom. de med. et de chir., March 28, 1891. a Centralz. f. Kiuderh., 1878, 1879, ii. * Quoted by Bourges. ' Centrablatt f. die med. Wissen., 1883, xxi. « Allgemeine med. Centralz.. 1SS3, lii. 7 Quoted by Berg6, Pathog(§nie de la scarlatine, Paris, 1895. s Quoted by Berg6. 9 Milk Scarlatina, Loudon, Report of the Medical Officer of Local Government Board, Febmarv. 1885, 1886. 10 The Etiology of Scarlatina, Proceedings of the Royal Society of London, 1887, xlii. 432 SCARLET FEVER it began with fever, followed in two or three days by swelling of the eyes. From the fourth to the sixth day there appeared an erup- tion, oculonasal catarrh, cough, and rapid breathing. Desquamation occurred about the third or fourth week, with loss of hair. In severe cases sore throat and enlargement of the submaxillary glands were present. On the fifth or sixth days several vesicles appeared upon the udders, which dried into crusts and fell off about the fifth or sixth week. Diplococci sometimes arranged as streptococci were found in these lesions. Klein, in studying the blood of scarlatina patients, found from the fourth to the sixth day of the disease, in 4 out of 11 cases, a streptococcus of the same character as that obtained from the Hendon cows. He regarded this as the cause of the disease, and looked upon the disorder in the cows as bovine scarlatina. Klein's conclusions were attacked by Duclaux, by C. B. Brown, and also by Crookshank. Crookshank^ saw an analogous epidemic among cows in Wiltshire from which no scarlet fever was spread. The disease was recognized by him as cowpox. Both Crookshank and Thin con- tended that the streptococcus found by Klein was the ordinary strepto- coccus of suppuration. In 1887, Edington,^ working with Jamieson, isolated from the scales and blood of scarlet-fever patients a bacillus which he regarded as the cause of the disease. The organism was quite uniformly found in the blood after the third day and in the scales after three weeks. This so-called bacillus scarlatinse was motile, grew in long threads, and fluidified gelatin. Inoculations of rabbits and guinea-pigs produced fever and an erythema followed by desquamation. Brown later demonstrated this bacillus in the scales of ordinary dermatitis. A committee of the Medico-Chirurgical Society of Edin- burgh investigated the claims of Jamieson and Edington, and was able to find the bacillus in but 3 of 10 cases of scarlet fever; of nine blood cultures results were obtained in four; cultures from scales were negative and inoculation experiments were without result. In 1889 Madame Raskin' read before the St. Petersburg Congress a communication in which she described a peculiar micrococcus which was found in the blood cells at the beginning of scarlet fever. It was likewise discoverable in the internal organs, skin, and mouth at autopsy. It killed rabbits and guinea-pigs, but did not induce symptoms of scarlet fever. In 1893, Fiessinger^ announced his belief that the streptococcus was the cause of scarlet fever. Dowson^ in the same year expressed the opinion that scarlet fever was due to the streptococcus and that the tonsil was the seat of the primary infection. This assumption was later championed by Berge and by Eemoine. 1 Communication to thie Pathological Society of London, 1887. 2 Jamieson and Edington, British Medical Journal, 1887, i. 3 Centralblatt f. Bakt. u. Parasit., 1889, v. •• Semaine m^d., July, 1893. 6 Med. Chron., Manchester, 1893, 1894, xix. p. 217. 77//'; HAdTFjaoinaY of hcaulht f/':vi':r 433 Bergd/ in a l)rocliurc pul)li.she(l in 1S95, disfMisses at length the njitiire of scarlet fever and fonnnlates the following conclu.sions: 1. Ordinary scarlatina is a local infection of the tonsils. The scarla- tinal enij)tion (exiuithern and enjinthem) is the resnlt of a toxic erytheni- agenic action of tlie inicrohic poisons secreted in the infeftterl tonsils. 2. An imposing array of evidence points to the strc})tococcns in one of its virulent forms as the pathogenic agent of the disease. Lemoine^ in ISOf) likewise affirmed his belief that the streptococcus bore an etiological relationship to scarlet fever, and that the point r)f entrance of the germs was the throat. Class'* in 1S07 described a diplococcus, sometimes appearing in short chains, which he found constantly in the pharynx in scarlatina. It was also found in the blood, but rarely after the first day of the disease. Intravenous injections of this organism in white swine were said to produce an aflFection closely simulating scarlet fever. Schamberg and Gildersleeve,^ in a bacteriological examination of the throats of 100 cases of scarlet fever, found the diplococcus described by Class in but 15 cases. They found that, while this organism appeared as a large diplococcus when first isolated and cultivated on certain media, it later decreased in size to about 0.6/^, and appeared as a micrococcus, occurring singly and in pairs, with an occasional short chain. The organism reacted upon the various media in a manner similar to the ordinary staphylococci. In 1900 Baginsky and Sommerfeld^ described a streptococcus almost constantly found in the throat and blood of scarlet- fever patients. This organism sometimes appeared in short chains and in pairs. These investigators tentatively regard the streptococcus as the cause of the disease. Protozoa in Scarlet Fever. — In 1887 L. PfeifFer'' described protozoa- like bodies in the blood of scarlet fever and vaccinia. The significance of these was not explained. Mallory^ recently described certain bodies in the skin in four cases of scarlet fever which he regarded as stages in the developmental cycle of a protozoon. They form a series which are closely analogous to the series seen in the asexual development (schizogony) of the malarial parasite, but in addition there are certain coarsely reticulated forms which may represent stages in sporogony or be due to degeneration of the other forms. These bodies found in the skin fixed in Zenker's fluid and stained with eosin and methylene blue can be divided into two groups. The first group consists of round, oval, elongated, and lobulated bodies 1 La paUiog&nie de la scarlatine, Paris, 1895, p. 126. 2 Bull, et m^m. Soc. mM. des hop. de Paris, 1S95 and 1S96 '* New York JVIedical Record, September, 1899, p., 330; Journal of the American Medic&l Associa- tion, 1900, vol. xxxiv.. No. SI ; ibid., 1900, No. 13, p. 799. ■• Transactions of the Philadelphia Pathological Society ; also Medicine, September, 1904. 5 Berliner klin. Woehenschrift, 1900, Nos. 27 and 2S, p. 688. Zeitschrift f. Hygiene, Bd. ii., 1SS7. 7 Protozoon-like Bodies Found in Four Cases of Scarlet Fever, Journal of Medical Research, Janu- ary, 1904. 2S 431 SCARLET FEVER from two to seven microns or more in diameter. Most of the bodies seem to be composed of a close-meshed, finely granular reticulum. The second group of bodies have a striking radiate structure. They are found in vacuoles and in the protoplasm of epithelial cells, and free in the lymph spaces and vessels of the corium just underneath the epidermis. These radiate bodies vary from four to six microns in diameter. They are usually spherical, contain a central round body around which are grouped ten to eighteen narrow segments, which in some cases are united, but in others are sharply separated laterally from each other. Sometimes the segments are free. Mallory proposes for these bodies the name "cyclaster scarlatinalis," in consequence of the frequent wheel and star shapes of the rosettes, its most distinguishing characteristic. These bodies were found only early in the disease, most abundantly in the skin of a boy who died forty-eight hours after the appearance of the eruption. A number of cases in the desquamative stage of the disease were examined with negative results. The Relation of the Streptococcus to Scarlet Fever.— The finding of streptococci in scarlet fever by Frankel and Freudenberg, Babes, Loeffler, Klein, Crookshank, Fiessinger, Dowson, Berge, Lemoine, and Baginsky and Sommerfeld has already been referred to. Lemoine, in a study of the throat in 117 cases of scarlet fever, found the streptococcus alone in 93 cases and present with other bacteria in 14 cases. In 1900 Baginsky and Sommerfeld^ published the results of a large number of bacteriological examinations in scarlet fever. In 411 cases of this disease streptococci were constantly found in the throat. In a later series of 290 cases streptococci were found in 285. In this group they were found alone 21 times, with staphylococci 222 times, with diplococci 25 times, and with diphtheria organisms in mixed cases 17 times. In 701 cases, therefore, streptococci were absent but 5 times. Pearce^ found streptococci alone or associated with other organisms in scarlet fever, in abscessed ears, in the antra of Highmore, in bron- chopneumonia, serofibrinous pleurisy, empyema, acute mitral endo- carditis, cervical lymphadenitis, embolic abscesses in the lungs and kidneys, acute pericarditis, acute diphtheritic endometritis, etc. In 11 cases of general infection the streptococcus was found in 9. Strepto- cocci have been found at autopsy in the heart's blood, liver, kidneys, and other organs. Weaver' found streptococci in the tonsils of 18 cases. Cultures from the skin of 15 cases disclosed nothing of interest. Slawyk* in 98 fatal cases found bacteria in the blood of 52; strepto- cocci were found 39 times, and streptococci and staphylococci 6 times. Hektoen'^ found streptococci in the blood of scarlet-fever patients, 1 Berliner klin. Wochenschrift, 1900, Nos. 27 and 28. 2 Report of Boston City Hospital, 1899. s Journal of the American Medical Association, 1903, vol. v. p. 609. ■4 Jahresber. f. Kinderheil., 1901. ^ Journal of the American Medical Association. 77//'; BA(!TI<:iil()l/)(!Y OF SCAUfJ-:T FHVHIi 435 more particiiliirly in (Ik' sov(;re cjisos. 'J'liry wen; ahsent, however, in some of tli(^ IVUiil cas(!.s. S('lijunl)er^ and Gildcrsleevc' oxiiinincd, harlcriolof^ically, tlif throats of 100 patioTils snflVritif»; fi-oiii scarhit fever. A f^reat vari(;ty of orpjanisins was isohitcd. Strej)toeoeci were found in SS rases and staphylococ(;i in 73. The staphylococci varied in pathogenic power, but, as a rule, killed rabbits and guinea-[)igs in a sliort time. ('ultures were also made from the throats of 100 apf)arently well jKM'Sons and from S2 per cent, of them stre[)tococci wen; f^btained. A number of these were tested and found to l)e as virulent as tho.se from other sources. The almost constant presence of streptococci in throats of scarlet- fever patients and their activity in the production of such complications as otitis media, cervical abscess, and endocarditis have led certain writers to afHrm their belief in the streptococcal origin of scarlet fever. Dowson, Berge, and Lemoine have, in recent years, particularly cham- pioned this view. There can be no question as to the constancy with which the streptococcus is found in scarlet-fever throats, and at autop.sy in the various organs and tissues. This would constitute a strong argu- ment in favor of its specific pathogenicity in scarlet fever, were it not for the frequency with which it is found in other infectious diseases. For instance, in smallpox it is scarcely less ubiquitous than in scar- latina. It is commonly found in the late pustules of smallpox, and in many of the cutaneous complications, such as boils, impetigo, abscesses, erysipelas, gangrene, etc. After death streptococci are found in the cutaneous lesions and internal organs in nearly all cases. There would appear to be in many cases an agonal or post-mortem diffusion of streptococci throughout the tissues. In 40 autopsies on smallpox patients made by Perkins and Pay, streptococci were found dis- tributed throughout the body in 38. Ewing found streptococci in about 90 per cent, of the skin lesions at autopsy; he also noted the presence of streptococci in the blood after death in every one of 29 cases examined. It is evident from the above and other investigations that the strepto- coccus is almost constantly found in fatal cases of smallpox. While no one can seriously entertain the idea that its role in smallpox is causal, it is so uniformly present that some writers believe it bears a peculiar relationship to the disease differing from most secondary infections. Many writers regard the smallpox bacterjiemia as the most frequent cause of death in smallpox. Councilman" says: "As a result of the study of the disease, both by culture of the lesions and organs and by microscopic examination of the tissues, we are inclined to regard bac- terial infection as a more important agent in bringing about a fatal termination than the specific parasite The bacteria are 1 A Bacteriological Study of the Throals of One Hundred Cases of Scarlet Fever, etc. : Trausac- tions of the Philadelphia Pathological Society ; also Medicine, September, 1901. » Journal ot Medical Research, February, 1904, p. 358. 436 SCARLET FEVER chiefly streptococci." Perkins and Pay, and likewise Councilman, sug- gest that the streptococci in smallpox gain entrance to the circulation through the bronchial and pulmonary mucous membrane. It would seem that the relationship of the streptococcus to scarlet fever and to smallpox is quite similar. It gives rise in both to numerous complications and not infrequently leads to a fatal termination. The proof that it is not the cause of smallpox is easy of demonstration; the proposition that the streptococcus bears no etiological relationship to scarlatina is more difficult to disprove. It appears to us reasonable that in certain infectious diseases, particu- larly scarlatina and smallpox, the resisting powers of the tissues are so weakened against the streptococcus, that this organism invades the system and works its noxious effects. Until the streptococcus found in scarlet fever is shown to possess properties which trenchantly distinguish it from other streptococci, and until this disease is experimentally produced by inoculation of a pure culture of such an organism, the belief in the causal relationship of the streptococcus to scarlet fever cannot be maintained. THE PATHOLOGY OF SCARLET FEVER. The Blood. — The older writers contented themselves with a descrip- tion of the fluidity, coagulability, and color of the blood. At the present day accurate methods are in use which throw considerable light upon the changes in the circulating fluid. Felsenthal and Bernard, from a study of the specific gravity of the blood, conclude that it is reduced in all cases of scarlet fever. The reduction in haemoglobin is disproportionately great as compared with that of the specific gravity. Hayem was one of the first writers to point out a reduction in the red blood corpuscles and an increase of the leukocytes. He also called attention to the frequent increase of fibrin, especially in attacks accom- panied by bad throats and suppurative complications. Ewing^ states that the gradual loss of red cells noted by Hayem has been fully verified by Kotschetkoff, who found a reduction to three millions or less in nearly every case. Zoppert, on the other hand, found more than four million corpuscles in 5 out of 6 cases. A number of other observers have also found in a considerable number of cases but a slight decrease of the red cells. Estimations of the hoBmoglohin percentage were made by Widowitz^ in 14 cases of scarlet fever. In all but 1 the haemoglobin was strikingly high in the beginning, then falling until the commencement of con- valescence, when it again increased in quantity. When nephritis develops a more decided fall takes place. 1 Clinical Pathology of the Blood, 1901. 2 Hamoglobingehalt des Blutes Gesunder und Krankerkinder ; Jahrbuch f. Kinderh., N. F. xxviii. p. 384. 77//'; I'ATiioLodv ()!<' scMiLhrr /<■/':]■ f'ju, 437 Leukocytes.- 'Ili(! white cells have been carefully .studied by a nurrilxM" of iiivcsti<^ji,t()rs, uotahly Kot.sclietkfjn' and Bowie. 'Jlien; i.s f^eneral a^eeineiit as to the uniform ;i,nd early a[)})earance of leuko- cytosis. Kot.schetkoff .states that leukocyto.sis is influenced hy the type of the disease; mild cases show usujilly from 10,000 to 20,000 white cells; tnodcrately severe cases, from 20,000 to .'->0,000 cells; and the severe an(] usually fatal cases from 30 ,000 to 40,000 cells; in some rapidly fatal ca.ses over 40,000 leukocytes were present. Yet Rieder's^ cases seldom gave more than 20,000 cells, although some were complicated and fatal. FelsenthaP found in six attacks of moderate severity in (-liildren from 1S,0()0 to 30,000 leukocytes. Bowie^ gives the results of the careful and repeated examination of 167 cases. He concludes that (1) practically all cases of scarlet fever show leukocytosis; (2) the leukocytosis begins in the incubation period, very shortly after infection; it reaches its maximum at or shortly after the acme of the disease and then gradually diminishes to normal; {'S) in simple uncomplicated cases the maximum is reached during the first week, and the normal generally some time during the first three weeks; (4) the more severe the case, the higher is the leukocytosis and the longer it lasts ; the milder the case, the slighter the leukocytosis and the shorter time it lasts; (5) a favorable case of any variety of the disease has always a higher leukocytosis than an nnfavorable one of the same variety; (6) the temperature has no effect on the leukocytosis. These observations are in complete accord with those of Kotschetkoff. Differentiation of Leukocytes. — Bowie states that the poly- morphonuclear leukocytes are increased relatively and absolutely at first, and then fall to normal; the lymphocytes act in an inverse manner. In simple cases this cycle occurs within the course of three weeks. Kotschetkoff estimates the number of the polymorphonuclears as vary- ing between 85 per cent, and 98 per cent., according to the severity of the disease; the highest point is reached on the second day of the erup- tion, a gradual diminution then occurring. The lymphocytes are at first diminished, but later increase to normal. According to Bowie, the eosinophiles are diminished at the onset of the fever. In simple favorable cases a rapid increase then occurs until the height of the disease is passed, when a gradual decline to normal takes place, the latter occurring after the disappearance of the leukocytosis. The more severe the case the longer are the eosinophiles subnormal before they rise again. In fatal cases they never rise, but sink rapidly toward zero. Kotschetkoff says that eosinophiles in all but severe cases are normal or subnormal at first; after two or three days they steadily increase, reaching a maximum of 8 per cent, to 15 per cent, in the second or third week, and then decline slowly to normal about 1 Quoted by Ewing, loc. cit. s Quoted by Ewing. * Quoted by Ewing. * Leukocytosis in Scarlet Fever, Journal of Pathology and Bacteriology, March, 1902. 438 SCARLET FEVER the sixth week. The eosinophiles may disappear early in the disease in cases which prove fatal. While the above quoted results of Kotschetkoff and Bowie are in striking harmony, certain other observers have noted divergent findings. Sevestre/ frorn an examination of 13 cases, concluded that "in severe cases it was found that the percentage of the finely granular eosinophiles was always high," and "in the majority of cases examined the per- centage of the coarsely granular eosinophiles was found to be dimin- ished during the whole period of the disease." Ewing says that Weiss found no eosinophiles in 1 case at the height of the exanthem, and Rille observed marked eosinophilia in a fatal case; Bensaude observed as high as 20 per cent, of eosinophiles in one instance. Influence of Temperature, Rash, and Complications. — Kots- chetkoff states that the grade of the leukocytosis depends upon the severity of the disease, especially the angina, but not upon the height of the temperature. Complications such as lymphadenitis, otitis, and nephritis usually have little effect on the leukocytosis. According to Bowie, the temperature has no effect on the leukocytosis. In complications, the leukocytes go through a cycle of events similar in all respects to that of the primary fever as regards both sum-total and differential leukocytosis, and the same laws govern the behavior of the leukocytes in both cases. Sevestre says that "complications such as otorrhoea, rhinorrhcea, and adenitis tend to increase the number of white cells." He also states that a relationship exists between the leukocytosis and the rash; the former varies with the severity of the latter, and with the fading of the same the leukocytes show a marked diminution in number. Rieder and Turk^ have noted a high persistent leukocytosis, especially in those cases followed by nephritis or other complications. Pee^ found an increase in the leukocytes in 2 cases during a late adenitis. Bowie believes that the simple counting of the leukocytes is of but little diagnostic value. A differential count may, however, be of aid, for scarlet fever is one of the few acute infections in which one finds an early increase of the eosinophile cells and a persistence of the increase for some time. As regards ^prognosis he says: "In simple, severe scarlatina, if the leukocytosis be high and rising, a favorable course may be predicted; if it be low and stationary a tedious course may be expected. If the eosinophiles show a relative increase the augury is good; if they are normal or subnormal after the first day or two, then, in all probability, the case will be severe. The persistence of a relative increase of the eosinophiles suggests some complication, whereas, if they come down to normal in the usual manner, one may be free from anxiety as regards complications." 1 St. Bartholomew's Hospital Reports, 1896, vol. xxxii. p. 225 et seq. 2 Quoted by Ewing. s Quoted by Ewing. MOiaHI) ANATOMY OF SCAh-U'lT Fl'JVKR 439 MORBID ANATOMY OF SCARLET FEVER. But lilUc iul'ornuitioii is obtained by {>ost-rii(>rlf]ji (■xuniiiiutiou in uncomplicated cases of scarlet fever that cannot be foretold by the symj)tc)iniit()l()(jjy of tlic disease. The fj;ross morbid changes are usually observed in ilie skin, tongue, throat, and lyniplialit; structun;s of the body. Indeed, the most uniform j^ross alteratifjn is a hyperplasia of all of tlic lymj)hoid structures of the body. After death the eruption commonly fades away completely except in those cases in whicli the rash has been intense. In the hemorrhagic forms the |)etecliial S])ots will, of course, remain visible. Histological Changes in the Skin.^ — Tlie skin has been studied by a number of investigators, but principally by Klein, Unna, and Pearce. Klein^ studied the changes in the skin in 20 cases. He found the epidermis slightly thickened, particularly the mucous layer. Many of the rete cells showed dividing nuclei. Between the horny and mucous strata were small spaces containing granules resembling micrococci. In the rete Malpighii were found lymph corpuscles with deeply stain- ing nuclei. In the corium the epithelial cells of the follicles and sweat glands exhibited an increase of the nuclei. The bloodvessels were distended by corpuscles and occasionally by fibrin. The nuclei of the lymphatics and of the endothelial and muscular coats of the arteries were increased. Neumann^ noted swelling of the rete cells and elongation of the prickle cells, between which was evident a cell infiltration, occasionally containing red blood corpuscles. The bloodvessels and lymphatics were dilated. There was slight cellular proliferation around the sw^eat glands, hair follicles, and bloodvessels. Kaposi^ regards the changes in the skin as the result of vascular congestion with moderate cell infiltration; the papules and vesicles occasionally seen are due to an excessive exudation and cell proliferation in the papillfe and in the rete mucosum. Unna* examined the skin of 7 cases of scarlet fever. His findings are briefly as follows : There is a marked wrinkling of the whole epidermis along with the papillary body, which is due to an overstretching of the epidermis by the sodden, engorged cutis and to subsecjuent distortion, after excision of the skin, when the cutis contracts. The elasticity of the cutis indicates that during life it could not have been the seat of oedema. The bloodvessels of the true skin are enormously dilated, suggesting almost distention by artificial injection. This distention, which is present even after death, is the result of a vascular paralysis. White blood corpuscles are extremely scant, scarcely more than is found under normal conditions. 1 Local Government Report, viii. 24, London, 1876 ; quoted by Pearce, loc. cit. 2 Med. Jahrbiicher, 1882, p. 152. 3 Path, und Therapie der Hautkr., Vienna, 1899, p. 243. * Loc. cit., p. 629. 440 SCARLET FEVER No particular changes are found, at the height of the eruption, in the prickle layer. There is absence of mitosis, oedema, and of any dilatation of the interepithelial lymph spaces. Mitoses are found first and pretty numerously in the stage of desquamation. In view of the above findings, Unna regards the changes in the scarlet fever sisin as paralytic and not inflammatory. Pearce^ examined the skin in 8 cases between the second and sixteenth days, and 1 on the thirty-second day. On the second day, beyond a congestion of the bloodvessels and slight dilatation of the lymphat cs, no changes were observed. In 3 cases examined on the third day, a few leukocytes and lymphoid cells were seen in and grouped around smaller lymphatics beneath the rete Malpighii. From the fifth to tenth days the most marked condition was an nfiltration of the epithelium with polymorphonuclear leukocytes. The cells apparently leave the bloodvessels beneath the rete and pass up between the epithelial cells and collect in the superficial layers of dead cells, with which they are thrown off. In the connective tissue beneath the epithelium were numerous polynuclear leukocytes and a few plasma cells. The lymphatics were widely dilated and contained many leukocytes. By the twelfth and sixteenth days the leukocytic infiltration had nearly disappeared. In a late desquamating case the rete contained numerous mitotic figures. Tongue. — When death occurs early in the course of the disease the enlarged papillae may be visible at post-mortem. Pearce^ made a microscopic study of the tongue in 8 cases, all between the second and ninth days. The process in the tongue is said to be similar to that in the skin, but is more marked and begins earlier. The chief changes consist of a dilatation of the papillary bloodvessels and lymphatics, a leukocytic infiltration of the epithehal layers, particularly pronounced over the papillae, and the presence of leukocytes in and around the bloodvessels. The polymorphonuclear leukocytes wander between the epithelial cells, collect beneath the superficial epithelium, with which they are cast oft*. The most pronounced cell infiltration is seen between the fourth and ninth days. Mast-cells are increased in number and plasma cells are seen in small numbers about the bloodvessels. Mitoses in the epithelial cells are frequent. Pearce regards the process as inflammatory and suggests that the exciting cause of the leukocytic infiltration may be a positive chemotaxis excited by the presence in the tissues of the scarlet-fever toxin, or by substances formed by its action on the super- ficial epithelial cells. Lymphatic System. — In 1872 Harley^ studied the post-mortem changes in 28 cases of scarlet fever and concluded that it was a disease of the lymphatic system characterized by hyperplasia of the lymph glands, spleen, tonsils, liver, and other lymphatic structures of the 1 Scarlet Feyer, its Bacteriology and Gross and Minute Anatomy, Medical and Surgical Reports ot Boston City Hospital, 1899. 2 Loc. cit. 3 Med. Chir. Trans., London, 1872, Ix. p. 102. MOItBIl) ANATOMY OF S(!AlilJ':T h'KVKIi 441 body. Tie, thcnvfore, proposed to .substitute for the riaine, searlet fever {\w. tenn lyin|)liatic fev(^r. Then! eaii be no (loii})t tliat proiioiirK;(!(l liyperplasia of \\\c lyjn{>hoifl tissues is a coiistant {irid eoiiS})ieiioiJS aeeoin})aniiiient of sc;arlct fever. Pearee' found the mesenteric, retroperitoneal, bronchial, and tracheal glands enlarged in all cases. The superficial lymph nodes, such as the cervical, axillary, and inguinal, were also found enlarged. The glands were quite firm, and, on section, pale and watery. Klein and J'earce have both jnade histological studies of tlie glands. Klein^ examined the lymph glands in 8 cases. The centres of the glands were transparent and composed of large cells resembling giant cells. There were also large cells with transparent vesicular nuclei. In the sinuses were small cells and also large granular cells, with one or two transparent nuclei (endothelial). Pearce studied the glands, including the mesenteric, cervical, and bronchial, in 20 cases. The changes observed were similar to those seen in the spleen, but were not present in all cases. The bloodvessels were congested, and in 3 cases small hemorrhages were seen. The lymph sinuses were dilated and contained many large endothelial cells lyhig loose in their lumena. These cells were frequently observed to be phagocytic, containing a number of disintegrated lymphoid cells. Plasma cells, exhibiting numerous mitotic figures, were found through- out the lymph nodes. Spleen. — The gross appearance of the spleen, according to Pearce, permits of a classification into two different groups. There is no increase in pulp, but a marked enlargement of the Malpighian bodies. In such cases the spleen is firm, and the capsule smooth but not tense; on section there is seen a dark-reddish background, dotted everwhere with regularly or irregularly enlarged Malpighian bodies. This con- dition was noted in 13 out of 23 cases examined. In the other class the splenic pulp is greatly increased and the Mal- pighian bodies indistinct. The spleen is then large and soft. This condition was seen in 7 cases, in 2 of which, however, there was enlarge- ment of the Malpighian bodies. In the remaining 3 cases absolutely no change in the gross appearance of the spleen was visible. The differences described do not seem to depend upon the age of the patient, the stage of the disease, nor the intensity of the infection. Klein^ noted, in 8 cases examined histologically, an enlargement of the Malpighian bodies. A peculiar pale area, composed of endothelial- like cells, was observed in the centre of the bodies. The intima of the bloodvessels exhibited a hyaline degeneration, at times leading to obliteration of the lumen. Pearce made a careful histological study of the spleen in 21 cases. The enlargement of the IMalpighian bodies was found to be due to a central massing of large endothelial cells in addition to the presence of numerous plasma cells. These were abundantly present also around 1 Loc. cit. - Transactions of the Pathological Society of London, 1S77 ; quoted by Pearce. 3 Quoted by Pearce. 442 SCARLET FEVER the bloodvessels, in the lymphatics, and along the trabeculse. The bloodvessels were greatly congested. A peculiar condition noted was a collection of cells, chiefly plasma and lymphoid cells, but occasionally also a few leukocytes, beneath the endothelial lining of the vessels. Liver. — The gross changes in the liver are not pronounced. It exhibits usually, although by no means constantly, some degree of enlargement. The consistence is ordinarily less firm than the normal liver. In 1 case Pearce noted on the surface a number of minute, yellowish areas, which were shown to represent necrotic foci. Roger observed in 2 cases a number of scattered red spots due to subcapsular ecchymosis, a sort of purpura of the liver. Histologically, the changes in the liver are those of an acute febrile infectious disease. In 22 cases examined by Pearce the liver cells in each instance exhibited the degenerative changes common to fevers. In 4 cases distinct fatty degeneration was noted, and in 7 cases extensive fatty infiltration. An infiltration of lymphoid cells with a few poly- morphonuclear leukocytes was found around the portal vessels in 11 cases. A few eosinophiles and plasma cells were seen, the latter more particularly in the bloodvessels. Phagocytic endothelial cells were found in the bloodvessels in 5 cases. Focal necrosis of the liver was observed in 4 cases. The focal areas seemed to arise from endothelial cells, derived in part from the capillary endothelium of the liver, and, in part, from embolism through the portal circulation of cells originating in the spleen. The changes are similar to those described by Mallory as frequently occurring in the liver in typhoid fever. Roger and Garnier^ made histological examinations of the liver in 12 cases. The changes described by them are of different types: one series concerns the mesodermic elements of the liver — leukocytic infil- tration, thickening of the capsule of Glisson, etc., inflammation of the vessels; the other affects the epithelial tissue. The first stage of inflam- mation in the liver is leukocytic infiltration of the portal spaces. Later, the epithelial cells are altered; they may merely show unequal coloration of the nuclei or they may degenerate in considerable number around the portal spaces, or, finally, a number only may degenerate, forming a limited focus which may subsequently become infiltrated with leuko- cytes. At the same time inflammation of the conjunctive tissues may increase and the cells present may undergo hyaline and fatty degen- eration or fatty infiltration. When parenchymatous hepatitis is extensive the interstitial changes also become pronounced. Gastrointestinal Tract. — The mucous membrane of the pharynx, tonsils, and soft palate show, under the microscope, the usual changes observed in inflammation of these structures. Fenwick^ described changes in the mucous membrane of the stomach analogous to the desquamation of the cutaneous surface; in severe cases there was an absolute loss of epithelium. In addition he found a 1 Des modifications anatom. et chimiq. dufoie dans la scarlatine, Rev. de m6d., March 10, 1900, and Roger, Les maladies infect., p. 1056. 2 Medico.-Chir. Trans, of London, 1862, xlvii. MOUIill) ANATOMY OF SCARfJ'//' FFVh'fi 443 dilatation of the l)loo(lve,ssels and a filling up of the ga.stric tii};iil<.s witli a granular and fatty nuitcrial and small cells. Crooke, in a study of cases, found catarrhal gastritis in all, anrl, in the severe cases, interstitial and folhcnhir gastritis characteri'/(;d hy hyperplasia and necrosis of the lymph follicles, and infiltration of the muscular coat with round cells. Ilesselwarth found 21 instances of severe gastroenteritis among -SI autopsies. I'earce examined the stomach histologically in 6 cases. In a case dying upon the second day the surface of the stomach was covered with a thick layer of mucus and necrotic epithelial cells, containing numerous leukocytes and cocci. Polymorphonuclear leukocytes and granular material were found in the tubular glands, and numerous plasma cells between the tubules. Enlarged and altered lymj>h nodules were seen in the lower part of the mucous membrane; 4 other cases showed similar but less-marked changes. The intestines exhibit changes very similar to those seen in the stomach. Virchow described marked hyperplasia and swelling of the lymph follicles. Crooke says that Peyer's patches at times look like those found in typhoid fever during the first week. Bone-marrow.— Pearce^ examined the bone-marrow in 11 cases, of which 2 were adults. In all the cases the Ijone-marrow was very cellular. Giant cells and nucleated erythrocytes were seen and eosinophile cells were found in abundance. Lymphoid cells and neutrophilic leukocjies were present in fair numbers. The principal cells, however, seen in all cases were about the size of and closely resembled the plasma cell. They formed the bulk of the cells found in the bone-marrow. Roger^ found the bone-marrow absolutely normal in 1 case, and in another evidence of slight reaction of the medullary tissue. Heart. — The cardiac muscle suffers in scarlet fever from two chief causes- — the scarlatinal poison and, secondarily, from involvement of the kidneys. The most common changes observed are cloudy swelling and fatty degeneration, processes which are observed in many infectious diseases. Romberg^ has pointed out that the interstitial connective tissue, as well as the myocardial tissue, shows pathological alteration. The muscle fibres are separated by masses of cells and the arterial bloodvessels exhibit distinct inflammatory changes. Pearce, in an examination of 9 cases, demonstrated fatty degen- eration in 5. Segmentation and fragmentation of the myocardium were observed in a few instances. The above changes doubtless result from the poison of the disease. The heart frequently undergoes hypertrophy and dilatation as a result of a coexisting nephritis. Friedlander* states that in children with nephritis the heart increases 1 Loc. cit. : Loc. cit. 5 Ueber die Erkrankungen des Herzmuskels bei Typhus abdom., Scharlach und Diphtheria; Deutsch. Archiv f. klin. Med., Bd. xlviii. and xlix. * Ueber Herzhypertrophie ; Du Bois-Reymond, Archiv f. Physiolog., 1891. 444 SCARLET FEVER in weight on an average about 40 per cent. Jager is of the opinion that two-thirds of all cases of scarlatinal nephritis are accompanied by cardiac hypertrophy and often by dilatation. When the integrity of the heart muscle is compromised in the earlier days of the disease by the fever and the scarlatinal poison, it becomes unable to withstand the increased' pressure later when the kidneys become involved, and thus undergoes dilatation. Silberman^ explains the heart changes as follows: (1) there is no disease in which the elimination of water is so suddenly and enormously diminished as in scarlatinal nephritis; (2) the glomeruli are principally affected; (3) there is extensive involve- ment of the kidney structure; (4) the oedema compresses the blood- vessels of the skin and in this way increases heart pressure ; (5) increased resistance in the aortic system is more readily followed by cardiac hypertrophy in children than in adults. RiegeP states that increased arterial tension accompanies all cases of scarlatinal nephritis, and as a result thereof hypertrophy of the heart takes place. The enlargement is sometimes observed a few days after the development of the nephritis. Forchheimer believes that from the effects of the scarlatinal toxin dilatation commonly takes place, even if lasting only a short time, with hypertrophy following as compensa- tory. A clinically demonstrable pericarditis is distinctly uncommon in scarlet fever. Slight grades of pericardial inflammation are occasionally seen at autopsy. When nephritis is present effusion of serum often occurs, in some cases giving rise to enormous distention of the peri- cardial sac. When inflammation is present the exudate may be sero- fibrinous or purulent; in the latter event streptococci and staphylococci are usually found upon culture. Endocarditis. — Endocarditis of the cardiac wall is said by von Jiirgensen,'^ to be more common than valvular endocarditis. Forch- heimer considers endocarditis as a very common complication of scarlet fever. The margins of the valvular segments are, in mild cases, the seat of small excrescences, in severe cases larger ones constituting a verrucous endocarditis. Roger in 2213 personal examinations, of which 1727 were in adults, observed endocarditis but twice, while extracardiac murmurs were found 692 times. In 1 of the cases of endocarditis there were ulcero- vegetating lesions and an abscess of the myocardium. The strepto- coccus was found to be the cause of the abscess. Antra of Highmore. — Pearce found an inflammation of these cavities in 3 cases. In 2 both cavities were filled with an abundant purulent fluid, and the process was a true empyema. In both of these cases both middle ears were infected, and in one of them the sphenoidal sinus was filled with a greenish-yellow pus. 1 Jahrbuch f. Kinderheilk., N. F., 1894, xxxvii. ; quoted by Forchheimer, loc. clt. 2 Ueber die Veranderungen des Herzens u. des Gefassystems bei Acuter Nephritis ; Zeitschr. f. klin. Med., 1884, Bd. vii. 3 Log. cit. MORIill) ANATOMY Oh' SCAUfJ'/I' F/'JVKR 445 Pulmonary Complication. — In a series of 23 autopsies Pearce fourxl hronckopyummonia in S eases, usually in the form of small, discrete noduUss, scattered alonfr the })aek or base of the lung. In 2 cases the process was confluent, involvin<( tiu; greater [)ortion of one or more lobules. In 5 of these cases both tiie strej)toeoccus and the staphylo- coccus aureus were found. In I case the latter was found associated with the pneumococcus; in 1 case the streptococcus was founfl alone. A fierojihriiious fleurisy was noted in 1 case as the result of strepto- coccus infection, and in another an em])yema witli atelectasis of the lung. In the latter a small abscess cavity was found on the surface of the lung. Kidneys. — A voluminous and somewhat confusing literature has accumulated upon the sul)ject of scarlatinal nephritis. Klebs, in 1870, was one of the earliest writers to call attention to a glomerulonephritis occurring during convalescence from scarlet fever. He divided the kidney alterations into three groups: (1) a granular desquamation of the epithelium in the febrile stage; (2) an interstitial nephritis frequently seen late in the disease; the kidney in this condition is large, lax, smooth on section and shows grayish-w'hite nodules; (3) a glomerulonephritis during convalescence. In 1883, Friedlander, from a careful study of the kidney in 229 autopsies, divided scarlatinal nephritis into three classes: (1) an early catarrhal nephritis, occurring during the first week; (2) an interstitial nephritis in which the kidney is large, white, and hemorrhagic; this form occurs in severe cases with bad throats and other septic com- plications; and (3) an acute glomerulonephritis which develops during convalescence. The latter condition occurred in 42 cases and was egarded by Friedlander as the most characteristic kidney 'esion of scarlet fever. In this condition the interstitial tissue is practically normal, the glomeruli being solely involved. Councilman in 1897 characterized the condition of the kidney in 3 cases of scarlet fever as a pure interstitial nephritis. He states ihat glomerular nephritis occurs chiefly in measles, acute endocarditis and diphtheria, and acute non-suppurative interstitial nephritis in diph- theria and scarlet fever. In the latter disease the kidney is large, pale, and mottled. The principal lesion is an acute cellular infiltration with a few phagocytic endothelial cells and leukocytes. The origin of the plasma cells is presumed to be lymphoid cells which have undergone conversion in the spleen, and which emigrate from the bloodvessels and undergo mitotic change in the kidneys. Pearce,^ in a study of 23 cases, found degenerative changes in all. Of 8 specimens examined in the fresh state, 6 showed a more or less marked fatty degeneration. Acute interstitial nephritis was the most important lesion present. In 4 cases this process was extensive and in 5 slight. In the former the cellular infiltration was most marked in the cortex just beneath the capsule, around the glomeruli and around ' Loc. cit. 446 SCARLET FEVER the bloodvessels in the intermediate zone. The cellular areas were made chiefly of plasma cells with a few lymphoid cells and leukocytes. The glomeruli were unaffected. These cases were fatal on the e ghth, ninth, fourteenth, and fifteenth days respectively. From the writings of various authors it is seen that a considerable difference of Opinion exists as to the most characteristic kidney changes in scarlet fever. Councilman expresses the view that differences in local resistance doubtless influence the susceptibility of the various structures. He believes that in all serious lesions of the kidneys the changes in some cases may be principally in the glomeruli, and in others in the interstitial connective tissue. The glomerular lesions may be accompanied by degenerative alterations in the epithelium of the tubules, which may or may not be secondary. Hyperplasia of the connective tissue cannot be regarded as secondary to tubular changes. Certain investigators, particularly Marie, Haskine, Guinon, and Babes have found streptococci in nearly all forms of scarlatinal nephritis. How far the inflammatory changes are due to such micro-organisms and to what extent the scarlatinal toxin is responsible, time and future research must determine. CHAl'TKR VIII. SCARLET FEVER. {Continued). THE DIAGNOSIS OF SCARLET FEVER. When scarlet fever exhibits itself in a prononnccd mid typifjil forin the (lias[)ital three times vdthin a year with the diagno,sis of scarlet fever, lie was admitted to the llos- {)ital first on June li, 1902. He had vomiting, sore throat, slight fever, and a generalized searlatiniform eruption. He desquamated y)rofusely. The sealing lasted almost nine w(>eks, and the patient was diseliarged on September 8, 1002. The patient was readmitted on January 9, 1903. He had sore throat, headache, slight fever, and a well-marked searlatiniform rash. Slight desquamation occurred upon the face and trunk. The patient was admitted for the third time on June 28, 1903. He had had repeated vomiting, headache, sore throat, and some fever; on admission there was a generalized, well pronounced searlatiniform eruption, not punctated, however. The tongue was heavily coated, but after this disappeared there w^as no enlargement of the papillfe. Desqua- mation was well marked, being particularly copious on the hands and feet. The latter were still peeling in large lamellae at the end of a month. Each of these attacks resembled scarlet fever sufficiently to cause the resident physician to admit the patient. We would call attention, however, to the fact that the fever and sore throat on each occasion were very slight. There was no prostration and the characteristic tongue was absent. We have no doubt that the patient was suffering from a searlatiniform erythema, possibly due to intestinal autointoxication. Drug Rashes. — Quinine, antipyrin, opium, belladonna, chloral, and mercury at times produce eruptions which may closely simulate that of scarlet fever. The eruption resulting from quinine is the most frequent and the most likely to be confounded with scarlet fever. x\s a rule, in these eruptions the constitutional disturbance is dispro- portionately slight, and severe sore throat, swelling of the glands, strawberry tongue, and middle-ear disease are absent. The eruption often fails to begin on the chest and pursue the normal progression of the scarlatinal exanthem. The occurrence of desquamation has no diagnostic value in these cases, as the drug rashes may be followed by a variable amount of epidermal exfoliation. Measles. — There is no difficulty in distinguishing between measles and scarlet fever under ordinary circumstances. There are, however, irregular cases of each disease in which the elimination of the other in the diagnosis is by no means easy. The rash in scarlet fever is now and then blotchy, especially upon the extremities; in other cases, particularly of septic scarlatina, a profuse rhinorrhoea may be present, even early in the course of the disease; these symptoms, associated with an otherwise irregular s^Tnptom- complex, may produce quite a resemblance to measles. The eruption of measles may, as a result of coalescence of the macules, 454 SCARLET FEVER closely simulate that of scarlet fever. In some epidemics the proportion of confluent measles eruptions appears to be greater than in others. A few years ago during the prevalence of a particularly severe form of measles, we noted a frequent tendency of the exanthem, after the lapse of twenty-four or forty-eight hours, to become confluent and present the appearance of a diffuse scarlatiniform eruption. Usually, however, there may be seen somewhere on the trunk or extremities sharp margin- ation of the eruption with contiguous areas of pale, normal skin. In measles the face is earlier and more copiously affected than in scarlet fever; the eruption is dusky red in color, palpably raised above the skin, and distinctly blotchy; it appears later than the eruption of scarlet fever (about the fourth day) ; there is a prodromal stage, during which time catarrhal symptoms affecting the eyes, nose, larynx, and bronchial tubes are present, producing watery eyes, sneezing, running nose, hoarseness, and frequent cough. The initial fever is not as high as in scarlatina and the tendency to vomiting is less. Sore throat, great glandular intumescence, strawberry tongue, lamellar desquamation, and nephritis, commonly seen in scarlet fever, are absent in measles. The presence of Koplik spots upon the buccal mucous membrane would decide in favor of measles. The discovery of a marked leuko- cytosis would, it is claimed, point strongly toward the scarlatiniform nature of the disease. At times a secondary roseolous or measles-like eruption appears later in the course of scarlet fever. This is regarded by Thomas as a pseudo- relapse, but it seems to us to be of the nature of a septic rash. Smallpox. — Scarlet fever may be confounded with the prodromal scarlatiniform rash that is occasionally seen during the initial stage of smallpox. The absence of angina and the appearance of the variolous papules will make the diagnosis clear. During the later pustular stage of variola an intense scarlatiniform eruption at times develops which may raise the question of a secondary infection with scarlet fever. There may be high fever, prostration, and subsequent desquamation. The absence of vomiting, sore throat, . the strawberry tongue, and the development of the eruption about the twelfth to the fifteenth day of smallpox will usually enable one to recog- nize the character of the rash. Influenza. — Influenza is sometimes accompanied by a scarlatiniform eruption which may cause scarlet fever to be suspected. The presence of severe muscular pains and catarrhal symptoms, and the absence of the angina and the characteristic tongue, together with attention to the character of the prevailing epidemic will usually suffice to distinguish the two affections. Rubella. — With the usual type of rubella scarlet fever scarcely comes into differential confiict. It is with that form which tends to present a diffuse eruption that errors may arise. (See article on Rubella.) Diphtheria. — Ordinarily scarlet fever and diphtheria have but little in common, and yet errors in diagnosis are not infrequent. Too often physicians glance into the throat, see exudate present upon the tonsils, THE DTACJNOSrS OF SCARLET FEVER 4.55 and perhaps iij)()ii tlie soft pnlatc, and straightway make the diagnosis of (lipl)theria. Time and time again liave w(; received calls at the Municipal Hospital for cases of diphtheria, only to discover on seeing the patient the presence of a scarlatinal rash. l)ij)htheri;i is ordinarily not accom])anied by an exanthem. Vomiting is nnich more common as an invnsive sym{>tfjm of scarlet fever than of diphtheria. The exudate in diphtheria is tough and thick, of a grayish or grayish-yellow color, and quite firmly adherent to the underlying mucous membrane. That of scarlet fever is yellowish, thin and smeary, and more easily wiped off. In scarlet fever, moreover, the tln-oat ordinarily shows more intense redness and oedema than in diphtheria. The soft palate commonly presents a punctated, reddened appearance. Enlargement of the maxillary and submaxillary glands occurs in both diseases. The temperature in diphtheria tends to subside in a few days; in scarlet fever it commonly persists for a longer period. The straw- berry tongue of scarlatina is absent in diphtheria. Otitis media may occur in both diseases, but it is more common in scarlet fever. Albuminuria is an early symptom in diphtheria and a late symptom in scarlet fever. It is present in about one-half or more of the cases of diphtheria and is commonly found on the third or fourth day. A transient albuminuria may occur early in severe cases of scarla- tina accompanied by high fever, but the true scarlatinal nephritis is ordi- narily discovered about the end of the third week. The early albuminuria of diphtheria is apt to be associated with the presence of tube casts. While the finding of Klebs-LoefHer bacilli in the throat is of great diagnostic importance, their presence does not exclude scarlet fever. At the Municipal Hospital we have cultures made of all scarlet-fever patients on admission to the hospital. The percentage of cases in which diphtheria bacilli have been found varies from time to time. It has been as low as 8 in 100 and as high as 30 in 100. It is by no means always the bad throats that give positive cultures. In many of the cases in which the Klebs-LoefHer bacilli are found there is no exudate at all in the throat. That diphtheria and scarlet fever may occur at the same time is generally admitted. In our experience scarlet fever has more often developed in the course of diphtheria than the reverse. Diphtheria is more apt to appear after the acute symptoms of scarlatina have subsided. Scarlet fever, on the other hand, not infrequently makes its appearance early in the course of diphtheria. To distinguish between the scarlatiniforin rash that occasionally occurs in diphtheria and a true complicating scarlet fever is a most difficult and, indeed, an often impossible task. Clinicians of experience recognize this fact. Osier, for example, says: "Scarlet fever and diph- theria may coexist, but in a case presenting widespread erythema and extensive membranous angina, with Loeffler's bacillus, it would puzzle Hippocrates to say whether the two diseases coexisted, or whether it was only an intense scarlatinal rash in diphtheria." 456 SCARLET FEVER It has been our custom to regard as a complicating scarlet fever any well-pronounced scarlatiniform rash accompanied by distinct elevation of temperature; if vomiting occur and the lingual papillae become enlarged the diagnosis is much clearer. We have sent all such cases to a mixed ward in which there have been undoubted cases of scarlet fever, and it has been extremely rare for any children thus transferred to contract scarlet fever. We have never seen an intense, well-pro- nounced scarlatiniform rash in diphtheria that we felt could be regarded as an erythema diphtheriticum. Since the introduction of the use of diphtheria antitoxin the difficulties of diagnosis have been increased, for a third possibility presents itself, namely, a scarlatiniform antitoxin rash. The occurrence of scarlatiniform eruptions in diphtheria wards is always a source of anxiety. If the patient is allowed to remain, other children may be exposed to scarlet fever; if, on the other hand, the patient is transferred to a mixed ward, there is a risk of his contracting scarlet fever. It is well to have nearby a number of small rooms in which patients may be placed for a few days and watched. These cases tax the diagnostic acumen of even the most experienced physicians. Tonsillitis. — ^An inflammation and enlargement of the tonsils with the development of exudate in the crypts is so often seen in scarlet fever as to constitute a part of the symptom-complex of this disease. It is recognized that scarlatina may occur without an exanthem. The determination of the scarlatinal character of a tonsillitis occurring in a person exposed to the infection of scarlet fever is a most difficult matter. If the exposure has been intimate, the individual unprotected by previous attack of scarlet fever, the characteristic tongue appearance and the angina present, and otitis media or nephritis develop, the existence of angina scarlatinosa would be highly probable. Follicular tons llitis not infrequently develops in persons exposed to scarlatina who have previously had the disease. Thomas says that all such cases should be regarded with suspicion, but we would hesitate to regard them all as scarlet fever. The symptoms are identical with follicular tonsillitis occurring from other sources. We have known persons unprotected by a previous attack of scarlet fever to contract, on exposure to the disease, what appeared to be an ordinary foil cular tonsillitis; although no eruption was discovered in these patients, they have at times desquamated on the feet in a quite characteristic manner. Patients with sore throats of this nature have also been known to communicate scarlet fever to others. It is often impossible to determ ne with positive- ness whether or not cases of follicular tonsillitis resulting from exposure to scarlet fever are to be regarded as angina scarlatinosa. Occasional y an erythema develops in the course of an ordinary follicular tonsillitis. This eruption is often partial and may appear first on any part of the body. The exclusion of the diagnosis of scarlatina is only possible after a careful study of all of the symptoms, general and local, and attention to the circumstances of exposure and epidemic influence. 77//'; J'UOfJNOS/S OF SdAlffJ'/I' FI'lVFIi 457 THE PROGNOSIS OF SCARLET FEVER. The most important factor bearing upon the prognosis of .scarlatina is the character of the prevaiHng epi(l(;mio. Some outbreaks of scarlet fever are of extreme mildness and others are frightfully severe. Syden- ham never saw a severe cas:^ of the disease and, tlierefore, spoke of it "with a sort of coutcmj)t wliich ho was fjir from having for measles or smallpox." According to Trousseau, his illustrious master, liretonneau, had not seen a fatal case of scarlet fever from 1799 to 1822; he was, therefore, satisfied that "scarlet fever was the mildest of all the exan- themata." Later experience with a severe form of the disease caused him to change his opinion and regard the malady as equally mortal with plague, typhus, and cholera. The character of scarlet-fever epidemics, as regards benignancy or severity, commonly persists for a period of years before a change in type occurs. Graves^ has pointed out that a very fatal epidemic ravaged Ireland in 1800 to 1804. Then the type changed, and from 1804 to 18,31 the affection was so wonderfully mild that scarcely any deaths occurred. In 1831, however, a malignant epidemic broke out and in a few years spread throughout Ireland, causing tremendous loss of life. It is evident, therefore, that the mortality from scarlatina has an extremely wide range. It may fall as low as .3 per cent., or reach the frightful figure of 40 per cent. Johannsen states that in an epidemic in certain localities in Norway the death rate actually reached 90 per cent.; this murderous outbreak is absolutely without precedent. Hirsch and Thomas hold that the average mortal ty of scarlet fever is about 10 'per cent.; the more that the death rate exceeds this figure, the greater is the severity of the epidemic. When the death rate remains below 10 per cent., the epidemic may be looked upon as mild. Thomas, in enumerating the most fatal epidemics of scarlet fever, says Hambursin in Namur lost about 30 per cent.; Arrigoni about 40 per cent. ; Salzmann, in Esslinger, from 1853 to 1857, about 36 per cent.; at Hornbach, in the Palatinate, in 1868 to 1869, 34 per cent. The severity of scarlet fever has been diminishing within recent years. Johannsen says that among 84,580 reported cases in Norway there were 12,789 deaths, a mortality of 14.17 per cent. He regards the normal mortality in Norway as 13 per cent. Caiger^ states that during the past twenty-three years 81,350 cases of scarlet fever have been treated in the hospitals of the ^Metropolitan Asylums Board of London, with a combined mortality of 8 per cent. Since 1874 the annual percentage has progressivelv fallen from 12.2 to 5.9. 1 Quoted by Trousseau, American edition, p. 137. - Loc. cit., p. 128. 458 SCARLET FEVER Year. Notifications. Deaths 1890 . 15,330 876 1891 . 11,398 589 1892 . 27,095 1174 1893 . 36,901 1596 1894 ' . . 18,440 962 SCAELET-FEVER MORTALITY IN LONDON HOSPITALS. (CaIGER.) General Mortality. Hospital Mortality. 5.71 7.86 5.17 6.67 4.33 '7.28 4.32 6.11 5.21 5.92 The higher mortahty in the hospitals is said to be due to the larger proportion of severe cases sent in. The death rate in the Municipal Hospital has been as follows: Scarlet-fever Mortality in the Municipal Hospital OF Philadelphia. Year. Cases. Deaths. Percentage. Year. Cases. Deaths. Percent 1891 . 63 2 3.17 1898 . 380 45 11.84 1892 . 159 14 8:80 1899 . 604 57 9.43 1893 . 170 32 18.80 1900 . 646 53 8.20 1894 . 129 11 8.52 1901 . . 1115 108 9.68 1895 . 163 11 6.73 1902 . 673 56 8.32 1896 . 253 18 7.11 — 1897 . 858 99 10.37 Total . 5213 506 9.72 It is seen from these figures that the mortality rate is somewhat higher in Philadelphia than in London. The factors that influence the prognosis in individual cases are (1) the age of the patient, (2) the virulency of the infection, and (3) the character and severity of the complications. Age. — Age affects the prognosis in a most striking manner. While the general mortality of scarlet fever is from 10 to 12 per cent., in chil- dren under five years of age, according to Holt, it is between 20 and 30 per cent. In our own cases the general mortality among 5213 cases was 9.72 per cent.; in children under five years of age it was about double this figure — 18.6 per cent. The mort.ality for the different age periods of patients treated in the Municipal Hospital is herewith subjoined: Cases. Deaths. Percentage Under one year of age . 40 13 32.5 One to five years . . . . . 1670 305 18.32 Five to ten years ... . 1766 106 6.0 Ten to fifteen years . 476 19 3.99 Fifteen to twenty-five . . 295 18 6.10 Twenty-five and upward . 133 7 5.27 The above table shows the h'ghest mortality under five years of age, and particularly under one year. In the first year of life about one- third of our patients died. After the age of five has been passed the mortality diminishes pro- gressively. The death rate, in our own experience, reaches its minimum in children between the ages of ten and fifteen years. Virulency of Infection. — Virulency of infect on is indicated by great severity of the invasive symptoms. The prognosis is bad when the tem- perature is excessively high — 106° or 107° F.; when convulsions, stupor. TIII<: TUf'JA TMMNT OF SCA IlLI'/r FKVKR 45'J or coma develop; when the eruption is irregular or partial in distribution, or when it is livid, suppressed, or beniorrliaf^ic. These are malignant cases and tlie patient is, as a, rule, overwli(;liried early iu tlie course of the disease. During the first or second week the a[)pearance of severe anginose or septic symptoms renders the diagnosis unfavorable. Patients witli a sloughy throat with tendency to gangrene, great lymphatic enlargement, purulent rhinitis, and otitis are apt to succumb to the poison of the disease. Influence of Complications. — The complications which are most apt to cause death are nephritis, purulent otitis, meningitis, endocarditis, pneumonia, etc. The symptoms of evil omen in nephritis have already been referred to. It shou'd be remembered that cases of scarlatina that begin in the most benign manner may develop a severe nephritis with its attendant dangers. This complication comes on late, during the third week, at a period when the patient and his family have per- haps looked forward to complete convalescence. A favorable course of the scarlet fever may be anticipated, under ordinary circumstances, when the invasive symptoms are but moderately developed, when the throat is but mildly involved, when the eruption appears at the proper time, gradually reaches its maximum, and is uniformly distributed; when the fever steadily declines with the fading of the exanthem, and when complications are absent or of short duration. In forecasting the result of an attack of scarlet fever, it is wise for the physician not to give an unqualifiedly favorable prognosis, even in mild cases; the liability to serious complications in this disease should cause him to make some reservation in the expression of an opinion as to the outcome of the illness. THE TREATMENT OF SCARLET FEVER. In the discussion of the treatment of scarlet fever, we shall take up first the prophylactic or preventive measures, then the hygienic care of the patient, and, finally, the direct treatment of the disease and its various complications. Prophylaxis. — Scarlet fever is an endemic disease in nearly all great centres of population, and the health authorities of these common- wealths require sanitary regulations for the control and prevention of the disease. As a prerequisite to the prosecution of this work compulsory notifica- tion is essential. The health authorities must know when and where scarlet fever exists in order to be able to check its farther extension. It is the custom in some cities to placard domiciles in which scarlet fever exists in order to warn persons who might be otherwise disposed to enter the infected houses. While this plan has certain distinct advan- tages it does not seem to have found favor among the general body of physicians. Boards of Health should have the power of thus labeling infected dwellings, but should exercise a discriminating judgment in 460 SCARLET FEVER the employment thereof. When scarlet fever breaks out in a dwelling which is also used as a store or which communicates with one, the threatened use of the placard will often determine the tenants to send the patient to an infectious disease hospital. In the event of refusal, the public should be apprised by means of the placard of the existence in the building of the disease in question. There can be no doubt that many infectious diseases are spread through the mingling of children in kindergartens and schools. Scarlet fever almost invariably decreases during the summer vacation when the schools are closed, and increases again when the sessions begin. Every effort should therefore be made by the proper authorities to prevent the infection from being transmitted in the schools. The procedure in vogue in most large cities at the present time is as follows: The head of the school is notified by the health authorities that one of the pupils is sick with scarlet fever, and that he is not to be permitted to return, save after certified examination by a medical nspector or some other duly authorized person. Other members of the same household that are in attendance at school should likewise be debarred until the patient has been sent to a hospital and the premises thoroughly disinfected, or until the patient has completely recovered from his illness and proper domiciliary disinfection has been carried out. A child who develops an attack of scarlet fever should be debarred from school for a period of time not less than tivo months. Where nasal or aural discharge or desquamation persists beyond this period the enforced vacation must be still further extended. While such a rule often works hardship it will be found to best conserve the public health and welfare. In large cities it is an excellent plan to have medical inspectors make frequent examinations of the pupils in the public schools, with a view to determining the existence of suspicious sore throats, late desqua- mation, etc. Where such medical service cannot be commanded, teachers should be instructed in the symptoms of scarlet fever, so that cases presenting suspicious symptoms might be immediately sent home. A careful and intelligent teacher may in this manner often discover the disease in its incipiency and send the patient away before infection is conveyed to others. If these precautions be carried out it will not be found necessary except, perhaps, in extensive epidemics to close public schools. The proper ventilation and cleansing of schools, rooms, and buildings will greatly lessen the danger of the transmission of contagious diseases. Isolation. — The methods of isolation which are employed in checking the spread of infectious diseases in general can be utilized with much effectiveness in the prevention of scarlet fever. This is true (1) because but a very brief period elapses before the appearance of the characteristic eruption, thus making possible an early diagnosis, and (2) because the infection is not apt to be transmitted during the first few days of the disease. An opportunity is thus given to separate the patient from other members of the family, who may in this manner be protected. In this THF. TUICATMFjNT OF HCAlifJiT FEVER 461 respect scarlet fever differs essentially from measles, the conta^ium of which is given off at a very early date; it is much more difficult to protect persons who have been exposed to a case of measles than thf>se who have ])een in contact with scarlatina during the (;;jrly flays. The con- tagious principle of scarlatina is much less diffusihU' than that of measles. This makes it possible to localize the infection more readily in a portion of a house or a hospital. In households in wliich an ell'ective isolation can be carried out, the protection of other members of the family can be accomplished with reasonable assurance. It must be recognized, however, under these circumstances that eternal vigilance is the price of safety. It is a safer plan to remove the well children to another place. The liability of their contracting the disease from an early and brief exposure and then carrying tlie infection with them is not very great. If there is fear that this will take place they can be detained at home, carefully separated from the patient for a week, which period will fully cover the stage of incubation. Where effective isolation cannot be carried out at home, and this is the case in the large majority of households in a community, the patient should be sent to a hospital, the whole or part of which is set apart for the treatment of this disease. There can be no doubt that the treatment of scarlet fever in special hospitals is one of the most important means of preventing the spread of the disease. It is possible, with hospital-treated patients, to continue the isolation until every vestige of desquamation has disappeared, and until discharges from the nose and ears have ceased. This may in some cases require detention in the hospital for a period of twelve weeks or longer. In patients treated at home, especially among the poor, who are not so apt to recognize the responsibility of their actions, isolation for this period of time can seldom be enforced. A very large number of cases of scarlet fever are doubtless contracted from patients who are prematurely permitted to associate with others. This naturally brings up the important question: i^oii' long are scarlatina patients to be isolated and quarantined f This query is by no means easy of solution. Indeed, in no disease is it so difficult to affirm that the danger of infection has passed. The rule which is commonly followed is to continue the isolation until desquamation has completely ceased and the patient is free from nasal and aural discharges. In the average case this will cover a period of six or seven weeks. In some cases it will be necessary to extend the isolation beyond this period to eight, ten, twelve, or even fourteen weeks. Despite the utmost precaution in this respect, second cases will at times be infected at a late date. All large scarlet-fever -hospitals receive what are known as return cases. A certain small proportion, about 2 per cent, of the dis- charged patients, will give rise to cases of scarlet fever in the same household. The infection may be conveyed by patients who have been in the hospital nine, ten, eleven weeks or longer; this occurs even though 462 SCARLET FEVER desquamation is complete, and the patient antiseptically bathed and clad in perfectly clean garments. The infection in these late cases is probably derived from the secretions of the nose, throat, or ears. We have already made mention of a fatal attack of scarlet fever contracted by a mother from a child who was discharged from the Municipal Hospital after a sojourn of nine weeks. This woman had been exposed to her child at an early stage of the disease, at which time she escaped infection. We have observed on a number of occasions that children who are exposed to the infection at an early period of the disease may escape only to contract the disease from a patient who is supposed to be free of contagion. The Contagiousness of Desquamating Epithelium. — The view has generally been maintained that the infection in scarlet fever persists as long as there is any desquamation. Within recent years the con- tagiousness of the scales has been seriously questioned. Millard,^ in a thoughtful article, challenges the view that scarlatinal desquamation is infectious. The author obtained the opinions of a considerable number of experts whose answers he has formulated as follows: Sixteen gentlemen out of twenty-one state that (1) they can adduce no evidence that desquamating epithelium is, per se, a source of infection; (2) they consider that too much importance has been in the past attached to desquamation as a source of infection; (3) their experience does not support the popular view that desquamation after scarlet fever is necessarily an indication that a patient is still infectious ; (4) they believe that a patient may continue to desquamate for some time after he has ceased to be infectious; and (5) they do not believe that it is necessary, in order to prevent the spread of infection, that patients who "otherwise are quite ready to leave the hospital should be detained until every visible trace of desquamating epithelium has disappeared. In conclusion the writer briefly sums up the principal arguments against the supposition that desquamation is infectious as follows: "1. The absence of evidence supporting it. It is difficult to believe but that if the old supposition were correct, strong evidence of it would ere this have been forthcoming, as is now the case with discharges from the nose and ears. 2. The fact that infectivity begins prior to the onset of desquamation and frequently continues long after desquamation has ceased. 3. The fact that scarlet-fever wards, although abounding in desquamation epithelium, are not a danger to neighboring houses. 4. The fact that the proportion of 'return cases' does not appear to be increased among patients sent out from hospital still desquamating. On the other hand, the principal argument in favor of the view that desquamation is infectious is the fact that patients still desquamating, but otherwise apparently free from infection, have frequently been known to convey the disease to others. The whole force of this argu- ment disappears, however, when we consider that patients apparently 1 The Supposed Infectivity of the Desquamation in Scarlet Fever, Lancet, April 5, 1902. Tni<: TfHe carried out with tlioroughness. If perfunctory fumigation is relied upon to destroy all infection, unfortunate consequences may follow. The infection of scarlet fever has a remarkable tenacity and may remain resident in articles for months or years. Numerous instances of this are referred to in the chapter on Ktiology. All articles of little or no value in the sick-room should be burned. This is particularly true of those things with which the patient has been in contact, such as body-linen, books and toys. The apartments should be thoroughly fumigated or sprayed, prefer- ably with formaldehyde solution; as a matter of extra precaution this should be used in greater amounts than that ordinarily prescribed for the given air space. (See chapter on Disinfection.) The floors, woodwork, and furniture should be vigorously scrubbed with a carbolic acid solution of about 1 part to 40. The walls, if painted, should be washed with the same solution. If the walls are covered with paper it is wisest to have them scraped and repapered. Blankets, mattresses, upholstered furniture, clothing, etc., should be disinfected by superheated steam under pressure. Many large cities are now equipped with dis nfecting plants to wh'ch all such articles may be sent. Where such is not the case the blankets and bed- linen after being fumigated had better be boiled and the mattress destroyed by burning. It is a wise plan, whenever possible, to allow the sick-apartments to remain unoccupied and exposed for some days or weeks to the purif\'ing influence of sunlight and fresh air. The above precautions may be troublesome and expensive, but it is by careful attention to these matters that attacks of scarlet fever are often prevented and human life and faculties thus preserved. In the event of death from scarlet fever the body should be enveloped in a sheet wet with a 1 : 1000 solution of bichloride of mercury. It should be placed in a hermetically sealed casket and buried at as early a date as possible. The interment should, of course, be private. Care of Patient. Diet.^ — During the early days of scarlatina, when the fever is high, milk constitutes the best and usually the most accept- able diet. Cool milk is soothing to the throat and assuages the intense thirst which is present in severe cases. ]Most writers insist upon an exclusive milk diet throughout the entire febrile period, and many counsel its continuance during the early convalescent stage. When the patient is willing to take a sufficient quantity of milk to maintain his body weight there can be no objection to an exclusive milk diet; but 30 466 SCARLET FEVER some children and many youths and adults object to the monotony of an exclusive milk diet. We have had an excellent opportunity of judging of the effect of diet in scarlet fever. For many years the scarlatina patients in the Municipal Hospital received an exclusive milk diet during the febrile period. For the past eight months, during which time over 500 patients were treated, the patients have had a more liberal dietary. They were encouraged to drink plenty of milk, but were permitted as soon as they cared to, to have bread and butter with their meals and a simple pudding and stewed fruit once a day. We found that patients desired nothing but the milk while the temperature was high, but that when it became lower they were eager to obtain bread and butter in addition. Our patients appeared to progress just as well under the enlarged dietary. Urinary examinations were made every other day and the results compared with those under the exclusive milk diet. Albuminuria was not more frequent in the former than in the latter and the renal complications altogether were of a mild character. We present these facts for what they are worth. It is a hardship for some patients to be denied solid food for weeks, and they may as a result receive an insufficient amount of nourishment. We have never seen the above diet do any harm. Caiger^ allows patients, during the febrile stage, milk with eggs beaten up, broths, and calves-foot jelly. When the temperature falls he permits eggs, custard, light puddings, and bread and butter. Ripe and succulent fruit is given at any time throughout the illness. Caiger states that there is no risk, as has been alleged, of inducing a nephritis by permitting these articles of food to be taken. Our present practice is to use an exclusive milk diet in infants and very young children and in cases of nephritis, but to allow older children and adults a little more latitude. The latter frequently request light solid foods, and we believe that when there is an appetite for such articles they do no harm. Confinement to bed should be enforced during the febrile period, and, during cold and inclement weather, in severe cases for a week or more after the subsidence of the fever. Young and restless children whose actions cannot be well controlled had better be kept in bed from three to four weeks, or until the liability of nephritis has passed. While it is generally believed that "catching cold" has been greatly exaggerated as a factor in nephritis, Griffith states that chilling of the surface certainly acts as a powerful accessory cause in the production of complications. The detention of the patient in his bed or room will be influenced by the age of the individual, the season, and other factors which the discretion of the physician must solve. In view of the liability to kidney complications, it is necessary to keep the skin, which is an important eliminatory organ, in a functionally 1 Loc. cit., p. 170. 77//'; rU/'JATMI'JNT OF HCAULI'/I' Fl-Vhlli 467 active state. All (clinicians are agreed as to the a(]visal)ility of cinployiiig sponge baths; tepid water is preferably used and should be; apph(;d twice daily. In addition to promoting gentle diaphoresis these baths subserve the ends of comfort and cleanliness. To lessen the tension of the skin and allay it(;hing the inunction of some unguentous substance is desirable. We have for years employed cacao-butter for this purpose and have found it cleanly and agreeable alike to nurses and patients. When much itching is present a 1 per cent, menthol or 2 per cent, carbolic ointment may be used. Inunctions of salves containing oil of eucalyptus, ichthyol, certain silver salts, and many other substances have from time to time been lauded as possessing special therapeutic virtues. Medical Treatment.^ — It must be frankly admitted that we possess no medicament capable of directly influencing or abridging the course of scarlet fever. Our therapeutic efforts must be directed toward combating excessive development of the symptoms and toward prevent- ing and modifying complications. The treatment is, therefore, purely symptomatic in character. In mild cases of scarlet fever special medication is often unnecessary, the disease progressing to a favorable termination under the influence of proper hygienic care and nursing. During the febrile stage it is customary to administer a febrifuge mixture. We have been in the habit of using a combination of the liquor ammonite acetatis and sweet spirit of nitre, sw^eetened with a little syrup. Vomiting, when present, may be controlled by abstinence from food and the administration of fractional doses of calomel. Constipation may be corrected by the latter drug, or one of the mild vegetable laxatives. It is advisable to use some mild antiseptic in the throat, not only to relieve the congestion and soreness, but to lessen secondary infection and the habihty of extension of inflammation to the middle ear. Fever. — There are many cases in which attention must be directed to the control of high temperature and the accompanying nervous phenomena. Scar.et fever is frequently characterized by a very high initial pyrexia, which tends in a few days to defervesce. When the fever is above 103° F., and particularly when there are severe nervous symptoms, such as headache, delirium, stupor, or convulsions, antipyretic measures should be employed. In the reduction of temperature preponderant reliance is now placed upon hydrotherapy. Different clinicians have individual preferences as to the mode of appl^-ing water ; the methods m vogue are tepid sponge baths, cold sponge baths, wet or cold packs, and warm, graduated, or cold tub baths. Ice-bags and Leiter's coils are also employed. The routine treatment of scarlet fever with cold tub baths, as in the case of typhoid fever, has not met with general favor. They may be employed in cases accompanied by great hyperpyrexia, provided there is no pronounced cardiac depression. Cold baths are not borne well 468 SCARLET FEVER ' by infants or very young children, and should not be used in such cases. In cases of average severity with high fever, sponging with cold water, with or without alcohol, will usually suffice to keep the temperature within proper bounds. If this does not control the fever and nervous symptoms, resort may be had to the cold pack, which has a more pro- nounced antipyretic influence. In milder cases it may be all sufficient to keep an ice-bag or cold coils applied to the head. Warm tub baths of about the temperature of 95° F. are recommended by many physicians. These will frequently reduce a high temperature, and are more acceptable to the patient and the members of his family than cold baths; or the graduated bath may be used, the temperature gradually being lowered until the desired reduction in the fever is accomplished. The old superstition about baths being dangerous and causing patients to "catch cold" has been dissipated, and a complete unanimity of sentiment now exists among physicians as to the desirability of using baths of one kind or another in scarlet fever. Medicinal antipyretics are used to a very limited extent nowadays. The general feeling is that they are dangerous in large doses and in- effective in small amounts. Phenacetin in small doses (2 to 3 grains) may be given as an adjunct to hydrotherapy in bad cases, or to relieve headache and nervous symptoms in milder cases, Antipyrin and acetanilid are not in favor, as they are apt to cause too much cardiac depression. Throat. — Where the throat shows but slight involvement mild anti- septic fluids may be employed, either in the form of a spray or a gargle. For this purpose a weak Dobell solution or a solution of boric acid or chlorate of potash may be employed. Very young children cannot use a gargle, and often vigorously object to efforts at swabbing or spray- ing the throat. Where the physical resistance is so pronounced as to exhaust the child the procedure is of doubtful advantage and had better be discontinued. In the anginose variety of the disease it is equally important to cleanse the nares and throat and to avoid an exhausting resistance. A firm and skilful nurse is of great assistance under such circumstances. When the throat is severely involved and a streptococcus pseudo- membrane is present, systematic and vigorous treatment is indicated. Not only does the pharyngeal inflammation tend to spread to the nares and middle ear, but a general infection is apt to result from strepto- coccic absorption. In these cases the throat should be frequently sprayed with peroxide of hydrogen, plain or diluted, according to the age of the patient and the degree of inflammation present in the fauces. In septic cases with ulceration of some of the soft tissues, Caiger^ speaks in terms of high praise of a strongly acid solution of chlorate of 1 Loc. cit., p. 171. 77//'; THKATM/'JNT OF SdAh'LI'/J' h'EVI'lll 4G9 potash -containing a large amonnf of Free cliloiinc.' Tlio lliro;it .-md nose are irrigated witli tliis fluid by means of a soft-rubber syringe with a vulcanite nozzle, the head being held over a bnsiri wifli tlie mouth kept open. Caiger says: "No amount of gargling, spraying, or swabbing fan compare with it (this method) in ])oint of cflicaey." Forchheimer speaks highly of direct applications to flic throat by means of a swab saturated with I^oeffler's iron-toluol solution. This shonld be applied once or twice a day and held in contact with the diseased parts for a little while to secure the best results. In cases of extensive streptococcic exudate in the throat this writer counsels the use of antistreptococcus serum, which, he believes, will occasionally improve the local symptoms in a remarkable manner. Purulent Rhinitis. — Purident rhinitis in scarlet fever is apt to accom- pany severe throat involvement. The extension of the suppurative inflammation to the nasal mucous membrane increases the 1 ability to general sepsis and augments the gravity of the disease. A sanious, sero- purulent discharge issues from the nostrils in great quantities. The efforts of the nurse must be directed toward systematic and frequent cleansing of the nasal cavities. But this must be done with great care and gentleness. The forcible projection of liquids into the nose will do harm, as will, hkewise, the use of strong and irritating antiseptics. It has been our custom to have the nose gently irrigated with a warm saline solution; this is done with a small glass piston-syringe with a blunt end. In obstinate cases we have recently employed a 10 per cent, solution of argyrol, one of the newer silver compounds. This remedy has lessened the profuse discharge and has led to a healthier condition of the parts. Patients with gangrenous destruction of the soft palate or tonsils do not, as a rule, recover. Apart from the stronger remedies referred to in the treatment of membranous angina, one may, in this condition, employ a warm solution of permanganate of potash, 1 : 2000. In circumscribed gangrenous patches we have frequently applied the tincture of iodine with good results. Noma. — Noma is fortunately an uncommon complication of scarlet fever. When the condition is still in its incipiency the pultaceous deposit upon the mucous surface should be scraped away with a curette and the base thoroughlv cauterized with fuming nitric acid. This had better be done under the use of ether, which can be given in just sufficient quantity to benumb the patient's sensibilities. If the cutaneous surface becomes attacked, free excision will be found to be a not too radical procedure. Glands. — The glands at the angle of the jaw commonly attain the greatest size and most frequently undergo suppuration. Glandular 1 According to Caiger the solution is prepared by pouring strong hydrochloric acid upon powdered chlorate of potash in a large, stoppered bottle. The proportions advised are 5 minims of strong acid to 9 grains of the salt, with suflScieut water to make an ounce. The solution is of a greenish cplor, and has a strong chlorine odor. 470 SCARLET FEVER abscess may be expected in nearly all cases of anginose scarlatina. In the beginning an ice-bag should be applied about the neck. A special bag manufactured for this purpose buttons around the neck and keeps the ice in close apposition with the affected glands. A piece of flannel should be interposed between the bag and the skin. A dried pig s bladder filled with small pieces of ice will answer the purpose when an ice-bag is not 'available. If, despite the application of cold, the gland increases in size and suppuration becomes inevitable, heat should be substituted. Flaxseed poultices, rendered antiseptic by having incorporated in them a 1 : 4000 solution of corrosive sublimate, hasten the suppurative process. Upon the first suspicion of pus formation an incision into the gland should be made and free drainage established. It is better to lance prematur-ely than to delay too long, for inflammation may spread to the periglandular tissues. When cellular infiltration takes place free incisions should be made, even though no pus focus can be demonstrated, for by this means the deep -burrowing pus which forms later may be anticipated and the most fatal of complications — Ludwig's angina — may be prevented. The Ears. — Inasmuch as otitis media is an extremely common com- plication of scarlet fever, it should be guarded against as much as possible and the condition promptly met when it develops. The prophy- lactic treatment relates to those measures which are designed to keep the nasopharynx clean and free of infective secretions. While this object is a laudable one, no treatment will, in bad cases, prevent the development of otitis media. Indeed, it may be stated that the liability to ear complications is directly proportionate to the severity of involve- ment of the throat and nose. Pain in the ear is best relieved by the application of heat; this may be accomplished by syringing gently with water as hot as can be borne, or, better still, by the use of external dry heat. The hot-water bag or hot salt or bran bag may be placed against the ear. Dench suggests heating a little salt in the tip of a kid-glove finger and thrusting the same into the ear. The instillation of a few drops of a warm 4 per cent, solution of cocaine is advised by some writers. When the pain continues despite these measures, suppuration is probable. If upon inspection of the tympanic membrane bulging is seen, an incision should be made to evacuate the pus. It should be remembered, however, that in very young children, in whom otitis is commonest, the small size of the canal and the restlessness of the patient make aural inspection and paracentesis extremely difficult and unsatisfactory. Furthermore, spontaneous rupture is the rule in these cases, and may be the first evidence of involvement of the ears. After drainage is established it is necessary to keep the external auditory meatus clean and free of pus. Various liquids are advised, such as 1:5000 solution of bichloride of mercury, 1 in 4 solution of peroxide of hydrogen, saturated solution of boric acid, etc. We have found boiled water containing a little carbolic soapsuds very useful. All solutions should be used warm and injected gently with a soft-rubber Till'] tiii<:atmi<:nt of s(jaiuj<:t Fi'!V/toms of measles during the epidemic of 1070-74, and his description of the disease (barring a few terms, for instance the use of the word pustule) com})ares not unfavorably with j)resent-day writings: "The measles generally attack children. On the first day th(;y have chills and shivers, and are hot and cold in turns. On the second day they have the fever in full — disquietude, thirst, want of appetite, a white (but not a dry) tongue, slight cough, heaviness of the head and eyes, and somnolence. The nose and eyes run continually, and this is the surest sign of measles. To this may be added sneezing, a swelling of the eyelids a little before the eruption, vomiting, and diarrhoea with green stools. These appear more especially during teething time. The symptoms increase until the fourth day. Then, or sometimes on the fifth, there appear on the face and forehead small red spots, very like the bites of fleas. These increase in number and cluster together, so as to mark the face with large red blotches. They are formed by small papulae, so slightly elevated above the skin that their prominence can hardly be detected by the eye, but can just be felt by passing the fingers lightly along the skin. "The spots take hold of the face first, from which they spread to the chest and belly, and afterward to the legs and ankles. On these parts may be seen broad, red maculae, on but not above the level of the skin. In measles the eruption does not so thoroughly allay the other symptoms as in smallpox. There is, however, no vomiting after its appearance; nevertheless there is slight cough instead, which, with the fever and the difficulty of breathing, increases. There is also a running from the eyes, somnolence, and want of appetite. On the sixth day, or thereabouts, the forehead and face begin to grow rough as the pustules (?) die off and as the skin breaks. Over the rest of the body the blotches are both very broad and very red. About the eighth day they disappear from the face and scarcely show on the rest of the body. On the ninth there are none anywhere. On the face, however, and on the extremities— sometimes over the trunk — they peel off in thin, mealy, squamulae, at which time the fever, the difficulty of breathing, and the cough are aggravated." To Sydenham belongs the distinction of trenchantly separating small- pox and measles. But scarlatina and measles were still confounded. Twenty years later jNIorton regarded measles and scarlet fever as due to the same miasm; he asserted that they bore the same relation to each other as discrete and confluent smallpox. ]Many writers of this period spoke of scarlatina under the designation of morhUli confJuenfes. Reports of epidemics which were undoubtedly mealses were, according to Fuchs, published bv Forestus (1563), Lange (1565), Ballonius (1574-75), and Schenk (1600). As far as any accurate knowledge is concerned, measles is a disease of comparatively modern origin. **^' 478 MEASLES THE ETIOLOGY OF MEASLES. Measles may be regarded as the inost contagious of the various exanthematous affections. When it breaks out in a household or an institution it is almost impossible to prevent its spread, so diffusible is the contagious principle which causes it. This fact and the universal susceptibility to the disease make ^measles the commonest malad^i.to which human flesh is heir. But few persons go through life without at some time or other passing through an attack of measles. When it is escaped during childhood it is extremely apt to be contracted during dult life; in this respect it differs markedly from scarlatina, against which most adults acquire an immunity. Whether or not measles can be successfully inoculated still remains in doubt, despite the very considerable experimentation and literature on the subject. In 1758, Francis Home, of Edinburgh, attempted the inoculation of measles at the suggestion of Monro. He saturated bits of muslin with blood obtained by incising through the measle lesions. These were laid open upon the excoriated arms of healthy persons. In this manner he claims to have inoculated twelve children, in most cases with success, although the disease appeared in a mild form. Pieces of muslin moist- ened with the nasal secretion which were placed in the nostrils of healthy children failed to produce the disease. Theussink,^ who attended Home's clinics and saw these experiments, expresses doubt as to Home's interpretation of the results. At Theussink's suggestion, his friend Themmen later repeated these inoculations in 1816 with negative results. In 1822 Speranza successfully inoculated measles, and claims to have had the disease himself in this manner. In 1854, an Italian physician, Bufalini, reported successful results both of his own and his countrymen, Locatelli, Rossi, and Figueri; Horst and Percival are likewise credited with positive inoculations. In 1842 Katona^ performed 1122 inoculations in twenty-six townships of the Borsoder Comitates; 93 per cent, of these were successful, the attacks being of a mild character. An admixture of blood and the con- tents of miliary vesicles taken at the height of the rash was rubbed into excoriations made after the manner of vaccination. At the end of seven days fever and the usual prodromal symptoms developed; the eruption appeared two or three days later, about the ninth or tenth day after the inoculation. Mayr successfully inoculated measles in 1848 and in 1852. He placed freshly secreted nasal mucus from a case of measles in the nostrils of two children living at a distance from one another. At the end of eight and nine days, respectively, catarrhal symptoms developed, followed in a few days by fever and the eruption. In an article on measles^ published 1 Abhandlung iiberdie Maseru, translated from the Dutch by Dr. Doden, of Giittingen. 2 Nachricht von einer im Grossen erfolgreich vorgenommenen Impfung der Masern wiihrend einer epidemischen Verbreitung derselben, Osterreich. med. Wochenschrift, 1842, No. 29, pp. 697-98. 3 Mayr's article on Measles in Hebra's Diseases of the Skin, 1866. 77//'; i<:ti()IJ)(!y of m/'JAsiJ'JS 470 in 1866, Mayr remarks: " Inoculations with l)Iood made by myself in 1848 and 1852 afforded iiepjative results." The use of d(;s(juainatin^ skin also failed to traiisnn't the disease, as had previously oeeurred in the ex])eriineiits of Ahix.'uider Monro. The negative n.-sults in the transmission of measles by the inoculation of blood, in the hands of Thenimen, Albers, Mayr, and Thomson, should cause us to accept the alleged successful results with some reservation. Only after there has been confirmation by ])erfectly relial)le and careful observers, under conditions that preclude the possibility of the natural transmission of the disease, should measles be regarded as an inoculable affection. The usual mode of contagion in measles is by direct exposure to a person suffering from the disease. The contagium of measles differs from that of scarlet fever in two respects — it is more diffusible anrl it is less tenacious; the infection does not tend to any marked degree to cling to objects or apartments, and transmission of the disease by fomites is, therefore, distinctly unusual. Richard^ claims that the contagium of measles cannot be carried by fomites nor by a protected person. Bard^ states that the contagium of measles does not remain viable in a locality from which patients have removed. Comby^ says that the germ of measles has but little vitality . outside of the body, and that every germ that emanates from a measles patient is dead at the end of a few hours. While we are not prepared to dogmatically state that measles cannot be carried by infected objects or third persons, our experience is in accord with that of most writers that such occurrences must be ver\' rare. Von Kerchensteiner calls attention to the observation that physicians' children do not as a class contract measles earlier in life than other children. Considering the frequent neglect of precautionary measures, this would not be the case if the disease were readily trans- missible through infected garments. Official reports of the extensive epidemic of measles in the Faroe / Islands in 1846 (at which time over 6000 persons were attacked) gave no instances of transmission of the disease by infected articles or by third persons, and this point was carefully investigated by the physicians who studied this epidemic. Theussink states that he knew of a case where the infection was conveyed by a letter sent through the post, and also an instance where it was attributed to an engraving sent by mail. The negative evidence of intermediate infection is so abundant that such cases must be sub- stantiated beyond the perad venture of a doubt before they can be unreservedly accepted. When measles breaks out in a family circle it attacks all of the sus- ceptible members thereof. Kindergartens and schools offer fertile opportunity for the dissemination of diseases. Consequently measles, as well as the other contagious diseases of children, is much more 1 Therapeutic Gazette, July 16, 18SS. - Revue d'hygioue et de Police Sanitaire, May 20, 1S91. 3 Trait6 des mal. de I'enfauce. 480 MEASLES common during the periods of the year that these institutions are in session. SusceptibiHty to measles is practically universal. All mankind, almost without exception, will take the disease when exposed to it. The temporary insusceptibility exhibited by very young infants will be referred to later. One of the most remarkable and instructive epidemics of measles in history is that which visited the Faroe Islands_ija,-I846.^ These islands had been free from measles since ITSl^ a period oFsixty-five years. The disease was introduced by a Danish cabinetmaker who had become infected in Copenhagen. On his arrival at Thorshavn, the chief port of the islands, he communicated the disease to two friends. These persons gave rise to an epidemic which in a short space of time attacked over 6000 subjects out of a population of 7782. Persons of all ages were stricken and almost every household was converted into a hospital. The old inhabitants who had passed through an attack as children in 1781 alone escaped. Not one old person who was exposed to the infection, and was unprotected by previous attack, failed to take the disease. That certain individuals may exhibit a temporary immunity against measles is recognized by most writers. THomas says :^**T~oB'served, during an epidemic among about 130 cases, 5 children, 2 of whom were boys of two and three years, evince an immunity during this epidemic, while 2, boys of eight and twelve years, and a girl of nine years had evinced it as well during previous ones." Hoff makes mention of 3 .men, acting as nurses in the epidemic of 1846 in the Faroe Islands, who remained exempt, but who contracted the diseas ' when it recurred in the islands in 1875. Spiess^ states that a number of children, varying in age from four to seventeen years, after having been previously exposed to measles without contracting it, fell ill in 2 cases after seven weeks, in 1 after two months, in 4 after two and a half months, and in 1 after five months. Moore^ reports the case of a boy who, passing through two epidemics of measles with impunity, fell ill during a third and gave the disease to a younger brother, who at the time of the first invasion was not born, but who had successfully resisted the second one. It is difficult to explain this temporarily absent susceptibility, but it is quite analogous to that observed in suckling infants. The presence of an acute disease is apt to temporarily diminish susceptibility to measles, or, when the infection is received, to postpone its outbreak until convalescence from the first disease. This is true of most of the exanthematous affections. The susceptibility to measles may even be temporarily abolished during the existence of another acute malady. An instance of this has recently attracted our attention. 1 This remarkable epidemic was carefully studied and reported by Panum, who visited seventeen of the twenty islands of the group during a period of four months. A later epidemic in 1875 was assiduously investigated by E. M. HoflF; SundhedscoUegiets Aarsberetning for 1876. * Quoted by Thomas, loc. cit. s Quoted by Thomas, loc. cit. 77//!,' KTIOLOCIV OF M/'JASLFS 481 A boy, aged five years, was believed to be su fieri ug from smallpox and was sent into the wards of the Municipal IFospitaJ devoted to this dis- ease. On making our rounds we discovered tliat the boy harl measles at the height of Uw. eruj)tive stage aufl not small[)Ox; he was immedi- ately transferred to other quarters. He had been in the ward about fifteen hours; in this same ward were about fifteen children, from a few months to twelve years of age, suffering from smallpox in its various stages. Some of these children later succumbed to small})Ox; but not one contracted measles. Age. — Measles most commonly attacks indivichials l^etween the ages of one and ten years. Jllliis age . incideucc is. determined by several factors ail ahnosi universal vulnerability to the disease, a diminished, "siiscepliltiliiy (hii-ing the (irst year of life, and. the imiiiunity conferred- by one altack. There can be no doubt that infants under one year of age and particularly those under six months will commonly escape measles when exposed to the disease. This is ef|ually true of rubella, and, in a measure, true also of scarlet fever. This immunity is not absolute, but only relative. There are numerous records of infants of tender age who have contracted measles, but under six rnontlis tliey are very apt to resist the infection altogether. Pfeilsticker^ reports an interesting epidemic of measles occurring in Hagelloch, near Tubingen, in which 188 out of 197 children under fourteen years of age, contracted the disease. Seven of the children were under six months of age and all of this number remained xcell. Of 10 infants between six months and one year, 9 contracted measles. Tiiis-^kperience would tend toshow that-infants under six mjonths of age ar e very nuKjli -more immune than those a few mouths older. r]e~13arbillier," in an epidemic of measles in the Foundling Hospital at Bordeaux, noted but 7 cases among 40 children under one year of age. Mayr reports that of 10 newborn and suckling infants exposed to the disease, but 1 contracted it. The susceptibility, then, to measles is largely in abeyance during the first six months of life; after this period it gradually increases so that after the first year the temporary immunity has entirely vanished. Measles may in extremely rare cases be contracted during intra- uterine existence, and children may be born with fully developed erup- tions. After careful search of the literature Thomas was able to find but 6 properly authenticated instances of this occurrence. Numerous authors refer to congenital measles, but the facts in many cases render the diagnosis doubtful. Several authors cited by Thomas record cases which bear the stamp of genuineness. Clarus reported to the ^Medical Society of Leipzig that he had seen the eruption of measles quite plainly on a foetus the mother of which had died during the exfoliative stage of the disease. Hedrich speaks of a female child born on the fourth day of an attack of measles in the mother that was covered with the measles exanthem and had catarrhal symptoms, sneezing, coughing, and inflamed 1 Beitriige zur Pathologie der Masern, etc., Tubingen, 1863. 2 Quoted by Thomas, loc. cit. 31 482 MEASLES eyelids. Vogel, Guersent, Hildanus, Lidelius, Michaelson, Seidle, Ballantyne, and others have also reported cases which in all number about 20. The diagnosis in such cases could be controlled, as Thomas suggests, by noting the susceptibility or immunity of these children in later years. He reports an attack of measles in a woman five months pregnant, in which the susceptibility of the foetus was not affected, for the child contracted measles at the age of nine years. Von Jiirgensen says: "The poison must be able to pass through the placenta. It is presumed that the child becomes infected very soon after the disease organisms have attacked the mother, since the disease presents the same stage of development in mother and child at the time of the latter's birth." Hoff, on the other hand, states that "without exception everybody born in the year 1846 whose mother, according to her own statement and as affirmed by comparison with the church records, contracted measles during pregnancy, was attacked by the disease, if exposed to it, at the time of the epidemic of 1875." Hoff states that this was true no matter what month of pregnancy the mother happened to be in when she was suffering from the measles. This experience throws a flood of light upon the question of the placental transmission of measles. Hoff draws therefrom the conclusion that "there is not the slightest ground for believing the contagion to be carried to the foetus through the placental circulation." Adult life offers no such immunity against meiE!j(;cts fix; inf(M;f.ion takes hold and an e})ideniic results. Thomas asserts that in large communities epidemics mny be expected al)ont every two or four years. In small towns and villii,ge. The eyes are reddened and watery, sensitive to light, and often show puffiness of the lids. The nose at first feels obstructed, but soon a discharge issues therefrom, accompanied by repeated sneezing. Occasionally nose-bleed occurs, but this is seldom severe. In pronounced cases the face may present a pufl^y and swollen appearance. The involvement of the larynx and trachea gives rise to hoarseness a^d to a dry, hjrd^ and-high-pitchfid ..,££aigh. At times the throat is sore, exhibiting'^upon inspection redness and swelling of the tonsils, soft palate, and pharynx. The constitutional symptoms consist of fever, headache, loss of appetite, drowsiness, and irritability. Somnolence is often a prominent feature. Chills are rare, 1 Cited by Thomas, loc. cit. 2 Diseases of Infancy and Childhood, New York, 1899, p. 911. 3 Quoted by Thomas, loc. cit. PLATE XLVIL Fig. I. 'ig- 2. Fig. 3. Fig. The Pathognomonic Sign of Measles (Koplik's Spots). ^^•^^ 1- The discrete measles spots on the buccal or labial mucous membrane, showing the isolated rose-red spot, with the minute bluish-white centre, on the normally colored mucous membrane. Fig. 2. — Shows the partially diffuse eruption on the mucous membrane of the cheeks and lips; patches of pale i)ink interspersed among rose-red patches, the latter showing numerous pale bluish-white spots. Fig. 3. The appearance of the buccal or labial mucous membrane when the measles spots completely coalesce and give a diffuse redness, with the myriads of bluish-white specks. The exanthema on the skin is at this time generally fully developed. Fig. 4.— Aphthous stomatitis apt to be mistaken for measles spots. Mucous membrane normal in hue. Minute yellow points are .surrounded by a red area. Always discrete. Tlir<: SYM/'T()MAT()I/)(;V OF M/'JASfJ'JS 489 occiirriiifi;, ;i,('Cor(lin<^ (o Zi(Mr),s,S(;n and KniMcr, only five limes in ''>\\ cases studied by tlicin. 'I'lie bowfds arc iisnjdiy conslipjilcd, idtlioiif^li occasionally a slight diarriura is ()l)serv('d. 3.^heje yer does not, ol)serv<; any set standard, hut ia subject to con- ._sideral)le variation. Ju some cases it rises rapidly fJuring tbe first i3Vuiaty-fonr Iionrs, reaching by eveniiif,' 102° to lO.T F. On tlie morning of the se<'()n UJ n < > s J < u. I X 'k ^ "- "- \ Y J / ri 4 /* "^ .«^~, .,.».«,...>■ : •»— 77//'; S)'MI"r()MAT()f/X;Y OF MFASLFS 497 Desquamation begins as tlu; rii.sli f.-ulcs iiwiiy inid is fir,-,( /irjfc*] upon inili.'u sites of llie ci'dpiioii, ii;i,iiH'iy, (Ik; tuc(; uiid (he neck, llie scaling is braiuiy ;ui(I fiirriirjiccous, and is often ,so fine as to require careful "scrutiny (o obsnvc il. 'i'he skin seldom comes off in large flakes as it does in scarlet icvcr. 'Vlw. junount of des()uair);itif)M varies in difl'erent cases and is usually ])ro|)()rti()nate to tlie intensity of the antec^edent eruption. In many [)atients no descjuamation will be seen at all. On the trunk the perspiration which is common in measles obscures the fine scales or enables them to cling to the body linen. The desquamation is usually most observable on the face. S<"ding continues ordinaVily from a few days to a week, but may rarely be j)rotracted for ten fJays or iwo weeks. Anomalous Cases of Measles. — All exanthematous diseases exhibit at times variations from what might be regarded as the normal standard. Anomalous cases of measles may develop individually during the course of a normal epidemic, or there may be special aberrant features peculiar to prevailing forms of the disease. The special predominance of the papular element of the eruption is more common in certain epidemics. Mayr says that the Nirlas or "Nirles of Alibert" was mostly probal^ly a papular form of measles. The chief deviations from the normal type are those forms that exhibit unusual benignity or exaggerated severity. Mild Measles. — In rare cases there may be an absence of one or several of the important manifestations of the disease that go to make up the characteristic symptom-complex, ^hus, measles inay exist ^^■ithout fever, without catarrhal symptoms, or, indeed, without an eruption. ^'Measles Without Fever (Morbilli sine febre), Morbilli Apyretica. — Leulje says: "Although there may be very little fever in mild cases, it is never entirely absent." Nevertheless, von Jiirgensen^ reports two cases of measles occurring in infants of four weeks and twenty-one months of age, respectively, who had catarrhal symptoms and undoubted eruptions, and who had been exposed to measles, who never had any elevation beyond 99° F. Extremely mild and abortive cases of measles appear to be more common in young infants, who, as has been stated, possess only a very limited susceptibility to the disease. Measles Without Catarrhal Symptoms (Morbilli sine catarrho). — The absence of catarrhal symptoms is occasionally noted in infants during the prevalence of measles of the ordinary type. In such cases there is usually very little elevation of temperature and the eruption is not intense. The genuineness of these attacks is established not only by previous exposure to regular measles, but by the immunity conferred against subsequent attacks. J.t.. 14. evident that when the fever and catarrhal symptoms are insignificant the case must present considerable resemblance to rubella. If a disease prevails epidemically, in which these two groups of symptoms are uniformly in abeyance, the strong probabilities are that the disease is rubella and not measles. 1 Loc. cit., p. 267. 32 498 MEASLES Measles Without Eruption (Morbilli sine exanthemate, Morbilli sine morbillis). — As is the case in sniallpox and scarlet fever, it is possible ^for measles to occur without the development of the exanthem.. Such cases are, of course, excessively rare, but are recognized by careful and conservative writers. Thomas says that the diagnosis is more often made than is justified, but remarks that "this form of the disease may be diagnosticated in persons previously unattacked, if in a single case, during an epidemic of measles, the characteristic mucous membrane synaptoms together with fever appear and become exactly as much developed as in measles with an exanthem, so that we have ground for assuming that this symptom alone is lacking from a normal course." Cases may occur in which the attack of measles is typical up to the eruptive stage, but at this point the anticipated exanthem fails to appear and convalescence is established. Embden^ claims to have observed 20 patients among 461 cases of measles in Heidelberg, in whom the eruption was absent. The cases were of a mild type, but some few had severe complications. Rush makes mention of persons who in 1789 presented the usual manifestations of measles, fever, cough, etc., but no eruption except in some cases a trifling efflorescence about the neck and breast. Webster^ claims to have seen similar cases in 1773 and 1783. Well-authenticated cases of this kind are said to have been seen in an epidemic in Paris in 1850. The usual premonitary symptoms of measles appeared in a number of children; the regular course was followed in a certain proportion, but in a number of others some present- ing unequivocal spots of measles on the neck and chest, which rapidly disappeared, the lungs became quickly involved.^ Rilliet* reports a case of severe measles without eruption in a twenty- one-month-old child who contracted the disease twelve days after other cases in the same family. There were fever, coughing, and sneezing, but the eruption did not appear. On the fourth day a lobular pneu- monia developed, the child succumbing on the eighth day. Some authors accept the statement that desquamation may occur in measles without eruption. We contend, as in the case of scarlet fever, that desquamation does not occur without some antecedent structural change in the skin, and that when desquamation occurs it signifies that a rash has existed which was unobserved. There are mild cases of measles in which all of the usual phenomena are present, but in an extremely moderate, and sometimes imperfect, degree. The maximum temperature in such cases does not exceed 102° F. and the fever lasts but four or five days. The eruption is faint, poorly marked, of short duration, and often so indefinite as to require other evidence to establish the diagnosis. The catarrhal symptoms are also slight, but present more uniformity than the cutaneous manifesta- 1 Quoted by von Jiirgensen, loc. cit. " — 2 Quoted in editor's notes in Bulkley's American edition of Gregory's Lectures, 1851. ' London Medical Gazette, June, 1850, p. 572 ; cited by Bulkley, loc. cit. * Barthez and Rilliet, p. 249 ; cited by von Jiirgensen. 77//'; HVMI'TOMATOIJXIY OF MI'lASLHH 4!)9 tions. This form is ;i,])(, l.o Ix^ iiii!itt,(;ii(lc(l Ity coniplications ;ui(l flic prognosis is exlixniicly fav()rjil>l('. Severe and Malignant Measles.- INJcuslcs of unusual severity may occur in isolaicd inslaiiccs in ordinary c|)i(lf the eruption, so that on the second or third day the rash became cjuite scarlatinal in appearance. In some cases characterized by great initial severity the system seems to be overwhelmed by the poison of the disease. The temperature soars to great height (105° to 107° F.), there is profound prostration , great restlessness alternating with stupor, and the patient succuml)s })efore the appearance of the rash. In these toxaemic cases the diagnosis may be extremely difficult, and, unless elucidated by the history, quite impossible. Severity may also be manifested by the early development of pvbnonari/ complications. The first few days of the invasive stage may be quite normal, but suddenly the lungs become attacked and a fatal result rapidly ensues. In the so-called typhoii form of measles the disease is ushered in with high fever and great prostration. The skin is hot and dry; there is great thirst and marked muscular relaxation. Nervous symptoms are pronounced, the patient being either apathetic and somnolent or delirious. The tongue is dry and furred, the lips glazed, and the teeth covered w^ith sordes. The abdomen is tender and distended and the bowels often loose. The eruption is poorly developed and bluish in appearance. These cases are usually fatal, death taking place within a week or, less commonly, convalescence may occur after a tedious and protracted illness. Such cases as the above were not rare during the Civil War. Camp measles does not differ essentially from measles seen among civilians save that as a result of privation and exposure the disease is apt to assume a more severe form. IMeasles is one of the most formidable of camp diseases, as is attested Ky^the morbiefore the heifjjht of the eruption is attained. The recession of the rash may l)e temporary, tlie eruption later reappearing, or it may be permanent. The lay community has a traditional dread of this "striking in" of the eru})tion, fearing the involvement of one of the internal organs. As a matter of fact the sudden fading of the exanthem is not tlie cause, but the result of such condition. 'J^y^. plienonienon is usually due to severe pulmonary involvement, leadii)g to canlijic fnihire "a^nfr'conj^^^ crippling of the circulatory aftpafafi is. TIk- skin necomes pale and the eruption fades either completely oy shows itself as indistinct, bluish spots. With an improvement in the heart action the spots naturally acquire more color and the eruption, so to speak, returns. Thomas believes that rapid disappearance of the eruption does not necessarily indicate the development of some complication. He says: "I have never had an opportunity to convince myself of the connection of a speedy fading of the spots with the sudden occurrence of a complication. A simple rapidly progressing paleness of these can certainly not be considered anomalous." Postrubeolic Eruptions. — Reference has already been made to the occurrence of a morbilliform rash, associated at times with renewed fever, developing after convalescence from measles. In rare cases other eruptions may make their appearance about this time. Roger^ has seen cases, both of recurrent measles and also accidental erythematous rashes after measles. He reports an instance of the latter in a young woman twelve days after an attack of measles, and another in an infant, two and one-half months old, thirty-eight days afterward. Meyer-Hoffmeister^ saw a scarlatiniform erythema during con- valescence from measles. COMPLICATIONS AND SEQUEL .X OF MEASLES. Larynx. — A moderate grade of catarrhal laryngitis is uniformly present in measles, and is, therefore, scarcely to be regarded as a com- plication. The laryngeal symptoms develop early in the invasive stage, giving rise to hoarseness, frequent cough, arid occasionally spasmodic dyspnpea* The cough is dry, loud and hollow in tone, and in the begin- ning unproductive of expectoration. The paroxysms of coughing are often violent and incessant, seriously interfering with sleep. I'pon the appearance of the cutaneous eruption the cough becomes looser and less frequent and is accompanied by expectoration. Holt states that severe catarrhal laryngitis is present in about 10 per cent, of all cases of measles. Ulcerative Laryngitis. — Ulcerative laryngitis occurs in a certain pro- portion of severe cases. In such instances the inflammation is so intense 1 Loc. cit., p. 875. 2 Quoted by Thomas, loc. cit., p. 90. 502 MEASLES as to lead to necrosis of the mucous and submucous tissues. The vocal cords are commonly involved in the destructive process. Barthez and Rilliet found ulcerations and erosions in almost one-half of the cases of measles that came to autopsy. Pseudomembranous deposits were present in about one-fifth of the cases. Gerhardt^ has seen these ulcerations by laryngoscopic examination during life. He has found them particularly upon the posterior wall of the larynx in cases that exhibit marked stenosis. They may be seen at times early, but are more commonly observed during the eruptive stage. The superficial ulcerations give rise to a rough, dry, frequently repeated cough, accompanied by spasmodic attacks. There is pain upon coughing, speaking, or swallowing, and often considerable dyspnoea. The most dangerous form of laryngitis is that accompanied by the formation of a pseudomembrane, the so-called membranous laryngitis. The fatality of this complication is frightful. In the Hospice des Enfants Assistes in Paris, Granlou^ found this complication 235 times among 1633 cases of measles; out of these 235 patients 218 died, a most appalling mortality. We have seen a number of these cases that had to be intubated; they all succumbed to the disease. Holt has collected 35 cases of membranous laryngitis out of 2837 cases of measles from miscellaneous sources; he remarks that this complication is more frequent than this in institution epidemics. ^^^^{Terpbranowg. Uryngitis JOjay resiult from the action of Jhestrepto;;;^ coccus, the diphtheria bacillus, and, perhaps, other organisms. ^Holt states that when the membrane forms in the larynx at the height of , the disease it is almost always, of, streptococcic origin; when it develops at*- a later period it is usually due to the Klebs-Loeffler organism. ,,, The .majority of cases appear to be due to pyogenic bacteria. The false membrane is not always limited to the larynx, but may invade the fauces, nose, and mouth. The laryngeal stenosis usually comes on gradually, although more commonly the symptoms may be sudden in their appear- ance. The dyspnoea frequently becomes so alarming as to necessitate intubation or tracheotomy. These procedures, however, give, as a rule, but temporary relief, for a fatal bronchopneumonia is almost sure to develop. «.^..«--- The diagnosis between true laryngeal diphtheria and membranous laryngitis of streptococcus origin can only be indubitably settled by a bacteriological examination; the former condition is apt to develop late and the latter at the height of the disease. The prognosis appears to be equally desperate in both conditions. Lungs. — The trachea and larger bronchial tubes are so commonly involved in the catarrhal process in measles that a moderate grade of tracheitis and bronchitis may be regarded as belonging to the normal symptomatology of the disease. It is only when the inflammatory 1 Lehrbuch der Kinderkrankheiteu, p. 63. - La rougeole h rh6spice des enfants assist6s, Paris, 189a. C.OMI'hldATIONH AND ^ICljU Ef.M 01'' Mf'JASL/'JS 503 disturbance is intense, ;ui(l downward extension takes ]:)lace that the complication assunies a sei'ious Jisjx'c-I. Severe hroneliiiiJ eatarrfi usually niMiiifests ilseU' just at or after tin; lieiirhi of iIk; eruptive statfe; if it )>e sudieienlly widespread, llie fever, wliicli at this time falls, will eoutinue to remain elevated. There is fre(|uent eouf^hin^, accompanied hy muco- purulent exj)ect()ration. Foreifi;!! writers still employ the term (•(lylllary hr one} litis; the tendency in this country is to look upon the involvement of the minute bronchioles as an essential part of a bronchopneumonia. The symptoms of capil- lary bronchitis, therefore, are virtually those of catarrhal pneumonia. Fk;. si DAY OF ILLNESS 1 3 3 4 5 7 8 9 1 10 1 1 1 12 13 14 15 10 ! ir ! 18 ' 1!) 1 lOG 105 ^104 < >^103 ^101 100 99 i E_, M. E_ M A. M. EM tl-M ?- M. E. M. E r a. S.J1J.M E M E M _ W_ J _ *L E_ ^M^E ^•^:*':H - - -, - - - - - r~ -- M H - - i E - ■ f ' E - E ~ ~ ~ m F ~J- It ^ f . ■y ~ z E E E - — - --- z: ~ _ 4 ^ w i - = ^ - - z 4- z z ~ -^-m ; i - _. ^ f -t - "Tft -j-i- -p -p-[- — 1 p / 1 1 / 1/ ' \ .1- * ■ / \/ 1 ] 1 1 ; f 1 \ - -V 1 \ ] ^ T \ » \ \/ A Measles. Pneumonia. Boy, five years old. (Tuley.) Bronchopneumonia. — Bronchopneumonia is the most common and most fatal of all of the complications of measles. Other conditions fade into insignificance when compared, to the slaughter tliat this complica- tteiToccasions. Over a half-century ago Gregory wrote: "I am sure I ^peaK much within bounds when I say that nine-tenths of the deaths by measles occur in consequence of pneumonia." *^Bartels met with 68 cases of bronchopneumonia among 573 cases of measles, or 11.9 per cent.; Ziemssen and Krabler report 50 attacks of pneumonia among 311 cases of measles, or 16.1 per cent. The figures of Embden give a much smaller incidence — 27 attacks in 461 cases, or 5.9 per cent. The frequency of this complication seems to vary con- siderably in different epidemics. It is much more common in foundling ■^sylums, orphanages, and similar institutions. It is more apt to attack feeBlelind poorly nourished children and those debilitated by previous illness. This complication is particularly prone to attack children 504 MEASLES under two years of age. Holt states that in two epidemics in the Nursery and Child's Hospital, embracing about 300 cases, nearly all in children under three years old, bronchopneumonia occurred in about 40 per cent, of the cases. Of those who had pneumonia, 70 per cent. died. Henoch says that a certain amount of pneumonia is seen in nearly all fatal cases 01 measles. Bronchopneumonia usually manifests itself when the eruption begins to decline, although the onset may be delayed to a later period. The posteruptive decline in the temperature fails to occur, the fever instead remaining in the neighborhood of 103° F., with, perhaps, morning remis- sions of a degree or so. The pulse is greatly increased in frequency, and the respiration is shallow and hurried, and not infrequently labored and difficult; it is a pitiful sight to see the little patient with dilating nostrils and a livid countenance raise itself in the bed to relieve its distressed breathing. The cough may be short and repeated or infrequent and spasmodic. In unfavorable cases there is protracted fever, progress- ive increase in the rapidity of respiration (60 to 80), cold extremities, extreme weakness, and rapid-running pulse. Nourishment is refused and, when taken, is often vomited. Great pallor develops and toward the end a characteristic lividity is seen. A few hours before death the temperature may rise to great height, 107° or 108° F. In favorable cases the temperature at the end of ten days or two weeks declines gradually to normal, the cough lessens, the respiration improves, the child becomes brighter, desires more food, and takes an increasing interest in its surroundings. The symptoms that indicate the presence of a bronchopneumonia are protracted fever^ cough, rapid pulse, hurried aiid labored breathing, and prostration. Percussion will often discover some dulness over one or both of the lower lobes posteriorly; the respiratory murmur is diminished and bronchovesicular breathing is heard; in addition to the coarse rales heard in the larger tubes, fine, moist rales are audible over the small, consolidated areas. Lobar Pneumonia. — Isobar or croupous pneumonia is a much less frequent complication of measles than the catarrhal form, and is apt, when it occurs, to develop in older patients. This form of pneumonia is characterized by higher fever with fewer remissions, by its limitation to one lung or lobe thereof, by the presence of pleuritic pains, a shorter course terminated by crisis, and a lower mortality rate. Pleurisy. — Pleurisy with effusion is an unusual complication of measles. In some epidemics it may develop secondarily to a sevejgL^ pneumonia7 in' which case it is apt to eventuate in an empyema.- '^^ Fiirbringer^ calls attention to the occasional occurrence of a primary pleurisy with effusion. He has observed a number of cases, most of which ran an acute course and were probably purulent from the begin- ning. Pulmonary Tuberculosis. — Pulmonary tuberculosis may manifest itself as a termination of a long-standing bronchopneumonia occurring after * Eulenberg's Real-Encyclopedia, vol. xii., second edition, p. 559; quoted by von Jilrgensea. COMPJACATIONH AND S/'JQf/l'Jf.A'J Oh' MHASLHH 505 measles. Tlie l)r()ncliial catarrli and llie l(;won-(l nisisfarioe of the patient render the iniphintation of tuhfa-ciilosis n'.-ulily fxpHc^able. Jr]_ rases in wliicli a Ijifciit glaiuhilar tuherculosis, particularly of the ihonicic lymph nodes, li;i,s existed, the "attack of measles stiniuTafeslHe j)revioiis disense to noxious activity. Tn some cases tuberculosis rnay ""develop as a direct se((uel of measles, an irregular temperature persisting after the incomplete convalescence from the latter disease. The tuber- culous disease may take the form of an acute miliary tuberculosis. Holt truly says: "An attack of measles in a child vv^ith tuberculous ante- ^ cedents should always be looked upon with a])prehension." Barthez and Rilliet have observed gmrjreji/; of the Inn.r/s in four instances, and Steiner and Neureutter have mcl wiih this complication in two patients. This much to be dreaded condition may have its origin in a severe bronchopneumonia. Alimentary Tract.- — From what has already been said concerning the measles exanthem it is evident that a mild inflammation of the buccal and pharyngeal mucous membrane is uniformly observed. This comes on in the invasive stage and tends to subside as the cutaneous eruption increases in development. The cheeks, gums, tongue, soft palate, tonsils, and pharyngeal wall all participate in the catarrhal process. In feeble and debilitated children this inflammation, especially under the influence of infection with pyogenic and other bacteria, may lead to complications which are not only subjectively distressing, but of serious import. Aphthous stomatitis has been reported by a number of writers. The sores may give rise to much pain and interfere with the desire of the child to take nourishment. Ulcerative stomatitis not infrequently develops, particu- larly in the buccogingival furrow. This is characterized by the form- ation of small patches covered with grayish, necrotic epithelium. When the dead epithelial covering is cast off there are disclosed to view ulcer- ations of varying depth, with sharp and irregular edges; the base is frequently covered with a pseudomembranous deposit. These losses of tissue are not infrequently seen on the gums, and about the lips, par- ticularly the oral commissures ; in the latter regions each movement of the mouth causes pain and induces bleeding. In poorly nourished children these ulcerations may last for a long time before complete healing occurs. A fortunately rare but most frightful complication of measles is that > form of gangrene variously designated cancrum oris, gangrenous stom- ^ otitis, or noma. The fatal character of this complication makes the ^"^-^ condition of sufficient importance to warrant a description elsewhere. To be sure, there are less serious forms of gangrenous stomatitis in which the loss of tissue is circumscribed. We have not infrequently seen necrosis of a portion of the gum and subjacent alveolar process which, after the throwing off of the slough, has been followed by thorough healing; in some of these cases a portion of the bone and the neighboring teeth have come away. In a certain proportion of cases membranous patches may be seen 506 MEASLES on the tonsils and neighboring palatal mucous membrane. This process may spread downward into the larynx and give rise to the dreaded membranous laryngitis. The pseudomembrane may be of streptococcic or staphylococcic origin like the exudate seen in scarlatina, or it may be true diphtheria. In some cases tonsillitis is observed, in which event there is enlargement and congestion of these structures and pain upon swallowing. The stomach is but rarely the seat of any serious complication. Diarrhoea. — ^piarrhoea_is a common and not infrequently a serious accompaniment of measles. It may exist in all grades, from a slight catarrhal enteritis, lasting but a few days, to a severe enterocolitis with fatal outcome. x4ls would naturally be expected, diarrhoea is more jcommon in the summer months and especially in extremely hot summers. This complication is also more frequently observed in tropical and sub- tropical countries. Gregory says: "In India and other hot countries thoracic complications are rare; diarrhoea and dysentery prove the usual and most troublesome sequelae." It is not at all uncommon for a mild diarrhoea to be present in the invasive and early eruptive stages. There are frequent loose and watery movements, with or without pain, which tend to subside as the eruptive stage advances. The severe forms of enteritis and ileocolitis usually develop late during the decline of the eruption. In some cases the large intestine is involved and symptoms of dysentery manifest themselves; pain and tenesmus are present and frequent; small, bloody stools containing mucus are passed. Diarrhoea appears to be more common in some epidemics than in others. Willischanin^ observed an epidemic of measles in a girls' school in which 10 out of 50 of the patients had diarrhoea during convalescence. It lasted from three to five days and was believed to be due to the elimination of special toxins. Intestinal inflammation is most frequently observed in infants and young children, in whom it not infrequently leads to a fatal termination. Cases are on record, however, in which adults have succumbed to measles as a result of this complication. Nervous System. — As is the case with most infectious diseases, measles may be accompanied or followed by a great variety of disturbances due to involvement of the brain, spinal cord, or the peripheral nerves. When the fact is recognized that measles attacks almost the entire human family, the relative infrequency of nervous complications may be appreciated. Mental Disorder. — Measles is, in rare instances, followed by insanity, which usually takes either the form of mania or dementia. Christian^ reports a case of temporary mania and paralysis. Finkelstein^ saw 2 cases of mania after measles, and Bond^ observed a case developing on the eighth day of the disease. Weber noted delusions of persecution in one of his patients. In an epidemic of 108 cases occurring in an insti- , 1 St. Petersburger med. Wochen., December 4, 1893 ; quoted by Williams, loc. cit. 2 Centralbl., 1874, p. 95. » Vratsch, 1898, No. 20. ■* Maryland Medical Journal, January 29, 1898. COMPIJdATIONS AND S/<;(J(/ l'J/..^(;rt instances of jraiifrreiie attackinf>; various portions of the eutaneons snrfa(;e. l7npelir/o, boils, and abscesses are occasionally observed duririf^ con- valescence from measles. They represent varying grades of infection witii tlie common pyogenic organisms. Kczema occasionally makes its initial ap})earance after an attack of measles and may persist for an indefinite period. On the other hand, chronic eczemas have been known to disappear after an attack, as in cases reported by Behrend and others. Psoriasis has been observed to appear for the first time after measles. Measles, of course, does not cause the ])soriasis, but merely determines the date of its outbreak. Disseminated tuberculosis of the skin may follow in the wake of measles, as in the cases reported by Du Clastel,^ Haushalter,'' and Adamson.'' Du Castel saw 3 cases and remarks that "it is not exceptional to see a disseminated tuberculosis of the skin as a sequel to measles." This usually attacks the face, legs, and especially the upper extremities. The lesions appear soon after the decline of the measles eruption in the form of small, deep-red nodules. Haushalter saw 2 cases of scrofulous lichen, 1 of which later developed enlarged glands and tuVjerculous gummata. Adamson's case was one of multiple warty lupus occurring on the arms and legs. The patient subsequently developed a post- pharyngeal abscess and later hip disease. Roger'^ observed, in the spring of 1900, 4 cases of erythema nodosum after attacks of measles. A girl, aged seventeen years, eleven days after the termination of an attack of measles of moderate intensity, developed fever, and twenty-four hours later a typical erythema nodosum of the legs and subsequently the arms, accompanied by painful joints; the condition lasted fifteen days. The other 3 cases were analogous; they occurred in patients fifteen, seventeen, and twenty-six years of age, respectively. Fever appeared from nine to ten days after the termination of measles. The erythem- atous nodes and the joint involvement persisted from seven to ten days. Eyes. — Ocular complications are not rare in measles, a fact which is easily explained by the severe catarrhal involvement of the conjunctiva during the invasive and eruptive stages. The eyes are particularly apt to suffer in scrofulous children. Corneal ulcerations mav occur, and, in bad cases, lead to perforation and general panophthalmitis. It is not rarejfor obstinate blepharitis, granular lids, or keratitis to persist a long Time after convalescence from the original disease. Comby states that proper Carre of the eyes gTeatly reduces the number of ocular complica- tions, and in support thereof mentions the fact that he observed only 17 cases of conjunctivitis of moderate intensity among 71.5 cases of measles. 1 Quoted by Thomas. - Annal. de derm., etc., 1898, tome ix., Nos. 8 and 9, p. 729. •' Ibid., No. 5, p. 455. •1 British Journal of Dermatology, 1899, p. 20. s Loc. cit. p. 875. 510 MEASLES Ears. — ^Inflaimnation of the middle ear is by ilo -^Hieaiis.,arLJ4iicommon complication of measles, although it does not develop as frequently as in scarlatina. The catarrhal inflammation of the nasal passages fre- quently extends along the Eustachian tubes to the middle ear. Bezold^ carefully explored the ears in 16 fatal cases of measles, in all of which he found inflammatory changes. The tympanic cavity contained either a mucopurulent exudation or a material that was frankly puriform. The streptococcus pyogenes was present in about 50 per cent, of the cases; in the other half the staphylococcus aureus and albus were found. The raucous membrane is red, swollen, and covered with a muco- purulent or seropurulent exudate. Tobietz^ examined the ears of 22 cases of measles at autopsy and confirmed the above-mentioned find- ings. Both ofjl^ese writers are in accord as to the early development jqJE, the aural catarrh. The ear troul)le is hot regarded as due to a secondary "infection, but is rather the result of the localization in this region of "the enanthe^3^ j^^^^ otitis may therefore develop in the early eruptive period. In a case studied by Tobietz that died twenty-four hours after the appearance of the eruption, otitis was already present. This early otitis is comparatively mild and usually does not lead to perforation of the tympanic membrane. The later-developing otitis media usually results from infection from the nasopharynx, and is much nibre prone to end in suppuration and perforation. Severe purulent otitis media appears to be more common in some epidemics of measles than in others. Downie'' states that children who have adenoid vegetations and suffer from catarrh of the throat and nose are more apt to develop middle-ear trouble. He furthermore claims that the horizontal posture of the sick child favors Eustachian infection and retention of the inflammatory products within the middle ear. Of 501 cases of tympanic involvement in children seen by Downie, the con- dition was attributable to measles in 131 instances, or 26.1 per cent. Curiously, only 63 cases (12.6 per cent.) were observed that developed during an attack of scarlet fever. It is not always easy to diagnose the onset of an otitis media, particu- larly in young children who are unable to make verbal complaint. ^ The^ complication most commonly develops about the end of the second week. Children are cross and fretful, frequently toss the head and cry out with pain. The temperature is usually elevated and may rise to great height. When an otherwise inexplicable rise of temperature occurs about this, time, the "possibility of purulent otitis must be con- -Jfdered. Inspection of the tympanic membrane is not an easy task in young children. When this can be accomplished the membrane is seen to be congested and lustreless, and when pus is present the tympanum bulges into the meatus, the puriform secretion shining through the lower tympanic segment. In severe cases of middle-ear disease necrosis of the ossicles or of the 1 MiiQchener med. Wochenschrift, March, 1896. 2 Quoted by Comby, loc. cit. 8 British Medical Journal, 1894, vol. ii. p. 1163. COMPLICATIONS AND HI'Kid KL/K OF M/'JASIJ'JS F)]] surl-oundiiifij bony walls uiuy take place. Huikner' says: "An invasion of the labyrinth by cocci causing necrosis has been repeatedly dernon- strated of late. The lesion results in a very serious loss of functional power." The suj)|)urative inflaniination may extend to the mastoid cells or, in rare (•iis(\s, to the membranes of the brain. Ashby arifl Wriglit have pointed out the fact thnt infection may take j>lace througli the petromastoid suture, which in infancy is still ununited. Purulent meningitis, abscess of the brain, or thrombosis of the lateral sinus might thus (levelop. In general it may be stated that mi(Jdle-ear troul)le complicating measles is^less serious than that whicli occurs in scarlet fever. " I\l;iny ciiscs of (Icaf-miiHsm are traceable to attacks of measles. Kerr, Love, and Addison^ have collected statistics from ihstitutions in Great Britain which show that of 1140 deaf-mutes, 138, or 9.8 ^per^ cent., attributed their lo.ss of hearingTo^-ttaCks of "measles. "O'f'lCTS accjufrerl cases in American institutions, 52, or 3.1 per cent., were due to measles. Among 1989 acquired cases on the continent of Europe, 84 cases, or 4.2 per cent., were ascribed to this disease. In these cases the deafness results from destructive changes in the internal ear which have resulted from extension of the inflannriatory process from the middle ear. The Heart. — Endocarditis, pericarditis, and myocarditis are rare complications of measles. Inflammation and degeneration of the cardiac muscle may occur in malignant cases, particularly when there is hyperpyrexia. We recall a malignant family epidemic some years ago which destroyed the lives of the three children of the household. The first child sat up in bed during convalescence and dropped back dead. The other two succumbed to a profound toxaemia. Cases of endocarditis have been reported by Martineau, West, and Kobler. Hutchinson^ records 4 cases in which mitral murmurs developed during the course of measles, and Cheadle refers to 2 cases found in the post-mortem records of Great Ormond Street Hospital. Gomby dis- covered mitral insufficiency in a girl nine years old, after an attack of measles. Although Sansom* states that the influence of measles in predisposing to endocarditis has been much underrated, most writers are of the opinion that this complication is a rarity. Pericarditis, according to Autenrieth, is not infrequent. Cases have been reported by Berndt, Majer, Espinouse, Braun, Siegel, Metten- heimer, and Heyfelder.^ When pericarditis occurs it is apt to be asso- ciated with a pleuropneumonia. Kidneys. — Renal complications are rare in measles, their infrequenCy coiitrasting sharply with their prominence in scarlatina. Nevertheless, Baginsky says that his recent experience leads him to believe that they would be discovered more often if carefully looked for. 1 Behandlung der bei Infectionskrankheiten Vorkommenden Ohraffectionen, loc. cit., p. 581. - Deaf-mutism, a Clinical and Pathological Study, Glasgow, 1896 ; cited by Dawson Williams, loc. cit. 3 Med.-Chir. Trans., 1891, vol. xxiv. * Quoted by Williams, loc. cit. ^ Mentioned by Thomas, loc. cit. 512 MEASLES Febrile albuminiiria of brief duration is not uncommon in well- pronounced attacks of measles, as in other infectious processes accom- panied by fever. When the kidneys are seriously involved there may be general anasarca, as in cases reported by Abeille, Denizet, and Comby (2 cases). Ascites and anasarca may, however, occur without albumin- uria, at times in association with chronic diarrhoea. Cases of true nephritis have been placed on record by Geissler, Roser, Frank, Rilliet, West, Kjellberg, Lehman, Bouchut, Malmsten, Spiess, Hauner, Steiner, Neuretter, Zehnder, and Thomas, who cites these various writers. Fatal cases with ursemic symptoms have been reported by Miiller, Demme, Browning, and Zichy-Woinarski.^ Vulvitis.— ^ Among 715 cases of measles treated in isolation pavilions, Comby observed vulvitis twenty-five times, an incidence which he thinks was kept relatively infrequent through systematic antiseptic irrigations. The inflammation of the vaginal orifice and vulva begins early, as a rule, and may persist for some time. The parts are red, swollen, covered with a mucopurulent discharge, and extremely tender. Micturition is accomplished with considerable pain. In some cases vulvar ulceration occurs and more rarely gangrene. Glands. ^ — ^A moderate grade of adenopathy is a part of the normal symptomatology of measles. In some cases the lymphatic glands become greatly enlarged, particularly in the cervical region. In rare cases suppuration may take place, as in cases mentioned by Gregory and Rilliet. In other cases the glandular enlargement may persist for a long time and eventually terminate in glandular tuberculosis. This is particularly true of the bronchial glands. Fichtbauer, Thore, Eiseman, Bufalini, and Battersey^ have reported cases of inflammation of the parotid gland accompanying measles, and Seidl, Schultze, and Kellner have seen the parotids involved at a later period. Purpura. — Hemorrhages developing late in the course of the disease or during convalescence should not be interpreted as evidence of malig- nant hemorrhagic measles, but as a secondary and superadded condition. Nearly all of the exanthemata may at times be complicated at a late stage by the development of hemorrhages into the skin and from the various mucous membranes, including the kidneys and intestines. Masarei^ saw eight patients convalescing from measles attacked with fever, dropsy without albuminuria, and "scurvy, mostly in the form of purpura;" all of the cases ended fatally. Gley* saw intense purpura hemorrhagica, together with scorbutic appearances in the mouth, some days after the disappearance of the measles rash. Gangrene. — iVlthough gangrene is not a common complication of measles, it appears to occur more often after this infection than any other, excepting, of course, cutaneous gangrene in smallpox. The necrosis is apt to take the form variously designated as cancrum oris, gangrenous stomatitis, or noma. This formidable complication 1 Australian Medical Gazette, October 15, 1893. 2 Quoted by Thomas. ^ Quoted by Thomas, p. 104. * Quoted by Thomas. COMPLICATION H AND HI':Q(J I<:L/I<: of Mf'JASLI'JS 01.3 commonly (lf;vel()])S during Uk; dcdinc of the (inipflon. If is r;ffr;n associated With or"|'5TCred'prt-hynTTTi}ccr,ativ(; sfoiniiiifis. 'J'lic syjnpforn.s that first attract attention arc salivation ;in(l a fetid breath. If the mouth is inspected there will usually he found, })etween tlie commissure of the mouth on the alVected side and the opein'ng r)f Steno's duct, a vesicular elevation of a violaceous color; this becomes f^radually darker and finally gives way to a blackish, pultaceous mass. The corresponding portion of the cheek on the exterior is swollen and of a wax-like pallor. Soon a bluish-red spot appears, which l)ecomes gangrenous and breaks through. From tl)is point the necrosis now spreads in all directions. The spreading border is surrounded by a dusky-red zone which is firm and infiltrated. The immediate spreading edge shows a raising up of the epidermis in the form of a vesicular ring. There may be an extension Fatal cancrum oris after measles. The necrotic tissue has been removed, exposing to view the alveolus and teeth. of gangrene from one-quarter of an inch to an inch in twenty-four hours. The gangrenous process m severe cases involves the entire cheek and the greater part of the nose and hps. It has been known to attack the ear, the eyelids, and a considerable portion of the neck. I'sually the patient dies of exhaustion before such ravages are possible. In a small proportion of cases the gangrene ceases, a line of demarcation is formed, and the sphacelated tissues are gradually thrown off. In such instances the deformity must subsequently be remedied by a plastic operation. In the fatal cases there is great prostration, the child takes nourishment with difficulty, and deatli takes place ordinarily in from one to two weeks. A horrible odor emanates from the patient, which pervades the entire room in whicli he lies. There is a less serious form of gangrenous stomatitis in which the 33 514 MEASLES Fig. S3 Cancrum oris complicating measles. Photograph taken two days after the cutaneous tissues became involved. Fig. 84 Same patient as Fig. showing the spread of the gangrene. Photograph taken three ( after the previous picture. COMPLICATION H AND HI':QUI<:L/K OF MFASLFS 515 necrotic process is limited to the iiiiieoiis inciriljraiif; and fjoriy tissues of the mouth. Tliis (lommonly lias its orif^iu uhout, fhc ^ums and alveolar process. After the loss of some of the teeth and a jjortion of necrosed alveolus, the process may cease and recovery take place. In some cases, however, this hony necrosis is merely j)art of the general gangrenous process wliich attacks the cheeks. The necrotic process may, in rare cases, attack the genitalia, particu- larly of female children, giving rise to the condition known as noma jiudendi. The course of the gangrene does not differ from that involving the mouth. Fig. 85 ^^^^^^^ |P^^^ '%. ' P -*•■'<►,■., ma^A gjjIH 1 5 k. ..J. — .^H Same patient as Figs. S3 and 81. Pliotograpli taken alter deatti on the eighth day after the beginning of the gangrene, and three days after Fig. 84. Measles has preceded about one-half of the cases of cancrum oris on record. In 106 cases of siangrene of the mouth, Tourde found 41 to follow or accompany attacks of measles. Caillout and Bouley, in 46 cases of gangrene of the mouth, noted measles as an antecedent dis- ease in 40 instances. Mahieux saw measles produce gangrene of the mouth in 3 out of 11 cases. Thus, in 163 cases of gangrene of the mouth measles preceded in 84, or over 50 per cent.^ Rilliet and Barthez observed 11 children with measles attacked with gangrene; the localization was as follows: gangrene of the mouth, 8 times; gangrene of the lungs, 4 times; gangrene of the pharynx, 3 times; gangrene of the larynx, once. The gangrene appeared in several localities in some of the patients. INIoynier saw 6 cases of gangrene in 1 Mentioned by Moynier. Des accidents graves de la rougeole, etc., Metz, 1S60. 516 MEASLES measles. In 4 cases the vulva was attacked, 2 dying. Gangrene was noted five times attacking the skin, the following regions being selected : abdomen, face (twice), arm, and buttock. A number of other cases of gangrene of the mouth were observed. Pneumonia and diarrhoea were frequent .complicating conditions. Hildebrandt^ and Perthes^ from the literature have collected 133 cases of cancrum oris in which the antecedent or accompanying disease is mentioned. Noma accompanied or followed measles in 53 cases. The diseases are as follows:^ measles, 53 times; typhoid fever, 26 times; chronic diarrhoea, 21 times; scrofula, 19 times; smallpox, 9 times; diphtheria and measles, twice; diphtheria and typhoid, once; diphtheria of the genitalia, once; diphtheria and scarlet fever, once. The affection is extremely rare in infancy and beyond the age of puberty; it may be remarked that measles is also uncommon during these periods. Von Bruns* collected 413 cases of noma, among which only 6 cases occurred in infancy. The cause of noma is but poorly understood. It has been variously attributed to embolism, nerve involvement, the use of mercury, and infection with some necrotizing micro-organism. The last-named theory is doubtless correct, although the identity of this microbe does not appear to have been determined. Walsh^ made a careful bacteriological study of 8 cases of noma occurring in a home for children in Philadelphia. It is an interesting fact that these cases occurred during a period of two and one-half years. The diphtheria bacillus was recovered by culture from each case. Inoculation and tinctorial tests were employed to identify the Klebs-Loeffler organism. Most of the cases followed measles, but several occurred after diphtheria. Four of the cases began with ulcer- ative stomatitis. A number of the cases of ulcerative stomatitis — 15 in all — were cultured, but diphtheria organisms were not found. Walsh states that "since noma is a species of moist gangrene, requiring probably from analogy two different micro-organisms, one a saprophyte to produce putrefaction, another a parasite to produce primary necrosis, it is possible that in these cases where diphtheria bacilli are found they may be the primary causative agents. When other pathogenic micro- organisms capable of producing necroses are found, it is possible that they may be the primary excitants." The above investigation is of considerable interest, particularly in view of the painstaking manner in which it was carried out. The result, however, is scarcely in harmony with our clinical experience. W^e have observed 4 cases of fatal cancrum oris within recent years; 3 occurred with measles following scarlet fever, the other with measles alone. We have never had a case of noma develop in the diphtheria wards, although on a number of occasions measles has broken out there. 1 Dissertation, Berlin, 1873. 2 Verhandl. deutsch. Gesellsch. f. Chir., 28 Kongress. 3 Mentioned by Walsh. Diphtheria Bacilli in Noma. Proceedings of the Philadelphia Patho- logical Society, June, 1901. * Handbuch der prakt. Chir., Band i., Abth. 2. ^ Loc. cit. (JOMf'fJC'ATIONS AND HKQd NIjA': OF ATh'ASfJ'JS .017 Noma is regarded l)y Matzenauer^ as a form of hospital gangrene, fjut feebly contagious and requiring, as a rule, a severe preceding disease to produ(;e a predisposition. He discredits tlie rliplitluiria bacillus as an etiological factor, and believes the exciting organism is the same anaerobic rod-sha])cd bacillus that is found in }iosf)itaI gangrene. One fact is undoubted, that measles for some reason more strongly predisposes to the development of noma than any other affection. Babes and Zambilovici^ announce that they have discovered a very small bacillus, cultures of which injected into the cheek of a rabbit have given rise to gangrene similar to noma. The mortality of noma is frightful, about 70 per cent, of the patients succumbing to the disease. Pregnancy.— Measles in 'pregnant women is uncommon, inasmuch as most individuals pass through an attack of measles in childhood. As is true of nearly all infectious diseases, the development of measles in parturient women is apt to prematurely terminate the pregnancy. Rosch has reported a case of abortion terminating fatally as a result of measles. Incidental Improvement in Chronic Diseases After Measles.^ — Every infectious disease produces a certain systemic comraotionor change; this may favor the development of diseases to which the patient may be inclined. On the other hand, existing diseases, sometimes of long duration, may disappear after such a systemic shaking-up. Thomas has collected a number of interesting instances from which we freely quote. Behrend saw an eczema of the scalp of three years' duration, in a woman of forty years of age, permanently cured after an attack of measles. The curative influence of measles upon long-standing diseases of the skin has also been attested by Rilliet, Taupin, Guersent, and Rayer. Barthez and Rilliet saw chorea, epilepsy, and incontinence of urine of several months' duration get well after measles. According to Weisse, a girl who suffered from convulsions was entirely cured. Guersent noticed, with the beginning of the fever of measles, permanent relief from epileptiform seizures, of which the patient had had several a day for a long time. Schmidt saw a six- year-old girl, who had had daily convulsions that had so reduced her strength that death was expected, completely recover after measles. Feith and Schroder van der Kolk report the case of a woman who for five years was confined to an asylum because of violent attacks of mania, who, after measles, was cured and discharged from the institution. Hildebrandt saw an obstinate disease of the joints, which had been unsuccessfully treated for three years, promptly get well after con- valescence from measles. Schmidt noted an almost magical recovery in a five-year-old boy with contraction of the lower extremities of six months' duration. Of course, such examples of the accidental curative influence of an attack of an infectious disease are met with not only I Arch. f. Derm. u. Syph., 1902, No. 60, p. 373. a Quoted by Koger, loc. cit, p. 402. 518 MEASLES after measles, but also at times after other processes. Mention is made elsewhere of a raving maniac, confined in an insane asylum, who was completely cured after an attack of smallpox. Coincidence of Measles with Other Infections. — Measles may be complicated by- almost any of the known infectious diseases. In the association of several infectious processes measles may be the primary disease, or it may develop secondarily after some other infection. We have, on a number of occasions, seen measles complicate diphtheria and scarlet fever. We are inclined to believe that the prognosis is more serious when measles is the secondary infection than when some other disease is engrafted upon it. We have seen measles develop during convalescence from smallpox and have also observed the reverse order. In the vast majority of cases the one disease develops during the decline of the other. We have never seen measles in its early eruptive Fig. 86 Boy exhibiting eruption of measles wliich developed during convalescence from smallpox. stage complicated by a second infectious disease. Measles and whooping- cough seem to succeed each with more frequency than any other disease. Among 166 cases of measles, Bernardy^ saw pertussis develop in 21 instances. THE PATHOLOGY OF MEASLES. Skin. — At autopsy the eruption of measles is not visibla .unless ,^ ^^^.^ ^as been HfEinic extravasation into the skin. The skin has been studied histologically by Neumann, Catrin, and Unna. Neumann^ found as the chief changes a round-cell infiltration , about the l)loodvessels, hair follicles, and sweat glands. Catrin^ likewise observed a pronounced infiltration of leukocytes, but in addition, in the nodular form of measles, a series of changes in the deep epidermal cells. 1 Annals of Gynecology and Pediatrics, July, 1894. 2 Histolog. Veranderungen der Haut. bei Masern u. Scharlach, Med. Jahrb., 1882, p. 159. 3 Les alterations de la peau dans la rougeole, Archiv. de med. exper., .1891, No. 2; quoted by Unna. 77//'; I'ATIIOIJXIV O/'' Mf'JASfJ'JS 519 These consistcMl of a colloid (l(;^eneration of tin; perinuclear /one <)\' soiric of the (l('ej)-lyin^ e|)i(,heli!il (lells. Around the areas of colloid cliarige were dilated interepithelial spaces eontaininj^ coagulated fibrin and leuko- cytes. In the centre of the papule the colloid masses run together and undergo coagulation necrosis, tliis taking place in the fjrickle layer. Catrin only found emigration of leid\ocytes from the pajnllary hlcjofl- vessels at those places where the surface ej)ith('lium contained cf^lloid cells. Unna regards the colloid change and necrosis of the epithelium as the result of the direct influence of the poison of the disease upon the epidermal structures. Unna' states that in measles a spastic resistance in the cutaneous vessels is added to the primary congestive hypenemia which develops around the infection in the capillaries, and this explains the cyanotic color, the papular swelling, and the urticarial oedema of the centre, as well as the frequent escape of coloring matter of the blood. The rapidly developing spastic oxlema always collects at the place of least resist- ance, which, in children, is in the fatty tissue around the coil glands and in the sheaths of the larger vessels, the cutaneous muscles and fol- licles. The individual coils, the hair follicles, and the muscles seem to swim free in widely dilated spaces. Dilated lymph vessels and enormously distended lymph spaces are seen m the lower and central parts of the cutis. Another characteristic is the almost complete absence of a cellular exudate. Leukocytic emigration is not more than in all simple stagnatory hyperpemias, less, indeed, than in most. But a few leukocytes are found in the epithelium. During the stage of scaling, the subbasal horny layer separates itself from the basal and, with the central and upper horny layers, form the scale. The lost epithelium is replaced, as usual, by mitotic proliferation. The above description, Unna remarks, refers merely to the ordinary flat or slightly papular eruption. Mucous Membranes. — The mucous membrane of the nose, mouth, pharynx, larynx, trachea, and bronchi is the seat of a catarrhal inflam- mation. The epithelial cells undergo a colloid change and are often swollen and detached. The lymph follicles and the surrounding struct- ures are infiltrated with cells. Occasionally when the inflammation is intense the follicles may break down and form ulcers. At times such ulceration m the larynx may lead to involvement of the cartilage. Slawyk,^ in a histological study of the oral mucous membrane, found the epithelium thickened and in places undergoing fatty degeneration, giving rise to the whitish dots described by Koplik. Steiner^ observed in several cases, at autopsy, a blotchy redness of the mucous membrane of the larynx and bronchi, and Wilson, Eisenmann. Rayer, and Gerhardt saw a similar condition in the trachea and bronclii. Heyfelder,^ one of the older writers, describes an eruption similar to that on the skin in the duodenum, jejunum, and, at times, in the stomach 1 Histopathology of the Skin, translated by Dr. Norman Walker, 1900. ' Deutsch. med. Wochenschrift, April 28, 1898 ; quoted by Corlett. * Quoted by Thomas, loc. cit., American edition, p. 72. * Quoted by Thomas. 520 MEASLES and ileum; this has been noted also by several other observers. More recently Steiner^ mentions a blotchy redness of the intestinal mucous membrane occurring in children dying during the eruptive stage. According to Worthington/ the lymphatic follicles and Peyer's patches of the bowel may undergo destructive ulceration, leading even to perfora- tion. Thomas says that Fuchs saw, upon the genital mucous membrane, numerous red, somewhat puffy spots overspread with mucus. This observation was likewise made by Henoch and Chomel. Lymphatic Glands. — ^The lympha,tic glands are enlarged in measles,_ but to a less extent than in scarlet fever. When bronchopneumonia Ts ■present the tracheobronchial glands may be found distinctly swollen. In a certain proportion of cases the glands show evidences of tuberculosis. Loomis, Pizzini, and Kalbe^ found tubercle bacilli in apparently normal tracheobronchial glands; the last-named observer noted the presence of these bacilli in 8 per cent, of apparently healthy glands. It is suggested that these lie dormant until an attack of measles or some other affection involving these glands stimulates the tuberculous process to activity. Lungs. — Bronchopneumonia is present in a large proportion of the fatal cases. The process is not essentially different from that observed in bronchopneumonia independent of measles save that there is a more pronounced tendency in many cases to suppuration. It is not rare for the pulmonary trouble to eventuate in tuberculosis, exhibiting usually the form of a caseous pneumonia. Cornil and Babes* have described a peripneumonia which occurs early in the so-called suffocative cases, and which they regard as peculiar to measles. It begins in the lymphatic tissue, involves the interlobular and interalveolar structures, and leads to fibrinous exudation into the air vesicles. StiebeP speaks of a blotchy redness of the pleural membranes which he observed in four autopsies. They were sharply contoured, red spots, apparently situated just beneath the pleura on both sides. Roger observed a purulent pleurisy during convalescence from measles in a five-year-old child. The sfleen is moderately swollen in measles, although this is more often determined at autopsy than at the bedside. Liver." — Freeman'' found focal necrosis of the liver in 4 out of 14 g^Utopsies on measles cases. The larger areas of necrosis are visible to the naked eye and may be confounded with tubercle. Microscopically there is a sharply circumscribed roundish area of necrosis in which the cytoplasm fails to stain, and fragmentation of the nuclei is seen. The condition is due to the local action of bacterial toxins. Blood. — In uncomplicated cases of measles the condition of the ; blood is unaltered. Fibrin may be increased when the catarrhal symp- toms are severe. 1 Quoted by Thomas. - Quoted by Dawson Williams. 8 Mentioned by Roger, loc. cit., p. 1004. * Quoted by Williams, loc. cit. 5 Quoted by Thomas, loc. cit. 6 Result of Work at the New York Foundling Asylum. Archives of Pediatrics, February, 1900, and New York Medical Record, 1898, vol. liv. TIIK BA(JTI<:h'l()l/)(!V Oh' M/'LASfJ-JS 521 The number oi red cdls is nof, strikingly reduced in mild or moderate cases, and may at times be actually increase;*!. In 8 cases Felsentlial counted from five to five and a half million eorjjuscles. I'lie h;/'mo- globin is likewise slifijhtly or not at all reduced. The v^hifc r.rlh not only are not increased in measles, but they are often reduced below tlie iiormal. In 8 cases Rieder noted an average of 7500 cells, the leukocytes being least numerous at the height of the disease, and increasing as the fever disappeared. Cabot^ states that during convalescence the lymphocytes and especially the large mono- , nuclear forms are increased. According to Coombe, uniform changes occur in the blood in the incubation period. Coonibe^ ^^J^.} "In the incubation period of measles tliere is a hyperleukocyfosis M'ithout other symptoms. Tliis is a constant siii;n of the inc.ubation period. During the last two days of the period of invasion or exanthem, and throughout the entire period of the *e:tanthem:, there is a hypoleuJcocytosis." '-■ These alterations are due to the change in the number of the poly- morphonuclear neutrophiles. These observations were confirmed by Platenga,^ Avho also found similar changes in rubella. The eosinophile cells are usually decreased or normal in number. Cabot found the differential counts normal; Felsenthal found the poly- morphonuclear cells much increased and eosinophiles never over 1 per cent. In cases in which the diagnosis between scarlet fever and measles is obscure, a differential blood count should 1)6 of distinct value. On the other hand, the examination of the blood is of no particular value in differentiating measles from rubella (rotheln), inasmuch as the cellular constituents are much the same in the two diseases. THE BACTERIOLOGY OF MEASLES. The extreme contagiousness of measles is proof of its microparasitic origin; some reservation must, however, still be expressed as to the etiological relationship of the organisms thus far described. Braidwood in 1878 called attention to a bacillus which he found in measles and which he regarded as the cause of the disease. Lombroso* described cocci in the rete mucosum of the measles spots. Similar bodies were found by von Leyden and Fiirbringer. In 1892 Canon and Pielicke found in 14 cases of measles a bacillus which they considered to be the specific causative agent. The discovery was made possible by a special method of staining.'^ The organism was variable in size, sometimes quite small and resembling a diplococcus, i Clinical Examination of the Blood, fourth edition, New York, 1901. » Archiv. de med. des enfants, 1903. ^ Archiv. de nied. des enfants, March, 1903. * Lo Sperimen., 1884, x. 5 Stain for the bacillus of Cauou and Pielicke. Blood is thinly spread upon a clean cover-glass and fixed by five to ten minutes' immersion in absolute alcohol. Then stain with the following solution and incubate at 37° C. for from six to twenty-four hours : Concentrated aqueous solution of methylene blue, 40 ; 0.25 per cent, solution of eosin in 70 per cent, alcohol, 20 ; distilled water, 40. 522 MEASLES and other times as long as a red blood cell. It was present in the blood, sputum, and secretions of the nose and eyes throughout the entire disease, but disappeared when convalescence set in. The bacillus could be grown on bouillon, but on no other media. Czajkowski^ found a bacillus in the blood and mucous secretions of 50 cases of measles, which was apparently identical with that above described. It grew, however, on various albuminous media, especially blood serum and glycerin agar, but not on gelatin and plain agar. Inoculations of mice produced a fatal septicsemia. Gregorieff, in an examination of the blood in 13 cases, found the bacillus in each case, and grew it in bouillon in 10 instances. Josias^ failed to find this organism in a study of the blood and secre- tions of 24 cases, and Barbier and Warschovsky also obtained negative results, the latter examining 21 cases. Arsamakor,^ in an examination of 665 cases of measles, found in the blood and mucous secretions, grouped, rod-shaped bodies, 5 to 6 microns in length, having bulbed extremities. In 1900 Lesage* published the results of a study of 200 cases of measles. He found a delicate micrococcus which grew best on gelose (agar), took stains slowly, and was decolorized by Gram's method. The cultures bore a resemblance to those of the pneumococcus. The organism was found constantly in measles, but was absent in 25 cases of scarlet fever and in 45 normal children. In 53 children who had had measles previously it was found twice. Rabbits were inoculated with blood and nasal secretions in many cases, and measles apparently reproduced in nearly all. Von Niessen^' examined the blood during the height of the measles exanthem and found a bacillus which in some respects resembled that of Canon and Pielicke. It produced, however, rose-colored colonies on gelatin and grew well also on glycerin agar, bouillon, and potato. He designated this organism "bacillus roseus." In 1891 Doehle^ found in the blood of 8 cases of measles certain bodies which he regarded as protozoa. In fresh blood they were observed not only in the plasma, but also in the red blood corpuscles. After the eruption appeared the bodies became visible almost exclusively in the red cells. They were from a half to one micron in diameter and exhibited an opaque nucleus with a surrounding clear zone. Later larger oval bodies with two nuclei were seen. More recently Weber^ has detected bodies in the blood which he regards as protozoa. From the above divergent findings it is evident that further research is necessary before any of the organisms described can be accepted as the specific cause of measles. 1 Centralbl. f. Bakt. u. Parasit., 1895, Nos. 17 and 18. s La medecine moderne, Paris, June 2, 1902. 3 Article abstracted in Revue de miSdecine, 1899, vol. xix. p. 561. 4 Bulletin de la Soci^tt^ des hOpitale de Paris, March 15-22, 1900. 6 Arch. f. Derm. u. Syph., 1902, vol. Ix. p. 429. 6 Centralbl. f. allgem. Path., etc., 1892, iii. p. 150. 7 Centralbl. f. Bakt. u. Parasit., 1897, vol. xxi. p. 286. 77//'; l)fA(JN()S/S (}/<• M/'JASfJ'JS f/Z' THE DIAGNOSIS OF MEASLES. It is a mii.ll<'r of f^rciU, iinporlfuicc, pjuliciihirly in iiishtutioiis for cliiMnMi, tlia-1, t])v. stablislied. The existenee of an epidemic of measles or knowled(i;(; of ('xpf)sure to th(^ disease will y;ijt the physician on guard and often enable hiin to make a diagnosis, or at least strongly suspect it, upon the first development of catarrhal symptoms. The statement is erjually true of measles and smallpox, that the diagnosis cannot be indubitably made before the appearance of the eruption, although when all of the invasive symptoms are typi- cally developed, when there has been exposure to the disease, and, particularly when the characteristic buccal enanthem is present, the diagnostic probability approaches almost to a certainty. _As in small- pox. th^ v;^cci nal condition of the patient often constitutes information o f impo rtant diagnostic value, so in measles does the history as to p-e vioiTs'allacks . It.js generally agreed that second attacks of measle.s. are of great rarity. In a doubtful case, an authentic history of a pre- vious attack, of measles would constitute strong presumptive evidence against the rubeolous nature of the disease under consideration. While the diagnosis of measles is usually announced when the eruption appears, it must not be thought that the rash is in itself all-sufficient evidence. The eruption of measles is merely its most conspicuous manifestation. T^ P ,g!he,.:-.: ,--.«-u..:*,-.-,„,._. ,.^., , :,■- The catarrhal symptoms affecting the eyes and respiratory passages, which are so constant in measles, are, absent in smallpox, at least dur- ing the prodromal stage. CJose^inspection of the mouth in smallppj^ may reveal the presence upon the soft palate of rounded, glistening, pinhead-sized, reddish elevations, but these differ considerably from the bluish-red spots on the buccal mucous membrane in measles. The maculopapules of measles are soft and velvety to the touch, as compared with the firm, shotty character of the smallpox papules. Fig. 87 Smallpox on the second day of tlic erupLioii, prcscntiiiL measles. resemblance to the eruption ot The sweep of an experienced hand over the skin will often suffice to differentiate the two diseases. Where there is doubt, twenty--fouiJiauxs,' ^^ay will dispel all uncertainty, for by this time the eruption of measle s will have become flatter and more diffuse, and the papules of smallpox firmer and xnore distinctly elevated. The prodromal morbilliform rash, the so-called roseola variolosa, may be confounded with measles. This eruption occasionally develops in mild cases on the second day of the invasive stage. The lesions are non-elevated, irregular in distribution, of brief duration, and unaccom- panied by catarrhal symptoms. Typhus Fever.— During the epidemic prevalence of typhus a con- founding of this disease with measles might take place when the eruption 77//'; l)fA(,'NOSlS OF MKAS/J'JS .027 is profuse. Pastau is (jiiofcd hy Tlioinas as saying' fliat. tlif exanflicrn of typlnis is by no incjiiis rjircly papiihir or even li(!inorrhaf^i(; like that of measles, arid a catarrhal afiectioti of the air passaf^es, especially of the trachea, is one of its usual concomitant symptoms. The fever and nervous symptoms are more pronounced in typhus and there is {^reat enlargement of the sj)leen; the eruption is usually absent on the face, and oculonasal catarrh is lacking. We recall a case of atypical measles which was sent to the Municipal IIosj)ital as a ca.se of typhus by one of the foremost physicians of this country. Roseola Syphilitica. — The macular eruption of syphilis has on more than one occasion been confounded with measles. The error of mis- taking syj)hilis for measles may be made when the ))atient is an adult and when the febrile symptoms are mild. On the other haufl, syphilis with pyrexial elevation might be regarded as measles. The eruption of syphilis is slower in development and the lesions are much more uniform in size and distribution. The face is but slightly, if at all, involved. Usually the initial lesion or the hardened remains thereof can still be discovered. In addition otlier evidence of the syphilitic infection maybe present, such as mucous patches, pronounced inguinal adenopathy, etc. Morbilliform Erythemata. — There are a number of conditions in which rashes bearing a more or less close resemblance to that of measles may occur. They may be divided into: (a) accidental rashes accom- panying the exanthematous fevers, (6) drug eruptions, and (c) serum eruptions. Mention has already been made of the resemblance of the roseola variolosa to measles. An analogous eruption, roseola vaccinosa, develops occasionally about the tenth day of vaccination. The same features which have been referred to as distinguishing the variolous roseola from measles may be applied to the vaccinal rash. jNIorbilliform rashes may in rare instances be observed also in the course of varicella, scarlet fever, and other infectious diseases. Drug Eruptions. — The drugs which most frequently give rise to eruptions simulating measles are antipyrin, quinine, chloral, copaiba, and cubebs. The most common eruption resulting from the administration of aritipyrifi is a morbilliform erythema. Of 52 instances of eruption from the use of antipyrin collected by Spitz, 41 were of the measles type. The eruption may be generally distributed over the trunk and extremi- ties or it may be limited to certain regions thereof; an important distin- guishing feature is that the face is usually exempted. Croker states that these eruptions may be accompanied by oronasal catarrh. The d ifficulty , in d iagnosia may be increased by the appearance of the anti- pyrin eruption following catarrhal symptoms, such, for instance, as are "eficountered in influenza, for which, the drug is administered. The con- jtmctrvTtis, photophobia, hoarseness, cough, and buccal eruption are all absent. Fever, when present, is slight and not characteristic of measles. Furthermore, the normal progression of the measles exanthem from the 528 MEASLES face and neck gradually downward will be found lacking. The eruption, moreover, is apt to be non-elevated and exhibit irregularities as to dis- tribution. If a large dose of antipyrin has been taken the drug can be found in the urine by testing the same with the perchloride of iron. Quinine. — Quinine gives rise not infrequently to erythematous erup- tions. Of 60 quinine eruptions analyzed by Morrow, 38 were of the erythematous variety. Most of these are of the scarlatiniform type, but some resemble measles. The rash may develop after the admin- istration of as small a quantity as a grain or even a fraction of a grain of the drug. The idiosyncrasy appears to be most frequently observed m women. Fig. SS A morbilliform eiythema somewliat resembling measles, probably due to intestinal autointoxication. The eruption may be generally distributed or limited to certain areas. It sometimes appears first on the face, spreading thence downward over the trunk and limbs. The lesions are bright or dull red macules or papules, which may quite strongly resemble the measles exanthem. Itching is apt to be a more prominent symptom than that accompanying measles. Desquamation not infrequently follows. In some cases febrile symptoms are present at the beginning; there may be a fever of 101° or 102° F., with headache, nausea or vomiting, and weakness. Catarrhal symptoms are absent. Eruptions from the administration of chloral are less common than those after antipyrin or quinine. Gee^ saw two cases in which there was 1 Quoted by Crocker, Diseases of the Skin, American edition, 1903, p. 483. 77//'; /'/>'()(,' NOSIS OF Mh'ASIJ'JS rj29 a dusky-red, papulnr eruption surrounded hy ;i more difl'use redness of the face and neck, and pateliy or mottled-re(J sj^fjts on the extremities, especially about the articulations. The absence of the catarrhal and constitutional manifestations of measles would enable one to exclude this infection. Coj'AHiA and CiiiiKHS. — C!opaiba and cubebs may give rise to scarla- tiniform or morbilliform rashes. The former (h-ug usually })roduces an eruption consisting of rose-red colored, slightly raised patches, which may be discrete or blotchy and generalized or limited. About the elbows and knees there is a tendency toward confluen(;e of tjje patches. Itching is apt to be a distressing symptom. The erui)tion may develop rapidly after the administration of the drugs or only after some days have elapsed. Most of the eruptions have occurred in persons who were receiving treatment for urethritis. A peculiar and disagreeable balsamic odor is often imparted to the skin when copaiba is taken. All of the drug eruptions are apt to exhibit irregularities as to the manner, rapidity, distribution, or duration of the eruption which will arouse suspicion as to its nature; furthermore, the prodromal stage of measles with its characteristic catarrhal symptoms is wanting. Antitoxic Sera. — Antitoxic sera occasionally call forth eruptions which are measles-like in character. Diphtheria antitoxin may now and then give rise to a morbilliform erythema, although much more commonly the eruption resembles urticaria or exudative erythema. Antitoxin rashes may develop at any time from three days to three weeks after its administration; most rashes, however, appear from eight to fourteen days thereafter. There may be elevation of temperature with joint pains and occasionally joint swellings accompanying the eruption. The temperature may rise suddenly to 102° F. or thereabouts, but it soon falls. Catarrhal symptoms are invariably absent. The antistreptococcus serum and antitetanic serum may, on rare occasions, also give rise to morbilliform eruptions. THE PROGNOSIS OF MEASLES. It appears to be a -difhcult matter to dispel from the minds of mothers the idea that measles is a trivial disease. When it is stated, according to the Twelfth Census Report, that measles in the United States, in the year 1900, caused 12,866 deaths, more- than twice the number that re?MiEed"lfom scarlatina, it is evident that this disease is not essentially "beniOTTin its outcome. The above statement must not be construed to mean that measles is more dangerous than scarlet fever, but that, attack- ing as it does a much larger percentage of humanity, the aggregate loss of life is greater. The prognosis of measles in vigorous and well-nourished children beyond the age of tw^o or three years is extremely favorable. The factors that exert an important influence upon the prognosis are the age of the patient, his previous health, and the nature of his surroundings. Season and climate are thought to exercise some influence upon the disease and its complications. 34 530 MEASLES Age. — The age of the patient is the most important factor in estimating the degree of danger attendant upon an attack of measles. During the first six months of Kfe infants usually resist the infection of measles altogether or take it in feeble form. "With this exception, children under two years of age who contract measles have a dangerous disease to contend with. Holt states that the average mortality from measles during this period is not far from 20 per cent. After the third year of life the danger rapidly diminishes, reaching a minimum after the age of five has been passed. The following figures of Tripe^ indicate the relation of age to mor- tality. Mortality of Measles in England from 1868 to 1872. — In 1000 fatal cases the age of the patients was: 0-1 year . . 200 cases. 5-15 years . . 72 cases 1-2 years . . 376 " 15-25 " . . 3 " 2-3 " . . 190 " 25-45 " . 4 " 3-4 " . . 101 " 45-60 " . . 1 case. 4-5 " . . 53 " Over 65 " . . " It is thus seen that about three-quarters of the deaths occurred in children under three years of age. Dawson Williams states that in the forty years from 1848 to 1887 there were in England and Wales 367,602 deaths attributed to measles, and of this number 335,874 occurred in children under five years of age, leaving only 31,728 to distribute among other ages. The best opportunity of judging of measles susceptibility and fatality at the various ages is afforded in studying an entire epidemic in a locality. Dr. Theodore Thomson^ presents such a table of an epidemic in an English town, from which the following data are abstracted : Measles Age. Population, attacks. Deaths. Mortality rate. 0-1 year 1-2 years 2-3 " 3-4 " 4-5 " 5-10 " 10 years and upward At all ages . This table indicates the lesser susceptibility of infants under one year of age and also the lower death rate as compared with the next two years. During youth and early adult life the mortality from measles is low. Patients who are advanced in years not infrequently succumb to the disease. This is shown in Panum's^ report of the Faroe Islands epidemic of 1845. . 1155 166 16 6.9 per ct 974 233 46 23.6 " . 1028 354 36 J7.5 " . 1000 324 16 8.0 " 951 324 5 2.6 " . 4530 560 6 0.7 " . 25,968 39 0.0 " . 35,606 1031 125 1.7 " 1 Quoted in Jahrbuch f. Kinder., vol. ix. p. 412. » Loc. cit.,p. 287. 2 Quoted by Williams, loc. cit. TIIM PROGNOSIS OF MEASLI'JS 531 Mortality Rate of Mrahmos in tiik Farok Ihi>ani)8 in 1845, Age. Mortality rate. Ak';. Mortality rate. Under 1 year . 30.0 per ct. 40-60 years . . 2.8 per ct. 1-10 years 10-20 " 20-80 " 80-40 " 0.6 " 60-60 0.4 " 60-70 0.75 " 70-80 2.1 " 80-100 4.5 7.8 Kll 26.1 These figures are unusual in that such a great mortality is shown in infants under one year of age and such a remarkably small dfath rate in those between one and three years. The increasing mortality in patients past the age of forty is well illustrated. In an extremely mild epidemic in the Faroe Islands in 1875, Hoff states that while only 8 out of 1123 cases ended fatally, 5 of these were vigorous adults between the age of twenty and thirty years. This must be regarded as an exceptional circumstance. Institutional Epidemics. — It will be found convenient to discuss here the influence of institutional environment upon the mortality rate of measles. It is a generally recognized fact that measles occurring among children in homes, nurseries, asylums, hospitals, etc., is much more fatal than when it develops among children in their private homes. Indeed, measles is regarded as the scourge of children's institutions, for it decimates the little patients like a plague. There are a number of reasons for this. Such children usually come from poor stock and therefore lack power of resistance. The children in foundling a.sylums, nurseries, and hospitals are of a tender age, which in itself accounts for a high mortality. They are usually frail and in poor health or already perhaps suffering from an acute or a chronic disease. The atmosphere is often vitiated and infected and the liability to such complications as pneumonia and diphtheria is increased. The mortality in such institutions as have been mentioned is often frightful. Holt speaks of an epidemic in 1892 in the Nursery and Child's Hospital in New York in which there were 143 cases with a death rate of 35 per cent. An epidemic in the same institution in 1895 had an almost identical mortality rate. Comby gives the following statistics showing the death rate in some of the Paris hospitals: Hospice des Enfants Assistes. Year. Cases. 1882 . . 280 1883 268 1884 328 1885 . . ~ 370 1886 .i29 Total in five years .... 1575 728 46.22 The death rate, therefore, during these five years was nearly 50 per cent., a truly appalling figure. In I'Hopital des Enfants Malades, for a period of seven years from 1882 to 1888, there were treated 2585 cases of measles, with a death rate of 40.15 per cent. Deaths. Percentage 128 45.0 128 47.0 187 57.0 147 46.0 138 42.0 532 MEASLES In I'Hopital Trousseau, from 1882 to 1886, there were 907 cases of measles, with a mortaHty rate of 25.02 per cent. From 1890 to 1894 there were 2248 cases treated in special isolation pavilions, but the mortality rate still remained high — 28 per cent. It is difficult , to obtain accurate information as to the death rate of measles in private practice, for while the deaths are recorded the number of attacks is usually not known. The fact is well established, however, that the fatality is very much less in this class of patients. Sex does not influence the mortality from measles. Of 12,866 persons who died of measles in the United States in 1900, 6231 were males and 6635 were females. The frequency of measles in pregnant women is not sufficient to disturb the balance. Moreover, the infection of measles superadded to pregnancy is not as serious as some of the other exan- thematous diseases, notably scarlet fever and smallpox. Previous Health of the Patient.^ — Measles as a primary disease is very much less serious than when it becomes engrafted upon some other acute or chronic affection. Secondary measles is an extremely fatal disease; occurring in patients who are convalescing from diphtheria, scarlet fever, whooping-cough, etc., the danger is greatly enhanced. The mortality is also high when measles attacks children who are badly nourished and who are scrofulous or anaemic. In those with enlarged glands and a tendency to pulmonary tuberculosis an attack of measles may be sufficient to stimulate this process into activity. The unfavorable influence of hardship and privation is exemplified in camp measles, which is nearly always characterized by a high death rate. Character of Epidemic. — The mortality of measles depends much upon the severity of the prevailing epidemic. At times the type of measles is unusually mild and the death rate extremely low; some epidemics, on the other hand, are characterized by special malignancy. Fatal epidemics of measles may cause a high mortality, not only through an excessive development of the regular symptoms of the disease, but through the frequency of serious complications. Indeed, it is the frequency or rarity of bronchopneumonia during an epidemic that determines in a large measure its malignancy. The average mortality of measles is from 4 to 6 per cent. The deaths may in some epidemics not exceed 1 or 2 per cent., while in others they may reach the murderous figures of 20 or 30 per cent. In 1856, in Lippe, Hungary, a malignant epidemic prevailed, destroy- ing the lives of 50 per cent, of those attacked. Measles again occurred in this locality thirteen years later, with a mortality of 3 per cent. Faber states that at Schorndorf in the epidemic of 1827-28 there were 2100 cases of measles, with a mortality of only 1.8 per cent. Among other mild epidemics may be mentioned the following, quoted by Thomas : According to Ranke the mortality in four epidemics in Munich varied from 0.7 to 2,7 per cent. Kostlin reports a mortality in Stuttgart of 1,8 per cent, for the years 1852 to 1865, Among severe epidemics (according to Thomas) may be mentioned the fatal epidemic in the district of Zolkiew in 1840; Seidl mentions that Cases. JJealhH. I'ercentagc. 582 139 27.7 45 13 28.8 125 40 32.0 457 1G8 36.7 TUIi l'J{()aNOS/S O/'' M/'JASLh'S 533 out of 1519 cases there were 196 deaths, a mortality of almost 13 per cent. Accord irif^ to Schiiz measles f)revailed at Nagold with a mortality of 10 per cent. Small (!f)idemics in certain localities have been accom- {)anie(l by even hipjher mortality. Colin^ gives the following figures: Year. J.ocalities. 1861 . . . . . Ruelle 1864 Arras 1860 Val-de-Grace 1870 BicCtre A mahgnant e})idemic raged in Sunderland, England, in 1885. Harris^ states that of 1316 cases 384 died, giving a mortality of 20 per cent. Measles often manifests unusual malignancy on reaching a virgin soil, particularly among savage tribes. It is stated on the authority of d'Alves that 30,000 Indians perished from mea.sles along the banks of the Amazon River in 1749-50. In 1806, in Madaga.scar, 5000 persons are said to have succumbed to the disease in a single month. Among the Fiji Islanders measles has exhibited as high a death rate as 30 per cent.; the disease has, as might be expected, inspired a wholesome dread among the natives. Season and Climate. — Inasmuch as the mortality of measles is greatly influenced by the frequency of pneumonia, one would naturally suppose that this complication would be more common and the death rate consequently higher in the cold and inclement seasons of the year. But such an assumption is not entirely borne out by facts. The figures which are published by writers as to the influence of season on measles mortality lack uniformity and preclude the possiblity of drawing there- from satisfactory conclusions. Deaths from Measles in England and Wales by Quarterly Periods. Quarterly Periods. 1837. 1838. 1839. 1840 January, February, and March 2022 2074 2836 April, May, June 1512 3204 2641 July, August, September . . 2362 1037 2767 1739 October, November, December . 2392 1943 2892 2110 Total deaths .... . 4754 6514 10,937 9326 Gregory, who publishes the above table, remarks that "season would appear to have less influence on the mortality of measles than might have been anticipated." According to Karajan,' measles occurring in lower Austria in 1862, during the presumably unfavorable cool months, was attended with a mortality of only 2.29 per cent., whereas the disease prevailed in the same district during the following summer with a mortality which reached 6.29 per cent. Passow* states that the fatal cases of measles in Berlin from 1863 to 1 Quoted by Comby. - Lancet, April 30, 1887, p. 970. 3 Quoted by Thomas, * Quoted by Thomas. 534 MEASLES 1867 were distributed as follows: winter, 41.4 per cent.; autumn, 33.4 per cent.; summer, 13.3 per cent.; spring, 11.9 per cent. In the United States the most fatal season from measles would appear to be the late winter and early spring months. In the city of New York, during a period of fifteen years from 1830 to 1844, in which time 2104 deaths from measles occurred, the seasonal mortality was as follows: January, February, March 610 deaths. April, May, June 574 " July, August, September 536 " October, November, December 384 " It is thus seen that the highest mortality was in the first three months of the year and the lowest in the last three. The United States Census Report for the year 1900 shows that the greatest number of deaths from measles occurred during the months of February, March, April, and May. Comparative Pboportion of Deaths in Each Month pee 1000 Deaths IN the United States for the Year J 900. January . . 95.0 July . . 48.5 February . . 150.1 August . 43.6 March . 176.0 September . . 34.7 April . . 146.8 October . 25.5 May . . 130.3 November . . 34.6 June . . 66.4 December . . 48.5 Climate doubtless has some influence upon the mortality of measles. Gregory says that "in hot countries measles is not viewed with alarm, evidently from the absence of thoracic complications." It occurs to us, however, that the greater tendency to intestinal complications might counterbalance the advantage. The mortality of measles varies in different localities. It is, as would be expected, greater in large cities, where there are greater numbers of overcrowded poor than in rural districts. Even in large capitals a considerable discrepancy in the mortality exists. Thus the mortality from measles is much greater in London than in Berlin; this is strikingly shown by the following figures: Measles Deaths per 10,000 of Population. Year. Paris. London. Berlin. Vienna 1880 to 1889 . . 52 60 30 00 1890 " 1894 . . 41 77 20 70 1895 .... . 26 59 17 49 From a consideration of the above remarks it will be seen that many factors influence the prognosis; chief among these, however, are the age of the patient, his general health and environment, and the severity of the epidemic. Those epidemics which furnish the largest number of anomalous cases and the greatest percentage of serious complications are most to be feared. ,B,,«*a***«'^«s?iBronchopneumonia causes nine .oiil^ ten deaths from measles. It is the principal danger to which measles patients are liable. Holt states THE TREAT Ml': NT OF Mf'JASLES 535 that of 51 fatal cases of measles 45 were due to bronchopneumonia, 4 succumbed to ileocolitis, and 2 to membranous laryngitis. Among 36 deaths observed by Northrup,' in an epidemic in the New York Foundling Hospital, bronchopneumonia was found post-mortem in 31 cases. Favorable Symptoms. — The symptoms of measles are favorable when the initial temperature is moderate, not exceeding 103° F., and when it remits in the pre-eruptive stage; when the temperature declines witli the beginning fading of the eruption; when the eruption is discrete, well developed, and of bright color; when it appears about the fourth day and progresses gradually over the body; when the catarrhal symptoms are of moderate intensity; when complications are absent. Unfavorable Symptoms. — It is unfavorable for the initial temperature to be very high (above 103° F.), or for it to persist high or increase be- fore the eruption appears. It is ominous for the fever to remain high after the rash fades, for this usually portends pulmonary complications. It is unfavorable for the eruption to appear late, for it to be unusually profuse or confluent or, on the other hand, sparse, pale, and livid. A partial or poorly developed eruption with high fever is a bad sign. Hemorrhagic eruptions are usually of evil portent, especially when accompanied by hemorrhages from the mucous membranes. Sudden and premature recession of the eruption indicates cardiac weakness. Convulsions or other marked nervous symptoms, severe diarrhoea, persistent hoarseness, with difficulty in breathing or continued high temperature, indicate serious complications. THE TREATMENT OF MEASLES. In discussing the treatment of measles it must be remembered that we are dealing with a disease which is far from trifling in its nature — one whose aggregate annual mortality exceeds, at the present day, that of any eruptive disease, not excluding smallpox. In 1889 there were 14,732 deaths from measles in England and Wales; in 1900 the mortality from measles in the United States was 12,866. These figures are not far from representing the average annual mortality in these countries. We have no doubt that at least 100,000 persons, chiefly children, perish throughout the world each year from measles. The subject is, therefore, of sufficient importance to warrant a full consideration of the prophylactic treatment of measles and its relation to the community at large. Prophylaxis — That the spread of measles can be greatly lessened by proper sanitary measures has been shown by the results accomplished by the Michigan State Board of Health.^ Public health measures may be considered under the headings of (1) Notification, (2) Isolation, and (3) Disinfection. 1 Medical News, 1897, vol. Ixxi. p. 817. " Baker, Reports and leaflets on the Prevention and Restriction of the Infectious Diseases, etc., 1900. 536 MEASLES Notification. — There is considerable difference of opinion as to the benefits derived from making measles a notifiable disease. Bearing in mind the fact that measles in many countries kills more children than scarlet fever and diphtheria combined, there can be but one point of view as to the desirability of checking its ravages. It is only through a knowledge of the distribution and extent of measles that health authorities are enabled to direct measures against its spread. How effective such measures are offers latitude for discussion. The chief difficulty arises from the early communicability of the disease. As soon as a patient manifests the first symptom of measles, those who have been exposed and are susceptible are almost sure to contract the disease, and isolation, as far as these persons are concerned, is too late. Infection may at times take place even before the patients sicken, as is illustrated in the following cases mentioned by Dr. Fenton, Medical Officer of Health for Coventry, England:^ "Thirteen children attended a dancing class one afternoon, including 3 of my own and 2 of a friend, who had just arrived in the district, and who had been exposed to the infection of measles before arriving. These 2 children came to my house and spent the evening in my presence. There was nothing to attract my attention to their condition, and, indeed, so well were they that they had walked six miles in the morning, had danced in the afternoon, and walked home about one mile at night. Next day they both sickened and developed measles. Of the remaining 11 children 2 were presumably immune, having previously suffered from measles, but the whole of the 9 developed measles during the following fourteen days." This incident is evidence of the early con- tagiousness of measles and the difficulties that are encountered in pre- venting its dissemination. But much can be accomplished in prevent- ing unnecessary exposure to the disease, and to this end notification is eminently desirable, if not essential. The education of the masses is a matter of paramount importance in stamping out measles. Mothers must be taught that measles is a serious disease — a disease that destroys many lives, and that exposure to it must be avoided. Even among the intelligent middle classes there is a tendency to regard escape from measles as futile, and mothers make little effort to avoid an infection which is regarded after all as inevitable. "The baby might as well take measles now as later" is the dangerous and erroneous view often expressed. Mothers should be made to realize the fact that measles kills more children under two years of age than any other disease save possibly whooping-cough, and that about 80 per cent, of all deaths from measles are in children under five years of age. If children be safely guarded through this period of their life without contracting measles an enormous saving of life would result. It is a good plan to send circulars of instruction to all households which are in the neighborhood of an infected domicile. 1 Quoted by Dawsbn Williams. THE TUKATMKNT OF MEASLES 587 Isolation. — When a child is stricken with measles in a househokl in which there are other susceptible (children it should be promptly isolated. The isolation should not be delayed until the dia^niosis is confirmed by the ap])earance of the eruption, but uj)Om the first suspicion that the disease mi^ht be measles. In selecting an apartment for the patient such a room or, preferably, a suite of rooms is to be chosen as can be most effectually separated from the rest of the house. It will usually be found that the uppermost rooms of the house are most suitable and available. In choosing the apartment care should be given to the facilities for ventilation. Admir- able ventilation is furnished by an open fireplace in which fire is kept constantly burning, but such a convenience will usually be found wanting. The most common method of securing the necessary change of air is from a window sufficiently removed from the sick-bed to avoid direct currents of air striking the patient. A rather safer method, particularly in such a disease as measles, is to ventilate through the adjoining room, as suggested by J. P. C. Griffith.^ The windows of this room may be kept open and the fresh air permitted to enter the sick- room through the communicating door, which is opened for this purpose from time to time. As this room also forms the channel of communica- tion with the remainder of the house, the opening of the windows will tend to dilute or dissipate the infection. All unnecessary articles of furniture, such as drapery, carpets, and upholstery should be removed. The spaces around doors communicating with parts of the house to be protected should be sealed by pasting strips of wrapping paper over them. The contagium of measles is so diffusible that unless this precaution is taken the infection will travel beyond the sick-chamber. Over the door leading into the corridor should be suspended a sheet which is kept moist with diluted Labar- raque's solution, carbolic acid (5 per cent.), or a 1 : 1000 solution of corrosive sublimate. The woodwork and the floors of the apartment should be kept clean by mopping with cloths saturated wdth antiseptic solutions. Owing to the liability to pulmonary complications in measles, sweeping of the sick-room should be assiduously avoided. The nurse or attendant should not leave the sick-apartments save after change of clothing and thorough ablution. If the mother wait upon her child she should devote her time exclusively to the patient, and not come in contact with susceptible members of the family. Such garments should be worn by the nurse or mother as can be readily washed. All articles coming in contact with the patient, such as dishes, bed and body linen, etc., should be disinfected in the adjoining room, where solutions for this purpose should be kept on hand. A 5 per cent, solution of carbolic acid will suffice for this purpose, although for the dishes boiling water is to be preferred. 1 Hare's System of Practical Therapeutics, p. 132. 538 MEASLES It is a difficult matter to state just how long measles patients should be isolated. Unlike scarlet fever the disease is most contagious early, and the period of infectiousness is short lived. Most pediatricians are of the opinion that the period of isolation should be in all from two to three weeks. In uncomplicated cases two weeks are probably sufficient if desquamation has ceased. Whether or not the desquamation of measles is infectious is an undetermined problem, with plenty of advo- cates to champion each side of the question. It is proper to state that certain physicians who have had unusual opportunities of judging, such as Hoff, Peterson, and Comby,^ deny the infectiousness of the stage of desquamation. The last-named observer says: "We know to-day that measles ceases to be contagious after the eruption." In institutions where so much depends on effective isolation, patients should be sepa- rated for the full period. Utility or Futility of Isolation. — There are many physicians who deem isolation in private residences futile and, therefore, do not advise it. It must be admitted that when measles appears in a child to whom susceptible children have been freely exposed, isolation is too late. If, however, patients are isolated upon the first suspicion of measles, a certain small proportion of the exposed will probably escape, particularly babies, whose susceptibility is slight and whom it is par- ticularly important to protect. Where such young infants can be sent to another household this course is eminently desirable, provided no susceptible children be there resident. It is unjustifiable to send exposed children to a home where unprotected persons reside, for these in turn would be exposed upon the former falling ill. It is, of course, recognized that the method of isolation above outlined could not be carried out among the poor nor in families living in re- stricted quarters. Moreover, there are many people who would refuse to go to such inconvenience and expense, with the knowledge that the benefits to be derived are doubtful. We feel that when measles breaks out in a household in which unprotected persons, particularly children under three years of age, live, the proper course to pursue is to isolate the patient. Such a procedure would, in the long run, save lives. When measles develops in an institution for children, the patient should be immediately isolated. No new admissions should be per- mitted save to quarters which are completely separated and protected from the infected apartments. The exposed children should be kept under close surveillance until the extreme limits of the period of incu- bation have been passed. Disinfection. — The germs of measles have comparatively little tenacity to life outside of the human body. It is unusual for the disease to be carried by infected articles or third persons. We do not subscribe, however, to the positive statements made by some physicians that the disease is never communicated in this manner. In hospitals and other institutions for children wards should invariably be disinfected after 1 Loc, cit., p, 200, THE TREATMENT OF MEASLES 539 measles has broken out; in private households tlionju^li cleansing and subsequent airing nifiy tjike tlu; })la(;e of the more rigid measures of disinfection eni[)loyc(i in otlutr infectious (h'seases. General Management of the Disease. — Measles runs its course in a definite period of time like other self-hmited affections, and tends in uncomplicated cases to recovery. No know^n drug is able to abridge or modify the course of the disease. The therapeutic indications, therefore, are: (1) to mitigate or control excessively developed symptoms and (2) to treat or, preferably, prevent complications. The temperature of the sick-room should be maintained in the neighborhood of 70° F., particularly during the cold months of the year. It is important that the temperature l:)e kept uniform and not be allowed to fall during the hours of the night. While it is desira})le to avoid direct draughts upon the patient, it is equally essential to keep the room well ventilated and the air pure. Owing to the irritating influence of dry air and the increased liability to dissemination of dust in such an atmosphere, it will be found advantageous to moisten the air by one method or another. A pan of water may be heated over an alcohol lamp or the old-fashioned kettle of steaming water may be brought into the room. This use of steam is even more important when a severe catarrhal laryngitis or bronchitis is present. Under such circum- stances aromatic and sedative medicaments, such as the compound tincture of benzoin may be volatilized by being placed upon the surface of the steaming water. The habit, fortunately obsolete for the most part now, of bundling up measles patients with an excess of bed-clothes is to be deprecated. Mothers should be instructed that the guide in this matter is the comfort of the patient. Sydenham proved several centuries ago that the "sweating regimen" was out of place with a feverish patient. In changing the bed-linen of patients in the winter months it is advisable to warm the sheets before they come in contact with the patient. It will be found necessary to protect the eyes of measles patients against too strong rays of light. It should be remembered, however, that it is not necessary to make a room absolutely dark in order to accomplish this purpose. Just sufficient light should be excluded to make the patient comfortable. The complete shutting out of daylight is not only depressing, but the air is robbed of the purifying and germ- destroying influence of the sun's rays. Patients with measles may be sponged daily with tepid water. The old-time prejudice against the use of water in the eruptive fevers is still harbored by some oversolicitous mothers, but is scouted by physicians of experience. In order to avoid complications which arise from the catarrhal inflammation of the nose, mouth, and conjunctiva, it is well to employ the following 'preventive measures as a routine. The mouth should be washed several times a day with a solution of boric acid to which a little glycerin and a few drops of oil of wintergreen may be added, or instead some other mild antiseptic w^ash may be employed. By this 540 MEASLES precautionary measure the liability to ulcerative stomatitis, a by no means rare occurrence, is lessened. Williams regards the use of anti- septic mouth washes as important, because "it has been shown that the microbes associated with bronchopneumonia are present in the mouth in more than half the cases of measles." The nares should be irrigated every few hours with a decinormal saline solution. Care should be taken that the syringe is gently manip- ulated and the forcible projection of fluid into the nose avoided. Comby prefers spraying of the nose, mouth, and throat with a steam- atomizer. He state's that Siredey obtained excellent results by this method at I'Hopital d' Aubervilliers ; before this treatment was used 50 cases of measles gave 23 complications (46 per cent.); since the employment of the spray 53 cases have only furnished 7 complications (13 per cent.). The genitalia, particularly in girls, should be kept scrupulously clean owing to the vulnerability of these parts to gangrene involvement. In addition to the use of soap and water a weak solution of bichloride of mercury or a saturated solution of boric acid may be employed. Measles patients should always be confined to bed for the entire febrile period of the disease; in severe cases the patient should not be allowed to leave bed until a week or ten days after the termination of fever. During the cold and rainy seasons this precaution should be carefully observed. During the balmy days of late spring or summer one need not adhere so rigidly to this rule. It is difficult to keep very young, rest- less children constantly in their cribs; where care is exercised as to the equability of the temperature in the room and to the clothing of the child, it is permissible to gratify its desire to be taken up in one's arms. Season and climate will influence the duration of the sojourn in-doors. Ordi- narily the patient should not go out for ten days to two weeks after the subsidence of fever; this period should be increased in cold, wintry weather, and abbreviated during a warm and dry spell. Diet. — For children, milk, preferably diluted with barley-water, is the best diet. This not only constitutes the most assimilable and nourishing food, but helps to assuage the thirst and acts on the kidneys. When the temperature is high the milk may be taken cool and will be found to be most acceptable to the patient. Where it is distasteful to a child it may often be rendered more palatable by flavoring it with a little extract of vanilla. As measles is a disease of short duration it is not essential to force nourishment upon the patients as in more pro- tracted affections, such as typhoid fever. It will be found that when the temperature is high, children will want nothing but cool milk; later there will be a desire for a more varied dietary. As the fever declines there is no objection to the use of junket, farina, milk-toast, broths, arrowroot, rice, custard, strained oatmeal, soft-boiled eggs. It will be well to avoid those cereals which, by reason of their husk, are apt to excite diarrhoea. I For the relief of thirst, apart from the use of cool milk, the patient may partake freely of water, provided it is not iced. In older children 77//'; TIINATMI'INT OF MJ'JASLKS o41 carbonated water is often gratefully received, or water acidulated with lemon or orange juice. There is no o})jection to the use of ice-creain, [>rovidcd it is taken in moderation. Medical Treatment in the Complicated Cases.-— Mild cases of measles require but little medication ; the nursing is of greater importance. It may be necessary to relieve constipation in the beginning. No irritant purgatives should be employed, but rather such gentle remedies as castor oil, elixir of cascara, or syrup of rhubarb, or a simple enema may be given. Drastic drugs might lead to a catarrhal inflammation of the intestines, to which measles patients are already predisposed. More often the physician will be called upon to check excessive bowel movements. If these are allowed to continue they soon ex- haust tlie vitality of the patient. Usually the diarrhoea can be con- trolled by a mixture containing paregoric and bismuth; if this does not suffice the deodorized tincture of opium may be used instead of paregoric. Where the bronchial catarrh is slight no treatment is necessary. When there is much cough it will be necessary to allay it by one of the simple cough mixtures. The well-known "brown mixture" may be admin- istered or a combination containing a little bromide of soda and ipecac- uanha may be used. For severe and incessant cough one may be obliged to resort to opium; it must be remembered that this drug must be used with caution in young children. Five to twenty drops of paregoric, according to the age of the child, may be given every few hours. The fever, when of moderate grade (102° F.), will require no treatment. It is customary to prescribe some simple febrifuge containing a little tincture of aconite, potassium citrate, and spirits of nitrous ether; this preparation has a gentle diuretic and diaphoretic action. When the temperature reaches 104° or 105° F., and particularly when it is accom- panied by marked nervous symptoms, such as restlessness, delirium, stupor, or convulsions, more active antipyretic treatment is demanded. Of all measures for the reduction of temperature, hydrotherapy is to be preferred. Cold tub baths are usually not well borne by young children, and it is best to employ tepid or warm baths, except where the fever cannot be thus controlled. Immersion in a bath of 85° F. to 90° F. will frequently bring down the temperature and quiet the disturbed nervous system. These baths may be repeated as often as the occasion demands. In those cases in which the temperature is not sufficiently controlled by this means, recourse may be had to the use of cold sponge baths or the use of the wet pack. The ice cap may be used as an adjunct to any of these measures. When the temperature is high and the extremities cold, the patient may be immersed in a hot bath with or without the addition of mustard; in such cases the ice-bag should be applied to the head. The cold bath under such circumstances is badly borne, as the depression is too great for an already weak heart. 542 MEASLES The hot bath with mustard is also useful in those cases in which the eruption is imperfectly developed or unusually slow in making its appearance. The reduction in the body temperature is accompanied by an amelio- ration of the pronounced nervous symptoms which accompany hyper- pyrexia. Where for any reason hydrotherapy cannot be employed, one may resort to the use of some of the coal-tar antipyretics. Antipyrin usually acts very well in children. It has been extensively employed by many physicians with satisfactory results. Not only is there a reduction in the temperature, but violent nervous manifestations, when present, are promptly quieted. One to 3 grains repeated according to indications will usually suffice. Comby has used this drug extensively in measles, giving it in dosage of 7| to 15 grains. We would feel a hesitancy about administering such a dose to a child, yet Comby states that he has never seen any bad results therefrom; a reduction of temper- ature of one or two degrees was obtained, which lasted from two to four hours. Phenacetin may, if desired, be employed instead of anti- pyrin. While these drugs usually act well, hydrotherapy is ordinarily to be preferred. Treatment of Complications. — Measles as an uncomplicated disease nearly always ends in recovery; it is its complications which render it frequently a grave and fatal affection. The preventive measures to be pursued have already been discussed. The complicating disorders must be treated much in the same manner as when they occur independently of measles. Nervous Symptoms. — The ushering in of an attack of measles with convulsions is not of bad augury unless they persist; convulsions in children take the place of the chill in adults. Where the seizure is brief no special treatment is necessary; when it is prolonged or repeated there is a possibility of a cerebral hemorrhage resulting therefrom and measures thould be taken to check the convulsions. A few inhalations of chloroform will frequently control the paroxysm, after which chloral hydrate or antypyrin should be administered. An ice-bag to the head will also be found to be of assistance. Restlessness, stupor, or delirium can be controlled by the hydro- therapeutic measures mentioned, for they almost always occur in association with high temperature. Skin. — The skin should be kept scrupulously clean throughout the attack; this may be accomplished by sponge baths with alcohol and water or mild antiseptic solutions. Itching of the skin may be so intense as to necessitate measures for relief. A lotion containing 1 drachm each of carbolic acid and glycerin to the pint of water or an ointment of 10 grains each of carbolic acid and camphor to the ounce of vaselin will control the pruritus. Not infrequently impetigo vesicles and pustules develop about the nose, mouth, or ears as a result of pyogenic infect'.on of the skin from purulent discharges. An ammoniated mercury ointment, 10 grains to the ounce, will effect the disappearance of these lesions. Tm<: treatmi':nt of mj'JA,s/jarle ('120 cases), Edwards (16G cases), Kingsley (21 cases), Atkinson, Griffith, and Hardaway. At the ])resent day there is a unanimity of opinion concerning the existence of rubella as a disease sui generis. THE ETIOLOGY OF RUBELLA. It is generally recognized that rubella, like the other exanthematous diseases, is derived from and begets a like disorder. It confers pro- tection only against rubella, and no immunity against it is granted by an attack of measles or scarlet fever. Many of the earlier vv^riters doubted and even denied the contagious- ness of rubella, but there is at the present day a unanimity of opinion concerning its transmissibility. As to the degree of contagiousness views are somewhat divergent. Chadbourne and J. Lewis Smith regarded it as feebly contagious; Thomas, Liveing, Tongue-Smith, Bourneville, and others, as less contagious than measles; Jacobi, Dukes, Squire, and Griffith look upon it as very contagious, and Edwards^ believes that "rubella is one of the most contagious of all of the eruptive fevers." Griffith states that in an institution of 100 children 37 took the disease despite prompt and careful isolation. In another institution 26 per cent, were attacked. Klaatsch believes that the degree of contagiousness varies in different epidemics. HatfiekP reports an asylum epidemic in which 110 inmates out of 196 contracted the disease. From our experience at the Municipal Hospital we are inclined to believe that a larger number of children escape rubella when this infection is introduced into the wards than escape measles under similar circumstances. Rubella is essentially an epidemic disease and appears to be more prevalent in the winter and spring seasons. The disease is about as common as measles, with which affection it has doubtless often been confounded. The infection of rubella seems to be more tenacious and persistent than that of measles. It is, therefore, more apt to be carried by fomites in the garments of third persons than is measles. Edwards alleges that about 75 per cent, of his cases could be directly traced to infection from the bunks of ships, and states that Emminghaus, Thomas, Veale, and others considered such an origin proved. Corlett^ remarks that rubella corresponds more with scarlet fever than with measles in the persistence of the vitality of the contagium. Opinions are at some variance in regard to the period of greatest contagiousness. Thierfelder looked upon the stage of convalescence as the time at which the disease was most transmissible. Squire con- sidered all stages contagious, from the pre-eruptive period late into 1 Article on Rubella, Keating's Cyclopedia of Diseases of Children, Philadelphia, 1889, p. 6S7. - Chicago Medical Examiner, August, 1881. s loq. cit. 550 RUBELLA convalescence. Edwards coincides with this opinion. Griffith con- cludes, from his observation in institution epidemics, that rubella is certainly contagious at a very early date, for prompt isolation failed to check the extension of the disease. Age.— Rubella behaves much like measles as regards age incidence. Infants under six months of age usually escape the infection, although now and then the disease will be contracted. We have seen a six-month- old infant live and remain well for months in a ward in which cases of rubella were constantly appearing. Smith, Roth, Steiner, and Hardaway have recorded attacks in early infancy, and Scholl reports a case occurring in a child a few days after birth, the mother having suffered from the disease two months previously. As in measles, those who escape the disease in childhood may contract it in adult life; indeed, even in advancd years, as is attested by Seitz, who reports a case in a woman seventy- three years old. Emminghaus saw only two adult attacks among 42 cases. Thomas noted 3 among 77 cases; Kassowitz observed 5 in 64 cases and Thomas but 1 in 100 cases. Edwards does not believe that adult life confers any special immunity; he regards infrequent exposures to the disease, and protection by an attack in childhood as the cause of the compara- tive rarity among adults. Thomas holds a rather different view. He says : "After the fortieth year the susceptibility is nearly lost, and we may consider it as essentially weakened at puberty, and as steadily diminishing subsequently." In Forchheimer's^ experience more physicians have been attacked by rubella than by all the other exanthematous diseases taken together. He adds that, "with the exception of variola, possibly no disease of this class so frequently affects adults." THE SYMPTOMATOLOGY OF RUBELLA. Period of Incubation. — Different observers have assigned incubative periods to rubella varying from five days to three weeks. This variable duration is regarded by Griffith as one of the diagnostic features of the disease and in striking contrast with the fixed incubation period of measles. To indicate the divergent observations of different clinicians we present a table compiled by Forchheimer, to which we have made additions : 1 Twentieth Century Practice of Medicine, article on Rubella, p. 180. 77//!,' SYMPTOMATOIJXJY ()!<' lilJ lihlLLA 551 Periods of Inctjra'i 'ION OF RUBKLLA. Atkinson . l-l to 21 days. Hardawny . 2 weekKor longer. Balfour. 2 weeks. Hatfield 10 days. Boudet . . 12 to M days. .laoobi . H to 2] days. Bourneville S days. Kas.sowitz . 2 to 3 wcekB. Bricon . . 8 to 10 days. Klaat8(;li 2]4. ^1 3 weeks. Bristowe 1 week. Longstcl 18 days. Cheadle . 15 days. Metteiiheirner 2 weeks or longer. Clausen . . 17 to 20 days. Musser . Just 6 days in lease CottiiiK . 3 weeks. I'icot 2 U> 3 weeks. Culling vvortl 1 . . 2 weeks. Pollock . f. to 1 days. Cuomo . . 17 days; never less. Juhel-r{enoy 15 days. Duckworth . Ifi days. Robinson G to 7 days. Duke . . 15 to 16 days. Scholl . 5 to 21 days. Earle . . 17 to 21 days. Steiner . 10 to 14 days. Edwards . 10 to 12 days. J. L. Smith . 7 to 21 days. Eichhorst 2 to 3 vVeeks. Tongue-Smith . 14 days. • Emminghau! 2 to 3 weeks. Squire . 8 to 21 days. Gerhardt 2 to 3 weeks. Tbierfelder . 2 weeks or longer. Glaister 4 to 5 days or longer. Thomas 2y^ to 3 weeks. Goodhart 2 weeks or longer. Vacher . 13 days. Griffith . 5 to 11 days. It is thus seen that the incubation may be either shorter or longer than that of measles. Eleven writers have noted minimum periods of five to eight days, and no less than thirty-two have seen the period extend beyond fourteen days. During the stage of incubation the patient is entirely free of any disturbance of health except, perhaps, in extremely exceptional cases. Period of Invasion. — In most cases of rubella this stage is either devoid of symptoms or presents only mild manifestations which are readily overlooked. It would appear that the more severe the attack is to be, the more apt is it to be preceded by pronounced prodromal symptoms. In the vast majority of our cases at the hospital the eruption was the first sign to attract attention. In a severe attack in a trained nurse, the symptoms of which will be fully detailed later, there was, however, a distinct and protracted stage of invasion. This nurse was on night duty in a ward in which rubella existed. On Wednesday, ^March 11, 1903, she was taken ill with headache and sudden vomiting; the emesis was persistent, the patient vomiting four or five times each day and retaining nothing. There were also feverishness, continued headache, recurring chilliness, perspiration during sleep, restlessness, and weak- ness. On March 16th, jour and a half days later, the eruption appeared. No catarrhal symptoms whatever were present. This case must be regarded as presenting exceptional initial manifestations. While most writers refer to very mild and brief prodromes, some rather severe invasive symptoms have been described. Edwards^ noted in a severe epidemic in the Philadelphia Hospital the following s^inp- toms: chilliness, languor, faintness, headache (more or less severe), pain in the back and limbs, coryza, red and watery eyes, sore throat, cough, occasionally a hoarse, husky voice, and a temperature from I Loc. cit. 552 RUBELLA 100° to 103° F.; nausea and vomiting, delirium and convulsions, and epistaxis were observed in three cases. Other unusual prodromal symptoms have been recorded. Prioleau reports 2 cases of hemorrhage from the eyes and ears; vomiting is mentioned as a rare symptom by Smith, Murchison, McLeod, and Emminghaus; convulsions by Smith, Lindwurm, Cuomo, and Alexander; delirium by Hardaway and Cuomo. Nymann observed rigor in 19 out of 119 cases; Earle, Kingsley, Thierf elder and Griffith mention a slight redness preceding the eruption, and Cuomo (in 7 cases) and Edwards (in 4 cases) a prodromal erythema. Such symptoms as those detailed are exceptional, but nevertheless of interest. The experience of most observers is that the prodromal symptoms are absent or mild, consisting of drowsiness, anorexia, "liquidy" eyes, sneezing, slight cough, etc. Earle found that prodromal symptoms were more frequently present in adults than in children. As to the duration of the invasive period, opinions differ somewhat; we would subscribe to the statement of Thomas, endorsed by Hardaway and Griffith, that in the vast majority of cases the prodromal stage is at most no longer than half a day. At the same time we recognize that it may vary from a couple of hours to five days. Various writers assign periods intermediate between these two extremes. It would seem that long periods of invasion presage attacks of greater severity than brief periods. Period of Eruption. — A half -day or so after the onset of mild invasive symptoms, or in many cases without any prodroma at all, the eruption of rubella makes its appearance. The rash is commonly the first symptom to attract attention, the other mild initiatory disturbances then being recalled. Not infrequently a child awakens in the morning with the eruption visible upon the face. In our cases at the Municipal Hospital, all of which developed in scarlet-fever convalescents, the rash was frequently discovered when the children were lined up for inspection during our visits. Most writers coincide in the view that the eruption appears first on the face; other locations are, however, mentioned by some observers as the initial site. Liveing and Morris state that it appears first on the trunk; Murchison, Day, and Balfour speak of the breast and arms as first attacked, Willcocks and Carpenter the face and margin of the hair, and Thomas and Corlett the face and scalp. Patterson and Copland assert that it comes out simultaneously on different parts of the body. In noting the eruption a short time after its appearance upon the face we have seldom failed to find it to some extent on the trunk and arms. In a severe case in a trained nurse (to which reference has already been made) the eruption was carefully looked for by another nurse occupying the same room and was observed to first appear at 3 a.m. on the legs below the knees; it then spread upward and by 6 a.m. was noticed on the wrists. At 3 p.m., the hour of our examination, it was 77//'; HYMI'TOMATOr/Xjy ()!<' Rf/Iif'JJ.A 553 present on the legs, arms, and trunk. 'I'lie face was flushet], but no distinet eruption was seen in this rej^ion until tlie follf)\vin{( day. It is evident that while the eruption of rubella normally appears first on the face, thence extending downward, anomalous cases may occur in which the origin is in other regions. The exanthem spreads (juit(! ra})idly over the body in the course of twenty-four to forty-eight hours. It is interesting to note, however, that the maximum intensity of the rash is not siniultaneously noted on the entire cutaneous surface. It is not unusual for the face, che.st, and Fin. 80 Faint eruption of rubella upon the face in a mild attack. arms to show the eruption at its height while the legs are yet unaffected. When the lower extremities exhibit the exanthem in its greatest mtensity it is fading upon the face and upper part of the body. In other words, the rash often seems to pass over the cutaneous surface in a sort of wave-like progression. The duration of the eruption at its height in any given region is from a few hours to half a day. The more severe the attack, the longer is the period of maximum intensity and the longer the duration of the eruption. This peculiar progression of the eruption is commented upon by Thomas in the following words: "It happens with tolerable frequency 554 RUBELLA that the maxima of its development occur at varying times upon different portions of the body." Some writers, particularly Emminghaus, Roth, Mettenheimer, and Hardaway, attach to this eruptive sequence great importance,, regarding it as one of the safest diagnostic signs of rubella. Griffith agrees with Thomas' statement as to the tolerable frequency of this occurrence, but questions its diagnostic value, as he has nearly as often observed that the rash persisted with equal intensity on the face while it spread to the rest of the body, reaching its acme everywhere upon the second day. Character of the Eruption. — The eruption, in its most typical form, consists of pinhead to lentil-seed sized, pale rose-tinted, slightly elevated, moderately defined macules. -The lesions are usually rounded or oval, but may be irregular. The elevation is scarcely sufficient to warrant the use of the term papules, but is appreciable to the finger passed over the surface of the skin. The macules are ordinarily discrete, with considerable intervening pale skin, particularly at the onset of the eruption and on the trunk. Later they are apt to become more closely set and may coalesce, with the production of irregular patches resembling measles or sheets of eruption of a scarlatiniform character. Ordinarily, macular grouping, such as is seen in measles, is absent, but we have now and then seen distinct linear and crescentic configu- ration indistinguishable from that observed in measles. Rubella in its purest form, however, shows smaller, more regular, and more discrete lesions than those of measles, which are inclined to present an irregular, blotchy appearance. The color of the macules of rubella has been described as a pale rose-tint or rosy-red by most writers. Shuttleworth refers to it as a brownish-red. The color doubtless varies to some extent in different individuals, as does the tint in all eruptive diseases, but it may be said in general that it is ordinarily not as vivid as the eruption of scarlet fever, nor as dusky or bluish as the measles exanthem. The discreteness of the slightly elevated macules gives the eruption its distinctive appearance, the reddish spots standing out in striking contrast with the pale integument. Confluence is, however, frequently noted in certain areas, particularly on the face. On the second or third day of the eruption it is not uncommon for the rash to become paler in tint and to assume a more diffuse appearance. Pressure or irritation of the skin seems to increase the intensity of the eruption and to encourage confluence. Klaatsch and Griffith both report cases in which the eruption was particularly well developed in circular bands above the knees, where the garters had made pressure. In scarlet fever, on the other hand, pressure, such as is produced by garters, is apt to produce anaemic or pale bands in the areas thus affected. Distribution of the Eruption. — The face almost invariably exhibits an abundance of eruption, especially upon the forehead, cheeks, and chin. The lesions may be so copious as to produce the appearance of slight oedema. The eruption does not respect the circumoral region as does the exanthem of scarlet fever. The scalp is profusely covered, as is also the neck. The chest, abdomen, back, and arms show rather Tim HYMI'TOMATOIJXIY OF lUJUHLLA 555 less eruption; the Inittocks and j)Ostorif)r aspect of the thighs, owing, perhaps, to pressure, commonly exhi})it eruption in such j)rofusion as to present confluent patches. The legs, as a rule, are the seat of the least eruption, the lesions often being widely scattered. It has been asserted by sonic writers that the palmar and |)lantar surfaces are exempted, but this is not true, as lesions are not infrcfiuently found in these regions in well-pronounced attacks. The above outline presents the distribution of the eruption in normal cases; it is not rare for depart- ures from this to take place. Barthez and Rilliet have noted the fading of the (;ruption followed by the reappearance of the same upon the same day or later. Griffith also mentions a case in which it was invisible during one day and returned. Duration of the Rash. — The duration of the rash is influenced by the intensity of the eruption and the character of the epidemic. The ous periods a Aitken . ssigned by dmerent v 4 to 5 days (bad cases i^riters are nei Gerhardt e tabulated: . J^ to 1 day. 6 to 10). Griffith . . 2 to 3 days Alexander . . 14 days (one case). Hatfield 4 days. Alibert . . 2 to 3 days. Kingsley 2 to 4 days. Balfour. 4 to 6 days. Klaatsch 1 to 5 days. Barthez . 2 to 3 days. Liveing . 5 to 7 days. Bourneville . . 2 to 3 days. Maton . 3 to 4 days Bricon . 2 to 3 days. Nymann 2 to 4 days Carpenter . 1 to 4 days. Picot . 3 to 4 days. Claussen 3 days. Rilliet . . 2 to 3 days. Copland 4 to 5 days. J. G. Smith . 3 days. Corlett . 2 to 4 days. Thomas . 2 to 3 days. Edwards 2 to 15 days ; average 5. Trousseau . 1 to 2 days. Emminghaus 2 to 4 days. Willcocks . 1 to 4 days Porchheimer . not exceedin J 5 days. It will be seen from the above figures that the duration of the eruption offers considerable latitude. The long periods are doubtless isolated instances. In about 100 cases which we have recently had the oppor- tunity of observing, the rash did not persist beyond three days save in the case of the nurse, in whom it lasted five days. In a great many of the children the eruption was scarcely apparent after the first twenty- four hours; the average duration was certainly not more than two days. The brief duration is, perhaps, to be accounted for by the very mild type of the epidemic. The average duration in over 200 of Edwards' cases was five days; the type of the epidemic which he observed was, however, distinctly more severe than ours. The rash appears to persist longer in some regions than in others, possibly the regions of greatest intensity. Edwards says that the face and upper chest exhibit the most persistent eruption; our experience coincides more with that of Griffith, who regards the face and buttocks as the seats of the most protracted eruption. Anomalous Features of the Eruption. — In rare instances miliary vesicles have been noted upon the reddish macules. This has been observed by Curtman, Cuomo, Thomas, Hardaway, and Copland.^ 1 Mentioned by Griffith, loc. cit. 556 RUBELLA Petechial spots have been recorded by Dunlop and Hkewise by Cheadle; Erskine reports similar lesions on the uvula and soft palate. A purpuric rash was also observed by Glaister. Claussen makes mention of lesions which gave the impression of small shot being buried in the skin. Griffith saw an unusual eruption which also imparted a shotty feel to the finger. Scarlatiniform Variety of Rubella. — Thus far reference has only been made to normal rubella and to the form which bears more or less of a resemblance to measles. There are other cases in which the exanthem bears a strong resemblance to that of scarlet fever. Some writers of prominence make no mention of this variety and express astonishment at any suggestion of similarity between the rashes of rubella and scarlatina. Thomas says: "According to my observations the exanthem of rubeola (rubella) possesses a similarity to that of measles only, not the slightest to that of a normal scarlet fever." Bristowe and Bourne- ville and Bricon entertain similar views. These opinions may be attributed to the fact that the scarlatiniform variety of rubella has not come within the range of the personal experience of these physicians. Mention could be made of a large number of writers who have observed this variety. Hatfield speaks of an epidemic in which the rash in many cases was indistinguishable from measles, and in other cases strongly resembled scarlet fever. J. L. Smith refers to a case which, had he been guided alone by the eruption, he would have regarded as a mild scarlet fever. Griffith describes a case in which the eruption was at first macular, yet on the second day it so closely resembled scarlet fever that he was unable for several days to make a diagnosis. The whole body was covered by a general scarlatinal blush and nowhere could a single macule or papule be found. A short time afterward the brother took rubella. We have seen in the Municipal Hospital one or two cases of rubella with scarlatiniform eruptions in children convalescent from scarlet fever. Griffith,^ from a careful study of a large number of cases, comes to the conclusion that there are two easily recognized types of variation from the character of the eruption in a normal case: 1. "An eruption in which the spots are for the most part nearly or fully the size of a split pea, more or less grouped, and, in fact, having the greatest resemblance to measles. 2. "A rash which is confluent in patches or universally not elevated, and which produces a uniform redness closely simulating that of scar- latina. Very careful examination will often reveal a few papules amid the general diffuse redness." Desquamation. — Upon the subsidence of the eruption a delicate brownish or yellowish staining may be noticed for a short time. A slight branny or furfuraceous desquamation occasionally follows the disappearance of the rash. The development of this scaling is proportionate to the severity of the attack and the intensity of the 1 Loc. cit., p. 15. Tlll'l KVMl'TOMATOfJXlY OF ItU I'.FLLA F)')! eruption. Many writers, inclufiing Steiner, Thomas, Fleisclimann, Brodie, McLeod, Wilson, Goodhart, Cuonno, Bourneville, and liricon have not ol)served des(|naniutioii. Eflwards, on tlie other hand, in a severe ej)ideniic discovered (Jescjiiamation in all of his cases. In quite a number the scaling was well marked; in others it was limited to certain regions, especially the nose. The buccal cavity, |)articularly the throat proper, participated in the desquamative process. The peeling was usually furfuraceous, beginning in the centre of the eruptive patch and extending to the circumference. Larger scales were seen on the hands and feet. The average duration of desquamation was three days, but Edwards has seen it last twenty days. In our cases, which it will be remembered were very mild, it was rare to .see any desquamation. Associated Symptoms of the Eruptive Stage. Fever. — The extent of febrile reaction in rubella is largely dependent upon the severity of the individual attack and the character of the prevailing epidemic. The variant observations of different writers on this point is evidence of the truth of the above assertion. There are some epidemics in which there is but an insignificant rise of temperature, if, indeed, there be any fever at all. Nymann failed to observe any appreciable rise of temper- ature in 58 out of 119 cases. Emminghaus, Thomas, Vogel, Wunderlich, Earle, Picot, and others have all seen afebrile cases. On the other hand, in severe cases high fever may be present. Edwards saw cases with temperature of 103° and 104° F. McLeod's cases ranged from 100° to 105° F. Cheadle reports an epidemic in which the initial temperature was 103° F., later reaching 104° and 105° F. Haig-Brown records a temperature of 105° F., and Davis saw a temperautre of 106° F. in a boy with a livid rash, convulsions, and rapidly running pulse. The fever is, as a rule, proportionate to the extent and severity of the eruptive and catarrhal symptoms. There is no febrile course which occurs with any degree of constancy. The evening temperature is, however, usually 1 or 2 degrees above the morning. Most cases of rubella will exhibit slight fever varving between 99° and 101° F. In most of our cases the temperature regis- tered 99° or 100° F. In two patients it reached 102° F. It 's not surprising that some of the older writers should have regarded rubella as a hybrid of measles and scarlatina, for we commonly note in this disease the catarrhal symptoms of the former and the angina of the latter, but both in very mild form. The catarrhal symptoms commonly affect the eyes, nose, throat, and bronchial tubes. The eyes are commonly seen to be "watery" or slightly injected. Our experience coincides with that of Griffith, who observed this symptom in about one-half of his cases. It is uncommon to find conjunctivitis and photophobia as pronounced as it is seen in measles. Sneezing. — Sneezing is a frequent symptom, although the paroxA'sms may be but few and limited to the first day of the eruption. In none 558 RUBELLA of our cases did we note any distinct discharge from the nose; neverthe- less, coryza is recorded as occurring in a considerable proportion of cases in some epidemics. Cough. — Cough occurs in a variable proportion of cases, depending upon the character of the prevailing epidemic. When it is present it is usually slight and in no sense comparable with the severe cough of measles. It was absent in the vast majority of our cases. Griffith says a loose, bronchial cough was frequently present in his cases and occa- sionally demanded treatment. In the severe epidemic observed by Edwards cough was generally present, increasing in frequency and severity and occasionally becoming laryngeal. In quite a large pro- portion of these cases bronchitic rales, more or less diffused, were heard. The cough lasted about as long as the eruption, so that it had entirely disappeared about the fourth or fifth day. Sore Throat. — Sore throat of a mild character is an extremely common symptom of rubella. The angina is much milder than that observed in scarlatina, and often does not lead to complaint on the part of the patient. Without inspection it would, doubtless, be frequently over- looked. The congestion is most pronounced upon the upper portions of the anterior pillars. Occasionally a more serious involvement of the throat is encountered, characterized by enlargement of the tonsils, swelling of the pharyngeal mucous membrane, and painful swallow- ing. Mild angina is regarded as a rather constant symptom by most writers. We have frequently seen upon the soft palate a number of pinhead- sized, glistening, reddish elevations. Similar reddish spots have been observed by Emminghaus, Nymann, Gerhardt, Picot, Parke, Dunlap, Kassowitz, Cuomo, and Griffith. Forchheimer regards as a character- istic exanthem "the small, discrete, dark-red, but not dusky papules" which are seen early on the soft palate and which disappear in twelve to fourteen hours. We have carefully examined the buccal mucous membrane in a number of cases and have frequently noted the presence of discrete, pinhead- sized, deep-red spots, bearing a considerable resemblance to the macules upon the cutaneous surface. We have never seen the central bluish- white dots which Koplik describes as characteristic of measles. Hoarseness. — Hoarseness, usually mild but occasionally severe, has been mentioned by Thomas, Emminghaus, Griffith, Aitken, Cheadle, Patterson, Edwards, and others. The catarrhal symptoms sometimes subside after a duration of !a day or two, but more commonly disappear with the eruption. Occasionally a certain amount of cough may con- tinue for some days. Tongue. — ^The tongue is usually covered with a thin, grayish coating, the tip occasionally exhibiting some prominence of the papillae. While a few writers (Balfour, Hemming, Tripe, Murchison, Burnie, and Tompkins) claim to have seen the typical "strawberry" tongue in rubella, this condition must be regarded as exceptional. In some cases the tongue is clean and presents no deviation from the normal appear- TILE SYMPTOMATOLOGY OF IKJIiKI.LA 550 ance. In severe cases Edwards states that tlie tongue may he dry and brown. Lymphatic Glands. — Enlargement of tlie lympliatic glands lias long been regarded as a symptom of considerable diagnostic im|K)rtance. Nearly all writers are agreed as to the constancy of tliis adenopathy. It must be remembered, however, that a general glandular intumescence occurs in scarlet fever and to a lesser extent in measles, and that lymph- atic enlargement, therefore, does not specially differentiate rubella from these diseases. According to Griffith, J. F. Meigs regards the enlarged postauricular gland as one of the most prominent diagnostic signs of rubella. It is claimed by some writers (Squire, Thierfelder, Glover, Jalland, Strover, Hardaway) that the glands increase in siz-e often before the appearance of the rash. In other cases, however, the glanflular tume- faction may not be noted until the second day after the appearance of the eruption. The glands behind the ears and those lying posterior to the sternocleidomastoid muscles are those most frequently enlarged, although other glands, such as the inguinal and axillary, may participate in the process. Kassowitz found lymphatic enlargement in but one- third of his cases, and Eustace Smith observed it only in certain epidemics. Nausea. — Nausea and vomiting are rare symptoms in cases of the average type. In severe cases, however, emesis may be severe and persistent. In one of our cases the vomiting continued for several days before the appearance of the eruption, the patient being unable to retain any nourishment at all. Edwards states that in a severe epidemic in the Philadelphia Hospital, vomiting occurred in a fair proportion of the cases as the eruption was approaching the maximum. In five of these cases it was almost uncontrollable. Griffith observed vomiting on the first day of the eruption in a few severe cases. The bowels are usually normal or constipated. In a nurse under our care, suffering from a very mild attack of rubella, diarrhoea was present on the first and second days of the eruption. About 40 per cent, of Edwards' cases had gastrointestinal irritation; this very unusual complication may be accounted for by the severity of the epidemic. Among these cases were 10 of enteritis and 2 of entero- colitis. Cuomo has also noted the presence of diarrhoea in severe cases. Earle encountered 4 cases of intestinal irritation. Balfour found catarrh of the colon a rather common symptom. The majority of writers make no mention of any disturbance of the bowels. Itching.— Itching varies both as to frequency and intensity, depending much upon individual peculiarity. It is present in only a minority of cases and is seldom severe. Pulse and Respiration. — The pulse and respiration usually keep pace with the elevation of temperature. The former may undergo acceler- ation to 140 or 150 per minute. Edwards says several of his cases presented well-marked symptoms of heart-failure, which yielded, how- ever, to appropriate treatment. 560 RUBELLA The following case of rubella in an adult patient under our care presents many points of interest: Miss R., trained nurse, aged twenty-seven years, had measles at the age of eight and scarlatina at the age of six. Was on night duty in convalescent scarlet-fever ward of the Municipal Hospital, in which rubella appeared on March 3, 1903. Patient had been exposed to measles in another building five weeks previously. March 16, 1903. — On Wednesday, March 11th, the patient was taken sick with headache and sudden vomiting. Since that time she has vomited each day (or rather night, as the patient has continued on night duty, not making known her illness.) Emesis occurred five or six times each night. Patient claims to have retained absolutely nothing. There has also been persistent headache, weakness, recurring chilliness, perspiration during sleep, and restlessness. No catarrhal symptoms whatsoever; neither coryza, cough, nor conjunctival redness. Although patient had felt feverish for some days, her temperature was first taken on March 15, 1903, in the evening, when it registered 102° F. This morning it is 100° F. Glands about the jaw and neck are not enlarged. The eruption was carefully watched for by another nurse who occupied the same bed-room; it was observed at 3 a.m. on March 16, 1903, making its appearance first on the legs below the knees, then spreading upward. At 6 a.m. the rash was noticed on the wrists. At 3 p.m. (the hour of our examination) the following notes were made: An eruption of pinhead to lentil-seed sized, dusky red, slightly elevated macules is seen, quite covering the legs and with even greater profusion the arms. The macules form typical crescents on the arms and are also arranged linearly. In other places they run together and present an appearance quite indistinguishable from an intense measles exanthem. The upper part of the chest shows a diffuse scarlatiniform redness. On the back are a number of discrete macules which have just appeared. The face shows no distinct eruption, but the cheeks are quite flushed. The buccal mucous membrane exhibits faint reddish spots. Ylth. The temperature last night was 101f°F. This a.m. it is 100° F. The patient is perspiring quite a little. The glands at the angles of the jaw are now enlarged to the size of almonds and are distinctly tender. There is also enlargement and tenderness of the cervical glands. The eruption has become fainter and more confluent on the legs and forearms and has extended to the hands, and also from the legs upward to the thighs and buttocks. In the latter region the exanthem is intense and of a morbilliform character. There is more eruption on the back and chest, in which region it has the form of dis- crete, lentil-seed sized, sharply defined macules. There is to-day some macular eruption upon the face. The uvula and soft palate are slightly injected. l^th. The temperature this a.m. is lOOf ° F. The patient is perspir- ing and complains of chilliness and pains in the back, arms, and legs. The eruption is now faint on the arms and legs, but is still quite con- COMPLICATfONS AND S/;ain this morning. \Mh. Tlie temperature hist nin;ht was H)J;i°F. and this am. is 100|° F. Patient is feeling better. The eruption is still well marked on the chest and back, where it shows many crescents. It is more })ro- nounced on the face to-(hay than at any ])revious time. 20///. The cruptif)n is still present on the back and chest, but is fading. There is still a little fever. 2lst. Temperature last night was 99 if ° F. This a.m. it is 99,!° F. The patient is feeling much better; the appetite is returning. The eruption has practically disappeared. There were many anomalous features in this attack, among which may be mentioned the long and severe prodromal symptoms, the origin of the eruption on the legs, the complete absence of catarrhal symptoms, and the distinctly morbilliform character of the eruption. COMPLICATIONS AND SEQUEL -ffi OF RUBELLA. Rubella and chickenpox rank together as exhibiting the lightest incidence of complications of the various exanthematous diseases. There is no special complication liable to develop during the course of rubella, and in the vast majority of cases there are none. Bronchitis and 'pneumonia have been mentioned by some writers. Edwards saw three attacks of pneumonia among 166 cases and Griffith observed two in 150 cases. Ryle and Edwards have each reported a case of 'pleurisy. Reference to enteritis and enterocolitis has already been made. Severe secondary sore throat has been reported by Tongue- Smith, Emminghaus, and Eustace Smith. Hatfield reports 2 cases of stomatitis and Edwards 4 cases. Earle and Edwards make mention of aphthce, the latter noting it in 30 cases. Rheumatis7n was seen once by Slagle and Edwards, and several times by Earle. Endocarditis has likewise been observed. Several cutaneous complications have been recorded. Alexander records 5 cases of facial erysipelas; urticaria is mentioned by Slagle, Earle, and Cullingworth; febrile a^dema and cedema of the legs have been described. Miliaria, furunculosis, and pemphigus have been recorded as rare complications. Blepharitis, conjunctivitis, phlyctenular keratitis, and otorrhaa have been met with. Mettenheimer speaks of chronic nasopharyngeal catarrh, permanent swelling of the tonsils, and gingivitis. Painful enlargement of the thyroid gland was observed by Slagle in 6 cases. Albuminuria. — Hatfield found albumin in the urine twice and Cuomo three times. Kingsley, Cheadle, Duckworth, and Reed each record a case. We noted transient albuminuria in a case of rubella sent into the scarlet-fever wards as a case of scarlatina; the patient clearly had rubella and was discharged in ten days. In an attack of rubella in a girl suffering from postscarlatinal nephritis, swelling of the eyelids and legs followed the disappearance of the eruption. 36 562 RUBELLA In a series of 166 cases seen by Edwards albuminuria was present in about 30 per cent., but in the next 100 cases but 3 per cent, showed albumin. In the first series 9 cases presented well-marked albuminous urine, with dropsy. In none of the cases could tube casts be found. Most of the complications above described excite interest rather because of their rarity. Association with Other Diseases. — We have observed 100 cases of rubella occurring in children convalescent from scarlet fever. In none of these cases did it occur earlier than the fourteenth day of the dis- ease and usually considerably later. (About one-half of these children had previously in their life had measles.) We have also seen rubella in children convalescing from a mixed attack of scarlatina and diph- theria. In one little girl still scaling from scarlet fever, and showing the crusts of a profuse chickenpox eruption, a well-marked eruption of rubella appeared. Relapse. — We have never observed a relapse in rubella, and from the absence of reference to such instances on the part of most writers it is evident that such occurrences are uncommon. Nevertheless, competent observers have recorded instances of recurring outbreaks. Emminghaus reports relapses in 3 cases and Earle in 2 cases. Edwards noted it once on the fourth day and once on the twentieth. Griffith noted a recurrence once at the end of eleven days and twice after a period of three weeks. Kostlin, Lindwurm, Golson, and Kingsley have also testified to the occurrence of relapses. The recurrent attack may equal the original in the intensity of its symptoms or it may be milder. There does not appear to be a single authentic case recorded of actual second attack — i. e., due to a second infection and occurring after a period of months or years. It may, therefore, be said that one attack of rubella offers protection against subsequent infection. THE DIAGNOSIS OF RUBELLA. The diagnosis of an atypical case of rubella, particularly when occur- ring sporadically, may be attended with the greatest difficulty. In its classic form and especially during epidemic prevalence the diagnosis is a very simple problem. There is no one symptom which in itself is characteristic; the diagnosis must be made from a consideration of the composite symptomatology. Measles. — ^Measles is the disease which bears the closest resemblance to rubella, and which has, doubtless, been most often confounded with it. The differential diagnosis between these two diseases may be prefaced by the remark that a morbilliform exanthematous affection occurring as an epidemic among children who have had measles is in all likelihood rubella. A confusion between measles and rubella may arise when the former disease presents itself in very mild form or when rubella appears, as it sometimes does, with severe manifestations. The history as to the 77//'; l>fy\aNOS/S OF IWIihlLLA 563 previous occurrence in the patient, of measles or rubella is evidenee of an important elinracter. It is nncommon for measles to attack an individual twice and still rarer for rnlx-lla to act in this manner. The incubation period of rub(^lla is from five days to three weeks. Griffith regards the variable duration of this stage as comy)arefl with the fixed incubation ])eriod (abotit ten or eleven days) of measles as a feature of diagnostic im})ortance. The prodromal stage is very brief, rarely lasting more than twenty- four hours, or it may be absent altogether. Slight conjunctival redness, sneezing, and sore throat maybe present. In measles there is a distinct pre-emptive stage characterized by considerable fever and marked catarrhal symptoms affecting the eyes, nose, larynx, and bronchial tubes. The catarrhal symptoms are more pronounced in mild attacks of measles than in severe attacks of rubella. Some redness of the throat is usually present in rubella, whereas in measles sore throat may be a}>sent. Pinkish pjnhead-sized elevations are at times observed upon the soft palate in rubella. The buccal mucous membrane sometimes exhibits reddish spots. The bluish-red spots surmounted by whitish dots described by Koplik as characteristic of measles are not seen in rubella. Fever m rubella usually ranges from 99° to 101° F., rarely exceeding this. In measles fever is a prominent symptom, commonly registering 103° F. or more. It is much more protracted in measles than in rubella. The eruption in rubella spreads more rapidly, fades on one part while spreading to another, and is of brief duration (one to three days). It consists of discrete, pale rose-red, slightly elevated, pinhead to pea- sized macules. In measles the eruption spreads more slowly, reaches a maximum intensity simultaneously all over the body, and lasts for four or five days or longer, being followed by a staining of the skin. The color is a deep red, at times being bluish. The macules are larger than in rubella, irregularly grouped, often being disposed in crescents, and presenting a distinctly blotchy appearance. Glandular enlargement occurs in both diseases, but is more prominent in rubella, intumescence and tenderness of the postauricular and post- cervical glands being frequently present. Measles is not infrequently complicated by pneumonia, an occurrence which is extremely rare in rubella. Children with rubella are often so little disturbed as to complain about being put to bed. Measles is accompanied by an amount of prostration and weakness which cause the patients to seek their beds. The above differentiation w^ll suffice for ordinary cases. We occa- sionally encounter, however, attacks of measles which present anomalous features. The fever may be extremely slight, the eruption may be poorly marked, or the catarrhal symptoms may be almost in abeyance. On the other hand, severe cases of rubella are occasionally met with; con- junctival redness, coryza, and cough may be developed to an unusual degree, and the fever may be high. In other cases the eruption may be deep red, the macules may be arranged in crescentic groups, the rash persisting for five or six days. We have seen at least one case in which 564 RUBELLA the eruption could not be distinguished from that of measles; in this instance, however, catarrhal symptoms were absent. It is extremely rare to find a case of rubella which in all respects answers to the descrip- tion of a normal case of measles, and it is still rarer to find a series of cases which fulfill this requirement. Scarlet Fever. — It is quite possible to confound one form of the eruption of rubella with that of scarlatina. Many writers have acknowl- edged their inability to distinguish at times between the confluent scarlatiniform type of rubella and the scarlet-fever exanthem. In these cases other symptoms than the skin appearance must be relied upon for the differential diagnosis. The incubation period of scarlet fever is distinctly shorter than that of rubella, lasting ordinarily from three to seven days. The invasive symptoms are sudden and quite severe; vomiting occurs in the majority of cases, followed by rapid rise of temperature, usually to 103° or 104° F. There is marked sore throat, the tonsils, soft palate, and uvula being particularly affected. The glands generally are enlarged, but more especially at the angles of the jaw. The tongue is at first coated, later exhibiting the characteristic red, papillated appearance. The eruption appears first on the neck and upper chest; the face usually shows the circumoral pallor. The eruption lasts ordinarily five to six days. Desquamation occurring in flakes and most marked on the hands and feet is quite uniform. Middle-ear disease and albumin- uria are extremely common complications. It will be seen that the symptomatology is quite different from that observed in rubella. In the latter disease there is no vomiting, except in rare cases; the temperature is seldom high; the eruption begins on the face and is of short duration; the "strawberry tongue" is absent; sore throat is usually mild; desquamation when present is branny; complications are extremely rare. In addition the presence or absence of an epidemic of rubella or scarlet fever will greatly aid in arriving at a correct diagnosis. Influenza. — Forchheimer states that in the epidemic of influenza in 1892 many cases were observed in which the differential diagnosis between scarlatina, rubella, and influenza presented difficulties, at least in the beginning. There may be present in influenza an erythematous eruption, M^hich may be localized or which may rapidly spread over the body. The fever, prostration, severe gastrointestinal or respiratory symptoms and the known prevalence of the disease will serve to distinguish it from rubella. THE PROGNOSIS OF RUBELLA. The prognosis is absolutely favorable in the vast majority of cases. Deaths have been so uncommon as to attract attention by their rarity; they have invariably been due to complications usually affecting the respiratory tract. The mortality depends somewhat on the type of the epidemic and 77/ /i' TIIKATMENT OF JiUJJJ'J/J.A 505 the previous coiulition of health of the patients. Destitute airl yjoorly noiivislied cliilth'cn are rnore apt to siifFcr from complications. IvJwarfls had a mortiility of 4\ per cent. amonfiori sparse. The rash of typhoid is generally limited to the trunk, whereas the typhus spots involve the trunk and extremities, even to the hands and feet. The typhoid spots come out in separate crops and are more papular and have a more defined border than typhus lesions. The latter, moreover, tend to become petechial, when they no longer dis- appear under pressure as do the typhoid rose spots. Typhoid fever is more often accompanied by meteorism, gurgling in the right iliac fossa, diarrhoea, and the peculiar pea-soup stools. The mean duration of typhoid fever is three weeks and of typhus two weeks. In addition to the above clinical symptoms, certain tests are of importance. The agghitination reaction of Widal will aid in the diagnosis of typhoid fever, but not during the early days. Eberth's bacilli may be recovered from the spleen, or from the urine, stools, blood, or rose spots. On autopsy Peyer's patches will be found to be ulcerated in typhoid fever, but not in typhus. Relapsing Fever. — The differentiation of typhus and relapsing fever may be attended with great difficulty, particularly during the onset of the disease. In both maladies the fever rises rapidly to great height. Typhus, however, is accompanied by much more severe constitutional commotion and by greater mental disturbance; in relapsing fever the mind remains clear and the general condition remarkably good. Further- more, there is entire absence of a cutaneous eruption. At the end of five or seven days in relapsing fever the temperature subsides to normal, where it remains for a similar period, then rising and ushering in the relapse. Jaundice is observed in a large number of cases. Examination of the blood will reveal the presence of the spirillum of Obermeier. Malarial Fever. — In tropical countries and even elsewhere at times, a malignant form of remittent fever is seen wdiich may in some respects closely resemble typhus fever. The high fever is accompanied by great_ prostration and early disorder of the mental faculties. Later, manifes- tations of the typhoid state may make their appearance. Where doubt exists the examination of the blood will reveal the presence of the hsematozoa of malaria and the diagnosis will thus be rendered clear. Meningitis. — Both in idiopathic meningitis and in the epidemic variety a similarity to typhus fever may be presented through the predominance of the cerebral s3^mptoms. Cerebrospinal meningitis is, moi'eover, accompanied by an eruption which may lead to error. It is only, however, when the symptomatology is irregular that real diffi- culties in the diagnosis are presented. In meningitis the headache is more intense and of a sharp, boring character. Nausea and vomiting, which are rare symptoms in typhus, are apt to be present. Rigidity of the muscles of the neck and retraction of the head are of great diagnostic importance in meningitis. Later various paralyses develop. 588 TYPHUS FEVER Pneumonia. — In certain forms of pneumonia attended with typhoidal manifestations and masked pulmonary symptoms, there may be a resemblance to typhus fever. The rash will be absent and a careful examination of the chest will discover the presence of consolidation of the lung. Delirium Tremens. — Typhus fever occurring in persons strongly habituated to the use of intoxicating liquors may present symptoms simulating mania a potu. Insomnia, delirium, and muscular tremblings may be present in both conditions. The high fever, eruption, and course of the disease will readily distinguish typhus fever. In the eruptive stage typhus fever may be confounded with measles, with hemorrhagic smallpox, and with severe forms of purpura. Measles. — During the evolution of the eruption, the typhus exanthem, particularly when it is profuse, with a tendency to coalescence, may closely simulate that of measles. This is especially true in the case of children, in whom it may occasionally appear upon the face. Roupell believes that Sydenham was probably dealing with an epidemic of typhus fever in 1674 when he described an anomalous and malignant form of measles. Sydenham^ says: "The measles of 1674 deviated from rule, did not preserve their type; the eruption came out irregularly, was often confined to the neck and shoulders. The bran-like desquamation did not result, peripneumonia more frequently took place, and in some cases the fever would last fourteen days or more. Typhus differs from measles in many particulars, and may usually be readily differentiated. The prodromal stage of measles is char- acterized by marked catarrhal symptoms giving rise to sneezing and coughing; the fever rises gradually and not to such a height as in typhus; the face is profusely covered with the rash, which spreads downward over the trunk and extremities. In typhus the fever soon reaches its maximum, and the febrile course is longer. The rash seldom occurs on the face, the rose spots later exhibit petechial change, and the sensorium is more prof oundly affected ; patients previously attacked by measles are susceptible to the disease. . Smallpox. — The symptoms of the initial stage of smallpox and typhus fever present a striking similarity. In each disease we have chills, sudden high fever, headache, general pains, and profound prostration. Vomiting is much more frequent in variola than in typhus. The appear- ance of the characteristic eruption on the third day after the onset of the fever in variola will clear up the diagnosis. Between purpura variolosa and hemorrhagic typhus fever a differentiation is often im- possible. Both are characterized by hemorrhages into the skin and from the various mucous membranes, associated with intense prostration and death in a few days. The knowledge of the prevalence of one or the other disease will aid in the diagnosis. Purpura. — Severe cases of purpura hemorrhagica may likewise be confounded with malignant typhus fever. The former, however, is 1 Opera, p. 232. 77//'; I'liOdNOHIH, 01'' 7'V/'II(J.H FJ'JVJ'JIi 589 seldom ushered in with intense fever and the prostration in the beginning is not extreme. It is only under exceptional circumstances that a con- fusion of the two diseases would take place. THE PROGNOSIS OF TYPHUS FEVER. The wide divergence in tlie mortality rates of epidemics of typhus fever many years ago is doubtless due to the fact tliat typhoid fever, relapsing fever, and typhus fever were often confounded and considered one and the same disease. The fatality of typhus is influenced by many factors, chief among which are the age of the patient, his hygienic environment, the con- dition of his health prior to the attack, and the severity of the prevailing type of the disease. These and other influences will be considered in detail. Age. — The age of the patient influences the mortality to a considerable extent. With the exception of very young children the disease is much less fatal in childhood and youth than in age periods beyond these. Beyond the age of twenty years the mortality progressively increases, reaching its maximum in advanced old age. Below are appended three series of age statistics. In the town of Greenock, according to Buchanan, the death rate was as follows: Age. Mortality. Under 10 years 5.0 per cent. 10 to 20 ' 20 " 30 ' 30 " 40 ' 40 " 50 ' Over 50 ' 8.6 15.6 21.5 42.0 66.6 The death rates of typhus fever in the London Fever Hospital, during a period of two years and including 3506 cases, have been calculated by Murchison as follows: Age. Admitted. Died. Per cent Under 5 years 17 3 17.65 Between 5 and 10 years 1S3 14 7.65 10 " 15 " 363 18 4.95 15 " 20 " . 546 26 4.76 20 " 25 " 495 47 9.05 25 " 30 " 348 52 15.15 30 " 35 " 323 55 17.02 35 " 40 " 270 89 32.96 40 " 45 " 292 87 29.79 45 " 50 " 212 83 39.15 50 " 55 " ■ 150 78 52.00 55 " 60 " 100 51 51.00 60 " 65 " 88 49 55.68 65 " 70 " 42 28 66.66 70 " 75 " 24 17 70.83 75 " SO " 6 5 83.33 Over SO years . 2 2 100.00 Age unknown 50 11 22.00 3506 20.89 15 ' ' 20 ' 20 ' ' 30 ' 30 ' ' 40 ' 40 ' ' 50 ' 50 ' ' 60 ' 590 TYPHUS FEVER Guttstadt^ gives the figures for 5545 cases admitted into Prussian hospitals from 1878 to 1880 : Age. Males. Females. Under 10 years 2.2 per cent. 3.3 per cent. Between 10 and 15 years 3.0 " 1.5 " . 5.2 " 4.5 " . 8.2 " 10.1 " . 16.0 " 11.2 . 31.9 " 20.2 . 43.7 " 35.5 Over 60 years 57.1 " 45.2 " It will be seen that while Guttstadt's tables exhibit lower mortality rates than Murchison's, the same general influence of age is shown. Curschmann believes that the increasing death rate after the age of forty is due to the greater cardiac weakness at this period and to the increased liability to hypostatic congestion of the lungs and other pulmonary complications as a result thereof. Sex. — Sex appears to exert but little influence upon mortality. Murchi- son's figures give 19.67 per cent, of deaths in males and 18.20 per cent, in females. Hygienic Environment. — The social position and financial condition of individuals influence to a large extent the character of their surround- ings. Food, mode of life, and domiciliary environment, by modifying the physical, mental, and moral tone of persons, influence to that extent their general health and resistance to disease, and also their ability to successfully cope with disease when stricken. The mortality of typhus fever is particularly high among people debilitated by famine and hardship. Physical exhaustion, such as occurs in soldiers and among hard-worked nurses and physicians, doubtless accounts for the comparatively high mortalities among these classes of patients. The overcrowding and unhygienic conditions which often prevail in barracks, prisons, and on board ships increase not only the incidence of typhus, but also its mortality. Murchison divided the patients admitted into the London Fever Hospital into three classes, according to their social and financial condition : Admitted. Died. Per cent. 1. Pay patients " . . 94 15 14.89 2. Patients admitted free, but not classified as paupers. 2674 497 18.6 3. Paupers 738 204 27.6 It is seen from these figures that the niortality is higher according to the poverty of the patients. Murchison believes, however, that the larger death rate among the poorer patients is to be explained by the more advanced age of these persons. He states that the current opinion in Ireland is that the disease is accompanied by a higher mortality among the rich than among the poor. Intemperance and Previous Health of Patient. — It is no less true of typhus fever than of smallpox and other infections that the disease is ' Quoted by Curschmann. 77//'; I'liOCNO^IH O/'' 7'VI'l/fJS Fl'JVJ'Jli 591 particularly fatal in alcoholics. Prolonged habits of intemperance produce structural changes in tlie heart, bloodvessels, kidneys, liver, and nervous system, and weaken the d(;ferisive resources of the body when attacked by disease. In typhus fever, as in sniallj>ox, hemorrhagic attacks are more common in drunkards than in other individuals. The previous existence of chronic organic diseases or of acute diseases unfavorably influences the prognosis in typhus fever, as would naturally be expected. Debilitating illnesses which lower the resisting power of the individual, or diseases in which the structural integrity of important organs is affected, very considerably lessen the chances of recovery. Unfavorable Symptoms. — Great intensity of any or all of the symp- toms of typhus fever constitutes an unfavorable condition, yet the comparatively brief course of the disease renders it possible for patients exhibiting even the most alarming symptoms to recover. High fever during the invasive stage and the remaining days of the disease, if unattended by symptoms hereafter to be mentioned, need not be regarded as of specially unfavorable significance. If, however, the temperature continues very high during the second week, it indicates an attack of great gravity. More important than the temperature is the condition of the heart and the bloodvessels. Lic^aga regards an early disproportion between the pulse rate and the temperature as a sign of fatal omen. A pulse rate of over 120 in the beginning of typhus fever should excite solicitude. But the frequency of the pulse is not the only factor to be considered. The rhythm, volume, and compressibility of the arterial pulsations and the character of the cardiac sounds are of equal or greater importance. Inaudibility of the first heart sound or irregularity, rapidity, or marked compressibility of the pulse occurring early in the disease are bad prognostic signs. The condition of the nervous system offers valuable evidence. Early wild delirium, persistent insomnia, progressively deepening stupor, subsultus tendinum, carphologia, muscular twdtchings, and convulsions are all of evil portent. The occurrence of profound coma or coma-vigil renders the prognosis hopeless. The presence of considerable albumin in the urine during the early days of the disease indicates a grave infection. When blood and casts are associated an alarming complication is present. Pulmonary complications are commonly the cause of death, particu- larly in persons advanced in years. Hypostatic congestion, severe and widespread bronchitis, and pneumonia swell the mortality list. Cursch- mann includes marked meteorism and "pinhole pupils" among the specially unfavorable symptoms. The profusion of the rash is of less prognostic import than its special characters. The early appearance of petechise and an unusual degree of hemorrhagic extravasation into the skin are grave signs. Pronounced cyanosis of the skin, particularly of the face and extremities, indicates cardiac weakness and is, therefore, an ominous manifestation. Among the favorable symptoms are moderate intensity of the fever, 592 TYPHUS FEVER ability to sleep, preservation of the faculties of the mind, moist tongue, moderate frequency of the cardiac pulsations, and early subsidence of the pyrexia. Mortality Rate. — The death rate of typhus fever varies considerably in different epidemics, but will be found usually to be in the nieghbor- hood of 18 or 20 per cent. Murchison found that the mortality of 4787 cases of typhus fever treated in the London Fever Hospital between 1848 and 1862 amounted to 20.89 per cent. The same author collected the immense number of 18,592 cases treated in London, Glasgow, and other cities, and calculated the mortality as 18.78 per cent. Lebert gives the general mortality in his experience as 15 per cent.; Buchanan, 10 per cent. ; and Curschmann, 23.4 per cent. The mortality in hospitals is higher than in private practice. This may be in part accounted for by the larger percentage of grave and moribund cases received in hospitals. In the most severe epidemics the mortality may reach 30, 40, or even 50 per cent. During military campaigns and in famine-stricken com- munities the death rate is apt to be particularly high. THE TREATMENT OF TYPHUS FEVER. Prophylaxis. — In the prevention of such a disease as typhus fever two lines of action are to be pursued. It is of paramount importance to limit the infection, as far as possible, to the first afflicted patients. This is to be accomplished through isolation of the sick and disinfection of all articles which have come into contact with the patients. If these measures could be carried out with precision and certainty, little else would be necessary. But epidemics within recent years demonstrate that even with the employment of modern methods it is impossible to completely circumscribe the infection of the disease. It becomes necessary, therefore, to remove all those causes in a community which favor the development and dissemination of typhus. It has already been pointed out that the congregation of large numbers of people in closely crowded and poorly ventilated quarters is a potent contributory cause in the spread of the disease. When the original infection is intro- duced such conditions offer the most favorable opportunity for the development of an epidemic. In countries in which typhus is prone to appear, the health authorities should prevent the concentration of men in barracks, prisons, lodging houses, tenement houses, and the like. When this cannot be avoided free ventilation of these quarters must be insisted upon. It is likewise desirable to control, as far as possible, the movements of beggars and vagrants in crowded slum districts; it is an oft -repeated experience that these persons serve as carriers of contagion. Licdaga quotes Monjares as stating that the removal from populous centres of the crowds of beggars who swarmed the streets of San Luis Potosi caused the disappearance of an epidemic of typhus fever which pre- vailed in that town. 77//'; tiii<:.\tmi<:nt of tvi'Ikjh fkvich 593 As typhus often follows in the wake of fainijK- iiiifj warfare, the most rigid precautionary measures should he em})loyed wlien these conditions exist. Proper camp sanitation and care as to tlie feeding and housing of troops are of great importance. This was exemplified in tlie Crimean War in the relative freedom of the English soldiers as compared with the French. The English army, owing to more stringent hygienic con- trol, suffered much less from typhus fever than did the French troops. Isolation. — As is true of all contagious diseases, the tyj)hus patient must be separated from other persons during the entire periofl of his illness. This can be most effectively accomplished by .sending him to a hospital specially set apart for the purpose. No one at the present day would hazard placing a typhus patient in the wards of a general hospital. Where the patient must be treated at his home, an airy room in the upper part of the house should be selected. Carpets, curtains, and all dispensable furniture should be removed from the apartment. A communicat'ng room should be occupied by the nurse and likewise utilized to disinfect all articles leaving the sick apartment. Over the door communicating with the corridor should be suspended a sheet wet with a 5 per cent, solution of carbolic acid or a 1 : loop solution of bichloride of mercury. Whenever possible the attendants and nurses should be chosen from those who have once passed through an attack of the disease. One attack of typhus fever protects against a second in the vast majority of cases. When an immune nurse cannot be secured, the one employed had better not sleep in the sick-room. Non-immune nurses should not be permitted to go abroad among people, for fear of spreading the disease. Immunes may be permitted this privilege only when every precaution as to personal cleanliness and disinfection is taken. Intercommunication between the patient and members of his family must be strictly prohibited. Disinfection. — The destruction of the infection in all articles with which the patient has come in contact is a measure of the highest impor- tance. Mention has already been made of the frequent transmission of typhus fever in the body linen of patients. To lessen the intensity of the infection in these articles frequent bathing of typhus patients is desirable. The baths, which may be sponge or plunge baths, subserve the double purpose of reducing temperature and lessening the dissemi- nation of the contagium of the disease. The body and bed linen should be changed once or twice a day. They should be received into an appropriate receptacle containing a 5 per cent, solution of carbolic acid or a 1 : 2000 solution of bichloride of mercury. The bodily excretions should be disinfected with chloride of lime or one of the above-mentioned antiseptics. While there is no con- vincing proof that the infection of typhus is resident in the dejecta, the disinfection of the stools and urine is a wise and easily carried out precaution. Eating utensils should be thoroughly boiled before being permitted to leave the sick-apartments. 3S 594 TYPHUS FEVER The physician in attendance upon typhus patients should protect his clothing by wearing a long gown and a cap which covers as much of his hair as possible. On leaving the patient he should carefully wash his face. and hands and air himself thoroughly before seeing another patient. After the recovery of the typhus patient the apartments occupied should be thoroughly fumigated with formaldehyde or sulphur and subsequently aired for a number of days before occupancy. Walls should be whitewashed, painted, or repapered according to desire. Blankets and mattresses should be subjected to superheated steam or hot air in the disinfecting plant provided by most large cities. When such facilities are not available, blankets should be boiled and mattresses burned and destroyed. Wooden furniture should be washed with a solution of carbolic acid or bichloride of mercury. The patients' clothing should be disinfected by formaldehyde, steam, or hot air. When death occurs the body should be enveloped in a sheet saturated with a carbolic acid or corrosive sublimate solution. An hermetically sealed casket should be used and interment should be private. Ventilation. — Ventilation is a preventive measure which appears to be of greater value in typhus than in other disease. That the free admixture and circulation of fresh air in the sick-apartment or ward lessens the danger of contagion is admitted by all writers. Lebert says he found it an excellent plan, even during the severest cold of winter, to keep the windows open part of the day and night; he adds that the patients bear cold well during the continuance of fever, but are sensitive to it later. When epidemics occur in the summer months it is a good plan to treat the patients in tents. The liability of attendants contracting the disease under these conditions is distinctly lessened. The temperature of the sick-apartments should be in the neighborhood of 65° F. The floor is to be mopped with an antiseptic solution and the atmosphere kept free from dust. Nursing.' — The nursing of typhus fever is of great importance and requires the services of a trained person. The body surface should be frequently sponged with water containing a little alcohol or with a weak carbolized solution. The teeth and oral cavity require careful attention from the beginning; mild antiseptic mouth washes should be employed. Diluted Dobell's solution, boric acid water, or a diluted peroxide of hydrogen may be used. The cleansing of the mouth is of particular importance when the patient is stuporous, as the mucous membrane becomes dry and covered with mucus and blood crusts. Careful attention is necessary to prevent the development of bed- sores. Frequent ablutions of parts subjected to pressure and soiled by excretions, and the use of pads or pneumatic cushions to relieve pressure, will accomplish the object desired. Diet. — The diet is the same as that prescribed in the other acute exanthemata. During the intense febrile period the patient will desire 77//!,' Tkf'JATMI'JNT OF TV I'll US I'l'lVKIi. 695 nothinjTj hut li((ni(] iiotirislimont. Milk ;ukI hroflis iriay Ik- ^ivcn every two or three hours. As soon as the j)atient cures for soft foods he may be allowed to have soft-boiled eggs, gelatin, gruels, milk-toast, and like foods. As the disease al)ates and the appetite incTeases, a gradual return to the usual dietary may be begun. For tlie relief of thirst lemonade and the carbonated waters may be given. The diet need not be as rigid as in typhoid fever, in which disease the presence of intestinal ulceration necessitates great caution. Medical Treatment.— Although numerous remedies have been advocated from time to time for their beneficial action upon typhus fever, it must be admitted that we know of no drug which materially affects the course of the disease. When the specific cause of typhus is discovered a specific cure for the disease may be forthcoming. The most approved treatment of typhus is that which is devoted to an alle- viation of the symptoms and the maintenance of the patient's strength. Fever. — The fever in typhus often reaches a great height and calls for measures to reduce its intensity. Almost exclusive reliance is to be placed upon hydrotherapy in one form or another. In the milder cases it may suffice to employ tepid sponge baths several times a day. The application of an ice-bag or Leiter's coil to the head is a useful supple- mentary measure. When sponge baths are not sufficient to control the pyrexia recourse may be had to the wet pack, the sheet being wrung out of tepid or cold water according to the intensity of the fever. The continuous tepid or warm bath will be found to control the temperature in a most satisfactory manner; the patient may be kept for twenty-four hours or longer in a bath the temperature of which is maintained between 93° and 98° F. When the graduated bath is employed the water is at first warm, but is gradually lowered by the addition of cold water to 75° or 70° F. The Brand method of cold bathing so extensively adopted in the treatment of typhoid fever does not seem to have been systematically tried in typhus fever, although its main features are referred to in favorable terms by those experienced in the treatment of typhus. With one or other of the above hydrotherapeutic measures it will be found possible to control excessive fever. It should be remembered that the reduction of fever by these measures is merely one of the objects desired. Baths exert a tonic influence upon the respiratory and circulatory centres and allay nervous excitability. The coal-tar antipyretics should not be used except in very moderate doses. Wlien given in large doses or over a long period of time they may produce serious cardiac depression. Phenacetin, antipyrin, and lactophenin are among the most eligible of these preparations. Nervous Symptoms. — Headache is commonly so persistent and distressing as to require remedies for relief. The light in the room should be kept subdued in order to lessen retinal irritation. An ice-bag should be applied to the head, and bromide of sodium, phenacetin, or antipyrin administered. When these remedies fail to control the cephalalgia it may be necessary to give opium. 596 TYPHUS FEVER Insomnia.— Inability to sleep is a bitter complaint of typhus patients during the early days of the disease. It is well to first try the bromide of sodium in 20-grain doses, repeated once or twice during the night. In other cases chloral appears to do well, but should not be used in large doses for fear of depressing the heart. Ten grains may be admin- istered in the evening, and followed later by a 15-grain dose if necessary. Where sleep cannot be otherwise obtained it is proper to give a hypo- dermic injection of morphine. The employment of a warm or tepid bath at the sleeping hour will often materially aid in quieting nervous excitement and inducing sleep. Delirium. — The bromides, chloral, and opium may be employed to quiet excessive cerebral activity. The best result in many cases is obtained by an ice-bag to the head and a prolonged warm bath, or, when the temperature is very high, a cold bath or pack. Constipation. — In the constipation which usually exists early in the disease calomel in fractional doses may be given or a mild saline may be used. One of the disadvantages of employing opium in typhus is the aggravation of the existing constipation. When there is much fever a cold, high enema will serve a double purpose. Vomiting, when present, may be controlled by pellets of ice, carbonated or lime water, and temporary abstention from food. The late diarrhoea is best checked by bismuth internally, and starch-water and laudanum enemata. Meteorism may, when mild, be relieved by laxatives, and turpentine internally and externally. Severe " gaseous distention occurring late is a grave symptom, often defying all treatment. Alcohol. — Alcohol is a remedy of great value in the treatment of typhus, when it is used with discrimination. It should not be employed as a routine, but rather to combat special symptoms. Many patients will not require its use at all. Buchanan says that alcohol is needed in two classes of patients — those who cannot take a sufficient quantity of nourishment, and those habituated to the use of stimulants. He enumer- ates the special indications as follows: Alcoholic stimulants are most serviceable in (1) old people; (2) in cases of great prostration with low delirium and coma; (3) where the pulse is very compressible and the first heart sound feeble; also when the pulse is rapid or irregular; (4) where the extremities are cold and the surface livid; (5) where there is much congestion of the lungs; (6) where there is any erysipelatous complication. It may be given in the form of whiskey, brandy, or wine, or, as Cursch- mann prefers, in Stokes' cognac mixture, the formula of which is as follows : Ji— Cognac opt., Aquse dest oa 15 ounces. Vitelli ovi No. 1. Syrupi 6 ounces. Tablespoonful every two or three hoars. When the pulse becomes compressible, rapid, or irregular, or when the first heart sound is weak, it may be necessary to resort to other cardiac stimulants in addition to alcohol. Strychnine, digitalis, stro- 77//'; tii[<:atmi<:nt of tyi'Iius fhyku r,u7 phanthus and cafl'eine may he employed with advantage. Nitroglycerin and camphor dissolved in olive oil may he used hypf)deririieally to tide over critical moments. Pulmonary and renal (•oTri|)hc;Uions are to he treated in the same manner as when these conditions arise indej)endently. In conclusion a v^^ord of caution should be uttered concerning the necessity for constant vigilance on the part of the nurses and attendants to prevent suicidal or lioniici(hd attempts during maniacal excitement. CHAPTER XI L DIPHTHERIA. Definition. — Diphtheria is an acute infectious disease characterized by the production of a fibrinous exudate or false membrane on certain parts of the mucous surface of the body. The regions by far most commonly involved are the tonsils, the pillars of the fauces, the soft palate, the uvula, the pharynx, and the nares. Not infrequently the disease extends into the larynx; or it may begin there primarily and remain limited to this locality. Except at the onset, or when there is laryngeal involvement, febrile reaction is not a prominent symptom. The disease is caused by a specific micro-organism and begins as a local affection, but becomes systemic as the result of absorption of toxins elaborated by the specific bacilli and, perhaps, certain associated bacteria. In severe cases the toxaemia may be extreme. After the general symptoms have disappeared, paralysis is liable to follow. This may be limited to a few muscles, or there may be complete ataxia. History. — Of the various diseases belonging to the infectious group, which have prevailed from time to time in epidemic form, diphtheria is believed to be one of the oldest. Some writers have sought to prove that it was known at the time of Hippocrates, and described under the name of Malum vEgyptiacum. While in the absence of suflBcient literature on the subject this cannot be determined definitely, yet it is true that Aretseus, a Greek physician of Cappadocia, who lived in the latter part of the first and the beginning of the second century, portrayed the critical features of this malady in language which warrants the belief that the disease he described was diphtheria. He speaks of a thick, white, moist material which forms over the tonsils and spreads over other parts of the mouth; of ulcers which appear on the tonsils, and which may be superficial and benignant, or extensive, putrid, and malignant, according as the case is mild or severe. In malignant cases the foetor from the mouth is loathsome. Fluids are sometimes regurgi- tated through the nose in the effort of swallowing, the voice is husky, and when the disease extends into the air passages death speedily results from suffocation. He mentions that the disease is most common among children. Aretseus believes that this malady originated in Egypt, Syria, and especially in Coele, Syria; hence the name of Malum ^gyptiacum. It was also known by the name of Egyptian and Syrian Ulcerations. During the fourth century a disease presenting the same symptoms prevailed in epidemic form in Rome, and was described by Macrobius. From this time forward for several centuries there seems to be a paucity of literature upon the subject; this may possibly mean that there was a long lapse of epidemic prevalence of the disease. DII'll'I'III'llilA 509 In the sixtecntli, sevciitctuitli, and (M^litcciitli (•(•rlfllri(^s (;[)i'leirii(.'.s of a disease presentui<:j tin; (isscntial cliaracterislics of dijjiitlieria arc said to have prevailed frequently, and often with great virulence in many parts of Europe, particularly in Holland, Spain, Italy, France, and Germany. The affection apj)eared also in England, and was described by Fothergill, Iluxham, and others. In Sy)ain the flisease was known by the name of fregar when confined to the fauces or the cavity of the mouth, but when it appeared in the laryn.x and caused suffocation it was called garotillo. In the different countries in which the disease appeared it was described by tlie physicians under various names, such as, besides those already mentioned, cynanche maligna, cynanche contagiosa, angina mahgna, angina gangrjcnosa, ulcerative sore throat, malignant sore throat, morbus suffocans vel strangulatorius, epidemic croup, etc. It is not known exactly when this malady made its appearance in America. In 1771, Samuel Bard, of New York, published a brochure entitled, '^An Enquiry into the Nature, Cause, and Cure of the Angina Sujfocativa, or Sore Throat Distemper, as it is commonly called by the inhabitants of this City and Colony." In this article a clinical descrip- tion is given of a disease comparable in its essential features to diph- theria. It prevailed chiefly among children under ten years, and was evidently infectious. Bard says the disease began as a sore throat, which, upon examination, showed that the tonsils were swollen and inflamed, and presented a few white specks which, in some cases, increased so as to cover the entire surface of the tonsils "with one general slough." The swelling was sometimes so great as to interfere with deglutition. In other cases there was difficulty of breathing, which was often of so great a degree as to threaten immediate suffocation. In his brochure Bard speaks of an article previously written by Douglass, of Boston, describing a new epidemic of an acute throat affection which was seen in that city, and which was quite similar in its clinical manifestations to the disease which later appeared in New York City. It must be said that these clinical descriptions by the earlier writers were not very exact, and that doubtless several diseases were not infre- quently included in the same category. It is safe to assume that some of the anginose affections other than diphtheria, especially scarlatina, were not always differentiated. Indeed, Bard speaks of "inflamed and watery eyes, a bloated and livid countenance, with a few red eruptions here and there upon the face," as being among the earlier sATiiptoms in many of the cases that came under his observation. Likewise, Douglass characterized the disease he described as "An Eruptive Miliary Fever, with Angina Ulcusculosia." In regard to the history of diphtheria in America, literature shows that the peculiar form of sore throat described by Douglass was seen about 1735 in certain inland towns in New England, and gradually spread westward, reaching the locality of the Hudson River two years later. The disease prevailed more particularly in towns to which people 600 DIPHTHERIA resorted for trade, and was spread by means of commercial intercourse and travel. In New York an epidemic was noted by Father Middleton in 1752. After Bard's description of the disease in 1771 very little seems to have been said about its presence in New York until 1826. From 1855 to 1858 it prevailed in some parts of the State, especially in Albany, with great malignancy. In 1856 Dr. J. V. Fourgeand published a monograph on a terrible ep demic of sore throat which occurred in San Francisco and other towns of California. An epidemic of a similar affection occurred in Philadelphia as early as 1809. Again in 1831 another epidemic prevailed. The records of the Health Office of Philadelphia, however, do not show that any deaths occurred in this city from "diphtheria" until 1860, during which year the number reached 307. From the preceding historical facts it is quite evident that diphtheria was not a newly imported disease in Philadelphia in 1860, but that it previously prevailed under other names. The earliest accurate observations on the clinical manifestations of diphtheria were made by Bretonneau, of Tours, in 1821, when he presented his first celebrated paper on the subject to the French Academic de M^decine. This paper, it is said, was not published until 1826. The name he suggested for the disease was Le Di'phtherite, or Diphther- itis. He gave it this name because of its essential characteristic, namely, the formation of a false membrane. Subsequently the name diphtheria was proposed by Trousseau. This title, as Flint suggests, has the negative merit of not involving any hypothesis as to the pathology of the affection. Bretonneau, however, believed that the membranous exudate itself constituted the pathological criterion for the disease ; that an inflammation without an exudation is not a diphtheritis, neither is an inflammation with an exudation when it is not infectious. In other words, he not only regarded the exudate as an essential part of the disease, but also as constituting the only source of the infection. He believed the contagium spread, not through the atmosphere, but by inoculation, as it were, resulting from particles of the exudate, either in a fluid or dust-like state, coming in immediate contact with the moist mucous membrane. Bretonneau's observations, which were quite extensive, led him to conclude that membranous croup and diphtheria were identical affec- tions ; the only difference being that in croup the disease process extended into the larynx and trachea. He at first fell into the error of regarding diphtheria as wholly a local disease, but later frankly admitted that systemic poisoning was an essential pathological condition. Angina gangrsenosa, he declared, is in no way related to this affection. Trousseau with his acute power of clinical observation directed attention to the difference between diphtheria and some of the throat affections, especially scarlatina, with which it was often confounded, and also pointed out the danger of this disease from its liability to extend into the air passages. The fact that death not infrequently resulted i>ii'iri'iii<:itiA 00] at an early period of the diseast; from an adynamic conrlition wa.s observed by him and e,s])ecially commented upon, lie is credited with rendering vahiable assistance to Bretonneau in establishing the operation of tracheotomy for tli(> r(;lief of membranons croup; even th(; inriications given by liim for its adoption woidd still s(!rve as a useful guide for u.s at the present day. Recognizing that the disease was primarily local, Jiouchut recom- mended the removal of hypertrophied tonsils when covered with an exudate, with the object of preventing the membrane from extending downward into the larynx and trachea. He was the first to practise "tubage" of the larynx for relief of the stenosis caused by membranous croup. This procedure, however, was condemned and fell into disuse for nearly a quarter of a century, when, in 1880, it was revived and brought to a high state of perfection by O'Dwyer, of New York. Intubation is now almost universally regarded as an indispensable auxiliary in the treatment of membranous croup. After Bretonneau's publication appeared diphtheria was recognized and described by the physicians of every civilized country, and there soon developed a wealth of literature upon the subject. Many excellent works were published by French, German, and English waiters. There w^ere, however, some conflicting notions regarding the nature of the disease. Some maintained that it began as a general systemic infection, entirely independent of any previously existing local affection. In other words, the exudate was regarded as a local expression of a constitutional disease, manifesting itself by preference upon the mucous membrane of the fauces, just as the rash of scarlet fever does upon the skin. This view was opposed by most of the ablest writers, and in the light of our present knowledge is regarded as untenable. The question about which there was perhaps the greatest difference of opinion was whether diphtheria and membranous croup were identical affections, or whether they constituted two distinct morbid processes. It may truly be said that physicians of the present day are not yet entirely agreed on this question. Bretonneau, Wagner, and many others contended that no clinical or pathological distinction between these diseases could be made, while Virchow threw the w^eight of his authority on the opposite side of the question. This distinguished pathologist sought to establish an anatomopathological distinction. He believed he had succeeded in showing that in the croupous form of inflammation the exudation is deposited upon the surface of a sound mucosa, while in diphtheritic inflammation the exudation takes place into the very substance of the mucosa as well as upon its surface, and that this mem- brane undergoes interstitial necrosis from want of nourishment caused by compression of the bloodvessels. This attempt to distinguish between membranous croup and diphtheria has been unsuccessful, and the leading clinicians and pathologists now admit their specific identity. The consideration of diphtheria has assumed a new phase since bacteriology has become so important a hand-maiden to the clinician. 602 DIPHTHERIA The study of micro-organisms in their relation to this disease dates back over a period of many years, even more than a quarter of a century. In 1868, Oertel, together with Buhl and Hueter, discovered bacteria in the false membrane, the blood, and in certain tissues of patients, which he believed sustained a causal relation to the disease. He described these organisms as presenting various forms, such as spherical, rod-like, and corkscrew-shaped. They were also demonstrated by von Recklinghausen, Nassiloff, Waldeyer, Klebs, Eberth, Heiberg, and others. While these investigators were evidently working along the right lines, and may have seen the specific bacillus, yet they failed to differentiate it from its associates. The credit of discovering the true bacillus of diphtheria belongs to Klebs, of Zurich. It is generally stated that this discovery was made in 1883, but Lennox Browne makes the following statement in reference thereto: "Professors Hamilton and Sternberg have drawn attention to its discovery by the same observer (Klebs), and to publication of the fact at a congress held at Wiesbaden so far back as the year 1875. The circumstance appears to have attracted but little attention, notwith- standing that on examination of the original reference it is found that Klebs had announced at this date that he had not only detected the bacillus, but that he had also made an effort to cultivate it, and, as far as one can judge, successfully. To Klebs, therefore, the credit of having discovered this organism is undoubtedly due. But since he never definitely announced that he had been able to obtain pure cultures of it, it must be said that he failed in establishing its causal relationship to the disease." This relationship was later established in 1884 by LoeflQer, who succeeded not only in obtaining pure cultures of the bacillus, but also in proving its specific character by communicating diphtheria to guinea- pigs and birds by inoculating them with this organism. Hence, through the combined labor of these two investigators, in discovering and establishing the specificity of this micro-organism, it is known by the name of Klebs-Loeffler bacillus. This discovery has had the effect of settling the long and often animated controversy as to whether diph- theria is primarily a constitutional or local affection in favor of the latter, and has placed the study of the disease on a scientific basis. THE ETIOLOGY OF DIPHTHERIA. In considering the causation of diphtheria in the light of our present knowledge it might be thought sufficient to give simply a description of the Klebs-Loeffler bacilli and the associated bacteria, with an explana- tion of their causative relation to the local and systemic manifesta- tions of the disease. This is the course pursued by many writers of the present day. But while it is impossible to convey a correct knowl- edge of the etiology of diphtheria without carefully describing its bac- teriology, yet for a comprehensive understanding of the subject it is necessary also to consider the predisposing causes as well as the means 77//'; I'VriOIJXIY f>F DII'IITIIHIilA 603 by which the disease may l)e disseminated, and tfie (■onditions favrjrable for its spread. The disease is (lontagious. While sporadic cases may be met with, yet when it once obtains a foothold in a community it is j>artionlarly prone to assume an epidemic character. The evidence of its infectiousness is very conchisive. When diphtheria appears in a family it frequently attacks many members in succession. The fact that some meml^ers of the family often escape is no evidence that it is not contagious, for this not infrequently hap})ens with scarlet fever, the contagiousness of which no one doubts. In regard to such instances it may be said that ever so little positive evidence outweighs any number of negative facts. Further evidence of its contagious nature is found in the fact that physicians and nurses in attendance upon cases very frequently contract the disease. In the Municipal Hospital of Philadelphia most of the resident 7>hysicians who have worked in the diphtheria wards have suffered from the disease in variable degrees of severity. In one instance the attack was so severe that death resulted at an early stage. The majority of the nurses have shown symptoms more or less marked soon after beginning work in the wards. It is not unusual for physicians and nurses who have been in attendance upon cases in private practice to be admitted to the hospital suffering from the disease. Not infrequently diphtheria has been communicated by direct contact with detached pieces of exudate or the secretions from the throat and nose of patients. We have known nurses to show symptoms of the disease within forty-eight hours after having had coughed into their faces some of the infectious material from the throats of patients. We have likewise known infection to result from kissing. ]\Iore than one physician has fallen a victim to diphtheria through his zealous efforts to save the life of a patient by clearing out an obstructed tube after tracheotomy by suction, or by trying to inflate the lungs after the oper- ation by blowing his own breath into them through a tube. Oertel says: "In this way Otto Weber, Seehusen, Valleux, Blache, Cillite, fell sacrifices to their professional devotion. Dr. Wiessbauer, of Munich, lost his child, who had a short t'me previous to its death unfortunately gotten hold of a cannula and put it in its mouth, the cannula having just been removed from a patient sick with diphtheria." Still further evidence that the disease is infectious is found in the fact that it has been com- mvmicated to some of the lower animals experimentally by inoculation. It is well known that diphtheria, like all contagious diseases, some- times occurs sporadically, at other times endemically, and then again epidemically. In attempting to explain these circumstances one must take into consideration not alone the causa causans, or the specific germ of the malady, but also the causa efjiciens, or that which determines the occurrence of widespread epidemics. In studying the latter it is neces- sary to enquire into the sanitary surroundings of each particular locality where the disease prevails, and into all conditions which may influence individual receptivity to the infection, such as climate, domestic environ- ment, age, sex, rainfall, season, etc. 604 DIPHTHERIA Geographical Distribution. — No country can be said to be absolutely exempt from diphtheria, although it prevails to a much greater extent in some places than in others. The disease has invaded both hemi- spheres, and it has occurred in the northern and southern portions of each. Altitude seems to exert but little influence over its spread, as it has been found in both high and low-lying countries. According to statistics of the United States, however, it has caused the greatest proportion of deaths in the Southern Central Appalachian region, the Central Appalachian reigon, and the region of the Western plains; while the proportion of deaths was least in the South Atlantic coast region and the Gulf coast region. The disease occurs in the higher degrees of latitude ; but of all localities it is most common in the temperate zone and that part of the frigid zone immediately adjacent thereto, and least common in the tropics. The records of India show that it is rare in the tropical climate of that country; nor does it thrive anywhere in the tropical parts of Asia. It is also rare in Central and South America. Conditions of the Soil.' — Some writers have ascribed to the soil a certain influence over the propagation of the disease. It was a common impression among the older writers, and, indeed, some of the more modern still hold to the opinion, that low, damp soil, such as is found in marshy regions with bad drainage, especially near rivers which frequently overflow their banks and where there is a good deal of vegetable matter undergoing decomposition, favors the development of diphtheria; while, on the other hand, a high, dry soil, or a soil composed largely of dry sand has been regarded as unfavorable to the spread of the disease. At least, some observers claim that it appears less frequently and is less likely to be disseminated in localities characterized by the latter geological conditions. While it is recognized that for the production and propagation of diphtheria the presence of the specific micro-organism must be regarded as a sine qua non, yet it is not improbable that these organisms may thrive under certain conditions and perish under others. Whether soil in any of its forms exerts any such influence one way or the other is uncertain. At times it does appear as though such an influence was especially marked, yet statistics show that the disease has occurred and even prevailed in epidemic form in districts where the local con- ditions were regarded as unfavorable for its spread. According to Lennox Browne, epidemics of diphtheria in England "have been very catholic in their distribution from both the geographical and the geological aspect." But an interesting table compiled by him seems to justify the belief that the disease has a decided preference for a clayey soil. This table bears out the opinion of Dr. Thorne Thorne, whom he quotes as saying that "where a surface soil is, by reason of its physical constitution and topographical relations, such as to facilitate the retention of moisture and of organic refuse, and where a site of this character is, in addition, exposed to the influence of cold and wet winds, there you have conditions which tend to the fostering and fatality of 77//'; F/riOLOdY OF DII'irrilFiilA OOo diphtheria, and also go to determine the specific (juality of local sore throat." The marked predilection of the disease for wet, clayey soils ha,s been commented upon by many writers, some of whom have yjointed out that diphtheria is not only more common but more fatal in localities with wet and retentive soils than in those with dry and pervious grounrl conditions. Evidence could be cited tending to show that the disease is fostered by decomposing heaps of manure and vegetable refuse, such as are found about stables where sheep, cattle, and other animals are kept. Outbreaks of diphtheria have been reported where this condition existed in close proximity to dwelling-houses. The drainage from decomposing animal and vegetable matter imparts to the soil a .serious contamination. The digging up of old drains, especially those connected with dwelling-houses, has been followed more than once by an outbreak of diphtheria. Surely the upturning of soil thus polluted is a fertile source of diphtheroid sore throats, or pseudodiphtheria, if not of the true disease itself. At any rate it cannot be denied that the emanations from such a source act as a predisposing cause to precipitate an attack when the diphtherial entity is present. Rainfall. — The question as to whether the annual amount of rainfall exerts any influence over the prevalence of diphtheria or its mortality has not been positively determined. Statistics have been cited to prove both the positive and negative sides of the question, and are, therefore, conflicting. After fully considering the evidence at hand we are inclined to believe with most writers that rainfall is not a very important factor in determining the diffusion of the disease. Season.^ — Diphtheria is undoubtedly much more prevalent during the cold-weather months than during the summer. This is shown very clearly by the statistics of all countries where the disease prevails, and is made especially clear in the last census report on vital statistics of the United States. While the returns of deaths in this report are, for obvious reasons, incomplete, yet they are sufficiently complete for comparative purposes. Of course, the number of cases of diphtheria is not given, but the number of deaths by months may be regarded as a fair index of the prevalence of the disease for the same periods. The following table shows for the United States the deaths by months from diphtheria in the census year 1900: Months. Deaths. Months. Deaths. January 1816 July 827 February 1496 August 89S March 1411 September .... 1303 April 115S October 1739 May 1081 November .... 1912 June 795 December .... 1904 This table indicates that diphtheria (including croup) is most prev- alent in the United States during the nine months beginning with September and ending with May, and least prevalent during the summer months of June, July, and August. The three months showing the greatest number of deaths are November, December, and Januarv. 606 DIPHTHERIA By dividing the year into quarters, representing the four seasons, we find the number of deaths for each season to be as follows: spring, 3648; summer, 2510; autumn, 4954; winter, 5246. The winter months, and especially the autumn and winter months, show by far the greatest proportion of deaths. The following table shows the admissions by months of diphtheria patients into the Municipal Hospital of Philadelphia during the last decade : Year. Jan. Feb. Mar. April May June July Aug. Sept. Oct. Nov. Dec. 1893 .... 36 24 21 ■J 16 24 7 13 5 21 26 17 1891 15 2ii 33 . 20 28 25 38 33 39 70 81 64 1895 65 65 66 46 56 54 68 61 38 48 66 73 1896 (i2 54 67 48 74 60 44 45 66 86 122 141 1897 107 97 76 87 61 105 109 112 87 145 149 150 1898 137 78 71 84 88 73 76 84 121 146 146 125 1899 117 72 81 83 109 103 94 139 110 123 178 164 1900 143 126 119 95 102 102 92 94 :08 133 141 112 1901 101 87 98 97 80 76 47 53 66 62 53 69 1902 89 58 59 45 51 55 36 611 25 36 52 46 45 Total 872 681 691 612 665 677 659 676 886 1008 960 This table also shows that the disease was most prevalent during the months of November, December, and January, and least prevalent during the three summer months. Considering the table as a whole, the total number of cases in each of the four seasons is as follows: spring, 1968; summer, 1937; autumn, 2560; winter, 3513. It will be noticed here that the autumn and winter months furnished by far the largest number of cases. This is in accordance with the observation of many writers. Newsholme says: "Diphtheria is most prevalent in autumn and in the early winter months, when the opti- mum temperature and the optimum degree of humidity of the soil are rapidly disappearing or have departed. It is also most prevalent after the wet weather, occurring in or immediately following exceptionally dry years. Both these conditions tend to raise the ground water and to drive out any pathogenic micro-organisms from the soil." The greater prevalence of diphtheria during the cold -weather months can be rationally explained, we believe, by the well-known observations that the fauces and upper air passages are then much more liable to attacks of catarrhal inflammation, thus affording an increased suscepti- bility to the disease, and that the sanitary surroundings in schools and dwelling-houses at this time of the year are apt to be at their worst. Domestic Environment.— Under this head might be included the unsanitary conditions of domestic life, such as result from the crowding together of a large number of people into tenement houses, narrow streets, courts, and alleys, where, besides the crowding, the drainage is bad, and the air almost necessarily impregnated with animal emana- tions and all kinds of foul odors. Surroundings of this nature are sure to prejudice health and exert a definite influence in determining an outbreak of diphtheria and favoring its spread. It is a matter of common Till': F/riOLOCV of UWIITIII'IKIA {]()- observation in all i;u-n;e cities when; this fiisc^ase is eiifleniic that the inhabitants of such localities sufler to the f^reatest extent. While j^ersons who live under more favorable circumstances are not spared, yet the transmission of the infection is particularly favored by poverty and uncleanliness. Not alone do overcrowded conditions of rlwcllin^-houses favor the propaf];ation of diphtheria, but in all congested institutions, especially those for the care of children, in factories, schools, barracks, and, in short, wherever there is a large aggregation of persons living under unhygienic environments, there the disease is wont to break out and assume an epidemic form. But, as already stated, more favorable modes of living do not ensure safety against the ravages of the malady. Oertel very truly says: "Robust children who enjoy the best of care and nourishment are seized and carried off by the disease, although the number of such cases does not reach that attained in other classes, in which poverty and uncleanliness favor the spreading of the pestilence." Even the rich and cultivated dwellings, under the most modern sanitarj- improvements of ventilation, plumbing, drainage, and the like, have furnished a fair quota of victims to this fell destroyer of human life. This shows that the specific organism of diphtheria is no respecter of persons; nevertheless, certain environments or conditions of life exert a very potent influence over the spread of the disease. Dissemination of the Infection. — The infection of diphtheria is commonly communicated through direct exposure to a person suffering from the disease. The dust from a sick-room, contaminated with particles of dried secretions from the throat and nose of a patient, may serve to convey the infection for a short distance through the agency of the atmosphere. The well members of a family in which the disease exists often unwittingly carry the contagium to others. It is frequently disseminated, especially where no attention is given to disinfection, by means of infected articles, such as clothing, bedding, towels, handker- chiefs, carpets, drapery, upholstery, books, toys, and the like. It must be admitted that physicians and nurses are sometimes the agencies of transmitting the infection. Even pet animals may play a part in this baneful work. Doubtless the disease is often spread by exceedingly mild cases — so mild, indeed, that the symptoms are not correctly interpreted. Of course no restrictions are placed on the movements of persons thus mildly afflicted. Adults continue at their daily vocation, and children go to school as usual. Such cases are constantly met with, especially in large cities where diphtheria is endemic. It is well known that some cases of chronic rhinitis are really of a diphtheritic nature, inasmuch as the Klebs-Loeffler bacilli are sometimes found in this disease. "When this condition exists, it is frequently not recognized, and therefore no restrictions are enforced, nor even any precautionary measures advised. Really, it is a question whether the mild and unrecognized cases of diphtheria are not much more often responsible for the spread of the disease than the severe cases, for the latter are usually surrounded with (308 DIPHTHERIA the proper sanitary measures, such as isolation, disinfection, and the like. Yet it should not be overlooked that after recovery from a well-marked attack patients not infrequently leave their homes and associate with the public before their throats are free from the bacilli. Experience shows that these organisms sometimes remain in the nose and throat in a virulent form for five or six weeks, and at times much longer, after the clinical symptoms have disappeared. Then again, it is not impossible for the disease to be spread by well persons in whose throats the bacilli are present. It has been estimated, by an able observer, that these organisms may be found in the throats of about 2 per cent, of all well persons. Milk has been charged with spreading diphtheria. In order that it should play this role the infection must be introduced through outside contamination. Once introduced, bacilli will find in milk a good culture medium in which to grow and multiply. In the reports of the majority of epidemics which were believed to have been caused by the milk supply, it is stated that either diphtheria prevailed at the dairies or the milk cans were washed with contaminated water. In some instances it is said the cows showed on their teats and udders inflam- matory conditions. After carefully studying a number of reports on epidemics alleged to have originated from infected milk, we feel obliged to say that the contention is supported only by very strong presumption that the milk was at fault. There is no evidence that amounts to absolute proof. So far as we know the Klebs-Loeffler bacilli have never been found in any of the suspected milk. A few years ago the Board of Health of Philadelphia collected samples of milk from sixty-two houses in which diphtheria prevailed and subjected them to careful bacteriological examination, but the result in every instance was negative. In this connection it might be well to add, on the authority of I^ennox Browne, "that the bacillus when grown in milk loses many of its chief character- istics, or, perhaps, it would be more correct to say it assumes others peculiar to its culture medium. It probably undergoes degenerative changes with rapidity; possibly these are due to the presence of lactic acid." Schools are commonly regarded as an important factor in the spread of diphtheria. It is a matter of observation in large cities where the disease is constantly present that the number of cases increases soon after the opening of the schools in autumn, and that the number is smallest during the summer vacation. The rules created and enforced by health authorities, excluding from school all children suffering from sore throats, and all those from families in which diphtheria exists, have done much to limit the spread of the disease. But in spite of this wise sanitary measure it not infrequently happens that children attend school while suffering from mild and unrecognized forms of diphtheria, or, at least, in whose throats virulent bacilli are present. Outbreaks of the disease in certain districts may often be explained in this way. On the contrary, efforts have been made to show that congregation in Till': hyrioLoav of hii'irriii'iniA (;0J> schools is not a common cause of cj)i(Jemics. In supjxjrt, of this negative view it has been pointed out that the mortality from diphtheria is by far the greatest among children imder five years, who have not yet arrived at the school age. Jt has been stated also that there frequently is a great increase of its prevalence in sf;hools irnmefliatcly after a holiday recess. The latter statement is undoubtedly true of boarding schools and kindred institutions; but when diphtheria breaks out in such a school it is aj)t to cause not only a local epidemic, but so great alarm among the pupils as to occasion a stampede, and thus the disease is often widely disseminated. When the infection is introdijced into a family it is not surprising that the younger children — those who have not yet attained to the school age — should be the principal sufferers. Therefore, the fact that the greatest mortality is found to be among children under five years does not invalidate the view that schools operate as an important factor in spreading diphtheria. While writing these lines a late issue of American Medicine comes to hand containing this paragraph: "Diphtheria of a somewhat malignant type is reported to be raging in Milton, Mass. The disease first appeared among the pupils of one of the public schools, and afterward spread to such an extent that the school was ordered to be closed. At this time there were 28 cases in the immediate neighborhood." Like all infectious diseases, diphtheria is most rapidly disseminated in countries and localities where there is the freest personal inter- communication. Hence, it is by far more common in urban than in rural communities. After having illustrated this fact in diagrammatic form, Newsholme says: "The whole of Michigan, which has a large proportion of rural population, has much less diphtheria than the neighboring city of Chicago; the whole of INIassachusetts has less diphtheria than Boston or New York; the whole of England less than London; the whole of Japan less than its great towns; the whole of South Australia less than Adelaide." Constitutional Predisposition.— The presence of catarrhal affections of the mucous membrane of the nose and throat seems to increase the liability to diphtherial infection. Children who suffer from adenoid growths in the pharynx, with chronic inflammation of the nasopharyngeal region, and from enlargement of the tonsils are regarded as being particularly susceptible to the infection. When these conditions exist together they usually cause what is known as mouth-breathing, by which act the air, instead of being warmed and filtered by passing through the nares, goes direct to the fauces cold and irritating, and, perhaps, laden with germs. Lennox Browne writes: "My personal experience leads me to say that diphtheria hardly ever, if ever, occurs in a child under seven years of age who is not the subject of one or other of these forms of glandular overgrowth. It appears needless to enforce their tendency to abrogate the hygienic function of the nose as the first avenue of respiration and to induce the marked deficiency in vitality and resisting power to contagion which are to be found in all such children." 39 610 DIPHTHERIA Everyone knows that the first evidence of diphtheria is commonly seen on the tonsils. It would, therefore, appear that these glandular organs were the most vulnerable part of the body for attack by the Klebs-Loeffler bacilli. The peculiar anatomical structure of the tonsils, having on their exposed surface deep crypts or lacunte into which the organisms may lodge and multiply, affords a very probable explanation why they are so often the seat of the disease process. When these glands are inflamed and swollen the lacunae become deeper and the mucous covering so delicate that they have been not inaptly compared by Virchow to open wounds. Hence, it is easy to see how this condition may increase susceptibility to diphtheria. Certain other diseases with anginose manifestations also furnish a marked predisposition to diphtheria. Of these we would mention particularly scarlet fever and measles. The frequency with which the Klebs-Loeffler bacilli are found in the throats of scarlet-fever patients is really astonishing; according to our experience at the Municipal Hospital they are present in 10 per cent, to 33 per cent, of all cases. Indeed, they are often found when the clinical conditions would not suggest the existence of diphtheria. These two diseases, however, not infrequently coexist, the symptoms peculiar to each appearing at the same time. But symptoms of diphtheria may develop during the course of scarlet fever or during conva'escence. As might be expected from what has already been said, the catarrhal affection of the fauces and upper air passage incident to measles renders the individual very responsive to the action of the diphtheria bacillus. Membranous croup associated with measles is by no means an infre- quent occurrence, and, moreover, is exceedingly fatal. When measles prevails in Philadelphia we have numerous applications for the admis- sion to the Municipal Hospital of cases complicated with membranous laryngitis. Many of them belong to the true type of diphtheria, but others, it must be admitted, are probably caused by other bacteria, as- the diphtheria organism is not always found. The predisposition to diphtheria varies greatly in different persons, and often quite independently of any known abnormal condition of the throat. Children are much more susceptible than adults. The pre- disposition is undoubtedly much more strongly marked in some families than in others. This may be explained on the supposition that in the more susceptible families there is an inherited tendency to the develop- ment of some form of chronic catarrh of the mucous membrane of the throat, thus favoring the operations of the bacilli. Some writers believe that infection through a healthy mucous membrane, if not impossible, is very unlikely. Recurrent Attacks. — In most infectious diseases one attack usually confers immunity against subsequent attacks. This is particularly true of measles, scarlet fever, and smallpox. But with regard to diphtheria this announcement cannot be made with equal stress, as recurrent attacks are by no means rare. We have frequently seen patients suffer from a second attack before leaving the hospital. Also children have been 77//'; I'JTfOLOaV OF DII'IITIIFUIA ()]] admitted to the hospital a second time, and, in two or thn^e instances, a third time sufl'ering from diphthc^ria, after intervals of a few weeks to three or four years. Age. — The (h'])htli(M-ial infection finds in childrfui the most favorahlf soil for its reception and propagjition. Th(; disease is exceedingly common amonj^ children up to the age of ten years, but those from one to five years are most susceptible. Some writers state that diph- theria attacks but seldom infants under a year old, and that in the first half-year of life there is complete immunity to the disease. It has fallen to our lot to see a large number of infants suffer and perish from this scourge, and many of them were under the age of six months. We believe, however, the infection is not so readily received at this early age. Adults not infrecpiently acquire the disease; but their chance of escaping it or of recovering when attacked is much greater than is the case with children. It is a recognized fact that in all epidemics of diphtheria as well as in endemics children are the first to suffer from the disease. They also furnish the principal part of the mortality. This will be considered more fully under the head of prognosis. It is worthy of notice that the laryngeal form of diphtheria is limited almost entirely to children. The following table shows the diphtheria patients admitted to the Municipal Hospital of Philadelphia during the last decade classified into age groups: Under 25 years and Year. 1 year. 1-5 yrs. 5-10 yrs. 10-15 yrs. 15-25 yrs. upward. Total. 1893 1894 1895 1896 1897 1898 1899 1900 1901 1902 217 16 218 120 31 52 28 465 26 327 187 46 56 65 706 33 404 276 71 49 36 869 34 560 437 126 89 49 1295 42 652 447 93 47 48 1229 38 659 462 102 62 50 1373 40 595 473 117 90 52 1367 30 374 287 106 56 36 889 38 305 159 40 33 26 601 Total 299 4076 2901 750 570 418 9011 This table bears out the statement that children from one to five years of age are most susceptible to diphtheria; and also shows that the susceptibility diminishes very considerably after the age of ten years. We would direct attention to the table as showing the large number of infants that have come under our care. As parents are naturally loath to send children of this tender age to a hospital it is not improbable that the table shows a smaller proportion of patients under the age of one year than if the entire number in the city were considered. Sex. — It scarcely seems probable that sex should exert any influence over susceptibility to diphtheria. It has been stated, however, by some observers that up to the age of four years there is no difference in suscept- ibility, but subsequent to this age males suffer more frequently than females. 612 DIPHTHERIA The last census report of the United States shows that for the census year the deaths were quite equally distributed between the two sexes — 14,878 were males and 14,081 were females. This very extensive statistical evidence warrants the conclusion that predisposition to the disease is not influenced by sex, and that where any disparity is found it is accidental rather than otherwise. The following table shows the number of patients admitted to the Municipal Hospital each year during the last decade divided as to sex: Year. Males. Females. Total. 1893 .94 123 217 1894 214 251 465 1895 315 391 706 1896 ........... 424 445 869 1897 636 659 1295 1898 562 667 1229 1899 641 732 1373 1900 669 698 1367 1901 416 473 889 1902 285 316 601 Total 4256 4764 9011 It is worthy of remark that of the diphtheria admissions to the Municipal Hospital, Philadelphia, the females have exceeded the males. The table shows that this was the case every year during the last decade. Race. — It cannot be said that race plays any prominent part among the predisponent causes of diphtheria. The opinion expressed by some observers that the Jews are especially liable to the disease cannot be accepted in the absence of positive proof. It is true in some of the large cities of this country the Russian Jews furnish a large contingent of the cases admitted to hospitals for infectious diseases, but this may be explained by the unsanitary environments of these people. The colored race has been thought to possess a considerable degree of immunity, but we have found no material difference between the death rates of the white and colored patients. THE BACTERIOLOGY OF DIPHTHERIA. In 1883 Klebs first observed and reported the constant presence of a bacillus in the false membranes in diphtheria patients. The following year Loeffler^ isolated these organisms in pure culture and demonstrated their pathogenic power by reproducing the disease by inoculation of the mucous membranes of animals. Roux and Yersin^ studied the effects of the diphtheria toxin elaborated by the bacilli, an investigation which led up to the development of serotherapy. By 1891 the requisite postulates of Koch concerning the specificity of the germ had been fulfilled as regards the diphtheria bacillus. Its 1 Mittheil. aus dem Kaiser. Gesundheitsamte, 1884, Bd. xi. '•i Ann. de I'Institut Pasteur, 1888-1889. PLATE LVII. K.O b. Colonic ^ iif i)^eu(ii)ili|)hll)oria b.ifilli. X KiO. ^•. ('(ilinii-x oi diphi Ikm ia i);ii-illi. 240. ;. Di|.hilieriabi.-i!i;. ^< 1000. r.. ;'. PseiKlodiphiherialjacilli. KKK). r/. SiiciiK, 1000. /i. Streptococci. )iplitheria Bacilli and Streptococ TlIK liACTI'UaOLOdV OF Dl I'llTII I'llilA (;].'} constant presence, its isolation in pure culture, the nrproductifni of flic disease in animals by inoculations of pure cultures, the presence of tlic bacilli in the orif,niial and in the experimentally induced disease, dernfjii- strated the bacillus of Klebs and r.oefllcr to b(; the cause f)f dij)li- theria. Morphology. — The diphtheria bacillus is a straight or slightly curved, rod-shaped organism with rounded ends; the diameter is ordinarily from 0.5 to 0.8 microns and the length from 2 to 3 or more microns. It is subject to the greatest variation of form; this is true to suc-h an extent that polymorphism is an important characteristic;. Abbott^ says that spindle and club shapes are extremely common, and that not rarely many of the rods stain irregularly; in some of them very deeply stained round or oval points can be detected. He adds: "When cultures are examined microscopically it is especially char- acteristic to find irregular, bizarre forms, such as rods with one or both ends swollen, and very frequently roc^s broken at irregular intervals into short, sharply defined segments, either round, oval, or with straight sides." The form and size of the bacillus vary gready according to the culture medium used; it is smallest and most regular on glycerin agar; on Loeffler's blood serum one sees, "instead of the very short spindle, lancet, club-shaped, always segmented and regular staining forms as seen upon glycerin agar, long sometimes, extremely slender, sometimes thicker, irregular-staining threads that are usually clubbed and frequently pointed at their extremities." In 1900 Wesbrook read before the Association of American Physicians a carefully prepared article on the various morphological types of diph- theria bacilli. He divided them into three groups — the granular (those with deeply staining granules), the barred (those with transverse bands), and the soHd or evenly staining forms. Further subdivisions of these groups were discussed. The granular type of bacillus is the one most commonly seen in the beginning of the disease; later these give way wholly or in part to the barred or solid forms; soHd types may sometimes be replaced by the granular when convalescence is established and just before the throat begins to clear. Wesbrook's findings have been more recently con- firmed by Gorham. The relation of the sohd forms to true diphtheria bacilli is still unsettled. They are said to be sometimes encountered as variants in pure cultures of diphtheria organisms. Certain of the sohd forms have characteristic i which seem to distinguish them from the diphtheria bacillus and to class them with the pseudodiphtheria organisms. For instance, some of the solid forms fail to produce acid in dextrose bouillon, a property which is possessed by the true diphtheria bacilli." Staining Properties. — ^llie diphtheria bacillus stains well with the ordinary aniline dyes and with the Gram stain. The best results are, 1 Principles of Bacteriology, fifth edition. 2 Statements made in a report on " Diphtheria Bacilli in Well Persons" by a Committee of the Massachusetts Association of Boards of Health, Boston, 1902. 614 DIPHTHERIA however, obtained with Loeffler's alkahne solution of methylene blue, which brings out the granules well. This solution is made up of Concentrated alcoholic solution of methylene blue .... 30 c.c. Caustic potash in 1 : 10,000 solution 100 " Neisser Staiii. — The stain suggested by Neisser in 1897 is said by Abbott to enable one to overcome in a very large part the difficulty occasionally experienced in differentiating the diphtheria bacillus from other throat organisms which may simulate it. The method is described by Abbott as follows : The culture to be tested should be grown upon Loeffler's blood-serum mixture solidified at 100° C. ; it should develop at a temperature not lower than 34° C. and not higher than 36° C, and it should be not younger than nine and not older than twenty-four hours. A cover-glass preparation made from such culture is stained for from one to three seconds in the following solution: Methylene blue (Grubler's) 1 gram. Alcohol (96 per cent.) 20 c.c. When dissolved, mix with Acetic acid 50 c.c. Distilled water 950 " After thoroughly rinsing in water the preparation is then stained for from three to five seconds in vesuvin (Bismarck brown), 2 grams dissolved in a litre of boiling distilled water, filtered and allowed to cool. It is again rinsed in water and examined as a water-mount or dried and mounted in balsam. When so treated the bacilli appear as faintly stained brown rods in which from one to three brown granules are always to be observed. The dark granules are at one or both poles of the cell, are more or less oval, and usually seem to bulge a little beyond the contour of the bacillus in which they are located. In the vast majority of cases it seems safe to regard all bacilli that do not stain in this manner as distinct from bacillus diphtherise (Abbott). ^ Biological Characters. — The diphtheria bacillus is aerobic, non- motile and liquefying, and does not form spores. It grows freely in the presence of oxygen, but is also a facultative anaerobic (Sternberg). The diphtheria bacillus is destroyed by exposure to a temperature of 58° C. (136° F.) for ten minutes. In the dried state it may maintain' its vitality for a long period. Park found active bacilli on dried membrane after seventeen weeks, and Roux and Yersin living but non-virulent bacilli after five months. Bacilli were found by Abel to persist for five months on children's toys kept in the dark. When the organisms are preserved in sealed tubes and protected from light and heat they may remain virulent for years. Growth on Loeffler's Blood Serum.^ — This is the best medium for the growth of the diphtheria organism and the one which is ordinarily employed for the culture test. It is a mixture of three parts of blood serum with one part of bouillon, containing 1 per cent, of peptone, Till': liACTF/illOLOCY OF hi I'II'I'IIIuH A 015 1 per cent, of grape-sugar, aixl 0.5 \n's cent, of .sodluni diloiiilf,-; the mixture is sterilized and solidified at a low tcniper.'itiire (Stfrnlx-rgj. I'he di[)litheria organism grows so mucli more {>njmptly upon tliis mixture than other mouth and throat bacteria that at the end fjf twenty- four liours the (H[)htheria colonies may be readily recogniyx-d while the other colonies are still inconspicuous. Growth on Glycerin Agar. — The development u[)on this medium is nuich more delicate and less luxuriant than U|>f)n bUjrjd serum. The colonies apj)ear at first on the surface as Hat, almost transparent, dry, non-glistening, non-elevated round points. When slightly inagnified they are seen to be granular with an irregular central marking. The colonies are always dry in appearance; the deep colonies are coarsely granular (Abbott). Bacilli taken directly from the throat develop poorly, or not at all, on agar, but subcultures may grow very well. Growth on Gelatin. — The colonies on gelatin do not present tlieir characteristic appearance in less than three days. If slightly magnified the colonies show a denser centre than periphery; the border is notched. The colonies are granular, particularly the deep ones (Abbott). Growth on Bouillon. — According to Abbott, the growth on bouillon produces fine clumps which fall to the bottom of the tube or become deposited on its sides without causing diffuse clouding. Sometimes the clumps cannot be discerned by the naked eye. The reaction of the bouillon is at first acid and later alkaline. According to Schabad the maximum acidity occurs most often on the second day, although sometimes it may be on the third and rarely on the fourth or later. Many observers regard the acid formation a feature of importance in distinguishing between the diphtheria and pseudodiphtheria organism ; the value of this test, however, is not yet definitely determined. Growth in Milk. — Sternberg states that milk is a favorable medium for the growth of the diphtheria bacillus and adds that, as it grows at a comparatively low temperature (20° C), this fluid may become a medium for conveying the bacillus from an infected source to throats of previously healthy children. The appearance of the milk remains if j. unchanged. ^'' Growth on Potato. — Welch and Abbott state that the diphtheria bacillus grows on ordinary steamed potato without any preliminary treatment, but that the growth is usually entirely invisible or is indicated by a dry, thin, glaze after several days. At the end of twenty-four hours, at a temperature of 35° C, microscopic scrapings of the potato reveal a decided increase of the bacilli. Pathogenesis. — According to Park the diphtheria bacillus is patho- genic for guinea-pigs, rabbits, chickens, pigeons, small birds, and cats; to a less extent it is pathogenic for horses, cattle, dogs, and goats, but not for rats and mice. The rat and the mouse exhibit a remarkable insusceptibility; a dose of 2 c.c. of a bouillon culture will kill a rabbit, but not a mouse. The inoculation of such animals as cats and rabbits by rubbing a pure culture of the diphtheria bacillus upon the mucous surface of the QIQ DIPHTHERIA opened trachea produces a disease which is essentially the same as that seen in man. The animal usually dies in from two to four days, not from a general invasion by the diphtheria organism, but as a result of the absorption of the soluble toxins formed at the seat of infection. The wound at autopsy is covered with a grayish, adherent, necrotic, distinctly diphtheritic layer. The surrounding subcutaneous tissues are oedematous and the lymphatic glands at the angles of the jaw are swollen and reddened. The mucous membrane of the trachea at the site of inoculation is covered with a firm, grayish-white, loosely attached pseudomembrane identical in all respects with that seen in human diphtheria. The membrane and the oedematous fluid about the wound show the presence both by smears and by culture of the diphtheria bacillus (Abbott). In animals that did not die too quickly Roux and Yersin have noted the development of paralysis of the posterior extremities. It is a well-established fact that the diphtheria bacillus under ordinary circumstances remains in the vicinity of the site of inoculation. When it is found in the blood or visceral organs its presence is probably accidental. The widespread changes in important organs in diphtheria must therefore be ascribed to a diffusible circulating poison produced by the diphtheria organism in its original nidus. That such is the case was proved by Roux and Yersin in 1888, when they demonstrated the presence of a poison in diphtheria cultures which were filtered through porous porcelain. It was found that old cultures and particularly those of alkaline reaction, had a much greater toxic potency than recent cultures of acid reaction. Injection of filtered cultures into susceptible animals produced local redema, congestion and hemorrhage of the internal organs, effusion into the pleural cavity, etc. It is thus seen that practically all of the symptoms produced by the injection of pure cultures of bacilli may be obtained by injection of the filtered cultures save the production of a false membrane. Sternberg remarks that this deadly toxin appears to be an albuminoid substance (a toxalbumin), but its exact chemical composition has not yet been determined. Virulence and Avirulence of Diphtheria Bacilli.^"V\hen virulent bacilli are grown in bouillon, soluble toxins are developed which produce certain noxious effects upon guinea-pigs. Even where the l>acilli are removed by filtration the injection produces death of the animal. Practically all bacilli derived from clinical cases of diphtheria produce toxins with these properties. Conversely, it would seem that bacilli that produce no toxins in bouillon will not produce them in the human subject. Wesbrook and Gorham rather dissent from the view generally accepted, and believe that animal inoculation of cultures is no definite test of virulence of the bacilli in the human species. Formerly the non-virulent bacilli were classed by some writers in a group apart from the genuine diphtheria organism. It is now pretty generally recognized that true diphtheria bacilli may possess varying grades of virulence. Those occurring in the throats of convalescent patients and those found in the throats of healthy persons have fre- 77//'; liACTI'lh-IOIJXlY 01'' Dl I'll'I'll Klil A (; | 7 quently a very low i^ritdc of vii-iilcncc. 'I'lic less vinilcni, lorins rominonly increase in niiinhcrs ;is |)r()^n-css lovvunl the rcfovery of (li[)litijeria advances. The Distribution of Diphtheria Bacilli in the Body. — Abbott says: "In a certiiiii luniihcr of cases (li[)litlihtheria bacilli in their throats. In the eastern part of the United States it is 1.3!) per cent. "This would mean in Boston, if the smaller figure be u.sed, abont the enl^e of tlie ('])i^1otli,s, the cartilafjje of Wrisher^, and the like. It very frecjuently covcu's c()inj)let<;ly not only the tonsils, hut tlie anterior and posterior pihars, the pliaryngeal wall, the uvula, an(J the entire soft palate. In severe cases it is not uncommon to see the exudate on the vault of the mouth piled up so high as to form a thick spongy mass, seriously interfering with deglutition. At the time of writing tliese lines we have in the l)os[)ital three or four patients in whose throats this extensive form of exudate is seen. The clinical history of f>ne of these patients is as follows: K. R., aged seven years, white, female, admitted December 7th, on ninth day of the disease. On the first and second days in the hospital the temperature was 100° F., on the third day it fell to y7;i°F. The pul.se ranged from 104 to 112 per minute during the first and second days, and on the third day fell to 82. The culture was positive. On admission the exudate covered completely and thickly both tonsils, the anterior pillars, the pharyngeal wall, the uvula, and the greater part of the soft palate. On the latter it was piled up in a thick, spongy mass. Deglu- tition was difficult. The face was swollen, pale, and glossy. The breath was very fetid. Both nares contained large plugs of exudate, and were constantly oozing blood. The cervical glands on both sides of the neck were very much swollen. Immediately after admission the patient received 4500 units of antitoxin; twelve hours later another dose of 3000 units was given, and again a third dose of 4500 units, making in all 12,000 units. Death resulted on December 9th, from toxaemia and exhaustion. We have seen the exudate even more copious than in the case just cited. Cases have come under our observation in v^^hich not only the entire fauces, including the soft palate, were covered, but even the hard palate and the greater part of the buccal cavity also. Sometimes it appears on the gums, but more often invades the edges of the tongue. It is frequently seen in the pharyngeal vault, and may extend into the Eustachian tubes. The nares and the larynx are so often involved that the behavior of the disease in these cavities will subsequently receive special notice. The exudate is usually of a yellowish-white or cream color, but it may present a dark-gray appearance. Its color is liable to be changed by the ingestion of certain drugs, or by remedial agents employed locally. It sometimes is rendered darker by having coagulated blood incorporated with it. But in perfectly typical cases it does not look unlike moist chamois skin. Indeed, when large fragments or casts are exfoliated and floated in water they have a strong resemblance to this material. The exudate may be thick, or thin and filmy. When very thick it may be seen, even at quite an early state, lying rather loosely on the mucous membrane, or partly detached at its margin, especially when located on the soft palate. If forcibly removed it is liable to be repro- duced in the course of a few hours, although in many cases it exfoliates quickly and does not reform. Instead of presenting the appearance of 624 ' DIPHTHERIA a distinct membrane lying upon the mucous surface, the exudate some- times forms into and becomes a part of the mucous membrane itself. In this case there is a grayish discoloration which disappears slowly, and often by the process of necrosis, rather than by exfoliation of the mem- brane. Of course, this process is followed by an ulcerating surface which heals by granulation. The involved parts of the fauces, especially the uvula, become oedem- atous and swell considerably. After the exudate has disappeared from the uvula, the latter is apt to present an ulcerated appearance, and, through loss of tissue, is not infrequently left smaller than normal. In all severe cases in which there is oedema and swelling of the fauces there is not only difficult and painful deglutition, but the respiration and articulation are also affected In the act of swallowing it is not uncommon to see milk regurgitated through the nares. As the case progresses the voice becomes distinctly nasal, and is apt to continue so for some weeks. At first the exudate is free from odor; but when the disease is severe a distinct odor is noticed in the course of two or three days. Indeed, the breath of the patient is often so peculiarly offensive that an experi- enced clinician might be led to suspect the nature of the affection before an examination of the throat has been made. In septic cases, when decomposition of the secretions and the exudate goes on rapidly, the odor is in the highest degree offensive, and is well calculated to excite suspicion that extensive necrotic changes of the tissues may be taking place. The tissue change, however, is not always as great as the odor would indicate. A copious mass of exudate is often thrown off very quickly by the process of exfoliation, leaving the parts only slightly ulcerated. In such cases the odor will promptly disappear, especially with the use of cleansing or antiseptic lotions. With this apparent improvement one should not be too hasty in pronouncing the patient out of danger, for the probabilities are that the most critical period of the disease is yet to be encountered. Where the mucous lining of the fauces is at all destroyed, leaving the absorbents exposed, the toxin of the specific micro-organisms is permitted to enter the circu- lation, and the subsequent danger from toxaemia is far greater than the primary local disease. While there is usually some swelling and tenderness of the cervical and submaxillary glands at an earlier stage of the diphtherial process, coincidently with intense involvement of the fauces, these glands, together with the surrounding areolar tissue, become indurated and infiltrated, giving rise often to extensive tumefaction. The face, besides being pale and sallow, presents also a swollen and glossy appearance. As the exudate and septic secretions disappear from the throat, the tumefaction of the neck subsides. Occasionally, however, the cervical glands take on suppurative action, but not so frequently as in scarlet fever. Nose. — Next to the fauces the nose is the most common site of the diphtheritic process. The disease not infrequently attacks the nares 77//'; HVMI'TOMATOl.OdY Oh' 1)1 1'llTII hlUI A 025 primarily, but most often the exudate ext(>n(ls I'rojii (lif (liro;it io flic nasal cavities l)y way of the posterior aspect of the uvula. When this occurs the posterior wall of the pharynx is also liable to be involved through contiguity of structure. At first there is but little discharge from the nares, as in the l)eginning of an a(;ute catarrh, but it soon increases and becomes Hoccnilent. When the disease has fully develofx-d, the discharge is often profuse and sometimes fetid. Before the diphtherial process has continued very long, evidence of copious exudation may be seen by inspecting the nares. In many cases the membrane is very thick and dense, and o(;cludes the nasal cavities completely. There is then but little discharge from the external orifices; but the voice becomes distinctly nasal, and the patient is obliged to breathe through the mouth. When the fauces are at the same time severely involved, the respira- tion becomes considerably hampered, and there is also difficult deglu- tition, with marked restlessness and insomnia. The amount of exudate that is sometimes expelled from the nares is enormous. The membrane is often thrown off in perfect casts, and on inspecting these one is apt to feel surprised that so much material could have been contained within the nasal cavities. When the exudate begins to separate, or has been either partly or wholly cast off, the discharge usually returns, and is often sanguinopurulent in character. There is no form of diphtheria more dangerous than that of the nares. The injury sustained by the capillary bloodvessels prepares the way for rapid absorption of the toxins, the effects of which are apt to become painfully visible in a short time. Not only is systemic poisoning seen, but the more common sequelae of diphtheria most often follow the nasal form of the disease. Epistaxis is of frequent occurrence even in mild cases; but when the diphtheritic involvement is intense the hemorrhage from the nose is liable to occur repeatedly, as the disease progresses, and may prove to be a very troublesome symptom. In some cases there is a constant oozing of blood, while in others the hemorrhage is sometimes so free as to be the immediate cause of death. In the severest form of nasal diphtheria the nose is slightly reddened externally, and moderately swollen or oedematous. The face also is oedematous, remarkably pale, and has a peculiar glistening appearance. The pulse is usually feeble, the circulation bad, vomiting often occurs, and not infrequently there is marked drowsiness. Indeed, the symptoms, taken together, are such as would indicate profound systemic poisoning. Many patients in this condition die at a comparatively early stage of the disease. In the more favorable cases the exudate is thrown oft' en masse in the form of casts, and the constitutional symptoms do not become so pronounced. But one should not feel too sanguine of recovery in any case, for danger of the development of toxaemia is never absent. Even when this serious condition does not arise, and the general symptoms seem most favorable, still there is a strong liability that the aftection 40 626 DIPHTHERIA may be followed by paralysis, either partial or general. Postdiphtheritic paralysis is more common after the nasal form of the disease than after any other variety. Nasal diphtheria sometimes assumes the form of chronic rhinitis. In such cases there is usually a discharge from the nares and often excoriation of the skin about the nose. But the affection may persist for months, with little or no nasal discharge. Persons thus afflicted often unwittingly spread diphtheria. It is important that such cases should be recognized and treated, and even isolation should be advised until a cure is effected and the specific organisms have disappeared. It is only by the aid of bacteriology that this form of diphtheria can be definitely determined. Middle Ear. — From the pharyngeal vault the exudate sometimes spreads by way of the Eustachian tube to the middle ear, causing an acute median otitis. This is often unattended by pain; hence the con- dition may not be recognized until suppuration takes place and the tympanum has ruptured. The purulent discharge which flows from the meatus will show the presence of the bacilli of diphtheria associated with certain other organisms, such as streptococci and staphylococci. There is usually some rise of temperature, often assuming a septic character. The otorrhoea frequently persists a long time, but is seldom followed by permanent deafness. Temporary deafness, however, may be seen as the result of a paretic condition of the muscles of the Eustachian tube and of the tympanum. Only in rare instances are the changes in the intratympanic cavity so great as to cause permanent deafness. This is not so likely to happen in diphtheria as in scarlet fever. Eyes. — Diphtheritic involvement of the conjunctiva is not very fre- quently seen. It occurs sometimes, but the wonder is that it is not more common in children, since they so often convey the infectious discharges from the nares to their eyes by means of their hands. Physicians and nurses who work among diphtheria patients are frequently subjected to the risk of infection by having the secretions from the throats of such patients coughed into their eyes. While we have sometimes seen a mild conjunctivitis occur from this accident we have never known it to assume a diphtheritic character, though such a result is not impossible. It has been suggested by some writers that the diphtheritic inflam- mation may extend to the conjunctiva by way of the tear duct, but this we believe is of rare occurrence. As an unhealthy mucous mem- brane is more prone to diphtherial infection, it is therefore probable that an acute or chronic inflammation of the eyes furnishes a predisposition to eye involvement when diphtheria occurs in a child thus afflicted. When the conjunctiva becomes involved the membrane usually spreads rapidly from one eyelid to the other, and the bulbar conjunctiva is almost always greatly chemosed. The exudate is first seen as flocculi, but it rapidly forms into a thick membrane, so thick, indeed, as to press hard upon the cornea, causing it to become hazy and often undergo a destructive necrosis. When the cornea of the eye becomes weakened 77//'; SYMPTOM ATOIJXIV OF 1)1 1'llTII HKI A (■,27 or perforated by lliis pnH-css (lie iris i)rolapses. J)uring tli<- foursc of the disease (lie eyelids swell and stiU'en, so that it is ainiost iinjjfjssihie to ins])e('t the vyc, itself. From wliat has heeii said it is evident that loss of vision is iniininent. Fortunately the affection is not always so destructive In thr mildci- cases recovery may take place without impairment of vision. I>iif \vl,atier)t to live for hours, sometimes even a day or tw(i, with no peree[)tible pulse at the wrist. It is remarkable to note that consciousness in this condition is usmdly retained to the last. Septic Diphtheria. — In diphtheria there are always associated with the specific micro-organisms streptococci and staphylococci in {^reat abundance, and the latter often give rise to a concurrent septic infection which constitutes an important factor in the course of the disease. It is sometimes difficult to determine to what extent this secondary infection is responsible for results, as distinguished from those of the primary infection. Doubtless in many cases of diphtheria streptococcus infection is the principal cause of death. Septic infection is most liable to occur in patients with intense nasal involvement, and in whose fauces the exudate assumes a dirty-gray or brownish appearance. Instead of becoming detached and peeling off en masse, the exudate breaks down into a semisolid or gnmious mass. In such cases the decomposing and liquefying membrane gives rise to an offensive discharge from the nares and mouth, and a fetid breath. This discharge, ichorous in character, causes reddening and excoriation at the orifices of the nose and corners of the mouth, and the denuded surfaces are often converted into ulcers v/hich quickly take on a dirty-gray coating. Sometimes there is considerable ulcerative action seen in the fauces and nares, but, strange to say, this process is commonly limited to the mucous membrane. It is only in rare cases that the subepithelial tissue is lost to a greater exteht than would result from a small ulcer here and there. These ulcers are apt to remain covered for a long time with a yellowish coating. The disorganization of the mucous membrane of the affected parts is commonly attended with capillary hemorrhages, more or less marked. As might be supposed, the color of the false membrane is changed by its becoming infiltrated with blood. When the hemorrhages are copious, and the blood is poured out between the mucous membrane and the exudate, the latter is quite sure to be separated to a considerable extent. It is, therefore, not unusual to find in such cases a good deal of loose exudate in the throat, and in the nose also, undergoing rapid decom- position. As the result of septic infection, the lymph glands of the neck become inflamed and swollen. The periglandular connective tissue may also inflame and swell to a certain degree. In some cases the swelling is so great that the neck is raised to an even line with the face. The skin becomes tense, smooth and shining, and may either feel doughy to the touch or as dense as a board. Suppuration may or may not result. Attention has already been called to the fact that in septic cases a rash is apt to appear on the skin. The rash may at first be erythematous or slightly macular, but as the disease progresses it often assumes a petechial character. In this form of diphtheria the temperature runs comparatively high — • 630 DIPHTHERIA ranging from 102° to 104° F. There is usually considerable variation between the morning and evening records. The pulse is rapid and feeble, and the extremities are often cool. Suppuration of the middle ear is liable to occur, and pneumonia sometimes develops. Children, restless at first, become apathetic later on, which condition increases until death supervenes. Death, however, is not the inevitable result, for the milder cases frequently recover. Fever. — Except at the onset of diphtheria, fever is not a prominent symptom. The disease almost always begins with fever, more or less intense. In the milder cases the temperature of the body may not rise Fjg. 93 104° 103° 2 102° < 1 101° < t 100° 99° 98° 97° M E M E M E M E M E M E M E M E M E M E M E M E M E M E M E M E M E M E M E \ I 1 1 1 1 _J L 1 ! 1 1 1 1 1 1 1 1 1 1 1 1 1 1 1 1 1 1 ^ _| Sl \ \ \ , \ I \ A A ' l\ V \, -»-U- N / V A / \ \, - i V /\ rf* s, . / \ , ^ r r ^ 7 1 f\ \/ \ \l ' — — V V V V Y , \ ^ \ \ V V '' DISEASE 1 a 3 i 5 6 7 S 9 10 11 12 13 It 15 16 17 18 19 PULSE RESPIRATION ^ i¥ ^;¥ -% ^S4 1^ ■% f^ f4 '^X y^ f4 fi % f4 f4 ^y^ -^ f^ y^ •S4 ^ f^ % H f4 f4 % % f4 % f4 94 14 r B. G., ordinary type of diphtheria, occurring in a child five years of age, showing a high initial temperature with a rapid decline. much above the normal, but in the severer cases, during the first day or two of the disease, it usually ranges from 101° to 102° F.; but after the full appearance of the exudate— that is, after the second or third day — the temperature commonly drops to normal, and sometimes below. Our experience accords with that of Lennox Browne, who says: "Of 1000 cases which came under observation, on an average, on the third day of the diphtherial attack, the temperature in 80 per cent, was 101°; while in 50 per cent, the average temperature during its course was below 99°." As already stated, the average temperature in the septic form of TlIK ^YMI'TOMATOIJJdY OK 1)1 1'llTllEIilA iuW diphtlieriii is always (:onif)aratively \\\li:}\, wliilf in \\\c fox;rrr)if; cases it falls to normal and ev(m lower. In acute adenitis, which often occurs as a cojnplieatioji in di|)htheria, the temperature ranges high, sometimes to the extent of i(J'1^ to MWy" V. [f suppuration takes place and the pus is liberated the hyperpyrexia at once subsides. In every case of continued liigh temperature one should suspect the existence of some complication. 'V\\v degree f>f fev(;r, under such a circumstance, is usually not did'crent from that which is characteristic of the associated disease. What has been said of the temperature in ordinary diphtheria does not apply with equal force to the laryngeal form of the disease. In this class of cases, instead of falling after the first two or three days of ill- ness, it frequently continues high, especially when intubation is required Fig. 94 104° 103° < S loi M E ^ M 1 M E M E M E E M E M E 3 E M $ I '- = _ ■■ :. IS _ ] . E — - 3 - ■ 3 M E E I E 1 M 1 e[m]£Im ^ m|e'm'e'm|e'm'em e|m|e -4 . . -t- ^100° 98' 97° ~ = - = 1 ^ I J 7^ s^ ^ 7 I t V ^ - 1 i — A ^ r -^ \ oF I ^ '- y t\ r 1 ■ 1 1 -^^ ? E - - =t w ;^ 1 - i - E E DAV OF DISEASE ^ ^ = J = = - ( - = r ~ » < 1 1 1 12 i:'. 1 1 15 ir. 17 IS 1 .1 20 21 22 i:; 21 25,20 i 27 1 28 1 29 PULSE s g ^ S 1 s|i => B § g => I ■s I 1 o 1 gIiSS = 5l = S^isS:J = 2523n=7lii2i '/.Si^js'^ 1 =l=is[J RESP. g ;', ■s s s .|. a r, s s •s ■?, i", 11 S s 3 :S -i'-¥"i"-^n"i"'''i" ?1,S SlSj^lS ■i\j^^^;^^^^S^s\iiS^^;^ ^ DATE 13 UL 15 IG 17 18 19 20 21 22 23 2i 25 28 27 1 28 29 30 1 2 3 j 1 5 f. 7 1 8 9 1 ^ .luno July M., aged five and one-half years ; septic type of diphtheria in a patient with copious exudate in the throat ; swollen cervical glands, later suppurating. Recovery. for relief of the stenosis, and while the tube is in the larynx. In the majority of such cases the temperature continues at 101° to 102° F. for a number of days. If bronchopneumonia develops, which is not an infrequent comphcation, the temperature will continue high for an uncertain length of time. Circulatory Symptoms. ^ — In all well-marked cases of diphtheria the pulse is frequent. Its rapidity, indeed, may be out of proportion to the temperature. In severe cases, especially in children, the pulse ranges between 120 and 160 per minute, and, as the disease progresses, becomes irregular and weak. The apex beat of the heart is often diminished in intensity and the first sound becomes indistinct. Atten- tion has already been called to the fact that the action of the heart is greatly influenced by the profound asthenia resulting from toxaemia. 632 DIPHTHERIA An abnormally slow pulse is of grave import, and will be referred to again when considering the question of prognosis. Fig. 95 DAY OF § ■o m ^ Ol CO -* lO 23 t- CO CJ o v^ DISEASE CO ■* in CO ^- z o J ^ J ^ J irl _! ^J _ ■o ■r+* >n JL o _ < 107° 10C° 105' 101° 103° 102° 101° 100° 09° 98° - - - - - - - - - - - - - - - - - - — — — — — — ^ — -^ ~ ~ "~ ~ ~ ~ "" ~ " ~ ~ " _ _ ~ ~ ■■ _ _ _ _ _ _ ~ t LI _ _ _ _ / ~ ~l 1 t 1 \ n A _ _ _ _ _ y V V _ _ _ _ _.. H \ - A "^ ~ " y / I ~ ~ " A 1 \, P y ^\ _ ~ ~~ ~~ ~ V' V \ A / \- ~ ~ ~ ~ / ^ r- 7 \ A J, \ V Sj ~ ~ "' 1 V \ i A i 1 f \ / V ~ ~ V V y y ]/ i V — — — — ~ ~ ~ ~ ■■ _ _ __ _ _ -^ \ — ~ ~ .V 170 160 150 140 130 120 110 100 90 80 70 -fiO- ~ ~ " _ ~ ~ ^ _ ~ ~ \, _ _ _ _ 1 ~ ~ f \ _ _ _ _ 1 ^ J _ _ L _ J f _ _ p >j - _ _ — — - — - ^ - - - - - - - - - - - - - 5 k I i- <^ ~ J : ^ ~ f. _ A I : I : _ z — _ - I - _ - - - - - - - A/ / ^ -/ - - -\ - n ^ 1 n — - - ^ ~ ~ I z I n /^ u J A A A I\ A r n — — — ~ ~ ~ ~ J V V 1 / V V \ 1 1- V ~ v J \ — — ~ ~ r- ~ / V V \ \ ' I — — — y t \l V- — — — — — ] \- ^ ~ ~ ~ " . ~ .J ~ _ _ _ , _ _ _j _ _ _ _.. ~ ~ " . _ _ _ _ -ft _ _ _ _ _ _ _ _ _ _ — - - — - L- C - -z. o V- 50 45 40 35 30 25 20 15 10 i — A h n Tz 5 — - - — - — - - - — — — — — -^ — — ~ — ~ ~" ~ '~ ~ "-' h V V _° 1 d A _ « _ _ _ _- __ _ — _ _ — - — - - — T 2 1 - - \, A A - f _A % A — A - - - — — ^ — ~ ~ ~ ~ A v v _ _ =3 J -/ \ y A __ 15 ~ V /" ' n* A ^ \r- -in — ' \ r ^ f V 7 \ -^ — — — — — ~ ~ ~ ~ ~~ V V 1 V >/ \ 1 1- ~ ~ ~ "" ~ ~ ~~ ^ V >J V "~ _ _ _ _ _ — 1- -1 ~ ~ V ~ ~ _ ~i. ~ ~ _ _ ~ _ _ _ _ _ _ _ _ _J _ _ _ _j _ _ _i _i Ij Za J — 1 — 1 — 1 — 1 —1—1 C. S,, case of laryngeal diplitheria of average severity admitted to the Municipal Hospital on the third day of the disease, showing decline of temperature after removal of the intubation tube. Recovery. The Urine. — In the milder cases no marked change is found in the urine, either in the quantity voided or its constituents. In severe cases it contains an excess of urea, and sometimes epithelial cells and casts. Hsematuria is much less common than in scarlet fever. Albumin in 77//'; ^YMr'rOMATOIJXIY Oh' l>ll'IITIII':iaA {Y.\:\ small (|tiiiiil,i(i('S is found ii) a- hir^c. profxtrlion of cases. It is said io be present in nhoul one-third of all cases; hut t[)is estirnate is, according to our experience, much too low. Some writers believe that albumin is more often found since antitoxin has come into use. Suppression of urine and ura'mic symptoms are rare. This subject will be n;ferred to afijain when considering; the complications of diphtheria. Nervous Symptoms. — In the acute stage of ch'phtheria nervous symptoms are not a prominent feature of the disease. Convulsions sometimes occur as an initial symptom in (children of nervous tempera- ment. In fatal cases convulsive movements are not infrequent in the death stru<2;,7 usually well marked from the hcfrinriin^. 'Vhv, tcmperaturf- runs up quickly to 102° or l():i'^ F., there is loss of appetite, the tliroat is painful, and the child is restless and unable to sleep long at a time, (^,'hilly sensations may be experienced, and oc(;asionally convulsions occur. When an early examination of the throat is made the mucous mem- brane will be found to l)e of a vivid-red color, with moderate swelling of the parts. The uvula soon becomes (x.'dematous, elongated, and swollen. This inflammatory action does not continue long, perhaps only a few hours, until the exudate appears. In its earliest manifestation it presents the form of grayish or yellowish-white spots of pinhead size. These form into groups which (juickly coalesce, and thus develop into large patches. In most cases the exudation is first seen on the tonsils and rapidly spread to other parts of the fauces. Frequently, in twenty- four to forty-eight hours it covers not only the tonsils, but the anterior pillars, the uvula, and a large part of the soft palate. With this increase of exudation the temperature, strange to say, often falls one or two degrees. The lymphatic glands of the neck, near the angle of the jaw, are almost always swollen. In favorable cases the local symptoms reach their maximum develop- ment in forty-eight hours, and after remaining stationary for a day or two begin to subside. The exudation sometimes exfoliates in large masses, and at other times melts away little by little. When it becomes detached and peels off it may disappear entirely in from six to eight days, sometimes sooner; but when it melts away gradually, a longer time is required. The mucous membrane of the parts involved is left reddened, and shows superficial ulcerations. Often the uvula suffers the greatest loss of substance from the ulcerative action, as it is honey- combed, shrivelled, and tapers down to a small point. The ulcers usually heal rapidly. Simultaneously with the decrease of exudate the pulse becomes less frequent, and, in favorable cases, maintains fair volume and regularity. The swelling of the glands of the neck subsides, the appetite improves, and the patient is fairly on the road of con- valescence. But even when recovery seems most probable, the physician in giving a prognosis should express himself with some reservation, for dangerous symptoms may yet follow, such as indicate toxaemia, heart-failure, or paralysis. In very severe cases all symptoms are, of course, greatly intensified, and complications are much more liable to ensue. The exudation is usually copious, covering thickly the entire fauces, and is often seen extending forward on the vault of the mouth beyond the junction of the soft and hard palates, on which location it is apt to be especially thick. It frequently travels backward to the pharyngeal wall, the postnasal space, and into the nares. It may even extend downward into the larynx and trachea. As already mentioned, the local and constitutional symptoms do not progress pari passii. On the contrary, while the exudation is increasing the fever may diminish to such an extent that the body temperature is but little above the normal. The pulse rate, however, does not 638 DIPHTHERIA always decrease proportionately, but may even grow more rapid. The appetite often improves, swallowing appears to be less painful, and not infrequently the general condition and strength of the patient seem improved, while the danger is in nowise diminished. The physician should be careful not to be misled by this apparent improvement while the disease is still progressing. When diphtheria assumes the se'ptic form, the secretion and exudation of the throat and nares undergo rapid decomposition, and, unless these parts are frequently cleansed with antiseptic washes, there is emitted with the breath a peculiar odor which is in the highest degree offensive. This odor is often so foul as to suggest the existence of gangrenous destruction of the tissues, and yet the disorganization of the parts rarely amounts to more than a superficial ulceration. Coincidently with this condition, the cervical and submaxillary glands, usually somewhat swollen from the beginning, greatly increase in size by inflammatory action, which also involves the adjacent cellular tissue. While abscesses frequently form, yet it is surprising how rapidly this swelling will often subside without abscess formation as soon as the throat symptoms show signs of improvement. In septic cases the fever, instead of diminishing in two or three days, as in the other varieties of diphtheria, continues, or may even increase, until the throat and nose symptoms improve and the swelling of the neck subsides. Recovery may take place from this form of the disease, but the majority of patients die. Death often occurs at an early stage, as early as the fifth to the seventh day, from extensive systemic poison- ing due to a mixed infection. Sometimes the poisoning is more gradual, in which case the exudate disappears, the glandular swelling subsides, and the temperature falls, but instead of improving the patient remains apathetic, loses weight, becomes anaemic, grows weaker and weaker, and gradually passes away. A not uncommon cause of death is pneu- monia of septic origin. The presence of epithelial and hyaline casts in the urine, together with a large amount of albumin, points to a rapidly developing systemic poisoning, and may often prove to be an early monitor of danger. When recovery takes place from the septic form of diphtheria con- valescence is usually very slow, often, indeed, extending through many weeks. The symptoms of septicaemia become less and less marked, and prostration gradually gives way to general improvement. But in the fourth or fifth week of the disease, even after an apparent recovery, some late complication, more especially general paralysis, is extremely liable to set in. This is true not only of the septic form, but of all well- marked cases of diphtheria. The vast majority of patients recover from the paralysis, but it is sure to prolong the period of convalescence for weeks or even months. In the malignant type of diphtheria the earliest symptoms give marked evidence of systemic poisoning. By the time the false membrane has formed, which is usually in twenty-four to forty-eight hours, the whole organism is profoundly affected. The membrane covers thickly PLATE LVIII. Malignant Diphtheria. Showing purpuric discoloration of the face, ecehynnoses of the eyelids, petechia upon the chest, s-welling of the tongue and the glands of the neck. Death ensued. 77//'; COUIiHI'], DUIiATION, AND Th'JlM IN ATIOS Oh' hi I'll'l II l:i{l A {]'.\\) the entire fiuices, often involving \hv iiares tilso; tli(; hreatli is fefifl, the saliva dribbles from the mouth, blood oozes from the nose, and pnrj)ijrir or petechial spots appear upon the skin; the f^lands of the neek ;irid the periglandular tissue are greatly swollen; th(; face is bloated, pale, and waxy in color; the tera})erature is either slight ly elevaterl or subnormal; the pulse may be rapid and feeble or slow and irregular, and the intel- lect, clear at first, soon becomes clouded. Death in these cases may occur in forty-eight hours, and is rarely delayed longer than three or four days. The course and duration of membra nous croup vary in different cases, according to the extent of the disease. In mild cases the symp- toms often disappear in a few days under ordinary treatment, withf)ut operative interference. When the larynx is involved to the extent of causing stenosis, death is sure to result speedily if relief be not afforderl If the exudation is limited to the larynx the obstruction to respiration is almost always overcome by intubation, and in the course of six or eight days the patient may be considered comparatively free from danger, at least so far as the primary trouble is concerned. But when the exudation extends into the trachea, intubation may give relief at first, though death is liable to occur a few" hours later. Death commonly results when the disease extends into the bronchi and bronchioles. It occurs through insufficient decarbonization of the blood, due to the mechanical obstruction caused by the false membrane and retained secretions in these parts. In cases which linger longer the fatal result may be brought on by collapse of certain parts of the lungs to which the air does not have access, or by the development of capillary bronchitis or broncho- pneumonia. Many patients develop the latter affection when they are believed to be well on the way to convalescence. This, indeed, is one of the principal causes of fatal termination in laryngotracheal diph- theria. When membranous croup is likely to terminate in recovery, improve- ment begins with a decrease in the fever and an abatement of the laryngeal symptoms. The false membrane usually disappears in from four to eight days. vSomethiies it is coughed up in cylindrical or irregular casts, but more often it disappears gradually, probably by being liquefied and expectorated; it is quite impossible to believe that it ever undergoes absorption. When throwai oft' in casts it is liable to reform, and when such new formations take place the disease is apt to terminate fatally. In patients that recover, hoarseness or aphonia, and often some difficulty in swallowing, continue for a longer or shorter tune after the intubation tube has been removed. This change in the voice, according to Oertel, is to be ascribed to a flaccid condition of the vocal cords and atony of the laryngeal muscles. 640 DIPHTHERIA RECURRENCE OF DIPHTHERIA. Many authors believe that a second attack of diphtheria seldom occurs in the same individual within a short space of time. While this may be accepted as the rule, yet it must be admitted that there are many exceptions. It is certainly true that a person who has survived the disease does not have conferred upon him for any considerable length of time that immunity which is so characteristic of scarlet fever, measles, and smallpox. We have quite often readmitted children to the hospital with recurrent diphtheria within a few months from the previous attack; and in two or three instances, at least, children have returned with a third attack. Quite often also have we seen patients suffer from a relapse of the disease before leaving the hospital. In such instances, after the sub- sidence of all constitutional symptoms and the complete disappearance of the membrane, the patient, during convalescence, is seized with a sore throat, the temperature rises, the glands of the neck become swollen and sensitive, and the exudation recurs in the throat, or nares, or both. The relapse is not, as a rule, so severe as the primary attack, but there are some exceptions. We have more than once seen death result from a recurrence of the disease. COMPLICATIONS AND SEQUELS OF DIPHTHERIA. Heart.^ — The poison elaborated by the bacilli of diphtheria is espe- cially prone to affect the heart. In all severe cases heart-failure is extremely liable to occur. Symptoms of this condition may appear before the pseudomembrane has entirely separated, but in most cases they are not apparent, or, at least, do not become prominent, until the characteristic feature of the local affection has, to a great extent, dis- appeared. In other words, signs of cardiac failure are rarely seen until the diphtherial process has made considerable progress. They do not often appear before the end of the first week, but during the four or five succeeding weeks the patient is in constant danger of heart- failure. It is believed by some authors that the heart is affected to a greater or less degree in all cases of diphtheria. Jacobi^ says: "There is no case ever so mild apparently that will not affect the heart's function at once to a certain extent. From mild cases to the gravest there are gradual transitions." In a large proportion of the severe cases which survive long enough the myocardium shows (post-mortem) certain anatomical changes, the most common of which is fatty degeneration. Undoubtedly, heart-failure not infrequently results from paralysis of the cardiac nerves, and quite independently, too, of any anatomical change in the heart muscle. Lennox Browne credits Vincent, of Paris, and P. Meyer with having found "widespread parenchymatous changes 1 Twentieth Century Practice of Medicine. COMPrJdATlONS AND SI'JQUKLAi: OF 1)1 1'llTII h'Jil A fJ41 in the cardiac plexus in two cases of y)afierits dyin^' of }ieart-failure during convalescence from dij)hlheria, in which the heart muscle was unaffected." He says: "The changes were exactly similar to those found in the peri})heral nerves in orflinary j)ostfli[)}itherific j)ara]ysis." The symftomn of heart-failure do not dilVcr from those of toxamia. Vomiting is often an early sign. The patient is pale and sallow, some- times livid and cyanotic; the pulse at first may be rapid and feeble, but soon becomes slow, irregular, and intermittent, or dicrotic. The pulse rate is frequently as slow as 40 to 50 per minute. The first sound of the heart grows less distinct. The circulation is sluggish, and the extremities are cold, but the mind remains clear. In severe cases, as the end approaches, the pulse becomes absolutely lost at the wrist, and death results gradually from asthenia, or it may result suddenly from heart-failure. Undoubtedly death sometimes occurs from paraly- sis of the cardiac plexus. Recovery but seldom takes place after the symptoms of heart-failure once assume a threatening character. Lungs. — In faucial diphtheria the lungs do not very often become affected. Bronchitis occasionally occurs, as does also bronchopneumonia. But in the laryngotracheal form of the disease these complications are extremely common. Indeed, bronchitis, more or less marked, is not very often absent in membranous croup. As the inflammation extends downward from the laryngotracheal surface to the bronchi, the inflamed mucous membrane is apt to become involved in the diphtherial process. But quite apart from this, bronchopneumonia, catarrhal in character, is of frequent occurrence, and constitutes one of the principal sources of danger. It most often sets in before the acute stage of membranous croup has passed, but it may occur at any period following this stage, even during convalescence. J. Lewis Smith says: "In 121 cases of bronchopneumonia complicating diphtheria, observed by Sannp, the pneumonia commenced in 2 on the first day of diphtheria, and in 71 between the second and sixth days inclusive." When it develops at a later stage, or during convalescence, it s in most cases preceded by a mild bronchitis that has never entirely dis- appeared. The existence of a bronchopneumonia is revealed by physical exam- ination. Both lungs may be found involved, although the disease is usually better marked in one than in the other. The physical signs may show that the inflammation is limited to the lower lobes, but more frequently disseminated areas of inflammation are found throughout one or both lungs. As already stated, bronchopneumonia is one of the chief sources of danger in diphtheritic croup. The mucopurulent material secreted in the bronchial tubes may be so abundant as to clog the tubes and prevent proper decarbonization of the blood. As the inflammation extends to the smaller tubes, these often become clogged in the same way so as to prevent the entrance of air to the alveoli, which gradually collapse. Autopsies often reveal areas of atelectasis disseminated throughout the lungs. Even where the tubes remain pervious it is almost impossible 41 G42 DIPHTHERIA for the child to expectorate the mucopus on account of its viscidity. Hence, the minuter tubes are usually found (post-mortem) to be filled with a thick, viscid material, containing also not infrequently floating particles of pseudomembrane. Bronchopneumonia is always attended by an elevation of temperature. The disease may either run an acute course, terminating in recovery or death in six to eight days, or assume a subacute form and continue to progress for two, three, or more weeks. In some of these persistent cases recovery finally takes place, but more often death results from exhaustion. Bronchopneumonia is the chief cause of death after tracheotomy. Lobar 'pneumonia is not a very frequent complication. It has been known to occur during the stage of convalescence. Areas of con- solidation in the lungs are not infrequently seen, but they are almost always associated with inflammation of the bronchi. Pleurisy does not very often occur as a complication. According to J. Lewis Smith, "Peter found the lesions of pleurisy 9 times in 121 autopsies in diphtheria, and Sannd observed them in 20 cases." The latter is quoted as saying that pleurisy always accompanies some other phlegmasia. In our experience in the hospital we have not seen more than two or three frank cases of pleurisy attended with pleuritic effusion. Lymphatic Glands. — Enlargement of the cervical and submaxillary glands is of common occurrence in diphtheria. It may be either slight or excessive. In septic cases this complication is usually most marked. As already stated, the inflamed glands sometimes break down into abscesses. Kidneys. — Renal complication occurs earlier in diphtheria than in scarlet fever. Albuminuria is frequently seen as early as the third or fourth day, sometimes even on the second, while the quantity of urine is not diminished, but may be increased. It is believed that the elimi- nation of the toxin with the urine irritates the kidneys, and thus tends to affect their function or even damage their parenchymatous structure. In cases showing albuminuria the kidneys may be found to be normal, or they may exhibit various degrees of parenchymatous inflammation. While acute nephritis is not so common as in scarlet fever, yet it does occur. This is evident from the fact that hyaline and granular casts are sometimes found. Red blood cells are rarely present. The urine in such cases is diminished, sometimes scanty, and the skin becomes pallid. Qildema is less pronounced, and ursemic symptoms are much less frequent than in postscarlatinal nephritis. Still patients die now and then from uraemia. According to Jacobi, "When albumose is found, together with considerable albumin, Berlin believes the prog- nosis to be rather favorable. Still, in most of the cases at the clinic at Strassburg in which he made his observations, the renal complications were only trifling." Park^ says that in most severe cases of diphtheria the kidneys are in 1 Loomis-Thompson, American System of Practical Medicine. COMPLldATIONH AND SI<:QI/ l':/..'l'J OF hi I'll'I'll I'.UIA 643 a state of more or less acute iiepliril is; tliat tliey an; usually hypenemic and enlarged; that the surface of the kidney is smooth, and frecjuently the seat of small hemorrhages, and that, microscopically, the signs of marked parenchyniatf)us changes are evident up to complete necrosis of the epithelium lining of the tubules. "In severe cases the urinr' contains abundant albumin, degenerated kidney epithelium, leukocytes and hyaline casts, and, in the most severe, coarse and fine granular casts. Blood cells are infrequent." Lennox Brow^ne believes that there is a decided tendency to renal complications in all cases intoxicated with the diphtherial poison. In a series of 1000 cases of diphtheria tabulated by him he found, however, that the mortality due to nephritis and its results was only 2.7 per cent. This is a much larger rate than was observed in all the Metropolitan Asylums' Board Hospitals in 1893, when, he says, out of a total of 2848 cases of diphtheria treated, with 865 deaths, only 8 cases of neph- ritis were reported. But while actual nephritis does not occur with great frequency, yet, as already stated, the parenchymatous structure of the kidneys is very commonly damaged to an extent that interferes with their proper function. Lennox Browne says albumin in some quantity is to be found in the urine in fully one-half of the cases of true diphtheria. Some other observers state that it is present even in a much larger proportion of cases, and believe, with Lennox Browne, that it is more frequently seen since the serum treatment has been employed. When it is present to the extent of more than one-eighth of the volume of urine, the amount of urine secreted is apt to be dimin- ished, and ursemic symptoms may appear. As to the frequency of albuminuria in diphtheria, J. Lewis Smith says: "Bouchut and Empis found it in two-thirds of their cases, Germain S^e in one-half of his, and Sann^ in 224 cases out of 410. In New York City, where diphtheria has been many years naturalized or endemic, I made, in the years 1875 and 1876, daily examinations of the urine in 62 consecutive cases, and found it present in 24, while 38 were recorded exempt. But the proportion of cases as stated in my statistics is probably below the truth, for the albuminuria is sometimes transient and it often occurs as a mere trace and is liable to be overlooked. Its duration is frequently not more than from one to three days, and in the majority of instances it does not continue longer than ten days; but we are all familiar with cases in which it continues fifteen or twenty days, or even months." As the amount of albumin in the urine varies in different patients, so also does the day of the disease on which it makes its appearance vary. In referring to Sanne's observations on this point J. Lewis Smith says: "In 224 cases albuminuria was detected on the first day of diph- theria in 3, on the second day in 10, on the third in 30, on the fourth day in 30, on the fifth day in 32. From the sixth day to the eleventh the number on each day in whom albuminuria was present for the first time varied from 10 to 33. After the eleventh day there were only 9 new cases, and after the fifteenth day only 1 new case. Hence, from 644 DIPHTHERIA these statistics we infer that there is Httle danger that albuminuria will occur after the second week, if the patient has exhibited no symptoms of it previously." In exa.minations of the urine made under our direction of 149 diph- theria patients in the Municipal Hospital, albumin was found to be present in 85 per cent, of the cases. The cases were not selected, but taken consecutively as they were admitted to the hospital in two differ- ent periods of time. The observations, therefore, include both mild and severe cases of diphtheria. The first series of examinations comprised samples of urine from 37 patients, and the second from 112 patients. Of the former, 73 per cent, of the cases showed albumin, and a few showed tube casts also. The urine was not examined in all cases as frequently as we desired, for the reason that most of the patients were young children from whom it was often impossible to obtain specimens. But in no case were there less than two examinations, and in some as many as twelve. In most of the patients that recovered the urine became normal during convalescence, but a few still showed a trace of albumin when discharged from the hospital. Of the second series of examinations pertaining to the urine of the 112 patients, albumin was found in 90 per cent.; 20 per cent, of these cases showed albumin in large quantity, and 70 per cent, in a less amount — not more than a trace being found in some. In 24 patients showing a large amount of albumin the urine was examined microscopically, and tube casts, hyaline and granular, were found in 2 of this number. We should add that 1 of these patients had nine months previously suffered from scarlet fever, and we had no knowledge of the condition of the urine since then. Strange to say, in a few of the fatal cases in which the kidneys were examined post-mortem there was macroscopic evidence of parenchy- matous changes, although examination of the urine had failed to show tube casts of any description. Scarlet Fever. — Scarlet fever is not an uncommon complication in diphtheria; or, more properly speaking, one of these diseases is often found associated with the other. We venture to say that anyone who has had experience in a hospital for contagious diseases will bear out this statement. Being familiar with the experience of, at least, two or three such hospitals, we know how frequently scarlatinal rashes are found in the diphtheria wards, and, on the other hand, how often diphtheria appears in the scarlet-fever wards. For the past two years we have been in the habit of examining (bacteriologically) the throats of all scarlet-fever patients as soon as they are admitted to the hospital. In dividing these examinations into series of 100 cases each, the Klebs-Loeffler bacillus has been reported present by The Bacteriological Division of the Bureau of Health, Philadelphia, in from 10 to 33 per cent, of the patients. Some showed well-marked clinical evidence of diphtherial complication, while in others, it must be said, such evidence was not apparent. It is not uncommon to admit to the hospital patients in whom these diseases coexist in a well-pronounced form. COMPLICATION H AND S/'JtjU l':/..K OF 1)1 1'll'lll lUilA f;4rj Lennox Browiic (jiiolcis Dr. \\r\\v.v. Low as sayiiif^ that "rJuritij^ flie prevalence of diphtheria in Hastings the two diseases in certain instances were concurrent, and in a number of persons who, on account of their suffering from scarlet fever, were sent to the borough sanatorium for isolation and treatment, were attacked by well-marked diphtheria during their convalescence," giving also several examj)l(;s "of irn[)or(a- tion of diphtheria into families by members returning home from the sanatorium after recovery from scarlatina, the patients in each instance not having been known to suffer from diphtheria during stay in the hospital." In many cases of diphtheria with concurrent scarlet fever it is impos- sible to explain the source of the double infection. In hospitals for contagious diseases it is sometimes felt that one disease is engrafted upon the other through exposure to the second infection; but in private families these diseases not infrequently coexist without any known or explicable cause. One of the writers has just witnessed an instance of this kind in which two children of a family of three took scarlet fever; subsequently an infant of eleven months, who had not been out of the house for some time, fell ill with the disease and in two or three days developed also symptoms of severe diphtheria. Copious exudate appeared in the fauces and nares, and death cpiickly ensued from systemic poisoning. Measles. — The relation of measles to diphtheria is a matter that has not received as much notice by writers as its importance deserves. Ryland referred to it in his Jacksonian Essay in 1837, and Dr. West in 1843. A few other observers have called attention to the fact that in times of concurrent epidemics of diphtheria and measles, subjects of the latter disease frequently suffer also from the former. In reporting on an outbreak of diphtheria in 1894 at Barnham Broom, England, Mr. T. W. Thompson says: "I find from my notes that with one or two exceptions, all the children, who later suffered from diphtheria, had about this time suffered from measles, which in some cases had been attended with considerable soreness and external swelling of the throat. The frequency with which diphtheria is found to coexist with or quickly follow in the wake of measles is such as to suggest a relationship between the two phenomena; though the relationship may be of an indirect kind only, the measles increasing susceptibility to diphtheria, mainly, in all likelihood, by the damage inflicted on the mucous membrane of the throat." There is no doubt that the catarrhal inflammation of the upper air passages incident to measles affords a fertile soil for the propagation of diphtheria bacilli. The occurrence of measles with diphtheria should be regarded with great apprehension. The diphtheria is liable to assume the laryngo- tracheal form, and the development of bronchopneumonia is to be feared. In the year 1900 measles of an unusually severe t^'pe broke out in the diphtheria wards of the INIunicipal Hospital, and in all 68 cases came under our observation. Of these 34 died, making the death rate 50 per cent. Of the 68 cases, 34 developed membranous 646 DIPHTHERIA croup, and of these 29 died — a death rate of 85.29 per cent. Broncho- pneumonia was the principal cause of death, though some sank and died in a state of adynamia. Paralysis. — Paralysis might be regarded with much propriety as a symptom of diphtheria, but as it is not seen until the acute stage is passed, and more often during convalescence, we have preferred to consider it as a complication or sequela. Very little seems to have been known of diphtherial paralysis prior to the latter part of the sixteenth century. Nicholas Lepois called attention to it in 1580, and Miguel Heredia in 1690. According to J. Lewis Smith, Ghisi, of Italy, in describing an epidemic which occurred in 1747-48, when his own son had paralysis in a severe form following diphtheria, says: "I left to nature to cure the strange consequences, . . . which had been remarked in many who had already recovered, and which had continued for about a month after recovery from the sore throat and abscess. During this period this child spoke through the nose, and food, particularly that which was least solid, returned through the nares in place of passing down the gullet." About the same time (in 1748) Chomel, of France, described two cases of paralysis following what he called gangrenous sore throat. In 1771, Dr. Samuel Bard, of New York, described the symptoms seen in a little girl of two and a half years who had recovered from "Sore Throat Distemper," as follows: "Whenever she attempted to drink she was seized with a fit of coughing; yet she was able to swallow solid food without any difficulty. She improved, but in the second month she could scarcely walk or raise her voice above a whisper." For the next fifty years and more but little is said of diphtheritic paralysis. This sequel must either have been overlooked, or regarded as a coincidence, or else diphtheria at that time was of so mild a type that paralysis did not often result. It appears that Bretonneau had not yet observed this sequela at the time of his first publication on diphtheria in 1826. It is said by J. Lewis Smith^ that Bretonneau "did not recollect that he had seen a case of diphtheritic paralysis prior to 1843. Although a close observer of diphtheria, the paralysis had not been observed by him, or at least had not attracted his attention, until it occurred in the person of his townsman. Dr. Turpin, in 1843." From this time on, until his second publication appeared, in 1855, he saw a sufficient number of cases to convince him that this sequela occurs not infrequently, and called attention to it in his paper of the latter date. Since then nearly every writer on diphtheria has described this peculiar form of paralysis, and its frequent occurrence is an accepted fact. Paralysis does not often follow mild tonsillar diphtheria. But when the soft palate and especially the nares are involved, partial or complete paralysis, not only of the muscles of the parts covered with exudate, but also of the entire muscular system is liable to occur. , General paralysis does not appear immediately after the local evidence of diphtheria has 1 Keating, Cyclopedia of the Diseases of Cliildren. aOMI'LICATION^ AND SFJjlII'.L.K Ol' I >l I'll! II HUI A 047 disappeared, hut (level()]),s grii(liiiilly and slowly. The parfs earliest affected are the soft j)alate and fh(; j)haryiix, wliile the upper and lower extremities show tliis syni[)toin later. From tlie slow development of the affection it seems probable that at first only a few fasciculi are inca- pacitated, and that gradually more and more of these become involved until the affected muscles are no longer under the control of the will. Paralysis is sometimes ol)served in the muscles of the eyes, the trunk, the bladder, the rectum, and the diai>hragm. In most cases the paralysis is incomplete, but in rare instances it progresses to such an extent that the entire muscular system becomes incapacitated. The cause and pathology of the paralyses are not fully understood. It seems probable that the condition is due to a toxic neuritis involving the peripheral nerves, causing an interruption of the nerve supply to the muscles involved. It is said that the neuritic change may extend the entire length of the nerves, from their periphery to their origin, not only of the spinal but also of the cranial nerves. It may be that some of the fasciculi of the enervated muscles undergo fatty degeneration, as this change has been seen in the myocardium. Anatomical changes have been found in the spinal cord, apparently resulting from myelitis. S. G. Henschrn has reported a case of acute disseminated sclerosis of the cord with neuritis. Some writers believe that changes of this nature contribute an important part in the pro- duction of the paralysis. , Hemiplegia is but rarely seen in diphtheria. Only 2 cases have come under our observation. One case has been reported by J. W. Brannan. This writer is quoted by Jacobi as saying: "There are 35 cases in all recorded in medical literature of postdiphtheritic paralysis of cerebral origin. Six cases have come to autopsy; in 1 of these a hemorrhage was found in the internal portion of the lenticular nucleus, with destruction of the neighboring part of the internal capsule. In the other 5 cases there was embolism of the Sylvian artery. . . . In the total 35 cases there was complete recovery in 4, death in 7; and in all the others there was permanent paralysis of greater or less extent." In studying the causes of diphtheritic paralysis Trousseau felt that the explanation of this symptom is beyond our comprehension and will probably never be known. Realizing the insufficiency of any one theory to explain all cases, Jacobi, in his renowned treatise on diph- theria, says: "It may be positively asserted that diphtheritic paralysis does not in every case depend on one and the same cause." The frequency with which paralysis follows diphtheria depends upon the character of the epidemics. It occurs, of course, much more fre- quently in severe attacks than in mild attacks of the disease. According to Lennox Browne, in 2S48 cases of diphtheria treated at the various Metropolitan Asylums' Board Hospitals of London, in 1SP3, it was noted in just 14 per cent. This proportion, he says, agrees in the main with that deduced from his own table of 1000 cases of diphtheria. While we have no data at hand of our own experience on this point, g48 DIPHTHERIA we believe that at least 14 per cent, of our patients developed paralysis more or less marked. Since paralysis develops very gradually and slowly, it is not always easy to determine at which stage of diphtheria it begins. The difficulty is increased from the fact that most of the patients are young children in whom the affection is usually not discovered until the more char- acteristic symptoms have appeared. However, it has been found from careful observation that paralysis of certain muscles, the palatal, for example, may occur in the acute stage, or, at least, immediately after the disappearance of the pseudomembrane. But the later manifesta- tions, as seen in muscles remote from the fauces, especially in those of the extremities, diaphragm, etc., are more serious, and usually do not appear in a pronour^ced form until after an interval of more than four weeks from the commencement of the diphtherial attack. We cannot better illustrate our experience with this affection than by quoting J. I^ewis Smith's account of two cases reported by Holt: "A child, aged two years, had diphtheria in August, and a second attack in the middle of October. She convalesced slowly, and in her convalescence had no paralytic symptoms, except a nasal voice, until December 1st, when multiple paralysis suddenly developed. A brother of this patient also had diphtheria in October, moderately severe, and early in convalescence - paralysis of the muscles of the palate began, followed by that of the other muscles; but it was not until the middle of December that the lower extremities were paralyzed." J. Lewis Smith very properly adds: ''These cases are examples of the usual mode of commencement and extension of the paralysis." While this sequela is not so often seen after the mildest attacks of diphtheria, at least not to any marked degree, yet instances have been recorded in which paralysis has occurred in persons who, presumably, were infected with the diphtherial poisons without having exhibited any of the ordinary symptoms of the disease. According to the author just quoted. Dr. Boissarie^ has related cases of this kind which are remarkable, if not indeed unique. He says an officer of the police force, after ailing for two or three days, had a nasal voice, and, in attempting to drink, the liquids returned through the nose. The velum palati was found insensible and motionless, but the fauces were otherwise apparently normal. "In the hospitals alongside the barracks in which the above case occurred, a young man without fever, redness, or swelling of the fauces, had also a nasal voice, and return of liquid food through the nose. The porter of the hospital was similarly affected, and the doctor stated that certain other patients in like manner pre- sented symptoms of paralysis, without the history of an antecedent diphtheria. Dr. Reynaud, called in consultation, expressed the opinion that the paralysis had a diphtheria origin; and this opinion was strength- ened by the occurrence immediately afterward of an epidemic of diph- theria in the place where these cases occurred." J. Lewis Smith follows 1 Gazette hebdomadaire, 1881. COMI'LI(!AT]()NH, AND SI<:Q(/I<:LA'J ()!<' 1)1 1'llTII KIU A VyW) the account of these unicjue cases witfi the pertinent reniark that it is probable an antecedent diphtheria had occurred of so mild a form as to have escaped notice. The paralysis, as a rule, affects princijjally tlie motor nerves, althou^li the sensory nerves are not infrequently involved also. Anaesthesia of some parts, particularly the fauces, has h)een observed, and tingling and numbness are sometimes felt in the extremities. The sense of taste has been known to be affected. Paralysis of the sensory nerves may be quite local, and is not seen until a somewhat later period than the motor paralysis. As the sympton)s and course of diphtheritic paralysis vary according to its location and muscles involved, it seems most convenient to speak of the clinical manifestations of its various forms separately. Paralysis of the palate is often seen at an early stage of the disease. It may be observed as soon as the exudate has disappeared, or as early as the tenth day of the diphtherial attack. The first evidence is mani- fested by a nasal tone of the voice. This results from dropping of the soft palate, causing the air to escape through the nose in the act of speaking. There may be slight difficulty in swallowing, enough to make it necessary for the patient to drink cautiously. Later, in the third or fourth week, or after convalescence has actually set in, the deglutition may become more difficult, so that fluids, instead of being easily swallowed, regur- gitate in large part through the nares, while some run down the larynx, causing cough and sopietimes pneumonia. As already mentioned , anesthesia is associated with this form of paralysis and adds to the difficulty of swallowing. In infants starvation may occur through their inability to suckle. Even in older children, and in adults also, when general paralysis of an extreme form develops, deglutition often becomes impossible, and death from starvation may result if feeding through an oesophageal tube be not resorted to. When paralysis of the palate has continued for a week or two, faulty accommodation of the ocular movements may be seen. Most frequently the paralysis of the ciliary muscles is bilateral. The most common variety of axis deviation met with is convergent strabismus, resulting from paralysis of the external recti muscles. Diplopia is not of infrequent occurrence. Slight facial paralysis occasionally occurs. It has been noted as appearing soon after the acute stage. We have seen but very few such cases, and in these the affection was unilateral. Paralysis of the cardiac and respiratory neri'^es may appear any time after the first week of the illness. The exudate may have disappeared, more food is taken, the patient appears to be gradually improving, and the members of the family are cheerful at the prospect of a speedy recovery, when suddenly the scene changes. The heart action becomes weak, the pulse feeble, slow and irregular, sometimes rapid, the respira- tions superficial, and the patient becomes pale, often slightly cyanotic. Severe precordial or epigastric pain is often complained of in cases of sudden heart-failure. In the more favorable cases improvement may 650 DIPHTHERIA follow active stimulation, and the patient may eventually recover. But too often the improvement is only temporary, for the heart-failure is liable to return after a few hours, or a day or two at the most, causing sudden and, to the inexperienced physician, unexpected death. There is no other disease in which symptoms of heart-failure occur so suddenly and unexpectedly, and there is perhaps no other disease in which physicians are so often deceived in the matter of prognosis. Involvement of the respiratory nerves leads to paralysis of the dia- phragm and sometimes pulmonary collapse. General paralysis does not make its appearance until a very late stage of diphtheria. It is not often seen earlier than the fourth week, and may occur later than the sixth week. In most cases it appears between the fourth and sixth week. In almost every instance it is preceded by well-marked palatal paralysis, sometimes by loss of function of the muscles of the eye, especially those presiding over motion and accommodation. As a rule, the loss of power is first noticed in the lower extremities. This may increase until the limbs, especially the lower limbs, are rendered entirely useless for weeks. The comparative immunity of the fingers in many cases may be mentioned as a peculiarity. Parsesthesia or anaesthesia, however, is frequently noticed in the fingers, palms of the hands, and feet. The degree of paralysis is not the same in all muscles ; in some it is complete, while in others it is only partial. When there is complete loss of power in the lower extremities it is not unusual to find that the patient has considerable use of the upper extremities. The muscles of the trunk are often partially paralyzed, but only rarely is there loss of sensation. In general paralysis the diaphragm is often affected, but rarely to the extent of seriously interfering with respiration. Its involvement is more apparent in the act of coughing. In this act, instead of the sudden expiratory explosion, the cough is slow and straining, and apparently attended with some effort on the part of the patient. But paralysis of the muscles of the pharynx, preventing complete closure of the glottis, may have more to do in causing this peculiar symptom than paralysis of the diaphragm. As J. Lewis Smith very truly says, even where the paralysis seems to be general there are groups of muscles which entirely escape. He, therefore, prefers the term multiple paralysis to that of general paralysis to designate this form of the disease. . Of the internal and visceral muscles liable to become involved, paralysis of the diaphragm or of the heart is of the most serious import, as it may be responsible for sudden death. The bladder is sometimes involved, but rarely to any marked degree. We have never found it necessary to catheterize a patient to relieve this viscus, nor have we ever observed any loss of power in the sphincter muscles. Paralysis of the muscles of the lower bowel and rectum is said to occur at times, giving rise to constipation, but not affecting the sphincters. The ensemble of symptoms of general or multiple paralysis is very COMPLICATIONH AND HI<:Q(J l<:i.A<: Oh' h/ f'lIT// l:UfA (;ol graphically described by Dr. C. W. Fallis in the Medical Summary, January, ]}itheria, Ifolt refers to some important investigations made upon this point by the New York Healtli l^epartment/ He says: "As the result of observations upon 450 cases which were followed, the cf)nchision was reached that the disease was so slightly contagious (if at all), and usually so njild, that strict isolation and subsequent disinfection wen; unnecessary. Of 113 cases occurring in 100 families, in only 14 was there a history of exposure to a similar case, and in only 9 was there another case in the same family. In many of the latter a common origin appeared more probable than that one case was derived from another. "At the present time the general opinion of the profession .seems to be that these cases are to a slight degree communicable, to be compared in this respect to ordinary catarrhal colds or possibly to pneumonia. They are probably more contagious in the presence of the poison of scarlet fever or measles." For the purpose of testing the communicability of p.seudodiphtheria, Park^ made some very interesting experiments by inoculating human throats with streptococci. He describes the experiments as follows: " A very thick culture was made on agar plates from a severe follicular tonsillitis in a young child, so that there was obtained a luxuriant growth of streptococci growing both in long and short chains, and also of other micrococci. A large amount of these mingled bacteria were, with the permission of the patient, plastered on a swab and then rubbed gently on the right tonsil and into its crypts. He felt a peculiar sensation in the tonsil for some twelve hours; this then passed away, and was probably simply the result of the mechanical irritation. " The next morning the tonsil appeared healthy except for a small patch in a crypt; from this, and from the throat, cultures w^ere made. The plates gave very numerous colonies of streptococci, w^hile cultures made from the same regions the day previous to the experiment gave very few streptococci. " A second trial was made in a similar w^ay from a culture of strepto- coccus pyogenes, eighteen hours old, from a case of extensive pseudo- membrane and tonsillar abscess. The results were also entirely negative, except for the increase of streptococci in the throat for some days. With the same streptococcus the tonsils of two other adults were daubed, and with similar negative results. "These trials having shown that in three throats the application of streptococci from cultures made from virulent cases of tonsillitis pro- duced no effect, a different experunent was tried. On two separate occasions a sterile swab was rubbed on the tonsils in a case of severe tonsillitis, and then immediately rubbed on a healthy tonsil. In neither case was' there any inflammation excited. On the third day after the last experiment a sudden fall in the temperature occurred, and after exposure a follicular tonsillitis developed, such as frequently has followed previous similar exposures." 1 Diseases of Infaucy and Childhood. - Loomis-Thompson, American System of Practical Medicine. 654 DIPHTHERIA These experiments seem to warrant the conclusion, as Park says, " that the pyogenic cocci are not sufficient, as a rule, to excite an inflam- mation in the throat." Or, in other words, that the presence of strepto- cocci in the throat are probably harmless so long as the mucous mem- brane is normal, or intact. In primary cases the disease makes its appearance like an ordinary sore throat. There may be vomiting, slight rigors, headache, general pains, painful deglutition, and fever. The constitutional symptoms are usually well marked at the beginning. During the second or third day of the disease the temperature may rise to 103° to 104° F., but it quickly falls and the other symptoms also subside. On inspecting the Fig. 97 A case of pseiKlodiphilifi'ia iu lui adult negro; the exudate covered pmuoiis of the hps, tougue, buccal mucous membrane, and fauces. Diphtheria bacilli were absent, but streptococci and staphy- lococci were present. throat the mucous membrane is found reddened and the tonsils swollen. Very soon an exudation appears upon the tonsils, and sometimes upon other parts of the fauces and the buccal mucous membrane also. The exudate is grayish in color, shreddy or pultaceous, and seems to lie upon the surface, as it may be readily removed with a cotton swab. It does not remain long, usually disappearing in three or four days. The in- flammation of the throat is often more marked than in genuine diph- theria, and swelling of the lymphatic glands in the neck may be seen, though this is not excessive in mild cases. In many cases of pseudodiphtheria in which the disease is secondary to another affection the symptoms are as mild as those just described. COMPLICATIONS AND SICQil HL/K OF 1)1 1'llTII Klfl A (\r,r, But frequently the local iri,'uiif(\stati()ii.s are as severe as in the worst forms of pharyngeal (iiphtlK^ria, and the constitutional syni[)torns as well marked as in the septic form of that disease. Indeed, the clinical description given of scarlatina anginosa by some of the older writers is not essentially different from that of sej)tic diphtheria, at least so far as the greater part of the local and constitutional symptoms are concerned. In scarlet fever the streptococcic process is liaV)le to set in at an early stage of the disease. In severe cases the process may reach its maximum in the latter part of the first week, and continue for two weeks or longer. The disease almost always involves the nose as well as the fauces, and very frequently extends to the middle ear, giving rise to a suppurative otitis media, which may permanently affect the hearing. The local process in the throat is often more destructive to the tissues than is the case in true diphtheria. Deep sloughing of tlie tonsils and soft palate is sometimes seen. The lymphatic glands of the neck and the periglandular connective tissue frequently inflame and break down into abscesses. This process also may be attended by considerable loss of tissue, and occasionally is followed by serious hemorrhage. When pseudodiphtheria occurs secondary to measles the throat involvement is mild as compared with scarlet fever, but the strepto- coccic process much more frequently extends to the larynx, giving rise to a dangerous form of membranous croup. When this condition develops there is not only danger from stenosis, but also from broncho- pneumonia. Sometimes the larynx is involved when there is no sign of exudate in the fauces. Holt believes that this is very infrequent unless the disease is true diphtheria; but w^e have seen a number of such cases in which the Klebs-Loeffler bacillus was absent. In secondary cases the temperature, as a rule, ranges higher than in the primary. The pulse rate is more rapid and feeble, and the constitutional symptoms as a whole are severe. When the primary disease is scarlet fever, there is usually restlessness, delirium, great prostration, and albuminuria. Death is liable to result from septic poisoning. If, however, the patient withstands the toxic effects of the streptococcus organisms, the throat symptoms improve, the constitutional disturbance subsides, and recovery takes place as from true diphtheria. But none of the secondary affections peculiar to the latter disease, such as heart-failure and multiple paralysis, are liable to follow. From a clinical point of view it is often difficult to distinguish between pseudo- and true diphtheria. We believe that in the majority of cases the experienced physician will make a correct diagnosis at the bedside, yet frequently one most skilled in the art of diagnosis will find it impossible to say, in a given case, that the pseudomembranous affection of the throat is not true diphtheria. In such cases, the assistance afforded by bacteriology is of great importance. Holt very truly remarks : " The bacteriologists have taught us to be cautious in pronouncing too positively upon even the mild cases, as it has been clearly shown that some of them may be caused by the most virulent of diphtheria bacilli." 656 DIPHTHERIA Even in the secondary cases one should not be too ready to exclude true diphtheria in making the diagnosis, for it is well known, as has been already pointed out, that this disease often co-exists with scarlet fever, and not infrequently follows in the wake of measles, particularly when it is prevailing in the neighborhood. The clinical features dis- tinguishing pseudo- from true diphtheria will be considered later. Except in rare instances of laryngeal involvement, primary pseudo- diphtheria is not a serious malady. Some mortality, however, seems to attend the disease, as death rates varying from nil to 5.5 per cent, have been reported by different observers. According to Holt, of 117 primary cases observed by Park in the Willard Parker Hospital, New York, "the mortality was 3.5 per cent.," while ''of 127 cases of true diphtheria seen in the same institution at the same time, the mortality was 34.5 per cent." Out of 34 primary cases of pseudodiphtheria, which, in a limited time, came under the observation of Baginsky (in hospital), the mortality was 5.5 per cent., against 38.2 per cent, from true diphtheria. Holt says : " From the same hospital, Philip has published a report upon 376 cases; 332 of these were true diphtheria, with a mortality of 37 per cent.; 31 were cases of primary pseudo- diphtheria, with no mortality." He also calls attention to the fact that " The Bulletin of the New York Health Department contains a report upon 324 cases of pseudodiphtheria in children, with a mortality of 9, or 2.8 per cent.; 4 of the fatal cases complicated scarlet fever; of the primary cases, the mortality was but 1.5 per cent." He adds, "These were not hospital cases." During the past ten years we have observed in the Municipal Hospital, Philadelphia, 172 cases of pseudodiphtheria, with no deaths. All of these cases were sent in as true diphtheria. There was present on the tonsils, rarely on other parts, a rather loose, filmy exudate, which disappeared in two or three days after admission. Streptococci and other pyogenic organisms were present, but the Klebs-Loeffler bacillus was absent. We have not included in this number the cases of acute follicular tonsillitis which were also sent to the hospital with the mis- taken diagnosis of diphtheria. The mortality among the secondary cases of pseudodiphtheria is often very high. It is highest when the disease occurs secondary to scarlet fever or measles. Holt is inclined to believe that under such conditions it is from 20 to 40 per cent., and that in institutions for young children it not infrequently reaches 70 or 80 per cent., especially when these diseases prevail epidemically. He says that under the latter conditions " the cases complicating measles give, as a rule, a higher mortality than those complicating scarlet fever." This statement accords with our own experience. As pseudodiphtheria is rarely communicated from one person to another the enforcement of stringent preventive measures, such as quarantine and disinfection, does not seem to be necessary. It is, however, advisable to exclude healthy children from the sick-chamber. In regard to the secondary cases, especially when the primary disease (JOMrLICATIONH AND SI'X^I ! HL.K Oh' hi I'll ■III i: HI A (;r,7 was scarlet fever or measles, the c()iii[)li(,'ate(J cases slioiihJ rner, IJaurngarten, Haginsky, Middcldor])f and Gokhiian, Neunian, and others have made interesting studies of the diphtheria membrane. Councilman, Mallory, and Pearce distinguish, microscopically, two distinct varieties of the membrane corresponding to the differences observed macroscopically. The dense, firm, elastic membrane which can be stripped off in large flakes is composed of a reticular structure with beams of uniform size. The reticulum contains masses consisting of leukocytes and epithelial cells which have undergone hyaline degen- eration. The other variety of membrane, which macroscopically is characterized by greater friability, is composed of fibrin. The fibrin forms a reticulum just as does the hyaline material, but varies greatly in the size of the fibres and the spaces. The spaces may contain numerous leukocytes, either well preserved or broken down. The fibrinous membrane is often continuous over the entire surface of the tonsil and extends into every crypt. The hyaline membrane never extends into the crypts, though occasionally small masses of hyaline reticulum are found in them. The changes in the tissues observed by the above investigators are summarized as follows: The first step in the membrane formation is degeneration and necrosis of the epithelium, often preceded by active proliferation of the nuclei of the cells by direct division. The cells may either break up into detritus or become changed into refractive hyaline masses. An inflammatory exudation rich in fibrin factors comes from the tissues below, and fibrin is formed when this comes in contact with the necrotic epithelium. The fibrin in part is formed into a reticulum around exudation cells and degenerated epithelium ; in part it combines with the hyaline degenerated cells to form a hyaline membrane. The latter is most often formed on those surfaces which are covered with epithelium having several layers of cells. The fibrinous membrane is formed both in the surface and in the tissues. The membrane is never formed primarily on an intact epithelial surface, but it may extend over it. There is nothing specific in the membrane formation in diph- theria, as typical hyaline and fibrinous membranes may be found in ovarian cysts in which bacteria play no part; but it is accompanied by degenerative and exudative changes in the tissue beneath. The connective tissue and bloodvessels undergo a hyaline fibroid degeneration. Necrosis may extend deeply into the tissues, but there is little tendency to ulceration or abscess formation. The degeneration in the mucous glands, particularly of the glandular epithelium, is so pronounced as to be almost specific. The extent of the necrosis in the primary lesions is greater than is found in the action of any other bacteria. G60 DIPHTHERIA Diphtheria bacilli were never found growing in the hving tissue or in connection with those degenerative changes in the epitheUum seen in the beginning. They were found in the necrotic tissue and in the exudation, usually only in the latter. The bacillus shows an affinity for solid structures and is found rather on the reticulum than in the spaces between. The beginning of the lesions is probably due to the toxic action of the bacilli possibly growing in the fluids of the mouth or throat. When necrosis is once produced the necrotic tissue forms a suitable culture medium. The membrane and necrotic tissue are often invaded by pyogenic cocci and by fungi. Heart. — The pronounced clinical evidence of involvement of the cardiac muscle has led to extensive investigations of the underlying pathological changes in the heart. This subject has received careful study on the part of many pathologists. Hayem was the first to call attention to the granular and fatty degen- eration of the heart muscle and to changes in the vessels and interstitial tissue. Rosenbach noted a granular and waxy degeneration of the muscles and a cell exudation into the interstitial tissue. In 2 cases of suddenly fatal diphtheria Birch-Hirschfeld found evidences of acute interstitial myocarditis. Martin regards the myo- cardial change to be secondary and a result of acute endarteritis of the coronary arteries. One of the most important studies of the heart in diphtheria has been contributed by Romberg/ who made careful examinations in 8 cases. He found that the cardiac muscle was not uniformly affected, but that some portions might be normal and other areas show extensive changes. Small foci of leukocytic infiltration were found around the smaller coronary arteries, but the most important lesion was the degeneration of the cardiac muscle. The degenerated fibres had a peculiar vacuola- tion in the centre and were without nuclei. The nuclei undergo hyper- trophy with an accompanying vesicular condition. The inner and outer portions of the myocardium showed most degeneration. Focal interstitial changes, most common beneath the pericardium, were present in all cases. In 5 of Romberg's cases pericarditis was present, and in 3 there was endocarditis. Hesse^ made a study of the heart in 29 cases of diphtheria. The parenchymatous changes were not marked under three days, and were more pronounced on the left side. In 25 out of 29 cases interstitial myocarditis was present, and in 4 it was marked. It was noticeable in the first week, but was more pronounced later. The interstitial changes were more frequent in the left ventricle. The leukocytic infiltration was believed to be due to an increased penetrability of the vessel walls which were acted on by the toxin. Papkow, who examined a number of hearts of patients who died on the third or fourth day, found extensive fragmentation of the muscle 1 Ueber die ErKrankung des Herz mnskels bei typhus abdom. Scharlach und Diphtherie, Deutsche Archiv f. kiln. Med., 1891, Bd. xlviii. - Beitrage zur path. Anatomie des Diphtherie Herzens, Jahrbuch f. Kinderheilk., 1893, Bd. xxxvi. Till': I'ATIIOI/XJY OF DII'irrilKKIA OGl fibres, with white and red cells between th(^ fni^rneiits. 'I'lie fragmenta- tion was eansed by the swelling juid destrneti(;n of the eenient snl>stanres. Tliis is an early change, while tin; waxy degenerafion and infersfifial infiltration occur later. Welch and Flexner found fatty defi;eneration and necrosis of the muscle fibres, l^'^lexner later described swelling and deeper staining of the nuclei, with final disaj)})earance. Conncihnan, Mallory, and Pearce have made an extended series of careful examinations of the cardiac muscle in 00 cases of dij)htheria. The results of this valuable study are herewith presented : Fatty degen- eration of the muscular fil)res, varying in extent, was found in 30 of the GO cases; there were prol)ably more than this numl)er, as only -^0 hearts were examined in the fresh state, and of this number 29 showed fatty change. This degeneration varies in extent, at times affecting the myocardinm generally, and at times in foci. The fatty change accompanies and appears to precede more advanced forms of degeneration which lead to complete destruction of the muscle. The sarcous elements become swollen, broken, and converted into hyaline masses. Vacuolation, fragmentation, and fracture of the degen- erated fibres are often seen. Simple fatty degeneration is found in severe cases of short duration, and the more extensive degenerations in protracted cases. The degenerations are due to the bacterial toxin, and account for the impairment of the heart function. Two kinds of interstitial lesions are found. In the one there are focal collections of plasma and lymphoid cells, which may be accom- panied by an independent myocardial degeneration, analogous to acute interstitial nephritis. In the other the interstitial change is secondary to the muscle degeneration. This form may lead to excessive connective- tissue formation and a fibrous myocarditis. Thrombosis is not infrequently seen as a result of prmiary necrosis of the endocardium. The only bloodvessel change of interest is pro- liferation of the intima, which is also observed in other organs. Lungs. — Pulmonary complications are present in a very large pro- portion of fatal cases of diphtheria and commonly determine the lethal outcome. The lesion found is a bronchopneumonia of varying extent. Holt^ says that in infants and young children bronchopneumonia is found at autopsy in at least three-quarters of the cases. Councilman, ^Mallory, and Pearce found bronchopneumonia in 131 out of 220 post-mortem examinations; 98 of these were in cases of diphtheria only, and 33 were in diphtheria complicated with scarlet fever or measles. The lung complication was much more frequently observed in patients in whom the larynx, trachea, and the bronchi were the seat of membrane. It is believed that the most important factor in the production of these pneumonias is the aspiration into the lungs of micro-organisms, chiefly micrococci. 1 Loc. cit. 662 DIPHTHERIA Of the 131 cases of bronchopneumonia, the areas were discrete in 76 and confluent in 55. In the majority of cases the posterior portion of the lung was affected, and especially the lower lobes. The bronchi were affected in the majority of cases. The mucous membrane of the large tubes was reddened and covered with exudation; drops of pus could usually be forced from the small bronchi by pressing the cut surface of the lung. In 43 cases there was a fibrinous exudation in the bronchi, forming in the larger ones a distinct membrane and completely filling the smaller. Councilman, Mallory, and Pearce conclude that there is no organ in which lesions accompanying diphtheritic infection are so generally found or so serious as in the lung. In very many cases they are so extensive that death may be considered as due rather to the condition of the lungs than to the throat affection. The essential lesion is broncho- pneumonia; true acute lobar pneumonia was never found. The cases resembling lobar pneumonia were found on close examination to be cases of extensive confluent bronchopneumonia. The character of the exudation varies; it may be fibrinous, hemorrhagic, serous, or almost entirely cellular; rarely it may be hyaline. Atelectasis is commonly present in varying extent, and the same is true of emphysema. The cellular exudate is in part made up of leukocytes and in part derived from proliferation of the lining of the membrane. I^ymphoid and plasma cells are also found. In some cases there is organization of the exudation and connective-tissue formation within the air spaces. The lining epithelium of the air vesicles shows proliferation. Necrosis, in some cases leading to abscess, is not an uncommon feature. Large objects considered to be marrow cells which in many cases have undergone degeneration are frequently found in the capillaries; it is possible that these have been frequently mistaken for hyaline thrombi. Thrombi are occasionally found in the large vessels, but not in the capillaries. The lymphatics are commonly dilated and contain coagu- lated albumin, fibrin, or cells. They are often found packed with lymphoid and plasma cells, and large cells similar to those seen in the air spaces. (This summary is based upon a microscopic study of the lungs in 133 cases.) Bacteriology of Complicating Bronchopneumonia. — Considerable dif- ference of opinion has existed as to the comparative influence of the diphtheria bacillli and other organisms in the causation of pneumonia complicating diphtheria. Thaon, in 1885, was the first to study the relation of the diphtheria organism to secondary bronchopneumonia. He showed microscopically in the lung tissues the relation of the bacilli to the inflammatory process. The diphtheria bacillus was not found alone, but in association with various cocci. Loeffler, iri his study of the bacteriology of diphtheria in 1884, reported the presence of the diphtheria bacillus in the lung, but regarded it as a post-mortem invasion. THE PATUOUMjIY OF Dl I'llTII I'UilA {](])>, Various observers since this time liav(; [)iiblis}if'(| t[i(; results of their study of tliis siihjeet. Tliese reports (ixhihit extretrxily fhver^erit firnJings. For instarice, Wriht}ifria liave l)een studied i)y Branlt, Fiirhrinf^er, l^'i.s(;hl, Cjcrtel, iiernard and Felsenthal, Reiehe, Katzenstein, and others. The alterations iriflueed by experimental diphtheria have been specially described l;y Flexner. Councilman, Mallory, and Pearce examined the kidneys micro- scopically in 171 cases. The ages of the patients varierl from two months to thirty years, and averaged three and three-quarter years. It v^as found possible to divide the kidneys into five classes according to the microscopic findings: 1. Those in which degeneration of the epithelium was the chief or the only lesion. 2. Those in which acute interstitial changes consisting of cell accumulations in the vessels and interstitial tissue were present. 3. Those in which the chief lesions were found in the glomeruli. 4. Those in which hemorrhages into the tubules were present. 5. Those in which chronic interstitial lesions were present as shown by atrophied glomeruli and increase in the connective tissue. 1. Degenerative Changes. — Degenerative changes of varying grades were found in 112 of the 171 cases examined. Many kidneys, almost or quite normal in appearance, showed under the microscope a con- siderable degree of degeneration. The degeneration was slight in 26 cases, moderate in 38, marked in 37, and extreme in 9 cases. The most extreme degree was found in severe cases dying shortly after entry into the hospital. Fatty degeneration, as determined by examination of frozen sections, was only slight in degree; it occurred in 44 out of 58 cases examined in this manner. Some degree of hyaUne degeneration w^as found in almost all the cases, affecting prominently the proximal convoluted tubules. Casts w^ere present in practically all of the cases, especially when the hyaline degeneration was pronounced. The most constant change seen in the glomeruli consisted of a small amount of granular coagulum between the tuft and the wall. In 40 cases of simple degeneration the urinary record is available. Albumin was found in 33 of the cases. There was, with some excep- tions, a general agreement between the presence of albumin and the degree of degeneration. There appeared to be no relation between the character of the degen- eration and general infection with various bacteria. In the 110 cases a general infection with diphtheria bacilli was noted in 20 cases, with the streptococcus in 29 cases, with the staphylococcus aureus in 4 cases, and with the pneumococcus in 3 cases. In the 9 cases of severe degeneration general infection was noted but once, and that with the streptococcus. 2. Acute Interstitial Changes. — iVcute interstitial nephritis, evidenced by infiltration of the interstitial tissue with cells of the plasma t^•pe, was present in 43 of the cases. The kidneys were but slightly, if at all, enlarged, save in the most marked cases, when considerable swelling was present. The interstitial infiltration was general in all parts of the kidney, but was more intense in foci; most of the cells were plasma 668 DIPHTHERIA cells with typical nucleus and protoplasm. Lymphoid cells and, in severe cases, large phagocytic cells were also present. The amount of epithelial degeneration varied in different cases. The infiltrating cells were usually limited to the interstitial tissue; the changes we.re accompanied by alterations in the vessels, the cell infiltration at times almost obscuring them. The degeneration found in foci of intense infiltration appears to depend on malnutrition resulting from blocking of the vessels by the cells. In all of the interstitial cases the duration of the disease was more prolonged than in the cases of simple degeneration. The average duration of the illness was twenty-one and one-half days. The inter- stitial process apparently takes some time for its development, and the cases dying early do not, as a rule, show the process at its maximum. Mixed infections with scarlet fever and measles are more apt to cause interstitial changes than simple degeneration. The urine was tested for albumin in 15 cases, in 14 of which it was found present. 3. Glomerular Changes.^ — This variety of the disease was found in 11 cases, in all of which the glomerular changes were the predominating ones. Lesions of the glomeruli were uncommon in the cases of simple degeneration and in those showing interstitial involvement. The first evidence of change in the glomeruli is increase in the number of cells. The endothelial lining of the vessels undergoes proliferation and occludes the vessel. Later a hyaline degeneration of the cells and the vessel walls takes place. Glomerular nephritis was present in subjects averaging a greater age than the degeneration and interstitial cases. The average duration of the disease at the time of autopsy was also greater. 4. Hemorrhage. — Slight hemorrhages in the kidney were seen in 3 cases, but true hemorrhagic nephritis was noted in but 1. The red blood cells were found chiefly in the tubules and the interstitial tissue. The rarity of hemorrhagic cases was considered surprising. 5. Chronic Cases. — In 4 cases chronic changes were present, as evidenced by atrophy of the tubules and increase in connective tissue. In these cases death occurred at entirely too early a date to attribute the changes to diphtheria; the lesions were evidently due to some ante- cedent disease. Councilman, Mallory, and Pearce conclude that lesions of the kidney, varying from simple degeneration to the more serious conditions of acute nephritis, are found in all fatal cases of diphtheria; there is, however, no type of lesion peculiar to the disease. Lymph Nodes. — The changes in the lymph glands have been studied by Bizzozero, Oertel, Bullock and Schmorl, Barbacci, Bezancon and Labbe, Flexner, and Councilman, Mallory, and Pearce. The most constant changes observed by these investigators have been a marked cellular infiltration and the presence of necrosis. Bullock and Schmorl found diphtheria bacilli in the nodes in 11 out of 14 cases. Councilman, Mallory, and Pearce examined the lymph nodes in 109 cases. They were constantly the seat of pathological changes. Tim PATIIOLOCV 01'' DII'II'IIIFJUA GOD Tlie nodes iiiosl. involved are tliose neuresl, l,o the seat of exudate - the tonsils aixl the cervical {glands. The distant nodes are very rarely aH'ected. The lesions are most prononnced in severe cases, in vviiich a fatal termination occnrs early. Two varieties of lesions are descril)ed : 1. The ordinary lesions, which may follow an injnry of almost any sort and wliicli consist in congestion, hemorrhage, and diffuse and circumscribed necrosis. Numerous new cells are found which are derived partly from the lymphoid cells, and partly from proliferation of the endothelial cells of the sinuses and reticulum. The swelling of the nodes is due chiefly to congestion, hemorrhage, and dilatation of the sinuses; the lymphoid cells do not increase perceptibly in number. 2. Lesions which are distinctive of diphtheria, but which may be found in other infectious diseases in children. Foci are formed which are similar in appearance to miliary tubercles; these are the result of a combination of processes^proliferation, })hagocytosis, and degen- eration. Large epithelioid cells are formed from proliferation of the endothelial cells of the reticuhim and vessels. These devour lymphoid cells, and they themselves ultimately undergo necrosis. Bacteria seem to exert no direct influence in the production of these lesions, and were not found in the nodes. The lesions are believed to be due to the absorption of the toxic products of the diphtheria bacilli and other organisms. The lesions found in the tonsils differed somewhat from those seen in other lymphoid structures. They were constantly present, and in most cases more pronounced than in the glands. Thymus. — Flexner studied the changes in the thymus gland in experimentally induced diphtheria in animals. He called attention to the frecjuency with which the degenerated cells occurred in the neigh- borhood of the Hassel bodies. The changes in general were similar to those observed in the lymph nodes. Councilman, Mallory, and Pearce examined the thynuis in 20 cases. The principal change found was degeneration of the lymphoid cells. The degenerated cells were usually seen in large cells with vesicular nuclei; the changes were most marked in the vicinity of the Hassel bodies. There was dilatation of the lymphatics and hyaline degen- eration of the walls of the vessels. No bacteria were found in the sections. Skeletal Muscles. — Councilman, jMallory, and Pearce state that where fatty degenerations of the heart and the nervous system are present, a similar change will be found in the skeletal muscles. In one case in which the nerve fibres of the central nervous system and of the per- ipheral nerves showed marked fatty degeneration, the muscles of the tongue, of the ulnar side of the forearm, the sartorius muscle, and the biceps of the thigh exhibited a similar degeneration. In another case where fatty degeneration of the heart and nervous system was pronounced the muscles of the tongue, the diaphragm, and the tibialis anticus were likewise degenerated. 670 DIPHTHERIA Pancreas, Adrenals, Thyroid Gland, Salivary Glands, Testicles, Pituitary Body. — No gross changes were observed in these glands by Councilman, Mallory, and Pearce; neither did a careful microscopic examination reveal the presence of pathological changes. In one case the submaxillary gland showed superficial necrosis and purulent infiltration due to extensive inflammation from the throat. Welch, Flexner, and Wright commonly observed congestion, hemor- rhage, and focal necrosis in the adrenal glands in experimental diph- theria, but such changes apparently do not occur in this disease in the human subject. Nervous System. — Councilman, Mallory, and Pearce refer to a study of certain nerve structures made in 28 of their cases by Thomas and Steensland. The cases were selected either on account of the presence of cardiac symptoms, paralysis, or the severity of the disease. Various cranial and other nerves were submitted to careful microscopic study. In all of them some grade of fatty degeneration was noted. The degen- eration seems almost invariably to begin in the myelin sheath. The change in the axis cylinder consists chiefly of an irregular swelling which often causes it to present a beaded appearance. The cerebrum was examined five times, the cerebellum twice, the pons three times, the medulla four times, and the cord seven times. In all of these examinations a varying degree of fatty degeneration was present in the white substance. The same change was noted in the anterior and posterior nerve roots. In general it may be said that a slight to a marked diffuse fatty degen- eration, involving the central nerve fibres and their peripheral exten- sions, occurs in certain cases of diphtheria. Bone-marrow. — Councilman, Mallory, and Pearce examined the bone-marrow in 48 cases of diphtheria. Of this number all but 3 were children. In all of the cases the marrow was hyperplastic, although in the 3 adults the hyperplasia was less pronounced. In the latter the marrow was reddish with areas of yellow fat. In the children the marrow varied in appearance, but was usually red, of firm consistency, and removable in solid pieces. Very little connective tissue was found in the marrow, and that was along the arteries. The veins were numerous and the walls like those of capillaries; it is through these thin walls that the marrow cells appear to enter the blood. The changes in the marrow in diphtheria are not distinctive of the disease, as they are also found in other infectious diseases. Blood. — According to Baginsky there is an increased coagulability of the blood in diphtheria due to the action of the toxin on the blood stream through weakness of the heart, and also as a result of the lowered blood pressure and changes in the lining of the bloodvessels. This, it is claimed, may lead to the formation of thrombi in the heart or blood- vessels. In severe septic cases a thinning or dissolution of the blood occurs, which may cause hemorrhages in various tissues. The specific gravity is said by Grawitz to be raised at the height of 77//'; I'ATIIOIAJdY ()/<' bll'IITllHUIA f;71 the disease, both in (h'phtheria, in man, and in exyx'rirnenf;)! (li])lith('ria in animals. Red Cells. -Diii'i 11 <^f the first f(^w (hiys of the disease the red eorjjuscles are about normal in number, according to the investigations of Morse, Ewing, Engel, and Billings. From the fifth to the fifteenth days, liillings observed an average loss of 510,000 cells per cubic millimetre. The loss ranged from 470,000 on the third day to 2,040,000 on the sixth. These were in cases not treated by antitoxin. Of 2?> severe and carefully counted cases treated with antitoxin, 3 alone exhibited a reduction in the erythrocytes, the loss being less than 400,000 cells per cubic centi- metre. Cabot remarks that "antitoxin largely prevents the ana'mia which usually develops in the first five to ten days." Healthy persons receiving antitoxin, according to a study of 15 cases by Billings, show a moderate loss of red cells in about one-half of the cases; the greatest diminution observed was 930,000 per cubic millimetre. Haemoglobin .^ — A reduction in the hajmoglobin occurs coincidently with the diminution in the number of red cells, but restoration of the former takes place more slowly than the latter. Billings states that in cases treated without antitoxin an average loss of 10 per cent, was noted; whereas, when antitoxin was administered the reduction of the haemoglobin was less marked. Leukocytes. — Gabritschewsky, in 1894, was the first to point out the more or less constant hyperleukocytosis in diphtheria. He demon- strated by animal experimentation that the increase in the white cells was due to the action of the diphtheria toxin. Morse found a leukocytosis in 26 out of 30 cases, Ewing in 49 out of 53, and Billings in 34 out of 36 cases. The grade of the leukocytosis is in a general way proportionate to the severity of the disease. Morse observed very high counts in the fatal septic cases. Cabot says that when leukocytosis is absent the cases are either very mild or very severe, conditions analogous to those noted in pneumonia and septicsemia. The counts range from normal to 48,000 (Morse), or to 38,000 (Billings). Bouchut counted over 75,000 white cells per cubic millimetre in some of his cases, and Felsenthal found 148,229 in one case. The white cells ordinarily increase as the disease progresses, and decrease as convalescence sets in. According to Ewing, the leukocyte count is not influenced by the use of the antitoxin serum, except during the first twenty-four hours after its injection. Within thirty minutes the leukocytes are said to be considerably diminished. Engel states that antitoxin in the beginning causes a slight increase in the percentage of lymphocytes; in some cases the increase is pro- nounced. In one case after injection they rose from 24 to 65 per cent. Engel also emphasizes the bad prognostic import of the presence of a considerable number of myelocytes. It is generally conceded that an examination of the blood in diph- 672 DIPHTHERIA theria lends little or no aid in diagnosis. The absence of leukocytosis and the presence of a considerable number of myelocytes would seem to be of ill augury. THE DIAGNOSIS OF DIPHTHERIA. As diphtheria is a communicable disease with a decided predilection for young children, among whom it is also most fatal, it is important that an early diagnosis should be made, both with regard to prevention and treatment. Without a history of previous exposure to the infection it is confessedly difficult to recognize the disease in its very earliest manifestations; for there is no throat affection more varied in its clinical aspect and more deceptive in its initial stage than diphtheria. But, fortunately, the disease is not long in revealing its true nature. In the majority of cases the diagnosis is not difficult after the affection has continued for twenty-four hours, since by this time the characteristic exudation may be seen on the tonsils or some part of the fauces. When thus clearly marked the nature of the throat disease is at once apparent on the first examination. But all cases are not so readily diagnosticated, even by experienced physicians. Neglecting to inspect the throat of a child, who is feverish and indisposed, may sometimes be a reason for failure in making an early diagnosis. While sore throat is one of the earliest symptoms of diphtheria, yet it is a fact that many children, even those old enough to make known their sensations, do not complain of the throat until the disease has made considerable progress. On his first visit to a child, on account of whose illness he has been summoned, the physician should be careful to examine the fauces, especially when diphtheria is prevailing in the neighborhood. In this way the disease may be discovered early and its spread to other members of the family prevented. In well-marked cases it is usually not difficult to make the diagnosis. In doubtful cases it may be helpful to know whether the patient has been recently exposed to the infection of diphtheria, scarlet fever, or some other infectious disease. If exposure to diphtheria is known to have occurred, the mildest form of sore throat should be regarded with suspicion and carefully watched for further development. But, in a section of the country where diphtheria is not prevailing, it is probable that a sore throat presenting some of the characteristics of the disease will turn out to be something else. It sometimes happens that an early diagnosis is not made because the exudation is concealed in the crypts of the tonsils, or in some other depressions of the faucial surface. When thus located it may be brought into view by pushing the tongue depressor far back on the tongue and causing the child to retch slightly; or these surfaces may be exposed to view by having an assistant make firm pressure on the neck near the angle of the jaw while an examination of the throat is being made. In some cases it is impossible to make a positive diagnosis, clinically, 77/ A' DIAdNOShH OF 1)1 1'lll'll Fill A 073 until the disease h;is been under ()[)servati()M for two or three days. Tiiis is more (!Sj)eeially triu; in some; forms of nasal diphtlieria, without involvement of the fauces to a greater ext(;nt than the oeeurrenee f)f a general hypenemia. The uneven surface of the cavities of the nose favors concealment of the disease until it has made some progress. It may then be discovered either by insjx'cting the nares at their external orifices, or by an examination with a nasal speeuhnn. In nasal flij;h- theria there is apt to be a mucopurulent diseharg(; from the nose, and when there are seen in this discharge small, white specks, exudate is probably present, although it may not yet be visible. It usually, however, makes its appearance before the disease terminates. There are no prodromata that are peculiar to (iij)htheria. The general malaise, followed by headache, nausea and vomiting, so commonly seen, are the forerunners of many other affections also. Even the sore throat, pain in swallowing, tenderness of the glands near the angle of the jaw, and swelling of the neck are all present in the ordinary forms of tonsillitis. The distinguishing feature of diphtheria is the peculiar exudation that appears upon the mucous membrane, particularly in the fauces. A knowledge of the fact that this exudation takes place not only into the epithelium, but also into the subepithelial tissue, is helpful only to a limited extent in solving the problem of diagnosis. Indeed, in many severe cases the diphtheritic process does not penetrate deeply into the mucous membrane, as it peels off quickly and leaves only small areas of superficial ulceration. On the other hand, an exudation of streptococcic origin is sometimes very adherent, and its disappearance may be followed by marked ulceration of the mucous membrane. But in most streptococcic affections of the throat, certainly in the milder varieties, the disease is limited to the tonsils, and the greater part of the exudation may be removed with a cotton swab. In considering the diagnostic feature of the diphtherial membrane it is necessary to recall some of its characteristics already described. It is deposited not only on the tonsils, but frequently also on the pillars of the fauces, the soft palate, the pharyngeal wall, in the nares, and in the larynx. One of the peculiarities of the meml)rane is that it is liable to start on some of the small prominences of the fauces, such as the uvula, epiglottis, and the like. As already mentioned, it is also liable to form in some of the small recesses, such as the lacunfe of the tonsils and the ventricles of the larynx. The formation of membrane on the uvula, especially on its posterior surface, is believed by some writers to be almost pathognomonic. When seen on the sides of the uvula it is quite sure to be present on its posterior surface also. Frequently the entire uvula is invested with membrane, which is often shed as a complete cast, resembling, as Trousseau has said, the finger of a glove. When the diphtherial exudation is examined carefully it is found to be distinctly membranous. It is of a yellowish-white color, and when exfoliated in large pieces or casts and allowed to float in water it bears a strong resemblance to pieces of chamois skin. Lennox Browne's description of the exudation is worth repeating. He says it "begins 43 674 DIPHTHERIA almost invariably as a thin, bluish-white deposit, something like a shaving from the boiled white of an egg of the duck, goose, or plover. As the deposit increases in thickness, it gradually becomes more white and opaque, resembling the boiled albumen of a fowl's egg, or it may then partake of a very pale lemon tint. Then it becomes of a yellowish or greenish gray, brown, and sometimes almost black, as the necrotic process advances, or as blood is extra vasated. Only in the comparatively uncommon case of a lacunar diphtheria do we see the exudation com- mencing as discrete spots of deposit, which may be of a yellow color at the very first onset, and, even when coalesced, may never exhibit the pearly or opalescent appearance which characterizes the more ordinary form on its first manifestation." He adds, "The membrane is sometimes plastered, as if put on with a palette knife, or laid on with a trowel." This latter comparison applies with much aptness to what is seen when the entire fauces and soft palate are covered with the exudation. Adenitis, or more or less enlargement and tenderness of the lymphatic glands of the neck, is a symptom rarely absent. Its im- portance depends to some extent on the region in which the glands are involved, and the degree of inflammation and swelling. In mild tonsillar diphtheria the cervical glands alone are swollen, but, as a rule, only very slightly. In the more severe cases, including the complex or septic form of the disease, the whole chain of cervical glands is converted into one large mass. The inflammatory enlargement includes also the periglandular cellular tissue. In such cases not only the cervical, but the submaxillary and sometimes the parotid glands are affected. Catarrhal Croup. — ^There is frequently some difficulty in distinguish- ing between membranous croup in its early stage, and catarrhal, spas- modic, or non-specific croup. But if a few of the principal points of difference be borne in mind the difficulty should not be very great. For instance, in membranous croup the symptoms are progressive, being as well marked in the day-time as in the night. The hoarseness gradually increases, so that the child in a short time can speak only in a whisper. The breathing becomes more and more obstructed as the exudation increases; the temperature reaches 100° to 103° F., and the child constantly grows more restless and cyanotic. There is marked recession of the ensiform process of the sternum, and of the lower ribs. These symptoms are not relieved by the relaxing influence of an emetic. Moreover, the characteristic exudation may be present in the fauces. On the other hand, in catarrhal or spasmodic croup the symptoms are usually intermittent, being due to a paroxysmal spasm of the glottis, resulting from subacute laryngitis. In the vast majority of instances the affection occurs at night-time, and more often in the early part of the night. During the day the symptoms, if present at all, are usually much more moderate. The duration of the paroxysm varies from a few minutes to several hours. The voice, though hoarse, is very rarely quite extinct or whispering, and scarcely ever more than temporarily so. 77//'; DIAdNOHIH OF 1)1 1'llTII l<:UIA 075 This is a diagnostic point of niucb value in (Jistinguisliing Ijetwccn tlip two forms of crouj). In sj)asnio(Jic croup an cnictic generally gives relief, but does not in membranous erouj). The fauees are free from exudate. Pseudodiphtheria. We have already remarked that a membranous sore throat, in whi(;h the streptococcus is the principal if not the sole orgaiu'sni present, sometimes occurs, and we have pointed out some of the characteristics of this ad'ection in comjjarison with those of true diphtheria. We repeat that, as a rule, in true diphtiieiia the exudate is so intimately connected with the mucous membrane that it cannot be removed without injuring the parts, while in pseuflodiphtheria it lies upon the surface and may be quite readily removcf]. It must be admitted, however, that there are many exceptions to this rule. The physician, therefore, will often find it impossible to make a positive diagnosis without a culture and a microscopic examination. Follicular Tonsillitis. — There is perhaps no throat affection more often mistaken for diphtheria than follicular tonsillitis. It is a very common disease, being more frequently seen in some families than in others. It sometimes spreads as though it were contagious. It begins with sore throat, fever, and tenderness in the neck below the angle of the jaw. There is often a good deal of constitutional disturbance, such as high temperature, headache, and chilliness, with sometimes pain in the back and extremities. The fauces at first are hypersemic, but the tonsils soon become enlarged and dotted over with rounded masses of whitish material of pinhead size. These dots frequently coalesce, forming quite large patches, particularly in the crypts of the tonsils. The dots or patches consist of a peculiar secretion having incorporated with it epithelial cells. It differs from the diphtherial exudate in that it is readily detached by a swab. The cheesy dots that form on the tonsils will, when crushed between the thumb and finger, emit a fetid odor. The disease is of short duration, and is not followed by sequel [e. The diagnosis is easily made, except in some cases of the mildest form of diphtheria when dift'erentiation may be difficult. In acute quinsy the jaws are stiff, and there is often considerable difficulty in opening the mouth sufficiently wide for a satisfactory inspection of the fauces. Where any doubt is felt as to the nature of the affection it may be readily dispelled by a bacteriological examination. Herpetic Pharyngitis. — There is usually no great diflaculty in recog- nizing an herpetic pharyngitis, but, like follicular tonsillitis, it is occa- sionally mistaken for mild diphtheria. If seen in the early stage, before the minute vesicles have disappeared, the diagnosis is easily made; but the ulcers that remain often show a whitish covering, which has often been mistaken for diphtherial exudate. As the ulcers are very small, the whitish concretions are usually seen in the form of dots. It is only when these concretions unite and form a patch that any difficulty is experienced in the diagnosis. It has been said that the presence of an herpetic eruption on some other part of the body would afford presumptive evidence that the throat affection was of the same 676 V DIPHTHERIA nature, but we have often seen herpes labiaHs in children suffering from diphtheria. Fortunately, in these diseases the clinician does not have to base his diagnosis upon symptoms alone; he can invoke the aid of bacteriology. Gangrenous Pharyngitis. — In our experience gangrenous pharyngitis is rare in diphtheria. We do not recall having seen a single case. The affection, however, is not uncommon in scarlet fever. The ulcerative action and loss of tissue are much more extensive than that which is seen in diphtheria. The necrotic tissue resulting from the gangrenous process has often been mistaken for diphtherial exudate. The pseudo- membrane in this variety of sore throat is, from the beginning, of a dark-gray or brownish color, and is exceedingly offensive. On the other hand, the pseudomembrane of diphtheria is white or yellowish-white in the commencement, and continues so to the end unless it becomes stained with blood. The foetor in the latter disease is mild in comparison with the former. The diagnosis is not difficult if the case comes under observation at the beginning. Stomatitis.' — In diffuse inflammation of the mucous membrane of the mouth the small ulcers that commonly appear show a whitish covering. This condition not infrequently increases to the extent that many of these ulcers coalesce, forming patches consisting of a whitish, curd-like matter; and the affection often extends gradually to the roof of the mouth, the inside of the cheeks, and may even reach the pharynx. The exudation is usually thin, and sometimes covers evenly a large part of the mucous membrane of the mouth, but more commonly it is seen in irregularly scattered patches and points. When the disease assumes this appearance it is occasionally confounded with diphtheria. In making a diagnosis it is important to note that the exudation is thin and filmy; it never becomes membranous. On parts where it is thicker it is curdy or cheesy. We have known gangrenous stomatitis and even syphilitic sore throat to have been mistaken for diphtheria. In view of the general character- istics of these affections the diagnosis is not difficult. The presence of albumin in the urine in diphtheria deserves some notice as a diagnostic sign. We have found it in quite a large pro- portion of our cases in which the urine was examined. Its presence would be of still greater diagnostic importance were it not true that it is occasionally found in some other varieties of inflammation of the throat. Since the advent of bacteriology as a science the clinician has at his command a most useful means of determining the diagnosis of diph- theria in all doubtful cases. While every well-informed physician should be familiar with the clinical evidences of the disease, yet as the clinical disguises of this throat affection are so varied it is fortunate that the doubtful points of diagnosis can be solved by bacteriology. Therefore, any consideration of the subject of diagnosis in diphtheria would be regarded as incomplete at the present day without some reference to the means employed to determine the presence of the Klebs-Loeffler bacilli in the pseudomembrane. 77//'; i)iA(JN()Sis OF nii'ii'i'iiKin \ 677 The Bacteriological Diagnosis of Diphtheria. In a patient presenting .suspicious cliuicjil evidences of diplillicria, the diagnosis may Ix^ firmly estahlislied by determining the [jresence or al)sence of the di})hth(;ria hacilH in the false inenihrane. 'i'his may be accomplished by examination of (a) smears, and (b) cultures. Smears. — In a large ])ercentage of cases a satisfncfory result may be obtained from an inunediate microscopic examinafion of the exudate present. A cover-glass is smeared with material taken from the throat by means of a swab. The cover-glass preparation is allowed to flrv, is then passed several times through a flame to fix the albumin, and is finally stained witli Loeffler's solution of methylene blue. By this means the presence or absence of bacilli may often be determined in a few minutes. The rapidity with which the examination can be made makes it a procedure of great value, particularly where an immediate diagno.sis is a matter of great importance. We have examined a considerable number of smears at the Municipal Hospital, and in these casts we were enabled in the vast majority of cases to predict the subsefpient cultural findings. The procedure just mentioned, however, has only a relative value and should not be depended upon to the exclusion of the culture. The bacilli found in smears are ordinarily much less typical than those grown upon culture media, and the chances of contamination are greater. Abbott^ says: "There are other organisms present in the mouth cavity, particularly in the mouths of persons having decayed teeth, the morphology of which is so like that of the bacillus of diph- theria that they might easily be mistaken for that organism, if subjected only to the usual method of microscopic examination." He adds, however, that where there is suspicious clinical evidence the direct examination of smears will serve to confirm or negative the diagnosis in the vast majority of cases. Cultures. — Cultures are ordinarily made with a swab, although a platinum loop may be employed for the purpose. The swab consists of absorbent cotton wrapped around the end of a piece of heavy w'uq. The swab, enclosed ordinarily in a plugged test-tube, is sterilized by heat. In taking the culture the tongue should be depressed by means of a spoon or depressor, and the swab firmly rubbed over the surface of the membrane. When no membrane is present, the swab should be brought in contact with the tonsils, faucial pillars, and pharyngeal wall. When laryngeal symptoms alone are present, the swab should be introduced as far down as possible. The moistened cotton is then rubbed lightly over the surface of a tube of Loeffler's blood serum, care being taken to carefully replace the cotton plug. The swab containing the remains of the infected material should be returned to its own tube and subsequently destroyed or disinfected. 1 The Principles of Bacteriology, 5th ed., 1899, p. 361. 678 DIPHTHERIA Great care should be taken not to make the culture directly after antiseptic applications have been applied to the throat. It is well, in such cases, to wait a half-hour or an hour before culturing. The inoculated tubes are incubated at a temperature of from 99° to 100° F. (37° C.) for twelve to fourteen hours, at the end of which time the colonies may be examined. The gross appearances of the culture are more characteristic at the end of twenty-four hours. The diphtheria bacillus grows so much more rapidly than other mouth organisms upon the surface of Loeffler's blood serum that they are often the only conspicuous colonies present. The colonies are large, round, grayish-white or cream-colored, elevated with irregular periphery, which is less dense in the centre. Examination of Cultures.— A drop of sterile water is placed upon a clean cover-glass and rubbed up with a couple of colonies which have been detached from the culture media with a platinum loop. The preparation is allowed to dry in the air and is then passed several times through the flame of a Bunsen burner or alcohol lamp. It is then covered with Loeffler's alkaline solution of methylene blue for ten minutes, after which it is rinsed, dried, and mounted in balsam. The specimen is examined with a one-twelfth-inch oil-immersion lens. Diphtheria bacilli may be found in pure culture, or micrococci of different varieties may also be present. In order to test the virulence of diphtheria bacilli a guinea-pig is subcutaneously injected with a small quantity of a pure culture in bouillon. Death results in from twenty-four hours to five days, usually within seventy-two hours. There is intense oedema with congestion and hemorrhage at the site of injection. The changes in the other tissues, according to Abbott, are as follows: Swollen and reddened lymphatic glands, increased serous fluid in the peritoneum, pleura, and pericardium; enlarged and hemorrhagic adrenal bodies; occasionally slightly, swollen spleen; and sometimes fatty degeneration in the liver, kidney, and myocardium. The bacilli are always to be found at the site of inoculation, most abundantly in the grayish-white, fibrinopurulent exudate. THE PROGNOSIS OF DIPHTHERIA. The forecast of diphtheria cannot be made with any degree of certainty. The disease itself, to say nothing of the complications that are liable to occur, is so treacherous that it is almost impossible to predict a favorable ending of any attack however mild the earlier symptoms may be. Not infrequently cases that appear to be mild in the beginning and give the best promise of recovery suddenly change into a severe form through extension of the diphtheritic process into the larynx, or the development of some dangerous secondary affection. On the other hand, cases that begin with marked severity, giving rise to gloomy forebodings, often take a favorable change and speedily end in ^recovery. Tim PiiocNOHJH OF j)ii'iiriii<:iiiA 071) So variable are the elements of prognosis in diphtheria that tliey cannot be considered from any single standpoint. C)ne mnst take into consideration the prostrating efl'ects of the toxins of the disease; the history, enviromnent, and age of tlu; f)atient; the complications affecting vital parts during the course of the attack, and the nature of the secjuehe. Likewise, the character of the prevailing epidemic must be taken into account. In some epidemics a large proportion of the cases are mild, and the death rate is low. In other epidemics, or in sr>me localities, the disease assumes a more severe form, and, in spite of the best treatment, the proportion that perish is much larger. A death rate as high as 60 per cent, has been reported; while in very rnihl epidemics it has been as low as 5 to 10 per cent. It is a question whether social status and domestic surroundiricjs have as much to do in determining the character of the disease as is generally supposed. It is true, however, that when diphtheria breaks out in an institution for children, especially foundlings, it is apt to be attended with great fatality. In our experience the patients sent to the hospital from careless and indigent families are not more liable to suffer from severe diphtheria than those which come from better and more sanitary homes. Nor do we find that delicate children perish in a larger pro- portion than the robust. In speaking of the influence exerted by social status, Lennox Browne says it has appeared to him "that when diph- theria attacks members of the upper classes it is often more malignant, and runs a more qiiickly fatal course than among the indigent; the disease finding, as it w^ere, a more receptive soil in the case of these delicately nurtured than in those whose systems are in a manner accus- tomed to insanitary influences. On the other hand, and for obvious reasons, recovery from the sequelae, when once the acuteness of the attack has passed off, is more expeditious and complete in the well- to-do." There can be no doubt, however, that when diphtheria is at all severe, unsanitary surroundings would contribute toward an unfavorable prog- nosis. The less adequate the facilities for caring for the patient and the poorer the service, the greater are the probabilities that the disease will spread and increase in virulence. Where no attention is paid to ventilation of the sick-room, the vitiated condition of the atmosphere tends to lower the resisting power of the patient, and thus diminishes the chances of recovery. Idiosyncrasy, or any family susceptibility to diphtheria that may be known to exist, should be taken into consideration as affording important prognostic data. Every practitioner knows how fatal the disease is in some families. It is worthy of notice that when diphtheria breaks out in a family, or in a neighborhood, children are almost always the first to be attacked, showing that in them the susceptibility to the disease is most marked. Age. — There is not only an age disposition to diphtheria, but there is also an age mortality, and this must be taken into account in a forecast of the disease. The vast majority of all deaths from this affection 680 DIPHTHERIA occurs among children under five years of age, and the mortahty rate at this age period is vastly higher than in any other quinquennial period of life. This statement is confirmed by the statistics of all large hos- pitals for the treatment of diphtheria patients. The following table shows the mortality, according to age, in the Asylums' Board Hospitals, London, 1892-93:^ Percentage. Age. Under one year f 1892 ^1893 One to two years fl892 1 1893 Two to three years J 1892 11893 Three to four years f 1892 11893 (1892 Four to five years < ^ggg rl892 Five to ten years i ,gg„ f 1892 Ten to fifteen years -j j^ggg f 1892 Over fifteen years ■! .g^g Admitted. Died. . 49 31 . 40 37 89 68 . 108 66 . 166 106 274 172 . 163 90 . 219 131 382 221 . 195 96 . 296 149 491 245 . 240 106 . 339 143 579 249 . 631 163 . 880 233 1511 396 . 209 15 . 298 30 507 45 . 414 16 . 610 36 76.4 62.7 26.2 5.0 Of 1000 consecutive cases of diphtheria observed by Lennox Browne the age mortality was as follows: Age. Under 1 year 11 1 to 2 years 2 ' 3 " 3 ' 4 " 4 ' 5 " 5 ' 6 " 6 ' 7 " 7 ' 8 " 8 ' 9 " 9 ' 10 " 10 ' 11 " U ' 12 " 12 ' 13 " 13 ' 14 " 14 ' 15 " Over 15 " f cases. Deaths. Percentages 11 5 45.45 71 45 63.38 85 34 40.00 117 54 46.15 118 43 36.44 108 34 31.48 84 24 28.57 57 9 15.78 31 11 35.48 38 5 13.15 29 8 27.58 20 16 22 2 9.00 15 2 13.33 178 7 3.93 1000 1 Lennox Browne, Diphtheria and its Associates. Till': I'UOdjMOSI.S ()!<' DII'li'l'IIICidA G81 Classified a(;c()nHii(^ to (juinqucnnial a^c [xtIcxIs, \\\c cusvh in the above tabU^ show as follows: Age. No. of rji,Ki,'H. Under 5 yearH WZ 5 to 10 " 31K 10 " 15 " 102 Over 15 " 178 1000 /)«fUllH. PcrceiitaKCH IHl 45.0 83 26.1 Vl 11.7 7 ■.•,'.)Z 283 2».3 In the following table of statisties, including over 9000 oases of diphtheria, which were treated in the Municipal Hospital, Philadelphia, during a period of ten years, from 1893 to 1902, iiichisive, the nuujljer of patients and the mortality rate within certain age [xriods are shown: Under 1 year. 1 to 5 years. 5 to 10 years. 10 to 15 years. 15 to 25 years. 25 years and upward. •6 •6. ^ . "^ . -c T3 . "O Year. ■oii "O o ^± o '^?. •o o ■C -i ■a o ■C ^ •d o ■6s 13 o ■<^ 0) s <;^ o ^■n a> t-. -t^.n a> "i^ a; <.t: 0) u* H ;; Ph U Q Ph ■a « Oh ti O Q^ " ft P. b « s:, 1893 3 2 66.66 82 35 42. 68 53 17 32.07 18 3 16.66 36 3 8.33 25 2 8.00 1894 16 i) 56. 25 218 98 44.95 120 36 30.00 31 6 19.35 52 3 5.77 28 2 7.14 1895 25 10 40. 00 327 122 87.3 187 43 22.9 46 7 15.2 56 4 7.1 65 4 6.1 1896 S3 IS 54.54 404 12S 31.68 27 (i 35 12.68 71 5 7.04 49 1 2.04 36 3 8.33 1897 34 16 47.05 560 199i 35.53 437 65 14.87 126 14 11.11 89 3 3.37 49 3 6.12 1898 42 20 47.61 552 200; 36.23 447 66 14.76 93 8 8.60 47 3 6.38 48 1899 38 24 63. 15 659 181 27.46 462 59 12.79 102 7 6.81 62 2 3.22 50 2 4.00 1900 40 21 52.50, 595 192 32.27 473 71 15.01 117 7 5.9S 90 4 4.44 52 3 5.76 1901 30 15 50. m 374; Il9i 31.81 287 28 9.75 ]06| 5 4.71 56 6 10.71 36 1 2.77 1902 38 12 31.57 3061 97 1 1 31.08 159 2901 25 445 15. 72 40 1 2.5 33 2 6.06 26 1 299 147 49.16 4076 1371 33.63 15.33 750 63 8.4 570 31 5.43 1 415! 20 1 4.81 Sex. — We see no reason why sex should exert any influence on the mortality rate, and yet according to our observation, as well as that of some other writers, the death rate among the males is almost constantly in excess of that of the females. The following table shows the mortality, according to sex, of all cases of diphtheria treated in the Asvlums' Board Hospitals, London, from 1888 to 1894, inclusive:^ Sex. Admitted. Males 5,245 Females 6,353 11,598 Died. Per cent 1677 31.97 1839 28.94 3516 30.31 The following table shows the mortality, according to sex, of 1000 consecutive cases of diphtheria observed by Lennox Browne: Sex. Admitted. Died. Males . . . 533 162 Females 467 121 1000 283 1 Lennox Browue. Loc. eit. 682 DIPHTHERIA The following table shows the mortality, according to sex, of all cases of diphtheria treated in the Municipal Hospital, Philadelphia, from 1893 to 1902, inclusive: Males Females. Year. Admitted. Died. Per cent. Admitted. Died. Per cent. 1893 . . 94 29 30.85 123 33 26.82 1894 . . 214 81 37.85 251 73 29.08 1895 . . 315 83 26.4 391 107 27.3 1896 . . 424 100 23.58 445 90 20.22 1897 . . 636 147 23.11 659 153 23.21 1898 . . 562 152 27.04 667 145 21.73 1899 . . 641 139 21.68 732 136 18.57 1900 . . 669 151 22.56 698 147 21.06 1901 . . 416 94 22.59 473 80 16.91 1902 . . 285 64 22.45 316 73 23. 10 4256 1040 24.43 4755 21.8 Race. — Race seems to exert no influence over the death rate from diphtheria. At least this is true in regard to the white and colored patients. Some observers believe that the blacks are more liable to perish from the disease than the whites, but this is not in accordance with our experience, as the following table shows: White. Black. Year. Admitted. Died. Per cent. Admitted. Died. Per cent 1893 208 60 28.84 9 2 22.22 1894 434 144 33.18 31 10 32.26 1895 660 178 26.9 46 12 26.00 1896 838 183 21.83 31 7 22.58 1897 1217 281 23.08 78 19 24.35 1898 1177 289 24.55 52 8 15.35 1899 1304 262 20.09 69 13 18.84 1900 1309 286 21.84 58 12 20.68 1901 843 163 19.33 46 11 23.91 1902 567 129 22.75 34 8 23.52 8557 1975 23,08 102 While it is impossible to predict at the onset of diphtheria the ending of any case, yet it may be said that when the inflammation of the fauces is mild and the pseudomembrane not extensive, with but moderate swelling of the lymphatic glands of the neck, the termination is usually favorable. When the exudation is limited to the tonsils the danger is not great; the vast majority of such cases recover without any untoward after-effects. On the other hand, if the inflamed surface be extensive, the pseudomembrane copious, the exhalations ofl^ensive, and the neigh- boring lymphatic glands and the adjacent tissue very much swollen, the patient's condition becomes perilous. It may be safely asserted that the danger is increasingly grave in proportion to the extent of surface involved and the copiousness of the exudation. The parts implicated in the diphtheritic process must also be taken into account in forming a prognosis. In Lennox Browne's analysis of 1000 cases of the disease, the mortality, according to the site of the exudate, was found to be as follows: DuathH. Per cent. 81 12,1<5 1 25.00 1 50.00 51 45.53 106 64.24 30 61.22 2 33.83 11 01.06 TTJE PROGNOSIS OF 1)1 1'llTII I'llil A 083 Site of iiioinhraiic. (/'aBCH. FauceH (alone) 666 Larynx " 4 Naros " 2 Fauces and larynx 112 " " narea 165 " larynx, and naros 49 Membrane involviiiB the buccal cavity and IIijh 6 Membrane involvhifi; the hard palate . . 12 If the fauces alone are involved the patient has a fair chance of surviving the attack. Ikit v\'here the exudate forms in a thick mass on the hard and soft palates the danger becomes imminent. Some- times, however, the membrane peels off quickly, leaving the parts quite free from ulceration, and recovery speedily follows, although paralysis, more or less marked, of the palatine muscles, is rarely absent. The chief source of danger in such cases is from the absorption of the tcjxins, giving rise to toxajmia and heart-failure. When the nares are involved the prognosis should always be guarded. Very many if not the majority of the milder cases of nasal diphtheria recover, and also some of the severe ones. But it is not often that the disease is limited to the nares. If the nasal cavities show distinct plugs of exudate in conjunction with marked faucial involvement, as is usually the case, the child's condition should be viewed with grave apprehension. The foregoing table shows that the mortality from faucial and nasal diphtheria was as high as 64.24 per cent. In the severe cases of diphtheria nasal involvement is commonly present. As the capillary bloodvessels are very superficial in the cavities of the nose, the slightest congestion or ulceration of the mucous mem- brane of this part is liable to give rise to troublesome hemorrhage. This of itself is .sometimes a source of danger. But the greatest danger is from systemic poisoning, which is extremely liable to occur, since the lymphatics, which are very numerous in the submucous connective tissue of the nostrils, take up the toxins and convey them to every part of the system. This condition always involves great danger of death by asthenia, due to toxpemia and heart -failure. If recovery takes place, more or less paralysis, local or general, is quite sure to develop during convalescence. The occurrence of middle-ear disease as the result of diphtheria is deemed of sufficient importance to warrant prognostic consideration. It is believed that the diphtheritic process not infrequently extends from the postnasal space through the Eustachian tube to the middle ear. The aural involvement may impair the hearing, but only in rare instances does it result in deafness. likewise, in severe nasal diph- theria the infection may be conveyed through the cribriform plate to the brain, causing meningitis. In analyzing liis 1000 cases of diphtheria, Lennox Browne says: "It may also here be mentioned that, in one case of nasal diphtheria, death ensued from meningitis, and no aural coni- plication was to be found. This circumstance offers a not improbable explanation of the gravity of nasal diphtheria. For, not only do the 684 DIPHTHEHIA turbinals constitute an extensive and readily absorbent surface, but there is a liability to direct cerebral infection through the cribriform plate, as has been observed in regard to cerebrospinal meningitis in which the specific organisms have been found in the anterior meninges." On the first , or second day of diphtheria there is but little to be learned from the subjective syiaptoms that is of prognostic value. A little later, in the graver forms of the disease, one may often see in the facial expression of the patient something indicating the serious nature of the malady that presents itself for treatment. This appearance has been characterized as a "peculiar facial cachexia." The face is pale and sallow, often puffy, bloated, or slightly oedematous; the skin is smooth and shiny, a mucopurulent discharge issues from the nostrils, the facial outline is somewhat changed by the swelling of the neck, the eyes are clear and bright, but the expression is often that of indolence and apathy. When the attack is likely to prove fatal the face becomes livid or of a dusky, pallid hue ; in case of nasal involvement blood may either ooze or flow freely from the nares, and, in malignant cases, petechiae or ecchymoses may appear, not only on the face, but also on other parts of the cutaneous surface. Altogether the facial expression is that of profound blood poisoning, and death may be expected at any moment. Only in the mildest forms of toxaemia is recovery possible. When the patient suddenly becomes extremely pale, vomits everything that is swallowed, and the first sound of the heart is found to be diminished in intensity or absent, and the pulse becomes feeble, slow, and irregular, or disappears entirely at the wrist, the fatal end is not far off. Often the little patient will utter a shriek, as if suffering from pain, and place his hand over the precordial region just as he is about to expire. In these cases death results from asthenia or heart-failure, due to profound systemic intoxication. W^hen diphtheria terminates in this manner, it is usually in the second week of the illness. Temperature. — The prognostic significance of the temperature has been, v/e think, overrated by most writers. With Lennox Browne we feel that "One is so accustomed to read and hear of the fever of diph- theria that we almost hesitate to declare our conviction — formed on personal observation and confirmed by others whose experience is much greater — that as regards fever there is little to speak of as com- pared with the acuteness of the constitutional disturbance characteristic of the disease." If the temperature continues high after the first few days of the illness it is most probably due to the development of some complication. In the worst cases of diphtheria the temperature soon falls to near the normal point, and, as the disease progresses, often becomes subnormal. With the other symptoms of toxaemia present, the occurrence of algidity should be regarded as a fatal omen, as it indicates the approach of death by asthenia. In septic cases the temperature may continue high, or it may fluctuate as in most other septic conditions, l^'his can readily be explained by the inflammation of the lymphatic glands of the neck Tiii<: ru.()(;N()Sis or i>ii'irriii:in.\ 085 which always accompanies this form of tlic fliscasc. 'J'hc })rognosis in this variety of (h'phtlieria should \m'. exceedingly quarried. Pulse.-- By carefully studying the pulse from time t(; time one may sometimes acfjuire information of considerabht prognostic value. So long as the j)ulse is not too rapid, remains regular and of normal volume, the case is j)rol)al)ly progressing favorahly. I^ut when it hecfjines very rapid and fe(>l)le, or slow and irregular, our gravest apprehensions should be aroused. The ])ulse rate as well as its volume is influeneed nif)re l)y the absorbed toxins than by the pyrexia. A ra])id j)ulse within certain limits is not necessarily unfavorable so long as it remains regular. But if it constantly grows more and more rapid, and becomes irregular in its rhythm and force, the prognosis is proportionately bad. If, with a frequent and compressible, or a slow and intermittent pulse, there is also subnormal temperature, a pale, puffy, apathetic, and cachectic face, the prognosis becomes most grave. In speaking of the prognostic value of the pulse in diphtheria, Sir William Jenner says: "An extremely rapid and feeble pulse is of grave import; a very infrequent pulse is of fatal significance." This disturbance of the circulatory system means that the heart's function is affected by the action of the toxin on the carrliac nerves, and possibly also that the myocardium is undergoing some change through the influence of the poison. When the heart's action becomes slow and weak there is danger of clots forming in the ventricles or in the large bloodvessels connecting with the heart. One of the special dangers to be feared in diphtheria is iuAolvement of the larynx, giving rise to membranous croup. The disease may occur primarily in the larynx, but more often it begins in the fauces and extends into the larynx. The patient cannot be considered free from danger of the pseudomembrane extending into this part so long as the disease continues, but the liability of such an occurrence pro- gressively diminishes after the first week. The danger in membranous croup is twofold: first, from laryngeal obstruction, causing suffocation and death; and, secondly, from bron- chitis or bronchopneumonia. Much may be done toward overcoming the first source of danger by operative measures, but even then the diphtheritic inflammation too often extends downward into the trachea, bronchi, and bronchioles, and not infrequently into the alveoli of the lungs, giving rise to bronchopneumonia. We believe that about one- half of the deaths we have seen in membranous croup resulted from the latter complication. The prognosis may be favorably influenced to a considerable extent by promptitude in employing such measures as intubation or trache- otomy for relief of the laryngeal stenosis. If, after either of these pro- cedures, the child continues to breathe easily and noiselessly, sleeps quietly, takes nourishment well, runs a temperature of not more than one or two degrees above normal, and has a good color, the chances of recovery are favorable. On the other hand, if the respirations are uneasy and noisy, the temperature continues high, a troublesome cough 686 DIPHTHERIA with rales throughout the lungs appear, and the color of the patient shows that the blood is not properly decarbonized, the chances of recovery are slim. Membranous croup is much less liable to be attended by toxaemia or followed by general paralysis than are most other forms of diphtheria. But these affections may occur in cases of membranous croup as the result of involvement of the fauces or nares synchronously with the larynx. Renal Complication.^ — Renal complication is not often of much prognostic importance. The slight amount of albumin that is fre- quently present in the urine is of no great significance, provided that granular and hyaline casts are absent. But when these, together with a large amount of albumin, are found, and the amount of urine excreted is greatly diminished, the outlook is not encouraging. If suppression of the urine occurs, death from convulsions and coma, as the result of ursemic poisoning, would soon follow if relief were not promptly afforded. In our experience such a termination in diphtheria is rare. The prognosis of diphtheria should be greatly qualified when it occurs coincidently with or as a sequel to some other infectious disease, like scarlet fever or measles. In patients suffering from the latter disease diphtheria seems especially liable to assume the form of membranous croup, probably because of the catarrhal affection of the larynx usually present in measles. In the year 1900, measles of a malignant type broke out in the diphtheria wards of the Municipal Hospital, Phil- adelphia, and the mortality assumed unduly grave proportions. Of 68 cases of diphtheria complicated with measles, 34 died, a death rate of 50 per cent. Indeed, any independent affection, however mild ordinarily, supervening on an attack of diphtheria may become inordi- nately severe in consequence of the changed condition of the blood and nervous system of the patient. Diphtheritic Paralysis.— The danger from diphtheritic paralysis depends very much on the parts involved. So long as the vital organs of the body remain unaffected the prognosis is not unfavorable. Par- alysis of the soft palate, however inconvenient it may be to the patient, is not fatal. Likewise, in the average case of multiple paralysis recovery may be expected. Even in the more extreme cases, if the heart's function and the respirations are not affected, the chances of recovery are fair, provided the patient receives proper attention during the critical period. When deglutition is impossible, life may be preserved by feeding the child through an oesophageal tube. Cardiac paralysis, which is most to be feared, often develops suddenly and gives rise to dangerous symptoms of heart-failure. It is liable to occur either early or late in the disease. We have already mentioned the fact that multiple paralysis does not make its appearance until the fourth to the sixth week of the illness. This complication, as well as some others to which attention has been called, tends to keep the patient's life in danger for a long time. Even when a well-marked case of diphtheria is progressing favorably, it is not too much to say that the danger period is not passed until at least six weeks have elapsed since the beginning of the attack. CIT APTER XI 1 r. DIPHTHERIA (Continued). THE TREATMENT OF DIPHTHERIA. Since antitoxin has achieved for itself so much credit as an immun- izing agent against diphtheria, it would seem that it deserves first place among the prophylactic measures to be considered. So important, indeed, is the question of serum treatment, not only with reference to its power of preventing but also of curing the disease, that we have concluded to devote a special chapter to the subject. We find it most convenient, however, to consider the question of treatment of diphtheria in the following order: first, the hygienic or preventive treatment; second, the medicinal treatment; third, the specific or serum treatment. Preventive Treatment. — As soon as the nature of the disease is known the patient should be separated as far as possible from the other members of the household. This is important even when the attack is ever so mild, as severe cases may result from mild ones. If the patient is to be treated at home the other children, if there be any, should receive an immunizing dose of antitoxin and should be immediately sent out of the house. If this is not feasible, they should be excluded from the sick-chamber and assigned to bed-rooms in the most distant part of the dwelling. Their hygienic conditon should be looked after; at least they should be properly fed, regularly bathed, and provided with plenty of fresh air day and night. Their throats and nostrils should be examined every day, and as soon as anything abnormal is discovered the child should be immediately separated from the others and given suitable treatment. One of the uppermost rooms in the house should be selected for the patient. It should be light and properly heated, and pronded with facilities for obtaining ventilation without incurring the risk from draughts. An open fire-place, with at least a little fire burning, is a very desirable aid toward maintaining the purity of the air in the room. The most suitable temperature is 70° to 72° F. All unnecessary hang- ings, furniture, and the like, that are liable to retain the contagium, should be removed from the chamber. In the winter months, when the heated air of the room is usually dry, it may be moistened by steam, which, if deemed advisable, may be slightly impregnated with eucalx-ptol, or some other fragrant essential oil. This is more especially advisable when the patient manifests croupy s}^Ilptoms. If more than one member of the family be ill with the disease, care should be taken not to overcrowd the patients. Each patient should 688 DIPHTHERIA be allowed at least 2000 cubic feet of air space, with an additional allowance for the nurse. The nurse should be instructed to keep the patients as quiet as possible; at least, so far as active bodily movements are concerned. When the heart is found to be weak, she should feed the patient by means of a feeding cup, and not allow him to rise or get out of bed under any circumstance whatever. During the illness of the patient the privileges of the well members of the household should be restricted. They should be advised not to attend church nor public assemblages of any kind. The children, if there be any, should at once be required to leave school, and should not be readmitted until the family physician or some qualified sanitary officer certifies that the sickness has ended, and that the house has been thoroughly cleansed and disinfected. The isolation of the patient should continue until the diphtheritic exudate has disappeared, and the affected mucous membrane has become entirely normal. When possible, cultures should be made to determine the absence of the specific bacilli; if two successively negative cultures be obtained it may be considered safe to allow the patient to associate with the other members of the family, provided he has had an antiseptic bath and is dressed in clean clothing. As the infecting principle of the disease clings to articles which have been used by the patient, or which have been in the same apartment, all such articles as are worthless should at once be burned. Only such books, toys, and the like, as may be burned at the termination of the illness should be allowed in the sick-chamber. All articles for the laundry should be steeped for some time in a disinfecting solution, such as two fluidounces of chloride of zinc, or four fluidounces of strong carbolic acid, to a gallon of water, and afterward boiled for half an hour. For the disinfection of woollen goods formalin may be used, but for efficiency there is nothing that ecjuals superheated steam. All utensils used by the patient in eating or drinldng should be purified each time by means of boiling water. The secretions from the patient's mouth and nose should be disinfected by receiving them into a strong solution of chloride of lime, or a mercuric chloride solution (1 : 1000), or some other equally powerful gerrn-destroying agent. Small pieces of worn cotton goods, or cheesecloth, may be used to receive such secretions, and should be destroyed at once by fire. T'he nurse or any other attendant should wear clothing made of such material as can be readily boiled and laundered. Before associating with well persons she should take an antiseptic bath, washing her hair at the same time, and change her entire clothing. The physician also, should exercise care lest he himself may be the means of conveying the infection to others. He should not remain in the sick-chamber longer than is necessary to make a proper examination of the patient. Before leaving the house he should take the precaution to wash his face, hair, and hands; the latter should be held for a few moments in some anti- septic solution, as inercuric chloride, 1 : 1000. He should delay visiting another patient until he has spent some time in the open air, or, what 77//'; tr,i<:atmI':nt of dii'ii'iiiI'IHIA 680 is better, chaiif^ed his clothing. It is (icsirahle for liini to w^-ar in the room a long rubber coat or Wuv.n gown, which shoiiM b<- kept hanging in i\\v o[)('n air (hiring th(; interval of In's visits. As the body of a patient who has died of diphtheria is slill eajKiljle of transmitting the contagium, certain j)reeaiitions in regard to it are necessary. An effort should be made to disinf(;ct th(! body by thf)roughly washing it with some powerful disinfecting solution. Ther(! is jx-rhaps nothing more relial)le than chloride of lime. Six ounces of tin's d their action on animals, and afterward on man. For the latter purjxjse Ix; emj^loyed a mixture containing irc^n, toluol, and creolin or rnetacresol. Finding, however, that this solution produced a marked smarting sensation in the throats of children, he added to it menthol. "A cotton tampon steeped in this solution is apy^lied to the affected parts twice in succession for ten seconds, and this treatment is r(!peated every three hours, until all the local symptoms have disappeared, which ordinarily occurs within four or five days. While the affection is still local, it may be arrested in its course by this solution; bacteriological examination will show that all the bacilli in the membranes are killed. Loeffler reports that in 96 cases treated in this manner, three-fourths of which were shown by bacteriological examination to be true diph- theria, not a single death occurred." Ijoeffler recommends two solutions, the formulae of which are as follows : Loeffler's Solution (1). '!^ — Menthol 10 grams. Solve in toluol ad 36 c.c. Alcohol, abs 60 c.c. Liq. ferri sesquichlorid 4 c.c— Nf . Loeffler's Solution (2). Jk— Menthol 10 grams. Solve in toluol ad 36 c.c. Alcohol, abs 02 c.c. Creolin 2 c.c— M. Either of these solutions may be applied with a cotton swab to the diphtheritic patches every three or four hours in the manner mentioned above. It may be well to clear the throat of mucus by mopping it with cotton before making the application. It is advised that the applications be made a little more frequently in bad cases. We have not used these solutions extensively, but have given them a fair trial without obtaining results anything like as favorable as those seen by Loeffler. Jacobi says: "Wlien the diphtheritic pseudomembrane is within reach, it should be either destroyed or disinfected. For that purpose one or two drops of a 50 per cent, solution of carbolic acid in glycerin may be applied once (not more than twice) a day, or of the tincture of iodine, or of a solution of 1 part of the bichloride of mercury in 100 or 500 parts of water, several times a day." But he calls attention to the fact that only a small part of the pharjnax is accessible to such treatment, and that it is possible to apply it to only a small class of patients. He condemns in forcible language the indiscriminate use of strong appli- 694 DIPHTHERIA cations to the throats of children. He says: "Smaller children will object, will defend themselves, will struggle. It takes many an anxious moment to force open the mouth; meanwhile, the patient is struggling, perspiring, screaming, and exhausting his strength. One may succeed in forcing open the jaws, then there begins the practice of making applications, of swabbing, of scratching off the pseudomembrane, of cauterizing, of burning. The struggling child will prevent the limitation of the application to the diseased surface. One cannot help injuring the neighboring epithelium, and thus the morbid process will spread. Instead of doing good, we have done harm; for, indeed, no local appli- cation can do so much good as the struggles of the frightened children do mischief. I have seen them die while defending themselves against the attempted violence, leaving doctor and nurse victorious and alive on the battle-field." Jacobi believes that a very good local effect may be produced by the swallowing of medicines which are at the same time disinfectants, digestible, and easy to take; that they should be given in small doses and frequently repeated. Of this class of medicines he mentions tincture of the chloride of iron, lime-water, solutions of boric acid, bichloride of mercury, or benzoate of sodium. Solvents. — For the destruction and removal of the pseudomem- brane, certain agents known as solvents have been employed from time to time. Among the unirritating solvents may be mentioned alkalies, pepsin, trypsin, and papayotin. The agent that has been most largely used is, perhaps, lime-water, or steam from slaking lime. Its solvent action, if it has any, is due to its alkalinity, which, as J. Lewis Smith says, may be increased by adding sodium bicarbonate to it. From observing its effects in a considerable number of cases, this author recommends with confidence the following formula: P — 01. eucalypti 5 ij. Sodii benzoat. S j. Sodii bicarbonat . 3 ij. Glycerinse ' . . S ij. Aqusecalcis Oj.— M. Sig. — To be used witb tbe hand atomizer from three to five minutes every half-hour, or with the steam atomizer almost constantly. The writer says: "This alkaline spray not only exerts a solvent action on the pseudomembrane, but also renders the mucopus thinner, less viscid, and, therefore, so changes its character by diminishing its viscidity that it is more easily expectorated." As trypsin is an active solvent in an alkaline medium, J. I^ewis Smith suggests that it may be added with advantage to the alkaline mixture just described. Indeed, this writer is inclined to believe that such a combination forms the best solvent mixture known. The pseudo- membrane has been seen to dissolve and disappear quickly under the use of the following formula: ]^— Trypsin gr. xxx. Sodii bicarb gr. x. Aquse destillat g j. — M. Sig,— To be applied frequently with the hand atomizer or a cotton swab. Tlll<: TIINATMI'INT Oh' 1)1 1'llTII hllU A P,05 Pepsin has hccu used as a .solvent, with varyini^ n-sults. It was recommended in di[)hth(M-ia solely on tlieoretif;al ^roniifls, and has proved to 1)0 of douhtful utility. Some writers sp(!ak favorably of pajmyotin. in s(;lution as a solvent of pseudomem})rane. Among these may he mentioned Ko.ssbach, J. K. l^auduy (Jr.), and Jaeohi. 'l^'he drug is said to he readily soluhle in 20 parts of water, and it is claimed hy Kosshach that if a few minims be placed on the tongue every five minutes tlu; membrane will dissolve in two or three hours. Jacobi has u.sed it with fair results, applying the solution with a swab or the atomizer. He says he employed the drug many years ago in greater concentration to dissolve, after trache- otomy, the diphtheritic meml)rane in the trachea below the tracheal tube. As already intimated, Lennox Browne gives lactic acid first place among the local applications. He believes its efficiency is due in a measure to the fact that an acid medium is inimical to the V)acillus, Vjut that its greatest merit is its power to disintegrate or digest false mem- brane. He makes this strong statement: "Truth to say, we have been so well satisfied with lactic acid that we have been loath to try any other local remedy. We have not found it injurious to contiguous healthy tissue — that is to say, wherever the epithelial layer is entire. Its action appears to be limited almost solely to unhealthy tissue, promoting its disintegration by a process analogous to that of digestion; there is, it is true, some circumferential inflammation, but as this is only of the degree of healthy reaction and leads to the outpouring of scavenging leukocytes, it is to be regarded as a desirable result." This author advises that the lactic acid be applied pure, or rather of (British) pharmacopoeial strength, by the physician at least once or twice a day, and that the drug, moderately diluted, be applied by the nurse every three or four hours until the membrane has disappeared. The following formula is recommended: ]^— Lactic acid (P. B.) 1 part. Distilled water 3 parts. — M. Sig.— To be applied by the nurse or attendant every three or four hours with a cotton swab or the hand atomizer. Our experience with the so-called solvents in diphtheria has led us to believe that they are not to be depended upon. They may act very well in the test-tube, but their digestive and solvent action is too feeble to be of much practical value during the short time that it is possible for them to remain in contact with the pseudomembrane in the throat. ^Vhile the antiseptic mouth washes, gargles, and sprays are useful to a limited extent, yet their action is too feeble and intermittent to be of any great practical value. We have already expressed our disapproba- tion of caustic applications, and we agree with those who believe that nothing is to be expected from mere astringents, ^^^len we consider that the purpose or design of local treatment is the prevention of extension of the pseudomembrane, promotion of its separation, destruc- tion of the bacilli, and the prevention of toxic absorption, we must 696 DIPHTHERIA admit that of the various remedies recommended, some of which even vaunted as specifics, no one has stood the test of experience. We would not be understood as discouraging local applications in diphtheria; on the contrary, we believe that when used with good judgment they may be of great service. We have but little confidence, however, in their power to accomplish to any marked degree the purposes mentioned above, although as cleansing agents they are very useful. Any unirritating antiseptic solution may be employed, but, after all, quite as much may be accomplished with a warm normal salt solution. It should be the aim of the physician to keep the parts involved as clean as possible without taxing too much the strength of the patient. This may be best accomplished by irrigation, either with a syringe similar to the one devised by Lennox Browne, or with the ordinary fountain syringe. Swabs should not be used, except by the physician or trained nurse, and then only with great care. At the very beginning of diphtheria, or even when the disease is simply suspected, the throat should be sprayed every hour, at least for a few hours in succession, with a mild and unirritating antiseptic solution, such as a 1 per cent, boric acid solution, diluted Dobell's solution, hydrogen peroxide with equal parts of water, or a solution of 1 : 4000 or 6000 of bichloride of mercury. Twenty-four hours will probably determine whether it is possible to prevent or limit the develop- ment of the exudation. If not successful, and the disease goes on to its fullest development, the same applications may be continued every hour or two for the purpose of cleansing the throat. As already mentioned, a warm normal salt solution will accomplish the same end. We now employ it almost exclusively. Park, consulting physician to the Willard Parker Hospital, New York, prefers, in older children and adults, irri- gation with a warm solution of salt every hour or two, and also every three to six hours to irrigate with some antiseptic solution, especially 1 : 1000 of bichloride of mercury. The irrigation of the throat, he believes, is best carried out with the fountain syringe. In the Mu- nicipal Hospital of Philadelphia we were in the habit of spraying the throat every two hours with peroxide of hydrogen. So long as the fauces are covered with exudate this drug may be used without dilu- tion, but when the exudate has thinned out very considerably, leaving the mucous membrane excoriated and irritable, the peroxide should be diluted with one or two or more parts of water. When the exudate has almost entirely disappeared, and the throat remains irritable, the following application is often useful: Jfc — Menthol gr. x. Oil of sweet almonds fS j.— M. Sig. — Apply in form of spray. An operative procedure consisting of removing the tonsils at an early stage of diphtheria has been recommended. Lennox Browne and his colleague, Mr. Percy Yakins, and also a few other writers, claim to have seen good results follow the operation. riii<: TUi<:ATMh:NT of Dii'irriihiiaA 697 The ol)jec'ti()ns to this treatment are that the exufhite is liable to reform on the cut surface and the adjacent parts; that the injury inflicted affords a fertile soil for the propagation of the bacilli, and that the exposed lymphatics will [XTmit of ready absorption f>f the tfjxins. 'J'he procedure has not met with much favor, and w(; would strtjiigly advise afjjainst it. Nasal Diphtheria. -As diphtheria of the nose and nasopharynx is most dangerous, immediate and persistent local treatmctnt should be adopted with the object of preventing, as far as possible, absor})tion of the noxious products. The treatment consists in frc^fiuent cleansing and disinfecting the nasal cavities. The remedies usually employed do not differ materially from those recommended in faucial diphtheria. The decomposing material and foul discharge should be washed away as fast as they form. In order to do this, it is necessary to irrigate the nose very frequently — often every hour, or every two hours, day and night. In severe cases with a profuse fetid discharge the nares should be kept clean, no matter how much the child resists. The little patient may be restrained without suffering any harm by rolling him up in a sheet. If much exhausted, the child should not be raised from the recumbent position during the cleansing process. Only bland solutions should be employed, such as boric acid (5 to 10 grains to the ounce of w^ater), chloride of sodium (teaspoonful to a pint of w'ater), or some other equally mild antiseptic solution. The nose wash should always be used lukewarm, and the more thorough the washing the better it is for the patient. Instillations wdth a small medicine dropper, so often used by physicians, are not sufficient. Nor will the atomizer convey a sufficient amount of liquid into the nasal cavities to accomplish the purpose aimed at. A small (not too small) blunt-pointed syringe will answer the purpose much better. If carefully used, there is perhaps no better irrigator than the fountain syringe. It should be held just high enough for the solution to flow without undue pressure, and thus obviate any possibility of injury to the middle ear. If the nose inclines to bleed, the irrigation should be very slow and gentle. But if the epis- taxis be free and quite uncontrollable, as sometimes happens, the irrigation will have to be dispensed with. It may then become necessary to direct attention to the hemorrhage. Alum, tannic acid, Monsel's solution, and the like, may be used. We have frequently found it necessary to plug the nares. I/Cnnox Browne says the hemorrhage may generally be arrested by syringing the nostrils with the following anti- septic solution at a temperature not less than 100° F. : 9i — Chlorate of potassium >2 oz. Bicarbonate of sodium 5^ oz. Borax J^ oz. White sugar (in powder) 1 oz. — M. Sig.— A teaspoonful dissolved in five or ten ounces of water at 100° F. and use with nasal syringe. For the local treatment of nasal diphtheria many physicians prefer some of the more active antiseptic and disinfecting solutions, such as peroxide of hydrogen, permanganate of potassium, carbolic acid. 698 DIPHTHERIA bichloride of mercury, and so forth. Peroxide of hydrogen is quite useful if it be properly diluted. It is very irritating to the mucous membrane of the nose, and will cause pain if not diluted with 8 or 10 parts of water. Carbolic acid has been used in solution varying from 1:1000 to 10:1000 parts of water. Care should be taken lest too much of this drug be swallowed. Permanganate of potassium has been highly recommended. It has been applied to the fetid nares with a cotton swab, in the strength of 1 : 250 of water, once or twice a day. For irrigation it may be used several times a day in a solution of 1 : 2000 to 1:4000. For washing out the nares, as well as the fauces, bichloride of mercury in solution has many advocates. Its well-known power as a germ destroyer has led to its use. It would doubtless be more freely employed were it not for the danger incurred through its poisonous qualities. As young children always swallow some of the liquid that is injected into the nares, most physicians hesitate to use a solution which is so highly poisonous. The same objection holds good against its employ- ment for irrigating the fauces. Among those who recommend this drug for washing out the nares may be mentioned Jacobi. He advises that 1 part of bichloride of mercury })e mixed with 10 parts of chloride of sodium or chloride of ammonium, and that from 2000 to 10,000 parts of water be added to form a solution, which should be used freely. He says if moderate quantities of this weak solution of mercuric bichloride be swallowed while being injected no harm is done. For correcting the fetid odor from the nares, he recommends, besides some of the solutions already mentioned, creolin in a 1 per cent, solution. After some experience with most of the nasal washes mentioned above, we have, for the last few years, settled down to the use of the warm normal salt solution almost exclusively. We find that it answers the purpose quite as well as any of the antiseptic washes, and that it has the advantage over some others of being perfectly safe and unirritating. We may add that we have used with benefit peroxide of hydrogen well diluted with lime-water. Aural Diphtheria. — But little treatment can be applied to the com- paratively rare form of acute median otitis of diphtheritic character other than what is suitable for that affection when it occurs ordinarily. As pain is not often complained of, the condition is usually not realized until a purulent discharge issues from the external m^eatus. Nearly all that can be done then is to syringe the ear with a warm solution of boric acid or some other mild antiseptic wash. At the same time the nose may be irrigated with a similar solution. It is advisable that Pollitzer infiation be also employed with the hope of clearing the Eus- tachian tubes. The insufflation of dry powders into the ear is not considered advis- able, as they are likely to form dry crusts which may prevent the escape of the purulent material. Extension of the suppurative action to the mastoid cells rarely occurs; but when it does occur surgical treatment applicable to that condition should be resorted to. TTTK TRI<:ATMKNT OF I)! I'llTII KIU A 699 Ocular Diphtheria. — For diplilliciific involvcnicnt nf the; conjunctiva, fortunately rare, the (^ye should he irri^'ated frefjuently- say every hour — with a boric acid solution (ten grains to the ounce of water), or some other equally mild antiseptic sohition. 'J'his will be found difficult when the eyelids are very much swollen; but an effort must l)e made to keep the pus from accuniulatincr under the lids. Ice applications, Fl«. 98 Position of child during irrigation of tliroat and nose. (After Park.l in the form of iced cloths, are always indicated at first; but later it may be better to use %varm applications. A strong solution of nitrate of silver may be applied to the pseudomembrane on the palpebral con- junctiva if care be taken to neutrahze the silver salt immediately with a solution of chloride of sodium^ According to Lennox Browne,^^Hermann, of Breslau, has employed very efficaciously hourly pencillings of the affected eyelids with a 5 per 700 DIPHTHERIA cent, solution of benzoate of sodium, and declares that since he began to use this treatment no patient under his care with this form of diph- theria has lost an eye. Paralysis of the muscles of the eye occurring as a sequel to diphtheria calls for no special treatment. It will almost always disappear entirely in the course of two or three months. Constitutional Treatment. — As diphtheria begins as a local disease very little internal treatment is required at the onset. Constitutional disturbance, however, occurs early, partly as a result of the local disease, but more especially from absorption of the toxic products of the diph- theria bacilli and the associated organisms. The prostrating effects of this poison are well known. The indications for internal remedies may be stated as follows : To aid the system in the elimination of the poison ; to reinforce the debilitated vasomotor system; to improve the quality of the blood; to combat the poisonous effects of the toxins; to sustain the vital powers; and, lastly, to conduct to a favorable termination the secondary affections that may arise. At the outset of the disease it is well to administer a gentle purge. For this purpose there is perhaps nothing preferable to calomel. Liquor ammonii acetatis (U. S. P.) is useful, as it tends to increase the secretions of the skin and kidneys. Water may be allowed ad libitum. Small pieces of ice held in the mouth will often have a soothing effect on the inflamed and painful fauces. Should the temperature of the patient be high, no attempt should be made to reduce it by the internal admin- istration of antipyretic drugs, especially the coal-tar products, as they ai'e too depressing. It is better to trust to tepid bathing. Bathing has the additional advantage of keeping the function of the skin active. At this early stage there is no article of diet equal to milk. There is, however, no objection to beef-tea and broth. As soon as the diphtherial character of the disease is recognized iron should be administered. For the past fifty years this drug has had the confidence of physicians in this country, as well as those in most of the European countries, and by many it is regarded as our sheet-anchor in the constitutional treatment of diphtheria. The preparation of iron that has achieved the greatest reputation in this disease is the tinctura ferri chloridi. It is believed to have both a local and general effect. It should be administered frequently and in positive doses. A child of one year may take as much as a fluidrachm in twenty-four hours, and a child of three to five years from two to three fluidrachms in the same period of time. It should be admin- istered every hour or two. Some WTiters advise that it be given every fifteen, twenty, or thirty minutes. It should always be given diluted with a little water, so that the dose is about a teaspoonful. The addition of glycerin makes the drug more palatable. One part of glycerin to three parts of water makes a very good vehicle. If there is too much dilution no local effect can be expected from the drug. As a rule, it is well borne by the stomach; but there are exceptional cases in which it is not tolerated at all. 77//'; Tfi/'JATM/'JN'/' Oh' 1)1 1'llTII HlilA 701 Jacohi, aftor iisin^ tlii.s pre[)aratif)ii of iron for many years, cxprrssps great confidence in it. He feels sure he has seen many bacJ cases recover through its use. But he has met with some cases in which its action was not so satisfactory. lie says: "Still, I have often been so .situatr-f] that 1 had to give it up in pecidiar cases. 'I'hey were those in which the main symj)toms were of so intense a sepsis that tlu; iron and other rational methods of treatment were not powerful enough to prevent the rapid progress of the disease. Children with nasopharyngeal diph- theria, large glandular swelling, feeble heart, and fref]uent pulse, thorough sepsis, and irritable stomach })esides, those in whom large doses of stimulants, general and cardiac, may pcjssibly bring any relief, are better oft" without the iron. When the circumstances are such as to leave the choice between iron and alcohol, it is best to omit the iron and rely on alcoholic stimulants mostly. The quantities required are so large that the absorbent powers of the digestive tract are no longer sufficient for both." J. Lewis Smith regards the ferruginous preparations as holding an important place in the treatment of diphtheria, and says the one which has stood the test of experience is the tincture of the chloride of iron. He believes it should be given in large and frequent doses, as five drops hourly to a child of three years. He thinks it probable that those Avho have not observed its good effects have treated unusually bad cases or have given the medicine in small and inadequate doses. The best vehicle, he says, is glycerin and water. Some writers maintain that an effort should be made to saturate the system as soon as possible with this drug, and, with this object in \iew, recommend that it be given in as large and frequently repeated doses as the stomach will tolerate. Ferguson, according to the author last mentioned, believes that this preparation of iron when freely admin- istered partially arrests the blood change in diphtheria, and he recom- mends for a child of ten years the following mixture : 1^ — Tinct. ferri chloridi S j. • Syr. simplicis . 3 iij — M. Sig.— One teaspoonful hourly in waler. If the stomach cannot tolerate this dose, it is advised that half a teaspoonful be given every half-hour. Prof. Joseph E. Winters,^ of New York, says that he has administered to a child of eight years as large and frequent doses of the tincture of the chloride of iron as two drachms, in combination with glycerin, every half-hour for forty-eight hours with marked benefit. And J. Lewis Smith cites an instance in which a woman, aged twenty-two years, greatly prostrated, having an excessive amount of exudate in the throat, and a very fetid breath, took daily one and a half fiuidounces of the iron for ten days. But, he remarks, "it is only in tlie most severe or malignant form of the disease, the form described by Sanne as septic phlegmonous, that such large doses are proper or are required." He 1 Diphtheria and its Management, 1SS5. 702 DIPHTHERIA believes, as do most physicians of the present day, that in the average case of diphtheria five drops given hourly is the proper dose for a child of three years. We have used in our hospital work for many years the ferric chloride in doses practically the same as those last mentioned; but we prefer to combine it with the bichloride of mercury, as in the following formula : ^ — Hydrargyri chloridi corrosivi g^- % Tinct. ferri chloridi 5j. Syrup, simplicis S j. Aquae q. s. ad fS iij.— M. Sig. — For a child of three years, one fluidrachm iu a little water every two hours. The internal use of bichloride of mercury in the treatment of diph- theria is not new. It was employed in this country as far back as 1860, by Dr. Tappan, of Ohio, with asserted benefit. It has, however, been used more frequently of late years, since it has been shown to be one of the most active germicides in medicine. The accepted theory of the microbic origin of diphtheria has led to the employment of this drug by many practitioners in the belief that when given internally it pene- trates all parts of the system, destroying all micro-organisms with which it comes in contact. But as diphtheria begins as a local disease and becomes a systemic affection later, not because the specific micro- organisms enter the circulation — for in only rare instances have they been found in the blood — but because of the absorption of their poisonous products, it, therefore, may be that the remedial power of corrosive sublimate is limited to its local eft'ect upon the organisms in the throat and pharynx. Whichever way its influence is exerted, locally or consti- tutionally, it has been found by many physicians to be very useful in diminishing the virulence of diphtheria and increasing the chances of recovery. Though this drug has been widely employed in diphtheria, and at times administered in what would appear to be dangerous doses, very few reports can be found of its toxic or injurious effect. Dr. Grant^ administered to a child of four years one-half grain of corrosive sublimate every half-hour until six doses were taken, and then hourly during the remainder of the day, every two hours on the second day, and on subse- quent days at longer intervals. Jacobi has also administered it freely, but not in such heroic doses as just mentioned. He states that an infant a year old may take half a grain every twenty-four hours — of course, in divided doses — for many days in succession, with very little, if any, intestinal disorder, and with no stomatitis. While large doses may be justifiable in extremely severe cases, we believe that smaller and safer doses are sufficient for general use. W^e agree with J. Lewis Smith, who says: "In ordinary cases the following may perhaps be regarded as about the proper quantities which should be administered in divided doses in twenty-four hours: For a child of two years, gr. | (gr. ^t every two hours) ; for a child of four years, gr. | 1 Quoted by J. Lewis Smith, Cyclopedia of the Diseases of Children, by Keating. 77//'; Till<:ATMI<:NT OF DII'IITIIF.UIA 703 (gr, -^^ every two lionrsj; for a cliild of six years, ^r. \ (\iv. .j',; every two hours); and for a child of ten years, ^r. h (^'r. ./, every two hoursj." Calomel. — Calomel as a remedy in diphtlieria has its advo(;ates. It has been recommended with the purpose of securing both its cathartic and alterative elfects. It may be useful as a gentle cathartic at the beginning of an attack, but to continue catharsis after the flisease is fully developed seems ol)jectionable on account of its tendency to weaken the patient and increase the ana?mia which so soon becomes manifest in all severe cases, whatever the treatment. Much more is claimed for it when administered in a fractional part of a grain at frequent intervals. Many physicians of ample experience recommend it very highly in doses of one-tenth to one-quarter of a grain, repeated every hour or two. Some advise that a fractional part of a grain in powder form be placed on the tongue every hour or two, or even more frequently, and allowed to disappear gradually. It is claimed that when given in this way it acts both locally and constitutionally. Its tendency to act on the bowels may be obviated by the administration of a little paregoric at proper intervals. Potassium Chlorate. — Potassium chlorate has been used in the treat- ment of diphtheria for almost as long a time as the tincture of the chloride of iron. It was formerly more often employed than at present, but it still has many admirers. Its great efficacy in stomatitis has encouraged the belief that it is also useful in diphtheritic pharyngitis. But, as the results have been disappointing, and the action of the drug tends to weaken the patient and injure the kidneys, especially when administered in doses believed to be sufficiently large to be of service, it has, to a great degree, fallen into disuse. Jules Simon says that while it acts wonderfully well in stomatitis he has obtained no benefit from it in diphtheria. Its tendency to cause albuminuria and nephritis when taken in large doses is well known. Where death has resulted from an overdose of this drug the kidneys have been found greatly damaged. Potassium chlorate in combination with the tincture of the chloride of iron was, a few years ago, almost universally regarded as the remedy far excellence in diphtheria. The following formula, vnXh. some variations in the proportion of the ingredients, w^as for a long time a favorite prescription with most physicians of this country, and is still used by many: P:— Potassii chlorat 5 j. Tinct. ferri ehloridi f5 ij. Acidi muriat. dilut gtt. x. Syr. simplicis fS j- Aquse q. s. ad fs iv.— M Sig.— One teaspoonful every hour or two hours iu a little water. A child of five years may take one-half of the above mixture in the course of twenty-four hours. Dr. Thomas ]\I. Drysdale, of Philadelphia, who has had considerable experience in the treatment of diphtheria, claims that chlorate of potash 704 DIPHTHERIA is so efficacious as to be almost a specific in this disease. He employs it in large doses. To an adult he gives fifteen grains, and to a child of tv/elve years seven and a half grains, every two hours. In such doses he does not fear any deleterious effect on the kidneys. In laryngeal diphtheria he recommends the following formula : Jfc — Potassii chlorat 5 ij. Syr. limonis . . fX j. Aquae fS iij.— M. Sig.— For a child under two years one teaspoonful, and for a child from two to ten years two tuaspoonfuls, every half-hour in urgent cases. After an extensive use of potassium chlorate in diphtheria, and failing to obtain the favorable results claimed for it, we have abandoned it entirely. We feel inclined to agree with that noted clinician of his day, J. Lewis Smith, who says: "From what is known of its action, it would probably be better to abandon its use in diphtheria, since it is a remedy of doubtful efficacy for throat affections. If it be employed, it should certainly be administered in small doses sufficiently diluted. If it be prescribed, it should not, I think, be in larger quantity than half a drachm in twenty-four hours for a child of five years." Turpentine. — Turpentine has its advocates in the treatment of this disease. It has been employed both locally and internally, with the result, as some writers believe, of arresting the formation and spread of the exudation, and preventing the secondary toxic effects. Cases have been reported in which severe croupy symptoms quickly dis- appeared under teaspoonful doses of pure turpentine, and the patient, in one instance, recovered without tracheotomy, which was before thought necessary. The dose more commonly employed has varied from ten minims to a teaspoonful, one to three times daily, in milk, sweetened water, or gruel. Good results have been reported from the use of this agent by men of large experience and good judgment, among whom may be mentioned Baruch and Jacobi. Dr. Llewellyn, of Washington, D. C, speaks favor- ably of the action of turpentine when vaporized and inhaled. Its sup- posed efficacy is attributed to the fact that it is antiseptic and germi- cidal in its action. J. Lewis Smith says he has employed the vapor of turpentine with apparently good results. The mixture he recommends for vaporization is as follows : P;— Acidi carbolici, Ol. eucalypti ad S j. Spts. terebinth S viij. — M. Two tablespoonfuls of this mixture are added to one quart of water, which is placed in a shallow vessel with a broad surface, and maintained in a constant ebullition or simmering upon a gas or other stove. He thinks that the vapor thus generated, "in passing over the inflamed surfaces, which are the seat of the exudate, with every inspiration, probably produces more or less local disinfection, apart from the systemic disinfection which it may cause by entering the blood and 77//'; TUJ'JATMl'JNT Ol'' l>l I'llTII KKI A 705 the tissues generally." We feel that, such ;i result is scarcely to be expected from turj)entine. As to its alleged cHicacy in dij)hth(Tia, how- ever, we are unable to speak from any personal experience. Sodium Benzoate. Sodium benzoate, for internal as well as local use, has been highly reconunciuJed by a nnnd)cr of writ,(*rs. Dr. I. N. Ix>ve regarded it as efficacious in from five to fifteen grain doses. Some; observers claim to have shown that it arrests the growth of micro- organisms. According to J. Lewis Smith, II(;lferich, Graham Brown, and Sanne beli(>ve that it is a specific against the virtis of diphtheria. Smith says: "On the other hand, M. Dumas, surgeon to the Hopital de Cette, has not derived any marked benefit from its use, and Prof. A. Jacobi says that it does not deserve the eulogies bestowed upon it from theoretical reasonings." Such drugs as pilocarpine, copaiba, cubebs, resorcin, hyposulphite of sodium, and many others, have been recommended from tim(! to time, but none of them deserves any prominent place among the therapeutic agents useful in the treatment of diphtheria. Of the internal remedies to which prominence has been given we would consider most useful the tincture of the chloride of iron and bichloride of mercury. To these we would add strychnine, digitalis, and alcohol. But as diphtheria is a disease of variable type, we must treat each case according to the indications. Strychnine.— Strychnine is useful to combat cardiac depression. It may be given combined with tincture of the chloride of iron, or it may be administered separately. It is often advisable to inject it hypo- dermically. The dose should be adapted to the age of the child, but the amount which children of tender years will bear without harm is astonishing, especially when in a condition of toxaemia. A child of three years will take y^-g- of a grain every four to eight hours; in an emergency a larger dose will be borne. Digitalis. — Digitalis is also of advantage when the heart action is weak. In case of irritability of the stomach, which always occurs in profound toxiemia, digitalin may be administered hypodermically. Strophanthus, sparteine, caffeine, and the like, are also recommended to combat cardiac failure. To a child of five years two drops and some- times as much as four drops of the tincture of digitalis may be given every four hours, or from one to six drops of the tincture of strophanthus. In a great emergency one or two unusually large doses of these drugs may be administered, followed by the more ordinary dose at proper intervals. Citrate of caffeine may be used in doses from \ grain to 5 grains. Jacobi says: "For subcutaneous injections the salicylate (or benzoate) of caffeine and sodium, which readily dissolves in 2 parts of water, is valuable for emergencies, in occasional doses of from gr. 1 to 5 (6 to 30 cgm.), in from 2 to 10 minims of water." Alcohol. — There are but few other diseases which demand more imperatively the use of alcohol than does diphtheria. Mild cases will frequently do well without stimulants; but no case, however mild it may 45 706 DIPHTHERIA seem to be, should be considered out of danger until recovery has taken place. In view of the well-known depressing effects of the poison of this disease, even mild cases should receive small doses of some stimulant. Severe cases require a very liberal amount of alcohol in some form; it should be commenced early in the disease by giving small doses at first, and increasing the amount as the indications for its use become more pronounced. Whenever the heart action shows any loss of force, or the first sound of the heart becomes less distinct, or pallor is noticed, or the patient's strength is declining, large and frequent doses of some active stimulant are required. It matters little how the stimulant is administered, whether plain or in the form of milk punch or wine whey, provided that sufficient is given to produce the desired effect. Whiskey is more often employed, for the reason, doubtless, that good whiskey can be more easily obtained than good brandy. If whiskey disagrees with a patient brandy should be tried. Either of these stimulants may be administered in teaspoonful doses properly diluted, to a child of five years. In septic cases the amount of alcohol which a child may take without showing evidence of intoxication is nothing less than astonishing. In this type of diphtheria it is not unusual for a child of five years to take one teaspoonful or even two teaspoonfuls of whiskey every hour, making the daily amount ingested from three to six ounces. While alcohol is ordinarily contraindicated in albuminuria or nephritis, yet rather than lose the support of so important an ally in combating toxsemia, it should, nevertheless, be cautiously em- ployed. If the toxaemia be well marked, alcohol in doses however large will not save the life of the patient, but it may prolong it somewhat. When the heart's action begins to wane, it is difficult to restore it. W^e cannot recollect of ever having seen a patient recover when the pulse was once lost at the wrist. Hence, the great importance of beginning the use of alcohol early. If the stomach will not tolerate either whiskey or brandy a good wine should be substituted. We have found cham- pagne useful when the stomach is irritable. Aromatic spirit < f ammonia is a good stimulant, and may be used temporarily, if it be found more agreeable to the stmoch. Attention should be given to the diet of a diphtheria patient throughout the entire illness. In the acute stage of the disease all food should be of a fluid character, consisting of milk, beef-tea, broths, and the like. It may be necessary to peptonize these, though, as a rule, the digestion is not bad. Ice and iced drinks may be allowed. Should there be a craving after cold articles, cold junket, frozen custards, and frozen beef-tea may be given. Soft-boiled eggs are useful when the patient is able to take them. Later, corn-starch, rice pudding, bread and butter, fruit and vegetables may be added. As early as possible a full, liberal diet should be allowed. In regard to the complications of diphtheria, we feel that but little time need be spent here in discussing their treatment. Adenitis, otitis media, bronchopneumonia, and nephritis are the more common com- 77//'; TREATMENT ()/<' 1)1 1'llTII IIIU A 707 plications ericoiintcnHl, and they j)rcs(;nt no incjicatioiis for treatment at all (liiTerent tlian wlicui these; all'ections oeeiir from other causes. The paralysis of diphtlieria, however, dillers from the; other compli- cations, in that it is [jcculiar to the disease. It cannot be prevented; and drugs avail but little in hastening the cure, ""d'he most dang<;rous form is cardiax; j)aralysis. It is well to anticipate this cf>nflition by keeping the patient (juiet, and endeavoring to sustain th(; strength of the heart by administering digitalis, strychnine, alcohol, and other cardiac tonics. As we have already seen, cardiac paralysis often develops suddenly, and the patient may die before the })hysician can be summoned. The earliest symptoms of this affection should receive prompt attention. The patient should remain as (juiet as possible in lied, with his head low. It is sometimes advisable to raise the foot of the bed slightly. He should remain in the recumbent position when taking food, water, or medicine. Under no circumstances should he be allowed to leave the bed to empty his bladder or rectum. Whiskey or brandy should be given in doses sufficiently large to be of service. If the stomach be at all irritable, champagne is to be preferred. In case of a sudden seizure of heart-failure, hypodermic injections of brandy should be administered. The hypodermic use of strychnine will also aid in sustaining the heart action. Ammonia, camphor, musk, and the like sometimes serve as useful auxiliaries. At the same time the general strength of the patient should be well sustained with a liberal amount of nourishing and easily digestible food, such as peptonized milk, beef-tea, broths, or some of the concentrated foods designed for invalids with feeble digestion. For large children and adults soft-boiled eggs are useful, unless the digestion be very feeble. When improvement takes place the physician should see that the patient does not get out of bed too soon. For the multiple paralysis which follows diphtheria the patient requires sustaining remedies, such as iron, quinine, strychnine, and alcoholic stimulants. Particular attention should be given to the diet, as there is ordinarily marked debility and anaemia, with a feeble digestion. Beyond the employment of a sustaining treatment we do not believe that much can be done to hasten the cure of diphtheritic paralysis. Some physicians believe that they have derived benefit from electricity, but a large number speak doubtfully of its efficacy. As strychnine is known to be efficacious in many other forms of paralysis, it is frequently employed on general principles for the neuroses of diphtheria. Some observers have reported good results from its use, while others question its utility, except as a tonic. Prof. Henoch, Reinard, and Gerasimow claim to have hastened the cure of diphtheritic paralysis by hypodermic injections of strychnine. This drug is said to have been employed in one case (a boy, aged three and one-half years) with marked improvement in the tonicity of the muscles within twenty- four hours after the first dose, wdiich consisted of about -^ oi & grain, and this was repeated each day for fifteen days, when the patient was considered cured. In. another case (a child, aged six years) a complete 708 DIPHTHERIA cure is reported from hypodermics of about -^-^ of a grain daily for seven days, followed by ^V of a grain each day for twelve days longer. We are not convinced that strychnine possesses any special value as a remedy in diphtheritic paralysis. It is our opinion that tonics and a sustaining diet will do more toward helping a patient through an attack than anything else. The paralysis is seldom permanent. We have never known it to be so. In most cases complete recovery takes place in from two to four months. There is, however, one thing connected with the treatment of multiple paralysis of diphtheria which is of great importance. We refer to the care a patient should receive when unable to swallow. In all severe cases deglutition is difficult and sometimes impossible. It is necessary then to sustain the strength of the patient by nutritive enemata, or by introducing food into the stomach by means of an oesophageal tube. The latter is preferable, as it gives us a better idea of the amount of nourishment that is utilized. The patient should be fed every four hours, and with each feeding there should be administered also such medicine, stimulants, and the like, as may be required. It is not often that a patient has to be fed with the oesophageal tube for a longer time than two weeks. We recall one case of paralysis in which this means of feeding was employed for sixteen days. By holding the jaws slightly apart with the gag of the intubation set, it is not difficult to introduce the tube through the mouth into the stomach. The tube will slip down more easily if slightly oiled. If a patient be safely carried over the period of difficult or impossible deglutition, his chances of complete recovery may be considered very good. Treatment of Laryngeal Diphtheria (Membranous Croup). It is deemed most convenient to consider the treatment of laryngeal diphtheria under three heads: 1. Prevention. 2. The means of promoting the separation and expulsion of the pseudomembrane. 3. The adoption of such operative measures as will overcome the mechanical obstruction to respiration. Prevention. — ^There is no certain way of preventing laryngeal diph- theria, unless it be to guard the child against exposure to the infection of the disease. But when diphtheria begins in the fauces something may be done in the way of diminishing the liability of the membrane extending into the larynx. We have seen that a mucous membrane which is inflamed or congested is thereby predisposed to the diphtheritic process. It is advisable, therefore, to guard the patient, as far as possible, against the development of a catarrhal affection of the larynx. As soon as faucial diphtheria is recognized, the physician should see that the child is placed in a room of equable temperature and free from draughts. If the case occur in the winter season, and the atmosphere of the room is warmed by dry heat, it would be well to moisten the air TIIK rilF.ATMKNT Ol'' 1)1 1'lll'll HIU A 70f) by the addition of a little steam. It has been suggested that the steaui be impregnated with eiicaly|)tol or some other fragrant essential oil, but we do not tliink tliat this is of any great importanee. (^are should be taken not to overcharge tiie air of the room with irioisture,, as this would be more harmful than benefieial. in the sununer months fresh air should be freely admitted, with precautions against draughts, and steam may, be dispensed with. Drugs are of no avail in preventing laryngeal involvement. Anti- toxin may be of great service as a preventive measure, but we have seen the pseudomembrane in the fauces extend into the larynx on a number of occasions even after the administration of antitoxin. Means of Promoting Separation and Expulsion of the Pseudo- membrane. — When false membrane has formed in the larynx, constitut- ing membranous croup, nature's method of effecting a cure consists in the gradual disintegration of the membrane, or its separation and expulsion. How this process may be best promoted has always been a problem difficult of solution. Emetics have been freely employed, and of these turpeth mineral was for a long time believed to be espe- cially useful. But they can be of no service unless the membrane be in good part detached. The persistent use of emetics is objectionable on account of their depressing effect. When, however, a flapping sound is heard in the larynx, indicating the presence of partly detached membrane, an emetic should not be withheld except in cases of profound asthenia. The one selected should be of that class which excites prompt and efficient vomiting without producing prolonged nausea and depression. Among those to be preferred we would mention ipe- cacuanha, powdered alum, and sulphate of zinc. Warm Steam. — For the purpose of hastening the separation of the false membrane in croup there is a general consensus of opinion in favor of the continuous inhalation of warm steam. This is frequently impregnated with an alkali, like lime, or with some mild antiseptic agent, like eucalyptol, the compound tincture of benzoin, or turpentine. But it is the steam upon which the chief reliance is placed. Oertel believes that the energetic use of hot vapor causes a rapid and abundant suppuration of the diseased tissue, until finally the pseudomem])ranous layer becomes completely detached from the rapidly regenerating tissue of the mucous membrane, and is expelled either piecemeal or in its entirety. He regards this as nature's process of resolution in favorable cases. The inhalation of warm steam is undoubtedly at times of much benefit, but we are inclined to believe that this treatment is often carried to excess. When shut up in a tightly closed tent in which a basin of water is kept constantly boiling, the child receives not only a diminished supply of oxygen, when the blood is already suffering from an oxygen dearth, but his skin is kept bathed in moisture, and his clothing and bedding are constantly damp. The effect of such treatment is certainly depressing. Warm steam inhalation should therefore be employed with some care. Lennox Browne savs that the bed should be curtained 710 DIPHTHERIA and the hot vapor "brought near it by means of a steam-kettle, but the croup-tent bed, which gives the httle patient a continuous vapor bath, is as unnecessary as it is depressing." Slaking Lime. — Inhalation of the warm vapor which arises from slaldng lime in water has been highly recommended as a remedy in membranous croup. The vapor thus generated, being strongly alkaline, is believed by some to act as a solvent of the membrane. Oertel found that when a piece of pseudomembrane weighing three grains was placed in lime-water it swelled up in fifteen or twenty minutes into a loose, flaky mass, which could easily be divided, and after from thirty to forty minutes was completely dissolved. The assumption that lime- water acts in the same way when inhaled in the forai of vapor as it does in the test-tube is not, we think, borne out by experience. At any rate this treatment is not so frequently employed now as formerly. Calomel Sublimation. — ^The inhalation of sublimated calomel has been extensively used for the last twenty years or more with some degree of success. It is said to act not as a germicide, but by hastening the separation of the pseudomembrane, through, possibly, an influence exerted both locally and constitutionally. We have employed it fre- quently, but with only indifferent results. The number of cases which were materially benefited was small. The method of using it is very simple. Place the child in an improvised tent, not so large but that it may be fairly well filled with the fumes. The calomel may be sub- limated by placing it on a small fire-shovel containing a few hot coals; or it may be placed on a red-hot shovel, or on a piece of sheet iron or tin, or in an iron spoon, either of which can be heated by means of an alcohol lamp or a Bunsen burner. Eight or ten grains should be sublimated every hour, or at longer intervals. The Internal Use of Mercury. — The internal or constitutional treatment of membranous croup is to be carried out on the same lines as in the other varieties of diphtheria. Mercury in some form has long been employed, and most physicians believe that it gives better results than any other internal remedy that has been recommended. Calomel is much used in small and frequent doses, to the extent of causing slight ptyalism. Many practitioners confidently expect improve- ment as soon as this effect is produced. Dr. T. Clarke Miller,^ of Massillon, Ohio, expresses great confidence in mercuric chloride in the treatment of all forms of diphtheria. He gives y ^^ grain of calomel every hour for twelve to twenty-four hours, and then continues the same dose every two hours. He says: "If I find that the exudate has originated in or extended to the larynx, I use antitoxin at once. If the nose is involved seriously, it is well to use antitoxin, though not to the exclusion of the calomel. I would omit the antitoxin rather than the calomel." The bichloride, cyanide, and iodide of mercury have also been highly recommended by some writers. 1 The Diagnosis and Treatment of Diphtheria, read at the Toledo Meeting of the Ohio State ^ Pediatric Society. THE THEjVTMENT OF Dl I'llTII l<:iiIA 711 It is a pleasure to quote so often an author whose articles on rJiph- theria are everywhcTe regarded as classic. We refer to Prof. Jacobi, who says: "For nearly twenty years I have employed the bichloride in doses of 1 ingin. (gr. ,.,,) or more once every hour. The smallest babies take one-fourth or one-third of a grain daily for days in succession. Almost never will a stomatitis follow, and no gastric or intestinal irrita- tion, provided the dilution be in the proj)ortion of at least 1:8000. An occasional slight diarrlux'a jnay re((uire the addition of a few drops of camphorated tincture of opium. 1 can repeat a fonner statement, that never before the antitoxin period have I seen cases of croup getting well in such numbers, either without or with tracheotomy or intubation, as when under mercurial treatment." We have already expressed much confidence in the mercurial treatment of diphtheria, including, of course, membranous croup. Operative Measures. — If it be found that the laryngeal symptoms do not improve under the treatment recommended, but, on the contrary, become more and more marked, or if the patient be not seen until the symptoms of mechanical obstruction have become alarming, recourse must be had at once to operative measures. The operation which is necessary to overcome the difficulty is either tracheotomy or intubation. Formerly tracheotomy was universally employed, but of late years it has been almost entirely superseded, in this country particularly, by intubation. Intubation.^ — This procedure is viewed more favorably, mainly because it does not require the use of the surgeon's knife. We all know how reluctantly parents give their consent to the operation of trache- otomy on their child. When this operation was the only means of overcoming the obstruction to the entrance of air through the larynx, it was too often postponed until the child was almost moribund, and, consequently, the results were discouraging. Intubation being a blood- less operation, and not requiring an anaesthetic, parents do not hesitate to give their consent to this procedure, and hence the lives of many children who suffer from membranous croup are now saved that would otherwise be lost. It is a matter of great importance that operative interference, whether intubation or tracheotomy, be not delayed too long. It is almost criminal to allow a child to die from suffocation without making an effort to save its life by resorting to one or the other of these mechanical measures. W^hile intubation is to be preferred in most cases, it cannot always take the place of tracheotomj/. A physician without experience in intubation would be likely to fail in the operation, and if no one possessing the necessary skill is available, he would be obliged to resort to tracheotomy. Or the latter operation may be preferred, or even become necessary, when the membrane extends far down into the trachea. In such cases the intubation tube will not afford relief. Tracheotomy may also become necessary when the intubation tube is repeatedly coughed up. The procedure for relieving the stenosis of membranous croup by placing a tube in the larynx with its upper end below the epiglottis 712 DIPHTHERIA was first adopted by Bouchut in 1858. But, as his devices were crude, and as the operation was deemed impracticable by his confreres, and even ridiculed by them, he was discouraged from pursuing farther his conception of intubation. It remained for Dr. Joseph O'Dwyer, of New York, to devise and perfect the instruments necessary for the operation, and to demonstrate beyond question the utility of the procedure. O'Dwyer's work of devising the intubation tubes was begun in 1880, without, it is said, any knowledge of the previous experiments of Bouchut. It required, however, some four or five years of diligent experimentation before the set of intubation instruments, herein described, was evolved into its present state of perfection. The New York Academy of Medicine has in its possession a complete collection of all the instruments used by O'Dwyer in his long series of experiments. The collection is interesting as showing the various changes in the size, shape, and construction of the intubation tube in its evolutionary process. Intubation Instruments. — In their completed state the O'Dwyer intubation instruments consist of a series of seven tubes, a scale for measuring the size of the tubes, an obturator, an introducer, a mouth gag, and an extractor. The tubes vary in size, both as to their calibre and length, so as to fit the larynx of a child at any age. Tubes are also made suitable for adults, though they do not form a part of the regular outfit. The head of the tube is irregularly oval, with its anterior surface flush with the tube itself, so as not to interfere with the epiglottis, while posteriorly it projects backward so as to rest, when in situ, upon the rima glottidis. A tube that is too small for a patient may slip down into the trachea. In the left side of the head of the tube there is a small hole into which a string may be inserted. The object of this string is that the tube may be withdrawn in case it is introduced into the oesophagus instead of the larynx. The circumference of the tube is somewhat larger in its centre. The anterior and posterior surfaces of the tube are straight, while a central bulging is seen on either side. This is called the "retaining swell,'^' as it helps to keep the tube in place, and to a great extent prevents its expulsion by the act of coughing. The lower end of the tube is rounded off and blunt, and its lumen throughout is elliptic (Fig. 99). The tubes were originally made of white metal plated with gold; but later the inventor had them constructed of hard rubber overlying metal. This is considered an improvement, as the tube is much lighter, and more easily coughed out when the lumen becomes occluded with fragments of the false membrane. It is believed, too, that it is less liable to injure the larynx when worn for a long time. Certainly, it is less irritating from the fact that lime deposits do not form on it, as on the metal tube. The latter, when worn for a few days, is quite sure to become rough from these deposits. All intubation sets made at the present time contain only hard-rubber tubes. Each tube is provided with an obturator which is fitted to the intro- ducer. The obturator extends throughout the lumen of the tube, Till': Tli'l'JATMI'JA'T OF I )l I'll'I'llilUI A 71i projectinfT .sH^^Iitly from the Iowcm- cihI, wIkwc it is rouiHleation of the tube may also be recognized by the fact that the string grows shorter as the tube descends into tlie o'sophagus. It should Ix- pulh-fJ oni at once. '^rhe tube being properly placed, it is well to remove the mouth gag and allow the child to cough and expectorate for a minute or two, anrl at the same time to be sure that there is no obstruction in tlic tube Everything being satisfactory the gag should be reintroduced, the string cut and withdrawn, while the; tip of the index finger rests on the head of the tube to prevent its displacement. 'J"'he child should then be released and put to bed. If the child is very young, having no molar teeth, and the operatfjr distrusts his ability to remove the tube with the extractor, the string, instead of being cut and withdrawn, may })e looped over the ear of the child and secured to the cheek with a strip of adhesive plaster. In this case the hands of the child must be muffled, else the offending string will be caught with the fingers and the tube pulled out. In children with teeth this procedure is not to be recommended, as the string is soon chewed off and rendered useless. Experienced operators, however, prefer to remove the string in all cases. There are still some other points in connection with the operation that the beginner should know. In the first step of the operation the operator's hand containing the introducer should be close to the chest of the patient. The tube should be pushed backward on the median line of the tongue until it reaches the chink of the glottis, then the handle of the instrument must be raised, and the tube should slip down into the larynx without much force being used. The tube, during its introduction, sometimes causes a slight spasm of the parts, in which case the operator should pause for a few moments, when the spasm will probably relax and the tube slip into place. It should be remem- bered that the epiglottis must be kept out of the way; if not the operation will surely fail. It is important, too, that the child should be under perfect control in the arms of the nurse, and that it should squarely face the operator. The position of the child's head and neck should be, as Northrup says, as if the child were suspended from the top of its head. In case the first attempt at placing the tube is unsuccessful, rather than exhaust the patient with repeated trials at one sitting it is better to remove the gag and allow the child a few seconds to rest, or to cough and expectorate. A beginner rarely succeeds the first time; it is far better that he should make several short attempts than a prolonged one. A vigorous cough following the introduction of the tube is favorable rather than otherwise, as it shows that the parts have not lost their sensitiveness, and it clears the mucus from the trachea. If there is no cough, and the breathing ceases and the cyanosis deepens, there is surely an obstruction at the lower end of the tube; in which case it 718 DIPHTHERIA should be removed immediately. If the same result follows a repetition of the operation, tracheotomy should be performed. Some operators prefer to have the child in the recumbent position during the act of intubation. The advantages claimed for this position are that the operation can be performed with but a single assistant, and that there is less danger of heart-failure if the patient be greatly prostrated. The child should be rolled up in a sheet or thin blanket, as already described, and placed squarely on its back. (See Fig. 102.) In other respects the operator should proceed as before. At the present time the resident physicians in the Municipal Hospital employ this method altogether. It is also employed in the Willard Parker Hos- FlG. 102 Showing the lirst steps of intubation in the dorsal position. Dr. B. Franklin Royer.) (Photograplied by pital, New York, and is recommended by Casselberry, of Chicago, and Carstens, of Leipzig. Dangers and Difficulties of Intubation. — The operation cannot be said to be dangerous when performed by an experienced operator. It is true, instances have occurred in which exudate has been pushed down into the trachea by the tube, causing suffocation and instant death. This condition, however, is easily recognized at once, and the prompt removal of the tube is usually followed by forcible expulsion of the detached mass of false membrane. When this occurs the dyspnoea may be so greatly relieved that reintubation is not necessary. But fre- quently the membrane reforms and the operation is again called for. 77//'; TIU much delay the sensitiveness of the parts soon becomes so blunted that cough, Fk;. 103 Fixation of the larynx. (Lejars. ) Fig. 104 The tube guided by the index linger. (Lejars.) on which the safety of the patient depends, is not excited, and death speedily results from suffocation. The inexperienced and clumsy operator may incur other dangers, such as asphyxia from prolonged attempts at intubation, lacerating the 720 DIPHTHERIA tissues, or forcing the tube into a false passage. All of these accidents can be avoided with care. There are but few serious difficulties liable to be encountered by the experienced operator. It has been said that the tube may be Fig. 105 The tube penetrates the larynx. (Lejars.) Fig. 106. The tube in its proper position . CLejars.) obstructed m its course by entering one of the ventricles of the larynx. This, we are sure, hardly ever happens Avith the O'Dwyer tubes which are so nicely rounded at their ends. Besides the pushing down of membrane before the tube, or the occurrence of a slight spasm of the TIIF. TltKATMNNT OF 1)1 1'llTII I'llil A 721 muscles of the larynx, as dcscrihcd alxjvc, in inlrofliir-Irif^ tlif tnljc the operator will soinetinics meet with (h"(licnlty caused hy swelHn^', inflam- matory thickening, or anlema of the subglottic tissues. \Vh(;ri it is found that the tube adapted to the age of the child will n(jt enter readily, it is advisable to try a smaller one. After this has been worn for a short time there is usually no difficulty in introducing (me of tiie j)roper size. The narrowest part of the lumen of the larynx is in the region of the cricoid cartilage. We have seen a few instances in girls in which the cricoid ring was abnormally small, a fact which we have been able to demonstrate post-mortem,. When this condition exists only a little sweUing or a^dema of the lining membrane is needed to ninkc the intro- Withdrawal of the thread. (Lejars.) duction of the tube difficult. The only thing to do in such cases is to use a smaller tube. Treatment and Feeding After Intubation. — It is advisal^le not to make any local applications to the throat while the tube is in the lar^iix; at least, irrigation or spraying should not be practised. The applications to the nose, if required, need not be omitted. Internal treatmeat, stimulants, and the like, may be continued as before. The feeding of the child is the thing that frequently gives us the most concern. Some children swallow with but little difficulty after intuba- tion, while it is really distressing to see others drinking liquids of any kind. The act of swallowing excites coughing, and this may be still further excited by some of the liquid running down the tube into the ^ 46 722 DIPHTHERIA trachea. The cough is often violent, causing a large part of the liquid in each act of swallowing to be forcibly expelled, not only through the mouth but through the nose also. Children, however, usually persevere in drinking, and after a little while they frequently get along better. Semisolid food is not so liable to cause coughing, and is, therefore, preferable. When a child is old enough, we prefer to have it fed on bread soaked in milk. This forms a bolus which can be swallowed, as a rule, without exciting much cough. Fig. 108 Casselberry's position for feeding intubated cases. (After Nortlirup.) It is claimed that the difficulty of swallowing, even of liquids, may be overcome by placing the child on its back with the body and legs elevated, while the head hangs over backward at an angle of forty-five degrees or greater. It is thought that any liquid that may get into the tube will, with the child in this position, run out again rather than into the trachea. The placing of the child in this position during feeding was first recommended by Casselberry, of Chicago. He and many other physicians who have tried this method speak of it very favorably. In our experience it has not proved so satisfactory. In bottle-fed babies 77//'; TRMATMIiNT Oh'lDII'UTII l-:i{IA 723 it sometimes answers fairly well. It should ])C stated that soirie [jhysieians believe that the child swallows b('tt<'r lyin^ on the; abdomen with the head hanging forward. If it be found that the child is not getting sufficient nourishm(;nt by either of the methods mentioned, gavagi; should be resorted to. This may be done by introducing either a small o'sophageal tube or a flexible catheter through the nose into the stomach. If this route is found inconvenient or dilficult, the child's jaws may be slightly separated and the tube introduced through the mouth. If one catheter should not be long enough another may be joined to it by means of a short glass tube. Some prefer rectal feeding, but v^'e have never found it. satisfactory. Removal of the Tube, or Extubation. — The time for remo^'ing the tube will depend very much on the age of the child and the stage of the disease. In older cliildren the tube may be removed earlier than in those who are younger. Likewise, when the tube is not required until a late stage of diphtheria, it may l)e removed sooner than when intro- duced at an early stage of the disease. We have seen it stated some- where that O'Dwyer recommended that the average time of wearing the tube should be seven days; and if the patient's residence is a long distance from the physician's office the time had better be eight days. It has been our rule to allow the tube to remain in place six days before removing it. Frequently, however, the resident physicians remove it earlier, but they often find it necessary to reintroduce it. Northrup thinks that five days for a child over two years is long enough for the tube to be worn in the average case. He says: "At the Willard Parker Hospital the time allowed is four days; at the New York Foundling Hospital, three days." He, with many other writers, believes that the length of time which the tube is required in membranous croup has been materially reduced by the use of antitoxin; also, that reintubation is now less often required. Cases are not infrequently seen in which the tube, after having been worn for only a short time, is coughed up and expelled, together with a mass of membrane. Such cases sometimes recover without reintubation being required. There are other cases in which the tube is not retained longer than it is needed; that is to say, in the course of four or five days, when the membrane in the larynx has disappeared and the oedema sub- sided, autoextubation takes place through the agency of the cough. This result is always gratifying, and especially so to the inexperienced operator. Whenever the tube becomes obstructed it must, of course, be instantly removed. Fortunately, in most cases it is coughed up. Wlien coughed up, the tube is either expelled or the child removes it from the mouth with his fingers. In rare instances it is swallowed. Should this occur, no great uneasiness need be felt, as we have never known a tube that was swallowed fail to pass through the intestines. The Technique of Extubation. — Up to a certain point the technique of the operation of extubation is exactly the same as that of intubation. After being rolled up in a blanket or sheet, as before, the child should 724 DIPHTHERIA be held in the upright position on the lap of the nurse, or placed in the dorsal position, according to the choice of the operator. It is equally important that the child's head should be held steady, and that the axis of the head, neck, and trunk should correspond. The mouth gag being in position, the operator passes his index finger of the left hand backward over the dorsum of the tongue until he feels the tube and determines its position. He should then tilt the epiglottis forward and control it. Holding the extractor in his right hand, with the handle of the instrument near the chest of the child, he should pass it backward along the side of the finger until the tube is reached; the handle of the extractor should then be raised to a horizontal position, and, with the aid of the tip of the finger which is controlling the epiglottis, he inserts the beak of the instrument into the opening of the tube. Having suc- ceeded in doing this, he presses down the lever at the upper part of the extractor with his thumb, which causes the two parts of the beak of the instrument to separate, and thus the tube is caught and held, very much as a glove stretcher holds the finger of a glove. The operation is completed by lifting the extractor with the tube until it impinges on the hard palate, then depressing the handle and withdrawing the instrument and tube from the mouth. If the tube should slip off, as it often does, after having been lifted from the larynx, its removal can easily be concluded by means of the finger. It is important to properly regulate the distance of separation of the two parts of the beak of the extractor. This may be done by means of the screw in the handle. If the jaws of the instrument are allowed to open too widely the orifice of the larynx may be lacerated by a clumsy operator. Tlie extractor should be held in the hand lightly, as no great force is required to remove the tube. Be careful not to place the thumb on the lever until the beak of the instrument is well within the opening of the tube. If the operator should have difficulty in grasping the tube, it is better to make repeated short attempts, allowing the child to rest for a minute or two in the intervals, than to make a single prolonged effort. As extubation is more difficult than intubation, beginners often become nonplussed in their efforts to extract the tube. In such a dilemma, enucleation, or removal by pressure, is recommended. Park^ says: " It is possible in an emergency, in the majority of cases, to easily expel the tube by placing the child face downward with the body slightly elevated, and pressing gently against the trachea along its anterior surface, just below the end of the intubation tube." One of the writers tried this expedient a few years ago, but did not succeed. It was feared that the amount of pressure required to accomplish the purpose might injure the larynx. After the tube has been removed the patient should be placed in bed and carefully watched for a while to see that the respirations continue easy. In family practice the physician should not leave the house for 1 Loomis-Thompson, American System of Practical Medicine. r///'; trmatmi<:nt of dii'IitiiI'Uua 725 at least thirty minutes. Tf tlu'rc is any Hifliculty in })r('afliinf( lio sliouM remain until lie feels reasonably sure that tin; jjaticnt is going to get along without the tube. Reintubation is often necessary. When dyspncjea returns after extubation the condition of the patient not infrequently becomes critical so (juickly that if })rompt aid be not afforded fleatli from suffocation will siu'ely result. It is, therefore, highly im[>fjrfant that the physician should be within easy call ff)r some hours. Having seen not a few children perish at this stage of the disease when their lives might have been saved by prompt aid, we feel that the importance of the advice just given cannot be emphasized too strongly. To lose a child (hu-ing the height of an attack of membranous frr)up is bad enough, but to see it die after the danger has apparently passed, and when the brightest hopes are entertained for its recovery, is much worse. Such a result may not inaptly be compared to the sinking of a ship in the harbor after it has weathered the storms of the ocean. For lessening the nervous excitability of the patient, as well as for its relaxing effect, a little morphine may be given just before removing the tube. Park says that at the Willard Parker Hospital, "immediately after the extraction of the tube, the child is given -^^ grain of morphine hypodermically, and an ice-bag is applied to the larynx. It is sought in this way to lessen the irritation and swelling of the larynx. The child is still kept in a recumbent position for one or two days." Perfect quietness at this time is of great importance. A few hours of quiet sleep after extubation is quite desirable, as it will sometimes tide a patient over the period at which the indications for reintubation are most likely to develop. Prolonged Intubation. — Despite the free use of antitoxin, and the greatest possible care in the operation of intubation and extubation, it frequently happens that the tube must be w^orn for a much longer period than five or six days. In other words, when the tube is removed at the time just indicated, the dyspnoea returns, making reintubation necessary; and this sometimes happens over and over again in the same patient through a long series of intubations and extubations. We know of nothing connected with the work of intubation that is more perplexing to the operator, or more distressing to the patient, than this unfortunate occurrence. Some of these cases require months and in rare instances years of intubating until recovery takes place. Indeed, a large proportion of the most obstinate cases perish from one cause or another before the difficulty is overcome. Prolonged intubation is not always due to the same cause; it may result from one of several causes, such as persistence of the false mem- brane in the larynx, oedema of the tissues, subglottic lar}Tigitis with thickening of the soft parts, ulcerations, exuberant granulations, cica- tricial contractions, destruction of the cartilages and collapse of the larynx, atony of certain muscles, or abductor paralysis. But it must be admitted that it is often difficult to differentiate between these various pathological conditions of the larjTix, or to explain satisfactorily the exact cause of the difficulty. 726 DIPHTHERIA Fig. 109 Some writers believe that the conditions rendering the prolonged use of the tube necessary are rare, or even extremely infrequent. We have met with very many cases in which it was necessary to continue the use of the tube longer than the usual period of five or six days without development of the pathological changes which lead to chronic stenosis. Such cases are able to get along without the tube in the course of two weeks, or three, at the longest. But postdiphtheritic stenosis occurs, according to our experience, in from 1 to 3 per cent, of all cases of intubation. Dillon Brown is reported as saying that he has encountered it in the pro- portion of about once in 75 or 100 cases. In discussing the causes of prolonged intuba- tion but little consideration need be given to traumatism resulting from the introduction or removal of the tube. While it is true that the unskilful use of the introducer or extractor, or too much pulling upon the epiglottis during the operation, may cause abrasions and oedema of the soft parts, and thus make reintubation neces- sary, yet it is certain that the principal cause of "retained tubes" is not due to such an injury, but to traumatism in the larynx occasioned by the tube itself. It is important that the tube should prop- erly fit the larynx; it certainly should not be too large. But no matter how well it fits, it some- times causes ulceration. It should, therefore, be dispensed with as soon as possible. It, however, should not be removed until there is reason to believe the patient can get along without it; for removing it too early would necessitate its reintroduction, and thus the risk of traumatism would be increased. When the tube is required longer than the usual length of time on account of the persistence of false membrane in the larynx, the con- dition, from our present point of view, is not serious, for as soon as the membrane disappears the tube can be dispensed with. We believe that the most common cause for retention of the tube, at least primarily, is subglottic laryngitis with oedema. Later, as the tube is worn longer, and has been removed and reintroduced many times, tissue changes of a destructive character sometimes take place in the larynx, with a marked tendency to terminate in chronic stenosis. We have removed, post-mortem, larynges which showed considerable loss of tissue from ulcerative action. These ulcers heal by granulation and the formation of cicatricial tissue, and hence permanent stenosis to a greater or less degree is liable to result in such cases. Many of the cases with subglottic laryngitis and oedema improve after two or three intubations, and recovery follows without any un- toward symptoms. Other cases are more troublesome, especially those which develop also atony of the muscles or abductor paralysis. With Pressure ulcer due to intu- bation. (Baginsky.) PLATE LIX. Larynx and Trachea Renioved at Autopsy. Sho'v\nng a large roundisli ulcer caused by pressure of the intubation tube. The lower linear -wound -was the result of a tracheotomy. From a patient in the Municipal Hospital. (Photographed by Dr. E. N". Fought.) 77//'; r/U'JATMJ'JNT OF 1)1 1'lmi Hiu A 727 this complication it may be necessary to repeat intubation many times, and the patient is fortnnate if he escapes ulceration of the larynx. He, however, rarely escapes bronchopneumonia, more or less marked. When there is marked ulceration of any part of the larynx, with little or no oedema, the child may get along fairly well witliout the tube for a few days, but as cicatrization takes place the lumen of the larynx becomes gradually diminislied, with a correspondingincrease of dyspna-a. In attempting to perform intubation in such a case, it has been found impossible to introduce the tube. We have been confronted with this difficulty more than once, and in order to save the child's life have resorted to tracheotomy. In cases of ulceration of the larynx we believe it is good practice to use the tube intermittingly until the ulcers have cicatrized. If there is difficulty in introducing the tube it had better be left undisturbed for a long time — i. e., from one to two weeks at least. In cicatricial stenosis, however, after the difficulty is overcome of introducing a tube, though small, but of sufficient calibre to supply the lungs with air, it is comparatively easy, after this tube has been worn for a day or two, to introduce a larger one. Having thus restored the normal lumen of the larynx, it is advisable to insert the tube two or three times a week for a while, leaving it in place from twelve to twenty-four hours. Later, as the conditions improve, it need not be introduced so frequently. But the tube should not be dispensed with until the tendency to recontraction of the cicatricial tissue has been overcome. In cases of prolonged intubation the vulcanite tube should by all means be preferred. The calcareous deposits which always form on metallic tubes make them very objectionable. They cannot be worn long without causing irritation and often ulceration of the larynx. As these deposits do not form on hard-rubber tubes, they may be allowed to remain in position for a long time without doing harm. One of our cases of four years' standing has worn a vulcanite tube continuously for periods of three months each, and once as long as five months without removal, with no unpleasant consequence except, as the parents say, an offensive breath. The tube never showed any calcareous deposits. It is worthy of remark that when the tube has been worn for a long time the child acquires the ability to swallow with little or no difficulty. We have called attention to the fact that in some cases of prolonged intubation, after the tube has been removed for a few days, it is impossible to reintroduce it, and that tracheotomi/ becomes necessary. Likewise, this operation may be deemed expedient when the tube cannot be retained in position. We have seen cases in which the tube was con- stantly coughed up, even when it was two or three sizes too large. In such a case it sometimes happens that the head of the tube enters the postnasal space and suffocation threatens if the tube be not immedi- ately removed or pushed down into the larjTix. To keep it in place would require a constant attendant. Under such circumstances it is better to perform tracheotomy. 728 DIPHTHERIA In this troublesome class of cases we are, however, reluctant to recommend tracheotomy except as a dernier ressort. This is because of the difficulty we have many times experienced in getting rid of a retained tracheal cannula. One such patient is at the date of writing in the hospital^ having worn the cannula for about two months. After returning to their homes, three of our patients of this description were taken to a general hospital in this city and placed under the care of a surgeon. An operation was performed with the view of overcoming the stenosis due to contraction of the cicatricial tissue in the larynx, but in each instance the operation was unsuccessful, and the tracheal cannula had to be continued. Two of these unfortunate children subse- quently contracted pneumonia and died. There are three other ex- patients of whom we have knowledge with retained tracheal tubes; in one the retention, at the time of writing, has extended over a period of six months, and in the other two of about four years each. The difficulty in getting rid of the tracheal cannula in this class of cases may not be due alone to cicatricial tissue in the larynx caused by the intubation tube. In addition to this a later obstruction is not infrequently developed as the direct result of the inflammation caused by the long-retained cannula. This occurs at the upper angle of the wound and may be in the nature of a stricture, or the larynx may be completely occluded by cicatricial tissue. This condition is even of more serious import than the former. We have seen two such cases in which it was impossible to pass a probe through the lumen of the larynx, either by way of the mouth or the tracheal wound; and the voice, even in the faintest whisper, was lost, which proved that no air passed through the larynx. According to O'Dwyer, a stricture of this description develops in a large proportion of young subjects when the operation is high, involving the cricoid cartilage or its immediate vicinity. He says: "When the wound is still higher, that is, wholly within the larynx, complete occlusion with adhesion of the vocal cords is very liable to occur," etc. As to the treatment of chronic stenosis of the larynx, we believe that long-continued intubation offers the best results. As soon as the tube is once introduced, no matter how small it may be, the chief difficulty is overcome. After this, tubes of graduated sizes should be employed, one after the other, until the one suited to the age of the child is reached. As already stated, the tube may have to be worn intermittingly for a very long time before the cicatricial tissue loses its power to contract. The physician should not become discouraged too soon, but persevere, as it may sometimes require years to remedy the difficulty. ^Vhen occlusion of the larynx is complete, or nearly so, whether caused by the intubation tube or a long-retained tracheal cannula, it will be found impossible to introduce a croup tube of the smallest size. Such cases are difficult of management by the general practitioner and had better be referred to the laryngologist. We believe, however, that instead of attempting to force an entrance from above downward, it is better to etherize the patient and enlarge the tracheal wound at rilK TREATMENT OF J)I I'llTII Kill A 729 its upper angle so as to admit of tlic introduction of a soniul from hfilow. In this way the sound is h'ss Hable to injure the parts by catching in the ventricles. The intubation tube should then be introduced and worn continuously for one or two weeks, after which it should be employed intermittingly until a cure is eff('ct(;d. This procedure was recommended by 0'J)wyer in a ])af)er read l)('for(! the; British Medical Association in 1804, on "Treatment of Chronic Stenosis of the Larynx by Intubation." In this paper O'Dwyer says: "The length of time that intermittent intubation will be required to effect a permanent cure will be influenced largely by the amount of cicatricial tissue present, and its location. If confined to the chink a more S})C(;dy result may be expected, because of the stretching which is exerted by the expansion of the glottis with every breath. After the normal lumen of the larynx has been restored, or at least ample breathing room secured, a tube should be inserted once or twice a week, and allowed to remain in position from twelve to twenty-four hours. This interval can Ije gradu- ally increased according to indications, and continued imtil the tendency to recontraction has been permanently overcome." After the introduction of the intubation tube in these cases of chronic stenosis in which tracheotomy has been performed, it is desirable that the tracheal wound should be kept open for some time. If it could be kept patulous — a thing difhcult to accomplish in a child — the liability of the tube being coughed out would be greatly lessened. A special tube or combination of tubes that would meet this indication seems to be an important desideratum. At any rate, O'Dwyer's advice should be heeded. It is as follows: "In practising intubation for the removal of a tracheal cannula, the wound under all circumstances must be kept open until sufficient breathing room through the natural passage has been secured to sustain life, in case the tube should be coughed out. This is, as a rule, extremely difficult to accomplish, especially in cliildren. The hard-rubber plug devised by Drs. Pitts and Brook, and used in a series of cases, appears to be most practicable for this purpose. It is provided with a collar similar to that on a tracheal cannula, by which it can be held in position." Shurly,^ of Detroit, believes that the cure in cases of prolonged intu- bation may be hastened by smearing the tube with an ointment com- posed of alum and vaselin. Louis Fischer, of New York, likewise recommends 10 per cent, alum or ichthyol-gelatin. 1 A paper read in the Section on Diseases of Children, American Medical Association, 1903, on " Prolonged Intubation Tubes, with a Method Leading to their Extraction." CHAPTEKXIY. DIPHTHERIA {Continued). THE SERUM TREATMENT OF DIPHTHERIA. The antitoxin method of treating infectious diseases may be said to have had its origin in the scientific investigations of Pasteur in 1880. He then made the discovery that an unusually mild attack of fowl cholera may be produced in chickens by inoculating them with an attenuated or non-virulent virus of that disease. Chickens thus inocu- lated, he found, were thereby rendered immune to this affection. He also applied this discovery to anthrax in sheep with similar results. Later — in 1886 — Salmon and Smith showed the great practical value of Pasteur's discovery by an application of this principle to the protec- tion of swine against hog cholera. With a knowledge of the fact that the rat and the frog were peculiarly refractory to the operations of the anthrax bacilli, Behring showed by experiment that the blood taken from these animals was, within cer- tain limits, efficacious against the production of anthrax in other animals. In 1890 Behring and Kitasato startled the medical world with the announcement that if an animal be immunized against tetanus or diphtheria the serum of the blood of that animal, when injected in sufficient quantity, is capable not only of immunizing other animals against an attack, but also of effecting a cure when attacked. These observers published their discovery in the follovdng language: "Our researches on diphtheria (Behring) and on tetanus (Kitasato) have led us to the question of immunity and cure of these two diseases, and we have succeeded in curing infected animals and in immunizing healthy animals, so that they have become incapable of contracting diphtheria or tetanus."^ In this connection it is due Aronson to state that, with equal diligence in this field of labor, he also succeeded soon afterward in immunizing animals against diphtheria. After the investigations of these men, it is only fair to mention the confirmatory experiments of Fraenkel, Wernicke, Roux, and others, who likewise succeeded in producing in animals an immunity against diphtheria by inoculating them with virulent or somewhat attenuated cultures or with diphtheria toxin. But, as already shown, Behring carried these researches one step farther by demonstrating that the blood of immune animals contained a substance which antagonizes ' Quoted by Lennox Browne, Diphtheria and its Associates. THFj Sr<]RJIM TRMATMMNT OF DH'II'I'II FltlA 7.';] tho (liphtlicria, toxin. Tlicsc iinporlaiii studies fDiisfiliitc tlic foiiriflufion upon which has been based the mocJern antitoxin treatirif-nf of rjiph- theria. The last link in the chain of these interestinff investigations having been forj^ed, it now remained to apply the dis(;overies tiiat liad been made to their special purpose of ciwin^ (Hj)htlieria in human beings. Here, as in the entire field of this research, the work of Behring was most productive. Tie succeeded in reaching the goal of his investigations, and, together with Kossel, in 1898, recorded 30 cases of fiif)htheria in human subjects which had been benefited l)y the use of serum from the blood of animals artificially immunized. In 1894, Ehrlich, Kossel, and Wassermann reported 223 cases treated with antitoxic serum, with a mortality rate of 23 per cent. In June, 1894, Katz, a colaborer of Baginsky, reported to the Berlin Medical Society 128 cases of diphtheria which had been treated with serum produced from one of Aronson's horses. This number was subsequently increased by Baginsky to 163 cases, with the surprisingly low death rate of 12.9 per cent. While the announcements of the foregoing results were received with intense interest, the culminating point of enthusiasm was reached at the Eighth International Congress of Hygiene and Demography, held at Budapest in September, 1894, when Roux presented his brilliant paper on the subject of the serum treatment of diphtheria (I>ennox Browne). He announced that he had confirmed, by experiments in the Pasteur Institute, all the important statements made by Behring and others who labored contemporaneously, and presented the records of a large number of cases in which the serum treatment had been employed successfully in the human subject, "and," as Lennox Browne so aptly says, "by comparative statistics, enforced the attention of the whole medical world to a consideration of its claims." Theory of the Action of Antitoxin. — There seems to be very Uttle known as to the modus operandi of antitoxin in the treatment of diph- theria. It exerts no bactericidal effect upon the Klebs-I.oeffler bacilli, although it is supposed to arrest the inflammatory process caused by these organisms. It is also believed that it does not act chemically or otherwise upon the toxin circulating in the blood, but rather upon the living cells of the body, through whose agency the cure is effected. Park says: "After the cells have been to a certain extent affected by the toxin, the protective power of the antitoxin can no longer be exerted and the lesions progress in spite of it." While the mode of action of the antitoxic serum cannot be satisfac- torily explained, yet there is no doubt that it is capable of neutrahzing the effect of the toxin of diphtheria in animals. This has been demon- strated thousands of times in the laboratory by bacteriologists. Park says: "We have every reason to expect that, since the toxin in human diphtheria is, so far as we can determine, exactly the same toxin as that in diphtheria in animals, tliis power of the antitoxin to make harmless the toxin will manifest itself in man under similar conditions." 732 DIPHTHERIA Preparation of Antitoxin. — As already pointed out, to render an animal immune to the diphtherial poison it is held to be sufficient to gradually accustom that animal to the action of the poison. The serum of an animal thus treated is believed to possess not only prophy- lactic but also .curative qualities. The goat has been used in this way for the production of antitoxin; but in order to obtain a more abundant yield — as well as for some other reasons — the horse is the animal now generally preferred. Having eliminated the possibility of the existence of glanders and tuberculosis by the proper tests, the horse is brought into a good con- dition by rest, diligent grooming, and careful feeding, preparatory to beginning the process of immunization. According to Park, the follow- ing method is employed in the production of antitoxic serum by the Health Department of New York City: To prepare a strong diphtheria toxin a virulent culture of the Klebs- Loeffler bacillus, grown under special conditions, is, at the end of a week's growth, rendered sterile by the addition of 10 per cent, of a 5 per cent, solution of carbolic acid. In twenty-four hours it is filtered through sterile filter paper and stored in bottles in a cool place. A number of horses are injected with an amount of toxin sufficient to kill ten thousand guinea-pigs of 250 grams weight each (about 44 c.c. of strong toxin). With each injection of toxin 10,000 units of antitoxin are given. After from three to five days, when the fever has subsided, a second injection of a slightly larger dose is given. Increasing doses of toxin are then given at intervals of five to ten days, until, at the end of two months, from ten to twenty times the original amount is given. The horses are then bled and the blood serum tested for antitoxin. Those animals yielding less than 200 units in each cubic centimetre are discarded. The remaining horses are then further treated with ascending doses of toxin. At the end of three months the serum should contain from 300 to 800 units of antitoxin to each cubic centimetre. The best horses will furnish high-grade antitoxin for years. A three months' freedom from toxin injection should be given the horses each year. The blood is obtained by plunging a sharp-pointed cannula into the jugular vein. It is received in Ehrlenmeyer flasks and allowed to clot, the serum then being siphoned off. Antitoxin is a proteid substance of unknown chemical composition. It is destroyed by heat 55° C, and is precipitated from its solution in the- same manner as globulins. As already pointed out, antitoxin possesses the property of neutral- izing, within certain limitations, the diphtheria toxin within the body. That is to say, when a given amount of antitoxin is injected into an animal with or just before a certain quantity of the toxin, it abrogates the poisonous effect of the latter. Behring and Ehrlich applied the term "antitoxin unit" to an amount of antitoxin capable of protecting the life of a guinea-pig weighing 250 grams from one hundred fatal doses of toxin. Ehrlich later Till': HI': HUM Tia<:ATMi:NT oi'' Dii'iiriiHiaA 733 pointed out the variability of ihv. (Ilplithcria toxin, and tlicreFore tli(! liability of error in such standardization. Park, who experimented with toxins of did'erent potencies, gives the following definition of an antitoxin unit: "The amount of antitoxin necessary to f)roteet the hfe of a guinea-pig from one himdred fatal doses of a toxin similar to that adopted as a standard, namely, one liaving th(! cliaraeteristics of toxins in cultures at the height of their toxicity." lie .says: "This amount of poison is produced by the growth for one week of a virulent baciHus in 1 c.c. of bouillon." The Serum. — The serum varies considerably in color, though it should be clear and free from anything that looks lik(! bacterial growth. It is maintained in an aseptic state by putting it into sterilized bottles, which are hermetically sealed and kept in a cool place. It is fpiite common to use some preservative, such as camp»hor, carbolic acid, trikresol, and the like. The serum on the market varies greatly in antitoxin units. It is believed that each cubic centimetre should contain at least 100 anti- toxin units, but it is desirable to have it much stronger. Originally, Behring's firm put up three strengths in vials of about 10 c.c. each, as follows : No. 1, containing 600 units, which was regarded as a suitable dose for a child at the onset of an ordinary attack of diphtheria. No. 2, containing 1000 units, for a severe attack in children. No. 3, containing 1500 units, for adults, or a very severe form of the disease in children. The serum prepared in this country is put up in vials containing from 5 c.c. to 10 c.c, and represents a strength of 100 to 500 antitoxin units to each cubic centimetre. The number of units in each vial should appear on the label. Dosage. — In considering the dose one should think of antitoxin units rather than the quantity of the serum; but it must be admitted that there is no fixed dose. In the present state of our knowledge it is impossible to fix the dose on the basis of age, as in the case of drugs. Perhaps most practitioners inject as many antitoxin units into a child as into an adult. This does not seem unreasonable when we consider that the amount of toxin absorbed, and which we seek to neutralize or counteract, is in all probability as great in the former as in the latter. It is also not improbable that the younger the child the greater the susceptibility to the toxin of the disease, with a less power of resistance, and "consequently," as Lennox Browne remarks, "if, as has been suggested, the remedy acts by cell stimulation, the greater the necessity for a large dose of the serum; or, in other words, since the young cell elements are so extremely sensitive to the diphtherial poison, they require to be fortified all the more strongly in order to exercise an effective resistance." We may state, on the authority of the writer just quoted, that Roux, in his first announcement, speaking of the serum prepared at the Pasteur Institute, advised that 20 c.c. (repre- senting, probably, 2000 units) be given to every patient — adult, or child 734 DIPHTHERIA above one year — so soon as seen, and even in advance of the bacterio- logical diagnosis, stating that for children under one year the first dose should be as many cubic centimetres as the child is months old. In very severe cases, he said, the dose should be as much as 30 c.c, or even more. It has been deemed advisable by the most competent observers to regulate the dose according to the time that has elapsed since the onset of the disease and the severity of the attack. As we have just shown, Behring believed that a dose of 600 units was sufficient for a child at the onset of an ordinary attack, but if the case be a ery severe, or far advanced when first seen, the dose should be increased to 1500 units. We feel that what Park^ has said on the subject of dosage is worth quoting. He writes: "The size of the dose should be measured chiefly by the extent and intensity of the disorder; also, but to a less degree, by the size of the patient and the duration of the illness. For young children, with but moderate lesions of the tonsils or palate, a single dose of 1000 to 1500 units will suffice. For older children and adults 1000 to 2000 units should be given. In children who are already seriously ill or who already show the toxic effects, or in whom the larynx is involved, a dose of 1500 to 3000 units ... is necessary. "If the symptoms do not abate, another 1000 to 2000 units may be given on the following day. In a few cases still a third injection is required. Exceptionally, a week or ten days after administering the antitoxin, a slight return of exudate may appear; here another moderate injection is indicated. Where these doses have not benefited it is doubtful if larger ones will succeed. "At the New York Hospital for Contagious Diseases for several months one-half of the severe cases received on admission 3000 units, and again on the following day 3000 more. If no improvement followed, a third 3000 units were given. The other half received 2000 units on admission, and a second 2000 in eighteen hours. So far as one could judge, those receiving the lesser amount did as well as those receiving the very large amounts. On the other hand, no additional disagreeable effects were noticed from the larger quantities."^ McCollom,^ of the South Department Hospital, Boston, recommends that antitoxin be administered in large doses. He advises that 4000 units be given at once, and that this dose be repeated at intervals of 1 Loomis-Thompson, American System of Practical Medicine. - While these pages are going through the press we note in the Archives of Pediatrics, December, 1904, an abstract of a discussion in the New York Academy of Medicine on the dosage of diphtheria antitoxin In which Dr. Park's views are given as follows : He said that for three years he had experi- mented with antitoxin in doses greatly varying in size : during one year the dose was 10,000 to 20,000 units; the next year it was between 5000 and 10,000 units; the third year it was between 3000 and 5000 units. Hfe said it was very difQcult to find out which dosage produced the best results. In bad cases of diphtheria Dr. Park advocated using large doses. In mild cases, either early or late, involving tonsils and pharynx, he used 2000 units ; in severe early cases 4000 units ; in ordi- nary laryngeal cases 5000 units; in malignant cases, tonsillar, pharyngeal, or nasal, 10,000 units, and repeating this dose at the end of twelve hours unless the patient is distinctly better. He emphasized the fact that the antitoxin should be given for the diphtheria and not for any accompanying condi- tion like pneumonia. 3 A Plea for Larger Doses of Antitoxin, Medical and Surgical Reports of the Boston City Hospital, 1900, eleventh series. 77//'; sf<:ni/M tiiilished data, Biggs and Guerard arrived at the following conclusions:' "It matters not from what point of view the subject is regarded if the evidence now at hand is properly weighed, but one conclusion is or can be reached — -whether we consider the percentages of mortality from diphtheria and croup in cities as a whole, or in hospitals, or in private practice; or whether we take the absolute mortality for all the cities of Germany whose population is over 15,000, and all the cities of France whose population is over 20,000; or the absolute mortality for New York City, or for the great hospitals in France, Germany, and Austria; or whether we consider only the most fatal cases of diph- theria, the laryngeal and operative cases; or whether we study the question with relation to the day of the disease on which treatment is commenced, or the age of the patient treated; it matters not how^ the subject is regarded or how it is turned for the purpose of comparison with previous results, the conclusion reached is always the same, namely, there has been an average reduction of mortality from the use of anti- toxin in the treatment of diphtheria of not less than 50 per cent., and under most favorable conditions a reduction to one-quarter, or even less, of the previous death rate. This has occurred not in one city at one particular time, but in many cities, in different countries, at different seasons of the year, and always in conjunction with the introduction of antitoxin serum and proportionate to the extent of its use." Among the earlier effects of antitoxin is the whitening process which the false membrane undergoes. Following tliis, the membrane begins to separate, and, according to Roux and many other observers, entirely disappears in four or five days after the injection of the serum. The subjoined table shows the day of the disease w^hen antitoxin was administered to 350 patients in the Municipal Hospital, Phil- adelphia, and the day on which the throat was declared free of mem- brane. These were not selected cases, but taken at random. 1 Quoted by Park, Twentieth Century Practice of Medicine. 740 DIPHTHERIA The Day of the Disease on which the Throat was Declared Free of Membrane. Day of disease on which anti- toxin was administered. No. of cases. i •6 (N CO iTJi si .£3 00 OS g .0 CO S J3 ^' 01 o3 First . . Second . Third . Fourth . Fifth 25 118 91 53 26 12 8 12 4 1 1 2 3 8 6 17 6 ■5 19 16 1 3 18 16 7 2 2 12 15 8 8 2 10 10 7 3 2 1 10 9 10 6 3 4 1 12 7 5 2 1 4 2 1 4 2 3 1 1 2 1 2 2 3 1 1 1 1 1 2 1 1 1 1 3 3 1 1 4 1 1 1 1 2 1 2 1 1 On the 28d, one. Sixth On the 30th, one. Seventh Eighth . Ninth . On the 27th, one. 1 2 Tenth . ! I Total 350 1 2 11 29' 41 46 1 45 35 42 35 15 10 8 7 6 1 5 3 3 1 It may be seen in the above table that the earher in the disease the antitoxin was administered, the sooner the membrane disappeared. Lennox Browne, however, beheves that antitoxin is not a very im- portant factor in hastening the separation or disappearance of the mem- brane. He shows comparisons between 92 cases treated with serum and 67 without, as follows: Day op Treatment on which the Throat was Declared Free of Membrane. Day. Series A, without serum. Series B, with serum. Second .... 4 cases or 6 per cent. 1 case or 1.08 per cent Third 13 " 20 4 cases or 4.3 " Fourth 14 " 21 9 " 9.8 " Fifth 14 " 21 18 " 19.5 Sixth 8 " 12 18 " 19.5 Seventh 6 " 9 " 10 " 10.8 Eighth 5 " 7.4 " 2 " 2.1 Ninth 1 case or 1.5 " 1 case or 1.08 " Tenth 1 " 1.5 " 1 " 1.08 Eleventh 1 " 1.5 " " Twelfth . 2 cases or 2.1 " Thirteenth 2 " 2.1 " Fourteenth 2 " 2.1 Seventeenth 1 case or 1.08 " Twenty-fourth 1 " 1.08 Twenty-eighth Thirty-ninth 1 " 1.08 " 1 " 1.08 74 + 18 = The author of this table says: "In Series A this fact (the day on which the membrane disappeared from the throat) was noted in only 77//'; HNIiUM 7'n/<:ATMl'!NT OF 1)1 1'llTII EHIA 74] 67 of the cases, and in 02 in Scries li. Only I occnrntfJ (in Scries Aj in which membrane reappc^arccJ, and that on the foijrtccnt}i day after a(hnission; whereas, in Series B there were 5 cases of reappearance, 18 cases in which d(>ath occurred Ix^forc; it hiid cleared entirely, anri in 1 case it was observed as latrurn application." Kassowitz reproduces graphic charts from an article published by de Maurans/ in which it is shown that the mortality from diphtheria in Birmingham, Liverpool, Dublin, and Stockholm has strikingly risen during the serum period. The rise began in some instances a year or so before the use of serum and in others after its use. This writer still further shows that the curves of diphtheria mortality were not influenced by the introduction of serum treatment in Budapest, Glasgow, Zurich, Lille, Cologne, Berne, Christiana, Beriin, Lyons, Brussels, Leipzig, Edinburgh, Paris, Geneva, Copenhagen, Havre, Nantes, Toulouse, Turin, Antwerp, Stuttgart, Munich, Hamburg, Buenos Ayres, and London. As tending to show the inutility of antitoxin, Kassowitz says that in 1897, according to the German Imperial Board of Health Reports, 42.9 per cent, of those who died of diphtheria were given serum within three days of the onset of the disease, and 22 per cent, within two days. The value of the antitoxin treatment is forcibly demonstrated in the reports of the Metropolitan Asylums' Board. In 1894, 3042 patients of all ages were treated without serum, in the hospitals controlled by the Board, with 902 deaths — a death rate of 29.6 per cent. In 1895, the first year of the serum treatment, 3529 patients were thus treated, with a death rate of 22.5 per cent. This shows a fall in the mortality of 7.1 per cent. In the annual report of the Metropolitan Asylums' Board for 1901, it appears that, in that year, (i499 cases of diphtheria were treated with antitoxin in the Board's hospitals, with 817 deaths — a death rate of 12.5 per cent. There has, therefore, been a reduction in the mortahty from 29.6 per cent, in 1894, without antitoxin, to 12.5 per cent, in 1901, with antitoxin. The treatment in other respects is said to have been the same. According to this report, the laryngeal cases treated in the Board's hospitals in 1901 with antitoxin numbered 753, of which number 159 died, yielding a death rate of only 21.1 per cent. 1 Semaine modicale, 1901, p. 401. 746 DIPHTHERIA Goodall/ of London, presents the following compilation of statistics from reports of the statistical committee of the Metropolitan Asylums' Board, showing the case mortality of the city of London, before and since the advent of antitoxin: Mortality per cent, of all notified cases Mortality per cent, of notified cases admitted to ) Asylums' Board hospitals J Mortality per cent, of notified cases not admitted Per cent, of notified cases admitted to hospitals Before antitoxin. 1892 1893 1894 23.8 24.8 21.5 30.1 24.8 27.1 23.7 24.5 24.7 25.0 24.5 38.8 Since antitoxin. 1895 1896 1897 21.2 18.3 23.3 41.5 19.9 17.7 21.3 39.9 17.4 14.9 20.1 51.4 Goodall also shows the case mortality of diphtheria treated in the hospitals of the Metropolitan Asylums' Board, as follows: Table I. 1892. 1893. 1894. 1895. 1896. 29.5 30.4 29.2 22.8 21.2 " Later years contain larger number of adults." 1897. 17.6 Table II. — Mortality in children under five years of age. 1892. 1893. 1894. 1895. 1896. 1897. 51.5 53.3 43.9 39.5 30.3 24.9 " Including fatalities from other diseases combined with or following diphtheria." The annual reports on the work of the Metropolitan Asylums' Board for the year 1903 show that the Board received during the year notifica- tions of 7582 cases of diphtheria; of these 5072 were treated in the hospitals, with a death rate of only 9.6 per cent. The average death rates in the Board's hospitals in quinquennial periods since the year 1887 are as follows: 1887 to 1891. 33.6 per cent. 1S92 to 1896. 25.5 per cent. 1897 to 1901. 13.7 per cent. 1902 and 1903. 10.4 per cent. According to a pamphlet issued by the authorities of the Institute for Infectious Diseases, of Japan, the serum treatment of diphtheria has affected the statistics of this disease in that country as follows: Previous to the sale of serum the average death rate of diphtheria patients was 50 per cent.; but since the sale began it has gradually decreased to 38 per cent, in 1896, 36 per cent, in 1897, and finally as low as 28 per cent, in 1902.^ Most of the statistics collected in this country are equally positive as showing the value of antitoxin in the treatment of diphtheria. The 1 British Medical Journal, 1899, vol. i. p. 197. 2 It is surprising to note in this pamphlet that, while the death rate from diphtheria in Japan has been greatly reduced since the advent of antitoxin, there has been a large increase of both cases and deaths annually, Till': ^i<:uiiM Tui:ATMiii'irriih:niA 747 comparative mortality from this disease in (^liiea^o, l)cJV>n' and aft<'r the introchietion of tlie serum treatment, as shfjwn in tlic linllcliit of February 13, 1004, of the Health I)<'[)artment of that eity, is as follows: During the preantitoxin period the deaths amujally J)er 10,000 of population were 12.4r) j)er cent., while since the serum has been uscfj the ratio of deaths has been reduced to 4.55 per cent. 'J'hc increase of population amounts to 52 per cent.; the decrease of diphth(;ria deaths, 63.4 per cent. Between ()ctol)er 5, 1895 (date of first case treated) and December 31, 1003, th(> Tlealtli Department treated 7435 ca.ses of bacterially verified (Jiphtheria, of which number 470 died, yielding a death rate of 6.44 per cent. It is stated that the average mortality without antitoxin still remains about 35 per cent. We are indebted to Dr. J. H. McC-ollom, of Boston, for the following table, showing the ratio of m()rl)idity and of the mortality of diy)htheria in Boston, per 10,000 of population, for ten years — 1S04 to 1003 inclusive: ^, , ^. „ Ratio of T^ ^u Ratio of Years. Population. Cases. ,.,., Deaths. _ . ,» , morbidity. mortality. 1894 .... 4«6,830 3019 61.01 878 18.03 189.5 .... 501,083 4059 81.00 654 11.73 1896 .... 516,305 4489 86.94 572 9.80 1897 .... 528,912 3398 64.24 -456 7.77 1898 .... £41,827 1661 30.65 185 3.15 1899 .... 555,057 2836 51.08 304 4.99 1900 .... 560,892 4977 88.73 537 9.57 1901 .... 573,579 3319 57.86 353 6.15 1902 .... 588,741 1940 34.72 225 3.82 1903 .... 600,929 2091 34.79 211 3.51 McCollom says the South Department Hospital of Boston was opened for patients September, 1895, and antitoxin has been given to every case of diphtheria admitted. In 1896 he published the following table, which shows the number of patients, by ages, admitted to the hospital from September 1, 1895, to May, 1896, together with the mortaUty rate in each age period: Age. Cases. Deaths. Mortality per ct. Under 1 year 17 3 17.64 1 to 2 years 74 20 27.02 2 " 3 " 136 37 27.2 3 " 5 " 329 55 16.71 5 " 10 " 410 39 9.51 10 " 20 " 189 9 4.76 20 years aud upward 206 7 3.38 1359 170 12.5 In presenting these statistics McCollom says that from February, 1891, until February, 1894, there were 1062 cases of diplitheria, with 493 deaths — a death rate of 46.42 per cent. The cases treated in the South Department Hospital, Boston, since the introduction of antitoxin have vielded the following annual mortalitv : 748 DIPHTHERIA Year. Cases. Deaths. Mortality per ct. 1895 844 96 11.37 1896 1,779 276 15.54 1897 1,291 181 14.02 1898 : 892 103 11.54 1899 . 1,672 180 10.78 1900 ? . . « . . ' . . 2,600 294 11.3 1901 ' . . 1,448 172 11.87 1902 1,018 103 10.11 Total 11,544 1405 12.17 In an interesting^ paper detailing the results, of antitoxin in New York City in 1902, by Dr. J. S. Billings, Jr./ the following diagram appears: TABLE SHOWING DEATH RATE PER (0,000 FROM DIPTHERIA IN THE BOROUGHS OF MANHATTNaN and the BRONX FROM 1888 TO 1902 YEAR 64 1888 89 90 91 92 93 94 95 9fi 97 98 99 1900 01 20 18 GO 17 S 50 \, 16 52 >- 48 ^44 < H 40 a: 1 36 UJ 32 en < 28 ^^ 24 20 IG 12 \ 15 o 14 § o 13 -- tc 12 u. 11 UJ 1- 10 < 9 I 1- 82 7^^ 6 \ A z \ / / \ \s 4 \< \ / \ K' N LU \^ V ^ ID K > \ o \, 3 \ \ O K \ z V- -^ Y^ ^ -^ ^ 6^ Lv \ 8 4. DOTTED. --CASE MORTALITY SOLID DEATH RATE l^his diagram shows in a very striking manner how greatly the mor- tality from diphtheria in New York City has diminished since the introduction of the serum treatment. After presenting considerable statistical evidence, Billings concludes his paper by saying: "There is no longer any doubt as to the curative action of antitoxin in diphtheria. Of 15,792 cases injected with anti- toxin furnished free of charge by the Department of Health or by its inspectors, 1860 died, a case fatality of 11.8 per cent. If the cases moribund when injected (722 in number) are deducted the case mortality is further reduced to 7.5 per cent." 1 New York Medical Journal and Philadelphia Medical Journal, December 12, 1903. Tiii<: si'Ua/M Tui<:ATMierio(J. We are infiennox Hrowne he found that paralysis was more common than in ])revious years when antitoxin was not employed. Goodall,^ of Ivondon, lias shown that paralysis became more frcfjuent in the Metropolitan Asylums' Board hospitals after the introduction of antitoxin. He presents the following table showing the percentage inci- dence of paralysis in the Board's hospitals from 1S9.3 to 1897, inclusive: Non-antitoxin. 1893. 1894. 189.i. Antitoxin. 1896 1897. Eastern Hospital . . 12.1 10.8 16.0 21.4 15.1 Northwestern Hospital . 14.0 11.1 18.9 14.1 12.8 Western Hospital . . 18.1 8.2 17.7 21.5 11.0 Southwestern Hospital . 14.3 18.3 22.0 20.6 20.5 Southeastern Hospital . . 16.2 20 2 34.7 42.3 45.9 Total. . 14.3 13.2 20.1 21.3 20.3 Alleged III Effects of Antitoxin. — In the vast majority of cases no immediate ill effects are noticeable. An abscess at the site of the injection may occur, but this is preventable. Many observers believe that antitoxin has increased the incidence of nephritis. It does seem that albuminuria is more frequently seen now then formerly. Referring to the results in his 1000 cases of diph- theria, Lennox Browne says his figures show a very considerable and undoubted increase in the proportion of cases of nephritis under serum treatment as compared with the old. Speaking of Baginsky 's experience to the contrary, he remarks: "It is only fair to quote the experience of Professor Baginsky. . . . On a comparison of 993 cases without serum and 525 with serum, he has come to the conclusion that the injection of serum does not increase the frequency of nephritis. gi\ing tables in support of his contention. This observer is careful to give separate and widely different figures for clinical nephritis, as distin- guished from that observed post-mortem." Hansemann, Washbourn, Goodall, and T>ennox Browne have noted the liability to anuria under serum treatment. The last-named writer says he was particularly unfortunate in his own early experience in this respect, as 6 out of a series of S patients died Avith anuria as the most prominent symptom. R. W. Marsden," of London, believes that the early use of antitoxin 1 British Medical Journal, 1S99, p. 197. s Ibid., 1900, vol. ii. p. 65S. 4S 754 DIPHTHERIA lessens the liability to albuminuria, and that when it appears late in diphtheria it may be due to antitoxin. He says that "though it may have an irritant effect upon the kidneys, yet this is by no means the rule, and in any case its action is only temporary." Winters/ of New York, one of the attending physicians to the Willard Parker Hospital, believes that pneumonia in diphtheria has become mo]*e frequent since the employment of the serum treatment. He says that "the pneumonia of the antitoxin cases of diphtheria differed from the pneumonia we were in the habit of seeing in diphtheria; that it was a totally different disease from that' seen before in the course of diph- theria; that it occurred as a sequela and not as a complication." He regards it as septic in character. In an earlier part of this article we called attention to the frequency of bronchopneumonia in the laryngeal form of diphtheria, and expressed the belief that it resulted from diphtheritic involvement of the respiratory tract. It is true that bronchopneumonia often occurs late in the disease, and. even at times during convalescence from the faucial form of diph- theria, but we have never felt that it was due to the serum treatment. Before concluding it may be well to mention the fact that more than one death has been reported as immediately following the injection of the serum. This accident has been almost entirely confined to the use of the serum for immunizing purposes. While no very satisfactory explanation has been given for the occurrence of these sudden deaths, it is not believed that they were caused by the serum fer se. The only ill effect which we are able to attribute to antitoxin with any degree of certainty is a peculiar exanthem, often attended with rise of temperature and more or less joint pains. Antitoxin Eruptions. Frequency. — The use of antitoxic serum in diphtheria is followed, in a certain proportion of cases, by a train of phenomena, the most conspicuous of which is the development of a cutaneous eruption. The proportion of cases in which antitoxin rashes develop is most variable. Hartung has collected from the literature a series of 2661 injections, of which 294, or 11.4 per cent., developed rashes. 253 of these eruptions are accounted for in the following table: Eruptions. Injections. Per cent. Heubner (Berlin cases) 54 298 ]8.1 Heubner ........ 22 77 28,5 Baginsky 49 525 9.3 Soltmann 5 89 5.6 V. Ranke 5 118 4 2. Seitz |20 140 14.3 I 4 180 2.22 Forster 7 73 4 9.6 Schucolty 4 38 10.5 Gunther 3 33 9.0 Bokai ;il 120 9.1 < 30 147 20.4 Moizard, Paris 33 231 14 2 Risel, Halle 6 114 5.2 253 22S-3 11.08 1 Medical Record, June 20, 1896. Rflsh. Percent. 18 17 ■23 2.'} 19 33 22 33 77//'; SI'Jh'f/M rUI'JATMMNT Of DI I'llTII IIRI A 755 The Imperial Board of Health of Germany reports 4358 cases of diphtheria injeeted with seru?n from January to July, 1805, with the production ol" 354 rashes, or 8.1 per cent. Among 7S cas(\s of diphtheria treated in the Scarlet P'ever and I)ij)h- theria Hospital of New York, in lOOl, rashes occurred in 25.4 per cent. The Investigating Committee of the Clinical Society of London collected records of 663 cases; 220 of these, or 33.1 per cent., develf>ped antitoxin rashes. liCnnox Brown(^^ noted 38 eruptions in UK) cases. Herg^ gives the follmv- ing figures for the Willard Parker llos})ital of New Yoi-k for four months : Canes. May 107 June 103 July 02 August . , fi5 Total 337 «2 24 The great variability in the frequency with which antitoxin eruptions develop may be best appreciated when it is stated that Monti, of \^ienna, observed rashes in 52 per cent, of one of his series of cases, whereas Hager did not observe a rash in a single instance among 61 cases. In our own experience an eruption has developed in about 20 per cent, of the cases injected. Date of Appearance of Eruption. — The rash may appear in from one day to one month after the injection of the serum. The subjoined table will show the day of occurrence of 120 antitoxin eruptions observed by us in the Municipal Hospital of Philadelphia. It will be seen that the greatest number of rashes occurred upon the sixth, seventh, and eighth days after the administration of the serum. Indeed, by actual computation over 49 per cent, of the total number appeared on these days. The date of appearance of the rash depends much upon the particular serum employed. A few years ago we used a serum the rashes from which quite uniformly appeared about the end of fourteen days. Days upon which Antitoxin Eruptions Developed in 120 of Our Cases. Eash appeared in 1 case on the second day after the serum injection. 6 cases fourth 6 " fifth 18 " sixth 17 " seventh 24 " eighth 5 " ninth 7 " tenth 5 " eleventh 7 *• twelfth 5 " thirteenth 5 " " fourteenth 1 case ■' fifteenth 8 cases sixteenth 3 " seventeenth 1 case eighteenth 1 ■' twentieth 1 Diphtheria and its Associates, London, 1S95. - New York Medical Record, 1S9S, pp. S65-S73. 756 DIPHTHERIA In the report of the Clinical Society of London, the largest number of rashes appeared from the seventh to the twelfth day; the figures are as follows: Day of Appearance of Antitoxin Eruptions. First to sixth day 33 cases. Seventh to twelfth day 147 " Thirteenth to eighteenth day 34 " Nineteenth to thirty-first day 6 " The rashes noted by I^ennox Browne appeared for the greater part from the seventh to the twelfth day. The statement is made by some writers that the scarlatinoid rashes are prone to occur early, in the neighborhood of the third day. We have seen some rashes of this character occur quite early. Character of the Eruption. — In our experience the vast majority of the rashes have been of an urticarial character, either made up of frank wheals or consisting of an urticarial erythema. Next in frequency have been the rashes belonging to the class of polymorphous erythema. These may consist of irregular marginated and non-elevated patches of redness, or may show a distinct tendency to annular or gyrate con- figuration. It is not uncommon to see an erythema made up of small, round, red patches with perfectly pale centres. In other cases the erythema may be of the scarlatinoid type and bear a close resemblance to the exanthem of scarlet fever. These appear to have occurred much more frequently in New York City than in Philadelphia. In other cases the rash may be a morbilliform erythema, looking not unlike the eruption of measles. Vesicular and bullous eruptions are quite uncommon; but we have observed one well-pronounced case, which is shown in the accompanying photographs. We have also observed a case in which there was extravasation of blood into the vesicles. Purpuric antitoxin eruptions are not very frequent, for of many hundreds of rashes that have occurred in the Municipal Hospital we have seen not more than eight or ten characterized by hemorrhage into the skin. Antitoxin eruptions are frequently polymorphous, exhibiting wheals, patches of non-elevated erythema, and occasionally papules and vesicles. Mixed urticarial and erythematous lesions are frequently obserA'ed. Indeed, all of the lesions which may occur in erythema multiforme may be present in the rashes following serum injections. Most of the rashes are accompanied by severe itching; this is particularly complained of by adults, who are, perhaps, better able to give expression to their discomfort. (Edema of the skin is commonly noted in association with antitoxin rashes. The face is puffed, particularly about the eyelids, and not infrequently the penis, scrotum, and feet are oedematous. Among the 220 rashes recorded by the Clinical Society of London, 161 were erythematous, 37 were urticarial, 17 were mixed, and 5 were petechial; 2 of the 5 petechial cases died. Of 33 rashes noted by Moizard, PI. ATI: LX. An Unusual Antitoxin Eruption exhibiting Erythematous Patches on the Trunk and Vesicular Lesions on the Face. PLATR I.XI, The Saine Patient as Plate LX. , showing the Vesicular Character of the Lesions on the Face. THE SI'JIiUM TREATMENT OF hi I'llTII l-llll A 757 14 were urticarial, .sciirlaliiiiforin cin l,liciii;i, !) polymorplioiis erythema, and 1 purpura. DiS'i'iuiuri'ioN. 'Ilic (lisli-ihiilioii of tlic ii of the culaiieous surfaee. It is noted with particular frequency about the arms, lej^s, and huttock.s, although the trunk is scarcely less commonly atta(;ked. The face often escapes, but by no means always. The most frecjuent region for the ajjpearance of the rash is the site of the injection. It is quite common for an erythematous or nrtiearial eruption to appear about the cutaneous puncture and the surrounding skin within twenty-four hours after the injection; this frequently dis- appears only to return some days later as the herald of the general eruption. Among the 220 antitoxin rashes recorded by the C'linieal Society of London, 40 were first seen at the site of the injecticMi. The eruption may consist of but a few scattered patches, or it may be so profuse as to involve the greater part of the cutaneous surface. The eruption ordinarily persists for about forty-eight hours, although in some cases it may last three, four, or five days. The purpuric rashes continue much longer. Occasionally the rash will begin to fade and almost disappear, and then in twenty-four or forty-eight hours reappear. Recurrent Rashes. — The eruption following the use of diplitlieria antitoxin is occasionally subject to recurrence. The rash may disappear and return in a few days or several weeks afterward. Among 134 rashes observed by us within a year and a half, there were 14 recurrent rashes. The earliest relapse occurred three days after the first eruption and the latest seventeen days. There is sometimes more than one re- currence. The GHnical Society of London reports 11 recurrent rashes among 220 eruptions collected. The following table gives the day of appearance and of recurrence of the cases observed by us: Eecurrent Antitoxin Eruptions. Primary rash appeared in : 1 case 7 days after serum injection, and again 3 days later. " " " " " 5 " " " " " ■' " ]" " " " •' " 4 " " 14 " 4 .. ' 7 ' 4 ' 7 ' 6 ' 10 '■' 6 " 8 ' 8 ' 8 ' 6 ' 10 ' 6 ' 6 Total 14 Constitutional Symptoms. — Antitoxin rashes are commonly accom- panied by constitutional disturbance of a more or less pronounced character. In the majority of cases there is elevation of temperature 758 DIPHTHERIA with its usual concomitant symptoms. The pyrexia is extremely variable ; in some cases there may be hyperpyrexia. We have occasionally observed temperatures in children of 104° and 105° F. More commonly the fever does not rise above 101° or 102° F. In the 220 rashes reported by the Chnical Society of London, fever accompanied the eruption in 136 of them. The fever lasts ordinarily from twenty-four to seventy-two hours, although it may persist longer. It declines, as a rule, with the subsidence of the rash. Headache is commonly associated with the fever and a variable amount of prostration is present. In some cases the prostration is quite pronounced. Vomiting occurs occasionally in children, and now and then there is diarrhoea. Where the temperature is high delirium is said to occur (Sevestre and Martin). We have not observed delirium in any of our cases. A very commou symptom accompanying the antitoxin rash is pain in the joints; adults often bitterly complain of this arthralgia. Articular swelling is noted in a certain proportion of cases. The wrists, elbows, shoulders, knees, and ankles are the joints most commonly attacked. The swelling usually subsides in a few days. The Clinical Society of London reports arthropathies 40 times among 663 cases of diphtheria; in 35 of these cases the joint symptoms accom- panied the antitoxin eruption. Causation of the Serum Phenomena. — The phenomena which develop in a certain proportion of cases after the administration of antidiph- theritic serum are without doubt dependent upon something which is contained in the injected fluid. Inhere is strong reason to believe that the antitoxic principle itself has little or nothing to do with the eruption and other manifestations produced. It has been quite conclusively proven that plain horse serum when injected into individuals will produce eruptions of the character described in about the same pro- portion of persons as the diphtheria antitoxic serum. The serum of non-immunized horses was injected by Bertin into a number of children suffering from diphtheria with the development of rashes in a considerable proportion of them. Four children suffering from an ordinary sore throat were injected by Sevestre with serum of non-immunized horses, with the production of an erythema in each one. Johannsen,^ of Christiania, administered hypodermically 2 to 15 c.c. of pure blood serum from a healthy non-immunized horse to 23 persons free of diphtheria. The serum given to 19 of the individuals was filtered; 4 received unfiltered serum. A more or less generalized erythema developed in 12 of the 23 patients in from one to eleven days. The filtered serum produced less disturbance than the unfiltered. It has long been known that the injection into an animal of an alien or heterogeneous blood serum — i. e., a serum derived from an animal of another species — is followed by toxic symptoms. 1 Johannsen, Bertin, and Sevestre. Cited by Berg, loc. eit. THE SI'IRUM TRKATMl<:Nr Oh' Dl I'llTII FJUA 759 Rumno^ believes that the toxic vi^i^x-i of blood serum depends upon tli(; aetioii of sj)eciiil toxalbninins. Alexander Selinii(P is of the opinion that the toxie elVeet is (hie to the; action of the sohibh' fibrin ferment of OIK! l)lood sennn u])on the second ;mini;i,l. If Ehrlich's side-chain theory stands the test (A time it will pnjbably be found that the serum injected contains a substance which acts as an intermediary body. Herg, aft(M- using antitoxic serum filtered tliroiigh a T'liamberland filter, and comparing th(> results with unfiltered sennn, ef)nchided that filtered antitoxin is less likely to give rise to rashes. Park, of New York, is not convinced that this is actually so. The wide variability in the production of serum rashes Is doubtless due to two factors: 1. Individual susceptibihty or predisposition, and, 2, peculiarities in the blood serum of certain horses. There can be no question that the serum of some horses gives rise to a larger percentage of antitoxin rashes than that of others. Where the serum of an animal produces an unusually large num- ber of eruptions, that animal had better be given up as a source of antitoxin. Diagnosis of Serum Rashes. — It is often a matter of difficulty to dis- tinguish between an antitoxin eruption and the eruption of measles or scarlet fever, more particularly the latter. Secondary infection with scarlet-fever poison during the course of diphtheria is not an uncommon occurrence. When a scarlatiniform rash develops in a patient who has been given antidiphtheritic serum, the question arises. Is the rash the result of the serum, or is it an expression of scarlet fever? No more difficult problem in differential diagnosis arises than in these cases. The diagnosis may be easy when the scarlet-fever SMiiptoms are complete and well marked. When there is vomiting, rapid rise of temperature, an aggravation of the existing angina, a characteristic tongue, and an intense, diffuse, punctated rash, the nature of the phe- nomena may be readily divined. But when, as so often happens, there is moderate pyrexia (100° or 101° F.), and a diffuse rash of moderate intensity, the solution of the diagnostic problem is at times impossible. The difficulties are increased 'by reason of the fact that diphtheria patients suffer from an angina and from glandular enlargement, and the antitoxic serum may produce fever, a scarlatinoid rash, vomiting, and prostration. In our experience at the Municipal Hospital, scarlatinoid eruptions have formed but a very small percentage of the serum rashes. We have observed from time to time a large number of scarlatinoid rashes accompanied by more or less fever in the diphtheria wards, but we have regarded such cases as scarlet fever and have sent them to the "mixed ward" w^here cases of double infection with diphtheria and scarlet fever are treated. Although these wards always contain some well-pronounced cases of scarlet fever, the patients sent from the diph- ' Quoted by Berg, loc. cit. , - Ibid. 760 ' DIPHTHERIA theria wards with the scarlatinal rashes have rarely contracted scarlet fever. This experience has seemed to us to afl'ord confirmatory, though we admit not conclusive, evidence that the diagnosis was correct. In the city of New York scarlatiniform rashes after the injection of antitoxic serum seem to have been more common than in Philadel- phia, and within recent months, during which time there has been used, at the Philadelphia Municipal Hospital, the New York Board of Health serum, it has appeared to us that scarlatinoid rashes from the serum have been more frequent. The features Vvhich tend to indicate that the rash is of serum origin and not the exanthem of scarlet fever are: its development at about the proper time after the injection, the moderate grade of the accom- panying fever, the presence of severe itching, the absence of a recurrent angina and the scarlatinal tongue, the occurrence of joint pains or swellings, irregularity in the development or distribution of the rash, the brevity of its duration, and the absence of consecutive desquamation. It must be remembered, however, that all of these phenomena have but a relative value in the diagnosis and that in many cases, after due weighing of all the symptoms, the diagnosis remains obscure. Other observers of experience have recognized similar difficulties in diagnosis. CH A PTER X V. i)isiNFir, Embalming with strong solutions of foniialin or arsenic destroys all but the surface infection, and this may f)e treated with solutions of carbolic acid, (;orrosive snblimate, or formalin. Vehicles.- -Airdjulances, carringcs, street ears, and th(; like, an; best disinfected by running tiiem into a tightly closed ec^mpartirutnt which may be quickly filled with large quantities of strong formaldehyde gas. In a specially built structin-e of this kind satisfactory disinfection may be effected in an hour. Vehicles which can b(; tightly clf)sed may be thoroughly sprayed with a 5 to U) per cent, solution of fonnalin and the vapor allowed to act for about six hours.* * In preparing the above article tiie writers have consulted the excellent book on " Disinfection and Disinfectants," by Dr. M. J. Rosenau, Director of the Uygienic Laboratory and Passed Assisiant Surgeon U. S. Public Health and Marine Hospital Service. INDEX. Ar>l)()MINAL coiiiplicaXions in siiuili- pox, 287 Abortion in smallpox, 21G Abscesses in smallpox, 229 Accidental cowpox in man, 142 Actinomyces in va(!cine virus, 103 Adult chickenpox, 327 scarlet fever, 347 Aerial transmission of scarlet fever con- tagium, 357 of smallpox infection, 161 Age incidence in smallpox, 112 in measles prognosis, 530 Air transmission of smallpox infection, 161 Albuminuria in smallpox, 226 Alopecia after smallpox, 191 Altitude, influence of, on scarlet fever, 352 America, introduction of smallpox into, 147 of A'accination into, 25 Angina scarlatinosa, 390 Anginose scarlet fever, 382 Animal transmitted virus, 97 vaccination, 93 advantages of, 94 in America, 93 Anomalous measles, 497 Antipyrin eruptions and measles, diag- nosis of, 527 Antistreptococcus serum in scarlet fever, 474 Antitoxin of diphtheria, action of, 731 curative power of, 738 effect of, on local process, 735 limitations of, 736 prophylactic power of, 737 eruptions and measles, diagnosis of, 529 preparation of, 732 prophylactic influence of, in Munici- pal Hospital, 738 treatment of diphtheria, 730 unit, 732 An ti vaccination arguments, 114, 115, 119 Apepox, 143 Atmospheric conditions and smallpox, 156 transmission of smallpox infection, 161 Attack rate of smallpox, 120 BACrElMOLOGICAI. diagnosis <>i (liplitheria, 077 impurities of vaccinr-, virus, 102 Bacteriology of diphtheria, 612 of measles, 521 of scarlet fever, 430 of smallpox, 256 of tvphus fever, 572 Baths in smallpox, 299 lieaugency lymph, 92 Bed-sores in smallpox, 231 Bills of mortality, smallpox deaths, 109 Black smallpox, 204 Blattern, 145 Blood changes in chickenpox, 335 in diphtheria, 670 in scarlet fever, 436 in smallpox, 253 Boils after vaccination, S3 iu smallpox, 229 Bousquet's lymph, 92 Bovine lymph, 31 vaccination in America, 93 Bullous eruptions after vaccination, SO CALF-TRANSMITTED virus, 94, 97 Calf vaccination, 93 Camel, smallpox in, 143 Camp measles, 499 Carbuncles in smallpox, 230 Casual cowpox in man, 142 Chauveau's experiments with variolation, 88 Chemnitz smallpox statistics, 118 Chester smallpox statistics, 113 Chickenpox, 316 in adults, 327 blood in, 335 complications and sequelte of, 329 diagnosis of, 335 disseminated gangrene in, 330 eruptive stage of, 322 er3'sipelas complicating, 330 etiology of, 318 history of, 316 incubation period of, 320 nephritis in, 332 pathology of, 334 prodromal erythema, 322 prognosis of, 339 pyaemia complicating, 330 768 INDEX Chickenpox, scarring after, 326 second attacks of, 319 and smallpox coincident, 333 symptomatology of, 321 synovitis and arthritis in, 330 treatment of, 339 with other exanthematous diseases, 332 Chloral eruptions and measles, diagnosis of, 528 Clavelee, 135 Climate, influence of, on scarlet fever, 349 Cohasset lymph, 93 Coincident chickenpox and smallpox, 333 Comparative mortality rates of variola and varioloid, 278 Comparison of course of vaccinia with different virus, 96 Complications of chickenpox, 329 of diphtheria, 640 of measles, 501 of rubella, 561 of scarlet fever, 395 of smallpox, 229 of typhus fever, 583 of vaccination, 58 Compulsory vaccination law in Germany, 123 Confluent measles, 494 smallpox, 199 superficial, 212 Conjunctivitis in smallpox, 232 Contagious impetigo complicating vac- cination, 70 period of measles, 484 Contagiousness of desquamating epithe- lium in scarlet fever, 357, 462 Contraindication for vaccination, 32 Copaiba and cubebs eruptions and measles, diagnosis of, 529 Copeman and glycerinated lymph, 98 Corneal ulcer in smallpox, 233 Cowpox, 17 in cow, 142 Crede's ointment in scarlet fever, 469 Croup and diphtheria, diagnosis of, 674 meinbranovis, 633 Cutaneous gangrene in smallpox, 194 Cytoryctes variola^, 264 life cycle of, 265 of Guarnieri in vaccinia, 85 DEATH rate of smallpox among vac- cinated and un vaccinated, 117 Decline of smallpox after introduction of vaccination, 107 Decrustation in smallpox, 186 Definition of chickenpox, 316 of diphtheria, 598 of measles, 476 of rubella, 547 of scarlet fever, 341 of smallpox, 144 of typhus, 566 Delayed vaccination, 38 Delirium in smallpox, 182 ferox in smallpox, 182 Derivation of word smallpox, 144 variola, 144 Dermatitis bullosa after vaccination, 80 exfoliativa in smallpox, 196 herpetiformis after vaccination, 80 Desiccation in smallpox, 185 Deterioration of humanized virus, 95 Dewsbury smallpox statistics, 118 Desquamation, contagiousness of, in smallpox, 482 in measles, 497 in rubella, 556 in scarlet fever, 374 duration of, 376 Diagnosis of chickenpox, 335 and impetigo contagiosa, 338 and smallpox, 335 of diphtheria, 672 of measles, 523 of rubella, 562 of scarlet fever, 447 of smallpox, 266 and acne, 272 and acute gastritis, 268 and chickenpox, 269 and drug eruptions, 272 and eczema, 274 and glanders, 274 and impetigo contagiosa, 273 and la grippe, 267 and measles, 268 and meningitis, 267 and roseola vaccinosa, 272 and scarlet fever, 269 and syphihs, 270 and typhoid fever, 267 and typhus fever, 267 of typhus fever, 586 Diet and stimulants in smallpox, 301 Diphtheria, 598 age factor in prognosis of, 679 incidence, 611 albuminuria, 362 alleged ill-effects of antitoxin, 753 antitoxin in, action of, 731 alleged ill-effects of, 753 curative power of, 738 dosage, 733 effect of, on local process, 735 on paralysis, 753 eruptions, 754 fever with, 758 morbilliform, 756 recurrent, 757 scarlatinoid, 756 ill-effects of, 753 laryngeal form, 741 limitations of, 736 mode of administrating, 736 preparation of, 737 prophylactic power, 737 rashes, causation of, 754 date of appearance, 755 I NT) MX 7G0 I )i))liLli('ri!i,, ;i,nl.il,()\in niHlics, (li,'i,fi;ii(i.si.s of, fever in, 758 frequency of, 754 results in, 743 in (Jhicjimo, 750 iti .lap.'ui, 74() in l-lii' Mutiiciiwil Ho.spital in I'liiludclplii.'i, 749, 752 in N(W York (.'il.y, 7 IS, 751 in Willanl l';i.rk(',r Il().si)itiii, New York, 749, 751 treatment of, 730 unit 732 value of, 743 avirulent diphtheria bacilli, 616 bacilli of biolofrical characters of, 614 in blood and internal orj^ans, 617 distribution of, in body, 617 in lungs, 663 in lymph nodes, 668 in scarlet fever throats, 399 in throats of exposed persons, 619 of healthy persons, 618 persistence in the throat, 618 staining properties of, 613 types of, 613 virulence of, 616 bacillus, general infection with, 617 growth of, on bouillon, 615 on gelatin, 615 on glycerin agar, 615 on Loeffler's blood serum, 614 in milk, 615 on potatoes, 615 Neisser's stain of, 614 morphology of, 613 pathogenesis of, 615 bacteriological diagnosis of, 677 bacteriology of, 612 blood changes in, 670 in Boston City Hospital, mortality of laryngeal form, 743 results of antitoxin in, 747 bronchopneumonia in, 641 at autopsy, 661 bacteriology of, 662 catarrhal croup, diagnosis of, 674 causation of serum rashes, 758 changes in adrenal bodies, 670 in alimentary cjuial, 664 in blood, 670 in heart muscle, 660 in intestines, 665 in Iddneys, 667 in liver, 665 in lungs, 661 in lymph nodes, 668 in nervous s^'stem, 670 in panci'eas, 670 in pituitary bod}^ 670 I )iplil liiii;i, changes in pliiiml ni'-ni- branes, fi63 in salivary gl;i,nd.s, 670 in skeletal inuscles, 669 in Hpl(!en, (i64 in testicles, 670 in thymus gland, 669 in (liyroid glund, 670 in (Miicago, aniiloxiri n-sults in, 750 (4iroiiic stenosis of larynx in, 726 circulatory symptoms, 631 coni])licatirig scarlet fever, 397 corn})lications of kidneys, 667 of lung, 641 of lymph glands, 642 ol' scarlf^t fever, 644 Mild sequela; of, 540 conjiuictival, 626 constitutional predisposition to, 609 course of, 636 cultures of, for diagnosis, 677 ciitaneous, 627 definition of, 598 diagnosis of, 672 of serum rashes, 759 dissemination of infection, 607 duration of, 636 of membrane in throat, 740 ear inA^olvement in, 626 endocarditis in, 66 epistaxis in, 625 eruptions after antitoxin, 754 erythema in, 627 etiology of, 602 examination of cultures of, 678 exudate in, 624 location of, 658 of e3^es, 626 favorable cases of, 637 fever in, 630 folUcular tonsillitis, diagnosis of. 675 gangrenous pharj-ngitis, diagnosis of, 676 general paralysis in, 650 geographical distribution, 604 heart changes in, 660 failure in, 641 hemiplegia in, 647 hepatic changes in, 665 herpetic pharjTigitis, diagnosis of, 675 liistopathologv of membrane, 658 histoiy of, 598 indications for operati^•e interfer- ence, 715 infection in milk, 608 influence of domestic environment, 606 of race, 613 of rainfall, 605 of schools, 60S of season, 605 of sex, 611 isolation of well persons harboring baciUi of, 619 intubation in, 711^ 49 770 INDEX Diphtheria, intubation in, prolonged, 725 technique of, 715 in Japan, results of use of antitoxin, 746 kidney changes, 667 complications of, 642 laryngeal, 633 antitoxin in, 741 operative measures in, 711 leukocytosis in, 671 liver changes, 665 lobar pneumonia, 642 location of membrane, 658 Loeffler's solution as local applica- tion, 693 of methylene blue, 613 lung changes, 661 making of cultures of, 677 malignant type of, 638 measles complicating, 645 membrane in stomach, 664 mercurial applications in, 692 in Metropolitan Asylums' Board Hospitals of London, antitoxin results, 746 middle-ear involvement, 626 mild type of, 636 mortality of intubation cases in Wil- lard Parker Hospital, 742 in Mvmicipal Hospital, 743 of tracheotomized cases, 742 in Municipal Hospital of Philadel- phia, antitoxin results, 749, 752 mortality of intubation, 743 myocardial changes, 660 myocarditis, 660 nasal, 624 irrigations in, 697 treatment of, 697 nephritis in, 642, 667 nervous symptoms, 633 in New York City, antitoxin results in, 748, 751 of nose, 624 nose-bleed, 625 oedema in, 628 after antitoxin, 756 paralysis, 646 general, 650 incidence, 753 of cardiac and respiratory nerves, 649 of soft palate, 649 pathology of, 658 pericarditis in, 660 period of incubation in, 620 pleurisy in 642 prognosis, 678 prognostic significance of age, 679 of exudate, 682 of nasal involvement, 683 of paralysis, 686 of pulse, 685 of race, 682 of renal involvement, 686 Diphtheria, prognostic significance of sex, 681 of temperature, 684 of toxaemia, 684 pulse in, 631 rash in, 627 rashes of, 754 after antitoxin, 754 recurrence of, 640 recurrent attacks of, 610 in Russian Hospitals, antitoxin re- sults, 744 septic cases of, 638 variety of, 629 serum rashes in, 754 severe type, 636 site of infection in, 610 of skin, 627 smear preparation for diagnosis of, 677 statistical table of antitoxin results in Boston City Hospital, 747 in Chicago, 750 in Metropolitan Asylums' Board Hospitals, 746 in Municipal Hos- pital of Phil- adelphia, 749, 752 in Russian Hos- pitals, 744 in St. Petersburg, 745 in Willard Parker Hospital, 749 752 indicating duration of mem- brane in throat, 740 of date of appearance of antitoxin rashes, 755 of mortality from laryngeal form in Boston City Hospital, 743 from laryngeal form, 742 in tracheotomy, 742 of intubation in Muni- cipal Hospital, 743 in Willard Parker Hospital, 743 of recurrent antitoxin rashes, 757 of stomach, 664 St. Petersburg results of use of anti- toxin, 745 stomatitis, differential diagnosis of, 676 sj^mptomatology, 622 syphilitic sore throat, differential diagnosis of, 676 termination of, 636 throat appearances in, 622 tincture of the chloride of iron in, 700 IN/J/'JX 771 DipliUK^ri.'i,, loxiciiiiji, of, 628 tmclH'()(,()my ill, 727 iiidiciitioriH for, 71 I treatiiKMil, of, 0X7 nlcoliol ill, 705 iUi(.iH(\|)ti(t .Mnijlic'itions in, (HM of jLiinil, ()iW biciiluridc oT incnMiry in, 702 (■;ilnmcl in, 70;{ snMiin.'i.l ion in, 707 (•;uisU(! applic.'Uions in, 000 cliloratc, of potash in, (iOI oonstitiitioiijil, 700 digitalis in, 7or) ol' clijilit.iicril ic con jnncl i\i- tis, 099 emetics in ineinhnmoiis croup, 709 extubation, 733 technique of, 723 gargles in, value ol', 091 internal, 700 indications for, 700 irrigation in, 69(5 with saline solution, 698 intubation in, 718 dangers and difficulties of, 718 feeding after, 721 prolonged, 725 technique of, 715 lactic acid in, 695 of laryngeal form, 708 local, 690 Lfiefller's solutions in, 693 of membranous croup, 708 mercury in, 709 steam in, 709 mercurial applications in, 692 of ocular, 699 operative, indications for, 715 measin-es in laryngeal form, 711 of paralysis, 707 potassium chlorate in, 703 preventive, 687 removal of intubation tube, 723 serum, 730 slaked lime in, 710 sodium benzoate in, 705 solvents of exudate, 694 spraj's in, 696 strychnine in, 705 tincture of the cliloride of iron in, 700 turpentine in, 704 whiskey in, 706 ulcerations from pressure of intuba- tion tubes, 726 urine in, 632, 642 in ^^'illard Parker Hospital, mortal- ity in intubation, 742 results of antitoxin, 749, 751 with scarlet fe\-er, 644 with measles, 645 DiphthrTitic [jaralyHis, 610 Disinlcction, 761 of bcr|(lin(r, 761 of books, 761 of cadaverw, 764 of (:arj)ets, 764 of letters, 764 of money, 764 prcp.'ir.'ition of room for, 761 in sin.'illpox, 285 by spniying with loriiialin w>liitinris, 762 with paraforni pastils, 763 with sulphur dioxide, 763 of v(4iicl(;s, 765 Dissenting views as to air transmission of smallpox infection, 164 Domestic animals, tran.«mission of small- pox inf(!ction by, 165 EAR complications in smallpox, 235 Eaux aux Jambes, 138 Eczema following vaccination, 79 Effect of glycerin on bacteria, 101 Egyptian plague, 145 En anthem of measles, 489 of scarlet fever, 373 of smallpox, 180 Equination, 140 Equine variola, 138 Eruption of measles, 493 Eruptive stage of smallpox, 173 Erysipelas comphcating smallpox, 230 after vaccination, 72 Erythema multiforme complicating vac- cinia, 70 scarlatini forme in smallpox, 196 scarlatinoides, 419 Etiology of chickenpox, 318 of diphtheria, 602 of measles, 478 of rubella, 549 of scarlet fever, 344 of smallpox, 150 of tA'phus fever, 568 Exceptionally mild smallpox, 206 Exfoliative dermatitis in smallpox, 196 Extubation in diphtheria, 723 Eye complications of variola, 231 FALSE vaccination, 42, 49 Favorable s^•mptoms in smallpox. 281 ■ FeA'er in measles, 489 in scarlet fever, 366 in smallpox, 183 First vaccination of .Tenner, 91 Foetus, smallpox in, 221 Formalin, 761 Formaldehyde disinfection. 761 effects of. on vennin. 761 French and German Armv, smallpox sta- tistics. 121 French measles. See Rubella, 547 Furunculosis after vaccination, S3 772 INDEX GAIjBIATI and animal vaccination, 93 Gangrene, in scarlet fever, 422 in vaccination, 67 of skin in smallpox, 194, 231 Gangrenous angina in scarlet fever, 396 Generalized vaccinia, 60 German compulsory vaccination laws, 123 and French army smallpox statis- tics, 121 German measles. See Rubella, 547 vaccination commission, 123 Germicidal action of glycerin, 100 value of glycerin in lymph, 98 Glossitis variolosa, 181 Gloucester smallpox statistics, 118 Glycerin, effects of, on bacteria, 101 germicidal action of, 100 Glycerinated lymph, 97 advantages of, 101 duration of activity of, 105 preparation of, 103 value of, 98 Goat pox, 138 Golden rule of vaccination, 28, 31 Grease, 138 Guarnieri's bodies, 263 in vaccine lesions, 85 HEART complications in smallpox, 236 Heifer vaccination, 93 Hemorrhagic measles, 499 scarlet fever, 387 smallpox, 202 pathological changes in, 251 typhus fever, 585 vaccinia, 63 varioloid, 206 History of chickenpox, 316 of dijjhtheria, 598 of measles, 476 of rubella, 547 of scarlet fever, 341 of smallpox, 144 of typhus fever, 566 Histology of skin in smallpox, 242 of vaccine lesions, 83 Hornpox, 213 Horsepox, 138 Human equination, 140 ovination, 138 smallpox from material from vario- lated cows, 89 Humanized virus, 30 deterioration of, 95 Hygiene of vaccination, 30 ILLNESS, initial, of smallpox, 167 Iodine used locally in smallpox, 311 Impetigo contagiosa complicating vac- cination, 70 varicellosa, 325, 330 variolosa, 192 Immunity of vaccinated physicians and nurses against smallpox, 127 Incubation period of chickenpox, 320 of diphtheria, 620 of measles, 487 of rubella, 550 of scarlet fever, 363 of smallpox, 166 of typhus, 575 Infected articles, persistence of smallpox poison, 160 Infection of smallpox, 157 carried in garments, 160 transmitted in the air, 161 Infectious period of smallpox, 157 Infectiousness of blood in smallpox, 255 Infectivity, period of, in scarlet fever, 355 Initial stage of smallpox, 167 Inoculation, 148 declared illegal, J 15 with ovine lymph, 138 practice of, in England, 114 of smallpox in America, 25 and smallpox prevalence, 114 Inoculated smallpox, 214 Inoculability of measles, 478 of scarlatinal virus, 354 of varicellous fluid, 319 Insanity after smallpox, 237 after typhus fever, 584 Insects, transmission of smallpox infec- tion by, 165 Institution epidemics of measles, 531 Insusceptibility to smallpox, 150 to vaccination, 43 Intrauterine smallpox, 222 Intubation in diphtheria, 711 dangers and difficulties of, 718 instruments, 712 prolonged, 725 treatment and feeding after, 721 Invasive stage of measles, 488 Involution of eruption in smallpox, 185 Iritis in smallpox, 235 Irregularity in measles eruption, 500 in scarlet fever, 388 Itching in smallpox, 189 Isolation in scarlet fever, 461 of smallpox patients, duration of, 287 JAIL fever. See Typhus, 566. Jefferson's letter to Jenner, 133 Jefferson, Thomas, and vaccination, 28 Jenner, Edward, 17 Jefferson's letter to, 133 on relation of cowpox to smallpox, 90 Jenner's first vaccination, 91 Joint disease in smallpox, 237 KINEPOX, 17 Kindpocken, 112 Kilinarnock smallpox st^-tistics, 113 INDEX 773 Klcihs-T/Ocmcr h.-utilliis, discovrTy of, 502 KopliU'.M spol.s in incjislcs, 'lOl (liiif^iio.sMc v.'iliK' of, r)2.'i Kiili|)i)ck('n, 17 LA I'ETITE VEROI.E, Ur, Lady Montague and inoculalion, 148 Laryngeal dipliihoria, 033 Jioiwislcr smallpox statistirn, IIK, 1 H), 121 Leprosy after vaccination, 70 Leidvocytosis in scarlet fever, 137 Fjoeal irealnient of sniall|)ox, :i(J() Jjoelller's solution of methylene blue, 613 Long humanized virus, 07 Lord Ma(^aulay on the ravages of small- pox, 147 Louis XV. attacks of smallpox, 152 liupus vulgaris after vaccination, 78 Lymphatic glands in scarlet fever, 378 Lymph, glycerinated, 07 advantages of, 101 natural sources of, 91 preparation of, 103 Lyons Commission on variolation oi' cows, 88 MACAULAY, on the ravages of small- pox, 147 Malignant measles, 499 scarlet fever, 385 Marseilles smallpox statistics, 118 Martin's lymph, 93 Measles, 476 in adults, 482 age incidence, 481 albuminuria in, 512 anomalous cases of, 497 aphthous stomatitis in, 505 bacteriology of, 521 blood changes in, 520 bronchopneumonia in, 503 bullous eruptions in, 508 camp, 499 cancrum oris in, 512 capillar}^ bronchitis, 503 changes in blood in, 520 in the liver in, 520 in lungs in, 520 in lymphatic glands in, 520 in nmcous membranes in, 519 in skin in, 518 in spleen in, 520 character of epidemic and prognosis of, 532 chorea after, 508 climate and prognosis of, 533 complications of, 501 alunentary tract, 505 ear, 510 eye, 509 glandular, 512 heart, 511 Measles, compliraf ions of, kidney, 511 laryngeal, 501 lung, 502 nervous, 506 skin, 508 confluent, 494 contagious period, 484 deaf-mutism and, 51 1 desquamatif)n, 497 drug eniptions, differential diaiBfnoHiB of, 527 diagnosis of, 523 diarrluea in, 506 disseminated sclerosis in, 507 eczema after, 509 effect of, on chronic disea.sf^s, 519 season on, 483 exanthem, 489 endocarditis in, 511 epidemics of, 482 in institutions, 531 eruption in, 493 hemorrhagic, 499 irregularity of, 500 presence of papules, 494 of vesicles, 494 eruptive period of, 493 erythema nodosum after, 509 etiology of, 478 fever in, 489 gangrene of lungs in, 505 of skin in, 508 gangrenous stomatitis in, 512 hemorrhagic, 499 herpes facialis in, 508 history of, 476 incubation period of, 487 influenza, differential diagnosis of, 525 inoculabihty of, 478 insanity after, 506 isolation of, 537 utility of, 538 KopUk's spots, 490 lobar pneumonia in, 504 malignant form of, 499 membranous laryngitis in, 502 meningitis in, 508 mental disorders in, 506 mild form of, 497 type of, 498 mode of contagion, 479 morbilhform erythemata, differential diagnosis of, 527 noma in, 512 notification of, 536 paralysis after. 507 pathology of, 518 pericarditis in, 511 pigmentation in, 496 pleuris}-, 504 post-rubeoUc rashes in, 501 pre-eruptive rashes. 492 pregnant women. 517 pre\-ious health of patient and prog- nosis of, 532 774 INDEX Measles, prodromal or invasive stage of, 488 prognosis of, 529 prophylaxis of, 535 pulmonary tuberculosis after, 504 purpura- in, 512 recession of rash, 501 relapses in, 486 rubella, differential diagnosis of, 524 scarlet fever, differential diagnosis of, 524 season and prognosis of, 533 smallpox, differential diagnosis of, 525 susceptibility, 480 symptomatology, 487 favorable, 535 unfavorable, 535 syphilis, differential diagnosis of, 527 third attacks, 486 treatment of 535 of bronchopneumonia in, 544 of cancrum oris in, 543 of complications in, 542 of conjunctivitis in, 543 of itching in, 542 of laryngitis in, 543 of nose-bleed in, 543 of otitis in, 545 temporary immunity, 481 tuberculosis cutis after, 509 typhoid form, 499 typhus fever, differential diagnosis of, 526 ulcerative stomatitis in, 505 urticaria in, 508 vulvitis in, 512 with other infections, 518 without catarrhal symptoms, 497 without eruption, 498 fever, 497 Membranous angina in scarlet fever, 396 croup, 633 Mild measles, 497 type of smallpox, 206 Miliary vesicles in scarlet fever, 370 Milk, scarlet fever, infection in, 357 Miscarriage in smallpox, 216 Mitigated smallpox, 209 Modified smallpox, 209 Monkey, smallpox in, 143 Montague, Lady, and inoculation, 148 Montreal epidemic of smallpox, 159 Morbid anatomy of scarlet fever, 439 Morbilli confluentes, 494. See measles, 476 hemorrhagic, 495 Iseves, 494 miliaris, 494 papulosi, 494 vesiculosi, 494 Morphine in smallpox, 298 Mortality of smallpox in the prevaccina- tion period, 275 Mucous membrane eruption in smallpox, 180 Multiform erythema after vaccination, 70 NATURAL cowpox in cow, 142 Negri and animal vaccination, 93 Negroes, smallpox in, 154, 276 Neisser's stain for the diphtheria bacillus, 614 Nervous complications of measles, 506 in smallpox, 237 Noma in scarlet fever, 422 OCULAR complications of variola, 231 (Edema of glottis in smallpox, 181 Orchitis in smallpox, 237 Otitis media in scarlet fever, 400 in smallpox, 235 Ovination, 137 human, 138 PALMAR lesions in smallpox, 187 Paraform disinfection, 763 Paralysis in smallpox, 238 Paraplegia in smallpox, 239 Passy lymph, 92 Pathology of chickenpox, 334 of diphtheria, 658 of measles, 518 of scarlet fever, 436 of smallpox, 242 of typhus fever, 573 Pathological changes in hemorrhagic smallpox, 251 Pearson's lymph, 91 Pemphigus after vaccination, 80 Period of incubation of chickenpox, 320 of diphtheria, 620 of measles, 487 of rubella, 550 of scarlet fever, 363 of smallpox, 166 of typhus fever, 575 Petechial fever. See Tj^phus, 566. Phimosis in smallpox, 237 Phlebitis after smallpox, 237 Pigmentation after measles, 495 after smallpox, 190 Plantar lesions in smallpox, 187 Pleurisy in smallpox, 236 Pneumonia in smallpox, 236 Pock diseases of lower animals, 135 Pocken, 145 Postrubeolic rashes, 501 Postvaccinal lupus vulgaris, 78 Postvariolous rashes, 196 Prague, effect of introduction of vaccina- tion in, 107 Precocious vaccinia, 41 Pre-eruptive rashes in measles, 492 Pregnancy, influence of, in scarlet fever 359 Pregnant women, smallpox in, 215 Prevention of pitting in smallpox, 308 Prodromal erythema in chickenpox, 322 rashes in smallpox, 171 stage of smallpox, 167 iNi)i<:x 77r, l^r()f!;ru)His ol' cliiclu'ripox, XV.) of (li|)li( licria,, ()7X of mcMslcs, 520 (if fiilicll.'i,, r>(')\ of sciiJ-lcl. f(tvcr, •If)? of siii;i,lli)()X, 27r) of I yplms f(!vcr, 589 I'fopliyliixi.s of nitiiiIli)ox, 2 fc^vcr, I'A'.i in Viifiola .'uid vaccinia, 2(12 l's(Mi(lo(li|)litJicr'ia, ()r)2 bacilli, ()l!) coinnuinicabilily <>f, 0.^;^ (liiiSnosis of, <)75 Ij-calmcnl. of, (ir)7 Psoudokcloidal fj;rowths after sniaIli)ox, 2:^0 Psoriasis after vaccination, 82 i'lKM'pcral scarlet fcvor, 359 I'uerperium, influence of, in scarlet fever, 359 Purpura hemorrhagica in scarlet fever. 420 variolosa, 203 Pustular hemorrhagic variola, 205 J'ya^mia after vaccination, 64 in smallpox, 241 QUARANTINE in scarlet fever, 461 in smallpox, 283 Quinine eruptions and measles, diagnosis of, 528 RACE, influence of, on scarlet fever, 353 Raspberry tongue in scarlet fever, 374 Recurrent eruptions in scarlet fever, 393 smallpox, 151 Red light treatment of smallpox, 304 Relapse in rubella, 562 Relation of horsepox to cowpox, 139 Relationship of cowpox to smallpox, 87 of vaccinia to smallpox, 87 Respiratory complications in smallpox, 236 Retained intubation tubes, 726 Retroequination, 142 Retrogression of eruption in smallpox, 185 Retrovaccination, 51 Revaccination, 45 statistics of, 120 Rhazes' description of smallpox, 145, 146 Roseola vaccinosa, 37, 68, 171 Rotheln. See Rubella, 547 Royalty, smallpox deaths among, 149 Rubella, 547 age, incidence of, 550 albuminuria in, 561 coincident with other diseases, 562 complications and sequela^ of, 561 cough in, 558 definition of, 547 desquamation in, 556 HubcMa, diagnosis ol', 562 diiratioii of isolation in, 565 of rash, 555 eruptions of, anomalous, 555 character of, 554 (Miology of, 549 f(!ver in, 557 history of, 557 hoarseness in, 558 influenza, dilfercntial diagnosis of, 561 it,cliiiig in, 559 lymphatic glands, 559 measles, differential diagnosis of, 562 nausea and vomiting in, 559 period of eruption in, 552 of incubation in, 550 of invasion in, 551 prognosis of, 564 pulse and respiration in, 559 relapses in, 562 second attacks of, 562 scarlatinifonn variety^ of rash, 556 scarlet fever, differential diagnosis of, 564 sneezing in, 557 sore throat in, 558 symptomatology of, 550 synonyms of, 547 treatment of, 565 tongue in, 558 Rubeola. See Measles, 476 SACCO'S lymph, 92 Sanitation and vaccination in Glas- gow, 116 Scaling in scarlet fever, 374 Scarlatina. See Scarlet fever, 321 anginosa, 382 faucium, 390 hemorrhagica, 387 maligna, 385 miliaris, 370 papulosa, 370 pempliigoidea, 371 simplex, 365 sine angina, 392 eruptione, 390 exanthemate, 390 febre, 388 with desquamation, 392 vesicularis, 370 Scarlatinal infection, mode of reception, 355 rheumatism, 419 virus, inoculability of, 354 Scarlatinifonn erythema, 449 in smallpox, 196 Scarlet fever, 341 abscesses in, 425 of brain in. 403 in adults, 347 afebrile cases of, 368 age influencing prognosis, 45S 776 INDEX Scarlet fever amblyopia, 405 anginose form of, 382 antistreptococcus serum in, 474 and antitoxin rashes, 451 bacteriology of, 430 blebs in, 424 blood in, .436 bronchial catarrh in, 381 care of patients in, 465 changes in bone-marrow, 443 in gastrointestinal tract, 442 in heart, 443 in kidneys, 445 in liver, 442 in lungs, 445 in lymphatic system, 440 in skin, 439 in spleen, 441 in tongue, 440 chorea after, 430 choroiditis in, 405 circumoral pallor in, 372 complicated by diphtheria, 397 complications of, affecting ali- mentary canal, 425 bones, 429 nervous system, 428 the respiratory organs, 427 ear, 399 eye, 404 heart, 406 liver, 426 respiratory organs, 427 and sequelae,. 395 skin, 423 contagiousness of desquamating epithelium, 357 of scales, 462 contagium, aerial transmission of, 357 Credo's ointment in, 475 deafness after, 404 definition of, 341 dermatitis gangra;nosa in, 424 desquamation, 374, 448 diagnosis, 447 diagnostic value of desquama- tion, 448 of strawberry tongue, 448 diet, 465 diphtheria, differential diagnosis of, 454 bacilli in throat in, 399 disinfection, 465 dissemination of, in schools, 460 drug rashes, differential diag- nosis of, 453 duration of desquamation of, 376 of quarantine in, 461 eczenia after, 424 empyema in, 428 exanthem in, 373 Scarlet fever, endocarditis in, 406, 444 enteritis in, 426 etiology of, 341 facial palsy in, 403 family predisposition to, 349 fever in, 366 furuncles in, 425 gangrene in, 422 of neck .in, 385 gangrenous angina in, 396 hemiplegia in, 428 hemorrhagic, 387 hemorrhage from erosion of bloodvessels, 409 herpes in, 424 history of, 341 hot pack in, 472 hydrotherapy in, 467 hygiene of sick apartments in, 463 hyperpyrexia in, 368 hypodermoclysis in, 474 immunity and susceptibility to, 345 incubation period of, 363 infection in milk, 357 influence of pregnancy and puer- perium, 359 of race, 353 influenza, differential diagnosis of, 454 insanity after, 429 irregular, 388 isolation of, 460 itching in, 373 involvement of antrum of High- more in, 444 jaundice in, 426 keratitis i.n, 404 kidney changes in, 445 laryngitis in, 380 leukocytosis in, 437 lymphatic glands in, 378 malignant, 385 mastoid disease in, 403 measles, differential diagnosis of, 453 membranous angina in, 396 meningitis in, 403, 428 mode of transmission of con- tagium, 344 morbid anatomy of, 439 multiple neuritis in, 429 myocarditis in, 406 noma in, 422 oedema of lungs in, 427 optic neuritis in, 406 orbital cellulitis in, 405 otitis media in, 400 paraplegia in, 429 partial eruptions, 389 pathology of, 436 pericarditis in, 444 period of infectivity of, 355 phlebitis in, 425 pleurisy in, 428 INDEX 777 SoaTlcl. I'(!vcr, prKMinifniiji in, .'Wl, 427 \.nv.\i\\('.nw. <»r, iiifliic'dcc, of ulM- l,u(l<^ on, '.Wl ol' cliiii.'U.t! on, .'M!) ol' Jocniil.y on, 1352 of a(!ii.son on, '.ihO prognosis oF, 457 prognostic infliuincc of age, 458 ol' (;oinj)lic!il.ion,s, 459 ol' viruldiicy, 45S prophylaxis ol', 45!> protozoa in, 'V,V,i puerperal, 359 purpura heinorrJiagica in, 420 rccurronces of, 393 relapses of, 393 respiratory symptoms, 380 return cases of, 356, 4()1 rubella, differential diagnosis of, 454 second attacks of, 392 secondary angina in, 397 septicitniia and otitis media in, 401 septic erythema in, 391 form of, 382 sequelae of, 430 serotherapy in, 374 simplex, 365 smallpox, differential diagnosis of, 454 stage of eruption, 369 of invasion, 365 strawberry tongue in, 448 streptococcus, 434 suppurative arthritis, 420 surgical, 361 symptomatology of, 363 symptoms, gastrointestinal, 381 respiratory, 380 throat, 369 synonyms of, 341 tetany in, 429 thrombosis of lateral sinus in, 403 tongue, 374 tonsillitis, differential diagnosis of, 454 treatment of, 374 of ears, 470 of enlarged glands, 469 of fever, 467 of gastroiiitestinal tract, 473 of heart, 473 of joints, 471 of Ludwig's angina, 470 medical, 467 of noma, 469 of purpura, 473 of purulent rliinitis, 469 of throat, 468 of uraemia, 472 typhoid, 387 urticaria in, 424 use of blood serum of convales- cents, 475 I Scarlet fever virulencf; influenr-ing fjrog- nosis, 458 vomiting in, 3(>(i vvitlioiit angina, 392 desquamation, 392 eruption, 390 fever, 388 Scarring after ehiekenpox, 32(i Scars after smallpox, 190 vaccination, 51 Scratchy heel, 139 Season and smallpox incidence, 154 iiifhu^nce of, on scarlet fever, 350 Second attacks of ehiekenpox, 319 of measles, 485 of rubella, 562 of scarlatina, 392 of smallpox, 151 Secondary angina in scarlet fever, 397 fever in smallpox, 183 toxic or septic rashes in smallpox, 196 umbilication in smallpox, 180 Septic diphtheria, 629 scarlet fever, 382 Septicaemia after vaccination, 64 in smallpox, 241 Sequelae of cliickenpox, 329 of diphtheria, 640 of rubella, 561 of scarlet fever, 395 of smallpox, 229 of typhoid fever, 583 Serum treatment of diphtheria, 730 of smallpox, 306 Sheeppox, 135 Sheffield smallpox statistics, 118, 119, 121 Ship fever. See Tj-phus, 566 Simple scarlet fever, 365 Skin complications in scarlet fever, 423 Sloughing of vaccine site, 63 Smallpox, 144 abscesses in, 229 age incidence of, 112 albuminuria in, 226 alopecia after, 191 in America, 147 atmospheric conditions and, 156 bacteriologv of, 256 baths in, 299 continuous warm, 300 bed-sores in, 231 blood in, 253 boils in, 229 in camel, 143 carbuncles m, 230 changes in bone-marrow in, 250 in heart in. 250 ixx kidneys in, 249 in liver in, 249 in hTnphatic glands in, 250 in skin in, 242 in spleen in, 249 in testicles in, 251 complications of abdominal, 237 ear, 235 778 INDEX Smallpox, complications of, heart, 236 nervous, 237 ocular, 231 respiratory, 236 and sequelae of, 229 confluent, 199 superficial, 212 conjunctivitis in, 232 corneal ulcer in, 233 in countries where vaccination is neglected, 132 critical days of, 279 cytoryctes variolse, 264 deaths among royalty from, 149 decline of, after introduction of vac- cination, 105 delirium in, 182 diagnosis of, 266 diet and stimulants in, 301 disinfection, 285 disseminated spinal sclerosis in, 241 dviration of isolation of, 287 effect of season on, 154 eruption upon mucous membranes in, 180 erysipelas complicating, 230 etiology of, 150 exfoliative dermatitis in, 196 fever in, 183 in foetus, 221 gangrene of scrotum in, 231 of skin in, 194, 231 hemorrhagic, 202 incubation period of, 166 infected sick-room objects, 160 infection of, 157 carried by healthy persons, 160 transmitted in the air, 161 infectious period, 157 infectiousness of blood in, 255 initial stage of, 167 inoculation of, in America, 25 insanity after, 237 insusceptibihty to, 150 involution of eruption in, 185 iritis in, 235 isolation of patients in, 282 itching in, 189 joint disease in, 237 local use of tincture of iodine, 311 macules, 174 mild type of, 206 modified, 209 in monkey, 143 mortality in prevaccination period, 275 in negroes, 154, 276 number of lesions present, 179 oedema of glottis in, 181 orchitis in, 237 otitis media in, 235 papules, 174 paralysis in, 238 paraplegia in, 239 pathology of, 242 of mucous membranes, 248 Smallpox, peripheral neuritis in, 241 phimosis in, 237 phlebitis after, 237 pigmentation after, 190 pleurisy in, 236 pneumonia in, 236 in pregnant women, 215 prevalence of, before discovery of vaccination, 106 prevention of pitting in, 308 prodromal rashes of, 171 prognosis of, 275 prophylaxis, 282 pseudokeloidal growths after, 230 pustules, 177 quarantine of, 283 rashes in, 196 scarlatiniform erythema, 196 scars of, 190 second attacks of, 151 septicaeinia and pysemia in, 241 in sheep, 135 sore throat in, 181 stage of decrustation, 186 of desiccation, 185 of eruption, 173 of suppuration, 176 streptococcus pyogenes in, 261 symptomatology of, 166 symptoms, favorable, 281 unfavorable, 281 toxic or septic rashes, 196 treatment of, 282 of eye complications, 313 local, 306 of nervous svmptoms, 297 red light, 304 serum, 306 of throat, 297 urine in, 171, 225 use of morphine in, 298 vaccinated and unvaccinated, 116 vaccination during the incubation of, 290 varieties of, 199 vesicles, 174 Sore throat in smallpox, 181 Spontaneous cowpox, 142 at Cohasset, 93 Spotted fever. See Typhus, 566 Spurious vaccination, 42, 49 Stage of decrustation in smallpox, 186 of desiccation in smallpox, 185 Statistical evidence of efficacy of vac- cination, 105 Statistics of the German Vaccination Law, 123 of revaccination, 120 of smallpox mortality before and after introduction of vaccination, 108 Strawberry tongue in scarlet fever, 374 Streptococcus pyogenes in smallpox, 261 in scarlet fever, 434 INDEX 779 Siilplmr (linxidc (liHiiii'cctJoii, 7(»;i inclliod of, IM (Siipixinilivc lever in ,sin;ill|)o\, \K', .sl.'ifie ol' sMi.'illpox, I7(> Siir^ie.'il se.'irlel. lexer, ;',(il Siiseepliliilily to VMceiiii.'M)!' irifjirirs horn of \;ifi()l()iis niolliers, 221 Sweden, iiil i-()diiei'ioii of \;icein;il ion in, 107 v;icein;ition made eoinpnlsory in, 107 smallpox (leaXlis before and after introduction of vaccination, 11 Symptomatoloify of cliici